He mate pukupuku tōu o te repe adrenal? Me kōrero tātou mō tēnei (Adrenocortical Carcinoma)!

Kei te mamae tō puku, kei te piki ohorere rānei tō taumaha? I ētahi wā, ka puta mai ēnei i tētahi āhuatanga kāore e tino kōrerohia ana, engari he mea nui kia mōhiotia. He āhuatanga e kiia nei ko te Adrenocortical Carcinoma . Kaua e manukanuka, tera pea he ahua uaua te ingoa, engari kia māmā noa iho.

He aha te matepukupuku Adrenocortical?

Ki te kī māmā noa, ko te adrenocortical carcinoma he mate pukupuku e puta ana i te paparanga o waho o ō repe adrenal , arā, te adrenal cortex . Whakaarohia ēnei repe he potae iti e rua i runga i ō whatukuhu. He mea tino nui ēnei nā te mea ka whakaputa i ngā homoni e whakahaere ana i ngā mea maha i roto i tō tātou tinana, tae atu ki tō tātou pākia o te tinana, te toto toto tiketike, me te āhua o tā tātou urupare ki te ahotea.

I tēnei wā, i roto i tēnei take o te mate pukupuku adrenocortical, ka puta ngā pukupuku matepukupuku i roto i ēnei repe adrenal. I ētahi wā ka taea e ēnei pukupuku te whakaputa i te nui o ngā homoni i roto i te tinana. Kātahi ka nui rawa te pikinga o ngā homoni i roto i te tinana, ka pā ki te mahi a tō tātou tinana. Ka taea e ētahi pukupuku te tipu tere, ā, ka taea hoki te pēhi i ētahi atu okana huri noa i a rātou. Ahakoa ka taea e ngā tākuta te rongoā i tēnei mate i ētahi wā, i ētahi wā ka hoki anō tēnei mate.

Ahakoa he mea noa tēnei mate i roto i ngā pakeke, ka taea e ngā tamariki te whanake i ētahi wā. Heoi, i roto i tēnei tuhinga, ka arotahi mātou ki te adrenocortical carcinoma, e pā ana ki ngā pakeke.

He momo mate pukupuku adrenocortical anō kei reira?

Āe, e rua ngā momo matua. He rerekē anō hoki ngā tohu o ēnei momo e rua.

1. Ngā pukupuku e mahi ana: Koinei te momo tino noa. He nui ake ngā homoni pēnei i te aldosterone , te cortisol , te estrogen, me te testosterone e whakaputaina ana e ēnei pukupuku i te mea e tika ana. Nō reira, ko ngā tohu e whakawhirinaki ana ki te momo homoni e whakaputaina ana i te nui rawa.

2. Ngā pukupuku kore mahi: Kāore ēnei pukupuku e pā ki te hanga homoni. Heoi, ka taea e rātou te tipu nui me te pēhi i ngā whekau me ngā kiko e karapoti ana, ka puta te mamae.

He pēhea te noa o tēnei āhuatanga?

He mate pukupuku tino onge tēnei. Ahakoa koinei te momo mate pukupuku tino noa e puta ana i roto i ngā repe adrenal, he tino onge katoa. Tata ki te kotahi i roto i te miriona tāngata ka kitea tēnei mate i ia tau. Nō reira kaua e mataku ki te ingoa.

He aha ngā tohu o te mate pukupuku adrenocortical?

He mea whakamiharo te āhua o te pāngia o ētahi tāngata e tēnei mate pukupuku engari kāore he tohu.Kāore e puta. Kua whakaatuhia e ngā rangahau kei waenganui i te 20% me te 30% o ēnei tūroro ka kitea ā-tūponotia i te wā o te whakamātautau whakaahua mō tētahi atu mate.

Heoi, ina puta mai ngā tohu, ka kite pea koe i ngā mea penei:

• Te mamae o te puku, te koretake rānei.
• Te tupu huruhuru rerekē i te mata, i te tinana rānei o ngā wāhine (hirsutism). Ka rite ki te mea kei te tupu te pahau o te tāne.
• Te whakanui i ngā ū i roto i ngā tāne (Gynecomastia).
• Te toto toto tiketike.
• Te huka toto tiketike.
• Te pikinga o te taumaha, inā koa ki te mata, ki te kaki, me te tinana. Me te mea kua nui haere te taumaha o tētahi.

He pēhea te kaha o te mate pukupuku adrenocortical?

He mate pukupuku tino kaha tēnei. Ko te tikanga ka tere te tipu o te pukupuku, ka horapa (metastasize) ki waho o te repe adrenal ki ētahi atu wāhanga o te tinana, pērā i ngā pukahukahu me ngā wheua. Kia horapa, ka uaua ake te rongoā.

He aha ngā pūtake o te mate pukupuku adrenocortical?

Kāore anō kia kitea e ngā kairangahau te tino take . Ko ētahi tāngata ka pāngia e te mate nā runga i ētahi āhuatanga ira e tukuna iho ana i ia whakatipuranga. Ko te tikanga tēnei, mēnā kei roto i te whānau tētahi o te mate, ka nui ake te tūponotanga o ētahi atu ki te pāngia anō hoki.

I ētahi atu wā, ko ētahi whakarerekētanga ira te āhua nei ka whakanui ake i te mōrearea. Hei tauira, kua kitea e ngā rangahau ka taea e ngā panonitanga o ngā ira pehi pukupuku (TP53) me te (IGF2) te arahi ki tēnei mate pukupuku. He māmā noa iho, ko ngā ira pehi pukupuku he ira e whakahaere ana i te tipu o ō tātou pūtau. Mēnā he panonitanga kei roto i ēnei ira, ka taea e ngā pūtau te wehewehe me te whakanui me te kore e taea te whakahaere, ā, ka noho hei mate pukupuku.

He aha ngā āhuatanga tuku iho ka whakanui ake i taku mōrearea?

He nui ake tō tūponotanga ki te pāngia e te mate pukupuku adrenocortical mēnā kei a koe tētahi o ngā āhuatanga tuku iho e whai ake nei:

• Te mate Beckwith-Wiedemann
• Te matatini o Carney
• Te polyposis adenomatous whānau (FAP)
• Te mate Li-Fraumeni
• Te mate Lynch
• He maha ngā momo neoplasia endocrine 1 (MEN1)
• Neurofibromatosis Momo 1 (NF1)
• Te mate Von Hippel-Lindau (te mate VHL)

Mena kei roto i tō whānau ēnei āhuatanga, he mea pai kia kōrero koe ki tētahi tākuta, kia ako ai hoki mō ngā whakamātautau ira.

He aha ngā raruraru ka pā mai i te adrenocortical carcinoma?

Ka tere rawa te horapa (metastasizes) o tēnei mate pukupuku.Āe. He tino uaua ki te rongoā ina horapa ki waho o te repe adrenal. Waihoki, ka taea e ētahi pukupuku whakaputa homoni te whakaputa i ngā āhuatanga pēnei i:

• Te mate a Cushing: Nā te nui rawa o te homoni cortisol e whakaputaina ana e ngā repe adrenal tēnei. Ko ngā tohu ko te mata pupuhi me te tinana pupuhi.
• Te mate a Conn: Ka puta tēnei āhuatanga i te nui rawa o te hanga o te homoni aldosterone. Ka taea e ia te whakaputa i ngā āhuatanga pēnei i te toto toto tiketike.

Me pēhea te tātaritanga o te mate pukupuku adrenocortical? (Tauātanga)

Mena ka kitea he pukupuku repe adrenal koe i te wā e whakamātautau ana mō tētahi atu mate, mēnā rānei kei a koe ngā tohu kua whakahuatia i runga ake nei, ka whakahaerehia e tō tākuta ngā whakamātautau pēnei i:

• Ngā whakamātautau whakaahua: Ngā whakamātautau pēnei i te matawai MRI, te matawai CT, te matawai PET rānei hei tirotiro mēnā he pukupuku kei roto.
• Ngā whakamātautau toto me te tātaritanga mimi: Tirohia ō taumata homoni.
• Biopsy: Ka mahia tēnei whakamātautau hei whakaū mēnā he matepukupuku te puku, hei tiki tauira kiko rānei.

He aha ngā wāhanga o te mate pukupuku adrenocortical?

Ka whakamahia e ngā tākuta te whakatau i te taumata o te mate pukupuku hei whakamahere i te maimoatanga me te whakatau i ngā mea ka tumanakohia i muri i te maimoatanga (matapae). Ka whakatauhia te taumata o te mate pukupuku adrenocortical e te rahi o te pukupuku, tōna tauwāhi, me te mea kua horapa ki ngā kōpū lymph tata , ki ngā whekau tawhiti rānei.

Anei ngā wāhanga matua:

• Wāhanga I: E 5 henimita (tata ki te 2 inihi) te rahi o te pukupuku, he iti iho rānei. Kāore anō kia horapa ki waho o te repe adrenal.
• Wāhanga II: He nui ake te pukupuku i te 5 henimita, engari kāore anō kia horapa ki tua atu i te repe adrenal.
• Wāhanga III: Kua horapa te pukupuku ki ngā kōpū lymph tata.
• Wāhanga IV: Kua horapa te pukupuku ki ngā kōpū lymph tata, ki ngā whekau tata, ki ngā whekau tawhiti rānei.

He āhua pōhēhē pea ngā kōrero mō te taumata o te mate pukupuku i ētahi wā. Nō reira kaua e mangere ki te pātai atu ki tō tākuta mō ētahi whakamārama. Pātai atu hoki me pēhea te pānga o tēnei ki tō āhua.

He aha ngā maimoatanga mō te mate pukupuku adrenocortical?

Ko te maimoatanga tino noa ko te tango i te adrenal , arā, ko te tango i tētahi, i ngā repe adrenal rānei e rua mā te pokanga. Hei tāpiri, he maha ngā tākuta e tohu ana i ngā rongoā pēnei i:

• Mitotane (Mitotane (Lysodren®)):Ka mahi tēnei rongoā mā te whakawhāiti i te mahi a ngā repe adrenal. Ka taea e tēnei te whakaiti i te tūponotanga o te hokinga mai o te mate pukupuku. Ka whakamahia tēnei rongoā i muri i te tangohanga o tētahi repe adrenal, i te wā rānei kāore e taea te pokanga. Nā te mea ka aukati tēnei rongoā i te hanga homoni, me tango hoki e te hunga e tango ana i ngā pire homoni.
• Metyrapone (Metopirone®): Ka taea te tohu i tēnei momo rongoā hei whakaiti i ngā tohu e puta mai ana i te nui rawa o te hanga homoni e ngā ovaries.

Heoi, i ētahi wā, tera pea he nui rawa te pukupuku, kāore e taea te tango haumaru mā te pokanga ina kitea te mate. I ēnei wā, ka whakamahia pea e ngā tākuta te chemotherapy . Ahakoa kāore e taea e tēnei maimoatanga te whakakore katoa i te pukupuku matepukupuku, ka taea e ia te whakaiti i ngā tohu me te whakaroa i te tipu o te pukupuku.

Akene ka hiahia koe ki te whakaaro ki te tiaki mamae hei wāhanga o tō maimoatanga. Ko te tiaki mamae he momo maimoatanga e āwhina ana ki te whakahaere i ngā tohu me ngā pānga taha o te maimoatanga. Ka taea hoki e ngā tohunga tiaki mamae te whakarato i te tautoko hinengaro me te tautoko kare ā-roto ki a koe.

He aha ngā raruraru, ngā pānga taha rānei o te maimoatanga?

Ka taea e te pokanga me ngā rongoā te whakaputa i ngā raruraru maha, i ngā pānga taha rānei. Hei tauira, ka taea e te pokanga hei tango i te repe adrenal te whakaputa i ngā mea penei:

• Ngā pānga ki te hanga homoni: I te nuinga o te wā, ka tangohia e te repe adrenal e toe ana te mahi a te repe kua tangohia, ā, ka whakaputa i ngā homoni e ranea ana. Heoi, ki te kore tēnei e tupu, me tango pea e koe ētahi atu pire homoni kia puta rā anō ngā homoni e te repe e toe ana. Ka kiia hoki tēnei āhuatanga he koretake o te adrenal .
• Mate urutā: Ka pā pea ngā mate urutā ki roto i te puku, ki te wāhi rānei i pokangahia ai.
• Te toto nui rawa: Ka puta pea tēnei i te wā o te pokanga, i muri rānei i te pokanga.

He aha ngā raruraru, ngā pānga taha rānei o te rongoā?

Tērā pea ka tūtohu tō tākuta kia tangohia e koe te mitotane mō ngā tau e rua ki te rima i muri i te pokanga. Ko ngā pānga taha o te mitotane ko:

• Whakapairuaki me te ruaki
• Korere
• Ngā ponana kiri
• Pōhēhētanga

He aha ngā ōrau oranga mō te mate pukupuku adrenocortical?

I te katoa, e 50% o te hunga e pangia ana e te mate pukupuku adrenocortical e ora tonu ana i muri i te rima tau o te tātaritanga. Heoi, ko tēnei reiti oranga e whakawhirinaki ana ki ngā āhuatanga maha. Hei tauira:

• Te wāhanga o te mate pukupuku i te wā i tautuhia ai.
• Ahakoa kei te kaha te puku (e whakaputa ana i ngā homoni) kāore rānei i te kaha.
• tō tau.
• Tō hauora whānui.

Ko te reiti oranga mō ngā tau e rima i ia wāhanga koia tēnei:

• Wāhanga Tuatahi: 81%
• Wāhanga II: 61%
• Wāhanga III: 50%
• Wāhanga IV: 13%

Tērā pea ka mataku koe, ka manukanuka hoki i ēnei tatauranga. He mea noa tēnā. Engari kia mahara, i ahu mai ēnei tatauranga i ngā wheako o mua. Ka inehia e ngā tohunga ēnei reiti oranga i ia rima tau. He maha ngā mea ka taea te huri i roto i ngā tau e rima, ā, ka pā pea aua huringa ki ngā hua. Waihoki, kia maumahara ehara ēnei reiti oranga i te whakatau tata mō te roa o tō oranga.

Mena he pātai āu mō te oranga tonutanga mai i te mate pukupuku, kōrero ki tō tākuta. Ko ia te puna kōrero pai rawa atu māu, nā te mea ko ia te mea e mōhio ana ki tō āhuatanga.

Ka taea te ārai i te mate pukupuku adrenocortical?

Kāo, kāore e taea te ārai. E mōhio ana ngā kairangahau tata ki te haurua o ngā mate pukupuku adrenocortical ka puta mai i ngā whakarerekētanga ira i roto i ētahi ira e meinga ai ngā pūtau matepukupuku kia nui haere, kia hanga pukupuku. Heoi, kāore anō kia mōhiotia e rātou he aha te take o ēnei whakarerekētanga ira. Nō reira, kāore e taea e rātou te tūtohu i ngā huarahi hei ārai i a rātou kei puta.

Heoi anō, ka piki ake te mōrearea o te whakawhanake i tēnei mate i ētahi āhuatanga tuku iho. Mena he hītori whānau tōu mō ēnei āhuatanga, he mea pai kia kōrero koe ki tētahi tākuta me te ako mō ngā whakamātautau ira e taea ai te tautuhi i ngā whakarerekētanga ira e puta ai ēnei āhuatanga.

Me pēhea taku tiaki i ahau anō? (Me pēhea taku tiaki i ahau anō?)

He mate pukupuku onge te mate pukupuku adrenocortical, he mate pukupuku e hokihoki pinepine ana. Ka taea e ēnei wero e rua te whakawehi i a koe, te whakamomori, me te manukanuka. Waimarie, kei reira ētahi mahi ka taea e koe te mahi hei āwhina:

• Kimihia he tautoko: Pātai atu ki tō rōpū hauora mō ngā rōpū tautoko mō te hunga e pāngia ana e te adrenocortical carcinoma. He mea āwhina te whakapau wā me te kōrero ki te hunga e pāngia ana e ngā āhuatanga ōrite e pā ana ki a koe.
• Whakaarohia ngā kaupapa oranga mō te mate pukupuku: He maha ngā tāngata e pāngia ana e te mate pukupuku adrenocortical e mataku ana kei hoki mai anō te mate pukupuku. Ko ngā kaupapa oranga mō te mate pukupuku tētahi rauemi hei āwhina i te whakatau i taua manukanuka.
• Me haere tonu te tiaki mamae: Mena ka whiwhi koe i te chemotherapy i muri i te pokanga, tera pea ka hiahia koe ki te awhina ki te whakahaere i nga paanga taha o te maimoatanga.

Āhea ahau me toro atu ki taku tākuta?

He maha ngā wā ka hoki mai anō te mate pukupuku adrenocortical, inā koa i roto i ngā tau tuatahi e rua i muri i te pokanga. Ka whakaritea e tō tākuta he wā tirotiro hei aroturuki i ngā tohu o te hokinga mai o te mate. Hei tauira:

• Ngā whakamātautau whakaahua: Ia toru marama mō ngā tau e rua, kātahi ia toru ki te ono marama mō ētahi atu tau e toru.
• Ngā whakamātautau toto: Ka whakahaerehia e tō tākuta he whakamātautau toto auau hei tirotiro i ngā taumata homoni.

He aha ngā pātai me pātai atu e au ki taku tākuta?

He mate onge te mate pukupuku adrenocortical. Tērā pea he maha āu pātai mō ngā mea hei tumanako atu māu. Anei ētahi pātai e whakaaro ana mātou ka whai hua pea māu:

• He aha te tikanga ina kaha, ina kore rānei he mahi a te pukupuku?
• Kua horapa te pukupuku ki waho o taku repe adrenal? Mena koinā, kia pēhea te tawhiti?
• He aha ngā kōwhiringa maimoatanga kei a au?
• He aha ngā pānga taha o te maimoatanga?
• Me whakamātau ahau i ngā ira mō ngā whakarerekētanga ira e hua ai te mate pukupuku adrenocortical i roto i tōku whānau?
• Mena ka angitu te maimoatanga, he aha te tūponotanga ka hoki mai anō te pukupuku?

He mate pukupuku onge, kaha te mate pukupuku adrenocortical e pā ana ki tō repe adrenal. Tērā pea kāore he tohu e puta mai ana, ā, he maha ngā tāngata ka kitea i roto i ngā whakamātautau mō tētahi āhua tino rerekē. Tērā pea kei te āwangawanga koe, kei te mataku hoki mō tō tautuhi me te rongo ka hoki mai anō tō mate pukupuku adrenocortical i muri i te maimoatanga.

Ki te mea kei te pōuri koe i tēnei mate, me whai wā koe ki te mārama ki ngā āhuatanga e pā ana. Kaua e mangere ki te pātai mō ngā maimoatanga me te pānga ki a koe. Ka mārama ō tākuta ki te take e pāngia ai koe e ētahi tauhohenga. Ka noho rātou ki reira hei whakautu i ō pātai, mai i te tātaritanga, tae noa ki te maimoatanga, me ngā tau o te aroturukitanga.

Karere Tangohia ki te Kāinga

Ahakoa he mate kino te adrenocortical carcinoma, he mea nui kia mōhio ki tēnei āhuatanga, kia rapu tohutohu hauora tika, me te rapu tautoko.

• He mate pukupuku onge tēnei: ​​nō reira kaua e ngakaukore ki te ingoa.
• Kia tūpato ki ngā tohu: Kia tūpato ki ngā āhuatanga pēnei i te mamae o te puku, te pikinga taumaha rerekē, me ngā huringa homoni.
• Rapua he tohutohu hauora tonu: Ki te ruarua koe, tirohia he tākuta, ā, me tirotirohia koe.
• He maimoatanga kei reira: te pokanga, ngā rongoā, te chemotherapy, me ētahi atu. Mā tō tākuta e whakatau ko tēhea maimoatanga te mea pai mōu.
• He mea nui te tautoko hinengaro: Kāore koe i te mokemoke i tēnei haerenga. Kōrero ki te whānau, ki ngā hoa, me ngā rōpū tautoko.

Kia maumahara, he rerekē ia tūroro. He motuhake tō āhua, tō maimoatanga, me tō haerenga whakaora. Kaua e mutu te tumanako. Mahi tahi me tō tīma hauora, me te whakatata atu ki tēnei wero me te waiaro pai.

Matepukupuku adrenal , matepukupuku adrenal, pukupuku repe adrenal, pukupuku whakaputa homoni, cortisol, aldosterone, pokanga adrenal, mitotane