I ētahi wā, kāore tātou i te tino mōhio ki ngā mea e pā ana ki roto i ō tātou tinana, āe? Kua pāngia koe e te whero ohorere, te uaua ki te manawa, te mamae o te puku, me te korere? Ehara ēnei i te mea noa iho. I ētahi wā, he tohu pea ēnei o tētahi mate onge e kiia nei ko te Carcinoid Syndrome. Me kōrero taipitopito tātou mō tēnei i tēnei rā.
He aha te Mate Carcinoid?
He whakarāpopototanga noa iho, ko te mate carcinoid he kohinga tohu e puta mai ana i tētahi momo tipu matepukupuku i roto i tō tinana e kiia nei ko ngā pukupuku neuroendocrine (NET) . Ko ēnei pūtau neuroendocrine he momo pūtau motuhake e uru ana ki roto i ā tātou pūnaha io me ngā pūnaha homoni. Ka puta ngā NET ina wehea ohoreretia, ka tere te whakanuia o ēnei pūtau, ka hanga he pukupuku.
Tērā pea kei te whakaaro koe mēnā he mate tēnei e pā ana ki te katoa. Kāo, he mate onge tēnei. E whakaatu ana ngā rangahau tata ki te kotahi i roto i te rima o ngā tāngata he pukupuku neuroendocrine (NET) ō rātou ka pāngia e te mate carcinoid. Kāore hoki i te tino noa ngā NET, me te whakatau tata ki te 5 i roto i te 100,000 i te United States.
Ka tukuna e ēnei NET, inā koa ko ērā kei roto i tō ara kai, i tō pukahukahu rānei, he nui ngā homoni pērā i te serotonin me ētahi atu matū ki roto i te tinana i te wā kotahi. Koinei te wā ka puta mai ngā tohu o te mate carcinoid. I ētahi wā, ka mōhio tuatahi koe kei a koe he NET i muri i te putanga mai o ngā tohu o tēnei mate.
He tino onge, ki te kore e tika te tātaritanga me te rongoā i tēnei mate carcinoid, ka arahi pea ki tētahi āhuatanga ohorere e morearea ana ki te ora e kiia nei ko te 'raruraru carcinoid'. Nō reira, he mea tino nui kia mōhio ki tēnei.
He aha ngā tohu o te Carcinoid Syndrome?
Me titiro tātou ki ngā tohu tino kitea o tēnei mate. Tirohia mēnā kei a koe tētahi o ēnei tohu, takitahi:
- Te whero o te mata: He ahua whakamā tēnei. He rite ki te whero o te mata ina whakama koe, engari ki te puta pinepine, kāore he take, me āwangawanga koe.
- Te whewhe me te poto o te manawa (dyspnea): Tērā pea ka rite ki te uaua ki te manawa, ki te rite rānei ki te tangi whewhe e puta mai ana i te uma.
- Te mamae o te puku me te mate korere e tere ana, e pū ana: He mamae puku me te mate korere kino tonu. I ētahi wā he uaua ki te whakahaere.
- Ngā paru momona e haunga kino ana: Tērā pea te āhua hinuhinu o te paru, ā, he haunga rerekē.
- Te pupuhi, te pupuhi rānei o ō waewae me ō waewae:He tohu pea tēnei i ētahi wā o te ngoikore o te ngākau, nō reira he mea nui kia rapu tohutohu hauora tonu.
- Te hekenga o te hiahia moepuku, te ngoikore rānei o te ure i roto i ngā tāne: Tērā pea ka pāngia ētahi tāngata e ēnei āhuatanga.
- Te kōwhai o te kiri me te mā o ngā kanohi (Jaundice): Koinei te mea e kīia nei e tātou ko te 'jaundice'. Tērā pea he raruraru ate.
- Te whanoke, te ngoikore rānei: He tohu pea tēnei o te toto toto iti.
- Te ahua kei te tere haere te pao o tō ngākau: Tērā pea kei te tere haere te pao o tō uma.
Ki te mau tonu tētahi, ētahi rānei o ēnei tohumate ki a koe, me toro atu ki tētahi tākuta hei matapaki i ēnei. He tohumate anō hoki ēnei nō ētahi atu mate, engari he mea nui kia whakaūtia kei a koe te mate carcinoid.
He aha i puta ai tēnei mate carcinoid?
E ai ki taku kōrero i mua, ka puta te mate carcinoid mēnā he pukupuku neuroendocrine (NET) tōu. Ko ēnei NET he pukupuku e puta mai ana i ngā pūtau motuhake i roto i tō pūnaha neuroendocrine. Ka whakaputa, ka tuku hoki ēnei pūtau i ngā homoni ki roto i te tinana.
I te nuinga o te wā, ka taea e ēnei NET te whanake i roto i ngā wāhi pēnei i tō ara kai, i ō pukahukahu, me tō repeure. Heoi, ko te mate carcinoid te nuinga o te wā ka puta mai i ngā NET i roto i te ara kai, i ngā pukahukahu rānei e tuku ohorere ana i te nui o ngā homoni (ina koa ko te serotonin) ki roto i te toto.
Whakaarohia he rite ki te pūwero e tahuri mārire ana ki te wai, he iti noa te tukunga o ngā homoni e ēnei pūtau. Engari ina puta he NET, he rite ki te mea kua tahurihia te pūwero kia tuwhera rawa, ā, he maha ngā homoni e puta mai ana i te wā kotahi. Koinā te wā ka puta mai ai ngā tohu o tēnei mate.
Ko wai kei te mōrearea nui ake ki te whakawhanake i te mate carcinoid?
Ko te tino take mōrearea mō tēnei ko te whai pukupuku neuroendocrine (NET) i roto i tō ara kai, i tō pukahukahu rānei . Ara, ko te mate carcinoid kāore e puta me te kore he NET.
Arā, ki te mea kua tāpaetia koe ki te mate NET, me āwangawanga anō hoki koe mō tēnei mate. I ētahi wā, ki te mea kua pāngia tētahi o te whānau e te NET, ka taea hoki tēnei te waiho hei take mōrearea ki tētahi taumata, engari he tino onge.
He aha ngā raruraru ka pā mai i te Carcinoid Syndrome?
Ehara te mate carcinoid i te huinga tohu noa iho, engari ka arahi pea ki ētahi raruraru nui. Ko tētahi o aua mate ko te 'raruraru carcinoid' e morearea ana ki te ora i kōrerotia e au i mua ake nei.
Me titiro tātou ki ētahi atu raruraru:
- Te mate ngakau carcinoid:He mea onge hoki tēnei, engari ka taea te whakararu i te ora. Ka pāngia te arai o ngā rūma o tō ngākau, o ngā takirere, me ngā oko toto e ngā homoni e tukuna ana e ngā NET. Ka taea hoki e tēnei te arahi ki te ngoikore o te ngākau.
- Te mate pukupuku o te puku: Ka taea e ngā NET te whakamumura me te whakakorikori i te mesentery, te kiko e hono ana i ō whekau ki te pakitara o tō puku. Ka taea e tēnei te whakararuraru i te mahi a te puku.
- Pouri: Ka pāngia te kaha o tō tinana e te mate carcinoid ki te whakamahi i tētahi waikawa amino nui e kiia nei ko te tryptophan. Ka āwhina te tryptophan ki te hanga serotonin. He matū roro te serotonin e whakahaere ana i ngā mea pēnei i te wairua, te whanonga, me te moe. Nō reira, ka taea e ngā taumata serotonin iti te arahi ki te pouri.
Ko te āhua morearea e kiia nei ko te mate carcinoid
He tino onge te mate pukupuku carcinoid engari he āhuatanga ohorere pea ka morearea te ora . Ka puta pea tēnei hei hua o te pokanga, o ētahi atu tikanga hauora, o te whara rānei i puta mai i tētahi aituā.
Ko ngā āhuatanga o tēnei:
- Ngā huringa nui o te toto toto: Ka taea e te toto toto te heke ohorere ki raro rawa (hypotension) te piki rawa rānei ki runga rawa.
- Te whero nui: Ka whero whakarere te tinana katoa, ā, ka wera pea.
- Te uaua ki te manawa (Dyspnea): Tērā pea ka puta he poto rawa o te manawa.
- Pōhēhē: Tērā pea ka rite koe ki te mea kei te whakararuraruhia tō hinengaro.
He mea tino nui kia mauria e te tangata he mate carcinoid, he pukupuku neuroendocrine (NET) rānei, he kāri e whakaatu ana i tōna āhua. He tino āwhina tēnei mēnā e hiahia ana rātou ki te awhina hauora ohorere. Waihoki, mēnā ka pokanga koe, he mea nui kia kōrero koe ki ō tākuta mō tēnei āhua. Kātahi ka taea e rātou te hoatu rongoā ki a koe i mua atu, i te wā hoki o te pokanga hei whakaiti i te tūponotanga o te 'carcinoid crisis'.
Me pēhea te tautuhi i te mate Carcinoid?
He maha ngā whakamātautau e whakamahia ana e ngā tākuta hei tātaritanga i tēnei mate. Me titiro tātou ki ēnei:
- Whakamātautau mimi: Ka tirohia e tēnei te taumata o ētahi homoni i roto i tō mimi, inā koa he hua taha o te serotonin e kiia nei ko te 5-HIAA (5-hydroxyindoleacetic acid) .
- Te whakamātautau tinana me te hītori hauora: He rite tonu ngā tohu o te mate carcinoid ki ērā o ētahi atu mate iti ake te kino, nō reira ka pātai atu tō tākuta ki a koe mō ō tohu, te roa o te wā e pāngia ana, me te mea kei te kino haere.
- Ngā whakamātautau toto:Ka tirohia e ēnei ngā taumata o ngā matū ka tukuna ki roto i te toto mai i ō whekau me ō kiko. Mēnā ka piki, ka heke rānei ngā taumata o ētahi matū, he tohu pea tēnei nō te mate. Hei tauira, ka tirohia e rātou tētahi tohu e kiia nei ko te Chromogranin A.
- Matawai Neuroendocrine Positron Emission Tomography (PET): He matawai motuhake tēnei e whakamahi ana i tētahi tae e kiia nei ko te gallium 68 dotatate hei kimi i te wāhi o ngā pukupuku neuroendocrine (NET).
- .. (Computed Tomography (CT) scan): CT X- (3D) . .
- Matawai Ultrasound: Ka whakamahia ngā ngaru oro hei hanga whakaahua o ngā whekau.
- Matawai MRI (Whakaahua Āhua Aukume (MRI): Ka whakamahia he aukume nui, ngā ngaru reo irirangi, me te rorohiko hei whakaputa whakaahua taipitopito o roto o te tinana.
- (Endoscopy): , , . , .
He aha ngā maimoatanga mō te Carcinoid Syndrome?
Ko ngā pukupuku neuroendocrine (NET) te pūtake o te mate carcinoid. Nō reira, ina rongoatia aua pukupuku, ka rongoatia hoki te mate.
He maha ngā tikanga maimoatanga matua:
- Pokanga: Ka taea te tango katoa, te whakaiti rānei i te rahi o ngā pukupuku neuroendocrine. Ko te momo pokanga ka whakawhirinaki ki te wāhi me te rahi o te pukupuku.
- (Somatostatin analogs): . . (metastasis), . (Octreotide) (Lanreotide) .
- Whakaora arotahi: He tikanga maimoatanga motuhake anō hoki tēnei hei patu i ngā pūtau matepukupuku. I roto i tēnei, ka hoatu he rongoā hei arotahi ki ngā ira motuhake, ki ngā pūmua rānei i roto i ngā pūtau matepukupuku.
- Te rongoā matū: Ka whakamahia ngā rongoā hei patu i ngā pūtau matepukupuku. Kāore te rongoā matū e mahi ōrite mō ngā momo NET katoa.
- Te Whakapūngao: I tēnei tikanga, ka āraia te oko toto e tuku toto ana ki te pukupuku, ka whakangaro i te pukupuku. He maimoatanga tēnei e whakamahia ana mō ngā NET i roto i te ate.
Ka taea te ārai i te mate Carcinoid?
Tino,Kāore he huarahi hei ārai i te mate carcinoid nā te mea e pā ana ki ngā pukupuku neuroendocrine (NET). Nā te mea kāore he huarahi e mōhiotia ana hei ārai i te whanaketanga o ngā NET, kāore he huarahi hei ārai i ngā tohu e puta mai ana i aua tohu.
Heoi, ki te mōhio koe kei a koe te NET, mā te mōhio wawe ki ngā tohu o te mate carcinoid me te tīmata maimoatanga ka taea te whakaiti i te tūponotanga o ngā raruraru.
Me pēhea taku tiaki i ahau anō? / Me pēhea taku whakahaere i ngā tohumate?
Mena kei a koe te mate carcinoid, tera pea kei a koe he pukupuku neuroendocrine (NET). Nō reira, ki te mea kei a koe ngā tohu o te mate carcinoid, me kōrero tonu atu ki tō tākuta. Ka taea e rātou te arotake i tō āhua me te taunaki i ngā whakamātautau e tika ana kia kite ai mena kei a koe he NET.
Ko ngā tohu matua e toru o te mate carcinoid ko te whero o te kiri, te wheezing, me te korere. Anei ētahi mea ka taea e koe te mahi hei āwhina i te whakahaere i ēnei:
- Te whero o te mata: Koinei te urupare a tō pūnaha io ki te ahotea tinana, hinengaro rānei. Hei whakaiti i tēnei, manawa hōhonu, murua tō mata me tō uma ki te kakahu haukū, hopukia rānei he hau hou ki waho. Ka āwhina anō hoki te karo i te waipiro.
- Te whewhe: Mō te poto o te manawa, ngana ki te inu tī otaota, ki te whakamahi rānei i tētahi mea whakapūngao, i tētahi mea whakapūngao rānei . Ki te kaipaipa koe, ngana ki te whakamutu. Ka taea e te kaipaipa te whakamumura ake i ō ara manawa.
- Korere: Mena he raruraru tō te korere, kōrero ki tō tākuta mō ngā huarahi hei whakaiti i tōna auau me tōna kaha. He rongoā motuhake kua hangaia hei whakahaere i te korere i puta mai i te mate carcinoid. Waihoki, ko ngā kai momona, ngā kai raukikī, me ngā kai miraka ka kino ake tēnei āhuatanga mō ētahi tāngata. Nō reira kia tūpato ki tāu e kai ana.
Āhea ahau me haere ki te tākuta? / Āhea ahau me haere ki te rūma ohorere?
Ki te kino haere ō tohumate o te mate carcinoid, me toro atu ki te tākuta. Ki te mea kei te rongoatia koe mō te NET, me kōrero ki tō tākuta mēnā ka kite koe i ētahi huringa hou i roto i tō tinana e rite ana ki ngā tohumate NET. Kāore pea ēnei huringa e pā ana ki tō tātaritanga NET, engari ko te huarahi pai ki te mōhio ko te kōrero ki tō tākuta. Waihoki, ki te kino haere ō tohumate, ō pānga taha rānei i puta mai i tō maimoatanga, me kōrero ki tō tākuta.
Āhea te haere ki te Wāhanga Maimoatanga Ohotata (ETU)
Ki te kore e rongoatia te mate carcinoid, ka kino haere ngā tohu i roto i te wā, ā, ka huri hei mate morearea e kiia nei ko te 'carcinoid crisis'. Nō reira, haere tonu ki te tari ohorere o te hōhipera mēnā kei a koe ēnei āhuatanga:
- Mena he tere te tere o te manawa, he mamae rānei o te uma.
- Mena he nui te mate korere e pāngia ana e koe mō ētahi rā.
- Mena he mamae nui tō puku.
- Ki te ngoikore koe.
- Mena ka puta he whero ohorere, he nui hoki o te mata, o te kaki, me te uma (he whero nui).
He aha ngā pātai me pātai atu e au ki taku tākuta?
He tohu pea te mate carcinoid kei a koe he pukupuku neuroendocrine (NET). Nō reira, ki te mea he pātai āu mō te mate carcinoid, tera pea he maha āu pātai mō ngā NET. Anei ētahi pātai ka taea e koe te pātai ki tō tākuta:
- Mena kei a au te mate carcinoid, me pēhea taku mōhio mena he pukupuku neuroendocrine tōku?
- Mena he pukupuku tōku, kei hea i roto i tōku tinana?
- He aha ngā maimoatanga mō taku pukupuku?
- He aha ngā pānga taha o te maimoatanga?
- Ka taea te whakaora katoa i te pukupuku neuroendocrine i puta ai taku mate carcinoid?
- Ka taea e te mate carcinoid te hoki mai anō i muri i te rongoā o taku pukupuku neuroendocrine?
Karere Whakamutunga mō te Tango ki te Kāinga
He mate onge te Carcinoid Syndrome ka pā ki te tangata he pukupuku neuroendocrine (NET). He maha ngā wā, kua mōhio kē te hunga whai carcinoid syndrome kei a rātou he NET. I ētahi wā, ka mōhio tuatahi te tangata kei a rātou he NET i muri i te tātaritanga o te mate carcinoid.
Ko te mea pai rawa atu, ka taea te rongoā i ngā NET. Ko te mōhio kei a koe te mate pukupuku carcinoid te taahiraa tuatahi ki te kimi mēnā kei a koe te mate pukupuku, ā, mēnā kei a koe, me pēhea te rongoā. Nō reira, mēnā kua kitea tō mate pukupuku carcinoid, kaua e wehi ki te kōrero ki tō tākuta me te pātai atu he aha ngā mahi e whai ake nei hei whakaū mēnā kei a koe ngā NET. Ko te mea nui ko te tātaritanga me te rongoā wawe.
Kia maumahara, ehara i te mea ko koe anake. I roto i tēnei āhuatanga, he mea tino nui kia whai i ngā tohutohu hauora me te rapu tautoko a tō whānau.
Te mate Carcinoid, ngā pukupuku neuroendocrine, ngā NET, serotonin, ngā tohu, te mate pukupuku, ngā homoni











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