Kei te pāngia hoki koe e te mate korere wai i te roanga o te rā? Ahakoa te nui o te wai e inuhia ana e koe, kāore e tupu? Me ara ake anō hoki koe i ngā wā katoa, i ētahi wā i te pō, ki te mimi? Ahakoa ka mimi koe, he nui ō mimi wai mārama? He mea nui pea tēnei ki a koe. Ka karangatia tēnei mate ko te Central Diabetes Insipidus, ko te 'Central Diabetes Insipidus (CDI)' rānei. Ahakoa he "mate huka" kei roto i te ingoa, ehara tēnei i te mate huka e mōhiotia ana e tātou katoa. Me kōrero taipitopito tātou mō tēnei.
He aha te mate huka matua (CDI)?
He kupu ngāwari noa iho, he tino onge te mate "Central Diabetes Insipidus" (CDI). Ko te mea ka tupu, kāore i te nui te Hormone Antidiuretic (ADH) i roto i tō tinana, e kiia nei ko te Vasopressin . Ka āwhina tēnei homoni ADH ki te whakahaere i te nui o te wai i roto i ō tātou tinana. Ina iti tēnei homoni, ka tīmata ngā whatukuhu ki te whakaputa i te wai hei mimi. Nō reira, ka nui tō mimi, ā, ka pupuhi rawa tō puku.
Ka hangaia tēnei homoni ADH e te hypothalamus i roto i tō tātou roro. Heoi, ka rongoatia, ka tukuna ina hiahiatia e tētahi atu repe iti i roto i te roro , te repe pituitary . Nō reira, ki te mea he kino ki te hypothalamus, ki te repe pituitary rānei, ka taea te whakawhanake i te CDI.
Ki te mea kei a koe te CDI, ki te kore koe e inu wai nui hei whakakapi i te nui o te wai e ngaro ana i a koe mā te mimi, ka matewai koe. He tino morearea tēnei.
Tērā pea he kino ake te momo CDI o ētahi tāngata, arā, kāore te homoni ADH e mahi tika ana. Ka kiia tēnei ko te 'CDI katoa'. Ko ētahi atu he ngawari ake te āhua, arā, kei te mahi te homoni ADH ki tētahi taumata. Ka kiia tēnei ko te 'CDI wāhanga'.
Ko te mea nui, ina rongo koe i te ingoa 'Diabetes Insipidus', kaua e whakapoauau ki te 'Diabetes Mellitus'. He kupu 'diabetes' tō ēnei mate e rua nā te mea he rite tonu ngā tohu o ēnei mate e rua, arā, te nui o te matewai me te mimi pinepine. Nō te kupu Kariki 'diabainein' te kupu 'diabetes'. Ko tōna tikanga he 'haere'. Pērā i te wai e tere haere ana i roto i te tinana, ā, ka tukuna hei mimi.
E whā ngā momo matua o te 'Diabetes Insipidus':
- 'Te Mate Huka Waenga o te Mate Huka (CDI)' - Koinei te momo tino noa e kōrerohia ana.
- Mate Huka Insipidus Nephrogenic - Kāore ngā whatukuhu e aro ki te ADH.
- `Dipsogenic Diabetes Insipidus` - Nā te hiahia hinengaro ki te inu nui rawa i te wai.
- 'Te Mate Huka Insipidus Hāputanga' - He mate rangitahi ka puta i te wā e hapū ana.
He aha tēnei ADH (hormone antidiuretic)?
Ko te ADH, te vasopressin rānei, e ai ki te kōrero i mua ake nei, he homoni i hangaia e tō hypothalamus, ā, i rongoatia, i tukuna hoki e tō repe pituitary.He rite rātou ki ngā karere matū e whakarite ana i ngā mahi a ō tātou tinana. Ka haere ēnei i roto i te toto, ka kawe karere ki ō tātou whekau, uaua, me ētahi atu kiko. Ka tohutohu ēnei tohu i te tinana ki te aha me mahi, me te wā hoki hei mahi.
Ko te hypothalamus te wāhanga o tō tātou roro e whakahaere ana i te mahi a te pūnaha io motuhake me te repe pituitary. Ka hangaia e ia te ADH ka tukuna ki te repe pituitary hei penapena me te tuku ina hiahiatia.
He repe iti te repe pituitary kei te pūtake o te roro, i raro noa i te hypothalamus. He wāhanga ia o tā tātou pūnaha endocrine. Ko tana mahi he hanga, he penapena, he tuku hoki i ngā homoni nui. Ka rongoatia, ka tukuna hoki te ADH e te repe pituitary o muri.
Ko te ADH te mea matua e whakahaere ana i te nui o te wai e mimitihia ana e ō tātou whatukuhu ki roto i ō tātou tinana ina tātarihia e rātou ngā para mai i ō tātou toto, ā, mā reira ka mau tonu te taurite o te wai i roto i te tinana. I te nuinga o te wā, ina matewai koe, ina iti rānei tō toto toto, ka nui ake te ADH ka puta mai i tō tinana, ka tukuna atu hoki. He tohu tēnei ki ngā whatukuhu kia "pupuri i te wai i roto i tō tinana, kaua e tukuna ki roto i te mimi."
Nō reira, i roto i te CDI, kāore te hypothalamus e whakaputa i te nui o te ADH, kāore rānei te repe pituitary e tuku i te nui o te ADH. Koia te take he nui, he maha hoki te mimi e puta mai ana.
He aha te rerekētanga i waenga i te Central Diabetes Insipidus (CDI) me te Nephrogenic Diabetes Insipidus?
He rite ngā tohu o ngā mate e rua: te mimi nui me te inu wai nui. Ko te rerekētanga kei te pūtake me te maimoatanga o ēnei mate e rua.
Ka puta te Mate Huka Insipidus Nephrogenic ina tukuna e tō repe pituitary te nui o te ADH, engari kāore ō whatukuhu e aro tika. Ko te tikanga kāore e taea e ō whatukuhu te pupuri wai. He maha ngā take mō tēnei:
- Ko ētahi rongoā, hei tauira, te lithium me te tetracycline .
- Te iti o te pāhare pāporo i roto i te toto (Hypokalemia) .
- Te pikinga o te taumata konupūmā i roto i te toto (Hypercalcemia) .
- Te aukati i te ara mimi.
Ko te mate huka insipidus matua (CDI) ka puta mai i te kore mahi tika o te hypothalamus, te repe pituitary rānei, e kore nei e whakaputa i te ADH. Ko te tikanga ka puta mai i te kino o te hypothalamus, te repe pituitary rānei. Ka puta pea tēnei kino i ngā whara o te mahunga, i te pokanga, i te mumura, i ngā pukupuku rānei.
Ko wai ka pāngia e te CDI? He pēhea te noa o tēnei?
Ka taea te whakawhanake i te Central Diabetes Insipidus (CDI) i ngā tau katoa, engari he mea noa ake ka tīmata i waenga i te 10 me te 20 tau .
He tino onge te mate CDI, e pāngia ana e te kotahi i roto i te 25,000 tāngata .
He aha ngā tohu o te CDI?
Ko ngā tohu matua o te 'Central Diabetes Insipidus (CDI)' ko:
- Te mimi pinepine, ahakoa i te pō.
- Te mimi nui, he mārama, he mārama rānei te tae e puta ana i ia wā.
- E tino ngenge ana koe, e matewai ana hoki, nō reira me inu pinepine koe i ngā wai.
Ahakoa e whakaputa ana te tangata noa i te mimi tata ki te kotahi ki te rua rita ia rā, ka taea e te tangata whai CDI te whakaputa tae atu ki te 19 rita (20 kuata) o te mimi ia rā ! Whakaarohia te nui o tēnā!
Ngā tohu i roto i ngā pēpi nohinohi
Tērā pea ka kitea anō hoki e ngā pēpi me te CDI ngā tohu penei:
- Te koretake me te pukuriri tonu.
- Te ngenge, te hiamoe.
- Te ruaki.
- Te mate kōroke.
- Te kirika.
Ngā tohu o te matewai
Ki te kore e rongoatia te CDI, ki te kore rānei te tangata whai CDI e inu wai nui, ka tere te matewai . Ko ngā tohu o te matewai ko:
- Pōuriuri, māuiui te mahunga.
- Ngenge.
- Waha maroke, ngutu, kanohi.
- Te uaua ki te mahi i ngā mahi hinengaro māmā.
- Whakapairuaki.
- Te hemo.
Mena he nui rawa tō matewai, he maha hoki ō mimi, he maha rānei ō tohu o te matewai, he mea nui kia tere tonu te haere ki te hōhipera. Ahakoa he onge te CDI, ehara i te mea koinei anake te mate ka puta ai ēnei tohu. Ko te nui o te matewai me te maha o ō mimi he tohu kaha kei te kore tetahi mea e mahi tika ana i roto i tō tinana, ā, me rapu awhina hauora koe.
He aha ngā take o te Central Diabetes Insipidus (CDI)?
Ko te tino take o te Central Diabetes Insipidus (CDI) ko te korenga katoa, te korenga wāhanga rānei o te homoni ADH. Ko te nuinga o te wā ka puta tēnei korenga i te kino o tō hypothalamus, te repe pituitary, te kiko rānei e hono ana i ngā mea e rua (te pūtake pituitary). Ko ētahi o ngā take motuhake ko:
- Te pakaru o te hypothalamus, te pituitary rānei nā te pokanga.
- Te pakaru o te hypothalamus, te pituitary rānei nā te whara o te upoko, inā koa ngā whati o te angaanga turanga.
- Te mumura (granulomas) i puta mai i ngā mate pēnei i te sarcoidosis , te kohi rānei .
- Ngā pukupuku pērā i te craniopharyngioma , te germinoma rānei.
- Te histiocytosis pūtau Langerhans (he mate onge tēnei ka taea te whakakino i te kiko, te whara rānei i tētahi, i ētahi atu wāhi rānei o te tinana).
- He whakarerekētanga ira tuku iho i runga i te ira 20 (he tino onge tēnei - iti iho i te 100 ngā take kua pūrongohia i roto i ngā tuhinga hauora).
Mō te hautoru o ngā take CDI, kāore e taea e ngā tākuta te kimi i te tino take. Ka kiia tēnei ko te idiopathic central diabetes insipidus (CDI).E whakaaro ana ngā kairangahau ko ētahi take o te CDI idiopathic ka puta mai i ngā āhuatanga ārai mate. I roto i ngā āhuatanga ārai mate, ka tīmata te pūnaha ārai mate o tō tinana ki te whakaeke i ngā kiko hauora. I tēnei take, ka hanga pea te pūnaha ārai mate i ngā paturopi, i ngā lymphocytes rānei, hei whakaeke i ngā pūtau e whakaputa ana i te ADH.
Ka taea hoki te puta te CDI hei wāhanga o tētahi mate nui ake, pērā i te mate Wolfram ( he mate tuku iho) me te septo-optic dysplasia (he mate onge o te whanaketanga wawe o te roro).
Me pēhea koe e mōhio ai mēnā kei a koe te CDI? (Tauātanga)
Nā te mea ka taea hoki te matewai pinepine me te mimi e puta mai i ētahi atu mate, pērā i te mate huka, he mea nui kia whakakorehia ētahi atu mate i te wā e tātaritanga ana i te mate huka insipidus matua (CDI). Nō reira, ki te whai koe i ēnei tohu, ka whakahaerehia pea e tō tākuta ētahi whakamātautau.
Kei roto hoki i te tātaritanga o te CDI te kimi i te pūtake.
He aha ngā whakamātautau e whakamahia ana hei tautuhi i te CDI?
Ko te whakamātautau kore wai te huarahi māmā me te huarahi pono rawa atu ki te tautuhi i te CDI. Mēnā ka whakahaua tēnei whakamātautau e tō tākuta, ka āta tirotirohia koe i te wā o te whakamātautau, nā te mea ka matewai pea koe.
Ko tēnei whakamātautau he kore inu mō ngā haora maha, me te tirotiro i te urupare a tō tinana. Mena kei a koe te CDI, ka haere tonu koe ki te tuku i te nui o te mimi wai (wairewa), mārama te tae, ahakoa he iti noa te mimi kōwhai pouri, kukū.
Ka taea hoki e tō tākuta te tono i ēnei whakamātautau hei āwhina i te tautuhi i te CDI me te whakakore i ētahi atu āhuatanga:
- He whakamātautau toto hei tirotiro i te taumata o te ADH (hormone antidiuretic) i roto i te toto.
- He whakamātautau toto hei tirotiro i ngā taumata huka toto hei whakakore i te mate huka.
- Te tātaritanga mimi hei tirotiro i te kukū (osmolality) o te mimi, me/ranei hei tirotiro mō ngā ketone, e tohu ana i te mate huka.
- Hei whakatau i te urupare a ō whatukuhu, ka werohia koe ki te ADH hangai. Kāore te hunga whai Nephrogenic Diabetes Insipidus e urupare ki te ADH hangai nā te mea he ātete ō rātou whatukuhu ki ngā pānga o te ADH. I tētahi atu taha, ka urupare te hunga whai CDI ki te ADH hangai.
- Ka taea te whakamahi i ngā whakamātautau whakaahua pēnei i te MRI (Magnetic Resonance Imaging) hei whakatau mēnā kua pakaru tō repe pituitary, tō hypothalamus rānei, ā, mēnā kua pakaru, he aha te take.
He aha ngā maimoatanga mō te CDI?
Ko te maimoatanga mō te CDI ka whakawhirinaki ki te kaha o te korenga o te homoni ADH.
Kei a koe tētahi CDI katoa.Mena koinā te āhua, ko te desmopressin te rongoā tuatahi. He rongoā tēnei e rite ana ki te homoni ADH. Ka taea e koe te tango i te desmopressin hei werohanga, hei pire, hei rehu ihu rānei.
Mena kei a koe te CDI hapa , arā, kei te mahi tonu te ADH tūturu ki tētahi taumata, ka tohua pea e tō tākuta ētahi atu rongoā, pērā i te hydrochlorothiazide (HCTZ) .
Hei rongoā mō ngā pēpi me te CDI, ka taea te hoatu te miraka pēpi, te waiū u rānei i konatunatua ki te wai, ā, ka hoatu ki te hydrochlorothiazide.
He pānga taha anō kei te tango i te Desmopressin?
He rongoā tino haumaru te desmopressin, he iti noa iho ngā pānga taha. Ko ngā pānga taha pea ko:
- Te mamae o te upoko.
- Mamae puku.
- Whakapairuaki.
- Te ihu pupuhi, te ihu pupuhi rānei.
- Toto ihu.
Ki te nui rawa te desmopressin e tangohia ana e koe, ki te nui rawa rānei te wai e inuhia ana e koe i a koe e tango ana, ka nui rawa te wai e puritia ana e tō tinana. Ka puta pea ngā tohu pēnei i:
- Te mamae o te upoko.
- Pōuriuri.
- Pupuhi.
- Te iti o te tote (konutai) i roto i te toto (Hyponatremia) .
Ngā tohu o te Hyponatremia:
- He mamae upoko nui, he mamae upoko roa rānei.
- Pōhēhētanga.
- Whakapairuaki me te ruaki.
Mena kei a koe ngā tohu o te hyponatremia, me waea atu koe ki te 911, me haere rānei ki te rūma whawhati tata i te wā e taea ai.
Me pēhea e taea ai e te tangata whai CDI te whakahaere i tēnei?
Mena kei a koe te CDI, hei tāpiritanga ki te maimoatanga hauora, he mea tino nui te inu wai i ngā wā katoa kia kore ai e matewai.
He mea nui anō hoki kia kite i tō tākuta i ia wā, i ia wā, kia mōhio ai koe kei te pai te mahi a tō maimoatanga, ā, kei te tika hoki te horopeta o te rongoā kua tohua.
He aha ngā āhuatanga mōrearea e pā ana ki te whakawhanaketanga o te CDI?
Engari, kāore e taea te ārai i te nuinga o ngā mate o te Central Diabetes Insipidus (CDI). Ko ngā āhuatanga mōrearea mō te whakawhanaketanga o te CDI ko:
- Pokanga roro.
- He hītori whānau tō te mate huka insipidus me/te mate Wolfram rānei.
- Ngā whara o te upoko.
- Ngā mate pukupuku o te roro.
He aha te āhua hauora o te tangata whai CDI? (Te matapae)
He pai te āhua o te mate mō te tangata e pāngia ana e te 'Central Diabetes Insipidus (CDI)', ā, ki te tika te rongoā me te nui o ngā wai e inuhia ana, kāore e puta he raruraru nui.
Heoi, ko ngā tamariki nohinohi, ngā kaumātua, me te hunga whai raruraru hauora hinengaro, he nui ake te mōrearea ki ngā raruraru me te mate nā te mea ka uaua pea ki a rātou te kite i tō rātou matewai, te mahi rānei i tetahi mea.
He aha ngā raruraru ka pā mai i te Central Diabetes Insipidus (CDI)?
Ko te raruraru matua o te CDI koTe matewai . Ko te tikanga tēnei kei te ngaro i tō tinana ngā wai me ngā electrolytes hei mahi tika. Mena kei a koe te CDI, ka taea e koe te whakahaere i te nui o te wai e ngaro ana i roto i tō mimi mā te inu i te nui o ngā wai. Engari ki te kore, ka tere pea koe te matewai.
He mea morearea te matewai, ā, ka mate pea. Mēnā kei a koe ngā tohu o te matewai, pērā i te whanoke, te whakapairuaki, me te ngenge, haere ki te hōhipera tata tonu.
Ki te kore e rongoātia te CDI i roto i ngā pēpi nohinohi , ka taea e te matewai tonu te arahi ki ngā raruraru pēnei i:
- Ngā hopukanga.
- Te pakaru o te roro.
- Ngā whakaroa whanaketanga.
- Te tipu pōturi.
Mena ka waiho te CDI kia kore e rongoatia i roto i ngā tamariki me ngā pakeke, ka puta ngā raruraru pēnei i:
- Te pāorooro o te manawa (Arrhythmia) .
- Te kirika.
- Te maroke o te kiri me ngā kiriuhi mucous (hei tauira, i roto i te waha, i te ihu).
- Ngā hopukanga.
- Koma.
Tērā pea ka pāngia ngā pakeke whai CDI e te mate e kiia nei ko te orthostatic hypotension , arā, he hekenga ohorere o te toto toto i te wā e tū ana, e noho ana rānei. Ka pāngia pea ngā pakeke e te whanoke, te ngaro rānei o te māramatanga mō te wā poto.
Āhea koe me toro atu ki te tākuta?
Mena kei a koe te Central Diabetes Insipidus (CDI), he mea nui kia toro atu koe ki tō tākuta i ia wā, kia aroturukihia ai tō āhua, kia mōhio ai hoki kei te whai hua tō maimoatanga. Mena kei a koe ētahi tohu e āwangawanga ana koe, me whakamōhio atu ki tō tākuta.
Mena ka pāngia koe e ngā tohu o te matewai nui, pērā i te pōhēhē, te whakapairuaki rānei, haere ki te rūma whawhati tata i te wā e taea ai.
Ngā pātai hei pātai atu ki tō tākuta
Mena kua tāpaetia koe kei te mate koe i te Central Diabetes Insipidus (CDI), he pai pea te pātai atu ki tō tākuta i ēnei pātai:
- He aha ahau i whakawhanake ai i te CDI?
- He roa, he rangitahi rānei te mate CDI e pā mai ana ki ahau?
- He aha ngā kōwhiringa maimoatanga kei a au?
- He aha ngā painga me ngā ngoikoretanga o ngā momo maimoatanga rerekē?
- Kia hia te wai me inu e au i te rā?
- He aha atu anō taku e taea ai hei whakahaere i tōku āhua?
- Kei te tūpono te whānau ki te pāngia e te CDI?
Hei whakamutunga, ko te mea tino nui (Karere hei tango i te kāinga)
He mate onge te Central Diabetes Insipidus (CDI) engari he mate kino pea. Ko te rongo pai, ka taea te rongoā me te whakahaere.Mena kei a koe te CDI, he mea nui kia kite i tō tākuta i ia wā, kia mōhio ai kei te pai te mahi a tō maimoatanga. Mena he pātai āu mō tō āhua, kaua e wehi ki te pātai ki tō tākuta. Kei reira rātou hei āwhina i a koe ki te whakahaere i tō āhua. Kaua e wareware ki te inu i te nui o te wai, he mea tino nui!
` Te Mate Huka Insipidus Matua, CDI, ADH, whatukuhu, homoni, mimi nui, matewai nui











💬 Comments (0)
Kaore ano kia tukuna he korero. Tāpirihia to korero ki konei mo te wa tuatahi.
Tāpirihia to korero