He ngoikore te āhua o ō niho? Kua rerekē te tae? Tērā pea nā te (Dentinogenesis Imperfecta) tēnei!

Kua kite koe i tētahi wā he rerekē te tae o ngā niho o ētahi tāngata, he kikorangi-hina pea, he kōwhai-parauri rānei? He ngoikore rawa rānei ō niho, ā, ka pakaru, ka memeha rānei ahakoa ka kai koe i tētahi mea iti? Tērā pea he mea noa tēnei. Heoi anō, tera pea nā tētahi āhuatanga onge e puta ana i te wā e whanake ana ngā niho e kiia nei ko te `(Dentinogenesis Imperfecta)`. Me kōrero tātou mō tēnei i tēnei rā, āe?

He aha te `(Dentinogenesis Imperfecta)`? Me mārama noa iho, me pēhea?

Ki te kī māmā noa, ko te `(Dentinogenesis Imperfecta)` he raruraru e puta ana i te wā e hangaia ana ngā niho, arā, i te wā e tipu ana ngā niho. Ko te mea e tupu ana i tēnei take, ka ngoikore rawa ō niho, ka whati ngāwari . Pērā i te pihikete, ki te whati noa koe, ka whati. Waihoki, he mārama ngā niho o te hunga whai mate pēnei. Ko te tae hoki, e ai ki taku kōrero i mua ake nei , he kikorangi-hina, he kōwhai-parauri rānei .

Ko tēnei āhuatanga, e kiia nei ko te "Dentinogenesis Imperfecta," ka pā ki ō niho tuatahi me ō niho tuturu . Ko te tikanga ka tīmata ngā tohu i te wā taitamariki, ka puta rānei i muri mai i te wā o te oranga.

Nā, tirohia, ina tangohia he niho, he maha ngā paparanga. Ko te wāhanga kanapa, kaha o runga e kiia ana ko te `(Enamel)`. Kei raro iho i taua `(Enamel)` tētahi atu paparanga, e kiia ana ko te `(Dentin)`. Ko tēnei wāhanga `(Dentin)` te mea nui e homai ana te kaha me te tae ki te niho. Ko te mea ka tupu i roto i te `(Dentinogenesis Imperfecta)` ko te kore e whanake tika te wāhanga `(Dentin)`. Ka aha rā? Nā te ngoikore o te `(Dentin)`, kāore te `(Enamel)` o runga e piri tika ki te niho. Koia te take ka ngawari te pakarukaru me te memeha o te `(Enamel)`.

He mea nui: He rerekē te `(Dentinogenesis Imperfecta)` i te `(Amelogenesis Imperfecta)`. I roto i te `(Amelogenesis Imperfecta)`, ka pāngia tika te `(Enamel)` o te niho. I roto i te `(Dentinogenesis Imperfecta)`, kei te `(Dentin)` te raruraru.

E kiia ana he mate tino onge tēnei. I te nuinga o te wā, ka pā tēnei mate ki te kotahi i roto i te 6,000 ki te 8,000 tāngata.

He momo `(Dentinogenesis Imperfecta)` rānei?

Āe, e toru ngā momo matua o te `(Dentinogenesis Imperfecta)` e kōrero ana tātou. Kia kite tātou he aha ēnei momo.

1. `(Dentinogenesis Imperfecta)` Momo 1 (Momo I): He mea motuhake tēnei. Nā te mea ka puta tēnei momo me te mate e kiia nei ko `(Osteogenesis Imperfecta)`. Ko `(Osteogenesis Imperfecta)` he mate e tino pakarukaru ai ngā wheua (mate wheua pakarukaru). Nō reira, me ngā raruraru niho, he raruraru wheua anō hoki ō ēnei tāngata. Ko te take o tēnei he rerekētanga kei roto i ngā `(Ira)` o ngā ira `(COL1A1)` me `(COL1A2)`. Ka āwhina ēnei ira e rua ki te hanga i te pūmua `(Collagen)` i roto i tō tātou tinana.

2. `(Dentinogenesis Imperfecta)` Momo 2 (Momo II): He nui ake te kitea o tēnei momo i ngā niho tuturu.Ko te mea tino kitea i roto i ngā niho pēpi. He iti ake ngā mate tuku iho o ēnei tāngata. Heoi, kua kitea i ētahi wā ka pāngia pea e te ngaronga o te rongo e pā ana ki te koroheketanga .

3. Momo 3 (Momo III): Koinei te momo tino onge . He nui ake te pānga ki ngā niho tuturu i ngā niho pēpi. Kua pūrongohia e ngā kairangahau tēnei momo i waenga i te hunga Hūrai e kiia nei ko te `(Ashkenazi Jewish)`, me ētahi whānau e noho ana i te tonga o Maryland.

He aha ngā tohu o te `(Dentinogenesis Imperfecta)`? Me pēhea te mōhio ki tēnei?

E ai ki taku kōrero i mua ake nei, ko ngā tohu matua ko te rerekētanga o te tae me te ngoikore o ngā niho, pakarukaru hoki . He mārama te nuinga o ngā niho, he kōwhai-parauri, he kikorangi-hina rānei te tae .

Haunga tēnā, tera pea ka kitea e koe ētahi atu tohu pēnei i:

• Te ngaromanga o ngā niho pēpi i te wā tōmuri: Ka roa ake te ngaromanga o ngā niho pēpi i te wā noa.
• Te ngoikore o te enamel: Ko te tikanga kua ngaro rawa te paparanga enamel i te tihi o ngā niho.
• Te Nekenekehanga Nui o ngā Hononga: Ka taea e ētahi tāngata te piko i ō rātou hononga, pērā i ō rātou maihao me ō rātou tuke, ki mua, ki mua hoki.
• Te Agenesis Niho: Ko te tikanga o tēnei he whānautanga mai kāore he niho.
• Te enamel niho ngoikore: He ngoikore te enamel, ā, ka tere te memeha.

Whakaarohia, ki te mea he rerekē te tae o ngā niho pēpi o te tamaiti, he kikorangi te tae, he ngawari rānei te whati, me tino manukanuka koe mō rātou.

He aha i puta ai tēnei `(Dentinogenesis Imperfecta)`? He aha te take?

Ko te take matua mō tēnei he panonitanga o ō tātou ira. Ina koa, ko te panonitanga o te ira e kiia nei ko te `(DSPP) ` ka puta te `(Dentinogenesis Imperfecta). Mā tēnei ira `(DSPP)` ka hoatu ngā tohutohu ki te hanga `(Dentin)`, te paparanga waenga o ō tātou niho. Nō reira, ina he raruraru ki tēnei ira, kāore te `(Dentin)` e hanga tika.

Ka taea te tuku iho i tēnei rerekētanga ira mai i ngā mātua , ka taea rānei te puta noa mai.

Ko te hunga e pāngia ana e te Dentinogenesis Imperfecta momo 1, e ai ki taku kōrero i mua ake nei, he whakarerekētanga ō rātou ira i roto i ngā ira COL1A1, COL1A2 rānei. Koinei ngā whakarerekētanga ira e kitea ana hoki i roto i te hunga e pāngia ana e te Osteogenesis Imperfecta (he mate e pakarukaru ai ngā wheua).

Me pēhea te tautuhi a ngā tākuta i tēnei?

Mena kei a koe, kei tāu tamaiti rānei tētahi o ēnei tohu, me toro atu koe ki tētahi tākuta niho i te tuatahi. Ka tirotirohia e ia te tinana i te tuatahi, ā, ka pātai atu mēnā kua pāngia tētahi o tō whānau e ēnei mate..

Hei tāpiri, ki te whakapae koe kei a koe te Dentinogenesis Imperfecta, ka taea te whakahaere i ngā whakamātautau e whai ake nei hei whakaū i te mate:

• Te tango i ngā hihi-X o ngā niho.
• Tērā pea ka taea e koe te mahi i tētahi matawai CT .

Mā te titiro ki ēnei whakaahua, ka taea e te tākuta te mārama ki te āhua o roto o ngā niho, me te āhua o te dentin.

I ētahi wā, ka tūtohu pea tō tākuta kia whakamātauria he whakamātautau ira hei kimi i ngā huringa o tō DNA e puta ai te dentinogenesis imperfecta.

He aha ngā maimoatanga mō tēnei? (Maimoatanga)

Ko te arotahi matua o te maimoatanga mō te Dentinogenesis Imperfecta ko te whakapakari i ngā niho ngoikore . He maha ngā tikanga whakaora e whakamahia ana e ngā tākuta niho hei mahi i tēnei.

Hei tauira:

• Ngā whakakī: Whakakīia ngā āputa me ngā kapiti o ngā niho.
• Ngā Veneer: He anga angiangi ēnei e whakatakotoria ana ki mua o te niho. Ka taea hoki e ēnei te whakapai ake i te āhua o te niho.
• Karauna: He rite te karauna ki te taupoki e whakatakotoria ana ki te niho. Ka hipokina e ia te niho katoa, ā, ka whakakaha.

Ka whakamahia e ēnei maimoatanga ngā rauemi he rite te tae ki ngā niho, kia mau tonu ai te ataahua o tō ataata.

Ina pāngia koe e te Dentinogenesis Imperfecta, ka nui ake te tūponotanga ka ngaro ō niho i a koe e pakeke haere ana. Ki te ngaro ō niho, ka taea e koe te whakakapi ki ngā mea tāpiri niho , ki ngā niho rūpahu rānei.

He aha te momo tumanako ka taea e koe te whai i a koe e noho ana i roto i tēnei āhuatanga? (Tirohanga)

He maha ngā āhuatanga e whakawhirinaki ana ki tō tirohanga:

• Tō tau i te wā i kitea ai kua pāngia koe e te mate.
• Te tere o te tīmatanga o tō maimoatanga.
• He aha te momo Dentinogenesis Imperfecta kei a koe?

Ko te mea nui, kāore e taea te rongoā i te Dentinogenesis Imperfecta. Heoi, mā te tiaki tika i ō niho me ngā tikanga pai mō te akuaku waha, ka taea e koe te ārai i ngā kino atu ki ō niho, me te pupuri i a rātou kia kaha. Ko te tere o te tautuhi me te rongoā i te mate, ko te pai ake o te putanga.

Ka taea te ārai i te Dentinogenesis Imperfecta?

Engari, kāore e taea te ārai i te Dentinogenesis Imperfecta nā te mea nā ngā huringa ira kāore e taea te whakahaere. Heoi, mā te tīmata wawe i te maimoatanga ka taea te whakaiti i te kino roa ki ngā niho.

Me pēhea taku tiaki i ōku niho? (Te Tiaki i a Au)

Mena kei a koe te `(Dentinogenesis Imperfecta)`, he mea nui kia pai te akuaku o te waha.He mea nui kia tiakina. Hei whakaiti i te pirau me te pakaru o ngā niho, me mahi ēnei e whai ake nei:

• Pātai atu ki tō tākuta niho mō ngā maimoatanga whai fluoride hei whakapakari i ō niho.
• Paraia ō niho kia rua, kia toru rānei ngā wā i te rā mā te whakamahi i tētahi paraihe niho ngohengohe me tētahi paraihe niho whai fluoride .
• Whakaititia ngā kai huka, ngā kai waikawa.
• Horoia tō waha ki te wai horoi waha he fluoride kotahi i te rā.
• Haere ki te taote niho i ngā wā katoa mō ngā tirotiro me ngā horoinga niho .

He aha ngā mea pai hei kai me hei inu ina pāngia koe e te `(Dentinogenesis Imperfecta)`?

Ko te mea pai ko te whiriwhiri i ngā kai me ngā inu he iti te huka me te waikawa . Ko te tikanga me whakaiti i ngā inu pēnei i te houra tunutunu, ngā hua citrus pēnei i te raima, me ngā ranu tōmato kia rite ki te taea. He mea pai hoki kia whakaiti i ngā kai me ngaungau, he mārō, he pakari rānei .

Anei ētahi kai pai hei kai mā te tangata e pāngia ana e te `(Dentinogenesis Imperfecta):`

• Ika tunua
• Ngā momo kēhi
• Huawhenua kua tunua
• Ōti
• Pāta me te ranu kirīmi
• He hua manu i paraipanatia
• Ngā inu huamata

He kai ngāwari ēnei ki te kai, ā, kāore e nui te kino ki ō niho.

Āhea ahau me toro atu ki te tākuta?

Ki te kite koe, tāu tamaiti rānei i tētahi mea rerekē, rerekē rānei mō ō rātou niho, he mea pai kia kōrero tonu atu ki tō tākuta . Kia maumahara, ka puta pea ngā tohu o te DGI i ngā tau katoa. Ki te puta kikorangi, hina, parauri rānei ngā niho pēpi tuatahi o tāu pēpi , kia kite koe i tētahi tākuta niho tamariki mō ētahi tohutohu.

He aha ngā pātai me pātai atu koe ki te tākuta?

Mena kua tāpaetia koe kei te mate koe i te Dentinogenesis Imperfecta, me pātai atu pea koe ki tō tākuta i ēnei pātai:

• He aha te momo `(DGI)` kei a au?
• He aha te momo maimoatanga e hiahiatia ana e au?
• Kia pēhea te roa o ngā maimoatanga? Kia pēhea te roa o ngā maimoatanga?
• Kia pēhea te auau o taku horoi i ōku niho?
• He aha ngā mahi ārai ka taea e au te mahi hei whakaiti i te pakaru me te pakaru o ngā niho?

Heoi anō... (Karere hei kawe ki te kāinga)

He tino hoha te ngoikore o ngā niho, he ngāwari hoki te whati. He tino hoha hoki te tūpato i ia wā e kai ana koe. Mēnā kei a koe te `(Dentinogenesis Imperfecta)`, tera pea ka whakama koe mō te āhua o ō niho. Nā tēnei, tera pea kāore koe e hiahia ki te tū atu ki te aroaro o te hapori.

Engari kia maumahara, kāore koe i te mokemoke.. Kei reira ngā tākuta hei āwhina i a koe. Ka taea e rātou te tūtohu i ngā maimoatanga hei whakapakari i ō niho, hei whakapai ake i tō ataata, hei whakanui ake hoki i tō whakapono ki a koe anō. Nō reira, kaua e manukanuka ki tetahi mea, engari me whai i ngā tohutohu a tō tākuta.

Mā te tautuhi i te mate i te wā tōmua, te whiwhi maimoatanga tika, me te whai i ngā tikanga pai mō te akuaku waha, ka taea e koe te ora hauora, harikoa ahakoa kei a koe te mate `(Dentinogenesis Imperfecta).'

` dentinogenesis imperfecta, ngā mate niho, ngā niho ngoikore, te rerekētanga o te tae o ngā niho, ngā mate ira, te hauora o ngā niho, ngā niho pēpi