Kei te raru koe i te iti o te konupūmā i muri i te pokanga? Tērā pea ko te 'Hungry Bone Syndrome'!

E mōhio ana pea koe, i muri i ētahi pokanga, inā koa ko ērā e tango ana i te repe tairoiro i te kaki, i ngā repe parathyroid rānei e tata ana, ka pāngia te tinana e ētahi momo mamae rerekē. Tērā pea ka pāngia ētahi e te ngenge nui, te mamae o te tinana, te pōhēhē rānei. Nō reira, ki te pāngia koe, e tētahi rānei e mōhio ana koe e tētahi mea pēnei, tērā pea nā tētahi āhuatanga ka kōrerohia e tātou i tēnei rā e kīia nei ko te 'Hungry Bone Syndrome'. He ahua rerekē te ingoa, kāore? Tērā pea kei te whakaaro koe, "He aha te tikanga o te hiakai o ngā wheua?" Me titiro tātou ki te aha, i roto i ngā kupu māmā noa iho.

He aha te 'Hingry Bone Syndrome'?

Ki te whakarapopototanga, ko te Hungry Bone Syndrome he āhuatanga e heke ohorere ana te nui o te konupūmā i roto i te toto. Ka kiia tēnei e ngā tākuta ko te "Hypocalcemia". He maha ngā wā ka kitea tēnei āhuatanga i muri i te pokanga i ngā repe parathyroid. I mōhio koe he mea tino nui ngā repe parathyroid ki te whakahaere i te konupūmā i roto i tō tātou tinana?

Ko te hunga e pāngia ana e tēnei 'mate wheua hiakai', kāore pea i te iti noa te taumata o te konupūmā, engari i ētahi wā he iti anō hoki te taumata o te konupūmā (`(Hypomagnesemia)`) me te whākōkī (`(Hypophosphatemia)`) i roto i ō rātou toto. He kohuke nui anō hoki ēnei e hiahiatia ana e ō tātou tinana.

Engari kāore he mea hei manukanuka. Ko te 'Hungry Bone Syndrome' he mate ka taea te rongoā me te whakaora . Ko te mea nui ko te kite i te mate i te wā tika me te tīmata i te maimoatanga.

He pēhea te noa o tēnei āhuatanga?

Kāore anō kia tino mōhio ngā kairangahau ki te whānui o te pānga o tēnei 'mate wheua hiakai', nā te mea ka rerekē i ia tangata, i ia tangata.

Heoi, kua whakaatuhia e ētahi rangahau kei waenganui i te 4 me te 13 i roto i te 100 o ngā tāngata kua tangohia te parathyroid mō te mate e kiia nei ko te hyperparathyroidism tuatahi ka pāngia e tēnei mate. E ai ki ētahi pūrongo, i muri i te pokanga mō te hyperparathyroidism tuarua me te tuatoru, ka piki te tūponotanga o te whanaketanga o tēnei mate ki te 20 ki te 70 i roto i te 100. Nō reira, te āhua nei he nui ake te noa o tēnei i ētahi wā.

He aha ngā tohu o te 'Hungry Bone Syndrome'?

He tino rite ngā tohu o te 'Hungry Bone Syndrome' ki ērā i puta mai i te iti o te konupūmā toto (Hypocalcemia). Ka taea e ēnei te iti noa iho pērā i te puku iti i roto i ētahi tāngata, ki te kino rawa atu pērā i te pōhēhē, i te haurangi rānei i roto i ētahi atu. Anei ētahi o ngā tohu:

• Te hurihuri, te kukume rānei i te kikokiko: He āhua me te mea kei te hurihuri noa te kikokiko o ngā waewae, o ngā ringa rānei.
• Ngoikore o te uaua: Te āhua kore ora, te ngenge rawa hoki, kāore e taea te mahi i tetahi mea.
• Mamae wheua: Te āhua nei kei te mamae ngā wheua o te tinana.
• Ngenge nui: Te ngenge e kore e memeha ahakoa i muri i te moe.
• Pōhēhē: He uaua ki te arotahi, kāore e mōhio he aha te mahi.
• Ngā raruraru mahara: Te wareware i ngā mea.
• Te riri, te pukuriri rānei: Te riri mō ngā mea iti, te māharahara.
• Te pouri: Te āhua o te pouri me te kore tumanako.
• Te ngenge o ngā ngutu, o te arero, o ngā matimati, me/ranei o ngā waewae: Ka ngenge ēnei wāhi, ka rite rānei ki te omaoma haere a ngā pōpokorua.
• Te uaua ki te manawa nā te kōpeketanga o ngā uaua korokoro (`(Laryngospasm)`): He ahua morearea tēnei, ka uaua ai te manawa.
• Te pakari me te wiri o ngā uaua (`(Tetany)`): He āhuatanga e pakari ai, e wiri ai hoki ngā uaua o te tinana.
• Ngā mate hopuhopu: He tohu kino anō hoki tēnei.

Haunga ēnei tohu, e ai ki te kōrero i mua ake nei, ka puta pea te iti o te konupūmā me te whākōkī i roto i te toto (`(Hypomagnesemia)` me te `(Hypophosphatemia)`). He tino rite ngā tohu o ēnei āhuatanga ki ērā o te konupūmā iti. Ka taea hoki e rātou te whakararu i ngā uaua, te haurangi, me te ngakau pākiki koretake (`(Arrhythmia)`).

Ko te mate wheua hiakai ka puta i roto i ngā haora 18 o te pokanga parathyroid, tairoi rānei .

He aha i puta ai tēnei 'Hungry Bone Syndrome'?

He maha ngā tino take o te 'Hungry Bone Syndrome':

• I muri i te pokanga parathyroid (Parathyroidectomy) mō te hyperparathyroidism tuatahi, tuarua rānei.
• Ko te Thyrotoxicosis he mate e puta ana i muri i te tango katoa o te thyroid.
• Ina horapa te mate pukupuku repeure ki ngā wheua (kua horapa ki roto).

Hei mārama ki te take o tēnei, he mea nui kia mārama ki te whakahaeretanga o ngā taumata konupūmā i roto i ō tātou tinana.

Whakaarohia, kei muri i tō repe tairoiti i tō kaki, e whā ngā repe iti e kiia nei ko ngā repe parathyroid. Ka whakaputahia e ēnei repe he homoni e kiia nei ko te homoni parathyroid (PTH) . Ko te mahi matua o tēnei homoni PTH ko te whakahaere i te taumata o te konupūmā i roto i te toto (ehara i te mea i roto i ngā wheua, engari i roto i te toto). Ka āwhina hoki te PTH ki te whakahaere i ngā taumata o te phosphorus (he kohuke anō hoki) me te huaora D (he homoni anō hoki) i roto i te toto me ngā wheua.

Nō reira, ina rongo tō tinana kei te iti te taumata konupūmā i roto i tō toto, ka tukuna e ngā repe parathyroid te homoni PTH. Ka tukuna e tēnei PTH he iti noa te konupūmā mai i ngā wheua ka tāpiri atu ki te toto. Kātahi ka hoki te taumata konupūmā i roto i te toto ki te āhua noa.

Inaianei, whakaarohia he nui rawa te mahi a ngā repe parathyroid o tētahi, ā, ka pokangahia kia tangohia. Ko te mea ka tupu, ka heke ohorere ngā taumata o te homoni PTH i mua he tino tiketike. I ētahi wā, ina mahia he pokanga tairoi, ki te pakaru pōrearea ngā repe parathyroid tata, ka heke anō hoki ngā taumata o te PTH.

Ina heke ohorere ngā taumata PTH, ka heke te nui o te konupūmā i roto i ngā wheua tawhito e mimitihia ana ki roto i te toto (`(Resorption)`), ā, ka piki ake te nui o te hanganga wheua hou (`(Bone Formation)`). Mā tēnei ka "matekai" ngā wheua i te konupūmā. Koia te take i kiia ai tēnei ko te 'hunger bone syndrome'.

Koinei te mea ka tupu ina horapa te mate pukupuku repeure ki ngā wheua. I reira, ka piki ake te mahi a ngā pūtau hanga wheua (`(Osteoblastic activity)`), nō reira me nui ake te konupūmā e hiahiatia ana e ngā wheua.

Ko wai kei te mōrearea nui ake ki te whakawhanake i te 'Hungry Bone Syndrome'?

He nui ake te tūponotanga o ētahi tāngata ki te pāngia e tēnei mate. Me titiro tātou ko wai rātou:

• He tino tiketike ngā taumata o te homoni parathyroid (PTH) i roto i te toto.
• Kua piki ake te taumata o te phosphatase alkaline i roto i te toto.
• He iti noa iho ngā taumata konupūmā i roto i te toto i te nuinga o te wā.
• He ngoikore te huaora D.
• Te mahi i ngā pokanga tairoiti me ngā pokanga paratiroiroi i te wā kotahi.
• Te pikinga o ngā taumata hauota urea toto (BUN).
• Te momonatanga, arā, te tino ngako.
• Te tango pokanga i te repe parathyroid he nui ake i te tikanga.
• Te horapa o ngā pūtau matepukupuku ki ngā wheua (Ngā pukupuku metastatic o ngā wheua).
• Te noho mai o ngā mate e pā ana ki te wheua pērā i ngā pukupuku parauri me te osteitis fibrosa cystica.

Ko te hunga whai āhuatanga mōrearea nei ka nui ake te tūponotanga ka pāngia rātou e te 'mate wheua hiakai'.

Me pēhea te kitenga a ngā tākuta i tēnei?

I te nuinga o te wā ka whakatau tuatahi te tākuta mēnā kei a koe te 'mate wheua hiakai' mā te whakamātautau toto konupūmā. I te nuinga o te wā, ki te iti iho i te 8.4 mg/dL te taumata konupūmā o tō toto mō ngā rā e whā neke atu, ka kiia he take mōrearea mō te 'mate wheua hiakai'.

Ehara i te mea koinā anake, engari ka whakahaerehia pea e tō tākuta ētahi atu whakamātautau hei tirotiro mēnā kua pāngia e tēnei āhuatanga ētahi atu āhuatanga o tō hauora:

• Ētahi atu whakamātautau toto: Ka whakamātauria pea tō toto mō te konupora, te whākōkī, te homoni parathyroid (PTH), me/ranei ngā taumata huaora D.
• EKG (Electrocardiogram): Ka ine tēnei whakamātautau i te manawataki o tō ngākau mā te tāpiri i ngā irahiko ki tō uma. He mea nui tēnei nā te mea ka taea e te iti o te konupūmā toto (hypocalcemia) me te 'hunger bone syndrome' te whakararu i te ngakau.
• Ngā whakamātautau whakaahua wheua: Ka taea e ēnei whakamātautau te tirotiro mō ngā raruraru o ō wheua, pērā i te whati, te āhua rerekē, te pukupuku rānei.

He aha ngā rongoā mō te 'Hungry Bone Syndrome'?

Kaua e manukanuka, he pai ngā maimoatanga mō tēnei. Ko te whāinga matua o te maimoatanga he whakahoki i te taumata konupūmā i roto i tō toto ki tōna taumata hauora. I te nuinga o te wā, ka whiwhi koe i tēnei maimoatanga i a koe e noho ana i te hōhipera. Kei roto i te maimoatanga:

• Te hoatu konupūmā mā roto i tētahi uaua (`(IV Calcium - Calcium Gluconate)`): Mā tēnei ka āwhina i te whakahoki wawe mai i ngā taumata konupūmā.
• Ngā Tāpiringa Konupūmā ā-Waha (Calcium Citrate, Calcium Carbonate rānei): Ka hoatu ēnei hei pupuri i ngā taumata konupūmā.
• Ngā Tāpiringa Huaora D ā-Waha: He mea nui te Huaora D kia mimiti ai te konupūmā e te tinana.
• Whakakapinga konupora: Mena he iti ngā taumata konupora, me whakatika anō hoki tēnā.

Ka tirohia tō āhua e ngā tākuta, ā, ka whakatauhia te maimoatanga e tika ana māu.

Kia pēhea te roa o te wā e ora ai i tēnei mate? He aha te heke mai?

Ko te rongo pai, ko tēnei mate, arā, ko te 'Hungry Bone Syndrome', e tata kore e taea te whakaora . Ko te tikanga he tino pai te matapae.

Ahakoa te maimoatanga, ka rerekē te roa o te wā e ora ai tēnei mate. Ka ora ake ētahi i roto i ētahi rā, ko ētahi ia ka roa pea mō ētahi marama. I ētahi wā tino onge, ka roa pea mō te tau.

Ko te mea nui, ki te kore e rongoatia, ka taea e te hypocalcemia kino te arahi ki ngā raruraru morearea pērā i te haurangi. Nō reira, he mea nui kia rapu maimoatanga i te wā e taea ai mēnā ka puta ngā tohu.

Ka taea te ārai i te 'Hungry Bone Syndrome'?

I te mea ka puta te 'mate wheua hiakai' i muri i te pokanga parathyroid (`(Parathyroidectomy)`) i te pokanga tairoi rānei (`(Thyroidectomy)`), ka ngana ngā tākuta ki te mahi i ngā mahi hei ārai i tēnei mate i mua i te pokanga. Kia tirohia tātou he aha ēnei:

• Aromatawai i mua i te pokanga: I mua i te pokanga , ka tirohia e tō tākuta tō kiato kohuke wheua, ngā taumata konupūmā toto, ngā taumata phosphate, ngā taumata PTH, me ngā taumata huaora D. Ka taea e ēnei whakamātautau te āwhina i tō tākuta ki te whakatau mēnā kei te mōrearea koe ki te whakawhanake i te 'mate wheua hiakai'.
• Ngā mahi ārai:Mena kei te nui ake tō tūponotanga ki te pāngia e te 'mate wheua hiakai', ka tūtohu pea tō tākuta kia tango koe i ngā tāpiringa, i ngā rongoā rānei hei pupuri i ō taumata huaora D me te konupūmā i mua i te pokanga. Tērā pea ka āwhina tēnei ki te whakaiti i te tūponotanga me/te kaha rānei o te 'mate wheua hiakai'.
• Te aroturuki i muri i te pokanga: I muri i te pokanga, ka tirotirohia e te tīma hōhipera ngā taumata o te konupūmā, te phosphate, te konupora, me te PTH i roto i tō toto. Mā tēnei ka taea te tautuhi wawe mēnā ka pāngia koe e te 'mate wheua hiakai', ā, ka taea te tīmata tonu i te maimoatanga.

Heoi, ahakoa ēnei mahi katoa, i ētahi wā ka puta te 'mate wheua hiakai'. Kāore anō kia tino mārama ngā kairangahau he aha i puta ai tēnei.

Kia pēhea te wā me toro atu ahau ki te tākuta?

Mena kua pokangahia koe mō te parathyroid, te tairoi rānei, ā, i muri mai ka puta ngā tohu o te iti o te konupūmā toto (`(Hypocalcemia)`) i kōrerohia i mua ake nei, pērā i te mamae o te uaua, te ngoikore o te ngākau, ngā huringa o te hinengaro (pērā i te pōhēhē), me te ngoikore o ngā ngutu me ngā maihao, me toro atu koe ki te tākuta i te wā e taea ai.** Ka puta pea te 'Hungry bone syndrome' me te `(Hypocalcemia)` i muri i te pokanga parathyroid me/ranei te tairoi, ā, ka memeha haere i muri i ētahi rā, kātahi ka puta anō. Nō reira, he mea nui kia aro atu ki te tohu iti rawa.

Ko te 'Hungry bone syndrome' he mate ka puta i muri i te pokanga hei tango i te parathyroid, i te repe thyroid rānei. Ko te rongo pai, ka taea te rongoā me te whakaora. Heoi, tera pea ka roa te wā e ora katoa ai. I te mea he kino te hekenga nui o ngā taumata konupūmā toto ki tō hauora, he pai ake te toro atu ki te tākuta ina pāngia koe e ngā tohu.

Karere ki te kāinga

Nō reira, i roto i ngā kupu māmā, ko te 'Hungry Bone Syndrome' he mate ka puta i muri i te pokanga i te parathyroid, i te repe thyroid rānei. Ko tāna mahi matua ko te heke ohorere o te nui o te konupūmā i roto i te toto o te tinana. Nā te mea ka heke te taumata o te homoni parathyroid (`(PTH)`) i muri i te pokanga, ka "tono" ngā wheua i te konupūmā.

Kaua e wehi ki te whakarongo ki tēnei, nā te mea he mate te 'Hungry Bone Syndrome' ka taea te rongoā me te whakaora pai rawa atu.

Ko te mea nui, ki te pāngia koe e ēnei tohu (pēnei i te wiri o te uaua, te ngenge, te ngoikore), kaua e moumou taima, engari me toro atu ki te tākuta i te wā e taea ai. Mā tēnei, ka taea e koe te tautuhi wawe i te mate, te tīmata wawe i te maimoatanga e tika ana, me te whakaora i mua i te nui haere o te raruraru. Kia maumahara, kei roto i ō ringaringa te tiaki i tō hauora.

`Mate Wheua Hiakai, Mate Wheua Hiakai, Konupūmā, Hypocalcemia, Parathyroid, Pokanga Tairoiti, PTH