He uaua ki a koe te horomi kai? He ngenge tonu rānei koe, he puhoi hoki? I ētahi wā he āhua noa iho ēnei mea, engari tera pea he take anō kei muri i ēnei. I tēnei rā ka kōrero tātou mō tētahi mate hauora onge engari he mea nui. Ko te mate Plummer-Vinson tēnā.
He aha te mate Plummer-Vinson?
I te whakarapopototanga, ko te mate Plummer-Vinson (PVS) he mate e puta tahi ai ngā tohu e toru e pā ana. I ētahi wā ka kiia tēnei e ngā tākuta ko te "triad," ko tōna tikanga he "huinga o ngā tohu e toru." Me titiro tātou ki ēnei mate e toru:
1. Te mate toto iti-rino: Koinei te wā kāore i te nui te rino i roto i tō tinana hei hanga i te pūmua e kiia nei ko te hemoglobin i roto i ō toto toto whero. Kei te mōhio koe, ko te hemoglobin te mea e kawe ana i te hāora ki ia pūtau o tō tinana. Nō reira, ki te kore e nui te rino i roto i a koe, kāore te hemoglobin e hangaia tika, ā, kāore tō tinana e whiwhi i te hāora e hiahiatia ana. Koinei te take e puta ai ngā tohu pēnei i te ngenge me te kiri mā.
2. Ngā tukutuku korokoro: Koinei te wā e puta ai he kiko angiangi, kāore i te noa i roto i tō korokoro, i tō paipa kai rānei. Whakaarohia he rite ki te tukutuku pungawerewere e puta ana i tō korokoro. Mā tēnei ka whaiti, ka ārai hoki te korokoro. Mā tēnei ka uaua te tuku kai ki raro.
3. Te uaua ki te horomi (Dysphagia): Koinei te ingoa e hoatu ana e ngā tākuta mō te uaua ki te horomi i ngā kai me ngā inu nā ngā kupenga esophageal kua whakahuatia ake nei. Tērā pea ka uaua ki ētahi tāngata te horomi i ngā kai totoka me ngā wai hoki.
He ingoa kē atu anō tēnei. Ko tētahi ko te sideropenic dysphagia. Ā, i te United Kingdom, arā, i Ingarangi, e kiia ana ko te Paterson-Brown Kelly syndrome.
Nā, anei tētahi mea kaua e wehi. E kiia ana he nui ake te tūponotanga o te hunga whai mate pukupuku Plummer-Vinson (PVS) ki te pāngia e te mate pukupuku esophageal, te mate pukupuku hypopharyngeal rānei i muri mai i te oranga. Heoi, he tūponotanga noa iho tēnei . Ka tirotirohia koe e tō tākuta i ia wā, ā, ka aroturukihia koe ina hiahiatia kia kitea wawe ai aua āhuatanga.
He aha ngā tohu o tēnei?
Āe, kia tirohia tātou he aha ngā tohu e whakaatuhia ana e te tangata e pangia ana e te mate Plummer-Vinson (PVS). Kāore ēnei tohu e puta i te katoa i te ara kotahi, ā, ko ētahi tāngata ka pāngia e ētahi o ngā tohu.
- Te ngenge me te ngenge tonu: He tohu nui tēnei o te korenga o te rino. Ka ngenge tonu koe ahakoa te mahi i ngā mahi iti, ā, ka hiamoe tonu koe i te rā roa.
- Te uaua ki te manawa (dyspnea): Tērā pea ka pōturi te manawa, ehara i te mea i te wā e hikoi ana, e piki ana i ngā arawhata, engari i ētahi wā ahakoa e tū noa ana.
- Te uaua ki te horomi kai:Koinei te tohu tino kitea o tēnei mate. Ina koa ka horomia ngā kai totoka, pērā i te raihi, te taro, te mīti me te ika, ka puta he ahua pēhanga i roto i te korokoro me te uma. Me inu wai ētahi tāngata hei horomi i te kai. Ahakoa he uaua ngā kai totoka i te tīmatanga, i muri mai ka uaua pea te horomi i ngā wai.
- Ka mumura, ka pupuhi, ka whero te arero (glossitis): Ka maeneene, ka whero te arero, ā, i ētahi wā ka rite ki te wera.
- Waha maroke (xerostomia): Ka maroke tonu te roto o te waha, ā, ka puta te ahua kāore he huware.
- Te cheilitis koki: Ka ngatata, ka whero, ka rite ki te mamae ngā kokonga o te waha.
- Ka pakarukaru, ka papatahi ngā whao pērā i te pūnu: He ngoikore rawa ngā whao, ā, ka whati ngāwari. I ētahi wā ka totohu ngā whao ki waenganui, pērā i te pūnu (koilonychia).
- Te pupuhi me ngā puku o te repe tairoiti (ngā pona tairoiti): Ka taea e te repe tairoiti, kei mua o te kaki, te whakanui, ā, ka rite ki te puku.
- Te whēkau nui: Ko te whēkau nui he okana kei te taha maui o runga o tō tātou puku. Ka pupuhi pea i roto i tēnei āhuatanga, engari kāore e puta he tohu nui.
He aha te take mō tēnei?
Ina hoki, kāore anō kia tino mōhio ngā kairangahau he aha te pūtake o te mate Plummer-Vinson (PVS). Engari he iti noa ngā mea e whakaarohia ana e rātou, e whakapaetia ana hoki e rātou:
- Ko te korenga o te rino te mea tino whakapae: He tokomaha te hunga e whakaaro ana ko te korenga o te rino mō te wā roa ka ngoikore ai ngā uaua o te korokoro, ka hanga hoki i ngā kupenga. E hiahiatia ana te rino mō ngā whākōkī maha i roto i tō tātou tinana.
- Ngā ngoikoretanga o te kai: E whakaponohia ana ehara i te mea ko te rino anake, engari ko ētahi atu huaora me ngā kohuke ka pā ki tēnei.
- Ngā mate pūnaha ārai mate: Kua rongo pea koe i ngā mate pēnei i te mate rumatiki me te mate celiac. He mate pūnaha ārai mate ēnei e puta ana ina whakaekea e tō tātou ake pūnaha ārai mate ō tātou ake pūtau. Nō reira, i te mea kei ētahi tāngata whai PVS ēnei mate, e whakaaro ana ngā tākuta he hononga pea ki te pūnaha ārai mate.
- Te awe ira: E whakapono ana ētahi he mate ira tēnei, arā, mēnā he mate kei roto i te whānau, ka nui ake te tūponotanga ka pāngia anō hoki ētahi atu.
Heoi he ariā noa iho ēnei. Me whai rangahau anō kia kitea ai te tino take.
Ko wai kei te nui ake te mōrearea ki te whakawhanake i tēnei?
He tino onge te mate Plummer-Vinson (PVS). Kāore e pā ki te katoa. Heoi, e ai ki ngā tatauranga, ko te nuinga o te wā ka pā ki ngā wāhine mā. Ko te nuinga o te wā ka pā ki ngā wāhine waenga-pakeke, i waenga i te 40 me te 70 tau te pakeke.Koinei te tino take. Heoi, he tino onge, arā, he tino onge, kua pūrongohia kia pā ki ngā taiohi, tae atu ki ngā tamariki nohinohi.
I ngā tau o mua, arā, i ngā tau tōmua o te rautau 1900, he mea noa tēnei mate i ngā whenua Scandinavian (hei tauira, Huitene, Nōwei). Heoi, i te mutunga o ngā tau 1900, arā, i ngā tekau tau kua pahure ake nei, kua iti haere te kitea i aua whenua. Ko te take matua o tēnei ko te whakapainga o te tūnga kai o te iwi i aua whenua i taua wā, inā koa te ngāwari o te wātea o ngā kai he nui te rino.
He aha ngā raruraru ka pā mai i te PVS?
E ai ki tā tātou i kōrero ai i mua, he nui ake te tūponotanga o te hunga whai mate Plummer-Vinson syndrome (PVS) ki te whakawhanake i te mate pukupuku esophageal me te mate pukupuku hypopharyngeal, he mate pukupuku kei te pito o raro o te korokoro, e kiia nei ko te hypopharynx, i te hunga kāore he PVS.
Kaua e mataku ki tēnei. Ehara i te mea ka pāngia te katoa e te PVS e te mate pukupuku. He take mōrearea noa iho tēnei.
Nā te mea he tino onge tēnei mate, kāore i te rawaka ngā raraunga rangahau hei kī tika i te tokomaha o te hunga whai PVS ka pāngia e te mate pukupuku.
Engari ki te pāngia koe e tēnei mate, ka ngana tō tākuta ki te kite i tētahi mea pērā i te mate pukupuku i te wā tōmua , nā te mea he nui ake te tūponotanga ka taea te rongoā me te whakaora. Koia te mea nui kia tirotirohia koe i ia wā, e ai ki tō tākuta.
Me pēhea te tautuhi i te mate Plummer-Vinson (PVS)?
Mena kei a koe ngā tohu kua whakahuatia ake nei, ina haere koe ki te tākuta, ka pātai atu ia ki a koe, ka tirotirohia hoki koe. Kātahi ka whakahaua e ia he whakamātautau toto me ētahi tikanga whakaahua motuhake hei whakaū mēnā kei a koe te PVS.
- Ngā whakamātautau toto: Ko te nuinga o ēnei he tirotiro mō te mate toto ngoikore-rino.
- Te Tatau Toto Katoa (CBC): Ka taea e tēnei te tirotiro i ngā mea maha pēnei i tō toto whero, toto mā, me ngā taumata o te hemoglobin.
- Te Whakamātautau Toto Āpiti (PBS): Ko te tirotiro i tētahi tauira toto i raro i te karuārai hei tirotiro i te āhua me te rahi o ngā toto whero. Mēnā he kore rino, tera pea he iti, he mā te tae o ngā toto whero (microcytic, hypochromic).
- Ngā whakamātautau taumata rino: Mā ngā whakamātautau pēnei i te ferritin toto, te rino toto, me te TIBC (Total Iron Binding Capacity) ka taea te whakaatu i te nui o te rino i roto i te tinana.
- Ngā whakamātautau whakaahua: Ka rapua e ēnei ngā tukutuku korokoro me te pūtake o te dysphagia.
- Te tirotiro i te pito o runga (OGD - Oesophago-Gastro-Duodenoscopy):I roto i tēnei, ka whakauruhia he ngongo me te kāmera iti mā te waha, ā, ka tirohia te korokoro, te puku, me te wāhanga tuatahi o te whekau iti. Mā tēnei ka taea e koe te kite tika mēnā kei reira ngā tukutuku. Ki te tika, ka taea te tango i tētahi wahi kiko iti (biopsy) hei tirotiro.
- Te horomitanga o te barium / te esophagram: I tēnei whakamātautau, ka inu koe i tētahi matū e kīia nei ko te barium, ā, ka tangohia he pikitia hihi-X. Mā te barium ka kitea te esophagus i runga i te hihi-X, ka taea ai e koe te kite i ngā wāhi kua āraihia, kua matotoru rānei.
- Ataata-whakamātautau: He whakamātautau hihi-X anō hoki tēnei. Ka hopukina he ataata o koe e horomi ana i ngā momo kai rerekē. Ka āwhina tēnei i a koe ki te kite i te āhua o tō horomitanga me te wāhi kei reira te raruraru.
I ētahi wā, me mahi pea te tākuta i ētahi atu whakamātautau hei kimi i te tino take o te korenga o te rino. Hei tauira, ka rapu pea rātou i ngā mate puku, i te toto rānei i roto i ngā whekau.
Me pēhea te rongoā mō tēnei?
E rua ngā whāinga matua mō te rongoā i te mate Plummer-Vinson (PVS). Ko tētahi he whakatika i te korenga o te rino , ā, ko tētahi he whakatika i te uaua ki te horomi kai .
- Te rongoā mō te korenga o te rino:
- Ko te mea nui ko te whakarato i te rino e hiahiatia ana e tō tinana. Ka taea e koe te tango i ngā tāpiringa rino mō tēnei. Me tango e koe ēnei kia rite ki tā tō tākuta i tohutohu ai, mō te roanga o te wā e tohutohu ai ia ki a koe.
- Ki ētahi tāngata, ki te kore e mimiti tika ngā pire rino ā-waha, ki te tino kino rānei te korenga o te rino, ka taea te hoatu te rino mā te uaua (IV - Rino ā-uaua).
- Mena he mate hauora anō tōu e mate ai te rino (hei tauira, te toto nui o te paheketanga, te pukupuku, te mate puku), me rongoā anō hoki e koe.
- Te rongoā mō te uaua ki te horomi (Dysphagia):
- I te nuinga o te wā, ina rongoātia tēnei ngoikoretanga rino, ā, ka whiwhi te tinana i te rino, ka ngaro aunoa ngā tukutuku o te korokoro, ā, ka tino whakaitihia te uaua ki te horomi kai.
- Mehemea kāore te rongoā rino anake e tino whakaora i tō uaua ki te horomi. Mena koinā, he tikanga hei whakawhānui, hei whakaroa rānei i tō korokoro. Ka kiia tēnei ko te whakawhanui i te korokoro . Ka mahia tēnei i te wā o te endoscopy. Ka whakauruhia he taputapu iti rite ki te poihau ki te wāhanga whaiti o te korokoro, ā, ka pupuhihia, ka whakawhanuitia rānei hei whakawhānui i te korokoro. Ehara tēnei i te pokanga nui, engari he tikanga māmā noa iho, kāore he mamae, kāore e hiahiatia he tapahi i te korokoro. Tērā pea me mahi tēnei i ētahi tāngata neke atu i te kotahi.
He aha te tirohanga mō tēnei āhuatanga?
Ina hoki, ka taea e te tangata e pangia ana e te mate Plummer-Vinson (PVS) te tumanako ka pai ngā hua me te whakaoranga .
Mō te tini o te tangata, ina whakatikatikahia te korenga o te rino, ka tino heke ngā tohu o te anemia (pērā i te ngenge me te poto o te manawa). Waihoki, ka tino pai ake te uaua ki te horomi kai.
Ki te kore e ea te uaua ki te horomi mā te rongoā rino anake, ko te maimoatanga whakawhanui i te korokoro kua whakahuatia ake nei ka whakapai ake i te uaua ki te horomi. Tērā pea me mahi tēnei maimoatanga whakawhanui i ētahi tāngata neke atu i te kotahi. Engari he tikanga tino māmā, he iti hoki te mōrearea.
Tērā pea ka hiahia tō tākuta ki te mahi i tētahi tirotiro tirotiro endoscopic hei tirotiro i ngā āhuatanga pēnei i te mate pukupuku i roto i tō korokoro, i tō korokoro rānei. Engari kia maumahara, ko te PVS he take mōrearea noa iho mō te mate pukupuku. Ki te whai PVS koe, ehara i te mea ka tino pāngia koe e te mate pukupuku.
Kōrero ki tō tākuta mō te pānga o te PVS ki tō mōrearea matepukupuku, me pēhea te tiaki i a ia a muri ake nei, me te auau o ngā whakamātautau.
Ka taea te ārai i te Plummer-Vinson Syndrome (PVS)?
Kāore anō kia tino mōhiotia e ngā tākuta te pūtake o te mate Plummer-Vinson (PVS), nō reira kāore e taea te kī mārika mēnā he huarahi motuhake hei ārai i tēnei mate.
Heoi, mā te ārai i te korenga o te rino me te rongoā wawe tonu mēnā he āhuatanga tōu e puta ai te korenga o te rino, ka whakaiti pea i tō tupono ki te whakawhanake i te PVS.
Nō reira, he mea pai kia tino mohio koe kei te whiwhi koe i te rino e nui ana i roto i ngā mea e kai ana koe, e inu ana hoki. Whakaurua ngā kai whai kiko i te rino (hei tauira, te mīti whero, te pīni, te pīnihi, te rēneti, te pīni soya) ki roto i tō kai.
Āhea ahau me toro atu ki te tākuta?
Mena kei a koe ngā tohu o te anemia (hei tauira, te ngenge kore e taea te whakamanawa, te poto o te manawa, te kiri mā), ā, ki te kore aua tohu e pai ake i muri i te rua wiki pea, me toro atu koe ki te tākuta.
Waihoki, ki te mea kei te raru koe ki te horomi kai, ina koa kei te raru koe i te kai totoka , ā, kāore te āhua e pai ake, he pai ake te toro atu ki te tākuta mō ētahi tohutohu kaua e warewarehia.
He aha taku e pātai atu ai ki te tākuta?
Ina haere koe ki te tākuta, pātai atu ki a ia mō ō āwangawanga me ō wehi. Hei tauira, ka taea e koe te pātai i ngā pātai pēnei:
- He aha pea te take e pāngia ai ahau e tēnei mate toto iti?
- He aha ngā whakamātautau me mahi e au kia tino mōhio ai ahau mēnā kei a au te mate Plummer-Vinson (PVS)?
- He aha te momo maimoatanga e taunaki ana koe māku?
- Me pokanga whakawhanui te korokoro hei whakatika i taku dysphagia? E hia ngā wā me mahi?
- Me āwangawanga ahau mō te tūponotanga o te mate pukupuku ā muri ake nei? Me aha ahau mō tēnei?
Ki te whakaaro koe kei a koe ngā tohu o te mate Plummer-Vinson (PVS), me toro atu ki te tākuta tonu. Kāore koe e hiahia ki te noho me te ngenge puhoi e puta mai ana i te anemia. Kāore hoki koe e hiahia ki te noho me te mamae o te horomitanga (dysphagia) e waiho ai te kai hei mahi uaua. I ētahi wā, he māmā noa iho te otinga, pērā i te tango i ētahi papa rino. Ki te kore, tera pea ka kitea e koe he whakamarie mā te whakawhānui i tō korokoro. Heoi, kei reira ngā maimoatanga hei āwhina i a koe kia pai ake te ahua .
Hei whakamutunga, ko ngā mea tino nui hei maumahara
He mate tino onge te Plummer-Vinson syndrome (PVS). Heoi, ko ōna āhuatanga matua ko te anemia kore rino, te uaua ki te horomi (dysphagia), me ngā whatu korokoro . Mena kei te pāngia koe e te ngenge tonu, te uaua ki te horomi, te mamae rānei o te arero, he mea nui kia toro atu ki te tākuta kaua e whakakorea he mea noa.
He pai ngā maimoatanga mō te PVS. I te nuinga o te wā, ka pai ake ngā tohu ina whakatikatikaina te ngoikore o te rino, ā, ina whakawhanuitia te korokoro mēnā e tika ana.
Ahakoa e kōrero ana tātou mō te mōrearea o te mate pukupuku, kia maumahara he take mōrearea noa iho tēnei. Ki te kōrero koe ki tō tākuta, ki te whiwhi i ngā whakamātautau e tika ana, ā, ki te whiwhi i te maimoatanga tika, ka taea e koe te noho hauora. Nō reira kaua e wehi i tetahi mea, ā, ki te pā mai he raruraru ki a koe, rapua tonutia he tohutohu hauora. He mea nui tō hauora ki a koe!
👩🏽⚕️ Ngā pātai tāpiri (FAQs)
💬 He mate korokoro te Plummer-Vinson Syndrome?
Ehara i te mea he raruraru korokoro anake tēnei, he mate morearea e pā ana ki te korokoro nā te 'korenga kai nui'. Nā te mate toto nui o te korenga rino, ka puta he 'hanganga tukutuku' (whatunga esophageal) ki te tihi o tō esophagus, ka uaua ai te horomi kai.
💬 He aha ngā kare ā-roto e pā mai ana ina kai ahau me tēnei puku i roto i tōku korokoro?
Ko te tohu matua ko te (Dysphagia) te 'uaua ki te horomi'! Ahakoa ka taea e koe te inu wai, ina kai koe i ngā kai totoka pēnei i te raihi/mīti, ka rite koe ki te 'pūpū e mau ana i roto i tō korokoro'. Waihoki, nā te korenga o te rino, ka mamae ō ngutu i ngā taha e rua (Cheilitis), ka whero, ka pupuhi tō arero (Glossitis), ā, ka rite ō maikuku ki te pūnu (Koilonychia).
💬 Mā te pokanga ka tangohia tēnei kiriuhi/mata e ārai ana i te korokoro?
Kāore he pokanga nui e hiahiatia ana! Ko te mea tino miharo ki te tini o te tangata ko te wā e hoatu ana e te tākuta he 'tāpiritanga rino' me te whakatikatika i ngā taumata rino i roto i te toto, ka memeha te kiriuhi i roto i te korokoro, ā, ka taea te horomi i te kai! Engari ki te kore e ngaro, ka whakauruhia he kāmera endoscopy, ā, ka tukuna he poihau iti (Poihau whakawhanui) hei whakawhānui/wāhi i te kiriuhi.
Te mate Plummer-Vinson, PVS, te korenga o te rino, te dysphagia, te uaua ki te horomi, te varices esophageal, te anemia











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