Kua rongo koe i tētahi āhuatanga rerekē e pā ana ki te roro me te mahara? I ētahi wā, kāore tātou e mōhio ana ina kore ētahi huaora o roto i tō tātou tinana, inā koa ko te huaora B1 e kiia nei ko te "Thiamine", ka tino kino te pakaru o tō tātou roro. Ko tētahi o aua āhuatanga kino ko te "Wernicke-Korsakoff Syndrome" ("WKS") . He āhuatanga tēnei e hiahia ana kia rongoatia wawetia. Me kōrero noa iho tēnei, kia mārama ai koe?
He aha rawa te mate Wernicke-Korsakoff (`WKS`)?
Ki te kī ngāwari, he mate tēnei e pā ana ki tō tātou roro me te mahara. Ko te take matua mō tēnei he nui te hekenga o te 'Thiamine' (`Thiamine`) o te huaora B1 rānei i roto i tō tātou tinana. Whakaarohia, he rite tō tātou tinana ki te waka. Ko te roro te miihini o tēnei waka. Me whakamahi te miihini i te penehīni hei whakahaere. Waihoki, ko te huaora e kiia nei ko te 'Thiamine` (`Thiamine`) he mea nui kia mahi ai tō tātou roro me te pūnaha io. Ko tēnei huaora te mea e huri ai te kai e kainga ana e tātou hei pūngao. Nō reira, ina heke te 'Thiamine` (`Thiamine`), kāore te roro e whiwhi i te pūngao e hiahiatia ana, kātahi ka tīmata te pakaru o ngā pūtau roro.
E rua ngā wāhanga matua o tēnei `WKS`:
1. Te mate pukupuku o Wernicke: Koinei te whara roro tuatahi, ohorere, kino hoki. Me tere tonu te maimoatanga.
2. Te mate Korsakoff: He mate roa tēnei e tino pā kino ana ki te mahara.
I tapaina tēnei ingoa i muri i te tohunga roro Tiamana a Carl Wernicke me te tohunga roro Rūhia a Sergei Korsakoff, nā rāua i tautuhi tuatahi i te mate.
He aha te whanaungatanga i waenga i te 'Wernicke's encephalopathy' me te 'Korsakoff syndrome'?
He hononga tō rāua. Hei whakamārama, ko te mate e kiia nei ko te "Wernicke encephalopathy", ki te kore e rongoatia i te wā tika, ka whanake haere hei raruraru mahara nui e kiia nei ko te "Korsakoff syndrome".
E toru ngā tohu matua o te Wernicke encephalopathy:
- Pōhēhētanga: Te ngaronga o te māramatanga, te ngaronga o te wāhi me te wā.
- Te ngaronga o te taurite me te kore e taea te whakahaere i ngā nekehanga (`Ataxia`): Ka kore e pumau te hikoi, ā, ka uaua te whakahaere i ngā waewae.
- Ngā huringa tirohanga me ngā raruraru kanohi: Ngā nekehanga kanohi rerekē, pērā i te kitenga takirua.
Hei tāpiritanga ki tēnei, i ētahi wā ka ngoikore ngā uaua.
Ki te roa te mau o ēnei tohu, ka pā he kino tuturu ki te roro me ngā pūtau io. Koinei te wā ka ngaro nui te mahara, ā, kāore e taea te maumahara i ngā maharatanga hou. Ka kiia tēnei ko te "mate Korsakoff".
Ko te Wernicke-Korsakoff Syndrome (WKS) he mate ka kino haere i roto i te wā, ā, ka mate pea. Nō reira, he mea nui te rongoā tere ki te thiamine. Mā te mahi pera ka āwhina i te whakamamae i ngā tohu me te ārai i te kino tuturu ki te mahara me ētahi atu mahi roro.
Mena kei a koe, kei tētahi rānei e tata ana ki a koe ēnei tohu, me toro atu tonu koe ki te tākuta, me haere rānei ki te hōhipera tata.
Ko wai te mea tino pāngia e tēnei āhuatanga?
He nui ake te kitea o te mate Wernicke-Korsakoff (WKS) i roto i ngā tāne i ngā wāhine. I te nuinga o te wā ka pā ki te hunga i waenga i te 30 me te 70 tau te pakeke. Ko te nuinga o te hunga e pāngia ana e te WKS nā te inu waipiro he tāne neke atu i te 40 tau te pakeke. Heoi, ka taea hoki e ngā wāhine me ngā taiohi te pāngia e te mate mō ngā take ehara i te waipiro. He onge te pūrongo mō ngā tamariki nohinohi.
Ko wai kei te nui ake te mōrearea ki te whakawhanake i te mate Wernicke-Korsakoff?
Ko te mate Wernicke encephalopathy he mate e kitea nuitia ana i roto i te hunga e whakamahi nui ana i te waipiro (mate whakamahi waipiro). Ina roa te inu waipiro, ka kino te puku me te pūnaha nakunaku. Ka whakararuraru hoki i te kaha o te tinana ki te mimiti i ngā huaora (malabsorption). E kiia ana tata ki te 80% o te hunga inu waipiro kāore e taea te mimiti, te pupuri rānei i te thiamine.
Hei tāpiritanga, ko te hunga kāore e taea te mimiti tika i te kai nā ētahi āhuatanga hauora ka pāngia e te `WKS`. Hei tauira, ka puta pea i muri i te pokanga whakaiti taumaha (`pokanga bariatric`) he pānga taha rānei o te `chemotherapy` mō te mate pukupuku.
Anei ētahi atu āhuatanga mōrearea:
- Ngā mate puku, hei tauira, te mate mumura o te puku, te mate puku rānei.
- Te mate pukupuku (ina koa i ngā wā tino kino).
- Te nui rawa o ngā homoni tairoi (thyrotoxicosis).
- Ētahi whakarerekētanga ira.
- Te whakamahinga o te diuretic hei rongoā mō te ngoikore o te ngakau mo te wa roa.
- Ngā mate koretake o te thiamine pērā i te HIV/AIDS.
- Te ngoikore o te whatukuhu, nā te mea ka whakaitihia e te maimoatanga dialysis te kaha o te tinana ki te mimiti i te thiamine mō te wā roa.
- Te kore e taea te toro atu ki ngā whare hauora, te kore rānei e taea te tiki kai whai kiko.
- Te ruaki nui me te whakapairuaki i te wā e hapu ana (hyperemesis gravidarum).
He aha ngā take o te 'Wernicke-Korsakoff syndrome'?
Ko te take matua mō tēnei ko te korenga o te "Thiamine". Ko tēnei huaora nui te mea e huri ai te huka e kainga ana e tātou hei pūngao. Nō reira, ki te kore e ranea te "Thiamine", kāore e whiwhi te roro i te pūngao e hiahiatia ana hei mahi tika.
Ko te tino take o te korenga o te thiamineTe inu nui i te waipiro mō te wā roa. Ka uaua te mimiti o te thiamine me te penapena i roto i te ate e te waipiro. Ka whakararuraru hoki te waipiro i te whakamahinga o te huaora B1 mō ētahi atu mahi nui.
Tērā atu anō ētahi take:
- Kai tōtika kore: Te kore e kai i te kai taurite.
- Ngā mate kai: pērā i te anorexia me te bulimia.
- Ngā mate pāwera mau tonu.
- Ngā pokanga: Ina koa ko ngā pokanga pēnei i te pokanga bypass puku hei whakaiti i te taumaha.
- Te whara roro: Engari he onge noa iho tēnei.
He aha ngā tohu o te 'Wernicke-Korsakoff syndrome'?
Ka kitea pea tēnei i roto i ngā momo tohu. Ko tētahi o ngā tohu e kitea whānuitia ana i ngā wā tino kino ko te 'confabulation' . Arā, ko te tito kōrero i roto i tō hinengaro hei huna i ngā mea kāore koe e mahara. Whakaarohia, kāore tetahi e mahara ki tētahi mea i mahia e rātou inanahi, engari ka kōrero teka rātou hei huna, engari kāore rātou e teka nā te mea e whakaaro ana rātou i tupu tūturu. E whakapono ana rātou ki te kōrero.
He maha ngā wā ka pōhēhē, ka ngaro rānei te huarahi e haere ai te hunga whai mate pēnei. Nā tēnei pōhēhētanga ka uaua ki a rātou te mōhio kei te hē tetahi mea kei roto i a rātou, ā, ka uaua ki te rapu maimoatanga.
Ngā tohu noa o te encephalopathy Wernicke:
- Te ngaronga o te taurite, te kore rānei e taea te whakahaere i ngā nekehanga (ataxia).
- 'Whakataurite'.
- Pōhēhē, pōrangi.
- Te uaua ki te hikoi, te tūnga koretake.
- Te hiamoe.
- Te pāmahana tinana tino iti rawa (hypothermia).
- Ngā raruraru o te ngākau: te piki haere o te tere o te ngākau (tachycardia) te iti rānei o te toto toto (hypotension).
- Te ngaronga o te taunga o ngā uaua (ataxia).
He maha anō hoki ngā raruraru kanohi:
- Ngā nekehanga kanohi rerekē (nystagmus).
- Tirohanga takirua.
- Te piko o te kamo o runga (ptosis).
- Te ngoikore, te koretake rānei o te uaua o te kanohi (ophthalmoplegia).
Ki te kore e rongoatia te mate Wernicke encephalopathy, ka taea e ia te whanake hei mate Korsakoff, he mate mahara roa. Ko ōna tohu ko:
- Te ngaronga katoa o te mahara ('Amnesia') te kore rānei e taea te maumahara ki tētahi mea hou.
- Ngā huringa whanonga: te riri, te tere o te pukuriri.
- 'Whakataurite'.
- Te pōrangi me te kore aro.
- Te ngenge, te mangere rānei.
- Ngā moemoeā, inā koa i te wā e mutu ai te inu waipiro.
- Te kore e taea te arotahi.
- Te hikoi pōturi.
Ahakoa te rongoā, kāore ētahi tohu e tino pai ake. I ngā wā tino kino, ka ngaro pea te māramatanga (`coma`). Ki te ngaro te māramatanga o koe, o tētahi rānei e tata ana ki a koe, ki te pāngia rānei koe e ngā tohu o te `Wernicke-Korsakoff syndrome`, me toro atu ki te tākuta, me haere rānei ki te rūma whawhati tata tonu.
Me pēhea te tautuhi i te 'syndrome Wernicke-Korsakoff'?
He mea nui te kitenga wawe i tēnei mate `WKS` mō te angitu o te maimoatanga. Ka tātaritatia e ngā tākuta mā te whakamātautau tinana, te pātai mō ō tohumate, me te pātai mō tō hītori whānau. Heoi, he uaua ki te tātaritatia ina pōhēhē te tangata, ina ngaro rānei tōna mahara.
Ka tirohia motuhaketia e te tākuta ēnei mea:
- He raruraru whakamahi waipiro kei reira ('Te mate whakamahi waipiro')?
- He matekai koretake rānei?
- He ngoikore te thiamine?
He aha ngā whakamātautau ka āwhina i te tautuhi i te mate Wernicke-Korsakoff?
Ka whakahau tō tākuta i ngā whakamātautau toto hei tirotiro i tō huka toto me ngā taumata thiamine. Tērā pea ka whakahau ia i tētahi whakamātautau waipiro toto hei tirotiro i te whakamahinga waipiro me tētahi whakamātautau mahi ate hei tirotiro i te mahi ate, nā te mea tera pea he tohu tēnei kua pakaru te ate.
Tērā pea ka whakahaerehia ētahi atu whakamātautau hei tirotiro i ētahi atu take:
- Te whakamātautau hau toto uaua (ABG), e tirotiro ana i ngā taumata o te hauhā me te hāora i roto i te toto.
- 'Tau toto katoa' (`Tau toto katoa - CBC`).
- Te tirotiro i te paitini.
Me whai whakamātautau whakaahua anō pea koe pēnei i ēnei:
- 'Matawai CT'.
- 'MRI' (`MRI`).
- 'Whakamārama manawa-hiko' ('Whakamārama manawa-hiko - EKG').
Ka taea te whakaora i te mate Wernicke-Korsakoff? Me pēhea te rongoā?
Ina hoki, kāore e taea te whakaora katoa. Heoi, ki te tīmata wawe te maimoatanga, ka taea te whakamama i ngā tohu, ā, ka taea te whakakore i ētahi o aua tohu. Ko te tikanga o tēnei ka taea te aukati i te kino haere o te mate "Wernicke encephalopathy" ki te "Korsakoff syndrome".
I te nuinga o te wā, ka taea e te maimoatanga te whakahaere, te whakapai ake rānei i ngā tohu pēnei i te pōhēhē, ngā raruraru kanohi, me te ngaronga o te taurite. Ma tō tākuta e whakawhanake he mahere maimoatanga e tika ana māu.
Hei maimoatanga, ko ngā mahi e whai ake nei ka mahia i te nuinga o te wā:
- Te hoatu i te huaora B1 mā roto i ngā pire, i ngā werohanga rānei.
- Ki te matewai te tinana, hoatu he tote mā roto i ngā "wai werohanga".
- Te rongoā i ngā raruraru e pā ana ki te whakamahinga waipiro.
- Te whakarato tautoko kai.
- Whakaratohia ētahi atu rongoā mēnā e tika ana.
Me pēhea te whakaiti i te mōrearea o te whakawhanaketanga o tēnei mate?
I te nuinga o te wā, ko te whakamutu, te whakawhāiti rānei i te inu waipiro te mea nui rawa atu hei whakaiti i tō tupono ki te whakawhanake i te mate Wernicke-Korsakoff. Waihoki, mā te kai pai, me te tango i ngā tāpiringa thiamine i roto i te ahua o ngā werohanga, ngā pire rānei, ka āwhina i te whakaiti i tō tupono, inā koa mō te hunga e waranga ana ki te waipiro.
He aha te āhua o te mate mō te tangata e pāngia ana e te mate Wernicke-Korsakoff?
Mena kei a koe, kei tētahi rānei e tata ana ki a koe tēnei mate, ko te āhua o te mate ka whakawhirinaki ki te kaha o ngā tohu me te tere o te tautuhi me te rongoā i te mate. Mā te rongoā wawe ka taea te whakakore i ngā tohu me te ārai i ngā raruraru roa. Heoi, ki te kore e rongoātia, ka arahi pea ki te hauātanga me te mate.
Āhea koe me rapu tohutohu hauora mō tēnei mate?
Mena kei a koe, kei tētahi atu rānei e mōhio ana koe, ngā tohu o te mate Wernicke-Korsakoff, rapua tonutia he awhina hauora. Me waea atu pea koe ki tō tākuta, me haere rānei ki te rūma ohorere o te hōhipera tata rawa atu mō te maimoatanga ohorere.
Me pēhea taku tiaki i ahau anō?
Ehara i te mahi ngāwari te whiwhi tātaritanga mō te mate Wernicke-Korsakoff. Me kawe pea koe ki te hōhipera, ā, me whiwhi maimoatanga. Ko te mea nui ko te whai i ngā tohutohu a tō tākuta, pērā i te whakawhāiti i tō inu waipiro (te whakamutu rānei i te inu waipiro) me te kai i ngā kai totika. Mā ēnei mea ka tino tautoko i tō oranga.
Kia ata whai i ngā tohutohu a tō tākuta hei whakahaere i ngā raruraru me te rongoā i ngā tohumate. Māna e waihanga he mahere tiaki whaiaro e tika ana māu, ā, māna koe e āwhina kia hoki anō ki tō hauora.
He mate mahara onge engari he kino te mate Wernicke-Korsakoff. Me tere te maimoatanga hei whakamamae i ngā tohu me te ārai i ngā raruraru. I te haere whakamua o te mate, ka puta ngā tohu o te pūnaha io, pērā i te pōhēhē nui me te koretake o te hinengaro. Ka uaua pea māu, mā tētahi rānei e tata ana ki a koe te kite i tō āhua i ēnei tohu. Nō reira, he mea nui kia wawe te tātaritanga i te mate. Ka tūtohu tō tākuta i tētahi mahere maimoatanga e hāngai ana ki ō hiahia.
Ngā mea tino nui hei maumahara (Karere hei kawe ki te kāinga)
Āe, anei ngā mea matua hei maumahara māu mō te 'Wernicke-Korsakoff Syndrome' i kōrerohia e tātou:
- He mate kino tēnei e pā ana ki te roro me te mahara nā te korenga o te thiamine (huaora B1).
- Ko te tino take mōrearea ko te nui rawa o te inu waipiro.
- Ko te wāhanga tuatahi ko te Wernicke encephalopathy, ki te kore e rongoatia, ka arahi pea ki te raru mahara mo te wa roa e kiia nei ko te Korsakoff syndrome.
- Ko te pōhēhē, te uaua ki te hikoi, ngā raruraru tirohanga, me te ngaronga o te mahara pea ngā tohu matua.
- He mea nui te tere o te tautuhi mate me te maimoatanga ohorere ki te thiamine.
- Ahakoa kāore e taea te whakaora katoa, mā te maimoatanga wawe ka taea te whakahaere i ngā tohu me te ārai i ngā kino tuturu.
- Mena kei te whakaatu koe, tetahi atu rānei e mōhio ana koe i ēnei tohu, rapua tonutia he tohutohu hauora.
Ko tāku tumanako ka whai hua ēnei kōrero ki a koe. Kia ora tonu!
Te mate Wernicke-Korsakoff, te korenga o te thiamine, te huaora B1, te whakamahi waipiro, te ngoikore o te mahara, ngā mate roro, ngā mate pūnaha io











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