Kei te ngoikore koe i ētahi wā, kei te werawera koe, kei te kikorangi ō kanohi, kei te pōuri hoki? Tērā pea nā te hekenga ohorere o ō taumata huka toto ( hypoglycemia ) tēnei. He mea noa tēnei mō te tangata mate huka , pērā i te nui rawa o ngā rongoā e tangohia ana e rātou, te ngaro rānei i te kai. Engari, ki te pā tēnei ki te tangata kāore he mate huka i ngā wā katoa, tera pea he mea kāore koe e whakaaro ki te take. He āhuatanga onge tēnei me mōhio tātou katoa, e kiia nei ko te insulinoma .
He aha tonu te insulinoma?
He kupu ngāwari, he pukupuku iti te insulinoma, ehara i te matepukupuku e tupu ana i roto i tō tātou repe taiaki . Ka whakaputahia e tō tātou repe taiaki he homoni e kiia nei ko te insulin. Ko te mahi a tēnei insulin he whakahaere i te nui o te huka (glucose) i roto i te toto.
Whakaarohia, i te nuinga o te wā, ina piki ake te taumata huka o te tinana, ka whakaputa te repe taiaki i te insulin. Ina heke te taumata huka, ka mutu te whakaputa i te insulin. He rite ki te pana e tahuri ana, e whakaweto ana rānei i te wā tika.
Engari ina whanake tēnei pukupuku e kiia nei ko te insulinoma, ka puta tonu te insulin . Me te mea kua mau te pana ki te tūranga 'kā'. Ko te mea ka tupu, ka puta tonu te insulin ahakoa he tino iti te taumata huka toto. Ka taea e tēnei te heke iho i te taumata huka toto. Nā te mea he momo pūtau io motuhake ēnei pukupuku (ngā pūtau neuroendocrine), ka kiia pea rātou e tō tākuta he "pukupuku neuroendocrine". He iti rawa ēnei pukupuku (iti iho i te inihi) ā, neke atu i te 90% ehara i te matepukupuku. Nō reira, ka taea te whakaora katoa mā te pokanga.
He aha ngā tohu o tēnei mate?
Nā te mea kei te haere tonu te whakaputa insulin a te insulinoma, ka puta ngā tohu i te iti o te huka toto (hypoglycemia). Ka puta ohorere mai ēnei tohu.
| Tohu | He whakamārama māmā |
|---|---|
| Pōhēhētanga | Kāore e taea te mārama he aha te mea e tupu ana, kei hea koe, ā, e pōuri ana hoki koe. |
| Te werawera nui (Sweating) | Kātahi ka mātao, ka werawera, kāore he take. |
| ngoikore | Kei te āhua ngaro te ora o tō tinana, kei te wiri ō waewae me ō waewae. |
| Te manukanuka me te pikinga o te tere o te ngakau | Te wehi kore take, te āhua e tere ana te patu o tō uma. |
| Te ānini nui | Te tīmatanga ohorere o te mamae nui o te upoko. |
| Ngā huringa tirohanga | Ngā āhuatanga pēnei i te tirohanga pōuri, te tirohanga takirua, me ētahi atu. |
| Ngā huringa whanonga | Ka riri noa iho, ka pōrearea. |
| Te hopuhopu | Ina tino heke tō taumata huka, tera pea ka pāngia koe e te mate pāwera. |
Ko te mea nui: Ka taea e te hypoglycemia kino te morearea. Ka taea e ia te ngoikore, te koma rānei. Nō reira, ki te pāngia koe e ēnei tohu, me toro atu ki te tākuta tonu.
He aha ngā take o te insulinoma? Ko wai kei te mōrearea nui ake?
Kāore anō kia kitea te tino pūtake o ēnei pukupuku, engari tera pea ētahi āhuatanga ka piki ake te mōrearea.
- He paku teitei ake te āhua o ngā wāhine i ngā tāne.
- Ko te nuinga o te wā ka kitea tēnei mate i roto i te hunga i waenga i te 40 me te 60 tau te pakeke .
- He nui ake te mōrearea o te hunga whai mate ira . Hei tauira:
- He momo neoplasia endocrine maha 1: He āhuatanga e puta ai ngā pukupuku i roto i ngā repe whakaputa homoni.
- Te mate a Von Hippel-Lindau: He āhuatanga e puta ai ngā pukupuku me ngā hanganga rite ki te pukupuku ( ngā kiore ) i roto i ngā momo okana o te tinana.
- Neurofibromatosis momo 1: Ngā tipu ehara i te matepukupuku ki ngā io me te kiri.
- Te sclerosis ngongo: Ngā pukupuku kore-matepukupuku i roto i ngā whekau pēnei i te roro, ngā kanohi, te ngākau, me ngā whatukuhu.
Me pēhea te kitenga a te tākuta i tēnei?
He uaua pea te tātaritanga i te insulinoma, nā te mea he rite ngā tohu ki ērā o ētahi atu mate noa, nō reira ka roa pea te wā e tātaritanga ai tō tākuta.
Ko te mea nui ko te mahi i te 'nohopuku 72-hāora' . I roto i tēnei, ka noho koe ki te hōhipera mō ngā rā e rua, e toru rānei, ā, kāore e whakaaetia kia kai, kia inu rānei i tētahi mea engari ko te wai anake. I tēnei wā, ka tirotirohia tonutia e ngā tākuta tō huka toto me ō taumata insulin.
E ngana ana rātou ki te whakaū i ēnei mea e toru mā tēnei whakamātautau:
1. Kei te pāngia koe e ngā tohu o te huka toto iti (pēnei i te whanoke, te werawera?
2. Ina puta mai aua tohu, he tino iti rawa te taumata huka toto?
3. Ka memeha haere ngā tohu ina hoatu he huka (huka) ki waho?
Mena he insulinoma tōu, ka tino iti te taumata huka toto i roto i te nohopuku, engari ka teitei te taumata insulin. Koinei te taunakitanga matua. Haunga tēnei, ka rapua hoki e ngā whakamātautau toto ngā mea pēnei i te `(C-peptide)` me te `(proinsulin)`.
Kātahi ka mahia ngā whakamātautau whakaahua hei kimi i te wāhi tika kei reira te pukupuku repeure.
- Matawai CT `(Matawai CT)`
- Matawai Ultrasound `(Ultrasound)`
- Matawai MRI `(MRI)`
He aha ngā maimoatanga mō tēnei?
Ko te maimoatanga matua me te tino angitu mō te insulinoma ko te pokanga hei tango i te pukupuku . I te nuinga o te wā, ka ora katoa te mate i muri i te pokanga.
Ko te momo pokanga e mahia ana ka whakawhirinaki ki te momo, te rahi, me te taunga o te puku.
- Te tango i te pukupuku anake: Ka taea e ngā taote pokanga te tango marie i te pukupuku anake me te kore e kino te repe taiaki.
- Te tango i tētahi wāhanga o te repe taiaki: I ētahi wā me tango hoki tētahi wāhanga iti o te repe taiaki e pā ana ki te pukupuku.
Nā te hangarau matatau o ēnei rā,Ka taea hoki te tango i ēnei pukupuku mā te pokanga laparoscopic. Ko te tikanga, kaua e tapahia kotahi te tapahi nui, ka mahia te pokanga mā roto i ētahi tapahi iti me te āwhina o te kāmera. Ko ngā painga o tēnei he iti ake te mamae, he poto ake te maha o ngā rā e noho ana koe i te hōhipera, ā, ka taea e koe te hoki wawe ki tō oranga noa.
Te maimoatanga mō ngā pukupuku matepukupuku
He tino onge (iti iho i te 10%) te hurihanga o ēnei pukupuku hei matepukupuku. I ēnei āhuatanga, ka rerekē te maimoatanga. Mena kāore e taea te tango i te pukupuku katoa mā te pokanga, me tango pea koe i te rongoā hei aukati i te hekenga o te huka toto. Me whai chemotherapy anō hoki koe. Mō ētahi momo matepukupuku, he maimoatanga motuhake, pērā i te "Lutetium Lu 177 dotatate", arā, ko te hoatu i te rongoā irahiko mā roto i te uaua.
He raruraru kei muri i te pokanga?
Ahakoa e angitu ana te pokanga i te nuinga o ngā wā, pērā i ngā pokanga katoa, kei reira tonu te mōrearea o ngā raruraru iti.
- Te toto
- Mate pāwera
- Mamae
- Ki te tangohia tetahi wāhanga nui o te repe taiaki, tera te tūponotanga ka pāngia koe e te mate huka.
- Te turuturu o te wai mai i te repe taiaki (Pankreatic fistula)
- Te whakaiti i ngā whākōkī nakunaku.
Mena he pukupuku matepukupuku, tera pea ka puta he raruraru pēnei i te horapa o te mate ki ētahi atu okana (metastasis). Ma tō tākuta tēnei e whakamārama taipitopito atu ki a koe.
Karere Tangohia ki te Kāinga
- He pukupuku onge te Insulinoma e puta ana i roto i te repeure. Nā tēnei ka iti tonu te taumata huka toto.
- Ki te pāngia koe e ngā tohu ohorere pēnei i te whanoke, te werawera nui, me te pōhēhē, kāore he take e kitea ana, inā koa kei te hiakai koe, me toro atu ki te tākuta tonu.
- Me noho koe ki te hōhipera me ngā whakamātautau toto me ngā karapa motuhake hei tautuhi i te mate.
- Ko te maimoatanga matua ko te tango pokanga i te pukupuku, ā, he maha ngā wā ka ora katoa te hua.
- Ehara te nuinga o ngā insulinoma i te mate pukupuku, nō reira kāore he take e mataku ai. Heoi anō, me toro atu ki tō tākuta kia tika ai te tātaritanga me te maimoatanga.











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