Ka tīmata ohorere koe ki te mākūkū, ka whero tō kiri, ka puta he ponana? Ka pāngia rānei tō puku e te ruaki? I ētahi wā ka puta ēnei āhuatanga i muri i te whakamahinga o tētahi hinu kakara, i muri rānei i te kai i tētahi kai, ā, i ētahi wā ka puta noa iho, kāore he take. Ki te kore e kitea he take mō tēnei, ā, he rerekē ngā tohu i ngā wā rerekē, tera pea he mea nui atu i te mate pāwera noa iho. I tēnei rā kei te kōrero tātou mō tētahi o aua āhuatanga, ko te Mast Cell Activation Syndrome (MCAS).
He aha te Mast Cell Activation Syndrome (MCAS)?
Ki te kī māmā noa, ko te MCAS he āhuatanga e kore e hiahiatia, e nui rawa hoki te mahi a tētahi momo pūtau i roto i te tinana e kiia nei ko ngā 'pūtau mast', ka tukuna he nui o ngā matū kei roto i a rātou ki roto i te tinana.
Nā, kia titiro tātou ki ēnei pūtau mast. Whakaarohia ēnei pūtau hei kaitiaki haumaru o te tinana. He wāhanga rātou o tō tātou pūnaha ārai mate. Ko tā rātou mahi matua he whawhai ki ngā mate pāwera. Engari ko ēnei pūtau anō hoki te take o ngā mate pāwera. I te nuinga o te wā, ina uru mai tētahi mea kino ki a tātou, hei tauira, he mate pāwera ki te tinana, ka whakahohehia ēnei pūtau mast ka tukuna ngā matū e kiia nei ko ngā 'kaitakawaenga'. Ko ēnei matū te take o te urupare mate pāwera i roto i tō tātou tinana. I roto i te tangata hauora, ko tēnei tukanga hei tiaki i a tātou.
Engari, i roto i te tangata whai MCAS, he tino tairongo ēnei pūtau mast . Ka tino harikoa rātou ahakoa te mea iti rawa, ā, ka tukuna he nui o ngā matū i te wā kotahi. He rite ki te kawe mai i tētahi ope katoa ki te hopu i tētahi tahae iti. Ko ēnei matū kāore e hiahiatia te take o te maha o ngā tohu rerekē, whakarihariha i kōrerohia e tātou i mua ake nei.
He maha ngā mea ka taea te whakaoho i ēnei pūtau mast:
- Ngā mate urutā
- Ētahi rongoā
- Te paitini mai i ngā ngau pepeke
- Ngā kakara
- ahotea
- Whakakorikori tinana
- ētahi kai
- Ngā huringa ohorere o te pāmahana
He rerekē te MCAS me te Mastocytosis?
Āe, kaua e whakapoauau i ngā mea e rua. Ahakoa he rerekē ngā pūtau mast i roto i ngā āhuatanga e rua.
| Āhuatanga hauora | Hei whakarāpopototanga, he aha te mea ka tupu? |
|---|---|
| Te Mastocytosis | Ko te mea ka tupu i roto i tēnei , ka puta he nui rawa ngā pūtau mast i te tinana. He rite ki te whakauru i ngā kaitiaki haumaru maha rawa. Ka kohia ēnei pūtau taikaha ki roto i ngā whekau pēnei i te kiri, te ate, me ngā whekau. He tino onge tēnei mate. |
| MCAS (Mate Whakahohe Pūtau Matua) | Ko te mea e tupu ana i tēnei take, he noa te maha o ngā pūtau mast i roto i te tinana, engari ka kaha rawa te mahi a ngā pūtau kei reira. Ka oho ake ngā kaitiaki kei reira mō tetahi mea iti noa iho, ā, ka tukuna ngā matū. |
He aha ngā take o te MCAS?
E toru ngā wāhanga matua o te MCAS, i runga i te pūtake.
1. MCAS Matua: Ka puta tēnei i te raruraru o ngā pūtau mast. He maha ngā wā, ka rerekē te whanonga o ēnei pūtau nā te whakarerekētanga o te ira ``(KIT)``. Ko te mastocytosis te mate matua o tēnei momo.
2. MCAS Tuarua: Ka puta tēnei ina whakaohokia ngā pūtau mast e tētahi atu take o waho. Hei tauira, ka puta pea tēnei i tētahi mate pāwera nui, i tētahi mate pūmau, i tētahi atu mate hauora rānei.
3. MCAS Idiopathic: Ko te tikanga o te "Idiopathic" ko te "kāore e kitea he take." Ko te nuinga o ngā tūroro MCAS he momo MCAS tēnei. Ko te tikanga tēnei kāore he take motuhake e whanonga rerekē ai ēnei pūtau mast. Tērā pea ka puta ngā tohu mō ngā mea hou i ngā wā katoa.
He aha ngā tohu pea o te MCAS?
Ko tētahi o ngā wero nui o te MCAS ko te kanorau o ngā tohu, ā, ka pā ki ngā pūnaha tinana maha i te wā kotahi.
| Kāwai tohu | Ngā tohu e kitea whānuitia ana |
|---|---|
| Kiri me ngā āhuatanga whānui | Te whero o te kiri, te mākūkū, te ponana/te whewhe, te pupuhi, te werawera nui, te ngenge mau tonu, te mamae o te tinana. |
| Pūnaha nakunaku | Mamae puku, whakapairuaki, ruaki, korere, kōroke. |
| Pūnaha io (Neurological) | Te ānini o te upoko, ngā raruraru mahara me te aro (te kohu roro), te whanoke, te ngoikore, te manukanuka, te pouri, te kore moe. |
| Ngākau me te pūnaha manawa | Te tere o te manawa, te koretake o te manawa, te kikī o te uma. |
Aroturuki motuhake: Te ohorere anaphylactic
Ko te anaphylaxis te mate tino morearea, tino whakamataku hoki ka pā ki te hunga whai MCAS. He mate tēnei e hiahia ana kia rongoatia wawetia.
Ngā tohu o te anaphylaxis:
- He uaua ki te manawa, me te mea kei te kikī tō korokoro
- Te pupuhi o ngā ngutu, o te arero, o te mata rānei
- He tino tere te tere o te manawa.
- Te hekenga ohorere o te toto toto
- Te whanoke nui me te ngoikore
- Te ruaki me te mate korere
- Te whero ohorere me te ponana puta noa i te tinana
Ki te pāngia koe e tētahi, e ētahi rānei o ēnei tohu, kaua e whakaroa. Waea atu ki te waka tūroro tonu atu, haere rānei ki te Tari Ohotata (ETU) o te hōhipera tata.
Me pēhea taku mōhio mēnā kei a au te MCAS?
He uaua pea te tātaritanga o te MCAS nā te mea he rerekē ngā tohu. E toru ngā mea e rapuhia ana e tō tākuta.
1. Ngā Tohu: Ko te kitea o ngā tohumate pāwera mau tonu, e hokihoki mai ana i roto i ngā pūnaha tinana e rua, neke atu rānei (hei tauira, te kiri me ngā whekau).
2. Ngā whakamātautau: Ko ngā tauira toto, mimi rānei i tangohia ina puta ngā tohu ka whakaatu i ngā taumata teitei o ngā matū pēnei i te "tryptase" me te "histamine", e tukuna ana e ngā pūtau mast.
3. Tauhohenga ki te maimoatanga: Ka heke ngā tohu ina hoatu he rongoā e aukati ana i te mahi a ngā pūtau mast, pērā i ngā rongoā antihistamine.
Mena ka tutukihia ēnei paearu e toru, ka whakapae pea te tākuta he MCAS. I ētahi wā ka haere tahi te MCAS me tētahi āhuatanga e kiia nei ko te "(POTS)" - te Postural Orthostatic Tachycardia Syndrome. Koinei te wā ka piki haere te tere o te manawa i te tū.
Me pēhea te rongoā?
Kāore anō kia kitea he rongoā mō te MCAS. Heoi anō, ka taea te whakahaere pai i ngā tohumate, ā, ka taea te whakatutuki i te oranga noa. E rua ngā whāinga matua o te maimoatanga.
1. Te karo i ngā mea e whakaoho ana i ō tohumate: Ko te mea nui ko te kimi i ngā mea e whakaoho ana i ō tohumate, me te karo i aua mea.
2. Te whakahaere i ngā tohumate mā te rongoā: Ka tohua e te tākuta he maha ngā rongoā māu.
- Ngā rongoā antihistamine H1 me H2: Ngā rongoā pēnei i a Cetirizine, Loratadine, Famotidine.
- Ngā Whakaū Pūtau Mast: Ngā rongoā e aukati ana i te tukunga o ngā matū mai i ngā pūtau mast.
- Ngā aukati Leukotriene: Ngā rongoā pēnei i te Montelukast.
- Mō ngā āhuatanga ohorere: Mena he tūponotanga ka pāngia koe e te anaphylaxis, ka kī ngā tākuta kia noho tata tonu he werohanga-ā-roto (pēnei i te EpiPen) kei roto te '(epinephrine)'.
Ngā mea hei whakaaroaro māu ina noho tahi me te MCAS
He uaua te noho tahi me te MCAS, engari mā te whakahaere tika , ka taea e koe te noho angitu me te mate.
- Kai: Ka taea e ētahi kai te whakaoho i te MCAS. Kia tino tupato ki ngā kai he nui te histamine (tīhi whakapūkara, ika kēne, tōmato, pīnihi, tiakarete). He pai ake te kōrero ki tō tākuta me te kite i tētahi tohunga kai hei whakawhanake i tētahi mahere kai e tika ana māu.
- Te whakahaere i te ahotea: Ko te ahotea te take nui o te MCAS. Nō reira, he mea nui kia noho marino tō hinengaro. Ka taea e ngā mahi pēnei i te whakaaroaro, te yoga, me te whai wāhi ki tētahi mahi whakangahau tino pai te āwhina.
- Rapua he tautoko: Kōrero ki te whānau me ngā hoa mō tō āhua. He mea āwhina anō hoki te whakauru atu ki ngā rōpū tautoko me te hunga e pāngia ana e ngā āhuatanga ōrite.
- Te kōrero auau ki tō tākuta: Kōrerohia ki tō tākuta i ia wā, i ia wā, ka whakarerekē i tō mahere maimoatanga ina hiahiatia.
Karere Tangohia ki te Kāinga
- Ehara te Mast Cell Activation Syndrome (MCAS) i te moemoeā noa, engari he āhuatanga tūturu e pā ana ki te pūnaha ārai mate.
- Ka rerekē rawa ngā tohu i ia tangata, i ia tangata. Mēnā he maha ngā tohu kāore e kitea te pūtake, me toro atu ki te tākuta.
- He wāhanga nui o te maimoatanga te tautuhi me te karo i ngā mea e whakaoho ana i ō tohu.
- He āhuatanga ohorere e morearea ana te anaphylaxis, e hiahia ana kia rongoatia tonutia. Kia tūpato ki ōna tohu.
- Mā te maimoatanga tika me ngā huringa momo noho, ka taea te whakahaere pai i te MCAS, ā, ka taea e koe te noho i tētahi oranga noa, hihiko hoki. Mahi tahi me tō tākuta ki te mahi i tēnei.











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