Kodi mukudziwa za Hemophilia C? Tiyeni tikambirane za vutoli losowa!

Nthawi zina ngakhale kudula pang'ono kumatenga nthawi kuti magazi asiye kutuluka, sichoncho? Kapena mwamvapo kuti winawake m'banja mwanu ali ndi matenda okhudzana ndi magazi? Lero tikambirana za matenda a magazi omwe ndi osowa pang'ono, koma ndikofunikira kwambiri kudziwa za matendawa. Amatchedwa Hemophilia C.

Kodi Hemophilia C ndi chiyani?

Mwachidule, hemophilia C ndi mtundu wosowa kwambiri wa hemophilia. Hemophilia ndi vuto lomwe magazi anu satseka bwino, zomwe zikutanthauza kuti mukatuluka magazi, amasiya pang'onopang'ono kapena sasiya. Anthu omwe ali ndi hemophilia C ali ndi mapuloteni apadera a m'magazi otchedwa clotting factor , otchedwa Factor XI , omwe amathandiza magazi kuundana. Izi zimatchedwanso Factor XI Deficiency ndipo nthawi zina zimatchedwa Rosenthal syndrome .

Komabe, zizindikiro za hemophilia C nthawi zambiri zimakhala zochepa kuposa za mitundu ina ya hemophilia (A ndi B). Komabe, anthu omwe ali ndi hemophilia C amatha kutuluka magazi ambiri kuposa masiku onse panthawi ya opaleshoni kapena opaleshoni ya mano. Madokotala amachizira izi ndi plasma yatsopano yozizira, yomwe imapangidwa kuchokera ku magazi operekedwa. Plasma iyi imathandiza magazi kuundana.

Kodi hemophilia C ndi matenda ofala?

Ayi, kwenikweni izi ndi vuto losowa kwambiri . Tangoganizirani, m'dziko ngati America, pafupifupi munthu m'modzi mwa amuna ndi akazi 100,000 aliwonse amakhala ndi hemophilia C. Tikayerekeza ndi mitundu ina ya hemophilia, hemophilia A imakhudza pafupifupi amuna 12 mwa amuna 100,000 aliwonse, ndipo hemophilia B imakhudza pafupifupi amuna 4 mwa amuna 100,000 aliwonse. Ofufuza sakudziwabe kuti hemophilia A kapena B imakhudza akazi kangati.

Kodi pali kusiyana kotani pakati pa hemophilia A, B, ndi C?

Mitundu yonse itatu ya hemophilia ndi matenda obadwa nawo m'magazi . Izi zikutanthauza kuti, kusintha kwa majini kumakhudza njira yolumikizirana magazi. Koma pali kusiyana pang'ono pakati pa mitundu itatuyi. Tiyeni tiwone zomwe zili:

• Hemophilia A ndi Hemophilia B zimachitika munthu akalandira jini yosinthika kuchokera kwa m'modzi mwa makolo ake enieni. Komabe, mu hemophilia C, jini yolakwika imatha kulandira kuchokera kwa makolo onse awiri .
• Mosiyana ndi anthu omwe ali ndi hemophilia A kapena B, anthu omwe ali ndi hemophilia C nthawi zambiri samakhala ndi vuto la kutuluka magazi lomwe limakhudza mafupa kapena minofu . Ichi ndi kusiyana kwakukulu.
• Kawirikawiri, zizindikiro za anthu omwe ali ndi hemophilia A kapena B zimatsimikiziridwa ndi kuchuluka kwa mapuloteni oundana, kapena 'zinthu zoundana', m'magazi awo. Mwachitsanzo, munthu amene ali ndi hemophilia A yoopsa amakhala ndi kuchuluka kochepa kwa chinthu chimenecho. Koma modabwitsa, munthu amene ali ndi hemophilia C akhoza kukhala ndi kuchuluka kochepa kwa chinthu chimenecho, koma zizindikiro zake zingakhale zochepa kwambiri .
• Matenda a Hemophilia A ndi B amatha kupezeka mwa anthu amitundu yonse ndi mafuko onse. Komabe, matenda a hemophilia C amapezeka kwambiri mwa anthu a fuko la Ashkenazi Jewish . Izi sizikutanthauza kuti palibe wina amene angawapeze, koma amapezeka kwambiri pakati pawo.
• Matenda a Hemophilia A ndi B amapezeka kwambiri mwa amuna kuposa akazi, koma matenda a hemophilia C amakhudza amuna ndi akazi mofanana .

Kodi zizindikiro za hemophilia C ndi ziti?

Anthu omwe ali ndi hemophilia C amatha kutuluka magazi nthawi zonse komanso mosalekeza pambuyo pa opaleshoni yayikulu, kuvulala kwambiri, kapena kubereka. Komabe, satuluka magazi mwadzidzidzi , ndipo ndi pamene magazi amayamba kutuluka popanda chifukwa chomveka.

Anthu omwe ali ndi hemophilia C nthawi zambiri amatuluka magazi molakwika akachitidwa opaleshoni ya mano, kuchotsa mano, kapena kuchotsa tonsillectomy.

Zizindikiro zina zingaphatikizepo:

• Kutuluka magazi m'mphuno pafupipafupi.
• Mabala pathupi ngakhale kuchokera ku chinthu chaching'ono kwambiri.
• Magazi mu mkodzo .
• Kutuluka magazi ambiri mutadula.
• Mabala opweteka komanso otupa pambuyo pa opaleshoni.
• Kwa akazi, msambo ukhoza kukhala kwa masiku angapo, womwe ndi wautali kwambiri.

Kodi ndi zinthu ziti zomwe zimayambitsa hemophilia C?

Hemophilia C ndi matenda obadwa nawo m'magazi . Amayamba mukasowa mapuloteni m'magazi otchedwa Factor XI , chimodzi mwa zinthu 13 zomwe zimathandiza kuchepetsa kapena kuletsa kutuluka kwa magazi. Izi zimachitika chifukwa mulibe jini yoyenera ya F11 .

Kawirikawiri, jini ya F11 iyi imakhala ndi malangizo opangira Factor XI. Ngati jini iyi yasintha, ndiko kuti, ngati yasanduka yachilendo, hemophilia C imayamba. Jini yachilendo iyi singapange Factor XI yokwanira, kapena singapange konse.

Amuna ndi akazi onse amalandira hemophilia C pokhapokha ngati makolo onse awiri apereka jini yosinthika kwa mwana wawo . Ngati wina alandira jini imodzi yachibadwa ya F11 ndi jini imodzi yosadziwika bwino, munthu ameneyo ndiye amene amanyamula hemophilia C, koma sasonyeza zizindikiro.

Tsopano, onani zomwe zingachitike makolo omwe ali ndi jini losazolowerekali akabereka ana:

• Ana obadwa kwa makolo omwe ali ndi kusintha kwa majini a F11 ali ndi mwayi wa 25% wokhala ndi hemophilia C.
• Ana obadwa kwa makolo amenewo ali ndi mwayi wa 50% wokhala ndi matendawa, zomwe zikutanthauza kuti amanyamula jini yokha popanda matendawa.
• Ana a makolo amenewo ali ndi mwayi wa 25% wolandira jini yachibadwa ya F11.

Kodi madokotala amazindikira bwanji hemophilia C?

Kodi mukudziwa momwe madokotala amadziwira matenda a hemophilia C? Adzakuyezani kaye mwakuthupi . Kenako adzakufunsani za zizindikiro zanu, monga kutuluka magazi m'mphuno kapena kutuluka magazi mutatha kuchita opaleshoni ya mano. Adzakufunsaninso za mbiri ya banja lanu komanso ngati pali aliyense m'banja mwanu amene ali ndi matenda a hemophilia kapena matenda ena a magazi . Izi ndizofunikira kwambiri pozindikira matendawa.

Kodi mayeso akuluakulu omwe amagwiritsidwa ntchito kutsimikizira matendawa ndi ati?

Dokotala wanu adzagwiritsa ntchito mayeso awiri akuluakulu kuti atsimikizire kuti mwapezeka ndi matendawa:

• Mayeso a nthawi yoyeserera magazi (APTT): Iyi ndi mayeso omwe amagwiritsidwa ntchito pozindikira hemophilia. Amathandiza dokotala wanu kudziwa nthawi yomwe magazi anu amaundana .
• Kuyesa magazi kofanana ndi magazi: Kuyesa magazi kumeneku kumasonyeza mtundu wa hemophilia ndi kuopsa kwake .

Nthawi zina, dokotala wanu angakufunseni kuti muyesedwe ndi mayeso ena:

• Kuchuluka kwa magazi (CBC): Kuyeza kumeneku kumayesa ndi kuphunzira maselo a magazi.
• Kuyesa kwa Prothrombin (PT): Izi zimayang'ananso momwe magazi anu amaundana mofulumira.
• Kuyeza kwa Fibrinogen: Kuyeza magazi kumeneku kumayesa kuchuluka kwa mapuloteni a m'magazi otchedwa fibrinogen, omwe amathandiza magazi kuundana.

Ndikofunikira kudziwa kuti nthawi zina hemophilia C imakhala yovuta kuizindikira. Chifukwa chiyani? Zotsatira za mayeso a magazi, makamaka zotsatira za mayeso a clotting factor, sizingagwirizane ndi zizindikiro za wodwala. Mwachitsanzo, mayeso a clotting factor angasonyeze kuti mulingo wanu wa factor ndi wotsika kwambiri, koma mwina mulibe zizindikiro zilizonse. Komanso, mutha kukhala ndi zizindikiro za hemophilia C ngakhale mulingo wanu wa factor uli wabwinobwino. Chifukwa chake dokotala adzaganizira zonsezi ndikufika pamlingo woyenera.

Kodi hemophilia C imachiritsidwa bwanji?

Anthu omwe ali ndi hemophilia C sangafunike chithandizo mpaka atachitidwa opaleshoni kapena njira ina yachipatala. Ngati ndi kotheka, madokotala amagwiritsa ntchito 'plasma yozizira', yomwe imapangidwa kuchokera ku magazi operekedwa.ndi kuphatikiza mankhwala omwe amaletsa kufalikira kwa 'matenda oundana' omwe amaperekedwa ngati njira ina. Ngati akazi ali ndi msambo wochuluka kwambiri, womwe umatenga masiku angapo, madokotala amatha kupereka mapiritsi oletsa kubereka .

Kodi hemophilia C ingapewedwe?

Ayi, hemophilia C ndi matenda obadwa nawo m'magazi, kotero sangathe kupewedwa . Komabe, ngati inu kapena wina m'banja mwanu ali ndi vutoli, upangiri wa majini ungakuthandizeni kumvetsetsa chiopsezo chopatsira matendawa kwa mibadwo yamtsogolo.

Kodi munthu amene ali ndi hemophilia C angayembekezere chiyani?

Anthu ambiri omwe ali ndi hemophilia C amakhala ndi zizindikiro zochepa . Kawirikawiri sizimayambitsa mavuto aakulu azachipatala. Anthu ambiri sazindikira zizindikiro mpaka atakula, ndipo zizindikirozo nthawi zambiri zimakhala zochepa kwambiri.

Komabe, mungakhale ndi mavuto otuluka magazi mutachita opaleshoni kapena chithandizo cha mano. Ngati muli ndi hemophilia C, ndikofunikira kufunsa dokotala wanu za njira zilizonse zodzitetezera zomwe muyenera kutsatira . Mwachitsanzo, kudziwitsa dokotala wanu musanachite opaleshoni komanso kupewa mankhwala ena omwe amawonjezera kutuluka magazi (monga aspirin).

Pomaliza, zinthu zofunika zomwe muyenera kukumbukira

Chabwino, pali zinthu zingapo zomwe muyenera kukumbukira kuchokera pa zomwe takambirana:

• Hemophilia C ndi matenda osowa kwambiri m'magazi .
• Kawirikawiri, zizindikiro zake zimakhala zochepa kwambiri ndipo sizimayambitsa mavuto aakulu azaumoyo.
• Anthu ambiri amaonetsa zizindikiro akakula.
• Komabe, mutha kutuluka magazi ambiri kuposa ena panthawi ya opaleshoni kapena chithandizo cha mano , choncho ndikofunikira kudziwitsa dokotala wanu pazochitika zotere.
• Ngati mwapezeka ndi hemophilia C, musachite mantha. Lankhulani ndi dokotala wanu kuti mutsimikizire kuti mwamvetsa zomwe muyenera kudziwa komanso njira zodzitetezera zomwe muyenera kutsatira .

Kumbukirani, kumvetsetsa bwino matenda aliwonse ndiye njira yabwino kwambiri yothetsera vutoli! Simuli nokha, ndipo upangiri ndi chithandizo chamankhwala nthawi zonse zimapezeka kwa inu.

Hemophilia C, magazi kuundana, Factor XI, matenda a majini, kutuluka magazi, zizindikiro, chithandizo