Kodi mudamvapo za Medulloblastoma? Mwina ayi. Ndi mtundu wa khansa ya muubongo yomwe imapezeka kwambiri mwa ana aang'ono, makamaka omwe ali ndi zaka zosakwana 16. Koma musadandaule, tiyeni tifotokoze momveka bwino za izi. Chifukwa ndikofunikira kwambiri kudziwa za vutoli.
Kotero, medulloblastoma ndi chiyani?
Mwachidule, medulloblastoma ndi chotupa cha khansa chomwe chimayamba mu dongosolo lanu la mitsempha (CNS) , lomwe ndi ubongo wanu ndi msana wanu. Nthawi zambiri chimamera mu gawo la ubongo wanu lotchedwa cerebellum, lomwe lili kumbuyo kwa ubongo wanu. Kodi mukudziwa kuti ubongo waung'ono uwu umalamulira zinthu zambiri m'thupi lanu, monga kulinganiza bwino, kuyenda, ndi kusuntha manja ndi miyendo yanu?
Matendawa nthawi zambiri amakhudza ana ndi achinyamata osakwana zaka 16. Komabe, amathanso kuchitika kwa akuluakulu, ngakhale kuti nthawi zambiri sapezeka. Ngati amapezeka kwa akuluakulu, nthawi zambiri amapezeka pakati pa zaka 20 ndi 45.
Uwu ndi mtundu wa khansa wosowa kwambiri. Komabe, ndi mtundu wofala kwambiri wa khansa ya muubongo mwa ana . Nthawi zambiri amapezeka mwa ana azaka zapakati pa 5 ndi 9.
Matenda a Medulloblastoma amakula mofulumira ndipo amatha kufalikira kumadera ena a ubongo ndi msana kudzera mu madzi a m'mitsempha - madzi oyera omwe amazungulira ubongo wathu ndi msana.
Kodi zizindikiro za izi ndi ziti? Kodi mumazindikira bwanji?
Zizindikiro za Medulloblastoma zimatha kusiyana malinga ndi munthu. Zimatengera zinthu monga msinkhu wanu, kukula kwa chotupacho, komanso kukula kwake. Zizindikiro zina zingayambitsidwe ndi komwe chotupacho chili kapena kupanikizika kwakukulu mkati mwa chigaza. Ndibwino kusamala zinthu izi:
- Mutu wopweteka pafupipafupi: Izi zitha kukhala zosiyana ndi mutu wamba, ndipo zitha kukhala zoopsa kwambiri m'mawa.
- Kusanza ndi kusanza: Vutoli limatha kuoneka makamaka m'mawa.
- Mavuto a kusasinthasintha: Kusakhazikika poyenda, kulephera kuyima molunjika.
- Kuvuta kuyenda: Kulephera kuima bwino, kuvutika kukwera ndi kutsika masitepe.
- Chizungulire: Kumva ngati zinthu zikukuzungulira.
- Kusintha kwa masomphenya: Kusawoneka bwino mwadzidzidzi, kuona zinthu ziwiri.
- Kutopa: Kumva ngati sutopa ngakhale utagona tulo tochuluka bwanji.
- Kupweteka kwa msana: Nthawi zina, kupweteka kwa msana kungachitike ngati khansa yafalikira mpaka ku msana.
- Kulephera kulamulira mkodzo ndi ndowe:Ngakhale mutakhala kuti munali ndi ulamuliro wabwino kale, ngati mavuto ngati amenewa abuka mwadzidzidzi, muyenera kuda nkhawa. Pankhani ya ana aang'ono, kuchuluka kwa 'ngozi' kungachuluke.
Musaope medulloblastoma chifukwa chakuti muli ndi chimodzi kapena ziwiri mwa zizindikirozi. Komabe, ngati muli ndi zizindikiro zingapo motsatizana, makamaka kwa mwana wamng'ono, ndi bwino kupita kwa dokotala kuti akakupatseni upangiri.
N’chifukwa chiyani medulloblastoma imayamba? Kodi zimayambitsa chiyani?
Madokotala sakudziwabe chomwe chimayambitsa medulloblastoma. Komabe, zapezeka kuti matenda enaake a majini amatha kuwonjezera chiopsezo chotenga medulloblastoma. Izi zikutanthauza kuti kusintha kwina kwa majini komwe kumadutsa m'mibadwo kungayambitse vuto.
Nazi zina mwa matenda a majini omwe amawonjezera chiopsezo chotere:
- Kusintha kwa majini a BRCA1: Mwina mwamvapo za majini a BRCA1 ndi BRCA2. Mapuloteni omwe amapanga ndi omwe amachititsa kukonzanso DNA yathu ikawonongeka. Anthu omwe amalandira mitundu ina ya majini amenewa ali pachiwopsezo chachikulu chotenga mitundu yosiyanasiyana ya khansa.
- `Nevoid basal cell carcinoma syndrome (NBCCS): Iyi imatchedwanso `Gorlin syndrome.` Iyi ndi matenda obadwa nawo. Anthu omwe ali ndi vutoli ali pachiwopsezo chachikulu chotenga khansa ya pakhungu ya basal cell. Alinso ndi mwayi wa 5% wotenga medulloblastoma.
- Matenda a Turcot: Anthu omwe ali ndi vutoli akhoza kukhala ndi chotupa cha mitsempha yapakati, monga medulloblastoma kapena pituitary adenoma, pamodzi ndi khansa ya m'matumbo.
- Matenda a Li-Fraumeni: Anthu omwe ali ndi vutoli ali pachiwopsezo chachikulu chotenga matenda a sarcoma, khansa ya m'mawere, mitundu ina ya khansa ya muubongo (gliomas, choroid plexus carcinomas), khansa ya adrenal gland, ndi leukemia.
Matenda a majini awa ndi ovuta kwambiri. Ngati mukufuna kudziwa zambiri za izi, ndi bwino kulankhula ndi dokotala.
Kodi madokotala amazindikira bwanji izi?
Ngati inu kapena mwana wanu muli ndi zizindikiro zomwe zatchulidwa pamwambapa, dokotala wanu adzayamba wakuuzani za zizindikiro zanu ndikuwunikanso mbiri ya matenda a banja lanu. Kenako, ngati akukayikira kuti ali ndi medulloblastoma, adzayitanitsa mayeso angapo kuti atsimikizire matendawa.
Ndi mayeso ati omwe nthawi zambiri amachitidwa?
- Kuyezetsa ubongo: Pa izi, dokotala adzayang'ana kumva kwanu, kuwona kwanu, kugwirizana kwanu, ndi mphamvu zanu zogwira ntchito. Izi zingakupatseni lingaliro la gawo la ubongo lomwe lakhudzidwa.
- `Mayeso ojambula zithunzi`:Izi zikuphatikizapo MRI (Magnetic Resonance Imaging) kapena CT (Computed Tomography). Ma scan amenewa amatha kuona bwino ngati pali chotupa mkati mwa ubongo, kukula kwake, ndi komwe chili.
- Kufufuza za khansa: Nthawi zina, madokotala amafunika kutenga chitsanzo cha minofu ya chotupacho n’kuchitumiza kwa dokotala wa matenda, dokotala amene amadziŵa bwino kufufuza minofu. Kufufuza za khansa nthawi zambiri kumachitika ngati matendawa sangatsimikizidwe ndi ma scan okha.
- Kupopera kwa msana (Lumbar Puncture): Mu njirayi, dokotala wa opaleshoni amatenga chitsanzo cha madzi a m'mitsempha ya ubongo ndikuyang'ana maselo a khansa. Kuyesa kumeneku kumachitika chotupa chikachotsedwa kapena kuthamanga kwa magazi mkati mwa ubongo kwalamulidwa.
Kodi mankhwala a Medulloblastoma ndi ati?
Njira zochiritsira zimadalira zinthu zambiri, kuphatikizapo zaka zanu, thanzi lanu lonse, komanso kukula kwa chotupacho. Nthawi zambiri, chithandizo chachikulu cha medulloblastoma ndi opaleshoni yochotsa chotupacho. Izi zitha kutsatiridwa ndi chemotherapy, radiation therapy, kapena zonse ziwiri.
- `Opaleshoni`: Opaleshoni iyi imachitidwa ndi `Neurosurgeon`. Izi zitha kuchepetsa kuthamanga kwa magazi mkati mwa ubongo kapena kuchotsa chotupacho kwathunthu. Komabe, nthawi zina ngati chotupacho chili mkati mwa ubongo, m'malo ovuta, zimakhala zovuta kuchichotsa kwathunthu.
- Chithandizo cha radiation: Chithandizochi chimagwiritsidwa ntchito kuwononga maselo aliwonse a khansa omwe angakhalebe pambuyo pa opaleshoni. Nthawi zina chimaperekedwa pamodzi ndi chemotherapy.
- Chemotherapy: Chithandizochi chimaperekedwa ndi dokotala wa khansa. Mankhwalawa amatha kuperekedwa pambuyo pa opaleshoni, pambuyo pa chithandizo cha radiation, kapena pamodzi ndi chithandizo cha radiation. Nthawi zina, kuikidwa kwa maselo oyambira kungapangidwe pambuyo pa chemotherapy.
Kumbukirani, mankhwala onsewa amasankhidwa ndi gulu la madokotala, ndipo amakonzedwa mogwirizana ndi vuto lanu.
Zimatenga nthawi yayitali bwanji kuti munthu achire? (Nthawi Yochira)
Kutalika kwa chithandizo ndi nthawi yochira zimasiyana malinga ndi munthu. Ngati mwachitidwa opaleshoni ya ubongo, nthawi zambiri zimatenga milungu inayi mpaka isanu ndi itatu kuti muchire . Ngati mwalandira chithandizo cha chemotherapy kapena radiation, zingatenge milungu ingapo kapena miyezi ingapo. Zimatengera mtundu wa matendawa. Kuti mudziwe nthawi yeniyeni yomwe ingatenge kwa inu kapena mwana wanu, ndi bwino kulankhula ndi dokotala wanu.
Kodi ndiyenera kupita kwa dokotala liti?
Ngati inu kapena mwana wanu muli ndi zizindikiro zilizonse zomwe zatchulidwa pamwambapa (monga mutu, nseru, chisokonezo, kusintha kwa masomphenya), pitani kwa dokotala nthawi yomweyo . Komanso, ngati mukulandira kale chithandizo cha medulloblastoma, uzani dokotala wanu za zotsatirapo zilizonse zomwe mukukumana nazo. Zingathandize kuchepetsa zizindikiro zanu ndikuchepetsa kusasangalala kwanu.
Kodi munthu amene ali ndi medulloblastoma angayembekezere chiyani?
Pali gulu lalikulu la madokotala loti likuthandizeni pankhaniyi. Ena mwa iwo ndi awa:
- `Madokotala a khansa ya m'magazi`
- `Madokotala a opaleshoni ya mitsempha`
- `Akatswiri a matenda`
- `Madokotala a zamaganizo`
- 'Akatswiri a Radiyo'
- `Madokotala a khansa ya radiation`
- Anthu ngati `Neuropsychologists` angaphatikizidwe.
Pamodzi, amapanga dongosolo la chithandizo lomwe likugwirizana ndi zosowa zanu.
Kodi Medulloblastoma ingachiritsidwe?
Inde, nthawi zambiri. Ngakhale kuti medulloblastoma ndi matenda omwe amatha kufalikira m'mitsempha yonse, anthu ambiri amatha kuchiritsidwa. Makamaka ngati khansa sinafalikire kumadera ena a ubongo ndi msana, mwayi wopulumuka ndi waukulu.
Kodi chiyembekezo cha izi ndi chiyani?
Chiŵerengero cha anthu omwe ali ndi medulloblastoma omwe amapulumuka zaka zisanu ndi choposa 80% . Izi zikutanthauza kuti anthu opitilira 80% omwe amapezeka ndi medulloblastoma amakhalabe ndi moyo patatha zaka zisanu. Ziwerengerozi zimachokera ku zotsatira za anthu omwe adakhala ndi matendawa kale.
Koma kumbukirani kuti ziwerengerozi sizingakuuzeni zomwe zidzachitike ku vuto lanu. Kuti mudziwe bwino za vuto lanu komanso momwe mukuchira, ndi bwino kulankhula ndi dokotala wanu.
Kumva za chotupa cha muubongo kungakhale kovuta kwambiri mwakuthupi, m'maganizo, komanso m'maganizo. Makamaka ngati chikukhudza mwana wanu, chingakhale chovuta kwambiri. Komabe, pali mankhwala othandiza, kotero pali chiyembekezo . Funsani dokotala wanu za mankhwala atsopano, monga mayeso azachipatala. Komanso, lankhulani ndi dokotala wanu za zinthu ndi magulu othandizira omwe angakuthandizeni. Munthawi yovutayi, kungakhale gwero lalikulu la mphamvu ndi chitonthozo kukhala pafupi ndi anthu omwe adakumanapo ndi zinthu zomwezo ngati inu.
Mwachidule, zinthu zoti muzikumbukira
Chabwino, tiyeni tikukumbutseni zina mwa zinthu zofunika kwambiri zomwe takambirana zokhudza medulloblastoma:
- Medulloblastoma ndi khansa ya muubongo yomwe imapezeka kwambiri mwa ana., koma akuluakulu nawonso akhoza kukhala nayo.
- Dziwani zizindikiro monga mutu, kusanza, ndi kulephera kukhazikika.
- Ngakhale kuti chifukwa chenicheni sichikudziwika , matenda ena a majini angayambitse vutoli.
- Matendawa amapezeka kudzera mu mayeso monga MRI, CT scan, ndi biopsy.
- Pali njira zochizira monga opaleshoni, chemotherapy, ndi radiation therapy.
- Mwayi wochira ndi waukulu , makamaka ngati wapezeka ndi kuchiritsidwa msanga.
- Ngati muli ndi zizindikiro zilizonse , musaope kupita kwa dokotala .
Ndikukhulupirira kuti izi zikuthandizani. Kumbukirani, simuli nokha. Ngati muli ndi mafunso aliwonse, musazengereze kulankhula ndi dokotala.
👩🏽⚕️ Mafunso ena (Mafunso Ofunsidwa Kawirikawiri)
💬 Kodi Medulloblastoma ndi khansa yofala muubongo?
Ayi. Iyi ndi khansa yoopsa kwambiri komanso yomwe ikukula mofulumira yomwe imapezeka kwambiri mwa ana kuposa akuluakulu (20% ya khansa zonse za ubongo zomwe zimachitika ana). Imakula m'mbali ya ubongo yotchedwa cerebellum, yomwe ili kumbuyo kwa ubongo ndipo imayang'anira bwino thanzi lathu.
💬 Kodi makolo amadziwa bwanji ngati mwana wawo ali ndi vutoli?
Popeza chotupachi chimakula pansi pa ubongo, chimatseka machubu omwe amanyamula madzi a m'mitsempha ya ubongo (CSF) mkati mwa ubongo. Kenako ubongo umadzaza ndi madzi ndikupanga kupanikizika kwambiri (Hydrocephalus). Chifukwa chake, ngati mwana akusanza kwambiri akadzuka m'mawa (ngati akunena kuti mutu wake umapweteka m'mawa), ngati wagwa osakhazikika akuyenda, ndipo ngati maso ake agwa mwadzidzidzi (Maso opingasa / chifukwa cha kupanikizika kwa mitsempha ya ubongo), ndiye kuti MRI scan ya ubongo iyenera kuchitidwa nthawi yomweyo.
💬 Kodi wodwala uyu sangapulumutsidwe pomuchita opaleshoni?
Ngati yapezeka msanga, imatha kuchiritsidwa! Gawo loyamba ndikuchita opaleshoni kuti achotse chotupacho momwe angathere. Kenako, nthawi zambiri amapatsidwa radiation ndi chemotherapy ku ubongo wonse ndi msana (craniospinal radiation) kuti aphe maselo otsala a khansa (makamaka popeza izi zimatha kufalikira ku msana).
Medulloblastoma , khansa ya muubongo, khansa ya ubwana, dongosolo lamanjenje, zizindikiro za khansa, chithandizo cha khansa, matenda a majini











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