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Ese wigeze wumva aplasia? Reka tubiganireho!

Ese wigeze wumva aplasia? Reka tubiganireho!

Ese wigeze wumva ikibazo aho ibice bimwe na bimwe by'umubiri wacu, nk'ingingo n'ingingo, bidakura neza cyangwa ngo bikure neza burundu? Ibi nibyo abaganga bita aplasia . Ushobora kumva ufite ubwoba gato iyo wumvise iri zina. Ariko ntugahangayike, tuzabivugaho mu buryo bworoshye kandi busobanutse. Hanyuma ushobora gusobanukirwa neza ibi.

Mu by'ukuri (Aplasia) ni iki?

Mu magambo make, aplasia ni indwara aho igice cy'umubiri wawe, cyaba ari ingingo, urugingo, cyangwa ikindi gice cy'umubiri wawe, kidakura cyangwa ngo gikora neza. Akenshi, izi ndwara ziba mbere cyangwa mbere yo kuvuka, mu gihe umwana akiri mu nda. Hari igihe, iyo muganga asuzumye umwana uri mu nda cyangwa umwana uvutse, ashobora kubona ko igice, nk'ukuboko cyangwa ukuguru, kibuze cyangwa kitararemwa neza. Ariko, zimwe mu ndwara za aplasia, cyane cyane izifata ingingo z'imbere nk'umusemburo w'amagufwa, zishobora gupimwa mu bwana cyangwa no mu gihe cy'ubukure.

Igikuru ni uko aplasia atari indwara imwe. Ni ijambo rikoreshwa n'abaganga mu gusobanura indwara iyo ari yo yose aho igice cy'umubiri kiba kitararemwa neza.

Ni gute (Aplasia) itandukanye na (Agenesis), (Hypoplasia), na (Dysplasia)?

Aya magambo ashobora kugorana kumva, kuko asobanura ikintu kimwe. Ariko hari itandukaniro rito. Reka turebe ayo ari yo.

  • (Agenesis): Iki ni igihe igice cy'umubiri kinanirwa gukura na gato . Mu magambo amwe n'amwe y'ubuvuzi, (Aplasia) bivuze ko hari imiterere y'ibanze y'ingingo idakuze neza. Ariko muri (Agenesis), nta gice cy'urwo rugingo cyavutse. Urugero, iyo impyiko idakuze na gato, yitwa (Agenesis y'impyiko).
  • Hypoplasia: Ibi bibaho iyo igice cy'umubiri kidakuze neza . Ni ukuvuga ko kiba gihari ariko kikaba gito cyangwa kituzuye. Hari igihe aplasia ifatwa nk'ikibazo kiri hagati yo kubura (agenesis) na hypoplasia (kubura iterambere).
  • Dysplasia: Iyi ni ikura ridasanzwe ry’urugingo cyangwa igice cy’umubiri. Bitandukanye na aplasia, dysplasia ntihora iterwa n’ikibazo cy’imikurire ikiri kare (ni ukuvuga igice gitangira gukura hanyuma kigahagarara). Dysplasia ubusanzwe ni ikura ridasanzwe ry’uturemangingo cyangwa ingingo. Urugero, mu ntangiriro za kanseri, impinduka zidasanzwe mu turemangingo (`dysplasia`) zibaho, nyuma zikaza guhinduka kanseri.

Niba utazi neza aya magambo, banza ubaze muganga wawe kugira ngo ayasobanure . Ibi bizagufasha gusobanukirwa neza indwara wowe cyangwa umwana wawe mushobora kuba mufite.

Ni ubuhe bwoko bw'ingenzi bwa aplasia?

Ubwoko bwose bwa aplasia si bwo busanzwe. Ariko, hari ubwoko buke bwa aplasia twumva kenshi, cyangwa buzwi cyane. Ubu bwoko bugizwe n'uturemangingo dutukura tw'amaraso, uruhu, amagufwa, n'uturemangingo tw'imiti (ni ukuvuga intanga n'amagi). Aplasia ishobora no kugira ingaruka ku zindi ngingo, nk'ibihaha n'imitsi y'amaso.

Reka tuvuge kuri Pure Red Cell Aplasia (PRCA)

Muri iki kibazo, uturemangingo tw’amaraso dutukura (`Red Blood Seliers`) ntidukura neza. Ubusanzwe, umwongo wacu (`Bone Marrow`) ukora uturemangingo dushya dutukura tw’amaraso hafi buri minsi 120. Muri iki gihe, uturemangingo dutukura tw’amaraso dukura kuva ku ntambwe ya mbere, ``Erythroblast``, tukavamo uturemangingo dutukura tw’amaraso twuzuye.

Iyo ufite PRCA , umwongo wawe ushobora gukora erythroblast nke cyane cyangwa ntugire n'imwe. Ibi bituma umubiri utakaza uturemangingo dutukura ukeneye, bigatera amaraso make. Ibi byitwa "pure" kuko bigira ingaruka gusa ku turemangingo dutukura tw'amaraso. Izindi selile z'amaraso - selile z'umweru n'udupira - zikorwa mu buryo busanzwe. Ariko, iyo ubwoko bwose butatu bw'uturemangingo tw'amaraso budakozwe neza, byitwa aplastic anemia .

PRCA ishobora kubaho igihe umuntu avutse (congenital PRCA), cyangwa ishobora no kubaho mu gihe cy'ubuzima bwe. Ubwoko bwa PRCA bwo mu muryango bwitwa Diamond-Blackfan Anemia .

Niki Aplasia Cutis Congenita?

Iki ni igihe uruhu rw'umwana wawe ukiri mu nda, cyane cyane umutwe, rudakura neza cyangwa rukabura burundu mu bice bimwe na bimwe. Hari igihe ingingo n'amagufwa biri munsi y'urwo ruhu bidakura neza. Uruhu rushobora kandi kubura mu bice bimwe na bimwe by'umubiri w'umwana, amaboko n'amaguru.

(Aplasia Cutis Congenita) ishobora kugaragara nk'inkovu ku mutwe, nta musatsi uri munsi. Cyangwa, uruhu rudakuze neza rushobora kugaragara nk'ururenda ruto rudafite umusatsi.

Nk'uko izina ribigaragaza (`Congenita`), iyi ni indwara umuntu avukana, bivuze ko iba ihari kuva akivuka.

Reka twige kuri Radial Aplasia

Ibi bibaho iyo rimwe mu magufwa abiri ari mu kuboko kwawe, radius, rinaniwe gukura. Hari amagufwa abiri maremare mu kuboko kwawe, radius na ulna. Ulna iva mu nkokora yawe ijya mu kuboko kwawe, ku ruhande aho urutoki rwawe ruto ruri. Ulna iva mu nkokora yawe ijya mu kuboko kwawe, ku ruhande aho urutoki rwawe ruri. Umuntu ufite radius aplasia ashobora kuba afite ikiganza kidakora neza kandi kigoramye. Igikumwe gishobora kuba kibuze cyangwa kikaba kigufi kuruta ibisanzwe.

(Aplasia yo mu bwoko bwa Radial)Kubura imirasire ya radial ni ubwoko bw'indwara. Ni ikibazo mu mikurire y'igufwa rya radial. Kubura imirasire ya radial bishobora kuva ku byoroheje kugeza ku bikomeye. Hari igihe igufwa rya radial ribaho, ariko rikaba rigufi ugereranyije n'ibisanzwe. Hari n'igihe igufwa rya radius ritakura na gato.

Aplasia y'ingirabuzimafatizo cyangwa indwara ya Sertoli-Cell-Only Syndrome ni iki?

Iki ni igihe umuntu atakaza uturemangingo tw’ingirabuzimafatizo (`Uturemangingo tw’ingirabuzimafatizo`) mu mabya ye (`Testes`). Uturemangingo tw’ingirabuzimafatizo ni uturemangingo tw’imyororokere. Mu bagabo, uturemangingo tw’ingirabuzimafatizo ni two duhinduka intanga ngabo (`Intanga ngabo`). Iyo uturemangingo tw’ingirabuzimafatizo twabuze, intanga ngabo ntizishobora kuremwa. Ibi bivuze ko abantu bafite aplasia y’uturemangingo tw’ingirabuzimafatizo badashobora kubyara (`Ubugumba`).

Aplasia y'uturemangingo tw'ingirabuzimafatizo yitwa kandi Sertoli-Cell-Only Syndrome . Ibi biterwa nuko, nubwo uturemangingo tw'ingirabuzimafatizo tutaboneka, uturemangingo twa Sertoli tuba tukiri mu buryo bw'imyororokere. Ubusanzwe, uturemangingo twa Sertoli dufasha uturemangingo gukura tukavamo intanga. Ariko, iyo uturemangingo tw'ingirabuzimafatizo tubuze, uturemangingo twa Sertoli nta ruhare tugira mu ikorwa ry'intanga.

Reka turebe kandi Aplasia y'ibihaha.

Aplasia y'ibihaha ni indwara umuntu avukana ibihaha bidakuze neza. Iyi si indwara imwe, kandi ishobora kubaho mu buryo butandukanye. Ishobora kuva ku kubura imikurire y'ibihaha burundu (Pulmonary Agenesis) kugeza ku kubura imikurire y'ibihaha gato (Pulmonary Hypoplasia).

Aplasia y'ibihaha iri hagati ya Agenesis y'ibihaha na Pulmonary Hypoplasia. Muri Aplasia, imiterere y'ibihaha irakura, ariko ntishobora gukora akazi k'ibihaha bikora neza.

Akenshi, igihaha kimwe kiba kibuze cyangwa kidakora neza, mu gihe ikindi kiba gisanzwe.

Aplasia ya Thymic ni iki?

Thymus gland yawe ni imvubura ikora ubwoko bw'uturemangingo tw'amaraso tw'umweru twitwa T-seli. T-seli zifasha umubiri wawe kurwanya indwara zandura. Muri Thymic Aplasia , thymus gland yawe ntikura. Iyo uvutse udafite thymus gland, uba ufite amahirwe menshi yo kwandura indwara.

Kutagira thymus gland ni kimwe mu bimenyetso by'indwara yitwa DiGeorge Syndrome . DiGeorge Syndrome ishobora kugira ingaruka ku mikorere y'umubiri myinshi. Ishobora kugira ingaruka ku budahangarwa bw'umubiri wawe n'imikorere y'umutima, ndetse ishobora no gutera gutinda mu mikurire y'umwana.

Tumenye kandi Aplasia y'imitsi y'amatwi.

(Aplasia y'imitsi y'amaso)Ni ukubura ibice by'ingenzi by'ijisho rimwe cyangwa byombi, harimo n'umutsi w'amaso, igihe uvuka. Umutsi w'amaso ugira uruhare runini mu kureba kwawe. Ni wo utuma amaso yawe avugana n'ubwonko bwawe kandi agatunganya amakuru y'amaso. Kubera umutsi w'amaso, iyo amaso yawe abona ibintu nk'imiterere n'amabara, ubwonko bwawe bushobora guhindura ayo makuru mo ishusho igaragara bushobora gusobanukirwa.

Aplasia y'imitsi y'amaso ishobora gutera ibibazo bitandukanye by'amaso, bitewe n'uburemere bw'indwara yawe. Aplasia, indwara ifata amaso yombi, ishobora no gutera ibibazo mu mikurire y'ubwonko.

Aplasia ikunze kugaragara gute?

Aplasia ni indwara idakunze kugaragara cyane . Ubwoko bukunze kugaragara cyane ni `(Radial Aplasia)` n'ubwoko bwa ``Pure Red Cell Aplasia`` (PRCA). `(Radial Aplasia)` yibasira umwana umwe mu bana 30.000 bavutse. `(Radial Ray Deficiencies)` (harimo kandi `(Radial Aplasia)`) ni indwara ikunze kugaragara cyane mu kuboko. Ubwoko bwa congenital (PRCA) nabwo ni gake cyane, aho hagaragara ko hari abantu 5 kugeza kuri 7 kuri miliyoni bavuka. Ubwoko bwa congenital bukunze kugaragara gato, ariko ntabwo tuzi neza umubare w'abantu bavuka.

Ni izihe mpamvu zitera aplasia?

Ubwoko bwinshi bwa aplasia buterwa n'impinduka mu ngirabuzimafatizo, zikomoka ku babyeyi. Ingirabuzimafatizo zawe zikubiyemo amabwiriza agena imiterere y'umubiri wawe. Urugero, aya mabwiriza agena aho n'uburyo urugingo ruzakura. Ubona ingirabuzimafatizo ziturutse kuri nyoko wawe na so. Iyo ingirabuzimafatizo ifite impinduka, cyangwa inenge, ushobora kugira ibibazo nka aplasia.

Ni gake cyane, aplasia ishobora kugaragara uko igihe kigenda gihita. Urugero, PRCA iterwa n'izindi mpamvu n'ibindi bibazo, harimo indwara zandura, indwara ziterwa n'ubudahangarwa bw'umubiri, na kanseri imwe n'imwe.

Hari ubwo abaganga n'abahanga mu bya siyansi badashobora kubona icyateye aplasia. Ubwo bwoko bwa aplasia bwitwa idiopathic .

Ni gute wamenya (Aplasia)?

Amwe mu moko ya aplasia ashobora kumenyekana mu gihe utwite binyuze mu bipimo, nko gupimwa na ultrasound. Andi moko ya aplasia ntabwo agaragara inyuma kandi agaragara gusa mu gihe cyo kuvuka.

Iyo indwara idakomeye cyane, cyangwa niba ijyanye n'amaraso n'umusemburo w'amagufwa, ibimenyetso bishobora kutagaragara kugeza mu gihe cy'ubuzima. Bitewe n'ubwoko bwa aplasia, ushobora gukenera gukorerwa isuzuma ritandukanye, gupimwa amaraso, no gupimwa imiterere y'uturemangingo kugira ngo umenye indwara yawe.

Ni ubuhe buryo bwo kuvura (Aplasia)?

Uburyo bwo kuvura buratandukanye bitewe n'uburwayi bwawe. Kubagwa bishobora gukorwa kugira ngo imikorere y'ukuboko cyangwa ukuboko kudakomeye neza irusheho kuba myiza. Mu bihe bikomeye bya PRCA, guterwa amaraso bishobora kuba ngombwa. Bitewe n'uburwayi bwawe, imiti ishobora gutangwa kugira ngo igenzure ibimenyetso cyangwa ikumire ingorane ziterwa no kubura amaraso.

Hari ubwoko bumwe na bumwe bwa aplasia, nka aplasia y'uturemangingo tw'imiti, ntibushobora kuvurwa.

Ese aplasia ishobora kuvurwa?

Kuba indwara yawe izamera neza cyangwa itamera neza biterwa n'ubwoko bwa aplasia ufite n'impamvu zabiteye. Urugero, aplasia y'uturemangingo dutukura (PRCA) ishobora gukira, bitewe n'ikintu kibuza umubiri wawe gukora uturemangingo dutukura. Kuvura indwara itera kubuza ikorwa ry'uturemangingo dutukura rimwe na rimwe bishobora kunoza aplasia.

Aplasia ni indwara umuntu avukana idashobora gusubizwa inyuma, bivuze ko idashobora gukira burundu. Muri ibyo bihe, muganga ashobora kukugira inama yo kubagwa, imiti, cyangwa uburyo bwihariye bwo kuvura. Ibi bishobora gufasha kunoza imikorere y'ukuboko, ukuguru, cyangwa ku kuguru, cyangwa kugenzura ibimenyetso.

Ijambo "(Aplasia)" rishobora gusobanura ibintu byinshi bitandukanye. Biterwa n'ibintu byinshi, harimo igice cy'umubiri gitera ingaruka, ibimenyetso byawe, n'uburyo indwara yoroheje cyangwa ikomeye. Ntukibagirwe n'aya magambo. Niba wowe cyangwa umwana wawe mufite ikibazo nk'iki "(Aplasia)," "(Agenesis)," cyangwa ikindi gisa nacyo, baza muganga wawe icyo ayo magambo asobanura n'icyo wakwitega uko igihe kigenda gihita. Baza niba hari uburyo bwo kuvura buhari kandi niba bukenewe. Niba ari uko bimeze, ganira ku bwoko bw'ubuvuzi bushobora gufasha. Baza uburyo ibi bibazo by'iterambere bigira ingaruka (cyangwa bitagira ingaruka) ku buzima bwawe bwa buri munsi.

Ibintu by'ingenzi tugomba kwibuka

Sawa, rero, ndizera ko ufite igitekerezo ukurikije ibyo twavuzeho (Aplasia). Muri make:

  • Aplasia bivuze ko igice cy'umubiri kitarakura neza.
  • Iyi si indwara imwe, ishobora kuza mu moko atandukanye no ku rwego rutandukanye .
  • Amwe mu moko ya aplasia avukana, mu gihe andi avukana mu gihe cy'ubuzima.
  • Impamvu ziratandukanye; impamvu zikomoka ku ngirabuzimafatizo, indwara zandura, izindi ndwara, kandi rimwe na rimwe nta mpamvu iboneka.
  • Uburyo bwo kuvura buterwa n'ubwoko n'uburemere bwa aplasia. Bumwe bushobora gukenera kubagwa, imiti, cyangwa ubundi buryo bwihariye bwo kuvura kugira ngo ibimenyetso bigerweho kandi birusheho kunoza ubuzima.
  • Nubwo aplasia yo mu gihe cy'amavuko idashobora gukira burundu, iyo umuntu afashwe neza kandi agahabwa ubufasha, birashoboka kubaho ubuzima busanzwe.
  • Igikuru ni ukubonana na muganga no kubona inama n'amakuru akwiye niba wowe cyangwa umwana wawe mufite amakenga kuri iyi ndwara.Ntugatinye, ubaze ibibazo, kandi wumve neza uko ibintu bimeze.

Twizeye ko aya makuru wayabonye ari ingirakamaro!


Aplasia , Kudakura kw'ibice by'umubiri, Ubusembwa bw'ivuka, Aplasia y'uturemangingo dutukura, Aplasia Cutis Congenita, Aplasia yo mu bwoko bwa Radial, Aplasia y'uturemangingo tw'ingirabuzimafatizo

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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