Ese uruhu rwawe ruriyongera kandi rugakomera? Reka twige kuri Scleroderma!

Ese hari igihe wumva uruhu rwawe rukuze kandi rukonje kurusha uko bisanzwe? Cyangwa ufite ububabare bw'ingingo cyangwa ubukomere bwa mu gitondo? Ibi ni ibintu dushobora kutitaho cyane. Ariko, bishobora no kuba ibimenyetso by'indwara idakunze kugaragara yitwa Scleroderma . Reka tubiganireho birambuye uyu munsi, si byo se?

Scleroderma ni iki?

Muri make, Scleroderma ni indwara idakunze kugaragara aho ingingo z'umubiri wawe ziba nini kandi zikomeye kurusha uko bisanzwe. Akenshi, zigira ingaruka ku ruhu. Ariko rimwe na rimwe, iyo ndwara ishobora kugira ingaruka ku zindi ngingo z'umubiri.

Mu by’ukuri iyi ni indwara y’ubwiyongere bw’umubiri . Noneho ushobora kwibaza icyo 'indwara y’ubwiyongere bw’umubiri' ari cyo. Umubiri wacu ufite sisitemu isa n’ingabo iturinda indwara, yitwa sisitemu y’ubudahangarwa bw’umubiri. Ariko muri iki gihe, iyo sisitemu igenda nabi, kandi aho kurwanya mikorobe z’amahanga, itangira kwibasira uturemangingo twacu twiza. Ni nk’aho tudashobora kumenya uwacu n’uwacu. Ndetse n’abaganga ntibarabasha kumenya neza impamvu ibi bibaho.

Iyo urwaye scleroderma, ubudahangarwa bw'umubiri bwawe butuma uturemangingo tw'umubiri wawe dukora poroteyine nyinshi yitwa kolajeni . Mu by'ukuri, umubiri wacu ukeneye kolajeni. Ni yo ituma uturemangingo dufite imbaraga kandi dufite ubuzima bwiza dushyigikira ingingo zacu. Ariko iyo twiyongereye cyane, uruhu n'izindi ngingo birakomera kandi bikagira uturemangingo twinshi kuruta uko bisanzwe.

Scleroderma ni indwara idakira . Ibi bivuze ko ushobora kuba ugifite ibi bimenyetso igihe kirekire, wenda ubuzima bwawe bwose. Nanone, iyo bigira ingaruka ku ngingo z'imbere mu mubiri wawe, bishobora guteza ingorane zishobora gushyira ubuzima bwawe mu kaga. Niba wumva umeze nk'ufite indwara y'umutima, ugorwa no guhumeka, cyangwa ugorwa no kumira, hamagara 911 (cyangwa nimero y'ubutabazi bw'ibanze yo mu gace utuyemo) ako kanya, cyangwa ujye mu cyumba cy'ubutabazi bw'ibanze cy'ibitaro.

Niba ufite ububabare cyangwa ubukomere mu ngingo zawe, cyane cyane hafi y'intoki n'amano, ugomba kujya kwa muganga.

Ni ubuhe bwoko bw'ingenzi bwa Scleroderma?

Abaganga bagabanya scleroderma mu moko abiri y'ingenzi:

1. Scleroderma yo mu gace: 'Localized' bivuze ko ifungiranye mu gace kamwe. Ubu bwoko bw'indwara bufata igice kimwe cy'umubiri gusa (akenshi uruhu). Butera uduce duto cyangwa imirongo y'uruhu rwabyimbye kandi rumeze nk'ibishishwa. Ikintu cyiza ni uko scleroderma yo mu gace runaka ishobora kwiyakira ubwayo . Nanone ntabwo ikwirakwira mu bindi bice by'umubiri.

2.Sclerosis yo mu bwoko bwa Systemic: Ubu bwoko bushobora kugira ingaruka ku zindi ngingo uretse uruhu. Bushobora kugira ingaruka ku buryo bw'ubuhumekero bwawe (urugingo rugufasha guhumeka no guhumurirwa) no ku buryo bw'igogora (urugingo ruhindura ibiryo turya imbaraga). Iyo sclerosis igize ingaruka ku bushobozi bwawe bwo guhumeka cyangwa kwinjiza intungamubiri, uba ufite amahirwe menshi yo kugira ingorane zikomeye. Ishobora no kwica. Sclerosis yo mu bwoko bwa Systemic ifite ubwoko butatu bw'indwara - ikwirakwira, igabanya, na sine sclerosis.

Indwara ya Sclerosis ikwirakwira cyane

'Diffuse' bivuze 'gukwirakwira'. Muri iki kibazo, indwara ya diffuse sclerosis ibaho mu buryo butunguranye ku bice binini by'umubiri. Urugero:

• Igituza
• Inda
• Ibibero
• Amaboko
• Amaguru
• Isura

Nanone, ishobora kugira ingaruka ku ngingo nyinshi icyarimwe. Ibyo bivuze:

• Uduce tw’igogora (Uduce tw’igogora - GI)
• Impyiko
• Umutima
• Ibihaha

Sclerosis ifite ingano nto (syndrome ya CREST)

Abaganga bakunze kwita Limited Scleroderma syndrome CREST . Buri nyuguti muri CREST isobanura ikimenyetso giterwa nayo:

• C - Calcinosis: Kugabanuka kwa kalisiyumu mu ruhu. Bishobora kugaragara nk'uduheri duto tw'umweru ku ruhu.
• R - Indwara ya Raynaud: Guhinduka ibara no kubura ibinure by'intoki n'amano. Bishobora guhinduka ibara ry'umukara, ubururu, cyangwa umutuku iyo bihuye n'ubukonje.
• E - Kudakora neza k'umuyoboro w'amaraso: Kugorwa no kumira no gusubira inyuma kw'aside.
• S - Sclerodactyly: Gukomera k'uruhu ku ntoki, bigatuma bigorana kunama no kugorora intoki.
• T - Telangiectasias: Uduce duto, dutukura cyangwa twahinduye ibara ku ruhu. Ibi bishobora kumera nk'udusimba tw'igitagangurirwa.

Sine Sclerosis

Ku bijyanye na Sine Sclerosis, ibimenyetso bya Limited Sclerosis byavuzwe haruguru birabaho, ariko uruhu ntirwangirika . Ni ukuvuga ko ushobora kugira bimwe mu bimenyetso byavuzwe muri CREST syndrome, ariko nta bubyimba bw'uruhu bugaragara.

Scleroderma ikunze kugaragara gute?

Scleroderma ni indwara idakunze kugaragara cyane.Impuguke zivuga ko abantu bagera kuri 250 kuri miliyoni muri Leta Zunze Ubumwe za Amerika bafite ubwoko butatu bwa scleroderma. Muri bo, abantu bagera ku 100.000 bafite scleroderma.

Ni ibihe bimenyetso bya Scleroderma?

Bamwe mu bantu barwaye scleroderma bashobora kutagira ibimenyetso mu ntangiriro. Ariko, kuri benshi, ikimenyetso nyamukuru ni ukugaragara kw'uduce twabyimbye, tumeze nk'ibishishwa cyangwa imirongo ku ruhu. Byongeye kandi, hari n'ibindi bimenyetso byinshi bikunze kugaragara:

• Ububabare bw'ingingo
• Kubabara cyane , cyane cyane iyo ukangutse mu gitondo
• Umunaniro (kumva unaniwe cyane igihe cyose)
• Kugabanya ibiro mu buryo budasanzwe

Ibindi bimenyetso ubona (n'aho bikugizeho ingaruka) biterwa n'ubwoko bwa scleroderma ufite.

Ibimenyetso bya Scleroderma yo mu gace runaka

Abantu barwaye scleroderma yo mu gace runaka bakunze kugira uruhu rubyimbye gusa . Ubu bubyimbirwe bushobora kuba ahantu hamwe cyangwa bugashobora kubaho mu duce duto. Bushobora kugira ingaruka ku bice bikurikira by'uruhu:

• Igituza
• Inda (agace gakikije igifu)
• Amaboko n'amaguru (Amaboko n'amaguru yawe)
• Amaboko n'intoki
• Ibirenge n'amano

Ariko, scleroderma yo mu gace runaka, ifata ingingo z'imbere, ni gake cyane .

Ibimenyetso bya Sclerosis yo mu mubiri

Indwara ya “systemic sclerosis” ishobora gutera ibimenyetso bitandukanye. Ibi kandi bituma uruhu rukomera, ariko akenshi ahantu hanini no mu duce duto. Cyane cyane mu maso no mu biganza. Uruhu runini rushobora gutangirira ku ntoki no ku mano hanyuma rugakwirakwira mu mubiri wose. Niba ufite indwara ya Raynaud , intoki n'amano ku rugingo rwafashwe bishobora guhindura ibara iyo bihuye n'ubukonje (ubusanzwe umweru, umutuku, cyangwa ibara ry'ubururu bw'umuhengeri).

Sclerosis y’umubiri ishobora kandi gutera ibimenyetso mu zindi ngingo n’ingingo zawe. Urugero:

• Imitsi: Kubura ibinya no kubyimba, cyane cyane mu biganza no mu birenge (ku mpera z'amaguru).
• Ingingo: Kugongana, kubyimba, no kubura uburyo bwo kugenda.
• Ibihaha: Inkorora no kugorwa no guhumeka (kubura umwuka).
• Igogora: Kubabara mu nda, kuribwa mu gifu, kubyimba inda, kuribwa mu nda no gucibwamo.
• Umutima:Umutima utari umeze neza (arrhythmia), amazi yirundanya hirya no hino mu mutima (pericardial effusion), no kwiyongera kw'imitsi y'umutima (fibrosis).
• Impyiko: Kunanirwa kw'impyiko (ibi bishobora gushyira ubuzima mu kaga).
• Imyanya ndangagitsina: Kudakora neza kw'imyanya ndangagitsina (ED) ku bagabo no kuma kw'imyanya ndangagitsina ku bagore.

Ni iki gitera Scleroderma?

Mu by’ukuri, abaganga ntibaramenya impamvu nyayo itera scleroderma.

Ubushakashatsi bumwe bwagaragaje ko ishobora kugaragara mu miryango ku rugero runaka (bivuze ko ishobora kwanduzwa n'ababyeyi ijya ku bana), ariko ni gake cyane ku buryo nta bimenyetso bihagije bihari bigaragaza neza ko ari indwara iterwa n'uturemangingo .

Ibintu Bitera Ingaruka za Scleroderma

Umuntu wese ashobora kurwara scleroderma, ariko hari amatsinda amwe ari mu kaga gakomeye:

• Abagore bafite amahirwe angana n'inshuro enye yo kurwara iyi ndwara kurusha abagabo.
• Ikunze kugaragara cyane ku bantu bari hagati y'imyaka 30 na 50. Scleroderma ikunze kugaragara ku bantu bari munsi y'imyaka 30.
• Abirabura bafite amahirwe menshi yo kurwara scleroderma. Bakunda kandi kurwara iyi ndwara hakiri kare, bafite amahirwe menshi yo kugira ibimenyetso bigira ingaruka ku bihaha, kandi bakagira ibimenyetso bikomeye by'uruhu.

Ni izihe ngorane zishobora guterwa na Scleroderma?

Abantu barwaye scleroderma bari mu kaga gakomeye ko kurwara izindi ndwara ebyiri: Raynaud's syndrome na Sjögren's syndrome .

Indwara ya Raynaud ifata imitsi mito y'amaraso mu ntoki zawe no mu mano (imibare yawe). Abantu bafite iyi ndwara bagira ibimenyetso (rimwe na rimwe byitwa 'ibitero'). Iki ni cyo gihe imitsi y'amaraso mu ntoki zawe ihita yifata cyane. Ibi bishobora gutuma uruhu rwo mu ntoki zafashwe ruhinduka ibara ry'uruhu rwawe rusanzwe. Hari n'igihe rushobora kugaragara nk'urw'ubururu.

Indwara ya Sjögren ituma zimwe mu ngirabuzimafatizo z'umubiri wawe zikora ubushuhe buke - akenshi ni iz'amacandwe mu kanwa kawe n'iz'amarira mu maso yawe. Bamwe mu bantu bafite Sjögren na bo bababara imitsi n'ingingo.

Hari ubwoko bumwe na bumwe bwa scleroderma bushobora gutera ingorane zikomeye . Zimwe muri zo zirimo:

• Kunanirwa kw'impyiko
• Umuvuduko ukabije w'amaraso mu mitsi itwara amaraso mu mutima ikayajyana mu bihaha
• Ibisebe byo mu bihaha (pulmonary fibrosis)
• Indwara z'umutima n'imitsi (ibibazo bigira ingaruka ku mutima wawe n'imitsi y'amaraso)
• Kunanirwa k'umutima, indwara y'umutima
• Ubukene bw'ubudahangarwa bw'umubiri
• Indwara zo mu gifu (indwara zigira ingaruka ku buryo umubiri utunganya ibiryo n'uburyo ufata intungamubiri)
• Kanseri

Zimwe muri izi ngorane zishobora kwica . Nubona ibimenyetso bishya cyangwa bihinduka, gana muganga vuba bishoboka. Niba ubona ko ufite ibimenyetso by'indwara y'umutima, nko kugorwa no guhumeka cyangwa kumira, hamagara 911 (cyangwa nimero y'ubutabazi yo mu gace utuyemo) ako kanya, cyangwa ujye mu cyumba cy'ubutabazi bw'ibanze cy'ibitaro.

Indwara ya Scleroderma ipimwa ite?

Umuganga asuzuma indwara ya scleroderma binyuze mu isuzuma ry’umubiri n’ibindi bipimo byinshi.

Ushobora kandi gukenera kubonana n'inzobere mu kuvura indwara zo mu bwonko , umuganga w'inzobere mu kuvura indwara z'ubudahangarwa bw'umubiri. Azagusuzuma kandi akubaze ibimenyetso byawe. Ugomba kubwira umuganga wawe ibimenyetso byawe, igihe byatangiriye, ndetse niba hari ikintu gisa n'aho kibitera kurushaho.

Uzakenera kandi gupimwa inshuro nyinshi kugira ngo umenye neza ko nta zindi ndwara zitera ibimenyetso bisa.

Ni ibihe bipimo abaganga bakoresha kugira ngo bapime indwara ya Scleroderma?

Gusuzuma scleroderma ubusanzwe ni kimwe mu bigize inzira yitwa 'differential diagnosis.' Ibi bivuze ko muganga wawe ashobora gukuraho izindi ndwara kandi agakora ibizamini byinshi kugira ngo amenye icyagutera ibimenyetso mbere yo kugusuzuma urwaye scleroderma. Dore bimwe mu bizamini ushobora gukora:

• Gupima amaraso kugira ngo harebwe uko ubudahangarwa bw'umubiri bwawe bukora.
• Ibizamini by'imikorere y'ibihaha kugira ngo harebwe niba ibihaha byawe cyangwa uturemangingo tw'ubuhumekero byagizweho ingaruka.
• Uburyo bwo gusuzuma uruhu cyangwa izindi ngingo bufatwa bugapimwa muri laboratwari.
• Niba ufite ibimenyetso by'igifu (GI), endoscopi ni ikizamini kireba mu muhogo cyangwa mu nda yawe gikoresheje kamera nto ifatanye n'umuyoboro muremure kandi muto.

Byongeye kandi, uzakenera gukorerwa ibizamini byinshi byo gufata amashusho kugira ngo ufate amafoto y'imbere mu mubiri wawe. Ibi birimo:

• Isuzuma ry'umutima (Electrocardiogram) (ECG)
• Echocardiogram (Echocardiogram - Echo)
• X-ray yo mu gituza
• Gupima CT (Computed Tomography - CT scan)

Scleroderma ivurwa ite?

Nta muti uhari wa scleroderma , ariko muganga wawe ashobora kugufasha kubona uburyo butandukanye bwo kuvura bushobora kugufasha kugenzura ibimenyetso byawe no kugabanya ingaruka zabyo ku buzima bwawe bwa buri munsi.

Ubwoko bw'ubuvuzi ukeneye buterwa n'aho ibimenyetso byawe biri n'uburemere bwabyo. Dore bumwe mu buryo busanzwe bwo kuvura scleroderma:

• Uburyo bwo kuvura uruhu: Uzakenera gukoresha amavuta n'imiti igabanya ubushyuhe kugira ngo uruhu rwawe rudakama.
• Imiti igabanya ubukana bw'umubiri: Iyi miti ibuza ubudahangarwa bw'umubiri kwangiza uturemangingo n'ingingo z'umubiri.
• Imiti yo kugenzura ibimenyetso byihariye: Urugero, ushobora gukenera gufata imiti yo kugenzura umuvuduko w'amaraso, koroshya guhumeka, kuvura impyiko, cyangwa kugabanya ibimenyetso by'igogora.
• Ubuvuzi bw'umubiri: Umuvuzi w'umubiri ashobora kugufasha kunoza imigendere yawe y'umubiri.
• Kuvura uruhu: Ibi bikubiyemo gukoresha urumuri rwa ultraviolet rugaragara cyane (UV) mu kuvura indwara z'uruhu. Ibi bishobora gufasha kuvura uruhu rwabyimbye.
• Gutera uturemangingo tw’amaraso: Hari abantu bafite ibimenyetso bikomeye bashobora gukenera guterwa uturemangingo tw’amaraso. Ibi bikubiyemo gusimbuza uturemangingo tw’amaraso twangiritse uturemangingo tw’amaraso tuzima.

Niba mfite Scleroderma, ni iki nkwiye kwitega?

Ugomba kwitega ko uzavura scleroderma n'ibimenyetso byayo ubuzima bwawe bwose . Nubwo nta muti urambye uhari, abantu benshi babona uburyo bwo kuvura no guhindura imibereho yabo bishobora kugabanya ingaruka ibimenyetso byabo bigira ku buzima bwabo bwa buri munsi.

Kubana n'indwara y'igihe kirekire bishobora kugutera agahinda kenshi. Baza muganga wawe ibyerekeye amatsinda y'abaterankunga cyangwa amahirwe yo kwiga kugira ngo agufashe gucunga imihangayiko yawe n'ubuzima bwawe bwo mu mutwe.

Ese Scleroderma ishobora kwirindwa?

Kubera ko impamvu nyayo itazwi, nta buryo bwo kwirinda scleroderma .

Niyitaho nte? (Kwiyitaho)

Uretse uburyo usanzwe uvura, ushobora no guhangana n'ibimenyetso bimwe na bimwe uhindura imibereho yawe ya buri munsi. Bimwe muri ibyo birimo:

• Gukurikiza indyo yuzuye n'imyitozo ngororamubiri ikubereye.
• Kwirinda gukora imyitozo ngororamubiri ikomeye mu gihe wumva utameze neza.
• Rinda uruhu rwawe wambara imyenda ijyanye n'aho utuye kandi ukisiga amavuta meza yo kwisiga ku zuba iyo ugiye hanze.
• Sura umuganga w'amenyo (umuganga w'amenyo) kugira ngo asukure amenyo kandi ajye asuzuma amenyo buri gihe.

Ni ryari ngomba kubonana na muganga wanjye?

Scleroderma ishobora gutera ibimenyetso bitandukanye, bityo rimwe na rimwe bishobora kugorana kubimenya mu ntangiriro. Niba ufite ububabare bushya cyangwa ibindi bimenyetso, cyane cyane iyo birushijeho kuba bibi, gana muganga. Nubwo ibimenyetso byawe byaba biterwa n'ikindi kintu, muganga wawe ashobora kumenya icyabiteye no kukugira inama yo kuvura kugira ngo ubigenzure.

Niba uburyo bwo kuvura scleroderma busa n'aho budakora neza, cyangwa niba ibimenyetso byawe bihinduka cyangwa bikarushaho kwiyongera - cyane cyane iyo bigira ingaruka ku bushobozi bwawe bwo guhumeka cyangwa kumira - vugana na muganga wawe.

Ni ryari nkwiye kujya mu Ishami ry’Ubuvuzi bw’Ingoboka (ETU) ?

Niba ufite ibimenyetso by'indwara y'umutima , nko kubabara mu gatuza, guhumeka bigoranye, cyangwa niba wumva udashobora kumira, hamagara 911 (cyangwa nimero y'ubutabazi bw'ibanze yo mu gace utuyemo) ako kanya, cyangwa ujye mu ishami rishinzwe ubutabazi bw'ibanze mu bitaro.

Ni ibihe bibazo ngomba kubaza muganga wanjye?

Ntukibagirwe kubaza ibi bibazo igihe ugiye kwa muganga:

• Ese mfite Scleroderma cyangwa indi ndwara?
• Ni ubuhe bwoko bwa Scleroderma mfite?
• Ni ubuhe bwoko bw'ubuvuzi nkeneye?
• Ni izihe ngorane nkwiye kumenya cyane cyane?

Imyaka yo kubaho k'umuntu urwaye Scleroderma ni iyihe?

Abantu benshi barwaye scleroderma ntibagira ibibazo bishobora gushyira ubuzima bwabo mu kaga .

Ariko, niba ufite indwara ya “systemic sclerosis”, ifata ingingo z’imbere mu mubiri, uba uri mu kaga gakomeye ko kugira ibibazo bikomeye. Muganga wawe azakubwira icyo ugomba kwitega ndetse niba uri mu kaga gakomeye ko kugira ibibazo biguhitana.

Ese Scleroderma ni indwara ikomeye?

Kimwe n'indwara iyo ari yo yose idakira, scleroderma ni indwara ikomeye kandi ikomeye.Ibi biterwa nuko ushobora kuzahura n'ibimenyetso ubuzima bwawe bwose. Ariko, ibyo ntibivuze ko Scleroderma izayobora ubuzima bwawe. Ubunararibonye bwa buri wese buratandukanye. Vugana na muganga wawe ku bwoba bwawe, gushidikanya, n'impungenge ufite.

Scleroderma ishobora kuba indwara ibabaza cyane umuntu ashobora kwihanganira. Kubera ko abaganga batazi neza impamvu itera kandi nta buryo bumwe bwo kuvura, bishobora gufata igihe kugira ngo ubone umuti uzagenzura ibimenyetso byawe neza. Muganga wawe azagufasha muri buri ntambwe.

Izere ibyiyumvo byawe byo mu nda, kandi wizere icyo wumva 'kitameze neza'. Ndetse n'impinduka nto mu bimenyetso ishobora kuba ikimenyetso cy'ikibazo kigomba gusuzumwa na muganga wawe. Ntutinye kubaza ibibazo no gusangira ibitekerezo byawe ku bimenyetso byawe cyangwa uburyo uvurwa.

Kubana n'indwara idakira bishobora kunaniza cyane. Fata umwanya wo kwiyubaha no kwishimira akazi gakomeye wakoze kugira ngo ucunge ibimenyetso byawe.

Ibintu by'ingenzi ugomba kwibuka (Ubutumwa bwo kujyana mu rugo)

Noneho, twavuze byinshi kuri Scleroderma. Mu gusoza, dore bimwe mu bintu by'ingenzi ugomba kwibuka:

• Scleroderma ni indwara idakunze kugaragara, aho umubiri ukora kolajeni nyinshi, bigatuma uruhu ndetse rimwe na rimwe n'ingingo z'imbere zibyimba.
• Hari ubwoko bubiri bw'ingenzi bw'ibi: imiterere y'umubiri n'imiterere y'umubiri. Ubwoko bw'umubiri buteye akaga gato kuko bushobora no kugira ingaruka ku ngingo z'imbere.
• Ibimenyetso biratandukanye. Iby'ingenzi birimo kubyimba k'uruhu, kubabara ingingo, umunaniro, ndetse n'indwara ya Raynaud.
• Nubwo nta muti urambye uhari, hari uburyo bwiza bwo kuvura ibimenyetso. Vugana na muganga wawe kandi ushyireho gahunda y'ubuvuzi ikubereye.
• Gusuzuma no kuvurwa hakiri kare ni ingenzi cyane, bityo niba ufite kimwe muri ibi bimenyetso, menya neza ko wagisha inama kwa muganga.
• Kubera ko iyi ari indwara y'igihe kirekire, ni ngombwa gukomeza kugira imbaraga zo mu mutwe. Niba bibaye ngombwa, shaka ubufasha mu matsinda y'abaterankunga.

Wihangayika, ntabwo uri wenyine. Ufite ubumenyi bukwiye n'inama z'abaganga, ushobora kubaho neza ufite iyi ndwara.

Scleroderma , Scleroderma, Kubyimba k'uruhu, Indwara z'ubudahangarwa bw'umubiri, Kolajeni, indwara ya Raynaud, Scleroderma yo mu mubiri, Indwara z'uruhu