Wakambonzwa here nezvemamiriro ezvinhu apo dzimwe nhengo dzemuviri wedu, dzakadai semakumbo nenhengo, hadzikure zvakanaka kana kukura zvizere? Izvi ndizvo zvinonzi navanachiremba aplasia . Unganzwa kutya zvishoma paunonzwa zita iri. Asi usazvidya mwoyo, tichataura nezvazvo zviri nyore uye zvakajeka. Ipapo unogona kunzwisisa zviri nani izvi.
Chii chaizvo chinonzi (Aplasia)?
Zvichitaurwa zviri nyore, aplasia chirwere apo chikamu chemuviri wako, chingave chiri chinyama, nhengo, kana chimwe chikamu chemuviri wako, hachikure kana kushanda nemazvo. Kazhinji, zvirwere izvi zvinowanikwa panguva yekuzvarwa kana kuti asati aberekwa, mwana achiri mudumbu. Dzimwe nguva, kana chiremba achiongorora mwana ari mudumbu kana mwana achangoberekwa, vanogona kuona kuti chikamu, chakadai seruoko kana gumbo, hachina kuumbwa zvakanaka. Zvisinei, mamwe mamiriro e aplasia, kunyanya aya anosanganisira nyama dzemukati senge bone morrow, anogona kuonekwa panguva yehudiki kana kunyange kukura.
Chinhu chakakosha ndechekuti aplasia haisi chirwere chimwe chete. Izwi rinoshandiswa navanachiremba kutsanangura chero chirwere chinenge chisina kuumbwa zvakakwana mumuviri.
(Aplasia) yakasiyana sei ne (Agenesis), (Hypoplasia), uye (Dysplasia)?
Mashoko aya anogona kuvhiringa kunzwa, nekuti anoreva chinhu chimwe chete. Asi pane misiyano midiki. Ngationei kuti chii.
- (Agenesis): Apa ndipo apo chikamu chemuviri chinotadza kukura zvachose . Mune mamwe mazwi ekurapa, (Aplasia) zvinoreva kuti pane chimiro chenhengo chisina kukura zvakakwana. Asi mu (Agenesis), hapana chikamu chenhengo iyoyo chakagadzirwa. Semuenzaniso, kana itsvo ikasakura zvachose, inonzi (Renal Agenesis).
- Hypoplasia: Apa ndipo apo chikamu chemuviri chisina kukura zvakanaka . Kureva kuti, chiripo asi chiri chidiki kana kuti chisina kukwana. Dzimwe nguva, aplasia inoonekwa semamiriro ari pakati peagenesis (kusavapo) uye hypoplasia (kusakura zvakanaka).
- Dysplasia: Uku kukura kusina kujairika, kusina kurongeka kwenhengo kana nhengo yemuviri. Kusiyana neaplasia, dysplasia haisi nguva dzose inokonzerwa nedambudziko rekutanga kukura (kureva kuti, chikamu chinotanga kukura chozomira). Dysplasia inowanzo kuve kukura kusina kujairika kwemasero kana tishu. Semuenzaniso, pakutanga kwekenza, shanduko dzisina kujairika mumasero (`dysplasia`) dzinoitika, dzinozopedzisira dzava kenza.
Kana usina chokwadi nezvemashoko aya, iva nechokwadi chekubvunza chiremba wako kuti akutsanangurire . Izvi zvichakubatsira kunzwisisa zvakajeka chirwere chaungave nacho iwe kana mwana wako.
Ndedzipi mhando huru dzeaplasia?
Haasi marudzi ese e aplasia akajairika. Zvisinei, kune marudzi mashoma e aplasia atinowanzo kunzwa nezvawo, kana anozivikanwa nawo zvakanyanya. Aya anosanganisira masero matsvuku eropa, ganda, mapfupa, uye masero ehutachiona (kureva urume nemazai). Aplasia inogonawo kukanganisa dzimwe nhengo dzemuviri, dzakadai semapapu netsinga yemaziso.
Ngatitaurei nezve Pure Red Cell Aplasia (PRCA)
Mumamiriro ezvinhu aya, masero matsvuku eropa (`Masero Matsvuku Eropa`) haakure zvakanaka. Kazhinji, mupfupa wedu (`Bone Marrow`) unogadzira masero matsvuku eropa matsva anenge mazuva zana nemakumi maviri ega ega. Munguva iyi, masero matsvuku eropa anokura kubva padanho rawo rekutanga, ``Erythroblast``, kuita masero matsvuku eropa akakura zvakakwana.
Kana uine PRCA , mupfupa wako unogona kugadzira ma erythroblast mashoma kana kusaburitsa zvachose. Izvi zvinoita kuti muviri urasikirwe nemasero matsvuku eropa aunoda, zvichikonzera anemia. Izvi zvinonzi "pure" nekuti zvinongokanganisa masero matsvuku eropa chete. Mamwe masero eropa - masero machena eropa nemaplatelet - anogadzirwa zvakajairika. Zvisinei, kana marudzi ese matatu emasero eropa asina kugadzirwa zvakanaka, inonzi aplastic anemia .
PRCA inogona kuvapo panguva yekuzvarwa (congenital PRCA), kana kuti inogona kukura muhupenyu hwese. Rudzi rwePRCA rwekuzvarwa narwo runonzi Diamond-Blackfan Anemia .
Chii chinonzi Aplasia Cutis Congenita?
Apa ndipo apo ganda remwana wako achangoberekwa, kunyanya ganda remusoro, rinenge risina kukura zvakanaka kana kuti risisipo zvachose mune dzimwe nzvimbo. Dzimwe nguva, nyama nemapfupa ari pasi peganda iroro hazvikure zvakakwana. Ganda rinogonawo kushaikwa mune dzimwe nzvimbo dzemuviri wemwana, maoko, nemakumbo.
(Aplasia Cutis Congenita) inogona kuoneka sevanga pamusoro peganda, isina bvudzi pasi. Kana kuti, ganda risina kukura zvakanaka rinogona kuoneka seganda rakatetepa risina bvudzi.
Sezvinoreva zita racho (`Congenita`), ichi chirwere chekuzvarwa nacho, zvichireva kuti chinowanikwa kubva pakuzvarwa.
Ngatidzidzei nezve Radial Aplasia
Apa ndipo apo rimwe remapfupa maviri ari paruoko rwako, radius, rinotadza kukura. Pane mapfupa maviri marefu ari paruoko rwako, radius neulna. Ulna inomhanya kubva pagokora rako kuenda kuruoko rwako, parutivi panowanikwa chigunwe chako chidiki. Radius inomhanya kubva pagokora rako kuenda kuruoko rwako, parutivi panowanikwa chigunwe chako. Munhu ane radial aplasia anogona kunge aine ruoko rwakakombama, rwakaremara. Chigunwe chikuru chingave chisipo kana kuti chipfupi pane zvakajairika.
(Radial Aplasia)Kushaikwa kweRadial Ray imhando yechirwere. Idambudziko nekukura kweRadius bone. Kushaikwa kweRadial Ray kunogona kubva pakushoma kusvika pakukomba. Dzimwe nguva Radius bone inoumbwa, asi ipfupi pane yakajairwa. Dzimwe nguva, Radius bone haikure zvachose.
Chii chinonzi Germ Cell Aplasia kana Sertoli-Cell-Only Syndrome?
Apa ndipo panorasikirwa nemasero embeu (`Maseru eGerm`) mumachende avo (`Matestes`). Maseru embeu masero ekubereka. Muvarume, masero embeu ndiwo anozova mbeu yembeu (`Urume`). Kana masero embeu akarasika, mbeu yembeu haigone kugadzirwa. Izvi zvinoreva kuti vanhu vane aplasia yemasero embeu havakwanisi kuva nevana (`Kusabereka`).
Kupararira kwemasero emumajini kunonziwo Sertoli-Cell-Only Syndrome . Izvi zvinodaro nekuti, kunyangwe masero emumajini asipo, masero eSertoli achiripo muhurongwa hwekubereka. Kazhinji, masero eSertoli anobatsira masero emumajini kukura kuita urume. Zvisinei, kana masero emumajini asipo, masero eSertoli haana basa mukugadzirwa kweurume.
Ngatitariseiwo Pulmonary Aplasia.
Pulmonary Aplasia chirwere chinobata munhu kuzvarwa aine mapapu asina kukura zvakanaka. Ichi hachisi chirwere chimwe chete, uye chinogona kuuya mumhando dzakasiyana-siyana. Chinogona kubva pakusakura zvakanaka kwemapapu (Pulmonary Agenesis) kusvika pakusakura zvakanaka (Pulmonary Hypoplasia).
Pulmonary Aplasia iri pakati pePulmonary Agenesis nePulmonary Hypoplasia. MuAplasia, chimiro chemapapu chisina kusimba chinokura, asi hachigone kuita basa remapapu anoshanda zvizere.
Kazhinji, mapapu rimwe harisipo kana kuti harina kukura zvakanaka, nepo rimwe racho risingakurumidzi kukura zvakanaka.
Chii chinonzi Thymic Aplasia?
Gland rako rethymus igland rinogadzira rudzi rwemasero machena eropa anonzi T-cells. MaT-cell anobatsira muviri wako kurwisa hutachiona. MuThymic Aplasia , gland rako rethymus harikure. Paunozvarwa usina thymus gland, une mukana wekutapukirwa nehutachiona.
Kusavapo kwe thymus gland chimwe chezviratidzo zvechirwere chinonzi DiGeorge Syndrome . DiGeorge Syndrome inogona kukanganisa masisitimu emuviri akasiyana-siyana. Inogona kukanganisa masoja emuviri wako uye mashandiro emwoyo, uye inogonawo kukonzera kunonoka kukura kwemwana.
Ngatiziveiwo nezve Optic Nerve Aplasia.
(Optic Nerve Aplasia)Kurasikirwa kwezvikamu zvakakosha zveziso rimwe chete kana ese ari maviri, kusanganisira tsinga yemaziso, pakuzvarwa. Tsinga yako yemaziso inoita basa rakakosha mukuona kwako. Ndiyo inobvumira maziso ako kutaurirana neuropi hwako uye kugadzirisa ruzivo rwekuona. Nekuda kwetsinga yemaziso, maziso ako paanoona zvinhu zvakaita semaumbirwo nemavara, uropi hwako hunogona kushandura ruzivo irworwo kuita mufananidzo unoonekwa wahunogona kunzwisisa.
Optic Nerve Aplasia inogona kukonzera matambudziko emaziso akasiyana-siyana, zvichienderana nekuoma kwechirwere chako. Aplasia, chirwere chinokanganisa maziso ese, chinogonawo kukonzera matambudziko mukukura kwehuropi.
Aplasia yakajairika zvakadii?
Aplasia chirwere chisingawanzoitiki . Mhando dzakajairika ndi `(Radial Aplasia)` uye rudzi rwe ``Pure Red Cell Aplasia`` (PRCA). `(Radial Aplasia)` inobata anenge mwana mumwe chete pavana 30,000 vachangoberekwa. `(Radial Ray Deficiencies)` (iyo inosanganisirawo `(Radial Aplasia)`) chirwere chinowanzo itika paruoko. Rudzi rwekuzvarwa narwo (PRCA) haruwanzoitikiwo, runofungidzirwa kuti rune vanhu 5 kusvika ku7 pavana miriyoni. Rudzi rwekuzvarwa narwo rwakanyanya kuwanda, asi hatizivi kuti pane nyaya ngani chaizvo.
Ndezvipi zvikonzero zve aplasia?
Mhando dzakawanda dzeaplasia dzinokonzerwa nekuchinja kwemajini, izvo zvinotorwa kubva kuvabereki. Majini ako ane mirairo inosarudza hunhu hwemuviri hwauchava nahwo. Semuenzaniso, mirairo iyi inosarudza kuti nhengo ichakura kupi uye sei. Unowana majini kubva kuna amai vako nababa vako. Kana jini riine kuchinja, kana kuti chikanganiso, unogona kuva nematambudziko akaita seaplasia.
Kashoma kuti aplasia ibude nekufamba kwenguva. Semuenzaniso, acquired PRCA inokonzerwa nezvimwe zvikonzero nemamiriro ezvinhu, kusanganisira hutachiona, zvirwere zve autoimmune, uye mamwe marudzi ekenza.
Dzimwe nguva, vanachiremba nemasayendisiti havakwanise kuwana chikonzero che aplasia. Mhando dzakadaro dze aplasia dzinonzi idiopathic .
Nzira yekuziva sei (Aplasia)?
Mamwe marudzi e aplasia anogona kuonekwa panguva yekuzvitakura kuburikidza nekuongororwa, senge ultrasound scan. Mamwe marudzi e aplasia haaonekwe kunze uye anongoonekwa chete pakuzvarwa.
Kana chirwere chacho chisina kunyanya kuipa, kana kuti chinosanganisira ropa nemapfupa, zviratidzo zvacho zvinogona kusaonekwa kusvika pakukura kwehupenyu. Zvichienderana nerudzi rweaplasia, ungangoda kutorwa mifananidzo yakasiyana-siyana, kuongororwa ropa, uye kuongororwa majini kuti uone kana chirwere chako chiripo.
Ndeipi mishonga yekurapa (Aplasia)?
Nzira dzekurapa dzinosiyana zvichienderana nemamiriro ako ezvinhu. Kuvhiyiwa kunogona kuitwa kuti pave nekushanda zvakanaka kwegumbo kana ruoko rusina kukura zvakanaka. Muzviitiko zvakakomba zvePRCA, kuwedzerwa ropa kunogona kudiwa. Zvichienderana nemamiriro ako ezvinhu, mishonga inogona kupihwa kudzora zviratidzo kana kudzivirira matambudziko anokonzerwa neaplasia.
Mamwe marudzi e aplasia, akadai se germ cell aplasia, haagoni kurapwa.
Aplasia inogona kurapwa here?
Kuti chirwere chako chichavandudzika here kana kuti kwete zvinoenderana nerudzi rweaplasia yaunayo uye zvinhu zvakakonzera izvozvo. Semuenzaniso, aplasia yemasero matsvuku akawanikwa (PRCA) inogona kurapwa, zvichienderana nezviri kutadzisa muviri wako kugadzira masero matsvuku eropa. Kurapa chirwere chiri pasi pechirwere ichi chinodzivirira kugadzirwa kwemasero matsvuku eropa dzimwe nguva kunogona kuvandudza aplasia.
Aplasia chirwere chekuzvarwa nacho chisingagone kuchinjwa, zvichireva kuti hachigone kurapwa zvachose. Muzviitiko zvakadaro, chiremba anogona kukurudzira kuvhiyiwa, mishonga, kana kurapwa kwakanangana. Izvi zvinogona kubatsira kuvandudza mashandiro eruoko, gumbo, kana gumbo, kana kudzora zviratidzo.
Izwi rekuti "(Aplasia)" rinogona kureva zvinhu zvakasiyana-siyana. Zvinoenderana nezvinhu zvakawanda, kusanganisira kuti chikamu chemuviri charinokanganisa chii, zviratidzo zvako, uye kuti chirwere chacho chakanyanya kuderera kana kuti chakanyanya sei. Usavhiringidzwa nemashoko aya. Kana iwe kana mamiriro emwana wako munotsanangurwa nerimwe izwi rakaita sekuti "(Aplasia)," "(Agenesis)," kana chimwe chinhu chakafanana, bvunza chiremba wako kuti mazwi iwayo anorevei uye zvaunotarisira nekufamba kwenguva. Bvunza kana paine mishonga iripo uye kana ichidiwa. Kana zvakadaro, kurukura kuti ndeapi marudzi emishonga angabatsira. Bvunza kuti matambudziko aya ekukura anokanganisa sei (kana kuti haakanganisi) hupenyu hwako hwezuva nezuva.
Zvinhu zvinonyanya kukosha zvatinofanira kurangarira
Zvakanaka, saka, ndinovimba une pfungwa kubva pane zvatataura nezvazvo (Aplasia). Muchidimbu:
- Aplasia zvinoreva kuti chikamu chemuviri hachina kukura zvakanaka.
- Ichi chirwere hachina kufanana, chinogona kuuya mumhando dzakasiyana uye pamatanho akasiyana .
- Mamwe marudzi e aplasia anozvarwa ari ekuzvarwa nawo, nepo mamwe achikura muhupenyu hwese.
- Zvikonzero zvacho zvakasiyana-siyana; zvikonzero zvemajini, hutachiona, zvimwe zvirwere, uye dzimwe nguva hapana chikonzero chingawanikwe.
- Kurapwa kunoenderana nerudzi uye kuoma kwechirwere cheaplasia. Zvimwe zvingada kuvhiyiwa, mishonga, kana mamwe marapirwo chaiwo ekudzora zviratidzo uye kuvandudza hupenyu.
- Kunyange hazvo aplasia yekuzvarwa nayo isingarapike zvachose, kana munhu achitarisirwa zvakanaka uye achitsigirwa, zvinokwanisika kurarama hupenyu hwakajairika.
- Chinhu chinonyanya kukosha ndechekuona chiremba uye kuwana mazano akakodzera neruzivo kana iwe kana mwana wako muine chero chamunofungidzira nezvechirwere ichi.Usavhunduke, bvunza mibvunzo, uye nzwisisa mamiriro acho ezvinhu nemazvo.
Tinovimba kuti wawana ruzivo urwu ruchibatsira!
Aplasia , Kusakura kwenhengo dzemuviri, Zvirema zvekuzvarwa nazvo, Aplasia Yemasero Matsvuku Akachena, Aplasia Cutis Congenita, Radial Aplasia, Aplasia Yemasero Ejeru

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