Matama emwana wako anoita seakazvimba here uye shaya yake inoita seyakakura? Ingave Cherubism. Ngatitaurei nezvazvo!

Ungave uchinetseka kuti chiso chemwana wako chachinja zvishoma, matama ake achiratidzika seazvimba. Kana kuti chiremba akakuudza nezvekuchinja kwechirebvu chake here? Isu tinoti chirwere ichi (Cherubism) . Zita racho ringanzwika serisinganzwisisike, asi ngatirambei tichiri nyore. Ichi chirwere chisingawanzoitiki, asi zvakakosha kuti uzive nezvazvo.

Chii chinonzi Cherubism?

Zvichitaurwa zviri nyore, Cherubism chirwere chisingawanzoitika mumajini. Chinoitika kana nyama dzisina kujairika dzichikura mushaya yemwana wako panzvimbo pemapfupa ane hutano. Nyama iyi isina kujairika haina kenza uye kazhinji hairwadzi. Zvisinei, inogona kukonzera kuti shaya yemwana ive yakafara kumativi ese uye matama avo aonekwe akatenderera uye azvimba . Vamwe vana vanogona kurasikirwa nemazino kana kuva nemazino anokura zvisina kurongeka. Cherubism haikanganisi mamwe mapfupa mumuviri, shaya chete .

Zviratidzo izvi hazvitange kuoneka mushure mekuzvarwa. Zvinowanzoonekwa pakati pemakore maviri nemanomwe. Kuoma kwechirwere ichi kunogona kusiyana kubva pamunhu kusvika pamunhu. Vamwe vana vanogona kunge vasina zviratidzo zvachose, kana kuti zviratidzo zvacho zvinogona kunge zvisinganzwisisike uye zvisinganyatsooneki. Zvisinei, muzviitiko zvakakomba, mwana anogona kunetseka kutaura, kumedza, kana kutofema.

Chinhu chakanakisa ndechekuti cherubism inowanzopera yega kana munhu akura asina kurapwa. Vanachiremba vanogara vachitsvaga chirwere ichi uye vanokurudzira kurapwa chete kana zviratidzo zvacho zvakanyanya kana kuti zvichikanganisa hupenyu hwemwana zvakanyanya.

Cherubism yakajairika sei?

Cherubism haisi chirwere chinowanzoitika. Vaongorori havazivi kuti vangani vane chirwere ichi, asi vakaita fungidziro zvichibva pane zvakaburitswa muzvinyorwa zvekurapa. Ongororo yakaitwa muna 2019 yakawana kuti kune zviitiko 513 zveCherubism zvakashumwa mumabhuku ekurapa. Saka unogona kuona kuti hazviwanzoitiki.

Ndezvipi zviratidzo zveCherubism?

Izvi ndizvo zviratidzo zvinowanzoonekwa zveCherubism:

• Pfupa reshaya repazasi (manible) rakafara kupfuura zvaitarisirwa.
• Kukura kwakaita semaburi mushaya yemwana.
• Matama akatenderera, akazvimba.
• Kuchinja kwechimiro chemazino, mazino asipo, kana mazino akakuvara.

Vamwe vana vanogonawo kuva nezviratidzo izvi:

• Maziso anoita seari kubuda akatarisa mudenga. Chikamu chichena cheziso (sclera) chinoonekwa pasi peiris nhema.
• Nyama yakawedzerwa iri mushaya yepamusoro inokanganisa ziso netsinga dzaro, zvichikonzera kurasikirwa nekuona kana kurasikirwa nekuona zvishoma nezvishoma.
• Kufema nemuromo.
• Kungonorera.
• Kusakwanisa kufema zvakanaka pakurara.
• Kuoma kutaura kana kumedza.

Ndezvipi zvikonzero zveCherubism?

Zviitiko zvakawanda zveCherubism (zvinopfuura 90%) zvinokonzerwa nekuchinja kwemajini kunonzi `SH3BP2`.

Jini iri re'SH3BP2' rinodzidzisa muviri wedu magadzirirwo epuroteni ye'SH3BP2'. Puroteni iyi inobatanidzwa mukubvisa mapfupa ekare nekuvaka mapfupa matsva (kugadzirisa mapfupa). Kuchinja kwemajini kunoita kuti muviri ugadzire puroteni iyi ye'SH3BP2' yakawandisa.

Kana puroteni iyi ikagadzirwa yakawandisa, kuzvimba kunoitika mupfupa reshaya. Zvinowedzerawo kugadzirwa kwemasero anonzi osteoclasts . MaOsteoclasts rudzi rwemasero anoita basa rakakosha mukuputsa mapfupa ayo muviri usingachadi. Zvisinei, kana masero aya awanda zvakanyanya, anotanga kuputsa mapfupa mupfupa reshaya kana asingadiwi. Kurasikirwa kwemapfupa uku kusingawanzoitiki, pamwe chete nekuzvimba kunokonzerwa nekuwedzera kweSH3BP2, kunotungamira pakuumbwa kwekukura kwakafanana necyst mupfupa reshaya. Kukura uku kunowedzera zvishoma nezvishoma, izvo zvinokonzera zviratidzo zvechirwere ichi (Cherubism).

Zvisinei, vamwe vana vane Cherubism havana SH3BP2 gene mutation. Muzviitiko zvakadaro, mamwe majini mutations anogona kunge ari iwo anokonzera. Asi vaongorori havasati vaziva kuti kushanduka ikoko chii chaizvo.

Ko (Cherubism) chinhu chinobva kuchizvarwa kuenda kune chimwe chizvarwa here?

Ehe, vana vazhinji vanogara nhaka yekuchinja kwemajini kunokonzera Cherubism. Chirwere ichi chinopfuudzwa nenzira inotonga yega yega yekugara nhaka. Zvichitaurwa zviri nyore, kana mumwe mubereki aine kuchinja kwemajini, mwana ane mukana wekuchiwanawo.

Zvisinei, vamwe vana vanogona kuva nechirwere ichi kunyangwe pasina munhu mumhuri akambova nacho. Vaongorori vanoti ichi 'de novo mutation' . Kureva kuti, shanduko itsva yemajini inoitika mumunhu, isina nhoroondo yemhuri.

Saka, kunyange hazvo Cherubism ichiwanzogara nhaka, hazviwanzoitika. Kunyangwe pasina munhu mumhuri ane chirwere ichi, vanachiremba vanoona Cherubism sechirwere chinogona kuongororwa.

Pane zvimwe zvinhu zvine chekuita neCherubism here?

Mune vamwe vana, Cherubism inogonawo kuitika sechikamu cheimwe chirwere chemajini. Zvimwe zvezvirwere izvi zvinosanganisira:

• `(Dambudziko reFragile X)`
• `(Jaffe-Campanacci syndrome)`
• `(Neurofibromatosis rudzi 1)`
• `(Noonan syndrome)`
• `(Ramon syndrome)`

Muzviitiko zvakadaro, chikonzero cheCherubism hachisi chekuchinja kwemajini eSH3BP2. Asi, dzimwe shanduko dzemajini dzine chekuita nechirwere ichi ndidzo dzinokonzera.

Vanachiremba vanoongorora sei Cherubism?

Vanachiremba vanotevera matanho aya kuti vaongorore Cherubism:

• Kuongororwa kwemuviri: Izvi zvinosanganisira kutarisa mwana kana paine zviratidzo zvakaita seshaya yakafara zvisingawanzoitiki, mazino asipo, kana matambudziko emazino (Cherubism).
• Kuraira bvunzo dzemifananidzo: Izvi zvinosanganisira bvunzo dzakadai seX-rays kana CT scans (computed tomography scans) . Izvi zvinogona kubatsira kuongorora zviri nani mamiriro epfupa reshaya.
• Kuraira bvunzo dzemajini: Miedzo iyi inoitirwa kutarisa shanduko dzemajini.

Vanachiremba vanofanirawo kubvisa zvimwe zvirwere zvine zviratidzo zvakafanana, zvakaita sefibrous dysplasia kana aneurysmal bone cysts , uye kuona kana Cherubism iri chikamu che genetic syndrome.

Ndeipi mishonga yeCherubism?

Vana vazhinji vane cherubism havadi kurapwa kwakakosha. Vanachiremba vevana vanowanzo tora nzira yekuti "mira uone". Kureva kuti, vanoongorora mamiriro acho voona kuti anokura sei. Kazhinji, nyama idzi dzisina kujairika dzinokura kusvika mwana asvika pakukura, dzinogara dzakafanana kwemakore mashoma, uye dzotanga kudzikira zvishoma nezvishoma. Zviratidzo zvecherubism zvinowanzopera pakukura.

Zvisinei, kana mwana wako aine matambudziko ekudya kana kufema, chiremba anogona kukurudzira kuvhiyiwa. Zvisinei, vanachiremba vanowanzokurudzira kuvhiyiwa mushure mekunge kukura kwenyama kusina kujairika kwamira. Kana munhu achiri nezviratidzo uye achida kuchinja chitarisiko chechiso chake, kuvhiyiwa kunogona kufungwa. Kuvhiyiwa kwekugadzirisa kunobatsira kugadzirisa chiso chemunhu kuti chienderane nezvaanoda.

Kurapa Kunotsigira

Cherubism inogona kukanganisa zvinhu zvakawanda muhupenyu hwemwana, kunyanya kana chirwere chacho chakanyanya kuipa. Nokudaro, mwana angangoda kurapwa kwakakodzera zvaanoda. Sarudzo dzekurapa dzingasanganisira:

• Kurapwa kwemazino: Vana vane cherubism vangada kurapwa mazino, sekubviswa kwezino kana kuiswa muma implants . Kana matumbu akafanana necyst mushaya atanga kuderera, mwana angadawo mabraces (orthodontics) .
• Rutsigiro rwekuona: Muzviitiko zvakakomba zvecherubism, kuona kwemwana kunogona kukanganiswa. Chiremba wemaziso anogona kuongorora kuona kwemwana uye kuwana mhinduro yakanakisa yezvinodiwa zvake.
• Batsirai pakutaura nekumedza: Kana mwana achinetseka kutaura kana kumedza,Nyanzvi yekurapa mutauro wekutaura (SLP) inogona kubatsira.
• Rutsigiro rwepfungwa: Cherubism inogona kukanganisa kuzviremekedza kwemwana. Zvakakosha kutaura nemwana wako nezvekunzwa kwake uye kuti chirwere ichi chiri kukanganisa sei maonero ake. Mwana wako anogona kubatsirwa nekutaura nenyanzvi yepfungwa yevana nezvemanzwiro ake.

Chii chiri tarisiro kune avo vane Cherubism?

Vanhu vazhinji havazovi nezviratidzo zveCherubism pavanosvika makore makumi matatu. Panguva iyoyo, nyama isina kurongeka inenge yatsiviwa nenyama yemapfupa yakajairika.

Kashoma, zviratidzo zvecherubism zvinogona kuramba zviripo kusvika munhu akura. Kana izvi zvikaitika, chiremba achapa nhungamiro nerutsigiro zvinodiwa.

Ko Cherubism inogona kudzivirirwa here?

Vanachiremba havazivi nzira yekudzivirira chirwere ichi. Kana mumwe munhu mumhuri yako aine Cherubism, zvingava zvakanaka kuti uwane mazano ezvemajini usati wabata pamuviri.

Ndingatarisira sei mwana wangu?

Kana mwana wako aine Cherubism, ziva zvinhu zvinotevera:

• Rambai muchiendesa mwana wenyu kuna chiremba wevana. Chiremba achakuudzai kuti munodzoka kangani.
• Ongorora maziso emwana wako zvichienderana nenguva yakakurudzirwa nachiremba.
• Tsigira mwana mupfungwa. Mukurudzire, taura naye.

Ndinofanira kufonera chiremba riini?

Fonera chiremba wevana vako kana mwana wako aine chimwe chezvinotevera:

• Matambudziko ekufema, akadai sekushaya hope kana kushaya mweya wekurara .
• Kuoma kumedza.
• Kuoma kutaura.
• Matambudziko ekuona.

Zita rokuti (Cherubism) rakauya sei?

Chirwere ichi chakatumidzwa zita muna 1933 naDr. William A. Jones . Akasarudza zita rekuti "Cherubism" nekuti zviratidzo zvechirwere ichi zvinosanganisira kumeso kwemwana, kuzvimba uye dzimwe nguva maziso akatarira kumusoro. Aitenda kuti zvinhu izvi zvakafanana ne "kerubhi," chifananidzo chakanaka, chengirozi chinoonekwa muhunyanzvi netsika dzakasiyana dzechitendero. Zita iri rave richishandiswa kubvira ipapo.

Zvinogona kushamisa kuziva kuti mwana wako ane chirwere chisingawanzoitiki. Kana ari Cherubism, zviratidzo hazvionekwi pakuzvarwa, saka unogona kunetseka paunoona shanduko pachiso chemwana wako kana chiremba paanotaura nezvazvo. Asi yeuka, nyaya zhinji dzeCherubism dzinopera dzoga mwana paanosvika pakukura.Muzviitiko zvakakomba, vanachiremba vanogona kurapa migumisiro yechirwere ichi (Cherubism). Kupa mwana wako rudo rwakawanda uye rutsigiro rwepfungwa zvichamubatsira kuwana rubatsiro rwese rwaanoda kuti anyatsoshandisa hudiki hwake nekukura kwake.

Mharidzo Yekuenda Nayo Kumba

Cherubism chirwere chisingawanzoitika chinokanganisa shaya. Izvi zvinogona kukonzera kuti matama emwana azvimbe uye shaya iite seyakafara. Izvi zvinowanzova nani sezvo mwana achikura. Zvisinei, kana vachinetseka kufema kana kumedza, ona chiremba. Chinhu chakakosha ndechekuramba uchipa mwana wako rudo rwako nerutsigiro. Chinhu chakakosha ndechekubatsira mwana wako kuti arambe akasimba uchitevera mazano echiremba. Usazvidya mwoyo, hausi wega parwendo urwu.

` Cherubism, zvirwere zvemajini, pfupa reshaya, matama akatumbuka, zvirwere zvevana, matambudziko emazino, jini reSH3BP2