Wakamboona here kuti rumwe rutivi rwemuviri wemwana wako, kungava ruoko kana gumbo, kana rumwe rutivi rwechiso chake, runoita serwakakura zvishoma pane rumwe? Dzimwe nguva musiyano uyu mudiki zvekuti ungasaonekwa pakutanga. Asi mwana paanokura, musiyano uyu unova pachena. Nhasi tichataura nezvemamiriro ezvinhu akadaro.
Chii chinonzi Hemihyperplasia? Ngationei zviri nyore!
Zvichitaurwa zviri nyore, hemihyperplasia inguva apo rumwe rutivi rwemuviri wedu runokura kupfuura rumwe. Izvi dzimwe nguva zvinonzi overgrowth syndrome , uye dzimwe nguva hemihypertrophy . Kazhinji inokanganisa chiso, maoko, kana makumbo. Asi dzimwe nguva inogonawo kukanganisa nhengo dzemukati dziri mukati medumbu. Funga nezvayo segumbo rimwe rakareba zvishoma pane rimwe, kana ruoko rumwe rwakakora zvishoma. Pakutanga, mutsauko uyu ungave wakaoma kunzwisisa, asi mwana paanokura, unova pachena.
Ndiani anowana chirwere ichi? Chinowanzoitika sei?
Hemihyperplasia chirwere chinoitika muvana . Zvinoreva kuti hapana musiyano pakati pevarume nevakadzi. Idambudziko rekuzvarwa naro , zvichireva kuti mwana anozvarwa aine chirwere ichi. Dzimwe nguva vanachiremba vanochiziva pakuzvarwa. Asi dzimwe nguva chingasazivikanwe kusvika mwana akura zvishoma, kusvika musiyano uripo pakati pemativi maviri emuviri wanyatsooneka.
Ichi chirwere chisingawanzoitiki . Ongororo yakaratidza kuti Beckwith-Wiedemann syndrome , rudzi rwakajairika rwe hemihyperplasia, inoitika mumwana mumwe chete pavana 11,000 vanozvarwa. Saka unogona kufungidzira kuti izvi hazviwanzoitiki sei.
Hemihyperplasia inokanganisa sei mwana?
Nzira huru iyo chirwere ichi chinokanganisa nayo mwana ndeyekukonzera musiyano muhukuru hunoonekwa hwezvikamu zviviri zvemuviri izvo zvinowanzofanira kunge zvakafanana. Semuenzaniso, rumwe rutivi rwechiso runogona kutaridzika serwakakura kupfuura rumwe, zvichireva kuti runogona kutaridzika serwakakura.
Chinonyanya kukosha ndechekuti vana vane hemihyperplasia vari panjodzi yakakura yekubatwa nekenza . Njodzi iyi inosanganisira bundu reWilms, rudzi rwekenza yeitsvo, uye hepatoblastoma, rudzi rwekenza yechiropa yevana. Kuwanda kwenjodzi yekenza idzi kunokonzerwa nekuchinja kuri kuita nhengo dzemukati dzemwana.
Kana mwana wako aine hemihyperplasia, angangoda kuongororwa kenza nguva nenguva kwemakore manomwe . Miedzo iyi inowanzo sanganisira:
- Kuongororwa kwemudumbu: Izvi zvinoongorora kukura kwakaita semabundu.
- Kuongororwa kweropa: Izvi zvinotarisa chiratidzo chebundu chinonzi alpha-fetoprotein . Izvi zvinogona kupa ruzivo rwekuti kenza iripo here.
Unganzwa kutya paunonzwa nezvebvunzo idzi, asi kuziva zvinhu izvi pachine nguva uye kuita bvunzo nemazvo ndicho chinhu chakakosha pahutano hwemwana wako.
Ndezvipi zviratidzo zveHemihyperplasia?
Chiratidzo chikuru uye chinonyanya kuoneka chechirwere ichi ndechekuti rumwe rutivi rwemuviri runokura kupfuura rumwe . Dzimwe nguva musiyano uyu haunyatsooneki, asi unonyanya kuoneka nekufamba kwenguva.
Zvimwe zviratidzo (zvinowanzobatanidzwa neBeckwith -Wiedemann syndrome yambotaurwa) zvinosanganisira:
- Kuonekwa kwakakwenya panzeve.
- Zvimwe zvikanganiso mumadziro edumbu.
- Kukura kwenhengo dzemukati (chiropa, pancreas, itsvo).
- Rurimi rukuru.
- Kuderera kweshuga muropa (hypoglycemia) .
Kungoti chimwe chete kana zviviri zvezviratidzo izvi zviripo hazvirevi kuti chirwere chacho chiripo, asi kana mwana wako aine zvinhu izvi, zvakanaka kuti aone chiremba.
Ndeupi musiyano uripo pakati peHemihyperplasia neHemiatrophy?
Matambudziko ese aya anokonzera shanduko muhukuru hwemuviri. Zvisinei, hemiatrophy chirwere apo rumwe rutivi rwemuviri haruna kukura zvakanaka . Hemiatrophy inowanzo kanganisa nzvimbo imwe chete yemuviri, senge maoko. Hemihyperplasia inogona kukanganisa nzvimbo dzakawanda dzemuviri panguva imwe chete.
Chii chinokonzera hemihyperplasia?
Mune zvimwe zviitiko, hemihyperplasia inogona kukonzerwa nechirwere chemajini chinonzi Beckwith-Wiedemann syndrome . Mune zvimwe zviitiko, chirwere ichi chinogona kuitika pasina matambudziko emajini. Muzviitiko zvakadaro, vanachiremba havazivi kuti chii chinokonzera. Kana chisina chekuita nekusarongeka kwemakromosomu, chingangove chirwere chinongoitika nguva nenguva, zvichireva kuti chinoitika netsaona.
Hemihyperplasia inoonekwa sei?
Hapana bvunzo chaiyo yekuongorora hemihyperplasia. Kana chiremba wemwana wako akaona kukura kusina kuenzana pakati pezvikamu zviviri zvemuviri, anogona kuita ongororo yemuviri uye bvunzo dzemajini kuti aone kana uine Beckwith-Wiedemann syndrome . Kuongororwa kwemajini uku kunogona kubatsira chiremba wako kuona kana chirwere ichi chakakonzerwa nechirwere chemajini.
Uyewo, chiremba wemwana anogona kuita ultrasound kuti aone kana paine zvisizvo kana bundu riri munhengo dzemukati.
Pane mushonga wakakwana weizvi here? Mishonga yacho ndeipi?
Kwete, hapana mushonga weHemihyperplasia. Asi musazvidya mwoyo. Chikwata chevanachiremba vemwana wenyu chichagadzira hurongwa hwekurapa hunoenderana nezvaanoda uye zvichienderana nezviratidzo zvake.
Kurapwa kwehemihyperplasia mumwana kunoenderana nekusiyana kuripo pakati pemativi maviri emuviri. Chikwata chevanachiremba chemwana wako chinogona kusanganisira nyanzvi dzakadai se:
- Chiremba weHepatologist: Kune matambudziko ane chekuita nechiropa.
- Chiremba wemapfupa: Kune zvinhu zvakaita sehurefu hwemakumbo.
- Chiremba wepfungwa: Kune matambudziko ane chekuita neitsvo.
- Chiremba wepfungwa: Nezve tsinga.
- Chiremba wevana: Tarisa hutano hwemwana nekukura kwake.
- Chiremba wepurasitiki: Dzimwe nguva kugadzirisa shanduko dzechitarisiko.
Nyanzvi idzi dzese dzinoshanda pamwe chete kugadzira hurongwa hwekurapa mwana wenyu uye kutarisa nhengo dziri mudumbu remwana wenyu. Sezvo hemihyperplasia ichibatanidzwa nenjodzi yakawedzera yekenza, vanachiremba vanogara vachitarisawo zvirwere zvakaita sehepatoblastoma .
Mwana wacho achada kuvhiyiwa here?
Dzimwe nguva kuvhiyiwa kunogona kugadzirisa kusiyana kwehurefu hwemakumbo . Kune mhando dzakasiyana dzekuvhiyiwa kweizvi. Kana timu yevanachiremba ichikurudzira kuvhiyiwa, taura navo nezvekuti rudzii rwekuvhiyiwa rwakanakira mwana wako. Mwana wako anogona kunge aine:
- Kuvhiyiwa kwekurebesa ruoko/gumbo pfupi.
- Kuvhiyiwa kunodzora zvishoma kukura kwechigunwe chikuru/ruoko.
Pane matambudziko kana migumisiro yekurapwa here?
Kana mwana wako akavhiyiwa, anogona kunzwa aneta kwemavhiki mashoma achipora. Anogonawo kunzwa kurwadziwa panzvimbo pakachekwa. Bvunza chiremba wako nezvezvimwe migumisiro yekuvhiyiwa kwemwana wako.
Zvinotora nguva yakareba sei kuti munhu apore mushure mekuvhiyiwa?
Nguva yekupora inosiyana zvichienderana nerudzi rwekuvhiyiwa kwemwana wako. Unogona kuzvimba, kurwadziwa, uye kunzwa kusanzwa zvakanaka kwemazuva mashoma kana mavhiki mushure mekuvhiyiwa. Kana usingaoni kuvandudzika nekufamba kwenguva, taura nachiremba wemwana wako.
Mamiriro ezvinhu aya anogona kudzivirirwa here?
Hemihyperplasia, chirwere chinoitika netsaona panguva yekuzvitakura , hachigone kudzivirirwa . Zvisinei, mwana wako anogona kunge aine Beckwith-Wiedemann syndrome.Saka kana uine hemihyperplasia uye uchitarisira kuva nemumwe mwana, taura nachiremba wako nezvekuongororwa kwemajini . Kuongororwa uku kunogona kubatsira kuona kana vamwe vana vako vachavewo nezvirwere zvemachromosome zvisina kunaka.
Kana iwe kana mumwe wako muine nhoroondo yezvirwere zvemajini uye muri kufunga nezvekuva nemwana, zvakanaka kutaura nachiremba. Ungangodawo kufunga nezvemazano ekubatsira vana vasati vabata pamuviri .
Chii chandinofanira kutarisira kana mwana wangu aine hemihyperplasia?
Kana iwe kana mwana wako aine hemihyperplasia, kusaenzana kwehukuru hwenhengo dzemuviri kunogona kukonzera matambudziko . Semuenzaniso, zvinogona kuoma kuwana mbatya dzinokwana zvakanaka. Musiyano wehurefu hwemakumbo dzimwe nguva unogona kukanganisa zvinhu zvakaita sekukambaira, kufamba, uye kumhanya.
Uyewo, kana hemihyperplasia ikaonekwa, zvinoreva kuti mwana wako achada kuongororwa kenza nguva nenguva . Tarisira kuti bvunzo idzi dziitwe mwedzi mishoma yega yega kusvika mwana wako ava nemakore angangoita manomwe ekuberekwa.
Ndeipi tarisiro ye hemihyperplasia?
Hemihyperplasia chirwere chinogara kwenguva refu . Zvisinei, zvidzidzo zvakaratidza kuti kuonekwa nekukurumidza uye kuongororwa nguva dzose kwegomarara kunogona kuvandudza zvikuru tarisiro . Kunyangwe kana mwana anoongororwa nguva dzose akabatwa negomarara, rinogona kunge riri bundu diki uye danho rekutanga rechirwere. Kurapwa kunotanga, ndiko kunogona kubudirira.
Zvinokwanisika here kuva nehupenyu hwakajairika neHemihyperplasia?
Vana vazhinji vane hemihyperplasia vanorarama hupenyu hune hutano uye vane nguva yekurarama yakajairika . Kunyangwe zvichikosha kuongororwa kenza vachiri vadiki, njodzi yekenza iyi inoderera zvishoma nezvishoma mwana paanosvika pakukura.
Mibvunzo ipi yandinofanira kubvunza chiremba?
Kana mwana wako aine hemihyperplasia, ungave nemibvunzo yakawanda. Kuziva mhinduro dzemibvunzo iyi kuchakupa rugare rwepfungwa uye kuchakubatsira kugadzirira remangwana. Bvunza chiremba wemwana wako kana mukoti mibvunzo yakaita seyi:
- Chirwere chemwana wangu chinonzi hemihyperplasia here kana kuti chinoitika nguva nenguva?
- Sei muchikurudzira kurapwa uku kana kuvhiyiwa?
- Chii chandinofanira kuita kuti mwana wangu anzwe akasununguka asati avhiyiwa uye mushure mekuvhiyiwa?
- Mwana achafanira kugara muchipatara kwenguva yakareba sei?
- Rudzii rwekucheka ruripo, kana ruripo?
- Mwana achada mishonga here?
- Ndeipi njodzi dzekuvhiyiwa uye dzekushaya mushonga wekurwadziwa kwemwana?
- Zvinotora nguva yakareba sei kuti mwana apore mushure mekuvhiyiwa?
- Chii chandinofanira kutarisira nezveutano hwemwana wangu kwenguva refu?
Pamusoro pemibvunzo iyi, usatya kubvunza chiremba wako chero chauri kufunga nezvacho.
Pakupedzisira, meseji yekudzokera nayo kumba
Hemihyperplasia, inozivikanwawo sehemihypertrophy kana kuti overgrowth syndrome, chirwere chekuzvarwa nacho umo rumwe rutivi rwemuviri runokura kupfuura rumwe. Kusiyana uku kwekukura kungasaonekwa pakuzvarwa. Kana mwana wako akava nekusawirirana muhurefu hwemakumbo ake kana saizi yemuviri, taura nachiremba wevana. Sezvo chirwere ichi chichiwedzera njodzi yekenza, zvakakosha kuziva chirwere ichi nekukurumidza . Nekusatya, uye nekuwana mazano ekurapa anodiwa uye kurapwa, unogona kubatsira mwana wako kurarama hupenyu hune hutano.
Hemihyperplasia , Beckwith-Wiedemann syndrome, overgrowth syndrome, Wilms bundu, hepatoblastoma, congenital condition, utano hwemwana











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