Mwana wako ari kuita mapundu asingawanzoitika pamuviri wake here? Izvi zvinogona kuva chiratidzo cheComplex Lymphatic Anomalies (CLA)!

Dzimwe nguva tinotya zvikuru patinoona shanduko diki mumiviri yevana vedu, handiti? Kunyanya kana tisingazive chaizvo kuti zvinhu izvozvo chii. Nhasi tichataura nezvechirwere chisingawanzoitiki asi chakakosha zvikuru chekuziva. Izvi zvinonzi Complex Lymphatic Anomalies , kana kuti (CLA) muchidimbu. Vamwe vanhu vaizvitiwo (Lymphangiomatosis) kare. Saka unogona kunzwa mazita ese aya.

Kutanga, ngationei, chii chinonzi Complex Lymphatic Anomalies (CLA)?

Zvichitaurwa zviri nyore, Complex Lymphatic Anomalies (CLA) chirwere chisingawanzoitiki asi chinogona kuzvarwa nacho umo mwana anokura mabundu asina njodzi anonzi lymphatic malformations kana lymphangiomas mu lymphatic system yemwana. Mabundu aya anogona kukura kuita mapfupa emwana, connective tissue, nedzimwe nhengo dzemuviri, zvichikonzera kukuvara.

Chimbofungai, kunyangwe mwana wedu aine chirwere ichi paanozvarwa, kazhinji zviratidzo zvinotanga kuoneka paanokura zvishoma, pamwe makore mashoma gare gare. Ndosaka dzimwe nguva zvichinonoka kuzviona.

Saka, chii chinonzi Lymphatic System iyi?

Zvakanaka, ikozvino ungangove uchishamisika kuti lymphatic system chii. Zvichitaurwa zviri nyore, isystem inoshamisa yekudzivirira mumuviri wedu. Zvakafanana nemasoja ari munyika medu. Iyi lymphatic system inobatsira muviri wedu kudzivirira zvirwere uye kurwisa kana zvikaitika. Icho chikamu chakakosha cheimmune system yedu.

Sisitimu yelymphatic inoumbwa ne network yemachubhu madiki anonzi lymphatic vessels, glands dzakadai se lymph nodes, uye nhengo dzakadai se spleen. Iyi lymphatic vessels yakaita semachubhu madiki. Inounganidza lymph fluid kubva munyama yemuviri, yoisefa, yoichenesa, yozoidzosera muropa. Iri harisi basa rinoshamisa here?

Kune mhando mbiri dzeCLA: Isolated neSystemic.

Zvirwere zveLymphatic Complex zvinogona kukamurwa kuita mhando mbiri huru:

1. MaCLA Akaparadzaniswa: Apa ndipo apo mabundu anenge akavharirwa panzvimbo imwe chete yemuviri wemwana. Semuenzaniso, anogona kungokanganisa chipfuva chete. Panyaya iyi, mapapu nenyama dzakapfava dzechipfuva (mediastinum) ndizvo zvinonyanya kukanganiswa.

2. Systemic CLAs: Muchiitiko ichi, mapundu aya anogona kuitika munzvimbo dzakawanda pamuviri wemwana, dzakadai semapfupa, chipfuva, nedumbu.

Nenzira iyi, zviratidzo uye marapirwo zvinogona kusiyana zvichienderana nenzvimbo yakanganiswa.

Ndeapi marudzi makuru eComplex Lymphatic Anomalies (CLA)?

Kune mhando huru ina dzeCLA. Kunyangwe mhando imwe neimwe iine zvimwe zvezviratidzo zvakafanana, zvirwere zvakasiyana. Uye kushanduka kwemajini kunokonzera izvi kwakasiyanawo.

• Kusagadzikana kweLymphatic (GLA):Chirwere ichi chinowanzo kanganisa nhengo dzakasiyana dzemuviri wemwana. Semuenzaniso, mapundu aya anogona kuitika mumapfupa, spleen, chiropa, mapapu, uye nyama dzakapfava dzechipfuva (mediastinum).
• Kaposiform Lymphangiomatosis (KLA): Iyi ndiyo mhando yeCLA inonyanya kupararira uye inokurumidza. MuKLA, tsinga dzeropa dzinotakura lymph fluid mumuviri wemwana dzinokura. Izvi zvinoita kuti dzipinde nekukuvadza nhengo, mapfupa, uye nyama dzakamupoteredza.
• Central Conduction Lymphatic Anomaly (CCLA): Vana vane CCLA vanewo lymph vessels dzakakura. Zvisinei, muCCLA, midziyo iyi yakakura inowanikwa zvakanyanya mudumbu. Izvi zvinogona kukanganisa kugaya chikafu uye kudzivirira mwana kubvisa lymph fluid mumuviri wake zvakanaka.
• Chirwere cheGorham-Stout (GSD): Chinozivikanwawo sechirwere cheGorham, chirwere ichi chinoita kuti mapfupa akawanda anyungudike nekuda kwekuumbwa kwemidziyo ye lymphatic mukati memapfupa. Chinonziwo "chirwere chemapfupa chinopera." Chinogona kukanganisa chero pfupa. Zvisinei, vana vane GSD vanowanzo rasikirwa nemapfupa mumbabvu, dehenya, kora, uye musana wemuromo wechibereko.

Chirwere ichi cheCLA chakajairika zvakadii?

Zvirwere zveLymphatic Anomalies zvakaoma hazviwanzoitiki . Nekuti hazvina kujairika, dzimwe nguva zvinogona kuomera vanachiremba kuti vazviongorore nemazvo. Saka, kana uine zviratidzo, zvakakosha kuona nyanzvi nekukurumidza.

Chii chinokonzera CLA iyi?

Vanachiremba nevaongorori vachiri kuedza kutsvaga chinokonzera CLA. Zvisinei, tsvakiridzo yazvino inoratidza kuti chirwere ichi chinogona kukonzerwa nekuchinja kwemajini kunogarwa nhaka kunopfuudzwa kubva kuvabereki kuenda kuvana, pamwe nekuchinja kwemajini kunoitika mushure mekuzvarwa. Izvi zvinoreva kuti zvakabatana nemajini.

Ndiani ari panjodzi yekubatwa neCLA?

Zvirwere zveLymphatic Anomalies zvinogona kukanganisa chero munhu. Zvikurukuru, zviratidzo zvechirwere ichi zvinowanzoonekwa pazera rehudiki kana kuyaruka. Saka, kunyangwe chirwere ichi chiripo pakuzvarwa, zvinogona kutora nguva kuti zviratidzo zviratidzike.

Saka, zviratidzo zveCLA ndezvipi?

Zviratidzo zvinogona kusiyana kubva pamwana nemwana ane chirwere ichi. Zvakare, zviratidzo zvinosiyana zvichienderana nekuti nhengo ipi yemuviri inobatwa uye kuti yakanyanya sei. Kazhinji, chirwere ichi chinokura zvishoma nezvishoma. Nokudaro, tingasanyanya kutarisisa zvimwe zvezviratidzo, kana kuti tingafunga kuti zvinokonzerwa nechimwe chirwere.

Kana kufema kwemwana wako kwakanganiswa:

Panguva iyi, zviratidzo zvakafanana neasthma zvinogona kuoneka.

• Kukosora kunoramba kuripo.
• Kutadza kufema zvakanaka (dyspnea).
• Kufema ( kurira kwemuridzo ) kana uchifema.

Kana mapfupa emwana wako akakanganiswa:

• Kurwadziwa mumapfupa kana majoini.
• Kunyangwe kudonha kudiki kunogona kukonzera kutyoka .
• Kusanzwa simba mumakumbo.
• Marwadzo kana kushaya simba kunokonzerwa nekumanikidzwa kwetsinga .

Kana kugaya kwemwana wako kwakanganiswa:

• Kuzvimba kwedumbu uye kurwadziwa kwemudumbu .
• Kushaya ropa uye kuneta nguva dzose.
• Manyoka.
• Chikafu hachina kunaka.
• Kusvotwa nekurutsa.
• Kudzikira kwehuremu pasina chikonzero.

Kana weti yemwana wako yakakanganiswa:

• Ropa muweti (hematuria).
• Kurwadziwa kwepahuro.
• Kukwira kweropa muvana.

Kana mwana wenyu aine chimwe chezviratidzo izvi kana kupfuura, ndapota tsvagai mazano kuna chiremba. Izvi hazvisi zviratidzo zveCLA chete, asi zvakakosha kuti aongororwe.

Vanachiremba vanoongorora sei chirwere ichi cheCLA?

Nekuti CLA chirwere chisingawanzoitiki uye zviratidzo zvacho zvinosiyana, dzimwe nguva zvinogona kuoma kuti vanachiremba vaone chirwere chacho chaicho. Sezvo ichiwanzobata mapapu nemapfupa evana, chiremba wemwana wenyu anogona kuraira bvunzo dzakadai se:

• Bronchoscopy: Kuongorora hutachiona kana zvimwe zvinhu zvisina kumira zvakanaka munzira dzekufema.
• Kuongororwa kwebasa remapapu: Yera kuti mapapu ako ari kushanda zvakanaka sei.
• MRI yemuviri wese: Kuongorora zvinhu zvakaita senhengo dzakabatwa, maronda emapfupa, kana mvura iri mudumbu.
• X-rays: Kuongorora mapfupa anoita seanofungirwa kana kuti akakuvara paMRI. X-rays dzepachipfuva dzinogonawo kutsvaga kusarongeka mumapapu.

Dzimwe nguva vanachiremba vanotora sampuli diki yema lymph nodes nenyama (biopsy) voiongorora vachishandisa maikorosikopu. Kunyange zvazvo bvunzo iyi ichigona kunyatsoongorora CLA, dzimwe nguva inogona kukonzera matambudziko, akadai sekuunganidzwa kwe lymph fluid yakakomberedza mapapu (chylothorax). Nekuda kweizvi, vanachiremba vanowanzo vimba nebvunzo dzisinganyanyi kupindira kuti vaone kana paine chirwere.

CLA inorapwa sei?

Nekuti CLA inogona kukanganisa nzvimbo dzakawanda dzemuviri wemwana, vanachiremba vanoshanda pamwe chete, kureva kuti, vanoshandisa nzira dzakasiyana-siyana kuronga kurapwa kwakakodzera mwana. Pakurapa CLA, chinangwa chikuru ndechekudzora zviratidzo zvemwana. Kuti uite izvi, unogona kuita zvinhu zvakaita se:

• Kubatanidza mapfupa: Kukuvadza mapfupa mumamiriro ezvinhu akaita seGSD.
• Kudya zvine mapuroteni akawanda kana kudya kunovaka muviri netsinga (total parenteral nutrition kana TPN).
• Kurapa neSclerotherapy: Kuderedza kana kudzima bundu kana midziyo ye lymph.
• Kuvhiyiwa: Kubvisa bundu kana kuisa machubhu madiki (shunts) kuti mvura yelymph ifambe zvakanaka.
• Kurapwa nemwaranzi kana chemotherapy: Kuderedza bundu risiri rekenza (izvi zvinongoshandiswa chete muzviitiko zvakakomba, zvinoisa hupenyu pangozi).

Munguva pfupi yapfuura, mishonga yakanangana nekuchinja kwemajini kunokonzera chirwere ichi yakashandiswawo. Mishonga iyi yakaratidzwawo kuti inoshanda senzira yekutanga yekurapa CLA.

Ko Complex Lymphatic Anomalies (CLA) inogona kudzivirirwa here?

Zvinosuwisa kuti hapana . CLA inoitika panguva yekuzvitakura, uye chikonzero chaicho hachizivikanwe. Saka, hapana chawaigona kuita kudzivirira mwana wako kubva pakuva nechirwere ichi.

Ndezvipi zvinetso zvinogona kuitika nekuda kweCLA?

CLA inogona kuisa mwana wako panjodzi ye:

• Ascites: Kuungana kwemvura mudumbu.
• Kutyoka kwemapfupa.
• Chylothorax neChylopericardium: Muunganidzwa wemvura yakaita semukaka (chyle) ine mvura yelymph nemafuta ari mumembrane inofukidza mapapu (pleura) kana saga rakatenderedza moyo (pericardium).
• Mapapu akaputsika / pneumothorax.
• Kukundikana kwechiropa.
• Kuoma mitezo.
• Kubuda kweropa mumoyo.
• Kubuda kweropa muropa uye kuzvimba kwemapapu emwoyo.

Mamwe ematambudziko aya anogona kunge akakomba zvikuru, saka zvakakosha kuziva zviratidzo uye kutevedzera mirairo yachiremba wako.

Ramangwana remunhu ane CLA nderei?

Hapana mushonga weComplex Lymphatic Anomalies (CLA). Remangwana remwana wako rinoenderana nekuti ndeapi masisitimu emuviri akanganiswa uye kuti zviratidzo zvacho zvakakomba sei.

Kubuda kweropa muropa (pleural effusions) ndiko kunonyanya kukonzera rufu pakati pevanhu vane CLA. Zvisinei, kana mwana akarapwa zvakanaka uye akatarisirwa zvakanaka, anogona kubatsirwa kurarama hupenyu hwakajairika.

Ndinofanira kuona chiremba rini?

Kana mwana wako aine chimwe chezviratidzo izvi, enda kuna chiremba nekukasika:

• Kurwadziwa mudumbu kana muura.
• Kana ropa riri muweti.
• Kukosora nguva dzose, kufemereka, kana kuoma kufema.
• Kuda kurutsa, kuneta, kana kudzikira kwehuremu kusingatsananguriki.

Kana uine chimwe cheizvi, ndapota ona chiremba nekukurumidza.

Chii chandinofanira kubvunza chiremba?

Ungada kubvunza chiremba wemwana wako mibvunzo yakaita seiyi:

• Ndedzipi nhengo dzemuviri wemwana wangu dzakakanganiswa nechirwere ichi?
• Ndezvipi zvirongwa zvekurapa zviripo kumwana wangu?
• Mwana wangu anofanira kuvhiyiwa here?
• Ndinofanira kuziva zviratidzo zvematambudziko here?

Zvakakosha kubvunza mibvunzo iyi uye kunzwisisa mamiriro acho ezvinhu zvakajeka.

Pakupedzisira, ndinofanira kutaura kuti...

Kana ukaona kuti mwana wako ane CLA (lymphangiomatosis), zvakajairika kuti unzwe kutya uye kunetseka kuti zvichakanganisa sei hutano hwake neramangwana rake. Vazhinji vedu tinogona kunge tisina kumbonzwa nezvechirwere ichi. Uye hapana chaungadai wakaita kuti uchidzivirire.

Danho rekutanga rekubatsira mwana wako nderekuziva nezvechirwere ichi, zviratidzo zvacho, uye marapirwo acho. Ona chiremba ane hunyanzvi muzvirwere zve lymphatic system. Vanogona kupindura mibvunzo yako uye kupa rubatsiro rwekurapa rwaunoda.

Kunyange hazvo pasina mushonga weCLA, kurapwa kwakakodzera uye kutarisirwa zvakanaka kunogona kubatsira mwana wako kurarama hupenyu hunofadza uye hune hutano. Saka, ramba wakasimba uye ita zvese zvaunogona kuti mwana wako ararame.

` Zvirwere zveLymphatic Zvakakomba, Lymphangiomatosis, Zvirwere zveLymphatic System, Mabundu eVana, Osteomalacia, Zviratidzo zvePulmonary, Zvirwere Zvisingawanzoitiki zveVana