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Une chirwere ichi chinoshamisa here? Ngatikurukurei nezve Microscopic Polyangiitis (MPA)

Une chirwere ichi chinoshamisa here? Ngatikurukurei nezve Microscopic Polyangiitis (MPA)

Unowanzo nzwa kuneta, kuva nefivha isingatsananguriki, uye kudzikira uremu nekuda kwekurwadziwa kwemajoini here? Kunyangwe izvi zvingaita sezvinhu zvakajairika, dzimwe nguva zvakavanzika kuseri kwezviratidzo izvi zvingave chirwere chatisati tanzwa zvakawanda nezvacho uye chatinofanira kunetseka nacho. Nhasi tiri kutaura nezvechirwere chisingawanzoitiki asi chakakosha chatinofanira kuziva. Ichi chinonzi microscopic polyangiitis, kana MPA sekudanwa kwachinoitwa navanachiremba.

Zvichitaurwa zviri nyore, chii chinonzi Microscopic Polyangiitis (MPA)?

Zvichitaurwa zviri nyore, MPA chirwere apo mitsipa midiki nepakati (mitsipa yeropa) mumuviri wedu inozvimba, kureva kuti, kuzvimba. Mukurapa, tinowanzodaidza kuzvimba kwemitsipa yeropa kuti 'vasculitis'. Ichi chirwere chisingawanzoitiki.

Kana tsinga dzeropa dzikazvimba nenzira iyi, dzinotanga kukuvadza nhengo dzadzinopa ropa. Nhengo huru dzinogona kukanganiswa neMPA ndeidzi:

  • Itsvo
  • Mapapu
  • Tsinga
  • Ganda
  • Majoini (majoini)

Chii chinonzi 'Vasculitis'? Chinokonzera chii?

Funga nezvehurongwa hwemitsipa yeropa mumuviri wedu wese sehurongwa hwemapaipi anotakura mvura. Kana mapaipi aya achizvimba kana kuzvimba, matambudziko akati wandei anogona kuitika.

1. Kushaya simba kwetsinga yeropa: Nekuda kwekuzvimba, madziro etsinga yeropa anoshaya simba uye anogona kuzvimba sebharumu. Tinodaidza izvi kuti ``(Aneurysm)``. Dzimwe nguva nzvimbo iyi isina simba inogona kuputika nekubuda ropa munyama yakapoteredza.

2. Kutetepa kwetsinga dzeropa: Chimwe chinhu ndechekuti tsinga dzeropa dzinogona kutetepa nekuda kwekuzvimba mukati madzo, uye dzimwe nguva kutovharika zvachose. Ipapo nhengo dzinogamuchira ropa neokisijeni kubva mutsinga idzodzo dzeropa dzinotanga kukuvara. Kungofanana nemuti unofa kana ukashaiwa mvura.

Ndizvo zvinoitika muMPA. Nekuti tsinga diki dzeropa dzinokanganiswa, dzinokuvadza nhengo dzinonzwa dzinopa ropa, dzakadai seitsvo nemapapu.

Ndiani anowana chirwere ichi? Chii chinokonzera?

Ichi chirwere chisingawanzoitiki. Zvichienderana nehuwandu, chirwere ichi chinobata vanhu vari pakati pe13 ne19 pamamiriyoni ega ega pasi rose. Chinogona kukura pazera ripi zvaro uye chinoita sechinobata varume nevakadzi zvakaenzana.

Chikonzero chaicho chechirwere ichi hachisati chawanikwa, asi izvi zviri pachena:

  • Iyi haisi kenza.
  • Haisi chirwere chinotapuriranwa.
  • Kazhinji hachisi chirwere chinogara nhaka.

Tsvagiridzo yakaratidza zvakanyanya kuti ichi chirwere chinokonzerwa nekusashanda zvakanaka kwemasoja emuviri wedu. Zvichitaurwa zviri nyore, masoja emuviri, ayo anofanirwa kuchengetedza muviri wedu, anotanga kurwisa mitsipa yeropa yedu zvisirizvo. Ndizvo zvinokonzera kuzvimba uku.

Ndezvipi zviratidzo zvechirwere cheMPA?

Nekuti MPA inokanganisa nhengo dzakasiyana-siyana dzemuviri, zviratidzo zvinogona kusiyana zvakanyanya, uye zvinogona kusiyana kubva pamunhu kusvika pamunhu.

Chikamu chakabatwa Zviratidzo zvinogona kuitika
Zvinhu zvakajairika Kuneta, fivha, kushaya chido chekudya, kudzikira kwehuremu, kurwadziwa kwetsandanyama nemajoini.
Mapapu Kutadza kufema zvakanaka, kukosora ropa.
Tsinga Manzwiro asina kujairika (sekunge kuvhundutswa nemagetsi, masvosve achimhanya-mhanya), zvichiteverwa nekusanzwa simba, kurasikirwa nesimba.
Ganda Mavara matsvuku kana epepuru paganda (mapundu).
Itsvo Apa ndipo pane njodzi. Kana itsvo dzabatwa , kazhinji hapana zviratidzo zvinoonekwa pakutanga. Unogona kusatombozviona kusvika itsvo dzako dzatanga kumira kushanda.

Sezvo chirwere cheitsvo chichigona kuitika pasina zviratidzo, zvakakosha zvikuru kuti weti yemunhu wese anofungidzirwa kuti ane vasculitis iongororwe.

Chiremba anoongorora sei chirwere ichi?

Kuongorora chirwere cheMPA hakusi danho rimwe chete. Chiremba anofanira kusanganisa zvinhu zvakawanda kuti asvike pachinangwa chake.

  • Uchabvunzwa ruzivo rwakadzama: Chiremba achanyatsoteerera zviratidzo zvako, kuti zvakatanga sei, uye nhoroondo yako yehutano.
  • Kuongororwa kwemuviri: Chiremba wako achaongorora muviri wako kuti aedze kuona kuti ndeapi nhengo dziri kukanganiswa.
  • Kuongororwa kweropa neweti: Kuongororwa kweropa kunotsvaga mushonga unonzi ``(ANCA - Antineutrophil Cytoplasmic Antibodies)``. Izvi zvinogona kuva zvakanaka muzvirwere zvakaita seMPA. Zvakare, kutarisa weti kuti ione kana paine mapuroteni nemasero matsvuku eropa kwakakosha kuti uzive mamiriro eitsvo.
  • Kuskena: X-ray, CT scans, kana MRI scans zvinoshandiswa kutarisa kusarongeka kwenhengo dzemuviri dzakadai semapapu.
  • Kuongororwa kweropa: Kana chirwere ichi chikafungidzirwa, kanyama kadiki kanotorwa kubva panzvimbo yakakanganiswa (semuenzaniso, itsvo, ganda) koongororwa nemaikorosikopu. Iyi ndiyo nzira yakanakisisa yekusimbisa kana uine vasculitis.

Kungoonekwa kuti une chirwere ichi kana waongororwa neANCA hazvirevi kuti une chirwere ichi. Izvi zvinongobatsira pakuongorora chirwere chacho. Kuti zvive pachena, kuongororwa kweropa kunowanzo dikanwa.

Ndeapi marapirwo eMPA?

Chinangwa chikuru chekurapa MPA ndechekudzora kushanda kwakanyanya kwemasoja emuviri wedu uye kumisa kukuvara kwetsinga dzeropa. Mishonga inodzvinyirira masoja emuviri inoshandiswa pakuita izvi.

Kana chirwere chacho chakanyanya

Kana nhengo huru dzakadai seitsvo nemapapu dzikabatwa zvakanyanya, corticosteroids inowanzopihwa pamwe chete nemumwe mushonga wakasimba wekudzivirira muviri wakaita seCyclophosphamide (Cytoxan®) kana Rituximab (Rituxan®).

Kana chirwere chisina kunyanya kuipa

Muzviitiko zvisina kunyanya kuoma, corticosteroids ne methotrexate zvinogona kutanga zvashandiswa.

Chinangwa chekurapa ndechekudzora chirwere chose uye kuchiisa mumamiriro ezvinhu ekusaita chimwe chinhu. Izvi zvinonzi kuenda ku 'remission'. Kana chirwere changodzorwa, chiremba anoderedza zvishoma nezvishoma mushonga wemishonga inorwisa mabhakitiriya.

Mishonga yakasimba yakaita se'Cyclophosphamide' inongopihwa kusvika chirwere chapera simba (inenge mwedzi 3-6). Mushure meizvozvo, unochinjwa kuenda ku'Maintenance Medication', yakaita se'Azathioprine (Imuran®)` kana 'Mycophenolate Mofetil (Cellcept®)`, kuti chirwere chirambe chiri pasi pesimba uye chisadzoke. Kurapa uku kunogona kudiwa kweinenge gore rimwe kana maviri.

Unotyawo here kutaura kuti, "Iyi mishonga yekenza, handiti?"

Vanhu vazhinji vane mubvunzo pano. Mishonga inonzi `Cyclophosphamide` ne`Methotrexate` inopihwawo yegomarara, saka vanoti iyi mishonga ye`Chemotherapy`. Ehe, iyi inopihwawo yegomarara. Asi dose inopihwa ye`Vasculitis` yakaderera ka10-100 pane dose inopihwa yegomarara. Pano, basa remishonga iyi harisi rekuuraya masero egomarara, asi kudzora mashandiro emuviri.

Nekuti mishonga iyi inodzvinyirira masoja emuviri, pane mukana wekutapukirwa nezvirwere zvakakomba. Zvakare, mushonga wega wega unogona kuva nemigumisiro yakaipa. Saka, zvakakosha zvikuru kuongororwa nenguva uye kugara uchitariswa nachiremba, sezvakarairwa nachiremba.

Hupenyu huchava hwakaita sei nechirwere ichi?

Kunyange hazvo MPA iri chirwere chakakomba, kana ikarapwa zvakanaka, vanhu vazhinji vanogona kudzora chirwere ichi zvinobudirira. Zvinobuda zvinosiyana zvichienderana nekuti chirwere chacho chakakomba sei. Zvisinei, kazhinji, vanhu vanopfuura 80% vapenyu uye mushure memakore mashanu ekuonekwa vaine chirwere ichi.

Kuonekwa nekukurumidza uye kurapwa nekukurumidza kunogona kubatsira kuderedza kukuvara kwenhengo dzemuviri. Zvakakoshawo kugara uchionana nachiremba wako.

Kana chirwere chacho chapera simba, kureva kuti, mushure mekunge chatanga kurapwa ne "Remission", dzimwe nguva chinogona kudzoka. Tinoti izvi "Relapse". Varwere vanosvika 50% vanodzokera kuchirwere ichi. Saka, unofanira kuzivisa chiremba wako nekukurumidza nezvezviratidzo zvitsva zvaunowana.

Mharidzo Yekuenda Nayo Kumba

  • MPA chirwere chisingawanzoitiki umo masoja edu emuviri anorwisa mitsipa yeropa.
  • Izvi zvinogona kukuvadza nhengo dzinokosha dzakadai seitsvo, mapapu, uye tsinga. Kunyanya kana itsvo dzabatwa, panogona kunge pasina zviratidzo pakutanga.
  • Kuongororwa nekukurumidza uye kurapwa kunogona kudzivirira kukuvara kwenguva refu.
  • Nekuti mishonga inodzvinyirira masoja emuviri inoshandiswa pakurapa, zvakakosha kuti urambe uri pasi pekutarisirwa nachiremba uye uzvidzivirire kubva kuzvirwere.
  • Kunyangwe chirwere ichi chikadzorwa, pane mukana wekuti chidzoke zvakare. Saka, kana ukaona zviratidzo zvitsva, kunyangwe zvidiki, taurira chiremba wako nekukasika.

Microscopic Polyangiitis, MPA, Vasculitis, Vasculitis, Kuzvimba kweMitsipa yeRopa, Chirwere cheItsvo, ANCA
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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