Makumbo emwana wako anozvimbawo here? Izvi zvinogona kunge zviri chirwere chaMilroy!

Wakamboona here kuti makumbo emwana wako, kunyanya pasi pemabvi, anozvimba chete? Dzimwe nguva izvi zvinogona kuonekwa mushure mekuzvarwa. Kana kuti zvinogona kuonekwa mushure memazuva mashoma. Zvakajairika kuti vabereki vazhinji vazvidye mwoyo nezveizvi. Chimwe chikonzero cherudzi urwu rwekuzvimba mumakumbo chinonzi chirwere chaMilroy. Nhasi, tichataura nezvazvo zvakadzama, zviri nyore.

Chii chinonzi chirwere chaMilroy?

Zvichitaurwa zviri nyore, chirwere chaMilroy chirwere chiri muboka rezvirwere zvinonzi primary lymphedema . "Primary" zvinoreva kuti hachikonzerwi nechimwe chirwere, kuti chinoitika chega. Idambudziko rekuzvarwa naro , zvichireva kuti dambudziko racho rinogona kuvapo pakuzvarwa. Idambudziko remajini , zvichireva kuti rinogarwa nhaka.

Muviri wedu une sisitimu inonzi lymphatic system. Izvi zvakafanana nesystem yekubuditsa mvura inobvisa tsvina mumuviri wedu. Kana nzira dze lymphatic uye lymph nodes dziri musystem iyi ye lymphatic dzisina kugadzirwa zvakanaka, hadzigoni kushanda zvakanaka. Zvadaro, lymph fluid haifambi zvakanaka uye inoramba iri panzvimbo imwe chete. Aya ndiwo maitiro anoita lymph fluid uye inokonzera kuzvimba mumakumbo evana, kunyanya makumbo epasi netsoka. Fungidzira chimwe chinhu chakaita sepaipi yemvura painovharika, mvura inozara panzvimbo imwe chete.

Rimwe zita rechirwere cheMilroy inhaka yelymphedema rudzi rwekutanga.

Kuziva chirwere ichi dzimwe nguva kunogona kuoma zvishoma, nekuti vanachiremba havawanzoona varwere vakadai. Asi kana ukaona makumbo emwana wako akazvimba, zvakakosha kubvunza chiremba wako nezvazvo. Nekuti kana ukakurumidza kuona chirwere chacho, ndipo paunotanga kurapwa nekukurumidza. Zvakakoshawo kuti usatye.

Chirwere chaMilroy hachiwanzoitiki kangani?

Ichi chirwere chisingawanzoitiki . Chinobata mwana mumwe chete pavana 6,000 vanoberekwa. Chinowanzoitika kuvasikana kupfuura vakomana. Zvinonzi pavakomana vese vane chirwere ichi, pane vasikana vaviri.

Ndezvipi zviratidzo zvechirwere chaMilroy?

Mwana wako anogona kunge aine zviratidzo izvi kubva pakuzvarwa. Dzimwe nguva zvinogona kuoneka gare gare. Tarisa kuti uone kana mwana wako aine zviratidzo izvi:

• Kuzvimba mumakumbo ezasi (edema): Kuzvimba uku kunowanzoonekwa pasi pemabvi. Dzimwe nguva kunogona kuitika mugumbo rimwe chete, asi kazhinji kunoitika mune ese ari maviri.
• Kuzvimba kwetsinga dzemumakumbo epasi: Dzimwe nguva, nekuzvimba, tsinga dzinoonekwa zvakajeka.
• Kuzvimba kwemachende (hydrocele): Machende evakomana anogona kuzvimba ozadzwa nemvura. Izvi zvinogona kutyisa vabereki, asi zvinogonawo kuva chiratidzo chechirwere.
• Nzara dzezvigunwe dzakakotama mudenga:Chimiro chenzara chinogona kuchinja uye kuita sechakataridzwa mudenga.
• Mapundu madiki eganda (papillomatosis): Aya haasi mamiriro egomarara, asi anogona kuoneka semapundu madiki paganda, dzimwe nguva akafanana nekakoliflawa kadiki.
• Matambudziko emudumbu: Vamwe vacheche vanogona kusangana nedambudziko remudumbu, kurutsa, uye manyoka. Izvi hazviitiki kune wese munhu, asi zvinogona kuitika.

Ndezvipi zvinokonzera chirwere chaMilroy?

Chikonzero chikuru chechirwere chaMilroy imutation (variant) mu gene inonzi FLT4 . Majini akafanana nemirairo midiki inodzora zvese zviri mumuviri wedu. Jini iri reFLT4 rinobatsira lymphatic system kuti iumbwe zvakanaka. Saka kana paine shanduko diki mu gene iri, kureva mutation, lymphatic system haiumbwe zvakanaka.

Kazhinji, mumwe wevabereki vane chirwere cheMilroy ane chirwere ichi. Chinogarwa nhaka nenzira inotonga autosomal . Izvi zvinoreva kuti mwana anogona kuva nechirwere ichi kunyangwe mubereki mumwe chete ane gene rechirwere ichi. Semuenzaniso, kana vabereki vese vaine gene mutation, mwana wega wega ane mukana we50% wekugara nhaka chirwere ichi. Kunyangwe pakati pehama nehanzvadzi dziri mumhuri imwe chete, kuoma kwezviratidzo, kana zera rinoonekwa zviratidzo, zvinogona kusiyana. Mwana mumwe anogona kuzvimba zvakanyanya, nepo mumwe angave asina kuzvimba zvakanyanya.

Vana vapfumbamwe pavana gumi vane chirwere cheFLT4 gene mutation vanoratidza zviratidzo zvekuzvimba kwemakumbo pavanosvika makore matatu .

Chirwere ichi chinoonekwa sei?

Chirwere chaMilroy chinoonekwa nekuongororwa kwemuviri nachiremba . Chiremba achanyatsoongorora makumbo emwana kuti aone kana aine zviratidzo zvekuzvimba, kuchinja kweganda, uye chimiro chenzara. Pamusoro pezvo, bvunzo dzinotevera dzinogona kuitwa:

• Ultrasound: Uku kuongorora dumbu raamai panguva yekuzvitakura kunogona dzimwe nguva kuratidza kana paine kuzvimba mumakumbo emwana. Kunogonawo kuitwa pamakumbo mushure mekunge mwana aberekwa.
• Lymphoscintigraphy: Iyi bvunzo yakasarudzika zvishoma. Mubvunzo uyu, huwandu hushoma hwezvinhu zvine mwaranzi hunoiswa pasi peganda uye kamera inoshandiswa kuiona ichifamba nemuhurongwa hwe lymphatic. Izvi zvinogona kuratidza mashandiro ari kuita lymphatic system uye kana paine chakavharika.
• Kuongororwa kwemajini: Izvi zvinobatsira kusimbisa kana paine shanduko mujini reFLT4. Izvi zvinowanzo sanganisira kutora ropa.

Chiremba wemwana wenyu anogonawo kukutumirai kuna chiremba wezvirwere zve lymphedema ane certification yevana, uyo ane hunyanzvi mukurapa zvirwere izvi.

Chirwere chaMilroy chinorapwa sei?

Kune mishonga yekumba yekuzvimba kunokonzerwa nechirwere ichi. Mishonga iyi yakagadzirirwa kudzora kuzvimba, kuderedza matambudziko, uye kuvandudza hupenyu hwemwana. Mishonga yeMilroy's disease yemakumbo akazvimba inosanganisira:

• Kurapa kwekudzvanya: Kushandisa masokisi kana mabhandeji akakosha ekudzvanya. Izvi zvinoisa kudzvanya zvinyoro nyoro pamakumbo kuderedza kuzvimba uye kubatsira lymph fluid kuti idzokere mumuviri.
• Kinesiology tape (KT tape): Iyi itepi inonamira inoshandiswa nevatambi. Dzimwe nguva inogona kubatsira kuderedza kuzvimba nekukurudzira kuporesa.
• Shangu dzinotsigira: Zvakakosha kupfeka shangu dzinokwana zvakanaka, dzinotsigira, uye dzisingabati.

Kazhinji, kurapwa uku kuri nyore kunokupa mhedzisiro yakanaka. Kana zvikasashanda, unogona kuedza lymphatic drainage massage . Iyi inzira yekukwiza zvinyoro nyoro inoitwa nenyanzvi yekurapa yakadzidziswa. Inobatsira kubvisa lymph fluid munzvimbo dzakavharika uye kuibvumira kuti ibude mvura zvakanaka. Chiremba anogona kuita izvi, kana kuti unogona kudzidziswa maitiro ekuzviita kumba.

Kana nzira idzi dzisingashande, chiremba wako anogona kukurudzira kuvhiyiwa kuti abatsire mwana wako kushanda zvakanaka kwe lymphatic system. Zvisinei, izvi zvinowanzoonekwa senzira yekupedzisira. Izvi zvinogona kusanganisira:

• Kubvisa nyama yakakanganisika.
• Kushandisa nzira yekubvisa ropa kuti mvura yelymph iendeswe kunzvimbo dziri nani: Zvakafanana nekugadzira nzira itsva inotenderera mugwagwa wakavharwa.
• Kuisa ma lymph nodes ane hutano kubva kune imwe nzvimbo mumuviri wemwana kuenda kumakumbo. Izvi zvinonzi vascularized lymph node transfer .

Kana mwana wangu aine chirwere ichi, chii chandinofanira kutarisira?

Nekuti chirwere chaMilroy chirwere chisingawanzoitiki, ungangoda kuchitsanangura kuvadzidzisi vemwana wako kana vamwe vanhu vari muhupenyu hwemwana wako. Semuenzaniso, kana mwana wako akakuvara patsoka kuchikoro, zvinogona kunge zvakakomba kupfuura zvingaita kune mumwe mwana, uye pane mukana wakakura wekutapukirwa. Kutaura nezveizvi kunogona kubatsira mudzidzisi kunzwisisa kuti sei mwana wako achitora nguva yakareba achichinja mbatya mukirasi yejimu, kana kuti nei zvine njodzi kusapfeka shangu (nekuda kwenjodzi yekukuvara nekutapukirwa). Asi usazvidya moyo, mwana wako anogona kuita zvinhu zvakawanda zvinoitwa nevamwe vana vari mukirasi yake.

Chirwere chaMilroy chirwere chisingaperi, zvinoreva kuti chirwere chinotora nguva refu. Kuzvimba mumakumbo kunogona kuwedzera zvishoma nezvishoma mune vamwe vanhu, uye kuderera zvishoma mune vamwe. Kana zvikasarapwa, kuzvimba uku kunogona kukonzera kuti nzvimbo yakabatwa iome uye iome sedombo. Uyewo, vanhu vane chirwere ichi vanogona kuwana chirwere cheganda chinonzi cellulitis . Ichi chirwere chinoita kuti ganda ritsvuke, ripise, uye rirwadze. Ichi chirwere chine njodzi chinogona dzimwe nguva kupararira muropa. Saka, zvakakosha kuudza chiremba kunyangwe ukaona shanduko diki paganda rako.

Ndingatarisira sei mwana wangu?

Heano mamwe maitiro aungaita kuti utarisire mwana wako ane chirwere chaMilroy:

• Chengetedza ganda remwana wako zvakanaka. Chengeta ganda remakumbo rakachena zuva rega rega, omesa zvakanaka, uye isa moisturizer. Rapa chero kukuvara kudiki, mavanga, kurumwa nezvipembenene, kana hutachiona nekukurumidza. Izvi zvinogona kubatsira kuderedza njodzi yekuva nezvirwere zvakaita se cellulitis.
• Edza kudzivirira kukuvara tsoka dzako. Pfeka mbatya dzinofukidza tsoka dzako paunenge uchitamba, uchimhanya, kana uchisvetuka. Usavarega vachifamba panze vasina shangu. Vana vane chirwere cheMilroy vanogona kubatwa nezvirwere kupfuura vamwe.
• Musarega makumbo emwana wenyu achigara panzvimbo imwe chete, fambai nguva nenguva. Kurovedza muviri zvishoma uye kusimudza nekudzikisa makumbo kunogona kubatsira kuderedza kuzvimba.
• Kurudzira kurovedza muviri, kunyanya kushambira. Kumanikidzwa kwemvura kunobatsira kuzvimba. Zvakare, maekisesaizi anonyorovesa pamapfundo, akadai sekufamba netsoka nebhasikoro, akanaka.
• Bvunza chiremba wako usati wapa mwana wako chero mushonga. Mimwe mishonga, semuenzaniso, mimwe inoderedza marwadzo, inogona kuwedzera kuzvimba.
• Deredza huwandu hwemunyu muchikafu chako. Munyu unowedzera kuchengetwa kwemvura mumuviri, izvo zvinogonawo kuwedzera kuzvimba.
• Ipa mwana wako chikafu chinovaka muviri. Kudya miriwo, michero, uye mapuroteni asina mafuta akawanda kunobatsira kuona kuti mwana wako anowana zvinovaka muviri zvaanoda.

Mwana wangu anofanira kuona chiremba rini?

Mwana ane chirwere chaMilroy achaongororwa nguva nenguva . Izvi zvinoita kuti chiremba aone kuti mwana ari sei, kuti kuzvimba kuri sei, kana kurapwa kuri kushanda, uye kana mamiriro acho ari kuramba akafanana kana kuti ari kuwedzera kuipa. Kana uchifunga kuti kurapwa hakusi kubatsira, kana kuzvimba kwegumbo remwana wako kuri kuwedzera, kana kuri kutsvuka, kana kuchipisa, kana kana mwana wako aine fivha, iva nechokwadi chekutaura nachiremba wemwana wako. Dzimwe nguva mwana wako angangoda kuona chiremba wezvemabasa kuti amubatsire kushandisa makumbo ake zviri nyore uye kuita mabasa ezuva nezuva.

Mibvunzo ipi yandinofanira kubvunza chiremba wemwana wangu?

Heano mimwe mibvunzo yaunogona kubvunza chiremba wemwana wako:

• "Pane mumwe munhu mumhuri medu ari panjodzi yekubata chirwere ichi here? Tinofanira kutsvaga mazano ezvemajini here?"
• "Munoziva mapoka anotsigira vanhu vane chirwere chaMilroy here? Kune mapoka akadaro here muSri Lanka?"
• "Ndingasarudza sei mbatya dzekudzvanya dzakakodzera mwana wangu? Ndingadziwana kupi?"
• "Sezvawakaona, kurapa kuri nyore uku kunobudirira zvakadii? Papi patinofanira kufunga nezvekuvhiyiwa?"
• "Ndezvipi zvinhu zvakakosha zvaunofanira kuita kuti udzivirire ganda remakumbo emwana wako?"

Kuva nemwana ane chirwere chaMilroy hakuna kufanana nekuva nemwana ane chirwere chakajairika. Danho rekutanga mukutarisira mwana wako nderekudzidzisa iwe nevamwe nezvechirwere ichi. Dzidza zvakawanda sezvaunokwanisa nezvazvo, uye usatya kubvunza mibvunzo yechikwata chevanachiremba vemwana wako. Hausi wega, uye kune vanhu vazhinji vanogona kubatsira.

Zvinhu zvakakosha zvatinofanira kurangarira (Mharidzo Yekuenda Kumba)

Zvakanaka, ngatidzokororei pfungwa dzakakosha kubva pane zvatataura nezvazvo:

• Chirwere chaMilroy chirwere chinogona kuvapo pakuzvarwa uye chinokonzerwa nezvinhu zvemajini zvinokanganisa mashandiro ehurongwa hwe lymphatic, zvichikonzera kuzvimba kwemakumbo.
• Izvi hazviwanzoitiki , asi zvakakosha kutsvaga rubatsiro rwechiremba kana makumbo emwana wako akazvimba. Kuongororwa kwechirwere nekukasika uye kurapwa kwakakosha zvikuru.
• Nzira dzekurapa dzinosanganisira masokisi ekudzvanya, matepi akakosha, kukwiza lymphatic drainage massage, uye dzimwe nguva kuvhiyiwa.
• Sezvo chirwere ichi chiri chirwere chisingaperi , zvakakosha kutarisira mwana zvakanaka, kutarisira ganda rake, kumudzivirira kubva kuzvirwere, uye kumuchengeta ari pasi pekutarisirwa kwakakodzera nachiremba.
• Musazvidya mwoyo. Nekuziva zvakanaka nezvechirwere ichi uye kushanda navanachiremba venyu, mwana wenyu anogona kubatsira zvikuru pakurarama hupenyu hwakanaka.

Kana muine mimwe mibvunzo nezveizvi, iva nechokwadi chekutaura nachiremba wemhuri yenyu kana chiremba wevana.

` Chirwere chaMilroy, Sisitimu yeLymphatic, Kuzvimba kweMakumbo muVana, Lymphedema, Zvirwere zveKuberekwa, Zvirwere zveMajini, Kurapa