Matumbu anogona kukura here patsinga dzako? Ngatikurukurei nezveMatumbu eMutsinga muNerve Sheath nenzira iri nyore!

Tsinga dzinofamba mumiviri yedu dzakafanana netambo yewaya dzinotakura mashoko emagetsi. Ndidzo dzinotakura mashoko kubva kuuropi kuenda kumuviri wese, uye kubva mumuviri kuenda kuuropi. Fungidzira kuti masero aya etsinga, mapoka awo, ese akaputirwa nemamembrane anodzivirira, sepurasitiki yakakomberedza waya, kuti adzidzivirire uye abatsire masaini emagetsi kufamba nekukurumidza. Mumamembrane aya anodzivirira dzimwe nguva mabundu aya anonzi etsinga anokura.

Chii chinonzi Nerve Sheath Tumors?

Zvichitaurwa zviri nyore, mapundu aya anoumbwa mu "masheath" anodzivirira anotenderedza tsinga dzedu. "Sheath" iyi kana kuti chifukidziro ichi chakagadzirwa nezvikamu zvakasiyana-siyana:

• Masero eSchwann: Aya ndiwo masero anotenderera axon, chikamu chakareba chemasero etsinga, sechinodzivirira chakatenderedza waya.
• Endoneurium: Iyi ndiyo tambo inobatanidza tsinga imwe neimwe, yakafanana nekaburi kakatenderedza waya imwe chete yemhangura iri muwaya.
• Perineurium: Izvi ndizvo zvinopoteredza misumbu yetsinga.

Sisitimu yedu yetsinga inogona kukamurwa kuita zvikamu zviviri:

• Sisitimu yetsinga yepakati: Izvi zvinosanganisira uropi hwedu nemusana.
• Sisitimu yetsinga dzemumativi: Iyi ndiyo network yetsinga dzinobuda kubva muuropi nemumusana dzichienda kunhengo dzese dzemuviri.

Kazhinji, ma neurofibromas aya anoumbwa muhurongwa hwetsinga dzeropa .

Ndedzipi mhando dzenzungu dziripo?

Kune mhando dzakawanda dze neuromas. Ngationei kuti ndedzipi.

Schwannomas

Mabundu aya anokura mumasero eSchwann ambotaurwa. Anenge 60% eschwannomas anokura mutsinga yemukati menzeve yedu . Tsinga iyi inobatsira muviri wedu kuchengetedza kuenzana. Dzimwe schwannomas dzimwe nguva dzinogona kukura pasi peganda redu, kana mukati menyama nenhengo dzemuviri. Nzvimbo dzinonyanya kuonekwa mabundu aya ndeidzi:

• Mumaoko nemakumbo
• Mumusoro
• Mudumbu (ndiko kuti, nzvimbo iri pakati pemafudzi nechiuno)

Schwannomas rudzi rwegomarara rinowanzo vharwa nechikamu chakatetepa chenyama, kana kuti "rakavharirwa." Magomarara aya kazhinji haasi egomarara (asina kuipa). Zvisinei, kashoma, gomarara ragara kwenguva refu rinogona kuva gomarara (rinokuvadza).

Neurofibromas

Rudzi urwu rwebundu runosanganisira mhando dzakasiyana dzenyama dzinonzi Schwann cells, endoneurium, uye perineurium dzinofukidza tsinga. Izvi zvinowanzoonekwa semapundu pasi peganda, asi dzimwe nguva zvinogona kukura patsinga dziri mukati memuviri.

Kusiyana neschwannomas, neurofibromas hadzina kuvharwa. Dzinokura mukati metsinga. Plexiform neurofibromas rudzi rwebundu rinopararira semambure, rakakomberedza tsinga dzakawanda uye rinogona kupararira munyama dzakapoteredza.

Mazhinji e neurofibromas haasi kenza. Zvisinei, anenge 5% kusvika 10% emapundu aya anogona kuva kenza . Anonzi malignant peripheral nerve sheath tumors (MPNST) . Inenge hafu yevanhu vane mapundu aya anenge atopararira kune dzimwe nhengo dzemuviri panguva yaanoonekwa.

Muchero uyu wakajairika zvakadii?

Matumbu etsinga asina kenza haawanzoitiki.

• MaSchwannomas anowanzoonekwa muvanhu vane makore ari pakati pe50 ne60.
• Neurofibromas dzinowanzoitika kuvanhu vane makore ari pakati pe20 ne40.
• Ma "plexiform neurofibromas" anowanzo buda asati asvika makore mashanu.

Matumbu emugomarara emumutsipa anouraya vanhu vakawanda , anongobata munhu mumwe chete pavanhu vanosvika mamiriyoni gumi gore rega rega.

Sei bundu rakadai richikura? Ndezvipi zvinokonzera?

Kuchinja kwemajini kune simba guru pakukura kwemasero aya europi.

• Kukura kweSchwannomas kunobatanidzwa nekuchinja kwejini rinonzi NF2.
• Neurofibromas dzinobatanidzwa nejini rinonzi (NF1).

Kazhinji, shanduko idzi dzemajini dzinoitika nguva nenguva, pasina chikonzero chakajeka . Zvisinei, nhamba diki yeschwannomas ne neurofibromas inokonzerwa nechirwere chemajini chisingawanzoitiki chinonzi neurofibromatosis , chinogona kuitika mumhuri.

Mhando dzeNeurofibromatosis

Kune marudzi matatu makuru echirwere ichi:

• Neurofibromatosis type 1 (NF1): Vanhu vane NF1 vanokura ma neurofibromas akawanda. Vanewo mukana wakawedzerwa wekuva ne plexiform neuromas uye malignant peripheral nerve sheath tumors (MPNST). Mamwe matambudziko anoonekwa muvanhu vane NF1 anosanganisira macrocephaly , scoliosis, uye learning disability .

• Neurofibromatosis rudzi rwechipiri (NF2):Vanhu vanenge vose vane NF2 vanotanga kuva nevestibular schwannomas munzeve dzese vasati vasvitsa makore makumi matatu. Pamusoro pezvo, mamwe marudzi eschwannomas nemabundu anogonawo kukura muganda ravo, maziso, uye central nervous system.

• Schwannomatosis: Mumamiriro ezvinhu aya, schwannomas dzakawanda dzinokura mutsinga yevestibular (munzeve dzese) kwete mutsinga yevestibular.

Ndezvipi zviratidzo zvemapundu aya?

Vanhu vazhinji vane neuromastoid bundu havarwadziwi kana zvimwe zviratidzo . Zvisinei, kana bundu rikakura kana kudzvanya tsinga, zviratidzo zvakaita se:

• Bundu kana bundu riri pasi peganda (rinogona kurwadza kana rikadzvanywa).
• Kushaya simba kwetsandanyama .
• Kusanzwa simba .
• Marwadzo, kurwadziwa, kana kurwadziwa kwakapinza .
• Kunzwa kukwenya, sekunge warohwa nemagetsi .

Zvichienderana nenzvimbo yebundu, zvimwe zviratidzo zvinogonawo kuitika. Heano mimwe mienzaniso mishoma:

• Bundu retsinga reSciatic: Marwadzo anofamba kubva kumusana achidzika pasi pegumbo (sciatica).
• Bundu paruoko: Zviratidzo zvakafanana neCarpal Tunnel Syndrome.
• Bundu retsinga dzemutsinga: Kurasikirwa nekunzwa, tinnitus, matambudziko ekuenzanisa.

Kazhinji, kana munhu aine neurofibromatosis, ibundu rimwe chete. Zvisinei, kune vanhu vane chirwere chataurwa kare chinonzi neurofibromatosis, bundu rakawanda rinogona kuonekwa (kazhinji paganda).

Unoziva sei kana uine nzungu idzi?

Chiremba wako achatanga akuongorora muviri wako uye oongorora hutano hwako hwese. Izvi zvinosanganisira kubvunza nezvenhoroondo yako yezvekurapa, nhoroondo yezvekurapa yemhuri yako, uye chero zviratidzo zvaungave uchiona.

Kuti uongorore bundu riri kutoonekwa kana kuti bundu rinofungidzirwa kuti riripo, chiremba wako anogona kukurudzira bvunzo dzinotevera:

• Kuongororwa kwemifananidzo yekurapa: Izvi zvinosanganisira MRI scans, ultrasound scans, uye PET scans kuti bundu rionekwe zvakajeka.
• Kuongororwa kwemuviri: Kanyama kadiki kanotorwa kubva mubundu roongororwa nemaikorosikopu kuti zvionekwe kuti ndeapi marudzi emasero aripo. Izvi ndizvo zvinogona kukuudza zvechokwadi kana bundu iri riri regomarara kana kuti kwete.

Kana uine bundu rakawanda, chiremba wako anogonawo kukurudzira kuongororwa kwemajini kuti vaone kana uine zvirwere zvinonzi (NF1), (NF2), uye Schwannomatosis.

Ndezvipi zvinorapwa izvi?

Kana usina zviratidzo zve neuromastoid, chiremba wako anogona kukurudzira kuti "tarisa womirira."Unogona kushandisa nzira inonzi "monitoring." Izvi zvinoreva kutarisa bundu nguva nenguva kuti uone kana riri kukura kana kuti richichinja.

Kana paine zviratidzo zvegomarara, kana kuti uchida kubvisa gomarara racho nekuda kwerunako, kuvhiyiwa ndiyo nzira chete yaungasarudza .

Mamwe ma neurofibromas, kunyanya ayo anonzi plexiform neurofibromas, anonetsa kubvisa zvachose nekuti anokura mukati metsinga uye pakati pezvikamu zvechifukidziro. Kana bundu risingakwanise kubviswa zvachose mushure mekuvhiyiwa, chiremba wako achakutarisa zvakanyanya, sezvo bundu racho rinogona kukura zvakare.

Kurapa kweSchwannomas mumusoro

MaSchwannomas anoumbwa mumusoro, akadai sevestibular schwannomas, anogona kukanganisa tsinga dzinodzora mabasa akakosha mumuviri wedu. Muzviitiko izvi, vanachiremba vanoshandisa nzira inonzi stereotactic radiosurgery (semuenzaniso, Gamma Knife®) kudzivirira kukuvara kwetsinga.

Uku hakusi kuvhiyiwa kwechivanhu kunosanganisira kugadzira ganda. Kunosanganisira kutumira mwaranzi chaiyo nepaganda kuti iparadze kana kuderedza bundu.

Kurapa kwegomarara remudumbu remutsinga

Pamusoro pekuvhiyiwa, mishonga yegomarara yakadai seradiation therapy uye chemotherapy inogona kushandiswawo kurapa mamota ane kenza mumitsipa yeropa.

Ndezvipi zvinetso zvinogona kuitika kana munhu avhiyiwa?

Sekunge kune chero kuvhiyiwa kupi zvako, kune matambudziko akawanda anowanzoitika nekuvhiyiwa uku:

• Kubuda ropa
• Utachiona hwemaronda
• Marwadzo
• Mavanga

Pamusoro pezvo, kuvhiyiwa kwetsinga kune njodzi yekukuvara kwetsinga uye kuremara zvachose . Chikwata chako chekurapa chichakubatsira kugadzirisa chero kuremara kwenguva refu kunogona kuitika mushure mekuvhiyiwa. Marapirwo akasiyana-siyana (physiotherapy, occupational therapy, uye speech therapy) anogona kukubatsira kupora.

Matumbu aya anogona kudzivirirwa kuti asaumbwe here?

Hapana nzira inozivikanwa yekudzivirira bundu iri kuti risaumbe. Zvisinei, chiremba wako anogona kukurudzira kuongororwa kwemajini kana:

• Kana paine munhu mumhuri yako ane nhoroondo yekuva neurofibromas.
• Kana uine bundu retsinga dzakawanda (izvi zvinogona kuva chiratidzo chechirwere che neurofibromatosis).

Tinofanira kufunga nezvepfungwa idzi dziri mberi? (Outlook)

Mazhinji e neurofibromas haasi kenza . Anogona kurapwa nekuvhiyiwa uye haawanzo dzoka. Zvisinei, kana bundu rako risingakwanise kubviswa zvachose nekuvhiyiwa, uchafanira kuramba uri pasi pekutarisirwa nachiremba.

Vanhu vanosvika vatatu pavana vanorapwa chirwere chevestibular schwannoma vanokwanisa kuramba vachinzwa .

Njodzi yekuti bundu remutsinga rive kenza yakaderera zvikuru. Njodzi huru ndeyevanhu vane chirwere ichi (NF1) vanowana Plexiform neurofibroma. Kufungidzira kuti bundu iri richange rakaipa (MPNST) harina kunaka, kunyanya kana bundu racho rakakura kupfuura masendimita maviri. Vanhu vasingasviki hafu vane chirwere ichi vanorarama makore mashanu mushure mekuonekwa kuti vane chirwere ichi.

Unofanira kuona chiremba rini?

Kana ukaona bundu riri pasi peganda rako, kana kuti ukaona zviratidzo zvaunofunga kuti zvinogona kunge zviri neurofibromatosis , enda kuna chiremba nekukasika . Zvakare, udza chiremba wako kana paine mumwe munhu mumhuri mako akambova nerudzi urwu rwemabundu.

Mharidzo Yekupedzisira Yekuenda Kumba

Yeuka, bundu zhinji dzemuuropi dzine mabundu asina njodzi, anokura zvishoma nezvishoma . Kana usina zviratidzo, chiremba wako angasarudza kungokutarisa. Kana bundu richida kubviswa, kuvhiyiwa kunowanzo budirira zvikuru. Kashoma kuti matambudziko (akadai sekusakwanisa kubvisa bundu zvachose, kukuvara kwetsinga) aitike, kana kuti bundu rive kenza. Chiremba wako achakubatsira kugadzira hurongwa hwekurapa uye purogiramu yemiedzo yeramangwana kuti ikubatsire kugadzirisa mamiriro ako ezvinhu. Saka usatya kutaura nachiremba wako nezve chero chinhu.

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