Amatye ezintso yinto esisoyikisayo kancinci, akunjalo? Mhlawumbi ukhe weva ngaloo ntlungu. Kodwa ubusazi na ukuba kukho iintlobo ezahlukeneyo zamatye ezintso? Namhlanje siza kuthetha ngohlobo olunqabileyo kodwa olubaluleke kakhulu lwamatye. Lawo ngamatye e-cystine. Makhe sibone ukuba kutheni ebakho, zithini iimpawu, kwaye yintoni enokwenziwa ngawo.
Ngamafutshane, yintoni amatye e-cystine?
Amatye eCystine akwaluhlobo lwelitye lezintso. Amatye ezintso zizinto eziqinileyo, ezifana nelitye ezenziwe kukuqokelelwa kweekhemikhali ezahlukeneyo kumchamo wethu. Amatye eCystine enziwe yikhemikhali ebizwa ngokuba yiCystine . ICystine yi-amino acid ebalulekileyo emzimbeni wethu. Ukuchaneka, yinxalenye encinci yeeproteni ezinceda ekwakheni izihlunu nokulungisa izicubu emzimbeni wethu.
Ngokwesiqhelo, izintso zethu ziyayifunxa le cystine emzimbeni. Kodwa kwabanye abantu, le nkqubo ayisebenzi kakuhle. Emva koko, i-cystine engenakufunxwa iqokelelana kumchamo kwaye, ngokuhamba kwexesha, yenza amatye. La matye e-cystine anokukhula abe makhulu kancinci kunezinye iitshe zezintso. Ngoko ke ngamanye amaxesha kufuneka asuswe ngotyando ukuze kuthintelwe umonakalo kwizintso okanye kwindlela yomchamo.
Ngoko ke yintoni iCystinuria?
Eyona nto ibangela la matye e-cystine yimeko yemfuza ebizwa ngokuba yi -cystinuria . Le yimeko engaqhelekanga, efunyanwa njengelifa. Ngamafutshane, ukuba unale meko, umzimba wakho awukwazi ukuyinyibilikisa kakuhle ikhemikhali ebizwa ngokuba yi-cystine. Ngoko ke iyaqokelelana kumchamo wakho ize yenze amatye.
Into ebalulekileyo kukuba i-cystinuria yimeko yobomi bonke. Akukho nyango lwayo. Kodwa ngonyango olufanelekileyo, ungayilawula kakuhle le meko kwaye uphile ubomi obuqhelekileyo .
Ngenxa yokuba esi sisifo semfuza, umntwana kufuneka afumane esi sifo kumama nakutata ukuze asifumane . Umntu onesi sifo unokufumana amatye e-cystine amaxesha amaninzi ebomini bakhe.
Ixhaphake kangakanani le meko? Zithini iimpawu zayo?
Oku akwenzeki kumntu wonke, kunqabile kancinci. Ngokwesiqhelo, ukuba uthatha umntu omnye okanye ababini kubantu abali-100 abafumana amatye ezintso, omnye okanye ababini kuphela kubo abafumana amatye e-cystine. Kodwa okumangalisayo kukuba, le meko ibonakala rhoqo ebantwaneni nakubantu abadala abancinci . Malunga nama-80% abantu abafumana amatye e-cystine bavelisa ilitye labo lokuqala ngaphambi kokuba bafikelele kwiminyaka engama-20. Nangona kunjalo, la matye anokwakheka nakweyiphi na iminyaka.
Ngokuphathelele iimpawu, zifana kakhulu nezo zamanye amatye ezintso. Iimpawu azisoloko zivakala de kubekho ilitye.
| Uphawu | Inkcazo |
|---|---|
| Intlungu ebuhlungu emqolo okanye esinqeni | Ingavakala njengentlungu ebukhali. Oku kudla ngokuvakala kwelinye icala. |
| Intlungu esiswini okanye emqolo | Njengoko ilitye lihamba lisiya kumchamo, intlungu inokuvakala kwisisu esisezantsi. |
| Igazi kumchamo | Umchamo ungabonakala upinki, ubomvu, okanye umdaka. |
| Ukuhlanza kunye nesicaphucaphu | Isicaphucaphu nokuhlanza kunokubakho kunye nentlungu eqatha. |
| Intlungu xa uchama | Xa ilitye likufutshane nesinyi, ungaziva utshisa okanye intlungu xa uchama. |
Ngamanye amaxesha, la matye e-cystine anokuba makhulu ngokwaneleyo ukuvala indlela yomchamo aze abangele usulelo lwendlela yomchamo (UTI) .
Zeziphi iingxaki ezinokwenzeka?
I-Cystinuria yimeko ehlala ubomi bonke, kwaye ukuba ayiphathwa kakuhle, inokukhokelela kwiingxaki. Kubalulekile ukusebenzisana nogqirha wakho ukulawula le meko.
Iingxaki ezinokubakho ziquka:
- Usulelo lwezintso: Amatye anokuthintela ukuhamba komchamo aze avumele iintsholongwane ukuba zingene ezintso.
- Ukuvaleka komchamo: Umbhobho othwala umchamo ukusuka kwizintso ukuya kwisinyi (ureter) unokuvaleka lilitye.
- Usulelo oluqhelekileyo lwendlela yomchamo (UTIs).
- Umonakalo ongapheliyo wezintso:Ukuba ayinyangwa ixesha elide, ukusebenza kwezintso kunokuncipha.
Ugqirha uyifumanisa njani le nto? Zithini iindlela zonyango?
Ukuba uneempawu ezifana namatye ezintso, ugqirha wakho uya kwenza iimvavanyo ezininzi ukuze abone ukuba la matye angama-cystine na.
Iindlela zokuxilonga
- Ukubuza iinkcukacha: Ugqirha uza kukubuza ngeempawu zakho kunye nokuba kukho nabani na kusapho lwakho okhe waba neengxaki ezifanayo.
- Uvavanyo: Uvavanyo lomchamo kunye novavanyo lomfanekiso olufana ne- ultrasound scan okanye i-CT scan lunokufuneka.
- Ukuvavanya ilitye: Ukuba unelitye eliphumileyo kumchamo wakho, lingathunyelwa kwilabhoratri ukuze livavanywe ukuze kufunyaniswe ukuba loluphi uhlobo lwelitye. Le yindlela kuphela yokuqinisekisa ngokupheleleyo ukuba lilitye le-cystine.
Iindlela zonyango
Injongo ephambili yokunyanga amatye e-cystine kukuthintela ukwakheka kwamatye amatsha nokususa amatye akhoyo. Ugqirha wakho uza kwenza isicwangciso sonyango esifanelekileyo kuwe.
- Utshintsho kwindlela yokuphila kunye nokutya
- Sela amanzi amaninzi: Le yeyona nto ibalulekileyo. Ugqirha wakho angakuxelela ukuba usele ubuncinane iilitha ezi-3-4 zamanzi ngosuku. Oko kuthetha ukuba kufuneka uqhele ukusela iglasi yamanzi rhoqo ngeyure. Ungamangaliswa kukuba uvuka ebusuku ukuze usele amanzi. Amanzi ayawunciphisa umchamo wakho kwaye anciphise ukuqokelelwa kwe-cystine.
- Ulawulo lwetyuwa (i-sodium): Nciphisa ubungakanani betyuwa oyongeza ekutyeni kwakho. Kuphephe ukutya okufana nokutya okusemathinini kunye nokutya okukhenkcezisiweyo okanye okupakishwe kwiipakethe, okunetyuwa eninzi.
- Ukunciphisa iiproteni zezilwanyana: Unganciphisa ukutya kwakho iiproteni zezilwanyana ezifana nenyama, intlanzi, namaqanda kwaye endaweni yoko ugxile kwiiproteni ezisekelwe kwizityalo.
- Amayeza
Ukuba uva iintlungu ngenxa yelitye, ugqirha wakho uza kukunika amayeza okudambisa iintlungu. Ukongeza, kukho amayeza akhethekileyo anokunceda ukuthintela ukwakheka kwamatye amatsha e-cystine. I-Tiopronin kunye ne-d-penicillamine zezo mayeza. La mayeza anceda ekunyibilikiseni i-cystine. La mayeza kufuneka athathwe kuphela phantsi kweliso likagqirha .
- Utyando
Ukuba amatye makhulu kakhulu, avala umchamo, okanye abangela iintlungu eziqatha, kunokufuneka asuswe ngotyando.
- I-Ureteroscopy: Ikhamera encinci, eguquguqukayo idluliselwa kwi-urethra ukuze ifumane ilitye kwaye iqhekeze libe ziingceba okanye isuswe ngokupheleleyo.
- I-Percutaneous Nephrolithotomy:Inkqubo apho kwenziwa khona ukusika okuncinci eluswini lomqolo kwaye kudluliselwe ityhubhu kuyo iye kwizintso ukuze kususwe ilitye. Oku kudla ngokwenziwa kumatye amakhulu kakhulu.
Uphila njani nale meko? Ngaba yinto omele uyoyike?
I-Cystinuria yimeko ehlala ubomi bonke. Kodwa ukuba iphathwa kakuhle, akukho nto inokubangela ixhala ngayo. Le meko ayisoloko isongela ubomi. Ukuba inyangwa kakuhle, ayifane ifikelele kwiimeko ezinzulu ezifana nokungasebenzi kakuhle kwezintso.
Eyona nto ibalulekileyo kukugcina ubudlelwane obuhle phakathi kwakho nogqirha wakho. Ngokulandela imiyalelo ngqo nokuya kwiikliniki ngexesha elifanelekileyo, ungayilawula ngcono le meko.
Ukujonga impumelelo yonyango, ugqirha uya kwenza uvavanyo lomchamo rhoqo ukujonga inqanaba le-cystine kumchamo. Ukuba kuyimfuneko, isicwangciso sonyango siya kulungiswa ngokufanelekileyo. Ekubeni esi sisifo semfuza, kunokuba ngumbono olungileyo ukufuna iingcebiso zemfuza ukuba uceba ukuqala usapho.
Umyalezo Wokuya Ekhaya
- Amatye e-Cystine luhlobo lwelitye lezintso elibangelwa yimeko engaqhelekanga, yemfuza ebizwa ngokuba yi-cystinuria.
- Nangona le meko ithatha ubomi bonke, inokulawulwa kakuhle ngonyango olufanelekileyo kunye notshintsho kwindlela yokuphila.
- Ukusela amanzi amaninzi imini yonke yeyona ndlela ibalulekileyo nelula yokuthintela ukwakheka kwamatye.
- Kubaluleke kakhulu ukulandela ukutya okunetyuwa encinci kunye neproteni yezilwanyana.
- Ukuba ufumana iimpawu ezinje ngentlungu ebuhlungu emqolo, esinqeni, okanye esinqeni esisezantsi, okanye igazi kumchamo wakho, musa ukuchitha ixesha kwaye ubone ugqirha ngoko nangoko .
- Landela imiyalelo kagqirha wakho kunye namayeza ngokuchanekileyo. Ungakhathazeki, ungaphila ubomi obusempilweni xa unesi sifo.
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