Khawuthelekelele ukuba ubunesisu esibuhlungu okanye umkhuhlane malunga neveki ephelileyo kwaye uphilile. Kodwa ngequbuliso uqala ukuziva ubuthathaka obungaqhelekanga, uqala ngeenzwane zakho. Emva kosuku okanye ezimbini, olu luvo lusasazeka emilenzeni yakho, okwenza kube nzima ukuhamba. Emva koko iingalo zakho zivakala ngathi ziza kuba ndindisholo. Kuyoyikisa kancinci ukuva ngento efana nale, akunjalo? Namhlanje siza kuthetha ngesi sifo singaqhelekanga nesingaqhelekanga esibizwa ngokuba yiGuillain-Barré Syndrome. Nangona igama linzima ukulibiza, kubalulekile ukwazi ngalo.
Ngamafutshane, yintoni iGuillain-Barré Syndrome (GBS)?
I-Guillain-Barré Syndrome (GBS) yimeko engaqhelekanga apho amasosha omzimba wethu ehlasela inkqubo yethu yemithambo-luvo, ingakumbi imithambo-luvo ejikeleze amalungu ethu. Ikwabizwa ngokuba yimeko yokuzikhusela komzimba .
Cinga ngemithambo-luvo esemzimbeni wethu njengeentambo zombane. Kanye njengokuba kukho ukhuselo olujikeleze ezi ntambo zombane, kukho ukhuselo olubizwa ngokuba yi-myelin olujikeleze imithambo-luvo yethu. Xa i-GBS isenzeka, inkqubo yethu yomzimba yokuzikhusela ihlasela kwaye itshabalalise esi sigqubuthelo se-myelin. Emva koko, ngokungathi ukhuselo lwazo ezo ntambo zombane lususiwe, imiqondiso evela ebuchotsheni ngemithambo-luvo ayihambi kakuhle. Yiyo loo nto amalungu eqala ukuba ndindisholo aze aphulukane nobomi bawo.
Iindaba ezimnandi zezokuba ngonyango olufanelekileyo, uninzi lwabantu lunokuphila ngokupheleleyo kwesi sifo , kodwa kungathatha ixesha.
Ngubani onokuthi abe ne-GBS? Ixhaphake kangakanani?
I-GBS inokuchaphazela nabani na wanoma yiphi na iminyaka. Abantwana abancinci, abantu abadala abaselula, kunye nabantu abadala bonke basengozini. Nangona kunjalo, idatha ibonisa ukuba abantu abaphakathi kweminyaka engama-30 ukuya kwengama-50 banamathuba amaninzi okufumana esi sifo.
Le yimeko engaqhelekanga kakhulu. Kwihlabathi liphela, i-GBS iyenzeka kumntu omnye kwabayi-100,000 abatsha ngonyaka. Oko kuthetha ukuba ngokomyinge, umntu omnye kwabayi-78,000,000 uba nesi sifo minyaka le. Ngoko ke asisisifo esiqhelekileyo.
Ziziphi iimpawu eziphambili ze-GBS?
Kwi-GBS, iimpawu zinxulumene nomonakalo kwimithambo-luvo ejikeleze umzimba elawula izinto ezifana nokuhamba kwemisipha yethu, iintlungu, ubushushu, kunye nokuchukumisa.
Iqala ngobuthathaka bemisipha kunye/okanye ukungakhululeki (i-paresthesia) . Ezi mpawu zivela ngequbuliso. Zihlala ziqala emilenzeni nasezinyaweni kwaye zisasazeka kancinci kancinci ziye phezulu, ziye ezingalweni nasebusweni. Ubuthathaka emilenzeni bunokwenza kube nzima ukunyuka izinyuko okanye ukuhamba.
Ubunzima be-GBS buyahluka kumntu nomntu. Abanye abantu banokuba neempawu ezincinci kakhulu baze baphile. Abanye banokuba neempawu ezinzima. Nazi ezinye iimpawu ezinokubonakala.
| Uphawu | Inkcazo |
|---|---|
| Intlungu ebuhlungu yemisipha | Kunokubakho iintlungu ezinzulu nezibukhali, ingakumbi emqolo nasemilenzeni. |
| Ukukhubazeka komzimba | Izihlunu emilenzeni, ezingalweni nasebusweni zisenokungasebenzi kakuhle. Kwiimeko ezinzima, umzimba wonke unokuba buthathaka. |
| Ubunzima bokuphefumla | Ukubuthathaka kwemisipha yesifuba kunokwenza kube nzima ukuphefumla. Le meko yenzeka kumntu omnye kwabathathu abane-GBS. |
| Ubunzima bokuthetha nokuginya | Le meko (i-dysphagia) inokwenzeka ukuba izihlunu zomqala nomlomo ziyachaphazeleka. |
| Ubunzima bokuhambisa amehlo | Ukubuthathaka kwemisipha yamehlo kunokubangela iingxaki zokubona kunye nobunzima bokushukumisa amehlo. |
Iimpawu ze-GBS zinokukhula ngokukhawuleza emva kweeyure, iintsuku, okanye iiveki. Ukuba wena okanye umntu omaziyo ubuthathaka bemisipha ngequbuliso, funa uncedo lwezonyango ngokukhawuleza. Kubalulekile ukuqala unyango lwale meko ngokukhawuleza.
Ziziphi iingxaki eziyingozi ezinokubakho ngenxa ye-GBS?
I-GBS inokubangela iingxaki ezisongela ubomi ukuba ichaphazela inkqubo yethu yemithambo-luvo ezimeleyo. Inkqubo yemithambo-luvo ezimeleyo yinkqubo elawula imisebenzi yomzimba wethu ngaphandle kokuba siqaphele. Umzekelo, izinto ezifana nesantya sentliziyo, uxinzelelo lwegazi, kunye nokugaya ukutya. Ukungasebenzi kakuhle kwale nkqubo kubizwa ngokuba yi -dysautonomia .
Iingxaki eziphambili ezinokubakho ngenxa ye-GBS zezi:
- Iingxaki zentliziyo
- Ukungazinzi koxinzelelo lwegazi (oluphezulu kakhulu okanye oluphantsi kakhulu)
- Iingxaki zenkqubo yokugaya ukutya
- Ubunzima bokulawula umchamo, njengokugcinwa komchamo
Ngenxa yokuba kukho iingxaki ezinje ngezi, izigulana ze-GBS zihlala zigcinwa kwigumbi lonyango oluphezulu (ICU) esibhedlele kwaye zijongwa rhoqo.
Kutheni i-GBS ikhula? Yintoni unobangela?
Isizathu esichanekileyo se-GBS asikaziwa, kodwa oogqirha bayibiza ngokuba yi-neuropathy emva kokosuleleka, ebangelwa kukuzikhusela komzimba . Masiyichaze ngokulula.
1. Emva kokosuleleka: "Emva kokosuleleka " kuthetha "emva kokosuleleka." Oku kuthetha ukuba esi sifo sidla ngokukhula emva kokuba olunye usulelo luphelile. Malunga nama-70% abantu abafumana i-GBS baye baba nohlobo oluthile losulelo kwiveki ukuya kwiiveki ezintandathu emva kokuba iimpawu ziqalile.
2. Ukuzikhusela komzimba: Sikhe sathetha ngale nto ngaphambili. Esi sifo sibangelwa kukusabela okungaqhelekanga kwenkqubo yethu yokuzikhusela komzimba. Emva kokulwa nosulelo, amajoni omzimba abanye abantu ayayeka ukusebenza aze aqalise ukuhlasela imithambo-luvo yabo.
3. I-Neuropathy: Ngamafutshane, umonakalo kwimithambo-luvo. Kwi-GBS, umonakalo ukwimithambo-luvo engaphandle.
Izinto eziphambili ezibangela ukuba kubekho i-GBS
Abaphandi bafumanise usulelo olukhulu oluninzi kunye nezinye izizathu ezibangela uphuhliso lwe-GBS.
- Urhudo okanye usulelo lokuphefumla: Malunga nabantu ababini kwabathathu abane-GBS banesifo sorhudo okanye usulelo lokuphefumla kwiiveki ezimbalwa ngaphambi kokuba kubonakale iimpawu. I-Campylobacter jejuni , intsholongwane ebangela urhudo, ichongiwe njengeyona nto iphambili ebangela i-GBS.
- Usulelo lwentsholongwane: Abanye abaguli be-GBS baxelelwe ukuba banesifo sosulelo lwentsholongwane esifana nomkhuhlane, i-cytomegalovirus, i-Epstein-Barr virus, kunye ne-Zika virus .
- Iigonyo: Kwiimeko ezingaqhelekanga kakhulu , i-GBS ibike ukuba ikhula emva kweentsuku okanye iiveki emva kokufumana iigonyo ezithile. Nangona kunjalo, into ebalulekileyo ekufuneka uyiqonde apha kukuba iingenelo zokugonywa zingaphezulu kakhulu kolu mngcipheko ungaqhelekanga . Uphando lubonise ukuba umngcipheko wokufumana i-GBS ngenxa yokufumana umkhuhlane uphezulu kakhulu kunomngcipheko wokufumana i-GBS ngenxa yokufumana ugonyo lomkhuhlane.
- Utyando:Kwakhona, kunqabile kakhulu, i-GBS inokwenzeka emva kotyando oluthile.
Ifunyaniswa njani i-GBS?
Oogqirha baxilonga i-GBS ngokusekwe kwiimpawu zakho kunye nembali yakho yezonyango. Ugqirha wakho uza kukubuza ukuba iimpawu zakho ziqale njani kwaye nini, kwaye ukuba ukhe waba nazo naziphi na izifo kutshanje. Baza kuvavanya umzimba, ngakumbi ukujonga ubuthathaka bemisipha kunye nokuncipha kwe-deep-tendon reflexes, njengasemadolweni.
Nangona kunjalo, ekubeni kukho ezinye izifo ezininzi ze-neurological ezineempawu ezifanayo neze-GBS, ugqirha uya kucebisa iimvavanyo ezininzi ukuze aqinisekise ezinye izifo kwaye aqinisekise imeko ye-GBS.
- Uvavanyo lwe-Electromyography (EMG) kunye noVavanyo lokuHanjiswa kweMithambo: Olu vavanyo lunokuvavanya impilo kunye nokusebenza kwezihlunu zakho kunye nemithambo-luvo ezilawulayo.
- Ukubethelwa koMgogodla/Ukubhaqwa kweLumbar: Oku kuquka ukufaka inaliti encinci emqolo wakho ongezantsi ukuze kuthathwe isampuli encinci yolwelo lwe-cerebrospinal (CSF), olujikeleze ingqondo yakho kunye nomqolo. Malunga nama-80% ezigulana ezine-GBS zinamanqanaba aphezulu eeproteni kolu lwelo.
- I-MRI scan: Kungacetyiswa nokuba i-MRI scan yomqolo wakho ithathwe.
Ziziphi iindlela zonyango lwe-GBS?
Ukuba ufunyaniswe une-GBS, kusenokwenzeka ukuba ungeniswe kwigumbi lokunyamekela abagula kakhulu (ICU) lesibhedlele ukuze ufumane unyango olukhawulezileyo kuzo naziphi na iingxaki esizixubushile ngaphambili, ezinje ngobunzima bokuphefumla kunye notshintsho kuxinzelelo lwegazi.
Akukho ndlela ithile yonyango lwe-GBS okwangoku. Nangona kunjalo, kukho iindlela ezimbini eziphambili zonyango ezinokunciphisa ubunzima besifo kwaye zinciphise ixesha lokuchacha.
| Indlela yonyango | Ingaba isebenza kanjani |
|---|---|
| Utshintshiselwano lwePlasma / iPlasmapheresis | Okwenzekayo koku kukuba umatshini uthatha igazi lakho, wahlule iplasma kulo, wahluza ii-antibodies eziyingozi ezihlasela imithambo-luvo, waza wabuyisela iplasma ecocekileyo emzimbeni. |
| Unyango lwe-Immunoglobulin efakwa kwiMitha (IVIG) | Kolu nyango, iiproteni (ii-antibodies) ezibizwa ngokuba yi-immunoglobulins, ezithathwe kumawaka abantu abaphilileyo, zifakwa emzimbeni nge-saline. Ezi antibodies zilungileyo zithintela isenzo se-antibodies ezimbi ezihlasela imithambo-luvo yomzimba wethu. |
Ukuba naluphi na unyango luqalwe kwiiveki ezimbini emva kokuba iimpawu ziqalile, ixesha lokuchacha lingancitshiswa kakhulu.
Ukuvuselelwa
Njengoko imeko yakho iphucuka kancinci kancinci, ungadluliselwa kwiziko lonyango. Apho, iingcali ezahlukeneyo zonyango ziya kukunceda ufumane amandla akho kwaye ubuyele kwinqanaba apho unokwenza imisebenzi yemihla ngemihla wedwa.
- Unyango Lomzimba: Kunikezelwa umthambo kunye nonyango ukuze kwakhiwe kwakhona amandla emisipha kunye nokulawula iintlungu kunye nokuqina.
- Unyango Lomsebenzi: Lukunceda ufunde ukwenza imisebenzi yemihla ngemihla efana nokunxiba nokutya kwakhona ngokukhuselekileyo nangokulula.
- Unyango Lokuthetha: Ukuba unengxaki yokuginya okanye yokuthetha, singakunceda ubuyisele ezo zakhono.
Liyintoni ikamva lomntu one-GBS?
Uninzi lwabantu abane-GBS bayachacha kakhulu kwiinyanga ezimbalwa. Nangona kunjalo, abanye abantu, ingakumbi abantu abadala, basenokuba nobuthathaka bemisipha emva kweminyaka emithathu. Inkqubo yokuchacha ingathatha ixesha elide kwabanye abantu.
Iindaba ezimnandi zezokuba abantu abachacha kwi-GBS banokuphila ubomi obuqhelekileyo . Umngcipheko wokufa ngexesha lesigaba esiqatha sesi sifo ungaphantsi kwe-2%. Oku kungenxa yonyango oluphezulu olufumanekayo namhlanje.
Ngaba i-GBS ingathintelwa?
Kwiimeko ezininzi, i-GBS ayinakuthintelwa. Abaphandi abasazi ukuba kutheni abanye abantu befumana i-GBS xa befumana usulelo kanti abanye abalufumani.
Kodwa singayinciphisa ingozi ngandlela ithile ngokuzikhusela kwiintsholongwane ezinokukhokelela kwi-GBS.
- Hlamba izandla zakho ngesepha rhoqo.
- Ziphephe kubantu abanezifo ezisulelayo ezifana nesifo sorhudo kunye nomkhuhlane.
- Ukuze umzimba wakho uhlale uqinile, yitya ukutya okunesondlo kwaye uzilolonge.
- Fumana zonke iigonyo zakho ngexesha.
I-GBS yimeko enzima enokutshintsha ubomi bakho ngequbuliso. Kodwa eyona nto ilungileyo kukuba ngonyango olufanelekileyo kunye nokuvuselelwa, uninzi lwabantu lunokubuyela kubomi obuqhelekileyo. Uhambo lokuchacha lunokuba lude kwaye ludinise. Musa ukuthandabuza ukufuna inkxaso koogqirha bakho, abahlengikazi, kunye nosapho lwakho kunye nabahlobo endleleni.
Umyalezo Wokuya Ekhaya
- I-Guillain-Barré Syndrome (GBS) yimeko engaqhelekanga kodwa enzulu apho amajoni ethu omzimba ahlasela imithambo-luvo yethu.
- Oku kunokwenzeka rhoqo emva kwesifo esifana norhudo okanye usulelo lokuphefumla.
- Iimpawu zokuqala kukuba ndindisholo kunye nobuthathaka bemisipha obuqala emilenzeni bunyuke.
- Ukuba iimpawu ziya zisiba mandundu ngokukhawuleza (kwiiyure okanye kwiintsuku ezimbalwa) , bona ugqirha ngoko nangoko.
- Ukulaliswa esibhedlele, ingakumbi kwicandelo labagula kakhulu, kunokufuneka.
- Unyango olubizwa ngokuba yi-plasmapheresis kunye ne-IVIG lunciphisa ubukhali besifo kwaye lukhawulezise ukuchacha.
- Nangona inkqubo yokuchacha ithatha ixesha, abantu abaninzi banokubuyela kwimpilo entle.











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