Amatshe ezinso ayinto esithusayo kancane, akunjalo? Cishe uke wezwa ngalobo buhlungu. Kodwa bewazi ukuthi kunezinhlobo ezahlukene zamatshe ezinso? Namuhla sizokhuluma ngohlobo lwetshe olungavamile kodwa olubaluleke kakhulu. Lawo amatshe e-cystine. Ake sibone ukuthi kungani akheka, yiziphi izimpawu, nokuthi yini engenziwa ngawo.
Kalula nje, ayini amatshe e-cystine?
Amatshe e-Cystine nawo awuhlobo lwetshe lezinso. Amatshe ezinso ayizakhiwo eziqinile, ezifana netshe ezakhiwa ukuqongelela kwamakhemikhali ahlukahlukene emchameni wethu. Amatshe e-Cystine akhiwe yikhemikhali ebizwa ngokuthi i-cystine . I-Cystine iyi-amino acid ebalulekile emzimbeni wethu. Uma sikhuluma iqiniso, yingxenye encane yamaprotheni asiza ekwakheni imisipha nokulungisa izicubu emzimbeni wethu.
Ngokuvamile, izinso zethu ziphinde zimunce le cystine emzimbeni. Kodwa kwabanye abantu, le nqubo ayisebenzi kahle. Bese kuthi, i-cystine engenakumuncwa iqongelela emchameni futhi, ngokuhamba kwesikhathi, yakhe amatshe. Lawa matshe e-cystine angakhula abe makhulu kancane kunamanye amatshe ezinso. Ngakho-ke ngezinye izikhathi kudingeka asuswe ngokuhlinzwa ukuze kumiswe umonakalo ezinso noma emgudwini womchamo.
Ngakho-ke iyini i-Cystinuria?
Imbangela eyinhloko yala matshe e-cystine yisimo sofuzo esibizwa ngokuthi i-cystinuria . Lesi yisimo esingavamile, esizuzwa njengefa. Kalula nje, uma unalesi simo, umzimba wakho awukwazi ukuncibilikisa kahle ikhemikhali ebizwa ngokuthi i-cystine. Ngakho-ke inqwabelana emchameni wakho bese yakha amatshe.
Into ebalulekile ukuthi i-cystinuria iyisimo sokuphila konke. Akukho ukwelashwa kwayo. Kodwa ngokwelashwa okufanele, ungasiphatha kahle lesi simo futhi uphile impilo evamile .
Ngenxa yokuthi lesi yisimo sofuzo, ingane kumele ithole ifa lesi sakhi sofuzo kunina nakuyise ukuze sibe naso . Umuntu onalesi simo cishe uzoba namatshe e-cystine izikhathi eziningana empilweni yakhe.
Sivame kangakanani lesi simo? Ziyini izimpawu?
Lokhu akuyona into eyenzeka kuwo wonke umuntu, kuyinto engavamile. Ngokuvamile, uma uthatha umuntu oyedwa noma ababili kwabayi-100 abathola amatshe ezinso, oyedwa noma ababili kuphela abazoba namatshe e-cystine. Kodwa ngokumangazayo, lesi simo sibonakala kaningi ezinganeni nakubantu abadala abasebasha . Cishe abantu abangama-80% abathola amatshe e-cystine bakha itshe labo lokuqala ngaphambi kweminyaka engama-20. Kodwa-ke, la matshe angakheka nganoma yisiphi isikhathi.
Ngokuphathelene nezimpawu, zifana kakhulu nezezinye izinso. Izimpawu ngokuvamile azizwakali kuze kube yilapho sekukhona itshe.
| Isibonakaliso | Incazelo |
|---|---|
| Ubuhlungu obukhulu emhlane noma ethangeni | Kungazwakala njengobuhlungu obuhlabayo obubukhali. Lokhu kuvame ukuzwakala ohlangothini olulodwa. |
| Ubuhlungu esiswini noma embotsheni engezansi | Njengoba itshe lihamba phansi emgudwini womchamo, kungase kuzwakale ubuhlungu esiswini esingezansi. |
| Igazi emchameni | Umchamo ungase ubonakale upinki, ubomvu, noma unsundu. |
| Ukuhlanza kanye nesicanucanu | Isicanucanu nokuhlanza kungase kwenzeke kanye nobuhlungu obukhulu. |
| Ubuhlungu lapho uchama | Uma itshe liseduze nesinye, ungase uzwe ukushisa noma ubuhlungu lapho uchama. |
Ngezinye izikhathi, la matshe e-cystine angaba makhulu ngokwanele ukuvimba umgudu womchamo futhi abangele ukutheleleka komgudu womchamo (UTI) .
Yiziphi izinkinga ezingaba khona?
I-Cystinuria yisimo esihlala isikhathi eside, futhi uma singaphathwa kahle, singadala izinkinga. Kubalulekile ukusebenzisana nodokotela wakho ukuze uphathe lesi simo.
Izinkinga ezingaba khona zifaka:
- Ukutheleleka kwezinso: Amatshe angavimba ukugeleza komchamo futhi avumele amagciwane ukuthi angene ezinso.
- Ukuvaleka komchamo: Ipayipi elithwala umchamo lisuka ezinso liye esinyeni (ureter) lingavinjelwa yitshe.
- Ukutheleleka okuvamile komgudu womchamo (UTIs).
- Ukulimala kwezinso okungapheli:Uma ingelashwa isikhathi eside, ukusebenza kwezinso kungase kwehle.
Udokotela ukuxilonga kanjani lokhu? Yiziphi izindlela zokwelapha?
Uma unezimpawu ezifana namatshe ezinso, udokotela wakho uzokwenza izivivinyo eziningana ukuze anqume ukuthi lawa ngamatshe e-cystine.
Izindlela zokuxilonga
- Ukukubuza imininingwane: Udokotela uzobuza ngezimpawu zakho nokuthi ngabe kukhona yini emndenini wakho oke waba nezinkinga ezifanayo.
- Ukuhlolwa: Ukuhlolwa komchamo kanye nokuhlolwa kwezithombe njengokuskena kwe-ultrasound noma i-CT scan kungacelwa.
- Ukuhlola itshe: Uma unetshe eliphumile emchameni wakho, lingathunyelwa elebhu ukuze lihlolwe ukuze kutholakale ukuthi liluhlobo luni lwetshe. Lena yindlela kuphela yokuqinisekisa ukuthi liyitshe le-cystine ngokuphelele.
Izindlela zokwelapha
Umgomo oyinhloko wokwelapha amatshe e-cystine ukuvimbela ukwakheka kwamatshe amasha nokususa amatshe akhona. Udokotela wakho uzokwakha uhlelo lokwelapha olufanele wena.
- Izinguquko endleleni yokuphila kanye nokudla
- Phuza amanzi amaningi: Lena yinto ebaluleke kakhulu. Udokotela wakho angakutshela ukuthi uphuze okungenani amalitha angu-3-4 amanzi ngosuku. Lokho kusho ukuthi kufanele ujwayele ukuphuza ingilazi yamanzi njalo ngehora. Ungamangali uma uvuka ebusuku ukuze uphuze amanzi. Amanzi anciphisa umchamo wakho futhi anciphise ukunqwabelana kwe-cystine.
- Ukulawula usawoti (i-sodium): Nciphisa inani likasawoti olifaka ekudleni kwakho. Gwema ukudla okufana nokudla okusemathinini, ukudla okuqandisiwe noma okucutshungulwe, okunosawoti omningi.
- Ukunciphisa amaprotheni ezilwane: Unganciphisa ukudla kwakho amaprotheni ezilwane njengenyama, inhlanzi namaqanda bese ugxila kumaprotheni asekelwe ezitshalweni esikhundleni salokho.
- Imithi
Uma uzwa ubuhlungu obubangelwa itshe, udokotela wakho uzokunikeza imithi yokunciphisa ubuhlungu. Ngaphezu kwalokho, kunemithi ekhethekile engasiza ekuvimbeleni ukwakheka kwamatshe amasha e-cystine. I-Tiopronin kanye ne-d-penicillamine yimithi enjalo. Le mithi iyasiza ekuncibilikiseni i-cystine. Le mithi kufanele ithathwe kuphela ngaphansi kokuqashwa ngudokotela .
- Ukuhlinzwa
Uma amatshe amakhulu kakhulu, evimba umgudu womchamo, noma ebangela ubuhlungu obukhulu, kungadingeka asuswe ngokuhlinzwa.
- I-Ureteroscopy: Ikhamera encane, eguquguqukayo idluliselwa e-urethra ukuze kutholakale itshe bese liqhekeka libe yizicucu noma lisuswe ngokuphelele.
- I-Percutaneous Nephrolithotomy:Inqubo lapho kwenziwa khona ukusikwa okuncane esikhumbeni somhlane bese kudluliswa ipayipi ngayo iye ezinso ukuze kususwe itshe. Lokhu kuvame ukwenziwa ngamatshe amakhulu kakhulu.
Uphila kanjani nalesi simo? Ingabe kuyinto okufanele uyesabe?
I-Cystinuria iyisimo esihlala isikhathi eside. Kodwa uma iphathwa kahle, akukho okufanele ukhathazeke ngayo. Lesi simo asivamile ukuba yingozi empilweni. Uma selashwa kahle, asivamile ukuqhubekela ezimweni ezimbi njengokwehluleka kwezinso.
Into ebaluleke kakhulu ukugcina ubuhlobo obuhle phakathi kwakho nodokotela wakho. Ngokulandela imiyalelo ngqo nokuya emitholampilo ngesikhathi, ungasilawula kangcono lesi simo.
Ukuze aqaphe impumelelo yokwelashwa, udokotela uzokwenza njalo ukuhlolwa komchamo ukuhlola izinga le-cystine emchameni. Uma kudingeka, uhlelo lokwelashwa luzolungiswa ngokufanele. Njengoba lesi kuyisimo sofuzo, kungaba ngumqondo omuhle futhi ukufuna ukwelulekwa ngofuzo uma uhlela ukuqala umndeni.
Umlayezo Wokuya Nawe Ekhaya
- Amatshe e-Cystine uhlobo lwetshe lezinso olubangelwa yisimo esingavamile, esifuzo esibizwa ngokuthi i-cystinuria.
- Nakuba lesi simo singesokuphila konke, singaphathwa kahle kakhulu ngokwelashwa okufanele kanye nokushintsha indlela yokuphila.
- Ukuphuza amanzi amaningi usuku lonke kuyindlela ebaluleke kakhulu nelula yokuvimbela ukwakheka kwamatshe.
- Kubaluleke kakhulu ukulandela ukudla okunosawoti omncane kanye namaprotheni ezilwane.
- Uma uzwa izimpawu ezifana nobuhlungu obukhulu emhlane wakho, ethangeni, noma esiswini esingezansi, noma igazi emchameni wakho, ungachithi isikhathi bese ubona udokotela ngokushesha .
- Landela imiyalelo kadokotela wakho kanye nemithi ngqo. Ungakhathazeki, ungaphila impilo enempilo ngalesi simo.
💬 Comments (0)
Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.
Engeza amazwana akho