Wake wacabanga ngobuhlungu bethambo obuzwa nje? Sivame ukungacabangi kakhulu ngamandla amathambo ethu. Kodwa cabanga, ithambo eliqinile emzimbeni wakho liyancibilika kancane kancane lisuka ngaphakathi, futhi esikhundleni salokho ligcwele into efana nezicubu ezibomvu ezifana nentambo. Yilolo hlobo lwesimo esikhuluma ngaso namuhla, i-Fibrous Dysplasia. Lesi yisifo esingavamile. Ungakhathazeki, sizoxoxa ngakho konke kalula nangokucacile.
Kalula nje, iyini i-Fibrous Dysplasia?
I-Fibrous Dysplasia yilapho izicubu zethu zamathambo ezinempilo neziqinile zithathelwa indawo yizicubu ezingavamile, ezine-fibrous (ezifana nesibazi). Ngamanye amazwi, lapho kufanele kube nethambo langempela, izicubu ezibuthakathaka nezinezintambo ziyathathelwa indawo. Kwenzekani? Ngenxa yokuthi izicubu ezintsha aziqinile njengethambo langempela, ithambo liba buthakathaka kakhulu. Lokhu kwenza kube lula ukuphuka (ukuphuka) kalula .
Nakuba lesi simo singase senzeke kunoma yiliphi ithambo emzimbeni, sivame ukubonakala kulezi zindawo ezilandelayo:
- I-Femur
- Ithambo lesifuba (i-tibia)
- Izimbambo
- Amathambo ekhanda kanye nobuso
- Ithambo lengalo engenhla (i-humerus)
Kodwa nansi into ebalulekile okufanele uyikhumbule. I-Fibrous Dysplasia iyisimo esingeyona umdlavuza (esingesihle). Lokho kusho ukuthi ayisabalali isuka kwelinye ithambo iye kwelinye. Lokho kuyimpumuzo enkulu, akunjalo?
Kunezinhlobo ezimbili eziyinhloko ze-Fibrous Dysplasia:
Odokotela bahlukanisa lesi sifo ngokwenani lamathambo emzimbeni athintekile. Ngokufanelekile, kunezinhlobo ezimbili eziyinhloko.
| Uhlobo lwesifo | Incazelo elula |
|---|---|
| I-Monostotic Fibrous Dysplasia | Kulolu hlobo, lesi sifo sithinta ithambo elilodwa kuphela . Lolu uhlobo oluvame kakhulu. Izimpawu zivame ukuba zincane. |
| I-Polyostotic Fibrous Dysplasia | Kulolu hlobo, lesi sifo sithinta amathambo amaningana.Lokhu kungaba yinkimbinkimbi kancane. Ngezinye izikhathi lesi simo sihambisana nesinye isimo esingavamile esibizwa ngokuthi i-McCune-Albright syndrome, esithinta amathambo, isikhumba kanye nesistimu yama-hormone. |
Ziyini izimpawu zalesi sifo? Uzibona kanjani?
Enye yezinto ezimangazayo nge-Fibrous Dysplasia ukuthi abanye abantu bangaba nayo ngaphandle kwezimpawu . Ake sithi wenza i-X-ray yento ethile bese itholakala ngengozi.
Kodwa uma kuvela izimpawu, zingaba kanje:
- Ubuhlungu bamathambo: Lolu uphawu oluyinhloko. Kumane nje ubuhlungu obungajabulisi, obubuhlungu obuhlala buvela endaweni efanayo. Ngezinye izikhathi lobu buhlungu bungakhula kakhulu lapho uhamba noma uphakamisa izinsimbi.
- Ukuphuka: Njengoba kushiwo ngaphambili, ngenxa yokuthi amathambo abuthakathaka, amathambo ngezinye izikhathi angaphuka kalula, ngisho noma ewile kancane noma eshaywe kanzima.
- Ukuma kwethambo kuyashintsha: Njengoba izicubu ezingavamile zikhula, ithambo lingase libonakale livuvukele. Lokhu kungabangela ukugoba okuncane uma umlenze ugobile, noma ushintsho oluncane esimweni sobuso uma uthambo lobuso ligobile.
- Kungase kube nokuvuvukala kwezimbambo okungenabuhlungu .
- Uma umgogodla uthintekile, kungase kube nokugoba komgogodla (i-scoliosis) .
- Uma amathambo ekhanda ethintekile, izinto ezifana namehlo avuvukele, ushintsho endaweni yamathambo omhlathi, ukunyakaza kwamazinyo, kanye nokuminyana kwamakhala kungenzeka.
Into ebalulekile ukuthi umuntu onesifo se-polyostotic kungenzeka kakhulu ukuthi abe nezimpawu nezinkinga kunomuntu onesifo se-monoostotic.
Kungani lokhu kwenzeka?
Lokhu kubangelwa ukuguquka kwezakhi zofuzo okubizwa ngokuthi i-GNAS1 emzimbeni wethu. Lokhu kwenzeka ngemva kokuba umntwana ekhulelwe esibelethweni. Ngenxa yalokhu kuguquka kwezakhi zofuzo, umsebenzi wamaseli abizwa ngokuthi ama-osteoblast, asiza ekukhuleni kwamathambo, uyaphazamiseka. Yilapho lezo zicubu ezibuthakathaka, ezine-fibrous ziqala ukwakheka esikhundleni sethambo eliphilile.
Odokotela abasazi kahle ukuthi yini ebangela lokhu kuguquka kwezakhi zofuzo.
Kodwa khumbula lokhu: I-Fibrous Dysplasia ayisona isifo esizuzwa njengefa. Lokhu kusho ukuthi uma umama noma ubaba enalesi sifo, ngeke sidluliselwe ezinganeni zabo. Kumane nje kuyishintsho lwezakhi zofuzo olungahleliwe.
Udokotela ukuthola kanjani lokhu?
Uma uya kudokotela onesifo samathambo esingapheli, uzoqala akuhlole ngokucophelela. Uzokubuza imibuzo eminingi, njengokuthi ubuhlungu bukuphi, isikhathi esingakanani bukhona, nokuthi buzizwa kanjani. Ngemuva kwalokho, angenza izivivinyo eziningana ukuqinisekisa ukuthi unesifo.
- Ukuhlolwa kwegazi noma komchamo: Lokhu kuhlola amazinga athile e-enzyme emzimbeni. Ngezinye izikhathi, amazinga aphezulu ala ma-enzyme angaba uphawu lokukhula kwezicubu okungavamile emzimbeni.
- Ukuhlolwa kwezithombe: Lokhu kubaluleke kakhulu.
- I-X-ray: I-X-ray ingabona kalula ukukhubazeka, ukwaphuka, kanye noshintsho esimweni samathambo.
- I-CT scan noma i-MRI scan: Lokhu kunganikeza isithombe esicacile nesiningiliziwe sethambo nezicubu ezizungezile.
- I-Biopsy: Uma udokotela esakungabaza, uzothatha ingxenye encane kakhulu yezicubu ezingavamile ngaphansi kwe-anesthesia bese eyihlola ngaphansi kwe-microscope. Lokhu kungaqinisekisa lesi sifo ngokuqiniseka okungu-100%.
Yiziphi izindlela zokwelapha lokhu?
Ukwelashwa kwe-Fibrous Dysplasia kuncike ezimpawini zakho, ubukhali besimo, nokuthi sithinta kanjani impilo yakho. Akukho ukwelashwa okulingana nakho konke.
Izindlela zokwelapha eziyinhloko yilezi:
1. Ukubheka: Uma ungenazo izimpawu noma ubuhlungu, udokotela wakho angase angakuniki noma yimiphi imithi, kodwa umane akucele ukuthi ubuye uzohlolwa ngezikhathi ezithile. Lokhu kusho ukubheka ukuze ubone ukuthi kukhona yini ushintsho esimweni sakho.
2. Imithi: Imithi ethile (ikakhulukazi ama-bisphosphonates) inganikezwa ukusiza ukuqinisa amathambo nokuvimbela ukuqhekeka. Lokhu kunganciphisa nobuhlungu bamathambo.
3. Ukuqinisa ithambo: Uma lesi simo sivela ethanjeni, ikakhulukazi emlenzeni wengane ekhulayo, kunganconywa ukusebenzisa izinsimbi ezikhethekile ukusiza ithambo likhule kahle futhi livimbele ukugoba.
4. Ukuhlinzwa:
- Uma ithambo liphuka (liphuka), kuzodingeka ukuhlinzwa ukuze lilungiswe.
- Uma ithambo libuthakathaka kakhulu, lisesimweni esingalungile, futhi libangela ubuhlungu obukhulu, izicubu ezingavamile zingasuswa bese kushintshwa ithambo eliphilile noma kufakwe izinduku zensimbi ukuze kuqiniswe ithambo.
Kufanele ubonane nini nodokotela?
Uma ubuhlungu obungapheli emathanjeni ngaphandle kwesizathu esibonakalayo , ungabushayi indiva. Qiniseka ukuthi ubona udokotela bese ukhuluma ngakho.
Uma usuvele wazi ukuthi une-Fibrous Dysplasia, khuluma nodokotela wakho ngokushesha uma:
- Uma uzizwa sengathi izimpawu zakho ziya ziba zimbi kakhulu.
- Uma unomuzwa wokuthi ukwelashwa kwakho kwamanje akusizi.
Isimo esiphuthumayo!
Ngenxa yokuthi i-Fibrous Dysplasia yenza amathambo abe buthaka, kungenzeka ukuthi uphuke ithambo kunamanye. Ngakho-ke, uma uwa ngokuzumayo, ushaye ithambo kakhulu, noma uhileleke engozini yemoto, hamba ngqo eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela esiseduze ngaphandle kokulibala. Ngoba noma kungabukeki sengathi kufana nalokhu ngaphandle, kungase kube nokuphuka ngaphakathi.
Ungaphila kanjani nalesi sifo?
Ayikho impendulo eyodwa kulo mbuzo, njengoba i-Fibrous Dysplasia ithinta umuntu ngamunye ngendlela ehlukile. Kodwa into eyodwa eqinisekile: yisimo esingamahlalakhona, esihlala isikhathi eside esingelapheki .
Kodwa asikho isidingo sokwesaba noma sokudabuka ngakho. Lesi akusona isifo esibulalayo. Ngokwelashwa okufanele kanye nokuphathwa, umthelela walesi sifo empilweni yakho ungalawulwa kakhulu. Ungase ungadingi ngisho nokwelashwa. Ngisho noma kudingeka ukwelashwa, izindlela zezokwelapha zanamuhla zingakusiza ukulawula ubuhlungu, ukuvimbela ukuphuka kwamathambo, futhi uphile impilo evamile nejabulisayo.
Uma unalesi sifo, khuluma nodokotela wakho ngokukhululekile ukuze uqonde ukuthi yini ongayilindela esikhathini esizayo ngokusekelwe esimweni sakho nokuthi yiziphi izindlela zokwelapha ezikulungele.
Umlayezo Wokuya Nawe Ekhaya
- I-Fibrous Dysplasia yisifo esingavamile, esingesona umdlavuza lapho izicubu ezibuthakathaka, ezine-fibrous zikhula khona esikhundleni samathambo aphilile.
- Lokhu kwenza amathambo abe buthaka, kwandisa ingozi yobuhlungu nokuqhekeka.
- Lesi akusona isifo esizuzwa njengefa, kodwa sibangelwa ukuguquka kwezakhi zofuzo okwenzeka esibelethweni.
- Abanye abantu bangase bangabi nazimpawu futhi bangase batholakale ngengozi.
- Uma ubuhlungu obungapheli emathanjeni, kubaluleke kakhulu ukungabunaki futhi ufune iseluleko sezokwelapha.
- Nakuba kungelapheki ngokuphelele, izimpawu zingalawulwa futhi impilo evamile ingaphilwa ngemithi, ukuhlinzwa, kanye nezinye izindlela zokwelapha.
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