Ingabe imisipha yakho iyawohloka kancane kancane? Ingabe lokhu kungaba yi-Primary Lateral Sclerosis (PLS)?

Ingabe ngezinye izikhathi uzizwa sengathi imilenze yakho isinda kancane, sengathi yenziwe ngamatshe? Noma uzizwa sengathi ulahlekelwa yibhalansi yakho lapho uhamba, noma izitho zakho zilahlekelwa amandla kancane kancane? Uma lezi zimpawu zingaveli ngokuzumayo, kodwa zikhula kancane kancane, kungaba kubalulekile ukuthi uqaphele lesi simo esibizwa ngokuthi i-Primary Lateral Sclerosis (PLS). Ungakhathazeki, sizoxoxa ngakho konke ngamagama alula.

Kalula nje, iyini i-primary lateral sclerosis (PLS)?

I-Primary Lateral Sclerosis, noma i-PLS ngamafuphi, yisifo esithinta imizwa nemisipha yethu. Sibangela ukuthi imisipha yethu iqine kancane kancane, noma kancane kancane.

Ngokuvamile, lezi zimpawu ziqala emilenzeni yakho. Ngokuhamba kwesikhathi, lobu buthakathaka nokuqina kungasakazekela kwezinye imisipha emzimbeni wakho. Lesi yisimo esiqhubekayo , okusho ukuthi izimpawu ziya ngokuya ziba zimbi ngokuhamba kwesikhathi.

Akukho ukwelashwa okuqondile kwalesi simo (i-PLS), ngakho-ke ukwelashwa kuhloselwe kakhulu ukulawula izimpawu nokukusiza ukuthi wenze imisebenzi yansuku zonke kalula. Isibonelo, ukusebenzisa ithuluzi lokusiza njengenduku noma i-walker .

Lesi yisimo esingavamile kakhulu, okusho ukuthi asivamile ukubonwa emphakathini.

Uyini umehluko phakathi kwe-PLS ne-ALS?

Cishe uke wezwa ngesimo esibizwa ngokuthi i-Amyotrophic Lateral Sclerosis (ALS) . Nakuba zombili lezi zifo zihilela imizwa nemisipha, kunomehluko ocacile phakathi kwalezi ezimbili. Ukuze siqonde lokhu, ake siqale sibheke indlela imizimba yethu elawula ngayo ukunyakaza.

Kukhona uhlobo olukhethekile lweseli lemizwa elithwala imiyalezo esuka ebuchosheni bethu iye emisipheni yethu, esilibiza ngokuthi ama-motor neurons . Kunezinhlobo ezimbili zalezi:

1. Ama-Upper Motor Neurons (UMN): Lawa 'yizintambo eziyinhloko' ezithwala imiyalezo esuka ebuchosheni iye emgogodleni.

2. Ama-Lower Motor Neurons (LMN): Lawa 'ama-sub-neurons' athwala imiyalezo ngqo esuka emgogodleni iye emisipheni.

Manje kubaluleke kakhulu ukuqonda lo mehluko.

Izimpawu zokuqala ze-ALS zingafana kakhulu neze-PLS. Ngakho-ke ngezinye izikhathi udokotela angase akuhlole kuqala ukuthi une-PLS bese eyishintsha ibe yi-ALS lapho kuvela izimpawu ezithinta ne-LMN. Ngenxa yalesi sizathu, ukuze kuqinisekiswe i-PLS ngokuqinisekile, izimpawu kudingeka zibonwe okungenani iminyaka emithathu kuya kwemine .

Ziyini izimpawu ze-PLS?

Izimpawu ze-PLS ziqala kancane kakhulu. Nazi ezinye zezimpawu zokuqala ongase uzibone:

• Ukuqina kwemisipha emilenzeni.
• Ubuthakathaka bemisipha emilenzeni.
• Ubunzima bokuhamba noma ukuba nenkinga yokugcina ibhalansi.
• Ukuqhaqhazela kwemisipha noma ukuqaqamba noma ukuqaqamba okubuhlungu.

Njengoba lesi sifo siqhubeka, kungase kuvele ezinye izimpawu:

• Ukuqina kwemisipha kanye nobuthakathaka eminweni, ezandleni nasezingalweni.
• Ubunzima bokulawula umchamo(Isidingo esiphuthumayo sokuchama kanye nokuvuza komchamo).
• Ubuhlungu emhlane nasentanyeni.

Ezimweni ezingavamile kakhulu, imisipha yolimi nayo ingathinteka. Kulesi simo, ungase ubone izimpawu ezifana nalezi:

• Inkulumo engacacile (i-Dysarthria).
• Ubunzima bokugwinya ukudla (i-Dysphagia).

Yini ebangela i-PLS?

Eqinisweni, asikazi imbangela eqondile ye-PLS kubantu abadala. Esikhathini esiningi, kwenzeka ngokungahleliwe, ngaphandle kwesizathu esibonakalayo.

Kodwa-ke, kukhona uhlobo olungavamile kakhulu lwe-PLS oluthinta izingane kanye nabantu abadala abasebasha. Lubangelwa ukuguquka kwezakhi zofuzo (ushintsho ku-DNA).

Into ebalulekile ukuthi i-PLS ayisona isifo esizuzwa njengefa. Lokhu kusho ukuthi ungayihlakulela ngisho noma kungekho muntu emndenini wakho oke waba nayo ngaphambili.

Ubani osengozini enkulu?

Noma ubani angaba ne-PLS. Kodwa-ke, iziguli zivame ukutholakala zine-PLS ezineminyaka engaba ngu-50. Kodwa-ke, ingakhula nakubantu abancane noma abadala kunalokho. Lesi simo sivame kakhulu kwabesilisa kunabesifazane .

Lesi simo sitholakala kanjani?

Ngemva kokufunda ngezimpawu zakho, udokotela wakho uzokwenza ukuhlolwa ngokomzimba nangokwezinzwa. Bangase futhi benze izivivinyo ukuze banqume ezinye izimo ezinezimpawu ezifana ne-PLS, njenge-ALS noma i-multiple sclerosis. Ezinye zalezi zivivinyo zifaka:

• Ukuhlolwa kwegazi: Hlola ezinye izimbangela.
• Ukuhlolwa kwe-electrodiagnostic: Lokhu kulinganisa ukuthi izinzwa zakho nemisipha yakho zisebenza kahle kangakanani.
• I-MRI scan: Thatha izithombe ezinemininingwane zobuchopho kanye nomgogodla ukuze ubone ukuthi zikhona yini ezinye izinkinga.
• Ukubhoboza i-Lumbar (umpompi womgogodla): Lokhu kuhilela ukuthatha inani elincane loketshezi emgogodleni wakho bese ulihlola ukuthi alinazo yini izinkinga.

Yiziphi izindlela zokwelapha?

Njengoba sesishilo ngaphambili, ayikho ikhambi eliqondile le-PLS. Ukwelashwa kuhloselwe ukulawula izimpawu nokukusiza ukuthi uphile ngokuzimela ngangokunokwenzeka.

• Imithi: Imithi inikezwa ukunciphisa ukuqina kwemisipha, ukukhubazeka, kanye nobunzima bokugwinya (isib. iBaclofen, iTizanidine, iQuinine, iDiazepam).
• Ukwelashwa ngokomzimba: Kunconywa ukuzivocavoca ukuze kuncishiswe ubuthakathaka bemisipha, kwandiswe ukuguquguquka, futhi kugcinwe ukuhamba kahle kwamalunga.
• Amadivayisi okusiza: Amadivayisi anjengenduku, i-walker , noma isihlalo sabakhubazekile asetshenziselwa ukukusiza ukuthi uzihambele wedwa.
• Ukwelashwa ngenkulumo: Uma unenkinga yokukhuluma, kungasiza.

Kufanele ubonane nini nodokotela?

Uma unomuzwa wokuthi ukuqina kwemisipha yakho noma ubuthakathaka kukhula kancane kancane, qiniseka ukuthi ubona udokotela wakho.

Futhi, uma usuvele utholakale une-PLS futhi umuthi owuthathayo wenza izimpawu zakho zibe zimbi kakhulu noma udala imiphumela emibi, tshela udokotela wakho ngalokho futhi.

Uma ulimele ngenxa yokuwa noma ingozi ngokuzumayo, hamba uye e-Emergency Treatment Unit (ETU) yesibhedlela ngokushesha.

Kuvamile ukuzizwa ucindezelekile njengoba amandla emisipha yakho ehla kancane kancane futhi ungakwazi ukwenza izinto owawuzenza. Uma uzizwa ucindezelekile ngalezi zinguquko zomzimba, ukukhuluma nomeluleki wezempilo yengqondo kungasiza.