Cabanga nje ukuthi ngokuzumayo uthola umkhuhlane omkhulu. Ngesikhathi esifanayo, kuvela amabhamuza abomvu, aluma kancane, futhi abuhlungu emzimbeni wakho, ezingalweni nasemilenzeni. Akukhululeki neze, futhi umzimba wakho uzizwa sengathi uyabuhlungu. Noma ubani angasaba uma ebona into efana nale, akunjalo? "Kwenzekeni ngokuzumayo?" Ungase ucabange. Namuhla, sikhuluma ngesimo esibangela izimpawu ezinjengalesi, esingavamile ezweni lakithi, kodwa okubaluleke kakhulu ukwazi ngaso. Lokhu kubizwa ngokuthi i-Sweet Syndrome kwezokwelapha.
Kalula nje, iyini i-Sweet Syndrome?
I-Sweet Syndrome yisifo sesikhumba esivuvukalayo. Akuvamile kakhulu. Uphawu oluyinhloko ukuqala komkhuhlane ngokuzumayo kanye nokuvela kwamaqhubu noma amaqhubu abuhlungu emzimbeni, ikakhulukazi ezingalweni, emilenzeni, esiqwini, entanyeni, noma ebusweni. Inelinye igama lezokwelapha, i-Acute Febrile Neutrophilic Dermatosis . Leli gama lizwakala liyinkimbinkimbi kancane, akunjalo? Masihlale silula.
- Okubukhali: Lokhu kusho ukuthi lokhu kuyinto eqala ngokuzumayo.
- I-Febrile: kusho ukuthi "ngomkhuhlane."
- I-Neutrophilic: Lokhu kusho ukuthi kuhileleke uhlobo lweseli elimhlophe legazi elibizwa ngokuthi 'i-Neutrophil', okuwuhlobo lweseli ohlelweni lokuzivikela lomzimba wethu. Ungabona ukunqwabelana okukhulu kwala maseli ngaphakathi kwala ma-blister.
- I-dermatosis: kusho isifo sesikhumba.
Ngakho-ke, kafushane nje, lesi yisimo sesikhumba esibangelwa amangqamuzana abizwa ngokuthi ama-neutrophils afika ngokuzumayo nomkhuhlane.
Ngezinye izikhathi, i-Sweet's Syndrome ingavela nakwezinye izimo zezokwelapha. Isibonelo, lesi simo sibonwe sinomdlavuza, izifo zamathumbu, noma ngesikhathi sokukhulelwa. Singase futhi sibe nomphumela omubi wemithi ethile esiyisebenzisayo.
Ingabe lesi simo sivamile? Ubani osengozini?
Cha, i-Sweet Syndrome iyisimo esingavamile kakhulu. Inani elincane lamacala abikiwe emhlabeni wonke. Ngakho-ke asikho isidingo sokukhathazeka uma uzwa ngakho.
Nakuba lesi simo singakhula kunoma ubani, sivame kakhulu kwabesifazane abaneminyaka ephakathi kuka-30 no-50. Kodwa-ke, lokho akusho ukuthi asinakukhula kwabesilisa noma kwamanye amaqembu eminyaka.
Yini ebangela i-Sweet Syndrome?
Eqinisweni, odokotela abakayitholi imbangela ethile yalokhu. Lokhu kusho ukuthi isikhathi esiningi kwenzeka ngaphandle kwesizathu. Kodwa-ke, odokotela bahlukanisa lesi simo ngezigaba ezintathu eziyinhloko ngokusekelwe endleleni esenzeka ngayo. Lokhu kuhlukaniswa nakho kuyasiza kakhulu ekwelapheni.
| Uhlobo | Incazelo elula |
|---|---|
| Okwakudala (uhlobo olujwayelekile) | Lolu uhlobo oluvame kakhulu. Lungenzeka uma luhambisana nesinye isimo sezokwelapha. Isibonelo, ukutheleleka komphimbo noma kokuphefumula (njengomkhuhlane noma umkhuhlane), ukutheleleka kwamathumbu (njengohudo), noma ngesikhathi sokukhulelwa. |
| Okuhlobene nomdlavuza (okuhambisana nezimo zomdlavuza) | Ngezinye izikhathi, lesi sifo singavela nohlobo oluthile lomdlavuza. Lokhu kubonakala ikakhulukazi kumdlavuza ohlobene negazi, isibonelo , i-Acute Myeloid Leukemia . Kodwa-ke, lokhu akusho ukuthi wonke umuntu othola i-Sweet Syndrome unomdlavuza. Lokhu kubaluleke kakhulu. |
| Okubangelwa izidakamizwa | Lesi simo singabangelwa nayiminye yemithi esiyisebenzisayo. Amanye ama-antibiotic, ama-painkiller (ama-NSAID), futhi ikakhulukazi umuthi obizwa ngokuthi i-G-CSF (Granulocyte Colony-Stimulating Factor) (lo umuthi owandisa ukukhiqizwa kwamaseli e-neutrophil emzimbeni) ungabangela lokhu. |
Yiziphi izimpawu eziyinhloko?
Izimpawu ze-Sweet Syndrome zivame ukuvela ngokuzumayo, zingakapheli izinsuku ezimbalwa. Ake sibheke ukuthi ziyini.
- Izinguquko zesikhumba: Lolu uphawu oluyinhloko nolusobala kakhulu.
- Amaqhubu abomvu noma amabhamuza abuhlungu avela ngokuzumayo ebusweni, entanyeni, ezingalweni, emilenzeni, noma esiqwini.
- La maqhubu aqala njengamaqhubu amancane, kancane kancane akhule abe makhulu, futhi angaze ahlangane ndawonye akhe isilonda esikhulu.
- Ngezinye izikhathi la maqhubu angagcwala uketshezi olufana nobovu.
- Izilonda zingavela nangaphakathi emlonyeni.
- Umkhuhlane: Umkhuhlane ophezulu, ovame ukuba ngaphezu kwama-degree Celsius angu-38 (100.4 Fahrenheit) , uyenzeka.
- Izinkinga ezivamile:
- Ubuhlungu bomzimba kanye nobuhlungu bemisipha.
- Ubuhlungu bamalunga.
- Ikhanda elibuhlungu.
- Ukuzizwa ukhathele kakhulu futhi ungenampilo (Ukukhathala).
- Sekukonke, umzimba uzizwa ungaphilile kahle.
Ingabe lokhu kungabangela ezinye izinkinga?
Yebo, ngezinye izikhathi i-Sweet Syndrome ayigcini esikhumbeni kuphela. Ingathinta nezinye izinhlelo zezitho zomzimba. Kodwa lokho futhi akuvamile.
Amehlo avame ukuthinteka.
- Kungase kube nokucasuka kwamehlo.
- Kukhona ithuba lokuthi ingcindezi engaphakathi kweso inganda futhi ibangele i-glaucoma .
- Ukulimala kwe-cornea nakho kungenzeka.
Ngaphezu kwalokho, akuvamile kakhulu ukuthi isimiso sezinzwa, izinso, noma amaphaphu nakho kungathinteka. Yingakho kubalulekile ukubona udokotela ngokushesha nje lapho kuvela izimpawu.
Udokotela ukubona kanjani lokhu?
Uma uya kudokotela onezimpawu ezinjengalezi, into yokuqala azokwenza ukulalela ngokucophelela izimpawu zakho nokuhlola umzimba wakho ngokucophelela, ikakhulukazi amabhamuza esikhumbeni sakho.
Ngemuva kwalokho, kungenziwa izivivinyo eziningana ukuqinisekisa ukuxilongwa.
- I-Skin Biopsy: Lolu vivinyo olubaluleke kakhulu. Kuthathwa ingxenye encane kakhulu yezicubu esilondeni sesikhumba bese ihlolwa ngaphansi kwe-microscope. Uma kukhona i-Sweet's Syndrome, isampula yezicubu izobonisa inani elikhulu lama-neutrophils.
- Ukuhlolwa kwegazi: Ukuhlolwa kwegazi kwenziwa ukuhlola inani eliphezulu lamaseli amhlophe egazi (ikakhulukazi ama-neutrophil) kanye nezimpawu zokuvuvukala.
Ngaphezu kwalokho, udokotela uzokubuza nganoma yiziphi izifo osuzitholile muva nje, imithi oyiphuzayo, kanye nezinye izimo zezokwelapha.
Iphathwa kanjani?
Izindaba ezinhle ukuthi kunezindlela zokwelapha eziphumelelayo ze-Sweet Syndrome.
Ngezinye izikhathi, lesi simo singathuthuka kancane kancane ngaphandle kokwelashwa. Kodwa-ke, ngenxa yokuthi izimpawu zinzima futhi kungase kube nezinkinga, odokotela bavame ukukunikeza ukwelashwa.
Ukwelashwa okuyinhloko uhlobo lwemithi ebizwa ngokuthi ama-corticosteroids . Lawa anikezwa njengamaphilisi. Imithi evame ukusetshenziswa kakhulu yimithi efana ne -Prednisone .
Le mithi yama-steroid isebenza ngokulawula impendulo yomzimba yomzimba esebenza ngokweqile kanye nokuvuvukala. Umkhuhlane, ubuhlungu, kanye nokuqubuka kwesikhumba kuzophela ngokushesha ezinsukwini ezimbalwa zokuqala le mithi.
- Ukwelapha imbangela eyinhloko:
- Uma i-Sweet Syndrome ibangelwa umuthi othile, izimpawu zizophela uma umuthi usuyekiwe.
- Futhi, uma lokhu kubangelwa ukutheleleka noma esinye isimo sezokwelapha (njengomdlavuza), kubalulekile ukwelapha leso simo esiyisisekelo.
Yini ongayilindela ngemva kokwelashwa?
Kwabaningi, izilonda zesikhumba ezibangelwa yi-Sweet Syndrome ziyaphola ngokuphelele ngaphandle kokushiya izibazi . Lokhu kuyinto enhle. Kodwa-ke, ngemva kokuba izilonda ziphole, kungase kube nokushintsha kombala wesikhumba kulezo zindawo (njengezindawo ezimnyama noma ezinsundu) ezingase zihlale izinyanga ezimbalwa. Ngokuhamba kwesikhathi, lokhu kuzonyamalala kancane kancane.
Izimpawu zivame ukuhlala amasonto ambalwa noma inyanga, kodwa ngokwelashwa, ukululama kuyashesha. Uma kukhona esinye isimo sezokwelapha esiyisisekelo, isikhathi sokululama singase sibe side kancane.
Into ebaluleke kakhulu ukuthi lesi sifo asithelelani. Okusho ukuthi, asidluliselwa kusuka komunye umuntu siye komunye ngokuthinta noma nganoma iyiphi enye indlela.
Kufanele ngimbone nini udokotela?
Lona umbuzo obaluleke kakhulu.
Uma uhlangabezana nanoma yiziphi izimpawu ezishiwo kulesi sihloko, ikakhulukazi umkhuhlane osheshayo, ohambisana nama-blister abomvu abuhlungu noma amaqhubu esikhumbeni sakho , ungakushayi indiva lokho "njengokuvamile." Qiniseka ukuthi ubona udokotela wakho ngokushesha okukhulu.
Ngokuthola lesi sifo kusenesikhathi nokuqala ukwelashwa okudingekayo, izimpawu zingalawulwa ngokushesha futhi izinkinga ezingaba khona zingavinjelwa.
Umlayezo Wokuya Nawe Ekhaya
- I-Sweet Syndrome yisimo esingavamile esibangela amabhamuza abomvu abuhlungu esikhumbeni, ahambisana nomkhuhlane ongazelelwe.
- Ngokuvamile asikho isizathu esiqondile salokhu, kodwa kungase kuhlotshaniswe nezifo ezithile, imithi, noma ezinye izimo zezokwelapha.
- Lesi akusona isifo esithathelwanayo, ngakho-ke asikho isidingo sokwesaba.
- Ukuhlolwa ngokomzimba ngudokotela kanye ne-biopsy yesikhumba kubalulekile ukuze kutholakale ukuthi unesifo.
- Lesi simo singalawulwa ngempumelelo enkulu ngemithi ebizwa ngokuthi ama-corticosteroids.
- Uma wena noma othile omaziyo eba nalezi zimpawu, funa iseluleko sezokwelapha ngokushesha.











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