Wake wesaba yini lapho ingane yakho ivele ibe namabala amancane abomvu-onsomi emilenzeni nasemaqakaleni ayo? Kungenzeka ukuthi ikhalaze ngobuhlungu besisu kanye nobuhlungu bamalunga. Kuvamile ukuthi noma yimuphi umzali akhathazeke uma ebona into efana nale. Kodwa isikhathi esiningi, akuyona into embi kangako . Lezi zimpawu zingabangelwa yisimo esibizwa ngokuthi iHenoch-Schönlein Purpura (HSP), noma njengoba manje sibizwa kanjalo, i-IgA Vasculitis. Ake sixoxe ngakho kalula.
Kalula nje, iyini iHenoch-Schönlein Purpura (HSP)?
I-Henoch-Schönlein Purpura (HSP), ngokwezokwelapha, uhlobo lwe-"Vasculitis." I-Vasculitis yilapho imithambo yegazi emzimbeni wethu, efana namapayipi amancane athwala igazi, ivuvukala ngaphakathi. Njengalapho isikhumba sethu sivuvukala lapho silimala, kukhona ukuvuvukala ngaphakathi kwemithambo yegazi.
Ku-HSP, lokhu kuvuvukala kwenzeka kakhulu emithanjeni yegazi emincane kakhulu ngaphansi kwesikhumba. Kodwa-ke, ngezinye izikhathi lo mphumela ungadlulela nasemithanjeni yegazi ezinso, emathunjini nasemalungeni.
Lokhu kwenzeka ngoba iphrotheni ekhethekile (i-antibody) ebizwa ngokuthi `(Immunoglobulin A)` noma `(IgA)`, eyingxenye yesimiso somzimba wethu sokuzivikela (okungukuthi, uhlelo olusivikela ezifweni), iqoqana emithanjeni yegazi. Uma `(IgA)` iqoqana ngale ndlela, imithambo yegazi yonakala, iyaqhuma, bese kuvuza igazi elincane ngaphansi kwesikhumba. Yingakho sibona amabala ansomi nabomvu ngaphandle. Njengokulimala okuncane.
Lesi simo sibizwa nangokuthi i-`(IgA) Vasculitis` ngoba i-antibody ye-`(IgA)` ihilelekile. Nakuba singakhula kubantu banoma yibuphi ubudala, sivame ukubonakala ezinganeni .
Into ebalulekile ukuthi i-HSP ngokuvamile ayisona isimo esibucayi. Iningi lezingane liyalulama ngokuphelele ngaphandle kokwelashwa. Kodwa-ke, ingaba nzima kakhulu kubantu abadala.
Yiziphi izimpawu esizibonayo?
Izimpawu ze-HSP zingathinta kakhulu isikhumba sengane, amalunga, amathumbu nezinso. Uphawu oluvelele nolusobala kakhulu amabala abomvu onsomi avela esikhumbeni. Ake sibheke lezi zimpawu ngokwehlukana.
| Isibonakaliso | Incazelo |
|---|---|
| Ukuqhuma kwesikhumba | Lesi yisibonakaliso esiyinhloko. Sibangela amabala abomvu noma ansomi aphakama kancane ebusweni besikhumba. Ngezinye izikhathi kuba namabala ambalwa, ngezinye izikhathi angaba maningi. Lawa ngokuvamile awalunywa noma awabuhlungu . Avame ukubonakala emilenzeni nasezinqeni zengane. |
| Ubuhlungu nokuvuvukala kwamalunga | Amalunga, ikakhulukazi amadolo namaqakala, ayavuvukala futhi abe buhlungu. Ingane ingase ibe nobunzima bokuhamba. |
| Isisu esibuhlungu | Ubuhlungu besisu bungase buvele buphele. Ezinye izingane zingase zihlanze futhi zicanuzele. |
| Ezinye izici | Akuvamile kakhulu ukuthi kubonakale igazi esitulweni noma igazi emchameni (umchamo obomvu/onsundu). Lokhu kungaba izimpawu zezinkinga zezinso noma zamathumbu. |
Kungani lokhu kwenzeka? Yiziphi izizathu?
I-HSP iyisifo esihlasela amasosha omzimba . Kalula nje, "ibutho" lomzimba wethu (amasosha omzimba) liqala ngephutha ukuhlasela imithambo yegazi yalo enempilo. Abacwaningi abakazi kahle ukuthi kungani lokhu kwenzeka.
Kodwa into eyodwa icacile: Cishe ama-50% ezingane ezithola i-HSP ziye zaba nokutheleleka kokuphefumula okuphezulu, njengomphimbo obuhlungu noma umkhuhlane, ezinsukwini ezimbalwa ngaphambi kokuba lezi zimpawu zivele .
Ezinye izinto ezingadala i-HSP (Triggers)
Ngezinye izikhathi, i-HSP ingenzeka futhi njengokusabela okungavamile kwesimiso somzimba sokuzivikela kulezi zinto ezilandelayo:
- Ukutheleleka ngamagciwane, isibonelo umphimbo obuhlungu.
- Ukutheleleka ngegciwane.
- Ukudla okuthile.
- Ukulunywa yizinambuzane.
- Eminye imithi.
- Ezinye izinhlobo zemithi yokugoma (lokhu akuvamile kakhulu).
Ubani okungenzeka kakhulu ukuthi athole lesi simo?
Nakuba i-IgA vasculitis ingenzeka kunoma yimuphi ubudala, amacala angaphezu kuka-90% abikwe ezinganeni ezineminyaka ephakathi kuka-3 no-10 .
Ezinye izinto eziyingozi yilezi:
- Umlando womndeni:Uma othile emndenini wakho eke waba ne-HSP ngaphambili, ingane yakho isengozini enkulu yokuba nayo.
- Ithonya lezakhi zofuzo: Lesi simo sitholakale sivame kakhulu kubantu bozalo lwaseYurophu nase-Asia.
Ingabe zikhona izinkinga ezingase zivele ngenxa ye-HSP?
Iningi labantu liyalulama ngokuphelele phakathi nenyanga noma ezintathu ngaphandle kokwelashwa. Ngezinye izikhathi lesi sifo singaphinde sibuye, kodwa lokho kuvame ukuxazululeka ngokwaso.
Kodwa-ke, akuvamile, ikakhulukazi phakathi kwabantu abadala, ukuthi i-HSP ingaba yingozi futhi ibangele izinkinga.
- Ukulimala kwezinso: Isifo sezinso sesikhathi eside singaba khona. Lena inkinga enkulu okufanele uyiqaphele ku-HSP.
- Ukopha emathunjini.
- Ukulimala noma ukuvaleka kwamathumbu.
- Umfutho wegazi ophezulu ngesikhathi sokukhulelwa (kwabesifazane).
Ukuthola kanjani lokhu, Dokotela?
Uma uyisa ingane yakho kudokotela wezingane, izoqala ngokuyihlola ngokucophelela, ikakhulukazi ibheke noma yikuphi ukuqubuka kwesikhumba kanye namalunga avuvukele. Ngemuva kwalokho, izokubuza ngezimpawu zengane yakho kanye nanoma yiziphi izifo zakamuva.
Ukuze kuqinisekiswe ukuxilongwa nokukhipha ezinye izimo zezokwelapha, udokotela angase acele ukuhlolwa okuthile.
- Ukuhlolwa Komchamo: Ukuze kutholakale ukuthi izinso zithintekile yini, umchamo uhlolwa igazi noma amaprotheni.
- Ukuhlolwa kwegazi: Ukuhlola ukutheleleka noma ezinye izinkinga emzimbeni.
- I-ultrasound yezinso: Hlola isimo sezinso.
- I-ultrasound yesisu: Thola imbangela yobuhlungu besisu.
- Ukuhlolwa kwesikhumba: Kwezinye izimo, kuthathwa ingxenye encane kakhulu yesikhumba endaweni lapho kukhona khona i-mole bese ihlolwa ukuze kuqinisekiswe ukuthi ikhona yini imbangela.
- Ukuhlolwa kwezinso: Ukuhlolwa okwenziwa kuphela uma kukhona izinsolo zomonakalo omkhulu wezinso.
Yiziphi izindlela zokwelapha i-HSP?
Esikhathini esiningi, i-HSP ayidingi ukwelashwa okukhethekile. Into eyinhloko ukuphatha izimpawu ekhaya.
Uma uzwa ubuhlungu bamalunga nokuvuvukala, ungathatha i-paracetamol (Tylenol®) noma i-NSAID pain reliever (Advil®) njengoba kuqondiswe udokotela wakho.
Kodwa-ke, uma izimpawu ezifana nobuhlungu besisu zinzima, udokotela angase akunikeze umuthi we-steroid njenge-prednisone. Uma ukuqubuka kwesikhumba nezinye izimpawu kuqhubeka, qiniseka ukuthi ubona udokotela wengane yakho.
Khumbula, i-HSP ivame ukuba yisimo esingesihle esizixazulula sodwa. Kodwa akuvamile, ukuthi ingabangela izinkinga ezinkulu, okuhlanganisa nezinkinga zezinso namathumbu. Ngakho-ke, ezinye izingane kungadingeka zithathe imithi ukuze amasosha omzimba azo agcine amasosha omzimba esebenza kahle. Khuluma nodokotela wakho ngale mithi kanye nemiphumela yayo emibi.
Kufanele simbone nini udokotela?
Kungcono ukubona udokotela ngokushesha nje lapho ingane yakho inalezi zimpawu. Futhi, uma izimpawu ezilandelayo zivela ngesikhathi sokwelashwa noma ngesikhathi isifo sisalulama, bona udokotela wakho futhi.
| Isikhathi sokuthola iseluleko sezokwelapha ngokushesha | |
|---|---|
| 1. | Uma kukhona ukuvuvukala okungavamile. |
| 2. | Uma ingane isezinhlungwini noma ingakhululekile. |
| 3. | Uma izimpawu zihlala isikhathi esingaphezu kwamasonto ayi-12. |
| 4. | Uma izimpawu ziba ngcono bese ziphinde zivele. |
| 5. | Uma izimpawu ziba zimbi kakhulu usuku nosuku, esikhundleni sokuba zibe ngcono. |
I-HSP akuyona inkinga yokuphila konke. Ivame ukuphela phakathi nenyanga noma ezintathu. Ezinye izingane zingaba nesigameko sesibili, kodwa izimpawu ngokuvamile azibi kakhulu.
Okokugcina, i-HSP ingadala ubuhlungu nokungakhululeki kwengane yakho. Kungaba nzima kakhulu ngabazali ukubona ingane yabo isezinhlungwini. Kodwa khumbula, iningi lezingane liyalulama ngokuphelele ngaphandle kwezinkinga zesikhathi eside.Udokotela kungase kudingeke alandelele ingane isikhathi esithile ukuze ahlole isimo sezinso. Lokhu kubaluleke kakhulu.
Umlayezo Wokuya Nawe Ekhaya
- I-Henoch-Schönlein Purpura (HSP) yisimo lapho imithambo yegazi emincane engaphansi kwesikhumba ivuvukala khona, okubangela amabala abomvu onsomi emilenzeni nasemaqakaleni.
- Lokhu kuvame ukubonakala ezinganeni futhi ngokuvamile akuyona inkinga enkulu.
- Izimpawu ezifana nobuhlungu bamalunga kanye nobuhlungu besisu nazo zingase zivele ngalokhu.
- Iningi lezingane liyalulama ngokuphelele zingakapheli izinyanga ezingu-1-3 ngaphandle kokwelashwa okukhethekile.
- Kubaluleke kakhulu ukubona udokotela ngokushesha uma ubona la mabala esikhumbeni sengane yakho, njengoba engavamile ukuthinta izinso.
- Kubalulekile ukulandela imiyalelo kadokotela nokuhlolwa njalo.











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