Ɛyɛ ade a ɛfata sɛ mogya bɛtɔ na agyae mogya tu bere a yɛapirapira no. Ɛyɛ yɛn nipadua no ahobammɔ afiri ankasa. Nanso, sɛ mogya a ɛretu wɔ nipadua no ntini mu mpɛn pii a ntease biara nnim a, ɛyɛ asɛm a ɛhaw adwene. Titiriw sɛ wokɔ so tu nyinsɛn bere a wonyinsɛn a, ebia nea ɛde ba ne tebea a wɔfrɛ no Antiphospholipid Syndrome (APS) yi, a yɛrebɛka ho asɛm nnɛ no.
Dɛn ne APS kɛkɛ?
Sɛ yɛbɛka no tiawa a, Antiphospholipid Syndrome (APS) yɛ tebea a ɛma wo nipadua no tumi yɛ mogya a ɛtɔ sen sɛnea ɛte daa. Ɛtɔ mmere bi a nnuruyɛfo frɛ no Antiphospholipid antibody syndrome.
Saa mogya a ɛtɔ yi betumi de ɔhaw ahorow a emu yɛ den a ɛde nkwa to asiane mu mpo aba, te sɛ akisikuru . Tebea no nso ma asiane a ɛwɔ hɔ sɛ nyinsɛn betumi atu ne nsɛnnennen afoforo a ɛba bere a wɔyem no yɛ kɛse.
APS yɛ yare a nipadua no tumi ko tia nyarewa ankasa . Fa no sɛ, yɛwɔ ahobammɔ nhyehyɛe bi wɔ yɛn nipadua mu te sɛ asraafo dɔm. Yɛfrɛ no nipadua no mu tumi a ɛko tia nyarewa. N’adwuma ne sɛ ɛbɛbɔ yɛn ho ban afi mmoawa ne nyarewa a ɛde nyarewa ba ho. Nanso wɔ saa yare a nipadua no tumi ko tia nyarewa yi mu no, nea ɛba ne sɛ yɛn ankasa ahobammɔ nhyehyɛe no di mfomso fi ase tow hyɛ nkwammoaa pa a ɛwɔ yɛn ankasa nipadua mu no so.
Dɛn ne tebea yi ho sɛnkyerɛnne?
Ebia nnipa binom a wɔwɔ APS no benya nsensanee tuntum wɔ wɔn honam ani a ɛte sɛ asau. Wɔ aduruyɛ mu frɛ eyi livedo reticulitis . Nanso, nnipa dodow no ara a wɔwɔ APS no nnya yare no ho sɛnkyerɛnne biara kosi sɛ wobenya mogya a ɛbɛtɔ anaasɛ wobenya ɔhaw bi bere a wɔyem no.
Eyinom ne sɛnkyerɛnne ahorow a ebetumi aba sɛ mogya tuo a. Ɛsɛ sɛ wohwɛ yiye paa wɔ eyinom ho.
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛmu |
|---|---|
| Koko mu yaw | Ebetumi afi mogya a atɔ wɔ koma anaa ahurututu mu na ɛde aba. |
| Ɔhome a ɛyɛ den (dyspnea) . | Ebetumi afi mogya a ɛtɔ wɔ ahurututu mu (ahurututu mu ntini a ɛyɛ mmerɛw) mu titiriw. |
| Ti a ɛtaa yɛ no yaw | Ebia ɔhaw bi wɔ mogya ntini a ɛkɔ amemene no mu no mu. |
| Ɛyaw a ɛba mpofirim | Ɛyaw a ɛba mpofirim wɔ nsa, nan, akyi, kɔn, anaa anom. |
| Ɛhohoro anaasɛ ɛyɛ kɔkɔɔ | Ebetumi afi mogya a ɛtɔ, titiriw wɔ abasa anaa nan mu. |
| Yafunu mu yaw | Ebetumi afi mogya a ɛtwetwe ntini a ɛde mogya kɔ yafunu mu akwaa ahorow no mu no mu aba. |
Nea ɛho hia sen biara: Mogya a ɛtwetwe no yɛ tebea a egye ntɛmpɛ a ɛde ne nkwa to asiane mu. Sɛ wowɔ adwenem naayɛ bi sɛ mogya atɔ wo mu a, kɔ ayaresabea dwumadibea a ɛhwɛ ntɛmpɛ so (ETU) a ɛbɛn wo ntɛm ara.
Wɔ saa sɛnkyerɛnne ahorow yi akyi no, APS nso tumi de sɛnkyerɛnne ahorow bi a yentumi nhu anaa yɛnte nka aba.
- Mogya mu mogya mu nkwammoaa a ɛso tew.
- Mogya a ɛtɔ mogya mu.
- Koma mu ntini a ɛnyɛ ne kwan so.
Dɛn nti na eyi rekɔ so?
Antiphospholipid Syndrome ba bere a wo nipadua mu tumi a ɛko tia nyarewa no di mfomso fi ase yɛ antibody bi a ɛyɛ soronko no. Mpɛn pii no, nipadua mu nkwammoaa a ɛko tia nyarewa yɛ protein soronko a ɛhwehwɛ mmoawa ne nneɛma a ɛma yɛn ho yɛ hyew a ɛkɔ yɛn nipadua mu na ɛsɛe. Wɔte sɛ robɔt ahorow a wɔde bɔ wɔn ho ban.
Nanso wɔ obi a ɔwɔ APS mu no, saa nnuru a ɛko tia nyarewa yi a nipadua no mu tumi a ɛko tia nyarewa na ɛyɛ no tow hyɛ protein ahorow a ɛbata phospholipids (srade bi) ho wɔ yɛn ankasa nkwammoaa mu. Saa ntua yi sɛe phospholipids no, na ɛma ɛyɛ mmerɛw sɛ ɛbɛbata ho na ayɛ mogya a ɛtɔ.
Nnuru a ɛko tia nyarewa ahorow atitiriw abiɛsa na ebetumi ama wɔanya APS:
- Lupus aduru a ekum mogya a ɛtwetwe mogya
- Anticardiolipin a wɔde ko tia koma
- Glycoprotein a ɛko tia B2 1
Obi a ɔwɔ APS betumi anya nnuru a ɛko tia nyarewa yi biako, abien, anaa abiɛsa no nyinaa. Nanso nea ɛyɛ nwonwa kɛse mpo ne sɛ ebia nnipa binom wɔ saa nnuru a ɛko tia nyarewa yi nanso wonnya APS ho sɛnkyerɛnne biara da. Abenfo da so ara nnim nea ɛkanyan yɛn nipadua mu tumi a ɛko tia nyarewa no ma ɛyɛ nnuru a ɛko tia nyarewa a mfomso wom yi ankasa.
Hena na ɔwɔ asiane kɛse mu ma tebea yi?
Obiara betumi anya APS. Nanso, ebia wobɛkɔ asiane kɛse mu kakra sɛ wo:
- Sɛ woyɛ ɔbea a .
- Sɛ woadi fi mfe 30 kosi 40 a.
- Sɛ wowɔ nyarewa afoforo a nipadua no tumi ko tia nyarewa, te sɛ lupus anaa ntini mu yare a.
- Sɛ w’abusuafoɔ a wɔbɛn wo paa no mu baako (awofoɔ, nananom) wɔ APS a.
Nsɛnnennen bɛn na ebetumi aba esiane APS nti?
Antiphospholipid syndrome betumi de nsɛnnennen a emu yɛ den aba, ɛtɔ mmere bi a edi awu. Nsɛnnennen a emu yɛ den sen biara no ba bere a mogya a ɛtwetwe no hyehyɛ na esiw ntini a ɛde mogya kɔ wo nipadua akwaa a ɛho hia no mu no ano no.
- Amemene: ɔyare a ɛma obi hwe ase
- Koma: Koma mu yare (thrombosis) .
- Ahurututu: Mogya ntini a ɛwɔ ahurututu mu a esiw (pulmonary embolism) .
- Asaabo: Asaabo a ɛsɛe
Sɛ wunyinsɛn a, mogya a ɛtwetwe a esiw aduannuru a ɛkɔ awotwaa no mu no betumi ama nyinsɛn no atu. Ɛma asiane a ɛwɔ hɔ sɛ obi benya preeclampsia, tebea a mogya mmoroso ba bere a wɔyem no nso yɛ kɛse.
Catastrophic antiphospholipid syndrome (CAPS) yɛ APS ho haw a ɛntaa nsi nanso ɛyɛ aniberesɛm. Ɛyɛ tebea a ɛma mogya tu wɔ nipadua no akwaa pii mu wɔ nna bi mu. Nnipa a wonya saa tebea yi mu bɛyɛ fã wuwu. Nanso, CAPS ba nnipa a wɔwɔ APS no mu nea ennu 1% mu.
Mpɛn pii no, APS nnya wo nkwa nna so nkɛntɛnso. Nanso, sɛ mogya a ɛtɔ sɛe akwaa bi a ɛho hia, titiriw wɔ tebea te sɛ CAPS mu a, ebetumi akum obi.
Ɔkwan bɛn so na oduruyɛfo tumi hu yare yi pɛpɛɛpɛ?
Mpɛn pii no, wohu APS bere a mogya a ɛtɔ gu nipadua no mu anaasɛ bere a nyinsɛn agu mpɛn pii akyi no. Ebia nnipa binom wɔ antiphospholipid antibodies nanso wonnya sɛnkyerɛnne biara da.
Oduruyɛfo bi nam mogya mu nhwehwɛmu so bɛkyerɛ sɛ wowɔ APS anaa . Wɔbɛfa wo mogya no bi na wɔahwɛ sɛ nnuru a ɛko tia nyarewa ahorow abiɛsa a yɛadi kan aka ho asɛm no wɔ hɔ anaa. Sɛ wobetumi asi yare no so dua a, anyɛ yiye koraa no, ɛsɛ sɛ mogya mu nhwehwɛmu biako hu sɛ obi anya bi mprenu, na ɛda ntam bɛboro asram abiɛsa.
Dɛn ne ayaresa ahorow a wɔde sa eyi?
Wo duruyɛfo bɛkamfo ayaresa ahorow a ɛbɛtew asiane a ɛwɔ hɔ sɛ mogya bɛtɔ no so. Ayaresa a wɔtaa yɛ ne nnuru a ɛma mogya yɛ mmerɛw, anaa nnuru a ekum mogya a ɛtwetwe .
| Nnuru ahorow a wɔde di dwuma | Sɛnea wɔde di dwuma na wɔyɛ adwuma |
|---|---|
| Ayaresa a wɔde ma wɔ ɔkwan a ɛkɔ akyiri so | |
| Heparin a wɔde di dwuma | Eyi yɛ aduru a wɔde fa ntini mu (IV) a sɛ wɔde wo kɔ ayaresabea a, ɛboa ma mogya a ɛretu no tew. |
| Warfarin a wɔde di dwuma | Eyi yɛ aduru a wode fa w’ano nom. Ɛma mogya no yɛ teateaa na esiw mogya a ɛbɛtɔ foforo ano. |
| Aspirin a wɔde di dwuma | Ebia wo duruyɛfo bɛkamfo akyerɛ sɛ nom aspirin a ɛba fam na amma mogya a ɛbɛtɔ wo ntini mu. |
| Ayaresa a wɔde di dwuma bere a wɔyem | |
| Enoxaparin a wɔde di dwuma | Eyi yɛ aduru a wɔde twitwiw nipadua no honam ani. Wɔtaa kamfo kyerɛ sɛ ɛka aspirin a wɔmfa nni dwuma pii ho na amma nyinsɛn no antu. |
| immunoglobulin a wɔde fa ntini mu (IVIG) . | Saa ayaresa yi a wɔde fa ntini mu no hwɛ sɛnea nipadua no mu tumi a ɛko tia nyarewa no yɛ adwuma na ɛtew asiane a ɛwɔ hɔ sɛ nyinsɛn betumi atu no so. |
| Nnuru a wɔfrɛ no corticosteroids | Saa nnuru yi brɛ ɔfe a ɛwɔ nipadua no mu ase na ɛhwɛ sɛnea nipadua no mu tumi a ɛko tia nyarewa no yɛ adwuma boro so no so. |
Sɛ woanyinsɛn a, saa ayaresa yi yɛ nea asiane biara nni ho ma wo ne wo ba no, enti ɛho nhia sɛ wohaw wo ho wɔ ho.
Momma yɛnhu nsunsuanso bɔne a nnuru a ɛma mogya yɛ mmerɛw de ba nso.
Sɛ wonom nnuru a ɛma mogya tu a, ɛda adi sɛ mogya bɛtɔ wo nipadua mu. Enti ɛsɛ sɛ wohwɛ yiye paa wɔ saa sɛnkyerɛnne ahorow yi ho. Sɛ wowɔ eyinom mu bi a , wo ne wo duruyɛfo nkasa ntɛm ara.
- Mogya a ɛtɔ fi anom anaa hwene mu a ntease biara nnim .
- Mogya a ɛtɔ sen sɛnea ɛte bere a obi rekɔ brayɛ mu.
- Ɔfe a ɛyɛ kɔkɔɔ a ɛyɛ hare anaa kɔfe a wɔayam no kɔla .
- Mogya kɔkɔɔ a ɛhyerɛn wɔ nsu mu anaasɛ nsu tuntum a wɔde tar ayɛ .
- Yafunu mu yaw kɛse anaa tiyɛ a emu yɛ den .
- Nsakrae a ɛba mpofirim wɔ anisoadehu mu .
- Nkate a ɛyera mpofirim wɔ nsa anaa nan mu .
Nneɛma a ɛsɛ sɛ wususuw ho bere a wo ne APS te no
Ade a ɛho hia sen biara bere a wo ne APS te no ne sɛ wubesiw mogya a ɛbɛtɔ no ano. Eyi nti, ɛho hia sɛ wɔnom nnuru a ɛma mogya yɛ mmerɛw no yiye.
Nea ɛka ho no, ɛho hia sɛ wudi akwahosan tebea afoforo a ɛma asiane a ɛwɔ hɔ sɛ mogya bɛtɔ wo no yɛ kɛse no so. Sɛ wowɔ saa tebea horow yi bi a, wo ne wo duruyɛfo nkasa na ma wodi so:
- Asikyireyareɛ
- Mogya mmoroso
- Cholesterol a ɛdɔɔso
- Obolo
- Nyarewa afoforo a nipadua no tumi ko tia nyarewa
Sigaretnom ma asiane a ɛwɔ hɔ sɛ mogya bɛtɔ no yɛ kɛse, titiriw ma obi a ɔwɔ tebea bi te sɛ APS.
So ɛsɛ sɛ wohwɛ yiye wɔ aduan ne anonne ho?
Mpɛn pii no, ɛho nhia sɛ nnipa a wɔwɔ APS di aduan titiriw bi akyi. Nanso, sɛ worenom aduru Warfarin , a, ɛsɛ sɛ wohwɛ yiye wɔ nnuan a vitamin K (nhabannuru a ɛyɛ ahabammono tuntum te sɛ akutu) pii wom ho. Sɛ wudi nnuan a vitamin K pii wom prɛko pɛ a, ebetumi ama asiane a ɛwɔ hɔ sɛ mogya bɛtɔ wo no ayɛ kɛse. Enti bisa wo duruyɛfo no afotu.
Afei nso, bisa wo duruyɛfo no nsanom ho asɛm. Nsã ma mogya no yɛ teateaa, enti sɛ wɔde ka nnuru a ɛma mogya yɛ mmerɛw ho a, ebetumi ama nkɛntɛnso no ayɛ kɛse.
Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?
Sɛ worenom nnuru a ɛma mogya tu a, ɛsɛ sɛ wokɔ wo duruyɛfo nkyɛn daa kɔyɛ wo mogya mu nhwehwɛmu na ama woahwɛ ahu sɛ wo mogya a ɛtwetwe no dodow a ɛfata no mu.
Sɛ wowɔ anidaso sɛ wubenyinsɛn a, ɛho hia yiye sɛ wudi kan ne wo duruyɛfo kasa fa ho na wunya afotu.
Bere bɛn na ɛsɛ sɛ mekɔ Dwumadibea a Ɛhwɛ Nneɛma a Ɛho Hia Ntɛmntɛm (ETU)?
Kɔ ayaresabea no Dwumadibea a Ɛhwɛ Nneɛma a Ɛho Hia Ntɛmntɛm (ETU) ntɛm ara:
- Misusuw sɛ mogya atɔ wo.Sɛ ɛba a.
- Sɛ mogya a ɛretu ho sɛnkyerɛnne biara da adi a.
- Sɛ mogya retu wo a wuntumi nni so a .
Nkrasɛm a Wɔde Kɔ Fie
- Antiphospholipid Syndrome (APS) yɛ tebea a ɛma asiane a ɛwɔ hɔ sɛ mogya bɛtɔ no yɛ kɛse efisɛ w’ankasa nipadua mu ahoɔden a ɛko tia nyarewa no tow hyɛ wo nipadua so.
- Eyi nyɛ biribi a ɛsɛ sɛ wosuro, na wobetumi adi so yiye denam ayaresa a ɛfata (titiriw nnuru a ɛma mogya yɛ mmerɛw) so.
- Ɛwom sɛ nyinsɛn a woyi gu ne nsɛnnennen afoforo betumi aba wɔ nyinsɛn mu de, nanso wobetumi awo mmofra a wɔwɔ apɔwmuden wɔ aduruyɛfo hwɛ a ɛfata ase.
- Sɛ wuhu sɛnkyerɛnne ahorow a ɛkyerɛ sɛ mogya atɔ wo, te sɛ wo koko mu yaw, ɛyɛ den sɛ wobɛhome, anaa wo nan a wohoro a, bu no sɛ ɛyɛ ntɛm na kɔ ayaresabea ntɛm ara.
- Ɛho hia yiye sɛ wudi wo duruyɛfo akwankyerɛ akyi pɛpɛɛpɛ na wokɔhwɛ wo daa.











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