So wo ba no taa yare? Ebetumi ayɛ neutropenia a ɛkyinkyini.

So wo ba ketewa no nya atiridiinini, n’ano mu kuru, anaa ne menewa mu yaw nna koro no ara ɔsram biara? So yare biako kɔ, na adapɛn abien anaa abiɛsa akyi na ɛsan ba? Ebia woresusuw sɛ, "Me ba no nipadua mu ahoɔden a ɛko tia nyarewa no ayɛ mmerɛw." Yiw, ebia ɛno yɛ nokware. Nanso nea enti a yare a ɛkyinkyini yi ba no betumi ayɛ tebea a ɛntaa nsi koraa. Ɛnnɛ, yɛreka tebea a ɛte saa biako ho asɛm, cyclic neutropenia.

Sɛ yɛbɛka no tiawa a, dɛn ne cyclic neutropenia?

Sɛ yɛbɛte eyi ase a, ɛsɛ sɛ yedi kan hu ɔsraani bi a ɔwɔ yɛn mogya mu ho asɛm. Saa ɔsraani no din ne neutrophil . Saa neutrophil yi yɛ mogya mu nkwammoaa fitaa bi a ɛbɔ yɛn ho ban fi nyarewa ho denam mmoawa a wɔko tia mmoawa, titiriw mmoawa, a wɔhyɛn yɛn nipadua mu no so. Ɛte sɛ asraafo dɔm a wɔwɔ yɛn nipadua mu.

Neutropenia yɛ bere a neutrophil asraafo dodow a wɔwɔ mogya no mu no so tew sen dodow a ɛfata. Sɛnea asraafo dɔm yɛ mmerɛw bere a n’asraafo sua, sɛ neutrophils sua no, saa ara na yɛn nipadua mu tumi a ɛko tia nyarewa no yɛ mmerɛw na yefi ase nya ɔyare mmoawa ntɛmntɛm.

Afei ma yɛnhwɛ nea asɛmfua cyclic kyerɛ . Kyinhyia kyerɛ "kyinhyia." Eyi kyerɛ sɛ ɛnyɛ bere nyinaa na neutrophil dodow no sua. Ɛkɔ soro ne fam wɔ nhyehyɛe a wɔyɛ no daa so, wɔ kyinhyia mu. Sɛ yɛbɛka no pɛpɛɛpɛ a, mpɛn pii no adapɛn abiɛsa biara (bɛyɛ nnafua 21) , neutrophil dodow so tew kɛse nnansa kosi anum. Afei ɛsan kɔ sɛnea na ɛte kan no, na afei ɛsan kɔ fam bio wɔ adapɛn abiɛsa a edi hɔ no mu. Saa kyinhyia yi si wɔ ɔkwan a wotumi hyɛ ho nkɔm yiye so.

Saa tebea yi ho yɛ na koraa. Nhwehwɛmufo ka sɛ nnipa ɔpepem biako biara mu biako pɛ na ɔwɔ saa yare yi.

Dɛn ne yare yi ho sɛnkyerɛnne?

Ade titiriw a ɛwɔ yare yi mu ne sɛ sɛnkyerɛnne ahorow no da adi sɛnea kyinhyia a ɛma neutrophil dodow so tew no hyia. Ɛne sɛ, saa sɛnkyerɛnne ahorow yi da adi wɔ nnansa kosi nnan akyi bere a neutrophils no so atew no, na sɛ neutrophils dodow no san kɔ sɛnea na ɛte kan no a, sɛnkyerɛnne ahorow no yera.

Sɛnea saa sɛnkyerɛnne ahorow yi te betumi asesa wɔ asetra nyinaa mu. Wɔ nnipa pii fam no, sɛnea yare no ho sɛnkyerɛnne no mu yɛ den no so tew bere a wodu mpanyin afe so no . Ano mu akuru ne sẽ ho haw abu so wɔ mmerante ne mmabaa mu, bere a tiyɛ ne ntini mu yare (sinusitis) taa yɛ nnipa a wɔn mfe akɔ anim mu.

Dɛn nti na eyi rekɔ so?

Cyclic neutropenia fi awosu mu nsakrae bi mu . Nea ɛde ba titiriw ne nsakrae a ɛba ELANE awosu mu abɔde mu wɔ yɛn nipadua mu.

Fa awosu mu nkwaadɔm bi sɛ akwankyerɛ ahorow a ɛkyerɛ sɛnea nkwammoaa a ɛwɔ yɛn nipadua mu no yɛ adwuma. Akwankyerɛ ahorow wɔ ELANE awosu mu abɔde no mu sɛnea wɔyɛ enzyme bi a ɛboa ma neutrophils yɛ adwuma yiye. Sɛ sintɔ anaa nsakrae bi wɔ saa awosu mu abɔde yi mu a, neutrophils ntumi nyɛ adwuma yiye.

Saa tebea yi betumi afi awofo hɔ akɔ mmofra hɔ, anaasɛ ebetumi aba wɔ awotwaa no fã mu.

Esiane awosu mu sintɔ yi nti, .

• Ebia nipadua no rentumi nyɛ neutrophils a ɛdɔɔso.
• Sɛ ɛnte saa a, ebia neutrophils no bewuwu ntɛmntɛm.
• Anaasɛ ebia neutrophils no rentumi nyɛ adwuma yiye.

Oduruyɛfo, wobɛyɛ dɛn ahu eyi?

Mpɛn pii no, wotumi hu saa sɛnkyerɛnne ahorow yi fi awo mu, enti wɔtaa hu yare no wɔ mmofraase. Oduruyɛfo no susuw nneɛma pii ho de si yare yi so dua.

• Abusua abakɔsɛm a ɛfa yare no ho: Esiane sɛ eyi yɛ awosu mu tebea nti, wɔhwɛ mu hwɛ sɛ obi foforo biara wɔ abusua no mu (awofo, anuanom) wɔ saa yare yi anaa.
• Mogya mu nhwehwɛmu: Eyi ne nea ɛho hia sen biara. Wo duruyɛfo bɛhwɛ neutrophil dodow a ɛwɔ wo mogya mu mprenu kosi mprɛnsa dapɛn biara bɛyɛ adapɛn asia . Wɔbɛyɛ eyi de ahwɛ sɛ ebia wo neutrophil dodow so retew kyinhyia anaa.
• Nsɛnkyerɛnne no ho nhwɛso: Oduruyɛfo no bɛsua mpɛn dodow a sɛnkyerɛnne ahorow no ba (bɛyɛ adapɛn 3 biara) ho ade yiye. Saa kyinhyia nhyehyɛe yi boa ma wohu nsonsonoe a ɛda eyi ne neutropenia ahorow afoforo ntam.
• Awosu mu nhwehwɛmu: Ɛtɔ mmere bi a, wobetumi akamfo akyerɛ sɛ wɔnyɛ awosu mu nhwehwɛmu de si so dua sɛ ebia nsakrae bi wɔ ELANE awosu mu nkwaadɔm no mu anaa.

Sɛ oduruyɛfo no rehu saa tebea yi a, ɛsɛ sɛ ɔpo neutropenia ahorow afoforo a ɛwɔ sɛnkyerɛnne a ɛte saa ara, te sɛ `Severe congenital neutropenia` (kan no na wɔfrɛ no `Kostmann syndrome`), `Autoimmune neutropenia`, ne `Idiopathic neutropenia`.

Dɛn ne ayaresa ahorow a wɔde sa eyi?

Botae atitiriw abien na ɛwɔ ayaresa mu. Biako ne sɛ wɔbɛsa nyarewa a ɛwɔ hɔ dedaw no. Ɔfoforo no ne sɛ wɔbɛma neutrophil dodow akɔ soro na wɔasiw ɔyare mmoawa a ɛbɛba daakye ano.

So ayaresa no mu nsunsuanso bɔne bi wɔ hɔ?

G-CSF ayaresa betumi de ɔhaw nketenkete aba. Nanso, nnuruyɛfo taa fi ase sa yare yi a wɔmfa nnuru kakraa bi na ɛsa, enti nea efi mu ba no sua koraa.

• Tipaeɛ
• Ɛyaw a ɛba nnompe ne nkwaa mu
• Akisikuru ne akisikuru

Nneɛma a ɛte sɛɛ betumi asi. Wo ne wo duruyɛfo nkasa yiye mfa ayaresa a woregye ne nea efi mu ba no ho.

Bere bɛn na ɛsɛ sɛ mefrɛ oduruyɛfo no?

Sɛ wo anaa wo ba wɔ cyclic neutropenia a, ɛho hia yiye sɛ wohwehwɛ aduruyɛfo afotu bere a wuhu sɛ ɔyare no ho sɛnkyerɛnne biara ara pɛ .

Sɛ wuhu saa nsɛnkyerɛnne yi bi a, kɔ wo duruyɛfo nkyɛn ntɛm ara. Mma ntwentwɛn wo nan ase sɛ wobɛkɔ Emergency Department (ETU) sɛ ɛho hia a.

Dɛn na ɛsɛ sɛ yɛyɛ de bɔ yɛn ho ban fi ɔyare mmoawa ho?

Wɔ wo ho a wobɛbɔ ho ban afi ɔyare mmoawa ho akyi no, ɛsɛ sɛ wohwɛ yiye nso bere a wo neutrophil dodow sua no.

• Hohoro wo nsa yiye bere nyinaa, titiriw ansa na woadi ne bere a woakɔ tiafi awie no.
• Kura w’ano akwahosan pa mu. Brush wo sẽ da biara na kɔ wo sẽ ho oduruyɛfo nkyɛn daa .
• Nya vaccinations a wɔkamfo kyerɛ nyinaa wɔ bere ano.
• Kwati sɛ wode wo nsa bɛka w’anim, w’ani, ne wo hwene a worenhohoro wo nsa.
• Fa wo nnuru no sɛnea wo duruyɛfo akyerɛ wo no pɛpɛɛpɛ na ma wɔnyɛ wo mogya mu nhwehwɛmu wɔ bere ano.

Ɛwom sɛ tebea yi yɛ nkwa nna nyinaa de, nanso mprempren ayaresa a edi mu te sɛ G-CSF ama nnipa pii a wɔwɔ cyclic neutropenia atra ase sɛnea ɛsɛ koraa . Nea ɛho hia no, bere a neutropenia ahorow afoforo bi de asiane ba sɛ obi benya kokoram te sɛ mogya mu kokoram no, cyclic neutropenia nyɛ saa.