Dɛn ne Eisenmenger Yare no? So yɛbɛka ho asɛm akɔ akyiri?

So woate pɛn sɛ komayare ahorow bi a wofi awo mu betumi de tebea horow a emu yɛ den aba akyiri yi wɔ wo nkwa nna mu? Tebea a emu yɛ den a ɛte saa no biako ne Eisenmenger yare no. Ebia edin no yɛ foforo ma wo, nanso ɛho hia sɛ wuhu ho asɛm, titiriw sɛ obi a ɔwɔ w’abusua mu wɔ komayare bi a wofi awo mu a. Momma yɛnka eyi ho asɛm nkɔ akyiri kakra, efisɛ tebea yi a wobehu ntɛm na wɔahu no ho hia yiye.

Dɛn ankasa ne Eisenmenger Syndrome?

Sɛ yɛbɛka no tiawa a, Eisenmenger Syndrome yɛ tebea a ɛba bere a mogya pii sen fa mogya ntini (ntini) a ɛde mogya fi wo koma mu kɔ w’ahurututu mu no mu. Fa no sɛ nsu a ɛsen fa faucet mu ntɛmntɛm dodo. Eyi ma mogya mmoroso ba w’ahurututu mu mogya ntini mu ne wo koma nifa so, tebea bi a wɔfrɛ no Pulmonary Hypertension . Ɛte sɛ nea worebɔ mmɔden sɛ wobɛpia nsu pii afa paipu ketewaa bi mu, na ɛma nhyɛso kɛse ba paipu no mu.

Bio nso, mogya fi ase sen wɔ koma no benkum ne nifa ntam wɔ ɔkwan a ɛmfata so (`mogya a ɛkɔ nipadua no mu`). Eyi kyerɛ sɛ esiane nkitahodi bi a ɛnteɛ (te sɛ tokuru a ɛwɔ hɔ bere a wɔawo no) nti, mogya a efi koma no benkum so (a oxygen pii wom) sen kɔ nifa so (oxygen pii nni mu). Bere kɔ so no, wobetumi asan tebea yi nso, a ɛkyerɛ sɛ mogya a oxygen kakraa bi na ɛwom no sen fi nifa kɔ benkum.

Saa tebea yi a wɔfrɛ no Eisenmenger syndrome no taa ba bere a wɔannya komayare biako anaa nea ɛboro saa a wɔde awo no a wɔansa anaasɛ wɔanhu no . Sɛ saa tebea yi kɔ so kyɛ a, ebetumi ama ahurututu asɛe daa na ɛde ɔhaw afoforo a ɛde nkwa to asiane mu aba. Ɛno nti na eyi yɛ tebea a ɛsɛ sɛ wɔhwɛ so yiye no.

Hena na ɛda adi sɛ obenya saa tebea yi?

Eisenmenger syndrome yɛ tebea a ɛtaa ba mmofra ne mpanyimfo nkumaa a wɔwo wɔn a wɔwɔ Ventricular Septal Defect (VSD), tokuru a ɛwɔ ɔfasu no mu wɔ koma no mu nsu a ɛwɔ fam abien (benkum ne nifa ventricles) ntam .

Afei nso, Eisenmenger yare no betumi aba bere a wɔansa komayare afoforo bi a wɔde awo obi no yiye no. Nhwɛso kakraa bi ni:

• Atrioventricular canal no mu sintɔ
• Atrial septal mu sintɔ
• Cyanotic komayare (a nipadua no dan bruu) .
• Patent ductus arteriosus (mogya ntini bi a wɔkyerɛ sɛ ɛto mu wɔ awo akyi) .
• Tetralogy of Fallot (koma mu dɛmdi anan a wɔaka abom) .
• Truncus arteriosus `(Truncus ntini a ɛwɔ nipadua no mu)`

Ade foforo nso ne, Down syndrome.Mmofra a wɔwɔ Down syndrome nso wɔ asiane kɛse sɛ wobenya komayare a wɔde awo wɔn. Ne saa nti, ebia wɔn nso taa nya Eisenmenger yare no kɛse. Nokwarem no, akontaabu kyerɛ sɛ mpanyimfo a wɔwɔ Eisenmenger yare no mu 25% kosi 50% nso wɔ Down yare no.

Eisenmenger yare no abu so dɛn?

Nea eye ne sɛ, Eisenmenger yare no yɛ tebea a ɛntaa nsi koraa . Ɛka mpanyimfo a wɔwoo wɔn a wɔwɔ komayare a wɔde awo wɔn no mu 1% kosi 6%. Nanso, ɛmfa ho sɛ ɛntaa nsi no, ɛho hia sɛ wohu esiane aniberesɛm a ɛwom nti.

Dɛn na ɛde Eisenmenger yare no ba?

Sɛ wobɛte nea enti a eyi ba no ase pɛpɛɛpɛ a, ɛsɛ sɛ wunya sɛnea mogya sen wɔ yɛn koma mu no ho adwene kakra. Fa no sɛ yɛn koma te sɛ ofie a ɛwɔ adan anan.

Mogya a ɛkɔ koma a ɛte apɔw mu no kɔ so sɛnea edidi so yi:

1. Atrium nifa: Nipadua no mogya a wɔde adi dwuma a oxygen nni mu no di kan ba na ɛboaboa ano wɔ ha. Afei wɔde mogya yi kɔ nifa so ventricle no mu.

2. Right ventricle: Eyi ne baabi a wɔde mogya a oxygen nnim no kɔ ahurututu no mu ma enya oxygen foforo.

3. Benkum atrium: Mogya a ɛho tew a wɔde oxygen ahyɛ ahurututu mu no san kɔ koma no mu wɔ ha. Afei wɔde mogya yi kɔ benkum so ahurututu no mu.

4. Benkum so ahurututu: Eyi ne koma no pɔmpɛ titiriw. Ɛha na wɔkyekyɛ mogya a oxygen pii wom wɔ nipadua no mu nyinaa.

Afei fa no sɛ nhyehyɛe mu sintɔ bi wɔ koma no mu, te sɛ tokuru a ɛwɔ ɔfasu a ɛda nifa ne benkum ventricles (VSD) ntam no mu. Dɛn na ɛba saa bere no? Mogya a oxygen pii wom (wɔ benkum so) ne mogya a oxygen nni mu (wɔ nifa so) no fi ase frafra . Ne saa nti, mogya pii sen kɔ ahurututu no mu. Eyi ne nea ɛde ahurututu mu mogya mmoroso a yɛadi kan aka ho asɛm no ba. Afei nso, mogya a oxygen wom a ɛsɛ sɛ ɛkɔ nipadua no fã a aka no so tew. Eyi ne ɔhaw titiriw a ɛwɔ Eisenmenger yare no mu.

Dɛn ne Eisenmenger yare no ho sɛnkyerɛnne?

Eisenmenger yare no ho sɛnkyerɛnne betumi ayɛ soronko wɔ onipa biara ho. Wogyina komayare ko a obi wɔ ne akwaa a ɛka no so. Mpɛn pii no, saa sɛnkyerɛnne ahorow yi nna adi prɛko pɛ. Mpɛn pii no, wofi ase da adi wɔ mmerantebere ne mmabaabere anaa mpanyin afe so mfiase. Afei, yare no ho sɛnkyerɛnne no mu yɛ den nkakrankakra.

Eyinom yɛ sɛnkyerɛnne ahorow a wɔtaa hu no bi:

• Koko mu yaw anaasɛ ɛyɛ den (Angina) .
• Koma a ɛbɔ daa (Arrhythmias) - Wei kyerɛ sɛ koma no bɔ wɔ akwan horow so sen sɛ ɛbɛbɔ ɔkwan biako so.
• Nsateaa nnadewa ano a etrɛw ne nnadewa no a ɛyɛ kurukuruwa (Clubbing) - te sɛ sankuo ano.
• Mogya a wɔfefe.
• Honam ani kɔla a ɛsakra bruu anaa fitaa (Cyanosis) - Eyi fi oxygen dodow a ɛwɔ mogya no mu a ɛso tew.
• Adwene a ɛyɛ basaa anaasɛ obi a ɔtotɔ piti.
• Nan, anan, anan, anaa yafunu a ɛho ahonhon (edema).
• Sɛ wote nka sɛ wo koma rebɔ ntɛmntɛm, wobɛte nnyigyei a ɛne sɛ wo koko rebɔ (koma a ɛbɔ).
• Ɔbrɛ a ɛtra so ne ahoɔden a wonni (Lethargy).
• Dyspnea - Ɔhome a ɛyɛ den sɛ wobɛbɔ mmɔden kakra mpo.

Sɛ wowɔ saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa a, ɛho hia yiye sɛ wohwehwɛ aduruyɛfo afotu ntɛm ara.

Dɛn ne nsɛnnennen a ebetumi afi Eisenmenger yare no mu aba?

Nea ɛyɛ awerɛhow no, Eisenmenger yare no nyɛ yare a ɛtra baabi biako. Ebetumi de akwahosan ho nsɛnnennen ahorow aba. Ebi ne:

• Mogya a ɛretu akɔ amemene no mu.
• Amemene mu akisikuru esiane ɔyare mmoawa nti.
• Mogya a ɛnnɔɔso mma amemene no (Cerebral vascular insufficiency).
• Gout.
• Koma mu yare.
• Koma a entumi nyɛ adwuma yiye.
• Koma mu yare, sɛ nhwɛso no, endocarditis.
• Mogya a ɛyɛ den (Hyperviscosity syndrome).
• Asaabo a entumi nyɛ adwuma yiye.
• Nsɛnnennen a ɛba wɔ nyinsɛn mu (eyi yɛ asiane kɛse).
• Nnwodwoɔ.
• Owu a ɛba mpofirim.

Sɛ wohwɛ nsɛnnennen yi a, wubetumi ahu sɛnea tebea yi mu yɛ den fa, ɛnte saa? Ɛno nti na ɛsɛ sɛ yɛde yɛn adwene si eyi so titiriw no.

Ɔkwan bɛn so na wohu sɛ obi anya Eisenmenger yare no?

Mpɛn pii no, oduruyɛfo bɛhwehwɛ Eisenmenger yare no ho sɛnkyerɛnne bere a wɔreyɛ nipadua mu nhwehwɛmu no. Sɛ nhwɛso no, sɛ ebia wo honam ani yɛ bruu, sɛ ebia wo nsateaa abɔ, ne sɛ ebia wote nnyigyei a ɛnteɛ bere a woretie wo koma no.

Afei, oduruyɛfo no betumi ahyɛ sɛ wɔnyɛ nhwehwɛmu a edidi so yi mu biako anaa nea ɛboro saa mfa nkyerɛ sɛ wɔahu yare no:

• Oxygen dodow a ɛwɔ mogya no mu a wɔbɛhwɛ.
• Koma mu catheterization: Eyi hwehwɛ sɛ wɔde afiri ketewaa bi bɛhyɛ koma no mu de asusuw nhyɛso na wɔahwɛ sɛnea wɔahyehyɛ no.
• Koko so X-ray a wɔyɛ.
• Mogya dodow a edi mũ (CBC).
• Echocardiogram (Echocardiogram - echo): Eyi yɛ koma no mu nnyigyei a ɛkɔ akyiri. Ebetumi ahwɛ koma no mu adan, ntini ahorow, ne sɛnea mogya no sen.
• Electrocardiogram (EKG/ECG): Eyi sɔ sɛnea koma no mu anyinam ahoɔden yɛ adwuma hwɛ.
• Koma mu MRI nhwehwɛmu.
• Ahurututu mu dwumadi ho sɔhwɛ.

Oduruyɛfo no betumi agyina nsɛm a onya fi nhwehwɛmu ahorow yi mu so ahu yare no pɛpɛɛpɛ.

Ɔkwan bɛn so na wɔsa Eisenmenger yare no?

Botae titiriw a ɛwɔ Eisenmenger yare no a wɔsa mu ne sɛ wobedi yare no ho sɛnkyerɛnne ahorow so na wɔasiw koma anaa ahurututu no sɛe bio.

Wobetumi de nea edidi so yi adi dwuma sɛ ayaresa:

• Nnuru a ekum ɔyare mmoawa: Siw mmoawa a wɔde nyarewa ba koma ne ahurututu mu ano.
• Nnuru a ɛko tia mogya a ɛtwetwe: Ɛtew mogya a ɛtwetwe mogya ntini no mu no so.
• Diuretics (nsu mu nnuru): Tew nsu a ɛboro so a ɛboaboa ano wɔ nipadua no mu no so.
• Dual endothelin receptor antagonists: Eyinom yɛ nnuru titiriw bi a wɔde ma de tew mogya mmoroso a ɛwɔ ahurututu mu no so.
• Iron a wɔde ma: Sa mogya a ɛtɔ kɔ nipadua mu a iron a enni nipadua mu de ba no.
• Oxygen a wɔde ka ho: Ma home nyɛ mmerɛw na oxygen dodow a ɛwɔ mogya no mu no nkɔ soro.

Nea ɛho hia ne sɛ, sɛ Eisenmenger yare no nya ba pɛ a, ɛtaa ka akyi dodo sɛ wɔbɛyɛ oprehyɛn asiesie koma a wɔde awo no no, efisɛ ebedu saa bere no na wɔasɛe ahurututu no dedaw.

Nanso, ebia nnipa binom a wɔwɔ yare no ho sɛnkyerɛnne a emu yɛ den yiye na wɔn akwaa asɛe kɛse no behia sɛ wɔde wɔn koma anaa ahurututu si ananmu. Nanso ɛno nso yɛ adeyɛ a ɛyɛ den yiye na asiane wom.

So wobetumi asiw Eisenmenger yare no ano?

Yiw, ɔkwan biako pɛ a wobetumi afa so asiw Eisenmenger yare no ano ne sɛ wobehu komayare a wɔde awo obi ntɛm ara, ntɛm ara, na wɔasa no yiye, na sɛ ɛho hia a, wɔayɛ no oprehyɛn. Sɛ wohu saa sintɔ ahorow yi na wɔsa wɔ mmofraase a, hokwan kɛse wɔ hɔ sɛ wobesiw tebea a emu yɛ den te sɛ Eisenmenger syndrome ano.

Nnipa a wɔwɔ Eisenmenger yare no nkwa nna yɛ dɛn?

Ebia nnipa a wɔwɔ Eisenmenger yare no nkwa nna yɛ tiaa sen nnipa dodow no ara. Eyi fi nsɛnnennen a ɛba wɔ tebea no mu no. Nanso, nnipa binom tra ase kosi mfinimfini mfe mu. Bere tenten a wobetumi atra ase no gyina nneɛma te sɛ sɛnea wɔn yare no ho sɛnkyerɛnne no mu yɛ den, sɛnea komayare a wɔde awo wɔn no te, ne sɛnea wɔyɛ wɔn ade yiye wɔ ayaresa ho so. Enti, ɛho hia sɛ wudi wo duruyɛfo afotu akyi na wohwɛ w’akwahosan so.

Sɛ mewɔ Eisenmenger syndrome a, so metumi anyinsɛn?

Eyi yɛ asɛmmisa a ɛho hia paa. Nyinsɛn yɛ asiane kɛse ma obi a ɔwɔ Eisenmenger yare no. Ebetumi de asiane ahorow a emu yɛ den te sɛ komayare, mogya a ɛtwetwe, ne owu mpofirim aba. Sɛ wowɔ saa tebea yi na woresusuw ho sɛ wubenyinsɛn a, akyinnye biara nni ho sɛ ɛsɛ sɛ wokɔ oduruyɛfo bi a ɔhwɛ mpanyimfo awo mu koma tebea horow so (`(ɔbenfo wɔ mpanyimfo awo mu koma tebea horow ho ɔbenfo)`) kɔka asiane ahorow yi ho asɛm. Ɔno na obetumi de afotu a eye sen biara ama wo.

Mɛyɛ dɛn ahwɛ me ho a mewɔ Eisenmenger yare no?

Sɛ wowɔ Eisenmenger syndrome a, nneɛma pii wɔ hɔ a wubetumi ayɛ de atew asiane a ɛwɔ hɔ sɛ wubenya nsɛnnennen no so. Sɛ wudi anammɔn yi akyi a, ɛbɛboa ma wo nkwa nna ne w’asetra atu mpɔn.

Nneɛma a ɛsɛ sɛ woyɛ:

• Di aduan a sodium nnim: Sɛ wudi nkyene pii a, ebetumi ama nsu akɔ wo mu na ama mogya mmoroso akɔ soro.
• Nya nnuru a ɛfata: Bɔ wo ho ban fi nyarewa te sɛ ahurututu mu yare ne atiridiinini ho.
• Nom nsu pii na mma wo nipadua no nnyɛ nsu (`(Staying hydrated)`) : Nanso dodow a wo duruyɛfo atu wo fo no nkutoo.
• Di nnuru ne ayaresa afoforo a wo koma ho ɔyaresafo akyerɛ wo nyinaa akyi pɛpɛɛpɛ. Mma dose biako mpo nmpa wo ti so.
• Nom nnuru a ekum ɔyare mmoawa ansa na woayɛ wo sẽ ayaresa anaa oprehyɛn: Eyi betumi aboa ma woasiw komayare ano. Bisa wo duruyɛfo no eyi ho asɛm.

Nneɛma a ɛnsɛ sɛ woyɛ:

• Kwati sɛ wobɛkɔ mmeae a ɛkorɔn sen po kɛse (`(High altitudes)`): Ɔhome mu haw betumi ayɛ kɛse esiane oxygen a enni mmeae a ɛkorɔn nti.
• Kwati sɛ wode sauna, steam dan, anaa nsu a ɛyɛ hyew bedi dwuma: Eyinom betumi ama wo mogya so atew mpofirim.
• Kwati sigaretnom anaa tawa ho nneɛma a wode bedi dwuma koraa.
• Kwati apɔw-mu-teɛteɛ a emu yɛ den: Yɛ apɔw-mu-teɛteɛ a emu nyɛ den wɔ dodow a wo duruyɛfo apene so nkutoo.

Nkrasɛm a Wɔde Kɔ Fie

Eisenmenger syndrome yɛ tebea a ɛma mogya mmoroso wɔ mogya ntini a ɛwɔ ahurututu no mu ne koma no nifa so. Mpɛn pii no, komayare a wɔde awo obi a wɔansa no na ɛde ba. Mpɛn pii no, sɛnkyerɛnne ahorow no fi ase da adi wɔ mmerantebere ne mmabaabere anaa mpanyin afe so. Nsɛnkyerɛnne no bi ne honam ani bruu (cyanosis), ahome a ɛyɛ tiaa bere a ɔteɛteɛ n’apɔw mu, ne koma a ɛbɔ daa.

Saa tebea yi ho ayaresa atirimpɔw titiriw ne sɛ wɔbɛma yare no ho sɛnkyerɛnne ahorow no afi hɔ na wɔama koma ne ahurututu no asɛe no kakraa bi. Aka akyi dodo sɛ wɔde oprehyɛn bɛsa tebea yi. Enti, ɛyɛ papa sɛ wubehu koma mu dɛmdi a wɔde awo obi na woasa no ntɛm ara sɛnea wobetumi.

Sɛ wowɔ nsɛmmisa foforo bi fa eyi ho a, nsuro sɛ wo ne wo duruyɛfo bɛkasa. Wɔbɛboa wo.

` Eisenmenger syndrome, komayare, ahurututu mu mogya mmoroso, cyanosis, koma mu dɛmdi a wɔde awo obi, ɔhome mu haw, koma akwahosan