So mogya atɔ wo mpofirim, anaasɛ woanya ɔhaw bi wɔ nyinsɛn mu na oduruyɛfo no yɛɛ mogya mu nhwehwɛmu? So na ɛhaw wo bere a amanneɛbɔ no kae sɛ ‘Lupus Anticoagulant positive’ no? So ehu kaa wo bere a wuhuu asɛmfua ‘lupus’ na wususuwii sɛ eyi yɛ lupus no? Saa din yi yɛ nea ɛyɛ basaa kakra ankasa. Ɛno nti na nnipa pii nte ase wɔ ho. Momma yennyi ɔhaw ahorow a ɛwɔ eyi ho nyinaa mu nnɛ.
Dɛn ankasa ne Lupus Anticoagulant?
Sɛ yɛbɛka no tiawa a, eyi yɛ antibody bi a ebetumi aba yɛn mogya mu.
Susuw yɛn nipadua mu tumi a ɛko tia nyarewa no ho sɛ asraafo dɔm a wɔbɔ ɔman bi ho ban. Sɛ ɔyare mmoawa anaa biribi a epira fi abɔnten hyɛn nipadua no mu a, saa asraafo dɔm yi hu saa ɔtamfo no na wɔbɔ asraafo titiriw kuw bi a wɔfrɛ wɔn antibodies de sɛe no. Eyi ne nea ɛtaa ba.
Nanso, ɛtɔ mmere bi a yɛn nipadua mu ahoɔden a ɛko tia nyarewa no nkɔ yiye. Sɛ́ anka ɛbɛtow ahyɛ amannɔne ntuafo so no, efi ase tow hyɛ yɛn ankasa nkwammoaa a ɛte apɔw so . Saa na lupus anticoagulant (LA) yɛ antibody a mfomso na ɛyɛ na ɛsɛe yɛn ankasa nipadua.
Saa LA aduru a ɛko tia nyarewa yi, ne nnuru afoforo abien a ɛko tia nyarewa no betumi de tebea bi a wɔfrɛ no Antiphospholipid Syndrome (APS) aba . Eyi yɛ yare a nipadua no tumi ko tia nyarewa. Eyi su titiriw ne sɛ asiane a ɛwɔ hɔ sɛ mogya a ɛbɛtɔ nipadua no mu mogya ntini mu no dɔɔso sen onipa a ɔte hɔ no koraa.
Enti dɛn nti na wɔfrɛ eyi ‘lupus’? So eyi ne yare koro no ara ne lupus?
Ɛha na nnipa pii adwene tu fra na ehu ka wɔn. Ɛwom mpo sɛ ‘lupus’ fã bi wɔ edin no mu de, nanso nokwarem no, lupus yɛ nneɛma abien a ɛsono emu biara: Lupus Anti-Coagulant (LA) ne Lupus Yare. Ɛyɛ asɛm a ɛyɛ anigye yiye sɛnea saa din yi bae.
Wodii kan huu saa nipadua mu nkwammoaa a ɛko tia nyarewa yi mfe du du a atwam ni bere a nhwehwɛmufo yɛɛ mogya a wɔde fii ayarefo a wɔwɔ lupus mu hwɛe no. Enti wosusuwii sɛ ɛyɛ biribi pɔtee a ɛfa lupus ayarefo ho.
Wɔhyɛɛ no nsow nso sɛ mogya a saa nipadua no mu nkwammoaa a ɛko tia nyarewa yi wom no gyee bere tenten sen sɛnea ɛte biara ansa na ɛreyɛ ayɛ kɛse wɔ vitro. ‘Anticoagulant’ kyerɛ sɛ ‘ɛsiw mogya a ɛbɛtɔ ano.’ Enti, wɔtoo din ‘lupus anticoagulant’, a ɛkyerɛ ‘biribi a ɛwɔ lupus ayarefo nipadua mu a esiw mogya a ɛtwetwe.’
Nanso, akyiri yi wohui sɛ saa nsusuwii abien no nyinaa nyɛ nokware. Nokwarem no, nea ɛne eyi bɔ abira na ɛte. Nea saa antibody yi yɛ wɔ nipadua no mu ne sɛ ɛma mogya a ɛtwetwe no yɛ kɛse, na ɛnyɛ sɛ esiw ano!
Sɛ wopɛ sɛ woyi saa adwene a ɛyɛ basaa yi fi hɔ a, hwɛ pon a ɛwɔ ase hɔ no.
| Nokwasɛm | Lupus aduru a ekum mogya a ɛtwetwe (LA) . | Lupus yare (SLE) . |
|---|---|---|
| Abɔdeɛ | Nkwammoaa bi a epira a ɛwɔ mogya no mu. | Yare a ɛyɛ den a nipadua no tumi ko tia nyarewa a ɛka nipadua no akwaa ahorow. |
| Nkɛntɛnso titiriw | Ɛma asiane a ɛwɔ hɔ sɛ mogya bɛtɔ no yɛ kɛse. | Nhyehyɛe pii betumi aka, te sɛ honam ani, nkwaa, asaabo, koma, ne amemene. |
| Twaka | Sɛ wowɔ LA a, ɛnkyerɛ sɛ wowɔ lupus, nanso ebia nnipa binom a wɔwɔ lupus wɔ LA. | LA yɛ ade biako pɛ a wɔahu a ebia ɛne lupus wɔ abusuabɔ. |
Dɛn nti na biribi a ɛte sɛɛ to yɛn nipadua?
Nea enti a ɛte saa ne sɛ yɛn nipadua mu tumi a ɛko tia nyarewa no di mfomso. Saa LA antibodies yi tow hyɛ protein ahorow a ɛbata srade bi a wɔfrɛ no phospholipids a ɛwɔ yɛn nkwammoaa no akyi ho no so. Saa ntua yi sɛe nkwammoaa no, na ɛma wɔbata ho na ɛma asiane a ɛwɔ hɔ sɛ mogya bɛtɔ no yɛ kɛse.
Abenfo da so ara nnim nea enti a nipadua no mu tumi a ɛko tia nyarewa no fi ase yɛ nnuru a ɛko tia nyarewa a mfomso wom yi wɔ nea edi kan no mu koraa. Wogye di sɛ ebetumi afi awosu mu nneɛma, nneɛma a atwa yɛn ho ahyia, anaa tebea afoforo a ɛde ɔyare mmoawa ba.
Dɛn na LA positive kyerɛ? Ɛbɛka me dɛn?
Sɛ wowɔ LA wɔ wo mogya mu a, ɛkyerɛ sɛ wowɔ asiane mu sɛ wubenya tebea bi a wɔfrɛ no antiphospholipid syndrome (APS). Ɛha yi, ‘wɔ asiane mu’.Asɛmfua "ɔpɛ" no ho hia yiye. Ɛnkyerɛ sɛ ɛbɛba ampa.
Ɛwom mpo sɛ LA antibody no wɔ mogya no mu de, nanso nnipa pii wɔ hɔ a wɔkɔ so nya apɔwmuden wɔ wɔn nkwa nna nyinaa mu a wonnya mogya mu ntini anaa nsɛnnennen biara.
Enti mma wo ho dwiriw wo a ɛho nhia bere a wuhu eyi wɔ w’amanneɛbɔ so no. Nanso, ɛho hia sɛ wo duruyɛfo no hu eyi na ɔhwɛ wo so. Esiane sɛ ɛda adi sɛ mogya bɛtɔ wo sen afoforo nti, nyansa wom sɛ wubehu.
Dɛn ne ayaresa ahorow a wɔde sa eyi?
Ayaresa biara nni hɔ a ɛde saa LA antibody yi fi nipadua no mu koraa. Nanso ayaresa ahorow a eye paa wɔ hɔ a wɔde siw ɔsɛe a ebetumi de aba no so, a ɛne mogya a ɛbɛtɔ no.
Sɛ wunni sɛnkyerɛnne biara, a ɛkyerɛ sɛ woannya mogya a ɛtɔe da a, ebia wo duruyɛfo besi gyinae sɛ ɔbɛhwɛ wo ara kwa a ɔremma wo nnuru biara.
Nanso, sɛ mogya atɔ wo pɛn anaasɛ wɔahu sɛ wowɔ APS a, ayaresa titiriw ne nnuru a ekum mogya a ɛtwetwe mogya anaa nnuru a ɛma mogya tu . Wɔde nnuru te sɛ warfarin ne heparin ma na ama asiane a ɛwɔ hɔ sɛ mogya bɛtɔ no so atew. Ɛtɔ mmere bi a, wɔma nnuru te sɛ corticosteroids nso de tew nipadua no mu tumi a ɛko tia nyarewa no dwumadi a ɛboro so no so.
Wo duruyɛfo na osi ayaresa yi nyinaa ho gyinae, na wususuw nneɛma pii te sɛ wo tebea, mfe a woadi, ne nyarewa afoforo ho.
Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn? Dɛn ne ntɛmpɛ?
Sɛ wo ne tebea yi te a, ɛho hia yiye sɛ wuhu nsonsonoe a ɛda tebea horow a ɛfata ne tebea horow a egye ntɛmpɛ ntam.
| Akwannya | Nea ɛsɛ sɛ wɔyɛ |
|---|---|
| Nneɛma a wɔhwɛ wɔ ɔkwan a ɛkɔ akyiri so | Kɔ ayaresabea wɔ bere a wɔahyɛ no mu kɔhwɛ sɛnea oduruyɛfo no ka no. Wɔbɛyɛ mogya mu nhwehwɛmu ahwɛ sɛ nnuru dodow a wɔde ma no teɛ ne sɛ nsakrae foforo bi wɔ hɔ anaa. |
| Emergency (kɔ ETU ntɛm ara) . |
|
Kɔkɔbɔ nsɛnkyerɛnne a ɛkyerɛ sɛ mogya atɔ piti
- Nan (Deep Vein Thrombosis - DVT): Ɛhohoro mpofirim, ɛyɛ kɔkɔɔ, ɛyɛ hyew, na ɛyaw wɔ nan biako mu.
- Pulmonary Embolism: Ɔhome a ɛyɛ tiaa mpofirim, koko mu yaw a ano yɛ den (titiriw bere a ɔrehome), mogya a ɔfe.
- Stroke: anim fã biako a ɛbɛhwe ase, nsa biako a ɛyera, ɛyɛ den sɛ ɔbɛkasa.
Sɛ saa sɛnkyerɛnne ahorow yi mu biara da adi a, kɔ ayaresabea Ayaresa a Ɛho Hia Ntɛmntɛm (ETU) a ntwentwɛn wo nan ase .
Nkrasɛm a Wɔde Kɔ Fie
- Lupus anticoagulant (LA) nyɛ lupus ankasa. Ɛyɛ nipadua mu nkwammoaa a ɛko tia nyarewa bi a ɛwɔ mogya no mu ara kwa.
- Sɛ wowɔ LA wɔ wo mogya mu a, ɛkyerɛ sɛ wowɔ asiane kɛse mu sɛ wubenya mogya a ɛbɛtɔ. Ɛnkyerɛ sɛ ɛbɛba ampa.
- Mma wo ho nnpopo bere a woahu amanneɛbɔ no akyi. Nanso akyinnye biara nni ho sɛ wo ne wo duruyɛfo nka eyi ho asɛm na di n’afotu akyi.
- Botae titiriw a ɛwɔ ayaresa mu ne sɛ ɛbɛma mogya a ɛbɛtɔ no ankɔ. Wo duruyɛfo na ɔbɛkyerɛ ayaresa a eye sen biara a wobɛfa so.
- Hu bere nyinaa wɔ kɔkɔbɔ nsɛnkyerɛnne a ɛkyerɛ sɛ mogya atɔ (nan a ɛho ahonhon, wo koko mu yaw, ɛyɛ den sɛ wobɛhome). Sɛ sɛnkyerɛnne a ɛte saa da adi a, kɔ ETU ntɛm ara.
- Ɛyɛ ade a ɛfata sɛ wobɛte ehu ne dadwen nka bere a wususuw sɛ biribi a wuntumi nhu wɔ wo nipadua mu betumi apira wo no. Sɛ́ anka wobɛtra ehu mu no, fa nhumu ne adwene tra ase. Wo duruyɛfo betumi aboa wo wɔ saa akwantu no mu.











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