Ebia oduruyɛfo no aka akyerɛ wo sɛ wo ba ketewa no wɔ Sickle Cell Disease (SCD). Ɛyɛ ade a ɛfata sɛ wo, sɛ ɔwofo no, sɛ wote eyi a, wobɛte ehu ne dadwen pii nka. Sɛ yɛne saa yare yi te ase a, ɛsɛ sɛ yɛhwɛ yiye wɔ nneɛma pii ho. Ɛno nti na ɛsɛ sɛ yɛde yɛn adwene si so titiriw, na ɛnnɛ yɛreka ɔhaw bi a asiane wom a ebetumi de yɛn nkwa mpo ato asiane mu ho asɛm. Wɔfrɛ eyi sɛ ‘Splenic Sequestration’. Ɛwom sɛ saa din yi yɛ nwonwa kakra de, nanso sɛ wunim ho asɛm yiye a, wubetumi abɔ wo ba no ho ban.
Dɛn ankasa ne Splenic Sequestration?
Sɛ yɛbɛte eyi ase a, momma yenni kan nkae sickle cell disease (SCD) ho asɛm kakra. Mpɛn pii no, mogya mu nkwammoaa kɔkɔɔ a ɛwɔ obi a ɔwɔ apɔwmuden mu no yɛ kurukuruwa na ɛyɛ petee. Te sɛ diski ketewaa bi. Ɛnyɛ den sɛ wɔbɛfa mogya ntini no mu a wɔnkyere. Nanso, esiane nsakrae a ɛba hemoglobin a ɛwɔ abofra a ɔwɔ SCD mogya mu nkwammoaa kɔkɔɔ mu nti, saa nkwammoaa yi yɛ den na ɛyɛ te sɛ nkankyee.
Afei susuw ho hwɛ, so saa nkwammoaa a ɛte sɛ nkankyee yi nguare fa mogya ntini no mu ntɛmntɛm te sɛ nkwammoaa kurukuruwa a ɛteɛ no? Dabi, ɛnte saa? Wɔbata ho na wɔbɔ mmɔden sɛ wɔbɛkyere mogya ntini nketenkete no mu.
Ɛhɔ na ɔhaw no fi ase. Wɔ yɛn nipadua mu, wɔ yafunu no benkum so no, akwaa bi wɔ hɔ a wɔfrɛ no ‘ spleen ’. Eyi te sɛ ɔwɛmfo a ɔwɔ yɛn nipadua mu. N’adwuma titiriw ne sɛ ɛbɛtew mogya no ho denam mmoawa ne mogya mu nkwammoaa dedaw a ɛwɔ mogya no mu a ebeyi afi hɔ no so. Nanso wɔ abofra a ɔwɔ SCD mu no, saa nkwammoaa a ɛte sɛ nkankyee no kɔhyɛ mogya ntini a ɛyɛ mmerɛw a ɛwɔ akyi berɛmo no mu no mu. Ɛte sɛ kar akwan a akyeakyea wɔ ɔkwan bi so.
Sɛ eyi ba a, mogya a ɛsɛ sɛ efi akyi berɛmo no mu no ntumi nkɔ, na ɛboaboa ano wɔ mu. Nkakrankakra, mogya hyɛ akisikuru no ma, ɛhohoro, na ɛyɛ kɛse. Wɔfrɛ saa tebea a asiane wom no ‘Splenic Sequestration.’
Sɛ mogya pii a ehia sɛ ɛkyinkyini wɔ nipadua no mu kɔhyɛ akyi berɛmo no mu a, mogya mu nkwammoaa kɔkɔɔ a ɛde mframa pa kɔ nipadua no fã a aka no so tew mpofirim wɔ ɔkwan a ɛyɛ hu so. Wɔfrɛ eyi mogya a ɛtɔ kɔ nipadua mu a emu yɛ den . Eyi betumi ama abofra no ayɛ mmerɛw kɛse na ne ho ayɛ fitaa.
Dɛn ne tebea yi ho sɛnkyerɛnne? Nneɛma a ɛsɛ sɛ wuhu sɛ ɔwofo
Eyi ne ɔfã a ɛho hia sen biara. Sɛ wunim saa sɛnkyerɛnne ahorow yi a, wubetumi ayɛ ho biribi ntɛm na woagye abofra no nkwa. Ɛwom sɛ tebea yi taa ba mmofra nkumaa so de, nanso ebetumi aba nnipa a wɔadi mfe biara a wɔwɔ SCD mu.
| Nsɛnkyerɛnne a ɛkyerɛ | Nea ɛsɛ sɛ wohwɛ yiye wɔ ho |
|---|---|
| Ɛyaw a ɛba yafunu no benkum so | Eyi ne sɛnkyerɛnne a ɛtaa ba na ɛho hia sen biara. Sɛ wo ba nwiinwii sɛ ɛyaw wɔ baabi a akyi berɛmo no wɔ a, ma ɛhaw wo. |
| Spleen a ɛyɛ kɛse (a ɛho ahonhon) . | Bisa wo duruyɛfo na sua sɛnea wobɛbɔ wo ba no akyi berɛmo mu. Sɛ ɛte sɛ nea ɛsõ sen sɛnea ɛte daa na ɛyɛ den a, ɛno yɛ kɔkɔbɔ sɛnkyerɛnne. |
| Mmerewa a ɛba mpofirim ne ɔbrɛ a ɛtra so | Sɛ wo ba a na ɔredi agoru yiye no brɛ mpofirim na ɔyɛ mmerɛw araa ma ontumi nnantew mpo a, hwɛ yiye. |
| Wora a ɛyɛ mmerɛw | Sɛ wo ba no anofafa, n’anom, ne ne nsateaa mu yɛ fitaa a, ɛkyerɛ sɛ mogya atɔ no. |
| Ahome a wɔhome ntɛmntɛm anaa koma a ɛbɔ | Sɛ nipadua no nnya mframa pa a ɛdɔɔso a, koma ne ahurututu no yɛ adwuma ntɛmntɛm de tua ka. |
| Abufuw ne abufuw a wontumi nkyerɛkyerɛ mu | Esiane sɛ abofra no te yaw nti, ebia ne bo befuw na wasu wɔ nneɛma nketenkete ho. |
| Dae a ɛyɛ soronko | Sɛ abofra no da araa ma ɛrentumi nnyane no a, ɛno nso yɛ sɛnkyerɛnne a anibere wom. |
Nea ɛho hia sen biara: Ɛtɔ mmere bi a, sɛ yare no ho sɛnkyerɛnne afoforo nna adi mpo a, ahurututu a ahonhon betumi ama mogya mu nkwammoaa kɔkɔɔ dodow so atew wɔ ɔkwan a ɛyɛ hu so. Enti sɛ wuhu saa nsɛnkyerɛnne yi bi a, fa wo ba no kɔ ayaresabea hɔ Emergency Department (ETU) ntɛm ara. Eyi nyɛ tebea a wobetumi asa wɔ fie.
Ɔkwan bɛn so na oduruyɛfo no hu saa tebea yi?
Sɛ wode wo ba no kɔ ayaresabea a, oduruyɛfo no bɛyɛ nneɛma pii de asi tebea yi so dua.
1. Nipadua mu nhwehwɛmu : Nea edi kan no, oduruyɛfo no de ne nsa bɛka abofra no yafunu mu na wahwɛ sɛ akyi berɛmo no ahonhon anaasɛ ayɛ kɛse anaa.
2. Mogya mu nhwehwɛmu: Eyi yɛ nhwehwɛmu a ɛho hia. Wɔfa abofra no mogya bi na wɔhwɛ hemoglobin dodow mu hwɛ sɛnea mogya mu nkwammoaa kɔkɔɔ dodow no sua. Wɔhwehwɛ nsakrae a ɛba mogya mu nkwammoaa fitaa ne mogya mu nkwammoaa kɔkɔɔ dodow mu nso.
3. Nhwehwɛmu afoforo: Wɔ tebea horow bi mu no, wobetumi ayɛ X-ray anaa CT scan de ahwɛ sɛnea akyi berɛmo no te yiye.
Ɔkwan bɛn so na wɔbɛsa? Nsuro.
Ɛwom sɛ eyi yɛ tebea a egye ntɛmpɛ de, nanso sɛ wɔde wo kɔ ayaresabea ntɛm a, wobetumi adi ho dwuma yiye.
Ayaresa titiriw ne mogya a wɔde ma . Eyi kyerɛ sɛ abofra no mogya mu nkwammoaa kɔkɔɔ dodow san ba denam mogya a ɛfata a wɔde ma no so. Eyi boa nipadua no ma onya mframa pa a ehia, na abofra no tebea tu mpɔn ntɛmntɛm. Ɛtɔ mmere bi a, sɛ mogya dodow a ɛwɔ akyi berɛmo mu no dɔɔso dodo a, ebia ɛho behia sɛ oduruyɛfo no yi mogya no bi fi abofra no nipadua mu bere a ɔde mogya no rema no.
Sɛ ɛsan ba bio a, dɛn na ɛsɛ sɛ yɛyɛ?
Ɔhaw biako a ɛwɔ splenic sequestration ho ne sɛ sɛ ɛba pɛ a, ɛda adi kɛse sɛ ɛbɛsan aba bio . Ɛho behia sɛ mmofra binom di tebea yi ho dwuma mpɛn pii wɔ wɔn nkwa nna mu.
Sɛ ɔhaw yi kɔ so ba a, nnuruyɛfo betumi ahyɛ nyansa sɛ wɔnyɛ oprehyɛn yi akyi berɛmo no (splenectomy). Sɛ woyi akyi berɛmo no fi hɔ a, ebetumi asiw tebea a asiane wom yi ano koraa sɛ ɛrensan mma bio. Nanso, sɛ woyi akyi berɛmo no fi hɔ wie a, tumi a nipadua no tumi ko tia nyarewa (immunity) no so tew kakra, enti ɛho behia sɛ abofra no nom nnuru titiriw a ekum ɔyare mmoawa ne nnuru a wɔde bɔ ne ho ban de bɔ ne ho ban fi ɔyare mmoawa bi ho. Wo duruyɛfo bɛkyerɛkyerɛ eyi mu akyerɛ wo pefee.
Nkrasɛm a Wɔde Kɔ Fie
- Splenic sequestration, a ebetumi aba wɔ abofra a ɔwɔ sickle cell yare mu no yɛ tebea a emu yɛ den a ɛde ne nkwa to asiane mu a ɛhwehwɛ sɛ wɔsa no yare ntɛm ara.
- Hwɛ yiye bere nyinaa sɛ wubehu sɛnkyerɛnne ahorow te sɛ yafunu no benkum so ɛyaw, yafunu a ɛyɛ fitaa, ɔbrɛ kɛse, ne akyi berɛmo a ahonhon.
- Sua sɛnea wobɛbɔ wo ba no akyi berɛmo mu no fi wo duruyɛfo hɔ. Ebetumi aboa ma woagye wo ba no nkwa.
- Sɛ wuhu sɛnkyerɛnne ahorow a yɛaka ho asɛm wɔ atifi hɔ no biara ara pɛ a, nsɛe bere na fa wo ba no nkɔ ayaresabea a ɛbɛn wo no Emergency Treatment Unit (ETU) .
- Esiane sɛ asiane kɛse wɔ hɔ sɛ tebea yi bɛsan aba bio nti, wo ne wo duruyɛfo nni nkitaho bere nyinaa na di akwankyerɛ a wɔde ama no akyi sɛnea ɛfata.











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