Yala i denmisɛnnin kunkolo bɛ i ko a ka bon dɔɔnin wa? Walima i b’a miiri ko i bɛ kɔfɛ kojugu ka fɛnw kɛ u si hakɛ la wa? Tuma dɔw la, a bɛnnen don ka siran dɔɔni ni aw ye nin ɲɔgɔnna fɛnw ye. Bi an bɛna kuma bana dɔ kan min bɛ se ka kɛ kunkolodimi ye dɔɔni bangebagaw bolo, nka a bɛ se ka ɲɛnabɔ n’i y’a dɔn. O ye Dandy-Walker ka bana ye . Aw kana aw hakili ɲagami, an bɛna kuma o kan ka ɲɛ ani cogo nɔgɔman na.
Dandy-Walker ka bana ye mun ye?
N’an y’a fɔ cogo nɔgɔman na, Dandy-Walker Syndrome ye bana ye min bɛ sɔrɔ ni den bangera ni fɛn dɔ yera a ka hakili yiriwali cogo la . O bɛ Weele tuma dɔw la ko Dandy-Walker Malformation. O bɛ kɛ ka den to kɔnɔbara la, ni a kunkolo bɛ ka yiriwa. O kɔrɔ ye ko a ye bana ye min bɛ sɔrɔ bangekɔlɔsi fɛ .
O bɛ nɔ bila kosɛbɛ kunsɛmɛ na, o ye kunsɛmɛ fitinin ye min bɛ an kunkolo kɔfɛ, kunsɛmɛ na , ani a lamini yɔrɔ la. yala aw b' a dɔn ko nin yɔrɔ in min bɛ wele ko cerebellum , o ye an ka Cɛmancɛ-nɛrɛmugu yɔrɔ nafamaba ye wa . O de bɛ an farikolo lamagacogo ɲɛnabɔ. O dɔrɔn tɛ, nka a bɛ dɛmɛ don fɛn caman wɛrɛw fana na. Aw ye a lajɛ:
- A bɛ an farikolo ka balansi , a ka ɲɔgɔndɛmɛ ani a jɔcogo kɔlɔsi .
- A bɛ dɛmɛ fana don ko minnu bɛ tali kɛ yeli la .
- An ka se ka miiri (hakilila) fana bɛ tali kɛ fɛnw na i n’a fɔ fɛn dɔ faamuyali n’a hakili toli.
- Motɛri seko ye fɛnw ye i n’a fɔ farikolo yɔrɔw labɛnni.
- A fana bɛ kɛ sababu ye ka kɛwalew kunbɛn.
O bɛ wele ko Dandy-Walker ka bonya da farikoloɲɛnajɛla fila kan , Walter Dandy, MD, ani Arthur Walker, MD, minnu ye o bana ɲɛfɔ san 1900 waatiw la.
Mun bɛ kɛ mɔgɔ dɔ ka hakili la min bɛ ni Dandy-Walker ye?
O bɛ ɲɛ, o tuma na fɛ, mun bɛ kɛ mɔgɔ dɔ ka hakili la ni Dandy-Walker ye? Fɛn dɔw filɛ nin ye minnu bɛ se ka kɛ:
- Sugunɛ kɔnɔna naaninan bɛ bonya. O ye yɔrɔ ye min bɛ ɲɛgɛnɛsira lamini. O de bɛ kunsɛmɛnasumaya (CSF) dɛmɛ ka taa kunsɛmɛ sanfɛla ni duguma yɔrɔw ni kɔkolo cɛ .
- Kɔnɔbara-yɔrɔ fla, o kɔrɔ ye ko cɛmancɛ-yɔrɔ min bɛ fàn fla ni ɲɔgɔn cɛ, o bɛ Weele ko cerebellar vermis , wa a bɛ Se ka Tɔnɔ pewu walima a yɔrɔ dɔ.
- Kuru , min bɛ i n’a fɔ jikuru, o bɛ sɔrɔ kɔnɔbara naaninan kɛrɛfɛ.
- Kungolo dawolo, o kɔrɔ ye ko kɔfɛla, o bɛ bonya.
- Tuma dɔw la, kunsɛmɛnasumaya (CSF) bɛ se ka caya, ka dɔ fara degun kan kungolo kɔnɔ ani ka a funu. an bɛ min wele ko jibolisira , o ye nin ye .
Dandy-Walker ka bana ka ca cogo di?
Etazuni jamana ka kunnafoniw b’a jira ko Dandy-Walker Malformation bɛ den kelen ɲɔgɔn minɛ den 25 000 fo 35 000 o . A ka ca npogotigininw na ka tɛmɛ cɛdenw kan.
Mun de bɛ Dandy-Walker ka bana bila mɔgɔ la?
Nin bana in bɛ sɔrɔ ni gɛlɛya dɔ bɛ den kunsɛmɛ na min bɛ bonya kɔnɔbara la . Tuma dɔw la, o bana in bɛ se ka sɔrɔ jamu caman cili fɛ .
Dandy-Walker bɛ mɔgɔ minnu na , olu dɔw bɛ se ka kɛ ni kolosinsinnanw ka banaw ye . O kɔrɔ ye ko kolosinsinnanw yɔrɔ dɔw tɛ yen walima u bɛ fara u kan. I b’a dɔn ko kolosinsinnanw bɛ i n’a fɔ pakew minnu bɛ an ka jamu ta. Dandy-Walker Syndrome fana bɛ se ka kɛ jamu bana dɔ ye min bɛ sɔrɔ ka fara bangekɔlɔsi fɛɛrɛ caman wɛrɛw kan.
Kun damadɔ wɛrɛw bɛ yen minnu bɛ se ka kɛ:
- Banakisɛ suguya dɔw bɛ se ka bɔ ba la ka taa den na kɔnɔmaya waati.
- Tumu walima fura dɔw tali kɔnɔmaya waati.
- sukarodunbana bɛ n ba la .
Dandy-Walker taamasiɲɛw bɛ daminɛ tuma jumɛn?
Tuma dɔw la, bana taamasiɲɛw bɛ bɔ yɔrɔnin kelen ani ka jɛya . Tuma wɛrɛw la, bana taamasiɲɛw bɛ se ka kɛ bangebagaw la k’a sɔrɔ u m’a dɔn ko foyi man ɲi.
A ka ca a la , bana taamasiɲɛw bɛ ye den ka ɲɛnamaya kalo fɔlɔw kɔnɔ , nka a bɛ se ka kɛ denmisɛn dɔw tɛ se ka bana sɔrɔ fo u si bɛ san 3 walima san 4 la .
Dandy-Walker Syndrome taamasiɲɛw ye jumɛnw ye?
Taamasiɲɛ minnu bɛ se ka ye denmisɛnniw na, olu ye:
- yiriwali latɛmɛni ye waati latɛmɛni ye yiriwali siratigɛ la minnu bɛ bɛn san hakɛ ma . Misali la, ka mɛn ka sigi ka wuli, ka wuluwulu, ani ka taama.
- Kungolo ka bon ka tɛmɛ a cogo kɔrɔ kan.
- Hypotonia , o kɔrɔ ye ko farikolo bɛ sɔgɔsɔgɔ dɔrɔn.
- Spasticity kɔrɔ ye ko farikolo fasaw bɛ gɛlɛya ani ka kɔrɔta ka gɛlɛn.
Taamasiɲɛ minnu bɛ ye denmisɛn kɔrɔbaw la:
- Fɔɔnɔ, kirinni, ani dimi – o ye degun caya taamasiɲɛw ye kunsɛmɛ kɔnɔ.
- Baarakɛɲɔgɔnya bɔnɛ, taamacogo lamaga-lamagali, ani lamaga-lamagali minnu tɛ deli ka kɛ i n’a fɔ ɲɛkisɛw – o ye gɛlɛya taamasiɲɛw ye kunsɛmɛ na.
A taamasiɲɛ wɛrɛw bɛ se ka kɛ:
- Funu walima kuru dɔ bɛ kɛ kungolo kɔfɛ.
- Gɛlɛya minnu bɛ sɔrɔ nɛrɛmugumaw la minnu bɛ kɔ, ɲɛda ani ɲɛw mara.
- ninakilicogo tɛ kelen ye .
- Kɔnɔboli .
- Hakilila-jɔ-baaraw .
- Jilajidɛsɛ taamasiɲɛw .
Danfara jumɛn bɛ Dandy-Walker Complex ni Dandy-Walker Syndrome cɛ?
Nin bɛ se ka kɛ ko a ka gɛlɛn dɔɔnin, nka n bɛna a nɔgɔya. Dandy-Walker Complex ye bana kulu ye minnu taamasiɲɛw bɛ ɲɔgɔn ta. Dandy-Walker Syndrome ye o banaw dɔ dɔrɔn de ye.
Sariya wɛrɛw bɛ yen minnu bɛ Dandy-Walker Complex kɔnɔ:
- Isolated Cerebellar Vermis Hypoplasia walima Dandy-Walker Variant : Nin bana in na, kunsɛmɛnasumaya ka dɔgɔn walima a tɛ yiriwa ka ɲɛ. Nka, fɛn wɛrɛ minnu bɛ kɛ ka fɛnw sigicogo yeli kɛ denmisɛnniw ka hakili la, minnu bɛ ni Dandy-Walker Syndrome ye, olu tɛ ye. Denmisɛn minnu sɔrɔla ni nin bana in ye, olu fanba bɛ bonya cogo bɛnnen na.
- Mega Cisterna Magna : Nin cogo in na, kɔfɛla min bɛ kungolo kɔfɛ, o bɛ bonya, nka kunsɛmɛnasumaya bɛ kɛ cogo la. A ka ca a la, Mega Cisterna Magna tɛ kɛnɛya gɛlɛya si lase mɔgɔ ma.
- Posterior Fossa Arachnoid Cyst : Nin ye kuru ye min bɛ sɔrɔ kɔfɛla la. A man teli kosɛbɛ denmisɛnw ka bana taamasiɲɛw sɔrɔ hali ni nin kuru suguya in bɛ u la.
Bana wɛrɛ jumɛnw bɛ tali kɛ Dandy-Walker Syndrome la?
Dandy-Walker bɛ denmisɛn minnu na, olu fana bɛ se ka gɛlɛya sɔrɔ u farikolo yɔrɔ wɛrɛw la. I n'a fo:
- Corpus Callosum (ACC) tɛ yen , o ye bana ye min man teli ka sɔrɔ, a bangenen don.
- Gɛlɛya minnu bɛ fɛnw dilancogo la i n’a fɔ farikolo yɔrɔw, ɲɛda, dusukun, bolokɔniw.
Yala hakiliɲagami bɛna kɛ ne den na wa?
Dandy-Walker bɛ denmisɛn minnu na , olu tilancɛ tɛ se ka kɛ hakiliɲagami ye . Hakilila-dɛsɛ ka teli ka kɛ denmisɛnniw na minnu bɛ ni Dandy-Walker ye, nin bana ninnu bɛ minnu na:
- Jidɛsɛ jugumanba .
- Kɔrɔɲɔgɔnmaya cogoyaw .
- bangekɔlɔsi bana wɛrɛw .
Aw k’aw hakili to a la ko den kelen-kelen bɛɛ tɛ kelen ye, o la sa, den kelen ka ko kɛlen tɛna kɛ kelen ye ni den wɛrɛ ta ye.
Dandy-Walker ka bana bɛ sɔrɔ cogo di?
Tuma dɔw la dɔgɔtɔrɔw walima bangebagaw bɛ se k’a kɔlɔsi ko den kunkolo ka bon kojugu . Walima u bɛ se k' a kɔlɔsi ko den tɛ ka yiriwali siratigɛw dafa . Dɔgɔtɔrɔw bɛ se ka yamaruya di ko u ka hakili lajɛ walasa ka Dandy-Walker ka bana sɛgɛsɛgɛ. O sɛgɛsɛgɛliw bɛ se ka kɛ ninnu ye:
- Ultrason (ultrason) sɛgɛsɛgɛli.
- CT scan (CT scan) kɛcogo.
- MRI sɛgɛsɛgɛli.
Tuma dɔw la, nin bana in bɛ se ka sɔrɔ jiginni ɲɛfɛ ultrasound walima den ka MRI sɛgɛsɛgɛli senfɛ sani den ka bange.
Ni Dandy-Walker bɛ n den na, yala denbaya ka kan ka sɛgɛsɛgɛli kɛ a ka jamu kan wa?
Ni Dandy-Walker Malformation bɛ aw den na, a nafa ka bon aw ka kuma aw ka dɔgɔtɔrɔ fɛ jamu ladilikanw kan . Nin bana in bɛ mɔgɔ minnu na, olu hakɛ fitinin dɔ fana bɛ se ka kɛ ni denbaya kɔnɔmɔgɔ dɔ ye min bɛ ni bana in ye. Ikomi a bɛ se ka kɛ ko jamu dɔ bɛ a la, dɔgɔtɔrɔ caman bɛ a fɔ ko jamu sɛgɛsɛgɛli ka kɛ .
Dandy-Walker Syndrome furakɛcogo jumɛnw bɛ yen?
Furakɛli bɛ bɔ Dandy-Walker Syndrome taamasiɲɛw de la. A nafa ka bon ka dɔgɔtɔrɔ dɔ ka sɛgɛsɛgɛli kɛ ka ɲɛ sani aw ka furakɛli daminɛ. Misali la, dɔgɔtɔrɔw bɛ se ka ninnu fɔ:
- Ventriculoperitoneal (VP) Shunt : Operelikɛlaw bɛ minɛn fitinin dɔ don a kɔnɔ min bɛ wele ko VP shunt walasa ka ji tɛmɛnen bɔ kunsɛmɛ na. Nin shunt in bɛ se ka dɔ bɔ degun na kunsɛmɛ na ani ka bana taamasiɲɛw ɲɛ.
- Fura : Aw den ka dɔgɔtɔrɔ bɛ se ka furaw di aw ma walasa ka kirinni kunbɛn.
- Furakɛli : Farikoloɲɛnajɛ ni baarakɛ-furakɛli bɛ denmisɛnw dɛmɛ ka farikolo fanga sabati. Furakɛlaw bɛ se fana ka denmisɛnw kalan don o don baara kɛcogo kura la. Kuma furakɛli bɛ dɛmɛ don kanko ni kuma yiriwali la.
- Kalan kɛrɛnkɛrɛnnen : Kalan kɛyɔrɔ min bɛ kɛ ka kɛɲɛ ni mɔgɔw sago ye, o bɛ denmisɛnw dɛmɛ u ka se k’u ka kalanko ni sigidako kuntilenna sɔrɔ.
Dandy-Walker Syndrome bɛ denmisɛn minnu na, olu ka siniɲɛsigi ye mun ye?
Aw den ka siniɲɛsigi ni a ka ɲɛnamaya waati bɛ bɔ a ka cogoya de la.A bɛ bɔ a juguya hakɛ la , ani ni bangekɔlɔsi bana wɛrɛw bɛ yen minnu bɛ se ka kɛ den na.
Nin bana in bɛ mɔgɔ minnu na, olu bɛ se ka ko suguya caman sɔrɔ. dɔw taamasiɲɛw ka nɔgɔn . dɔw fana ka fiyentɔya jugumanba bɛ u la . Den dɔw bɛ se ka hakililata seko ɲuman sɔrɔ ni furakɛli kɛcogo ɲuman ye. Dɔ wɛrɛw fɛ, hali n’u ka dɔgɔtɔrɔso jɛkulu ye bana in sɛgɛsɛgɛ ani k’a furakɛ joona, a bɛ se ka kɛ u tɛ se ka se o hakɛ ma.
Yala Dandy-Walker Syndrome bɛ se ka bali wa?
Fɛɛrɛ dɔnta tɛ yen min bɛ se ka Dandy-Walker Syndrome kunbɛn. Nka, ladonni min bɛ kɛ tuma bɛɛ sani jiginni ka kɛ, o bɛ sababu ɲuman di aw ma ka kɔnɔta kɛnɛman sɔrɔ. Aw bɛ dɔgɔtɔrɔ ka laadilikanw labato walasa ka to kɛnɛya la ka aw kɔnɔma to.
Ne bɛ se ka ne den ladon cogo di ni Dandy-Walker ye?
Ni aw ye aw sen don a la joona, o bɛ se ka kɛ sababu ɲuman ye ka furakɛli ɲɛ. Ni aw y’a ye ko aw den tɛ ka yiriwali kɛcogo ɲumanw dafa i n’a fɔ a sigili, a taamacogo, walima a bɛ kuma a waati la, aw bɛ taa dɔgɔtɔrɔso la. O kɔfɛ, u bɛ se ka bana sɛgɛsɛgɛli tigitigi kɛ ani ka furakɛli fɛɛrɛ ɲumanba di aw den ma.
Aw den ka Dandy-Walker ladonni jɛkulu bɛ se ka kɛ ninnu ye:
- Denmisɛnw ka dɔgɔtɔrɔ .
- Yiriwali kɛrɛnkɛrɛnnenw .
- Kuma, baara ani farikoloɲɛnajɛ furakɛlikɛlaw .
- Kalan kɛrɛnkɛrɛnnenw baarakɛlaw .
Ne ka kan ka mun ɲininka n ka dɔgɔtɔrɔ la Dandy-Walker Syndrome ko la?
Ni a sɔrɔla ko Dandy-Walker bɛ den na, aw bɛ dɔgɔtɔrɔ ɲininka nin ko ninnu na:
- Yala ne den mago bɛna kɛ shunt la wa ?
- Furakɛcogo wɛrɛ jumɛnw bɛ ne den na?
- Ne den ka siniɲɛsigi (laɲini) bɛna kɛ cogo di?
- An bɛ se ka n den ka bana taamasiɲɛw ɲɛ cogo di ?
- Yala an ka kan ka jamu sɛgɛsɛgɛli kɛ wa ?
A laban na, aw hakili to nin na.
Dandy-Walker Syndrome, n’a bɛ fɔ fana ko Dandy-Walker Malformation, o ye kunsɛmɛ bana ye min bɛ sɔrɔ sani den ka bange. Dandy-Walker bɛ denmisɛn minnu na, olu ka teli ka se u ka yiriwali siratigɛ la kɔfɛ. Den dɔw mago bɛ shunt la walasa ka ji tɛmɛnen bɔ u kunsɛmɛ na. Furakɛliw bɛ se ka denmisɛnw dɛmɛ u ka don o don baaraw ɲɛnabɔ, ka ɲɛtaa sɔrɔ lakɔli la, ani ka ɲɛnamaya kɛ cogo la min bɛ u wasa. Ni aw y’a ye ko aw den kunkolo ka bon kojugu walima ko u tɛ sigi, ka taama, walima ka kuma i n’a fɔ a tun bɛ fɔ cogo min na, aw bɛ kuma aw ka dɔgɔtɔrɔ fɛ. A dɔnni joona ani a furakɛcogo ɲuman nafa ka bon. Aw kana aw hakili ɲagami, nin bana in bɛ se ka furakɛ ni dɔgɔtɔrɔw ka laadilikanw ye.
` Dandy-Walker Syndrome, Sugunɛbilenni, Bangekɛnɛ, Cerebellum, Hydrocephalus, Yiriwali kɔfɛ, Denmisɛnw ka kɛnɛya











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