Skip to main content

Yala ninakilidegun bɛ aw denmisɛnnin na i n’a fɔ nin wa? An ka kuma "Double Aortic Arch" kan!

Yala ninakilidegun bɛ aw denmisɛnnin na i n’a fɔ nin wa? An ka kuma "Double Aortic Arch" kan!

Yala tuma dɔw la, a bɛ kɛ i denmisɛnnin na i n’a fɔ a ninakili gɛlɛyara wa? Yala a bɛ sɔgɔsɔgɔ tuma min na a bɛ dumuni di walima ka sin di den ma wa? Walima a bɛ mankan kabakomaw bɔ k’a to ninakili la wa? Hali ni ninnu bɛ se ka kɛ denmisɛnniw ka banaw ye minnu ka ca, bana dɔ bɛ se ka kɛ o kɔfɛ, min ka jugu kosɛbɛ, nka a bɛ se ka furakɛ. O bana sugu dɔ min man teli ka sɔrɔ nka a nafa ka bon ka a dɔn, o bɛ wele ko "Double Aortic Arch". An ka kuma o kan ka ɲɛ bi.

N’an y’a fɔ cogo nɔgɔman na, joli siraba min bɛ joli ta ka bɔ i den dusukun na ka taa a farikolo tɔ la, o ye joli-sira-funu ye . A ka c’a la, o ye minɛn kelen ye, min ka bon. o joli sira kurulen min bɛ dusukun sanfɛ , o bɛ wele ko aortic arch .

Nka, den min bɛ ni "Aortic Arc double" ye, o "arc aortique" bɛ kɛ fila ye. O kɔrɔ ye ko joli sira wɛrɛ bɛ siri nin "aortic arch" kunba in na, ka kɛ arch filanan ye. O bɔgɔdaga fila bɛ na ɲɔgɔn fɛ, ka kɛ bololanɛgɛ ye den ka fiɲɛbɔlan (fiɲɛbɔlan) ni dumunikɛminɛn (dumunikɛyɔrɔ) lamini na . Miiri k’a filɛ, mun bɛ kɛ ni nin bololanɛgɛ in datugulen don? O waati de la den bɛ daminɛ ka taamasiɲɛ jugumanw sɔrɔ i n’a fɔ ninakili gɛlɛya, mankan bɔli ninakili la, ani dumuni munumunu gɛlɛya.

Nin "aortic arch" in bɛ sɔrɔ kɔnɔmaya daminɛ na kosɛbɛ, dɔgɔkun fila ni dɔgɔkun wolonwula cɛ. O waati kɔnɔna na, dusukun ni joli siraw bɛ yiriwa cogo gɛlɛnba la. Yɔrɔ dɔw bɛ Bɔ, wa waati dɔ tɛmɛnen kɔ u mago tɛ u la tuguni wa u bɛ tunun. "Aortic arque double" bɛ Sɔrɔ nin ɲɔgɔnna fɛn dɔ de fɛ. Kɔnɔmaya dɔgɔkun duurunan lamini na, joli sira min tun ka kan ka tunun, kun dɔ la min tɛ dɔn, o tɛ tunun wa o "arc double aortique" bɛ sɔrɔ. Nin ye dusukunnabana ye min bɛ sɔrɔ bangekɔlɔsi fɛ , o kɔrɔ ye ko den bɛ bange ni o ye.

Nin bana in min bɛ wele ko "arc aortique double", o bɛ dusukunnabana bangenenw kulu dɔ la min bɛ wele ko "vasculaire rings". Olu bɛ kɛ sababu ye ka den fiɲɛbɔlan ni a ka dumunikɛminɛnw degun.

Nin "vasculaire rings" ninnu ye mun ye?

O bɛ ɲɛ, "Vascular Rings" ye, i n'a fɔ n y'a fɔ cogo min na ka tɛmɛ, cogoyaw ye, "aortic arch" bɛ yiriwa cogo la min tɛ a cogo la, o bɛ se ka kɛ sababu ye den ka fiɲɛbɔlan (trachea), dumunikɛminɛn (esophagus), walima u fila bɛɛ ka degun. ninnu ye dusukunnabana bangenenw ye minnu man ca kosɛbɛ . Miiri k’a filɛ, den kɛmɛ o 100, kelen ɲɔgɔn bɛ bange ni dusukunnabana sugu dɔ ye min bɛ sɔrɔ bange kɔnɔ. Nka "vasculaire ring" bɛ den kelen dɔrɔn de minɛ den 10000 o 10000 la. A ka dɔgɔ o cogo la.

"Vascular Rings" suguya jɔnjɔnw ye jumɛnw ye?

O "vasculaire rings" suguba damadɔ bɛ yen. An k’a lajɛ u ye mun ye:

  • Aortic Arch fila : O la, "aortic arches" fila (numan fɛ ni numan fɛ) bɛ fiɲɛbɔlan ni dumunikɛminɛnw lamini. An bɛ kuma barokunba min kan, o de ye nin ye.
  • Aorte kinibolo ni aberrant subclavian artery ani left ligamentum: Aortic arque kelen bɛ yan, nka a bɛ fiɲɛbɔlan kinin fɛ (a ka c’a la, a bɛ kɛ numan fɛ). O cogo la, numanbolo-kɔnɔ-sira min bɛ joli di den bolokɔniw ma, o bɛ daminɛ aorte la ka tɛmɛ fiɲɛbɔlan ni dumunikɛminɛn kɔfɛ. O joli-sira-funu-bololan in bɛ dafa ni a faralen don ɲɔgɔn kan ni numanbolo-yɔrɔ ye, o ye joli-sira-funu tolen ye min tun bɛ den ka ɲɛnamaya kɔnɔ, o kɔfɛ a bɛ tunun.
  • Aorte numanbolo ni aberrant kinibolo subclavian artery: Yan, kininbolo subclavian artery bɛ tɛmɛ trachea ni esophagus kɔfɛ, ka u degun.
  • Innominate artery compression : Joli innominate (brachiocephalic) ye joli sira bolofara dɔ ye. O cogo la, a bɛ daminɛ fiɲɛbɔlan numan fɛ, ka sɔrɔ ka tɛmɛ fiɲɛbɔlan ɲɛfɛ ka taa kinin fɛ. O bɛ degun bila fiɲɛbɔlan na.
  • Fogonfogon la sɔgɔsɔgɔninjɛ : Fogonfogon kiniyanfan bɛ daminɛ fogonfogon kiniyanfan fɛ ka tɛmɛ fiɲɛbɔlan ni dumunikɛminɛn cɛ.

Fɛn min bɛ kɛ ninnu bɛɛ la, o ye ko fiɲɛbɔyɔrɔ walima dumunikɛminɛn bɛ nɔ bila cogo dɔ la.

Yala "Double Aortic Arch" suguya dɔw bɛ yen wa?

Ɔwɔ, "arc aortique double" suguya belebele saba bɛ yen. Olu bɛ danfara Bɔ ni jiribolo min ka bon, ani n’o jirisunba min ka bon, o bɛ fiɲɛbɔlan kinin fɛ walima numan fɛ.

  • Numanbolo-yɔrɔ min bɛ fanga la ni numanbolo-yɔrɔ fitinin ye: Nin ye suguya ye min ka teli ka kɛ, a bɛ sɔrɔ kɛmɛsarada la 80 ɲɔgɔn na.
  • Numanbolo-yɔrɔ min bɛ fanga la ni numanbolo-yɔrɔ fitinin ye: O bɛ ye kɛmɛsarada la 10 ɲɔgɔn na.
  • Arches balancées : O fana bɛ ye kɛmɛsarada la 10 ɲɔgɔn na.

"Vasculaire ring" sugu jumɛn de bɛ ye ka caya?

Dɔgɔtɔrɔw tun b'a miiri ko "arc d'aortique double" de ye "ring vasculaire" suguya ye min ka ca kosɛbɛ. Nka ɲinini kura y'a Jira ko "aortic arch kinin fɛ" ka ca tiɲɛ na.

Nka, fɛn wɛrɛ bɛ yen. Den minnu bɛ ni "aorte kiniyanfan fɛ" ye, olu ka teli ka dusukunnabana wɛrɛw sɔrɔ bangekɔlɔsi fɛɛrɛw la ka tɛmɛ denw kan minnu ka "aortic arch double" bɛ u la. Nka, u ka teli ka sɔrɔ u bange waati. O bɛ kɛ barisa "arc right aortic" bɛ se ka kɛ a tɛ taamasiɲɛw bila a daminɛ na. O la, opereli bɛ se ka kɛ o gɛlɛya in na kalo 6 ni kalo 18 cɛ.

Bana min bɛ wele ko ``Double Aortic Arch'' , o ye joli siraw suguya ye min ka teli ka kɛ . O la, den ka dɔgɔtɔrɔ bɛ se ka gɛlɛya in sɛgɛsɛgɛ joona. Ni aw ye den minnu suma ni joli sira suguya wɛrɛw ye, den minnu bɛ ni ``Double Aortic Arch'' ye, olu bɛ se ka kɛ opereli ye u bangenen kɔfɛ joona.

"Double Aortic Arch" taamasiɲɛw ye mun ye?

A ka ca a la, "aortique double" taamasiɲɛw bɛ sɔrɔ ni den ka fiɲɛbɔlan, a ka dumunikɛminɛnw walima a fila bɛɛ degunna. O degun in bɛ se ka nɔ bila den ninakili, a baloli walima a dusukun baara la.

A ka ca a la, nin taamasiɲɛ ninnu bɛ ye denmisɛnniw na (kɛrɛnkɛrɛnnenya la ni bana in ka jugu), nka tuma dɔw la, u bɛ se ka ye kabini san saba, walima hali funankɛya la.

A bɛ se ka kɛ ko denmisɛn dɔw bɛ se ka sɛgɛsɛgɛ cogo jugu la ko sɔgɔsɔgɔninjɛ bɛ u la barisa a taamasiɲɛw bɛ ɲɔgɔn ta. Nin bana in bɛ sɔrɔ dɔrɔn ni sɔgɔsɔgɔninjɛ furakɛli ma ɲɛ ani ni sɛgɛsɛgɛli wɛrɛw kɛra.

Ninakilidegun taamasiɲɛw

Denmisɛnw ni denmisɛn minnu bɛ ni "arc double aortique" ye, olu kɛmɛsarada la, 91 ɲɔgɔn bɛ nin taamasiɲɛ ninnu sɔrɔ ninakili fɛ. U ye:

  • Mankan kabakoma min bɛ kɛ ni ninakili bɛ (mankanba min bɛ wele ko `stridor` walima sɔgɔsɔgɔkan min bɛ wele ko `wheezing`) .
  • Sɔgɔsɔgɔ min mankan bɛ i n'a fɔ "seal barking". O ni sɔgɔsɔgɔninjɛ bɛ tali kɛ ɲɔgɔn na min bɛ kɛ bana dɔ senfɛ min bɛ wele ko "croup".
  • ninakilidegun minnu bɛ kɛ tuma caman na .

Kɔnɔbara basigilen taamasiɲɛw

Denmisɛnw ni denmisɛn minnu bɛ ni "arc double aortique" ye, olu kɛmɛsarada la, 40 ɲɔgɔn bɛ nin dumunikɛcogo taamasiɲɛ ninnu sɔrɔ. U dɔw ye:

  • Kɔnɔnafili ka a to sin dili la walima ka sin di den ma.
  • Munumunu gɛlɛya (dumunikɛbaliya) . A ka ca a la o bɛ ye den ye dumuni gɛlɛnw dunni daminɛ kɔfɛ.
  • Gɛlɛya sɔrɔli ka girinya .
  • Dumuni bɛ segin ka na san fɛ ka don dawolo la (`Regurgitation/reflux`) .

Dusukun taamasiɲɛw

Denmisɛnw ni denmisɛn minnu bɛ ni "arc double aortique" ye, olu kɛmɛsarada la, 30 ɲɔgɔn bɛ dusukun taamasiɲɛw sɔrɔ. Olu dɔw ye:

  • Disi dimi .
  • Dusukun mankan min tɛ cogo la (`Dusukun murmur`) .
  • Fari bulama (cyanose) .

Mun bɛ kɛ sababu ye ka "Double Aortic Arch" sɔrɔ?

"Double otic arch" sababu tigitigi ma Sɔrɔ fɔlɔ . Hali ni nin bana in ka teli ka ye denw na minnu kɔnɔma don "in-vitro fertilization" (IVF) fɛ , a sababu tigitigi tɛ dɔn.

Aortic arch fila bɛ se ka kɛ fana ni furakɛli cogoya wɛrɛw ye. Den kɛmɛsarada la 12 ɲɔgɔn minnu ka aorte fila bɛ u la, dusukunnabana wɛrɛ bɛ u bangenen fɛ, i n’a fɔ ventriculaire septal defect (VSD) ani tetralogy of Fallot . Ka fara o kan, den kɛmɛsarada la, 20 ɲɔgɔn minnu ka aorte arch fila bɛ u la, olu ka jamu banaw bɛ u la i n’a fɔ kolosinsinnan 22q11 bɔli ani trisomie 21 (Down syndrome) .

"Double Aortic Arch" bɛ dɔn cogo di?

Aortic arch fila bɛ sɔrɔ a danma walima ni a taamasiɲɛw daminɛna. Tuma dɔw la, a bɛ sɔrɔ a danma kɔnɔmaya waati, bange kɔfɛ, walima ja sɛgɛsɛgɛliw senfɛ minnu bɛ kɛ kun wɛrɛ la. Kabini san 2004, mɔgɔ minnu bɛ sɔrɔ ni nin bana in ye sɛgɛsɛgɛli fɛ kɔnɔmaya waati, olu hakɛ cayara. O nafa ka bon kosɛbɛ, barisa furakɛli bɛ se ka boloda den bangera dɔrɔn.

Walima, a bɛ se ka dɔn ni bana taamasiɲɛw bɔra den bangenen kɔfɛ. Den ka dɔgɔtɔrɔ bɛna kuma aw fɛ bana taamasiɲɛw kan ka sɔrɔ ka sɛgɛsɛgɛli dɔw kɛ.

Sɛgɛsɛgɛliw walasa ka "Double Aortic Arch" sɛgɛsɛgɛ.

Sɛgɛsɛgɛli kunbaba minnu bɛ kɛ ka nin bana in sɛgɛsɛgɛ, olu ye:

  • Disi lajɛ: A ka ca a la, nin ye sɛgɛsɛgɛli fɔlɔ ye min bɛ kɛ.
  • CT scan (CT scan) kɛcogo.
  • Echocardiogramme (Echo) sɛgɛsɛgɛli : O bɛ mɔgɔ dɛmɛ kosɛbɛ walasa ka a dɔn ni dusukunnabana wɛrɛw bɛ yen.
  • MRI (MRI) sɛgɛsɛgɛli.

Tuma dɔw la, fogonfogon lajɛ bɛ se ka kɛ walasa ka den ka fiɲɛbɔlan sɛgɛsɛgɛ. O bɛ se ka kɛ ninakilidegunw jaabi la sani aorte arch fila ka sɔrɔ. Walima, a bɛ se ka kɛ sani opereli ka kɛ walasa ka operelikɛla dɛmɛ a k’a dɔn fɛn min bɛ gɛlɛya lase mɔgɔ ma.

Jɛnkulu sɛgɛsɛgɛli bɛ dɛmɛ ka jamu cogoyaw dɔn.

"Arc Aortique Double" furakɛ cogo di?

Opereli ka kan ka kɛ walasa ka "arc aortique double" cogoya latilen. Hali den minnu ka bana taamasiɲɛ tɛ u la, opereli ka fisa u si kalo 6 ni kalo 9 cɛ. Denmisɛn minnu ka bana taamasiɲɛw bɛ u la, kɛrɛnkɛrɛnnenya la ni bana taamasiɲɛw ka jugu, olu bɛ se ka opereli kɛ ka kɔn o ɲɛ yɛrɛ.

Miiri dɔrɔn, bana min ye "arc aortique double" ye, o dɔnna fɔlɔ san 1737. Opereli fɔlɔ kɛra a la san 1947. An sera yɔrɔ min na kabini o waati! Nin bangekɔlɔsi fɛɛrɛ in bɛ den minnu na, olu sera ka ɲɛnamaya jan kɛ, kɛnɛya la, opereli furakɛli sababu la.

"Double Aortic Arch" opereli bɛ kɛ

"Double Aortic Arch" opereli tɛ mɔgɔ tɔɔrɔ kosɛbɛ, wa a nɔfɛkow bɛ ɲɛ kosɛbɛ . Aw den tɛna kɛ ni "cardiopulmonaire bypass" (dusukun-fogonfogon-masin) sirili ye .

Opereli bɛ kɛ ni fɛɛrɛ ye min bɛ wele ko "barakotomie latérale". O kɔrɔ ye ko operelikɛla bɛ tigɛ kɛ den disi fan kelen na, kɔkili fila ni ɲɔgɔn cɛ. O bɛ kɛ tuma caman na numan fɛ, barisa o yɔrɔ de la den fanba bɛ o kɔkili fitinin "extra" sɔrɔ. Jala sɛgɛsɛgɛli minnu bɛ kɛ sani opereli ka kɛ, olu b’a to operelikɛla bɛ se ka den farikolo kɔnɔna lajɛ ka ɲɛ ani ka opereli boloda ka kɛɲɛ ni o ye.

Operelikɛla bɛ baara kɛ ni "ligating and dividing" fɛɛrɛ ye . O kɔrɔ ye ko jiribolo fitini bɛ siri walasa ka joli bɔli dabila a fɛ. O kɔ, a bɛ tigɛ ka sutura. O kɛcogo bɛ segin ka kɛ fo ka se a kurukuruni ma pewu ani ka degun min bɛ fiɲɛbɔlan ni dumunikɛminɛnw kan, o ka ban.

Aw den bɛna kɛ dɔgɔtɔrɔso la dɔgɔkun kelen ɲɔgɔn, o kɔ a bɛ kɛnɛya ka na so.

"Kommerell diverticulum" (`Kommerell diverticulum - KD`) furakɛli.

A man teli, den dɔw minnu bɛ ni "arc double aortique" ye, olu fana bɛ se ka kɛ ni fɛn ye min bɛ wele ko "Kommerell diverticulum (KD)." O ka teli ka kɛ denw na minnu ka "aortic arch kinin fɛ" bɛ u la, nka a ka dɔgɔn kosɛbɛ fana ni "aortic arch double" bɛ u la.

Nin `KD` in ye `aneurysme` ye, joli sira min bɛ yiriwa `aorta` jigintɔ la `aortic arch` kɛrɛfɛ. Nin kurukuru in bɛ se ka yɔrɔ ta ka den ka fiɲɛbɔlan ni dumunikɛminɛn digidigi. A bɛ se ka kɛ a tɛna gɛlɛya si lase mɔgɔ ma joona. Nka, a ka di operelikɛlaw ye ka o fana bɔ ni u bɛ `aortique double` da walasa ka gɛlɛyaw bali kɔfɛ.

Dusukunnabana wɛrɛw furakɛli

Ni dusukunnabana wɛrɛw bɛ den na minnu ka kan ka opere, u bɛ se ka furakɛ waati kelen na ni aorte fila ye. O bɛ se ka kɛ sababu ye ka fɛɛrɛ dɔ kɛ min bɛ wele ko ``median sternotomy'' , o ye ka tigɛ kɛ ka jigin disi cɛmancɛ la. Aw den operelikɛla bɛna baro kɛ fɛɛrɛ ɲuman kan aw bolo, ka kɛɲɛ ni ko minnu ka kan ka furakɛ.

Gɛlɛya jumɛnw bɛ se ka sɔrɔ opereli fɛ?

gɛlɛya minnu bɛ sɔrɔ joli sira fila opereli fɛ , olu farati ka dɔgɔn kosɛbɛ . A man teli, den bɛ se ka balo gɛlɛya walima ninakilidegun bɛ to sen na. Ni ninakili gɛlɛya basigilen dɔw bɛ yen, a ka ca a la u bɛ ban opereli kɔfɛ san kelen kɔnɔ.

Opereli minnu bɛ kɛ walasa ka dusukun tantanni fila ni dusukunnabana wɛrɛw latilen, olu gɛlɛyaw bɛ se ka ɲɔgɔn ta. Aw bɛ baro kɛ o faratiw ni gɛlɛya ninnu bɛɛ kan ni aw den ka operelikɛla ye.

Yala "Double Aortic Arch" bɛ se ka bali wa?

Ayi, bana min bɛ wele ko "arc aortique double" o tɛ se ka bali . O ye fɛn ye min bɛ yiriwa kɔnɔmaya daminɛ na, wa a bɛ sɔrɔ bange waati.

"Double Aortic Arch" bɛ mɔgɔ minnu na, olu ka siniɲɛsigi ye mun ye?

Denmisɛnw ni denmisɛn minnu ye "Double Aortic Arch" opereli kɛ , olu ka siniɲɛsigi ka ɲi kosɛbɛ . U bɛ se ka ɲɛnamaya kɛ ani ka baara kɛ cogo bɛnnen na k’a sɔrɔ dankari si ma kɛ u la.

Opereli kɔfɛ, den bɛ se ka to ka ninakili mankan ye fo ka se san kelen ma. O bɛ kɛ barisa den ka fiɲɛbɔlan tɛ yiriwa ka ɲɛ ka a sababu kɛ "aortic arch double" ye. O la, a bɛna waati dɔ ta walasa fiɲɛbɔlan ka barika sɔrɔ.

A man teli kosɛbɛ, denmisɛnw ni denmisɛnw bɛ se ka ninakili taamasiɲɛw sɔrɔ hali bi ka tɛmɛ san kelen kan opereli kɔfɛ.

Min nafa ka bon kosɛbɛ, o ye ka taa ni den ye ka taa a lajɛ tuma bɛɛ ani ka a fɔ dɔgɔtɔrɔ ye ni bana taamasiɲɛ dɔw bɛ aw la minnu bɛ senna. Den kelen-kelen bɛɛ bolo minnu ye dusukun opereli kɛ, olu ladonni kuntaalajan nafa ka bon kosɛbɛ.

Tuma jumɛn na ne ka kan ka ne den ka dɔgɔtɔrɔ wele?

Ni aw ye taamasiɲɛ kura dɔw ye, walima ni a bɛ i n’a fɔ bana taamasiɲɛ kɔrɔlenw bɛ ka juguya, aw bɛ kuma den ka dɔgɔtɔrɔ fɛ o yɔrɔnin bɛɛ. Denmisɛnw ni denmisɛnni fitiniw bɛ ɲɔgɔn Changé fo a bɛ se ka gɛlɛya tuma dɔw la ka a dɔn fɛn min ye ko ye min bɛ se ka kɛ ani min tɛ cogo la. Nka ni o sɔgɔsɔgɔ "sɔgɔsɔgɔninjɛ" bɛ den na walima ni sɔgɔsɔgɔ mankan bɛ a la , aw bɛ o fɔ dɔgɔtɔrɔ ye o yɔrɔnin bɛɛ. A bɛ se ka kɛ denmisɛnniw ka bana ye min bɛ kɛ cogo la. Nka a man teli, a bɛ se ka kɛ dusukun gɛlɛya taamasiɲɛ ye min bɛ nɔ bila den ka ninakili seko la.

Tuma jumɛn na i ka kan ka 911 (kɔrɔtɔko nimɔrɔ) wele?

"Aortique double" bɛ se ka degun bila den ka fiɲɛbɔlan kan min bɛ se ka a ka ɲɛnamaya bila farati la . Ni den fari bɛ kɛ bulama ye (cyanosis) , walima ni den ninakili gɛlɛyara kosɛbɛ , aw bɛ 911 wele joona.

Ne ka kan ka ɲininkali jumɛnw kɛ ne den ka dɔgɔtɔrɔ la?

Ni a sɔrɔla ko "arc d'aortique double" bɛ den na, a ka ca a la aw ka ɲininkali caman kɛ. A nafa ka bon ka den ka bana dɔn, opereli ka kan ka kɛ waati min na, ani ni kɛnɛya gɛlɛya wɛrɛw bɛ den na. Aw bɛ se ka ɲininkaliw kɛ i n’a fɔ:

  • Tuma jumɛn na ne den ka kan ka opere?
  • Opereli bɛ kɛ min? Jɔn de b’a kɛ?
  • Ne ka kan ka n janto bana taamasiɲɛ jumɛnw na so kɔnɔ?
  • Ne bɛ se ka mun kɛ walasa a ka nɔgɔya ne den ma ka to so kɔnɔ?
  • Yala dusukunnabana wɛrɛw bɛ ne den na wa?
  • Yala ne ka kan ka n den walima n ka denbaya tɔw ka jamu sɛgɛsɛgɛli kɛ wa?
  • Ne den ka siniɲɛsigi bɛna kɛ cogo di?

"Syndrome d'arc aortique" ye mun ye? Yala a ni "Double Aortic Arch" tɛ kelen ye wa?

Ɔwɔ, kana o fila ɲagami ɲɔgɔn na. "Aortic Arch Syndrome" ye "Vasculitis" suguya ye min man ca kosɛbɛ . A bɛ fɔ fana ko "Takayasu ka joli-sira-funu" .

"Vasculitis" ye aw joli siraw kogow fununi ye. A bɛ se ka kɛ joli sira suguya bɛɛ la, hali joli sira misɛnniw na, n’o ye kapilɛriw ye. "Takayasu ka joli-sira-funu" ye joli-sira-funu cɛmancɛ ni joli-sira-funu belebelebaw fununi ye. A ka teli ka sɔrɔ "aortic arch" ni a bolo belebelebaw la. O de kama a bɛ wele fana ko "syndrome d'arc aortique".

Takayasu ka joli-sira-funu (a bɛ fɔ fana ko "aortic arch syndrome") bɛ sɔrɔ baliku fitiniw ni baliku fitiniw na . Nin ye gɛlɛya ye min ni "arc double aortique" bangenen tɛ kelen ye fewu , an ye baro kɛ min kan ka tɛmɛ, wa furakɛli min ka kan ka kɛ, o tɛ kelen ye.

A ka c’a la, den bangeli ye nisɔndiya ni seli waati ye. Nka, n’aw y’a ye ko dusukunnabana dɔ bɛ aw den na, kɔnɔmaya waati walima a bangenen kɔfɛ, o nisɔndiya bɛ bila jɔrɔnanko ni dannayabaliya nɔ na. Ni aw y’a dɔn sisan ko aw den bɛ ni “arc double aortique” ye, n’a sɔrɔ aw bɛ aw yɛrɛ ɲininka mun bɛ kɛ o kɔfɛ.

Kana jɔrɛ. Aw ka dɔgɔtɔrɔso jɛkulu bɛna aw dɛmɛ nin bɛɛ la senfɛ-senfɛ. Aw ye fɛɛrɛ fɔlɔ ta kaban, o ye ka fɛn caman dɔn aw den ka bana kan. Kibaru duman ye ko opereli min bɛ kɛ ni aorte fila ye, farati tɛ o la kosɛbɛ, wa a bɛ ɲɛ. Ni dusukunnabana wɛrɛw bɛ den na walima ni a ka banaw bɛ a la, furakɛli bɛ se ka gɛlɛya dɔɔni. Nka, ni ɲɛtaa kɛra den kuraw ladonni na, aw bɛ se ka den dɛmɛ ka ladonni ɲuman sɔrɔ a mago bɛ min na, ka kɛnɛya, ani ka denmisɛnya nisɔndiyalen sɔrɔ.

O la sa, an ye kuma minnu kan, an ka kan ka an hakili to fɛn jumɛnw na kosɛbɛ? (Take-Home Message)

O bɛ ɲɛ, an ka fɛn dɔw lajɛlen fɔ aw ka kan ka minnu to aw hakili la ka bɔ an ye kuma minnu fɔ ka ɲɛsin nin "Double Aortic Arch" ma:

  • "Double aortic arch" ye dusukunnabana ye min bɛ sɔrɔ bange kɔnɔ . Den ka aorte bɛ tila ka kɛ arc fila ye, o bɛ kɛ sababu ye ka fiɲɛbɔlan ni dumunikɛminɛnw degun.
  • A taamasiɲɛ kunbabaw ye ninakili gɛlɛya, sɔgɔsɔgɔninjɛ, dumuni munumunu gɛlɛya, ani ninakilidegun tuma caman .
  • Nin bana in bɛ sɔrɔ sɛgɛsɛgɛliw fɛ i n’a fɔ `CT scan`, `MRI`, `Echocardiogram` . Tuma dɔw la, a bɛ se ka sɔrɔ hali kɔnɔmaya waati.
  • furakɛli ye opereli ye . Nin opereli in farati ka bon kosɛbɛ, wa a bɛ ɲɛ.
  • Den ta opereli kɔfɛAw bɛ se ka ɲɛnamaya kɛ cogo bɛnnen na, kɛnɛya la.
  • Ni bana taamasiɲɛw bɛ den na i n’a fɔ ninakili gɛlɛya walima a daji, aw bɛ dɔgɔtɔrɔ ka laadilikan ɲini joona .
  • Kana jɔrɛ . Ni bi furakɛli yiriwara, o bana in bɛ se ka furakɛ ka ɲɛ. Aw mago bɛ dɛmɛ min na, aw ka dɔgɔtɔrɔso jɛkulu bɛna o di aw ma.

` Double Aortic Arch, Dusukun bana bangenen, Jolilabanaw, Denmisɛnw ka sɔgɔsɔgɔninjɛ, Denmisɛnw ka kɛnɛya, Dusukun opereli

Frequently Asked Questions (FAQ)

"Vascular Rings" suguya jɔnjɔnw ye jumɛnw ye?

O "vasculaire rings" suguba damadɔ bɛ yen. An k’a lajɛ u ye mun ye:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

No comments yet. Be the first to share your thoughts here.

Add Your Comment

Please calculate: 8 + 8 =