Ðe Sickle Cell Dɔléle le ŋuwòa? Eyata ne akɔta le veve sem na wò la, mègafe fefe o! Esia ku ɖe Acute Chest Syndrome ŋu!

Ðe wò akɔta vena kpata eye gbɔgbɔ sesẽna na wò ɣeaɖewoɣia? Ne dzesi siawo le ŋuwò kpe ɖe kɔdzidɔ kple asrã ŋu, vevietɔ ne dɔléle aɖe si woyɔna be Sickle Cell Disease (SCD) , le ŋuwò la, mègabu eŋu nu tsɛe o. Dzesi siawo ate ŋu anye dɔléle aɖe si nu sẽ wu si woyɔna be Acute Chest Syndrome ƒe dzesi. Mègatsi dzi o, míaƒo nu tso esia ŋu le mɔ si me kɔ eye wòle bɔbɔe nu egbea.

Nukae Nye Akɔta ƒe Dɔléle Sesẽ? Kpuie ko la,...

Enyo, azɔ kpɔ ɖa. `Akɔta ƒe Dɔléle sesẽ` sia nye kuxi sesẽ aɖe si ate ŋu ado tso sickle cell dɔléle (`SCD`) gbɔ . Kpuie ko la, enye ne akɔta le veve sem, kɔdzi, dzoxɔxɔ, oxygen ƒe agbɔsɔsɔ si mede wò ʋu me o, eye nusiwo mesɔ o, vevietɔ tsi, dze ƒoƒo ɖe lãkusi me (`lung infiltrates`).

Nɔnɔme sia ate ŋu ava sesẽ kaba ŋutɔ . Le nyateƒe me la, `Akɔta ƒe Dɔléle Sesẽ` sia nye nu vevitɔ si hea kɔdziyiyi kple ku ɣeaɖewoɣi vɛ na amesiwo ŋu sickle cell dɔléle le . Eyata ele vevie ŋutɔ be míanya esia.

Fifia ɖewohĩ èle eŋu bum be nukae nye Sickle Cell Disease (SCD) hã. Mina míaɖo ŋku edzi na wò vie tso eŋu. Enye domenyiŋusẽfianu ƒe dɔléle . Ema fia be enye domenyinu. Ekpɔa ŋusẽ ɖe protein si le míaƒe ʋumenugbagbevi dzĩwo me si woyɔna be hemoglobin dzi . Togbɔ be ame si le lãmesẽ me ƒe ʋumenugbagbevi dzĩwo le goglo hã la, ame si ŋu SCD le ƒe ʋumenugbagbevi dzĩwo ƒe nɔnɔme le abe lãmenugbagbevi dzĩwo ene (abe ɣletivimefakaka ene). Eyata lãmenugbagbevi siawo siwo le abe aŋɔ ene mate ŋu ato míaƒe ʋuka tsɛawo me bɔbɔe o. Ekema, ʋumenugbagbevi dzĩ la mete ŋu tsɔa ɔksidzin yia ŋutilã bliboa me nyuie o. Esiae nye kuxi vevitɔ si le SCD ŋu.

Aleke gbegbee Acute Chest Syndrome bɔe?

Le nyateƒe me la, `Acute Chest Syndrome` nye nɔnɔme si bɔ ŋutɔ le amesiwo ŋu sickle cell dɔléle (`SCD`) le dome. Le akɔntabubuwo nu la, amesiwo ŋu `SCD` le ƒe afã lɔƒo akpɔ nɔnɔme sia zi ɖeka ya teti le woƒe agbe me . Togbɔ be edze abe ɖevi sue siwo xɔ tso ƒe 2 va ɖo ƒe 4 mee wòbɔ ɖo wu ene hã la , ate ŋu asẽ ɖe ame tsitsiwo dzi wu ɖeviwo . Wogakpɔe hã be amesiwo ŋu `SCD` kple asrã le la le afɔku gã aɖe me be woaxɔ `Acute Chest Syndrome` wu ame bubuwo.

Nukatae Acute Chest Syndrome dzɔna? Nukawoe gbɔ wòtsona?

Dzɔdzɔmeŋutinunyalawo mete ŋu gblɔ nusi tututu hea `Acute Chest Syndrome` vɛ kple kakaɖedzi haɖe o. Gake woxɔe se be ɖewohĩ nu ɖeka alo esi wu nenema gbɔe wòtso. Mina míalé ŋku ɖe nusiwo wonye ŋu:

• Ƒumeŋuɖui ƒe kuku:Ènya be ƒumeŋuɖui ye nye akpa falɛfalɛ si le abe ƒumelã ene le míaƒe ƒu gãwo mea? Ne ƒumeŋuɖui sia ku le mɔ aɖe nu (si woyɔna be `necrosis`), eƒe akpa suewo ateŋu agbã eye woage ɖe ʋukawo me eye woazɔ to ŋutilã bliboa me. Ne kakɛ siawo zɔ mɔ yi lãkusi me la, ateŋu ahe `Acute Chest Syndrome` vɛ.
• Ami ƒe ʋuʋu: Nu bubu si ate ŋu ana ƒumeŋuɖui ƒe dɔmawɔmawɔ nyuie si míeyɔ ɖe etame tsoe nye ami ƒe ʋuʋu. Kpuie ko la, esiae nye ne ami sue aɖe (bu eŋu be enye ami sue aɖe) ge ɖe ʋuka aɖe me eye wòxe mɔ na ʋu ƒe sisi . Esia ate ŋu ahe Acute Chest Syndrome hã vɛ.
• Dɔlékuiwo : Dɔlékui vovovowo, vevietɔ aklãdɔ si dɔlékuiwo alo dɔlékuiwo hena vɛ , ate ŋu ahe akɔta ƒe dɔléle sesẽ vɛ. Dɔlékuiwo koŋue hea nɔnɔme sia vɛ le ɖevi suewo ŋu . Gake le ame tsitsiwo gome la , anɔ eme be ami ƒe ʋuka me ʋu ƒe sisi gbɔe wòtsona wu.

Nukae nye amesi ŋu Acute Chest Syndrome le ƒe dzesiwo?

`Acute Chest Syndrome` ƒe dzesiwo ateŋu ato vovo tso ame ɖeka gbɔ yi bubu gbɔ. Vovototo aɖewo le wo dome, vevietɔ le ɖevi suewo kple ame tsitsiwo dome. Zi geɖe la, ɖevi suewo ɖea dɔlékui aɖe ƒe dzesi geɖe fiana:

• Kpe
• Asrã
• Oxygen ƒe agbɔsɔsɔ si dzi ɖe kpɔtɔ le ʋu me (hypoxemia) .
• Yagbɔgbɔ kabakaba si mesɔ o (tachypnea) .
• Wheezing (gbeɖiɖi si dona tso akɔta ne wole gbɔgbɔm) .

Ame tsitsiwo hã ate ŋu akpɔ dzesi siawo. Tsɔ kpe ɖe eŋu la, àte ŋu ade dzesii hã be:

• Akɔtave , vevietɔ ne wole gbɔgbɔm, ate ŋu adzi ɖe edzi.
• Vevesese sesẽ, kpata le abɔwo, afɔwo, kple akɔta si tso ʋu ƒe sisi ƒe xexe (si woyɔna hã be `vaso-occlusive crisis`) gbɔ.
• Lãmetsi ƒe ƒuƒoƒo ɖe lãkusi kple akɔta (pleural effusion).
• Yagbɔgbɔ sesẽ (gbɔgbɔtsixetsixe).

Ne dzesi siawo dometɔ ɖeka alo esi wu nenema le ŋuwò, vevietɔ ne SCD le ŋuwò la, ele vevie ŋutɔ be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo enumake .

Aleke wokpɔa Acute Chest Syndrome ƒe dɔlélea? (Dɔléle ƒe dzesi) .

`Acute Chest Syndrome` ƒe dzesidede kaba ateŋu axɔ ame ƒe agbe.Ne SCD le ŋuwò eye woxɔ wò ɖe kɔdzi la, ahiã be woalé ŋku ɖe ŋuwò edziedzi eye woado wò kpɔ siwo hiã. Dodokpɔ geɖe li siwo ate ŋu akpe ɖe ɖɔktawo ŋu woakpɔ kuxi sia:

• Ʋukawo me gas me dzodzro: Esia ate ŋu adzidze acid (pH), oxygen, kple carbon dioxide ƒe agbɔsɔsɔ si le wò ʋu me.
• Ʋudodokpɔ: Ʋu xexlẽ blibo ate ŋu ana nyatakaka ku ɖe wò ʋumenugbagbevi dzĩwo, ʋumenugbagbevi ɣiwo, kple ʋumenugbagbevi dzĩwo ŋu.
• Akɔta ƒe X-ray: Woate ŋu azã esia atsɔ akpɔe ɖa be dɔlékui siwo le lãkusi me alo nu mawo siwo mesɔ o (siwo gena ɖe lãme) siwo ŋu míeƒo nu tsoe va yi la ƒo ƒu hã.
• Dekɔnuwo: Dodokpɔ siawo kpena ɖe ame ŋu wòdea dzesi dɔlékui ƒomevi vovovowo to wò ʋu, ʋuʋudedi, alo ŋutilã me tsi bubuwo me dzodzro me.

Wò ɖɔkta ate ŋu anɔ te ɖe dodokpɔ siawo me tsonu kple wò dzesiwo dzi atsɔ Acute Chest Syndrome ade hatsotso si mesẽ o, esi mesẽ o, alo esi nu sẽ .

Nukawoe nye atike siwo wozãna na Acute Chest Syndrome?

Le nɔnɔme sia me la , atikewɔwɔ gɔmedzedze kabae nye mɔ nyuitɔ si dzi woato axe mɔ ɖe kuxi sesẽwo nu . Atikewɔwɔ ƒe tiatia aɖewoe nye:

• Ʋudodo: Esia bia be woaɖe wò ʋu ƒe ɖewo ɖa eye woana ʋu alo ʋu ƒe akpa aɖewo wò tso amesi do ʋu na wò gbɔ.
• Lãmetsi siwo wodona ɖe ʋuka me: Esia kpena ɖe ame ŋu be tsi megale lãme na ame o (tsi ƒe gege ɖe lãme), si ate ŋu ana sickle cell dɔlélea nagado gã ɖe edzi eye wòana vevesese nadzi ɖe edzi.
• Vevesesenutsitikewo: Woateŋu ana atikewo abe `ketorolac` alo `opioids` be woatsɔ aɖu vevesese dzi.
• Spirometer si Dea Dzi ƒo na ame: Mɔ̃ sue sia kpena ɖe ŋuwò nègbɔa ya sesĩe. Ekpena ɖe ŋuwò be wò lãkusiwo nɔa dzadzɛ eye wowɔa dɔ nyuie.
• Oxygen-dɔdamɔnu kpeɖeŋutɔ: Ne oxygen ƒe agbɔsɔsɔ si le ʋua me mesɔ gbɔ o la, wonaa oxygen.
• Dɔlékuiwutikewo: Ne dɔlékui aɖe gbɔe nɔnɔme sia tso la, wona dɔlékuiwutikewo.
• Dɔlékuiwutikewo: Ne dɔlékui ƒe dɔléle gbɔe wòtso la, wonaa dɔlékuiwutike siwo sɔ.

Ðe woate ŋu aɖe afɔku si le Acute Chest Syndrome xɔxɔ me dzi akpɔtɔa?

Ne sickle cell disease (SCD) le ŋuwò la, ele vevie be nàƒo nu kple wò atikewɔlawo tso mɔ siwo dzi nàto axe mɔ ɖe Acute Chest Syndrome nu ŋu. Woate ŋu aɖo aɖaŋu na amewo abe:

• Yaƒoƒo ɖe aŋetu me edziedzi: Togbɔ be adze nu bɔbɔe aɖe hã la, esia kpena ɖe ŋuwò be wò yaƒoƒomɔ̃wo me kɔna eye wòɖea tsi si mehiã o ƒe ƒoƒo ɖe wò lãkusiwo ŋu dzi kpɔtɔna.
• Kamedede edziedzi: Esia ate ŋu ana wò lãkusi ƒe ŋusẽ nadzi ɖe edzi.
• Ʋudodo edziedzi: Ðewohĩ esia ahiã ame aɖewo.
• Atikewo abe `Hydroxyurea` alo `L-glutamine` nono: Atike siawo ateŋu akpeɖeŋu be woaɖe vevesese dzi akpɔtɔ eye woaɖe afɔku si le kɔdziyiyi enuenu me dzi akpɔtɔ. Gake atikewɔlawo ƒe aɖaŋuɖoɖo te koe wòle be woaxɔ esiawo.

Nukae nye mɔkpɔkpɔ (haya) na amesi ŋu dɔléle sia le?

Ele vevie be woadi atikewɔwɔ enumake ne `Acute Chest Syndrome` dzɔ. Ne womewɔe o la, ate ŋu ahe kuxi sesẽwo abe:

• Acute Respiratory Distress Syndrome (ARDS): Esia nye lãkusidɔ sesẽ aɖe si ate ŋu ade ame ƒe agbe afɔku me.
• Susu ƒe nɔnɔme si trɔ.
• Ayiku ƒe abixɔxɔ.
• Aklã ƒe dɔmawɔmawɔ nyuie.
• Ŋutinu geɖe ƒe dɔmawɔmawɔ nyuie.
• Yagbɔgbɔ ƒe dɔmawɔmawɔ nyuie keŋkeŋ.
• Vevesese sesẽ ŋutɔ.
• Nublanuitɔe la, ku gɔ̃ hã ate ŋu adzɔ.

Le akɔntabubuwo nu la, ame tsitsiwo ƒe ku le `Acute Chest Syndrome` ta anɔ abe 4% ene . Le ɖeviwo dome la, xexlẽme sia anɔ abe 1% ene . Esia fia be woate ŋu axɔ ame geɖe ɖe agbe ne wowɔ atike na wo kaba.

Azɔ hã, ɖo ŋku edzi be ne woda `Acute Chest Syndrome` dzidzedzetɔe eye wodae hã la, amesi ŋu `SCD` le ate ŋu agakpɔ nɔnɔme sia ake le etsɔme .

Sickle cell dɔléle le ŋunye. Nukae wòle be mawɔ ne Acute Chest Syndrome ƒe dzesiwo dze dzinye?

Esiae nye nu vevitɔ kekeake. Ne SCD le ŋuwò eye nèdze Acute Chest Syndrome (akɔtave, gbɔgbɔtsixetsixe, kɔdzidɔ, dzoxɔxɔ) ƒe dzesi aɖe kpɔkpɔ gɔme la, mègahe ɖe megbe aɖabaƒoƒo ɖeka pɛ hã o eye nàdi atikewɔlawo ƒe aɖaŋuɖoɖo enumake .

• Gblɔ na ɖɔktawo be sickle cell dɔléle le ŋuwò ne èyi xɔ si me wowɔa dɔ kpata le alo atikewɔƒe bubu.
• Bia be woawɔ akɔta ƒe X-ray enumake . Esia ate ŋu aɖo kpe edzi kaba nenye be Acute Chest Syndrome le ŋuwò eye wòadze atikewɔwɔ gɔme kaba.

Ðo ŋku edzi be nuwɔwɔ kabakaba le ɣeyiɣi sia tɔgbe me ate ŋu awɔ akpa gã aɖe le wò agbe ɖeɖe me.

Gbedasi si Wotsɔ Yi Aƒeme

Mienya azɔ be `Acute Chest Syndrome`, si ŋu míeƒo nu tsoe la nye kuxi sesẽ aɖe si ate ŋu ado tso sickle cell dɔléle me. Dzesi vevitɔwoe nye akɔtave, gbɔgbɔtsixetsixe, kɔdzidɔ, kple dzoxɔxɔ . Ne sickle cell dɔléle le ŋuwò la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake ne èkpɔ dzesi siawo dometɔ aɖe.. Mègaŋlɔ be be yeana yeƒe ɖɔktawo nanya be sickle cell dɔléle le ye ŋu o. Dɔlélea didi kaba kple edada kaba nye mɔ nyuitɔ siwo dzi nàto akpɔ ɖokuiwò ta tso nɔnɔme sia me. Nɔ lãmesẽ me! Akɔta ƒe Dɔléle Sesẽ, Sickle Cell Dɔléle, Akɔtave, Gbɔgbɔtsixe, Akɔta ƒe Dɔléle Sesẽ, Sickle Cell Dɔléle, Aklãdɔléle