Anɔ eme be èse "ʋusɔgbɔdɔ" alo "ʋusɔgbɔdɔ" ŋkɔ kpɔ alo? Kpuie ko la, ne míaƒe ŋutilã mewɔ ʋumenugbagbevi dzĩwo wòsɔ gbɔ o alo ʋumenugbagbevi dzĩ siwo le mía si la mewɔa dɔ nyuie o ye. Ʋumenugbagbevi dzĩwo koŋue tsɔa oxygen yia míaƒe ŋutilã katã me. Eyata ne woɖiɖi la, míate ŋu ase le mía ɖokui me be ɖeɖi te mía ŋu eye míegbɔdzɔ ɣesiaɣi. Ʋumenugbagbevi dzĩ siawo dzɔna le ƒumeŋuɖui, si nye lãkusi falɛfalɛ si le abe ƒumelã ene le míaƒe ƒuwo me la me. Diamond-Blackfan Anemia (DBA) nye ʋusɔgbɔdɔ ƒomevi tɔxɛ aɖe si dzɔna ne ƒumeŋuɖui mete ŋu wɔa ʋumenugbagbevi dzĩ siwo sɔ o.
Nukae hea Diamond-Blackfan Anemia (DBA) vɛ?
Diamond-Blackfan Ʋusɔgbɔdɔ, si woyɔna ɣeaɖewoɣi be ``acquired pure red cell aplasia'', zi geɖe la, ɖɔktawo kpɔnɛ hafi ɖevi xɔ ƒe ɖeka. Nusi koŋ gbɔ esia tsonae nye tɔtrɔ, alo tɔtrɔ, le domenyiŋusẽfianu siwo nye míaƒe ŋutilã ƒe xɔtunuwo me.
Ðo ŋku edzi be ɣeaɖewoɣi la, woate ŋu anyi domenyiŋusẽfianu ƒe gbɔdzɔgbɔdzɔ sia ƒe dome tso vidadaa alo fofoa gbɔ. Gake menye nenemae wònɔna ɣesiaɣi o. Ðevi aɖewo ƒe domenyiŋusẽfianu hã te ŋu trɔna le wo ɖokui si le susu aɖeke manɔmee. Nɔnɔme sia le ɖevi siwo ŋu DBA le ƒe akpa gãtɔ ŋu le domenyiŋusẽfianu ƒe tɔtrɔ yeye aɖe ta. Eya ta abe dzilawo ene la, mehiã be míatsi dzi ɖe esia ŋu madzemadzee o. Togbɔ be wokpɔ domenyiŋusẽfianu aɖe koŋ si gbɔ DBA dɔnɔwo ƒe afã kloe tso hã la, le ame aɖewo gome la, womekpɔ nusi koŋ gbɔ nɔnɔme sia tsona haɖe o.
Nukae nye DBA ƒe dzesiwo?
Ðevi siwo ŋu DBA le hã ate ŋu akpɔ ʋusɔgbɔdɔ ƒomevi bubuwo ƒe dzesi geɖe siwo bɔ. Ema nye,
- Ðeɖiteameŋu ɣesiaɣi
- Ŋutilã si ƒe ŋutigbalẽ le ɣie
- Sese le eɖokui me be yegbɔdzɔ
Tsɔ kpe ɖe nɔnɔme siawo siwo bɔ ŋu la, gotagome nɔnɔme tɔxɛ aɖewo ate ŋu anɔ ɖevi aɖewo siwo wodzi kple DBA ŋu le woƒe mo kple ŋutilã ŋu. Na míalé ŋku ɖe nusiwo wonye ŋu.
| Ŋutilã ƒe akpa aɖe | Nusiwo woate ŋu akpɔ |
|---|---|
| Ta | Ta si le sue wu esi sɔ ƒe amesinɔnɔ. |
| Mo | Ŋkuawo kple ŋɔti gbadzaa dome didime si dzi ɖe edzi. |
| Towo | To sue eve siwo woɖo ɖe anyi wu alesi wòle dzɔdzɔmee. |
| Glã | Aɖu sue si le ete ƒe amesinɔnɔ. |
| Kɔ | Kɔ kpui aɖe si ŋu lãgbalẽ le. |
| Abɔtawo | Abɔtaɖonu suewo. |
| Asiwo | Asibidɛ siwo ƒe nɔnɔme mebɔ o. |
| Nu | Aɖu alo nuyi si me ʋuʋu le. |
Tsɔ kpe ɖe eŋu la, DBA ate ŋu ahe ayiku me kuxiwo , dzidɔ , kple ŋku ƒe kuxiwo abe ŋkudɔ kple ŋkudɔ ene vɛ. Ŋutsuviwo hã ate ŋu axɔ vidzidzi ƒe gbɔdzɔgbɔdzɔ si woyɔna be hypospadias, si nye ɣeyiɣi si me aɖuɖɔtoe ƒe ʋuʋu mele ŋutsu ƒe vidzinu ƒe nugbɔ o.
Aleke woawɔ ade dzesi dɔléle sia pɛpɛpɛ?
Wò ɖɔkta ate ŋu awɔ dodokpɔ geɖe atsɔ anya ne DBA le viwòa ŋu. Ðevi siwo ŋu DBA le ƒe ʋumenugbagbevi dzĩwo mesɔ gbɔ o, gake ʋumenugbagbevi ɣiwo kple ʋumenugbagbevi dzĩwo ƒe xexlẽme sɔ.
Nu vevitɔe nye be mègatsi dzodzodzoe ne èkpɔ dzesi siawo o, ke boŋ be nàyi ɖɔkta bibi gbɔ kaba ale si nàte ŋui. Awɔ dodokpɔ siwo hiã eye wòana nyatakaka siwo de pɛpɛpɛ wu la wò.
Esiawo nye dodokpɔ vevi siwo ɖɔktaa wɔna la dometɔ aɖewo.
| Dodokpɔ | Nukae wòdia? |
|---|---|
| Ʋu Xexlẽme Blibo (CBC) . | Wodzidzea nu geɖe le ʋua me, abe ʋumenugbagbevi dzĩwo ƒe xexlẽme, ʋumenugbagbevi ɣiwo, ʋumenugbagbevi dzĩwo, protein si tsɔa oxygen hemoglobin, kple ʋumenugbagbevi dzĩwo ƒe agbɔsɔsɔ (hematocrit) . |
| Reticulocyte ƒe xexlẽme | Esia dzidzea ʋumenugbagbevi dzĩ siwo metsi o, alo esiwo do yeye, ƒe xexlẽme. Esia ate ŋu anya ne ƒumeŋuɖui le lãmenugbagbevi dzĩwo wɔm nyuie. |
| eADA ƒe agbɔsɔsɔ me toto | Amesiwo ŋu DBA le ƒe 80% lɔƒo ƒe enzyme aɖe si woyɔna be erythrocyte adenosine deaminase (eADA) ƒe agbɔsɔsɔ dzi ɖe edzi . Esiae nye nusi dim dodokpɔ sia le. |
| Fugboe ƒe ʋumenugbagbeviɣi ƒe agbɔsɔsɔ | Esiae nye ʋumenugbagbevi dzĩ si ƒomevi le vidzĩwo ƒe vidzidɔ me. Ele be wòaɖiɖi le vidzidzi megbe. Gake ɖevi siwo ŋu DBA le ate ŋu asɔ gbɔ kokoko ne wole tsitsim. |
| Ƒumeŋuɖui ƒe ʋuʋu kple ƒumeŋuɖui ɖeɖeɖa | Wozãa aŋe ɖea lãmenugbagbeviwo kple tsi sue aɖe tso ƒumeŋuɖui me hedoa wo kpɔna. Ʋumenugbagbevi dzĩ siwo le lãmesẽ me ʋɛ aɖewo koe le ɖevi siwo ŋu DBA le ƒe ƒumeŋuɖui me. |
| Domenyiŋusẽfianu dodokpɔwo | Esia doa domenyiŋusẽfianu siwo do ƒome kple DBA alo ʋusɔgbɔdɔ bubu siwo ƒe dome wonyi tso dzilawo gbɔ la kpɔna. |
Kuxi bubu kawoe ate ŋu ado mo ɖa le DBA ta?
Amesiwo ŋu DBA le la le afɔku me vie be woaxɔ dɔléle kple nɔnɔme aɖewo. Esiawo dometɔ aɖewoe nye ʋu kple ƒumeŋuɖui me kansa (acute myeloid leukemia), ƒumeŋuɖui (osteosarcoma), kple dɔléle bubu siwo me ƒumeŋuɖui mate ŋu awɔ ʋumenugbagbevi siwo le lãmesẽ me o (myelodysplastic syndrome). Gake mègatsi dzi ɖe esia ŋu o. Ðɔktawo le ŋku lém ɖe esia ŋu ɣesiaɣi, eyata àte ŋu awɔ atikewɔwɔ ƒe afɔɖeɖe siwo hiã le ɣeyiɣi nyuitɔ dzi.
Nukawoe nye atike siwo wozãna na esia?
Esiae nye akpa si le vevie wu eye wòfaa akɔ na ame wu. Ðevi siwo ŋu wokpɔ DBA le ate ŋu anɔ agbe didi, akpɔ dzidzedze ne wozã atike na wo. Ðevi aɖewo yia tsɔtsɔke keŋkeŋ me, si fia be dzesiawo nu yina hena ɣeyiɣi aɖe.
Dɔdamɔnu vevi eve siwo wozãnae nye corticosteroid-tikewo kple ʋudodo.
- Corticosteroid atikewo: Atikewo abe `(Prednisone)` doa ŋusẽ ƒumeŋuɖui eye wokpena ɖe eŋu wòwɔa ʋumenugbagbevi dzĩ geɖe.
- Ʋudodo: Esia nye tiatia nyui aɖe ne steroid-tikewo mewɔa dɔ o, alo ne ʋusɔgbɔdɔa nu sẽ. Esia bia be woana ʋu alo ʋumenugbagbevi dzĩwo tso ame si le lãmesẽ me gbɔ na ɖevia.
- Ƒumeŋuɖui/lãmenugbagbeviwo dodo na ame: Esia koe nye atike si daa DBA. Gake afɔku le eme vie. Azɔ hã, nunala si sɔ kplii didi ate ŋu asesẽ ɣeaɖewoɣi.
Ele vevie be nàdzro atikewɔwɔmɔnu siawo katã, woƒe nyonyo kple kuxiwo me kple wò ɖɔkta eme nakɔ ŋutɔ, eye nàtia nusi nyo na viwòa.
Gbedasi si Wotsɔ Yi Aƒeme
- Diamond-Blackfan Anemia (DBA) nye domenyiŋusẽfianu ƒe dɔléle si mebɔ o le ɖeviwo me si me ƒumeŋuɖui mete ŋu wɔa ʋumenugbagbevi dzĩ siwo sɔ o.
- Tsɔ kpe ɖe dzesi siwo bɔ abe ɖeɖiteameŋu enuenu kple ŋutigbalẽ ƒe amadede dzẽ ene ŋu la, dɔléle sia ate ŋu ahe gotagome nɔnɔme aɖewo koŋ hã vɛ le mo kple ŋutilã ŋu.
- Ðɔkta ate ŋu ade dzesi dɔléle sia pɛpɛpɛ to ʋudodokpɔ kple ƒumeŋuɖui dodokpɔ me.
- Atikewɔwɔ abe steroid-tikewo kple ʋudodo ene ate ŋu akpe ɖe ɖeviwo ŋu woanɔ agbe didi eye woanɔ lãmesẽ me. Ƒumeŋuɖui dodo na ame koe nye atike si woatsɔ adae.
- Ne ɖikeke suetɔ kekeake gɔ̃ hã le mewò be dzesi siawo le viwòa ŋu la, mègatsi dzodzodzoe eye nàyi ɖeviwo ƒe dɔdala gbɔ enumake o. Dɔlélea didi kabakaba kple edada le vevie ŋutɔ.
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