He pilikia paha kāu me kou enamel niho? E kamaʻilio kākou e pili ana i (Amelogenesis Imperfecta)!

Ua noʻonoʻo paha ʻoe no ke aha i loli ai ke kala o kou mau niho, a i ʻole e maʻalahi ka haki ʻana a i ʻole ka haki ʻana? I kekahi manawa, ʻoiai inā ʻaʻole ʻoe i ʻike i ke kumu, he pilikia paha ia me ka enamel ma kou mau niho. ʻO ia ka mea a mākou e kamaʻilio ai i kēia lā. He mea paʻakikī iki ia, akā e ho'āʻo kākou e wehewehe maʻalahi.

He aha ka (Amelogenesis Imperfecta)? E ʻike kākou maʻalahi!

I ka ʻōlelo maʻalahi, ʻo (Amelogenesis Imperfecta) kahi maʻi genetic . ʻO ka mea e hana ʻia ma kēia, ʻo ka uhi paʻa pale ma luna o kou mau niho, i kapa ʻia ʻo enamel, ʻaʻole ia e ulu pono. E noʻonoʻo e pili ana, ʻo kēia enamel ka mea e pale ai i nā ʻāpana palupalu i loko o ko kākou mau niho. Ke loaʻa iā ʻoe (Amelogenesis Imperfecta), ʻaʻole lawa ka nui o ka enamel i hana ʻia, a i ʻole ʻaʻole lawa ka ikaika o ka enamel i hana ʻia. Hiki i kēia ke hoʻololi i ke kala o kou mau niho a nāwaliwali . I ka pololei, ʻo kēia enamel ka ʻāpana o ka niho e hana ana e like me ka pale pale. No laila, i ka wā e loaʻa ai kahi pilikia me ia, he hopena nui ia i ka niho.

Hiki i kēia kūlana ke hoʻohilahila iā ʻoe e pili ana i kou minoʻaka a makaʻu hoʻi e hele i ke kauka inā loaʻa iā ʻoe kahi ulia liʻiliʻi me kou mau niho. He mea maʻamau loa ia. Akā me ke ahonui a me ka manawa, aia nā lāʻau lapaʻau e hiki ai ke hoʻoikaika i kou mau niho a hoʻomaikaʻi i ko lākou helehelena. Mai hoʻokuʻu i ka manaʻolana!

He aha nā ʻano nui o (Amelogenesis Imperfecta)?

ʻEhā ʻano nui o kēia maʻi. E nānā kākou i ko lākou ʻano, me nā kikoʻī hou aku:

• ʻAno 1 — Hypoplastic: He kūlana kēia i kapa ʻia ʻo enamel hypoplasia . ʻO ke ʻano kēia, ʻaʻole lawa ka enamel i hana ʻia. Hiki i ka enamel āu ke lilo i lahilahi, e like me ke aniani lahilahi. Hiki i kēia ke hana i kou mau niho e liʻiliʻi ma mua o ka maʻamau, me nā ʻili ʻino a me nā lua paha.

• ʻAno 2 — Hypomaturation: Hana ʻia kēia ʻano ke ulu pono ʻole nā ​​protein e kōkua ana i kou enamel e ulu. E noʻonoʻo e like me ka wā e hoʻōla pono ʻole ai ka sima i ke kūkulu ʻana i hale. ʻOiai ua kokoke kou enamel i ka mānoanoa maʻamau, hiki ke palupalu loa a haki maʻalahi . E like me kahi ʻāpana pōhaku lepo.

• ʻAno 3 — Hypocalcified: Loaʻa kēia ʻano ke hana ʻole kou enamel i ka calcium lawa e hoʻoikaika ai, a paʻakikī paha. He maʻamau paha ka mānoanoa o ka enamel, akā hiki ke haki a mae wale. Hiki iā ia ke haki me ka liʻiliʻi loa o ke kaomi, e like me ka biscuit.

• ʻAno 4 — Hypomaturation/hypoplasia/taurodontism: Ma kēia ʻano, ʻike paha ʻoe i nā pilikia me kou enamel niho i maʻamau i nā ʻano 1 a me 2. ʻO ke ʻano kēia e lilo paha ka enamel i lahilahi a palupalu. Eia kekahi, taurodontismHiki ke pili pū kēia i kahi kūlana i kapa ʻia ʻo "protrusion of the auwae." ʻO kēia ka wā e nui loa ai ke kino o kou niho a pōkole loa nā aʻa. Hiki i kēia lakio ʻokoʻa o nā niho ke hoʻolilo iā ia i mea paʻakikī iki no nā kauka ke koho i nā koho lapaʻau.

Pehea ka maʻamau o kēia ʻano?

He maʻi laha ʻole ka (Amelogenesis Imperfecta). No ka laʻana, ma ʻAmelika Hui Pū ʻIa, hoʻokahi wale nō i loko o 14,000 poʻe e hoʻopilikia ai. ʻAʻole ia he mea maʻamau loa ma Sri Lanka. No laila, ʻaʻole paha ʻoe i maʻa i ka lohe ʻana e pili ana i ia mea.

He aha nā hōʻailona o (Amelogenesis Imperfecta)?

Inā loaʻa iā ʻoe ʻo Amelogenesis Imperfecta, e ʻike paha ʻoe i kēia mau hōʻailona ma kou mau niho. E nānā inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau mea:

• ʻOle ke kala: Hiki i nā niho ke lilo i opaque, keʻokeʻo ʻōkaʻakai, hina, melemele, a ʻeleʻele paha. I kekahi manawa, aia paha he mau kiko a i ʻole ka loli ʻana o ke kala.
• Liʻiliʻi loa: Hiki i kēia ke hana i nā hakahaka ma waena o kou mau niho.
• He ʻāʻī, he lua, a he ʻōpuʻu paha ka ʻili. Hiki ke ʻike ʻia kēia ʻāʻī ke hoʻopā ʻia.
• Pālahalaha a maʻalahi ka haki a me ke komo ʻana. ʻOiai inā ʻoe e nahu i kahi mea liʻiliʻi, hiki i kahi ʻāpana o ka niho ke hemo.
• ʻO ka maʻalahi i nā mea wela a me ke anu. E manaʻo paha ʻoe e mae kou mau niho ke ʻai ʻoe i ka ice cream a inu paha i ke kī wela.
• Kuhihewa: Loaʻa paha iā ʻoe kahi nahu hāmama, kahi i hui ʻole ai kou mau niho o luna a me lalo ke pani ʻoe i kou waha. ʻO ke ʻano kēia aia kahi hakahaka ma waena o kou mau niho mua ʻoiai ke pani ʻia kou waha.

He aha nā kumu o (Amelogenesis Imperfecta)?

Hana ʻia ka Amelogenesis Imperfecta i ka wā e loaʻa ai kahi mutation , a i ʻole ka loli, i hoʻokahi a ʻoi aku paha o nā genes e kāohi ana i ka ulu ʻana o kou enamel niho. Hiki i kēia mau loli genetic ke hana i nā pilikia me ka ulu ʻana o kou mau niho pēpē a me kou mau niho makua. Hoʻoilina ka hapa nui o ka poʻe i kēia mutation mai kekahi a i ʻole nā ​​mākua ʻelua.

He hana paʻakikī loa ke kūkulu ʻia ʻana o ka enamel. Hoʻopili ʻia e kekahi mau genes. ʻOi aku ka nui, aia nā genes e kāohi ana i ke ʻano o ka hui pū ʻana o nā protein a me nā minelala e hana i ka enamel. Inā he pilikia liʻiliʻi me kēia mau genes, hiki ke hana ʻia ka amelogenesis imperfecta. ʻO kekahi o nā mutations maʻamau i ka amelogenesis imperfecta e pili ana i kēia mau genes:

• `(FAM83H)`
• `(ENAM)`
• `(MMP20)`
• `(AMELX)`

He mea paʻakikī iki kēia mau inoa, akā eia kekahi o nā inoa gene a nā kauka e hoʻohana ai i ke kamaʻilio ʻana e pili ana i kēia kūlana.

Pehea e hoʻoili ʻia ai kēia mai kēlā hanauna a i kēia hanauna?

ʻOiai hiki ke hana koke ʻia nā hoʻololi genetic, ʻo ia hoʻi me ke kumu ʻole, hoʻoilina ka hapa nui o ka poʻe me Amelogenesis Imperfecta i ke kūlana. Ma muli o ke ʻano o Amelogenesis Imperfecta, hiki ke like ke ʻano hoʻoilina penei:

• Autosomal dominant: I kēia hihia, pono ʻoe e hoʻoilina i kahi gene mutated mai kekahi o kou mau mākua e hoʻomohala iā Amelogenesis Imperfecta. ʻO ke ʻano kēia inā loaʻa i ka makuahine a i ʻole ka makuakāne ka gene, hiki i ke keiki ke loaʻa. Penei ka hoʻoilina ʻana o ka hapa nui o nā ʻano Amelogenesis Imperfecta.
• Autosomal recessive: I kēia hihia, pono ʻoe e hoʻoilina i kahi gene mutated mai nā mākua ʻelua e hoʻomohala iā Amelogenesis Imperfecta. E ulu wale nō ke kūlana inā hoʻoilina nā mākua ʻelua i ka gene.
• Hoʻopili ʻia me ka X: I kēia hihia, ua hoʻoilina ʻia ka mutation ma o ka chromosome X , ʻaʻole ma o ka chromosome Y. E like me kou ʻike, ʻelua mau chromosome X (XX) ko nā wahine, a hoʻokahi X a me hoʻokahi chromosome Y (XY) ko nā kāne. ʻO nā keikikāne me ka X-linked (Amelogenesis Imperfecta) e loaʻa pinepine ana i nā pilikia a me nā hōʻailona ma mua o nā kaikamahine.

He aha nā pilikia e hiki mai ana mai ka Amelogenesis Imperfecta?

ʻO nā pilikia me ka enamel niho e hōʻike ana i nā ʻiʻo koʻikoʻi ma lalo, i kapa ʻia ʻo dentine , a hoʻonui i ka pilikia o nā pilikia niho. (Amelogenesis Imperfecta) hoʻonui i ka pilikia o:

• Nā lua a pala niho paha. Ma muli o ka nāwaliwali o ka enamel, hiki i nā germs ke komo maʻalahi.
• Ka ʻino ʻana o nā niho.
• Maʻi ʻāʻī. Hiki ke loaʻa nā maʻi ʻāʻī no ka mea he paʻakikī ke hoʻomaʻemaʻe pono i kou mau niho.
• ʻEha niho.
• Hopohopo: Hilahila paha ʻoe a hopohopo hoʻi no ke ʻano o kou mau niho. Makaʻu paha ʻoe e minoʻaka i ka lehulehu.

Pehea e ʻike ai i ke ʻano o ka Amelogenesis Imperfecta (Amelogenesis Imperfecta)?

Hiki i ke kauka niho ke ʻike i ka amelogenesis imperfecta i ka wā o ka hoʻokolokolo niho. Hiki i ke kauka ke loaʻa kahi manaʻo o ke kūlana ma ka nānā ʻana i ke ʻano, ke kala, a me ke ʻano o kou mau niho. ʻOiai ke holo nei kēia kūlana i loko o nā ʻohana, hiki iā ia ke nīnau e pili ana i kou mōʻaukala ʻohana o nā pilikia niho, e like me ka loaʻa ʻana o kou makuahine, makuakāne, a i ʻole nā ​​​​hoahānau i nā pilikia like.

Pono paha ʻoe a i ʻole kāu keiki e hana i kahi X-ray niho . E ʻae kēia i ke kauka e aʻo hou aʻe e pili ana i ke ʻano o nā niho o kāu a i ʻole kāu keiki, no ka laʻana, pehea ka lahilahi o ka enamel a me ke ʻano o ke aʻa o ka niho.

I kekahi manawa, hiki i ka hoʻāʻo ʻana i ka genetic ke hōʻoia i ka mutation kikoʻī a me ke ʻano o ka maʻi. Hiki i kēia ke kōkua i ka hoʻolālā ʻana i ka lāʻau lapaʻau.

Pehea e mālama ʻia ai ʻo Amelogenesis Imperfecta?

Ma muli o ke kūlana o kou mau niho a inā he mau niho pēpē a he mau niho paʻa paha, hiki i kāu kauka niho ke ʻōlelo aku i kekahi mau lāʻau lapaʻau. Pono ka nui o ka poʻe me Amelogenesis Imperfecta i ka hui pū ʻana o nā lāʻau lapaʻau e pale a hoʻomaikaʻi i ke ʻano o ko lākou mau niho. Hiki i kēia ke lilo i kaʻina hana lōʻihi.

ʻO nā lāʻau lapaʻau:

• Nā lāʻau lapaʻau hoʻihoʻi: Hoʻoponopono kēia mau lāʻau lapaʻau i nā niho i hōʻino ʻia. No ka laʻana, pono paha ʻoe i hoʻokahi a ʻoi aku paha mau lei niho e uhi a pale i kou mau niho. Ua like kēia me kahi pāpale e kau ana ma luna o kou mau niho. I kekahi mau hihia, inā ua hōʻino nui ʻia kou mau niho, ʻo nā koho hoʻololi niho piha e like me nā implants ( he niho prosthetic) a me nā dentures (kahi hoʻonohonoho o nā niho artificial) nā koho maikaʻi loa.
• Nā lāʻau hoʻonani: Hoʻomaikaʻi kēia mau lāʻau i kou helehelena. No ka laʻana, inā ua ʻeleʻele kou mau niho, ua māwae, a ua ʻaʻahu ʻia paha ma muli o ka amelogenesis imperfecta, hiki i ka hoʻopaʻa ʻana i nā niho ( ke kūkulu hou ʻana i ka niho me kahi mea kala niho) a me nā veneers (nā uhi lahilahi i hoʻopili ʻia i mua o ka niho) ke kōkua. Ma waho aʻe o ke kōkua ʻana i ka hoʻopaʻa ʻana i ka niho, hoʻomaikaʻi pū nā lei aliʻi i ke ʻano o ka niho. Hiki i nā lāʻau hoʻokeʻokeʻo ke kōkua me nā niho mottled.
• Nā lāʻau lapaʻau Orthodontic: Inā he mau niho kekee kou ma muli o Amelogenesis Imperfecta, a inā he pilikia nahu kou, pono paha ʻoe e komo i nā mea hana niho e like me nā braces a i ʻole nā ​​aligners .

ʻO ka mea nui loa, ʻo ke kamaʻilio ʻana me kāu kauka niho a hoʻomohala i kahi hoʻolālā lapaʻau e kūpono iā ʻoe.

He aha kāu e manaʻo ai inā loaʻa iā ʻoe (Amelogenesis Imperfecta)?

ʻO ka loaʻa ʻana o Amelogenesis Imperfecta (a i ʻole ka loaʻa ʻana o kahi keiki me ke ʻano) hiki ke hoʻonāukiuki a hoʻonāukiuki. ʻOiaʻiʻo nō. ʻO nā pilikia me ka enamel niho e hoʻonui i kou pilikia o kekahi mau pilikia niho. Pono paha ʻoe e hana i kekahi mau lāʻau lapaʻau i ka hala ʻana o ka manawa. Hiki ke hala nā makahiki e hoʻopau ai i ka lāʻau lapaʻau piha.

E nīnau i kāu kauka niho i nā lāʻau lapaʻau maikaʻi loa no kou mau niho. E nīnau pū e pili ana i ka papa hana lapaʻau, no ka mea, hiki ke ʻokoʻa mai kēlā kanaka a kēia kanaka. Ma kēlā ala hiki iā ʻoe ke ʻike i ke ʻano o ka hoʻomaikaʻi ʻana āu e manaʻo ai a me ka wā e hiki mai ai. ʻO ke ahonui ke kī ma ʻaneʻi.

Pehea lā e hiki ai iaʻu ke mālama iaʻu iho? A i ʻole pehea lā e hiki ai iaʻu ke mālama i kaʻu keiki?

Inā loaʻa iā ʻoe ʻo Amelogenesis Imperfecta, pono ʻoe e mālama pono e pale i kou mau niho. ʻO kēia kekahi:

• Ka hoʻomaʻemaʻe pinepine ʻana i kou mau niho:Mai poina i ka ʻike ʻana i kāu kauka niho no ka nānā ʻana ma ka liʻiliʻi ʻelua i ka makahiki, a pono paha ʻoe e hele pinepine aku.
• E mālama i nā ʻano hoʻomaʻemaʻe waha maikaʻi: Pono ʻoe e palaki i kou mau niho ʻelua i ka lā, e hoʻohana i ka floss i kēlā me kēia lā, a hoʻohana i ka toothpaste desensitizing a me ka wai mehana e pale aku ai i ka ʻike ʻana o nā niho .
• E ʻai i nā meaʻai maikaʻi no kou mau niho: ʻO nā meaʻai waiwai i nā wikamina A a me D (e like me ke kāloti, ka pata, a me ka ʻaila iʻa) he mea maikaʻi ia no kou enamel niho. ʻO nā meaʻai waiwai i ka calcium (e like me ka waiū, ka yogurt, ka tīhi, a me nā iʻa liʻiliʻi me nā pūpū) he mau koho maikaʻi nō hoʻi.
• E pale i nā meaʻai a me nā mea inu e hiki ke hōʻino i kou mau niho: E ho'āʻo e pale i nā meaʻai a i ʻole nā ​​mea inu i kiʻekiʻe i ke kō a i ʻole ka waikawa (toffee, kokoleka, nā mea inu palupalu). Eia kekahi, e kaupalena i kāu ʻai ʻana i nā meaʻai paʻakikī loa a paʻakikī ke nau (candy, hau hau). He manaʻo maikaʻi nō hoʻi e noho mamao mai nā meaʻai pipili e like me ka caramel.
• E lawe i nā lāʻau ʻeha inā pono: Inā ʻeha kou niho, e hoʻonohonoho i kahi manawa e ʻike ai i kāu kauka niho. I kēia manawa, hiki iā ʻoe ke lawe i nā lāʻau ʻeha ma luna o ke kauka e like me ka acetaminophen (a i ʻole paracetamol) a me ibuprofen . Akā, mai lawe i kēia mau lāʻau ʻeha no nā lā he 10 a ʻoi aku i ka manawa me ka ʻole o ke kamaʻilio ʻana me kāu kauka a mea mālama ola paha.

Āhea wau e ʻike ai i ke kauka?

Inā ʻike ʻoe i nā hōʻailona o kahi maʻi i kapa ʻia ʻo Amelogenesis Imperfecta, e like me ke kala ʻole, nāwaliwali, a haki maʻalahi paha o nā niho, e ʻike koke i kahi kauka niho. Hiki i ka lāʻau lapaʻau ke pale, hoʻihoʻi, a hoʻomaikaʻi i ke ʻano o kou mau niho - akā i ka wā e nalowale ai ka enamel, ʻaʻole hiki ke kūkulu hou ʻia. No laila, ʻo ka wikiwiki o kou loaʻa ʻana o ka lāʻau lapaʻau, ʻoi aku ka maikaʻi o kou manawa e mālama ai i kou mau niho i ke olakino.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

He mea nui e kamaʻilio me kāu kauka e pili ana i kēia maʻi. Eia kekahi mau nīnau hiki iā ʻoe ke nīnau:

• He aha ke ʻano o ka Amelogenesis Imperfecta aʻu (a i ʻole kaʻu keiki) e loaʻa nei?
• He aha ke ʻano o ka lāʻau lapaʻau e pono ai iaʻu (a i ʻole kaʻu keiki)?
• Pehea lā ka papa hana lapaʻau a kaʻu (a i ʻole kaʻu keiki)? Pehea ka lōʻihi?
• He aha nā mea kūikawā e hiki iaʻu ke hoʻomaʻamaʻa e mālama ai i nā niho o kaʻu (a i ʻole nā ​​niho o kaʻu keiki)?
• He aha nā pilikia ʻē aʻe e kū mai ana i ka wā e hiki mai ana ma muli o kēia kūlana?

ʻO ka mea nui e hoʻomanaʻo mai kēia ʻatikala!

ʻAe, i kēia manawa ua loaʻa iā ʻoe kahi manaʻo maikaʻi aʻe o ka mea a mākou i kamaʻilio ai (Amelogenesis Imperfecta). Inā loaʻa iā ʻoe kēia maʻi, pono ʻoe e hana pū me kahi kauka niho e nānā mau ana i kou mau niho. ʻOiai hiki ke hoʻonāukiuki ke mālama pono i kou mau niho, e hoʻomanaʻo he mau lāʻau lapaʻau e hiki ke kōkua i ka pale ʻana i ka enamel āu. Eia kekahi, inā ʻaʻole ʻoe hauʻoli i kou minoʻaka, aia nā lāʻau lapaʻau e hiki ke hoʻomaikaʻi i kona helehelena. Hiki ke lōʻihi kekahi manawa, akā hiki iā ʻoe a me kāu kauka niho ke hana i nā hana e mālama ai i kou mau niho. Mai hopohopo, ʻae? Me ka ʻike kūpono a me ka lāʻau lapaʻau, hiki ke mālama ʻia kēia maʻi.

ʻAmelogenesis Imperfecta, Enamel Niho, Nā Maʻi Hoʻoilina, Hoʻololi ʻAno o ke Kala o ka Niho, Lāʻau Niho, Ola Kino Niho, Nā Pilikia Niho