Ke luhi mau nei ʻoe a me ka palaualelo? A i ʻole loaʻa iā ʻoe nā maʻi koʻikoʻi mai nā mea liʻiliʻi loa? Ke ʻike nei ʻoe i nā palapū ma kou kino a puni? ʻOiai ke manaʻo nei mākou he mea maʻamau kēia mau mea, i kekahi manawa hiki iā lākou ke lilo i mau hōʻailona o kahi pilikia i loko o ko mākou kino. ʻO ia hoʻi, ua hiki i ka manawa e nānā ai inā e hoʻomaha ana ka hale hana koko nui o ko mākou kino, ʻo ia hoʻi ka iwi iwi.
He aha maoli ka anemia aplastic?
I ka ʻōlelo maʻalahi, he maʻi koko kakaikahi loa akā he maʻi koʻikoʻi ka anemia aplastic. ʻO ka mea e hana ʻia ana, ʻo ka ʻāpana huʻahuʻa i loko o ko kākou mau iwi, i kapa ʻia ʻo ka iwi iwi , e pau ana i ka hana ʻana i nā hunaola koko hou. E noʻonoʻo me he mea lā ua hoʻomaka koke ka hale hana koko nui o ko kākou kino e hana.
ʻEkolu mau ʻano nui o nā pūnaewele i loko o ko kākou koko:
- Nā hunaola koko ʻulaʻula: ʻO kēia nā mea e lawe ai i ka oxygen ma ke kino holoʻokoʻa.
- Nā hunaola koko keʻokeʻo: ʻO kēia ko mākou pūʻali koa e hakakā nei i nā maʻi a me nā maʻi ahulau.
- Nā Platelets: ʻO kēia nā mea e hoʻōki ai i ke kahe ʻana ke loaʻa kahi ʻeha.
I kekahi manawa, i loko o ka anemia aplastic, hoʻokahi wale nō o kēia mau ʻano ʻekolu o nā hunaola koko i hana ʻia. Akā ʻo ka hapa nui, ʻaʻole i hana ʻia nā ʻano ʻekolu. Hiki i kēia maʻi ke ulu mālie a koke paha. Inā emi nui ka helu o nā hunaola koko, hiki ke hoʻoweliweli i ke ola.
ʻOiai hiki ke ulu kēia ʻano i kēlā me kēia makahiki, ʻoi aku ka maʻamau i nā poʻe ʻōpio i ko lākou mau makahiki he 20 a me ka poʻe ma luna o 60.
He aha ke kumu o kēia kūlana?
Hiki i ka anemia aplastic ke loaʻa nā kumu like ʻole. E hoʻoholo nā kauka i ke ʻano o ia mea a me kona koʻikoʻi.
Anemia Aplastic i hoʻoilina ʻia
Hoʻokumu ʻia kēia e kekahi mau kīnā genetic i hānau ʻia me ʻoe. Pale kēia mau genes i kou iwi iwi mai ka hana ʻana i nā hunaola koko lawa. No ka laʻana, pili nā kūlana e like me Fanconi anemia a me Dyskeratosis congenita me kēia.
Nā kumu ma hope (Acquired Aplastic Anemia)
ʻO kēia ke ʻano maʻamau. ʻO ka mea e hana ʻia ma ʻaneʻi , ʻo ia ka hoʻouka hewa ʻana o kā mākou ʻōnaehana pale ponoʻī i kā mākou mau hunaola iwi ponoʻī. Aia kekahi mau kumu ʻē aʻe:
- ʻO kekahi mau maʻi e like me ka 'HIV' a i ʻole '(Epstein-Barr)'.
- ʻO kekahi mau lāʻau lapaʻau, ʻoiai kekahi mau antibiotics.
- Ka ʻike ʻia ʻana i nā kemika ʻawahia.
- ʻO ka radiation a i ʻole chemotherapy no ka maʻi kanesa.
- Nā maʻi autoimmune ʻē aʻe.
Nā hihia kahi i loaʻa ʻole ai ke kumu (Idiopathic Aplastic Anemia)
I kekahi manawa, ʻaʻole hiki i nā kauka ke loaʻa kahi kumu maopopo no kēia ʻano. Ua kapa ʻia kēia mau hihia penei.
He moʻolelo ʻokoʻa ka "pilikia aplastic". He kū koke ia o ka hana ʻana o nā hunaola koko ʻulaʻula. Akā, hoʻopau pinepine ia i loko o kekahi mau pule. ʻO ka anemia aplastic kahi maʻi lōʻihi.
He aha nā hōʻailona āu e ʻike nei?
E hilinaʻi ana kāu mau hōʻailona i ke ʻano o nā hunaola koko i nele. Eia nō naʻe, no ka mea, ʻo nā ʻano hunaola ʻekolu a pau e nele pinepine ana, e ʻike paha ʻoe i ka hui pū ʻana o kēia mau hōʻailona.
| Ua emi ke ʻano o nā hunaola koko | Nā hōʻailona hiki ke loaʻa |
|---|---|
| Ua emi nā hunaola koko ʻulaʻula |
|
| Ua emi nā hunaola koko keʻokeʻo |
|
| Ka emi ʻana o nā platelets |
|
Pehea ʻoe e ʻike ai i kēia, e Kauka?
Inā loaʻa iā ʻoe nā hōʻailona e like me kēia, e kauoha kāu kauka i kekahi mau hoʻokolohua e hōʻoia i ka maʻi.
- Helu Koko Piha (FBC): Ke ana kēia i ka nui o kēlā me kēia ʻano cell i loko o kou koko.
- ʻO ka Smear Koko Peripheral:Maanei, ua nānā ʻia kahi hāpana o kou koko ma lalo o kahi microscope e nānā i nā ʻano ʻē i ke ʻano a me ka nui o nā cell.
- ʻO ka ʻume ʻana o ka iwi iwi a i ʻole ka Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi a paʻa loa e hōʻoia i ka hōʻailona. Ma lalo o ka anesthesia, lawe ʻia kahi hāpana liʻiliʻi loa o ka iwi iwi mai ka iwi ʻūhā a i ʻole ka iwi kūpono ʻē aʻe. ʻOiai he hoʻāʻo paʻakikī kēia, he mea nui e ʻike pololei i ka maʻi.
He aha nā lāʻau lapaʻau no kēia?
ʻO ke ʻano o ka mālama ʻana ma muli o nā kumu e like me ke kumu o ka maʻi, kona koʻikoʻi, a me kou mau makahiki.
- Ke mālama ʻana i ke kumu: I kekahi manawa, inā he lāʻau lapaʻau a kemika paha ke kumu o kēia kūlana, hiki i ka hoʻōki ʻana ke hoʻomaikaʻi i ke kūlana.
- E Nānā a Kali: Inā ʻaʻole koʻikoʻi loa ka maʻi, ʻaʻole paha e kuhikuhi kāu kauka i kekahi lāʻau lapaʻau a nānā i kou kūlana ma ka nānā pinepine ʻana i kāu helu koko.
- Lāʻau lapaʻau:
- Nā Immunosuppressants: Kōkua kēia mau lāʻau lapaʻau i ka pale ʻana i kāu ʻōnaehana pale mai ka hoʻouka ʻana i kou iwi iwi.
- Nā mea hoʻouluulu iwi: Kōkua kēia mau lāʻau lapaʻau i ka iwi e hana i nā hunaola koko hou aʻe.
- Nā Hoʻoili Koko: No ka hoʻonui ʻana i ka nui o nā hunaola koko ʻulaʻula a i ʻole nā platelets i hoʻopau ʻia, pono e hāʻawi ʻia ke koko mai waho mai. ʻAʻole kēia he lāʻau lapaʻau, akā kōkua ia i ka kaohi ʻana i nā hōʻailona.
- Hoʻoili Kelepona Kumu: Ua kapa ʻia kēia he Hoʻoili Iwi ʻOmo . Pili kēia i ka hoʻololi ʻana i ka iwi ʻomo maʻi me nā hunaola kumu olakino mai kahi kanaka olakino (pinepine he hoahānau pili). Hiki i kēia ke ho'ōla loa i ka maʻi. He lāʻau lapaʻau holomua kēia, ʻoi aku hoʻi no nā poʻe maʻi ʻōpio.
Loaʻa i kēlā me kēia lāʻau lapaʻau kona mau pono a me nā pilikia, no laila ʻoi aku ka maikaʻi o ke kūkākūkā ʻana i ke koho lapaʻau maikaʻi loa me kāu kauka.
Pehea ʻoe e noho ai me kēia kūlana?
Inā loaʻa iā ʻoe ka anemia aplastic, pono ʻoe e mālama pono i kou olakino.
- E pale iā ʻoe iho mai nā maʻi: E holoi pinepine i kou mau lima. E noho mamao aku mai ka poʻe maʻi a me nā wahi piha kanaka i ka hiki.
- E pale i nā ʻeha: Ma muli o ka pilikia o ke kahe ʻana o ke koko, e pale i nā haʻuki a me nā hana e hiki ai ke hōʻeha.
- E hoʻomaha maikaʻi: E hoʻomaha maikaʻi ke luhi ʻoe.
- ʻAi kaulike: E ʻai i nā meaʻai momona.
- E hahai i nā ʻōlelo aʻoaʻo lapaʻau:E lawe i ka lāʻau lapaʻau i kuhikuhi ʻia e kāu kauka i ka manawa kūpono. Eia kekahi, e hōʻoia e kūkākūkā me kāu kauka i nā kūlana kūikawā, e like me ma mua o ka lele ʻana.
Leka Lawe-Home
- He maʻi kakaikahi akā koʻikoʻi ka anemia aplastic kahi e pau ai ka hana ʻana o ka iwi iwi i nā hunaola koko.
- Mai hoʻowahāwahā i nā hōʻailona e like me ka luhi nui koke, nā maʻi pinepine, a me nā palapū ma kou kino.
- I kēia manawa, aia nā lāʻau lapaʻau kūpono loa no kēia. No laila, he mea nui loa ka ʻike mua ʻana i ka maʻi a hoʻomaka i ka lāʻau lapaʻau.
- E wehe a ʻoiaʻiʻo me kāu kauka e pili ana i kāu mau hōʻailona, makaʻu, a me nā koho lapaʻau. Me ke alakaʻi lapaʻau kūpono, hiki ke hoʻokele pono ʻia kēia kūlana.











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