E aʻo kākou e pili ana i ka CNS Vasculitis: kahi maʻi kahi e pehu ai nā kīʻaha koko i loko o ka lolo a me ke kaula spinal.

Loaʻa iā ʻoe kahi ʻeha poʻo mau loa a ʻaʻole hiki iā ʻoe ke hoʻomanawanui? A i ʻole ke manaʻo koke nei ʻoe i ka poniuniu a poina i nā mea? I kekahi manawa manaʻo mākou he luhi maʻamau a he kaumaha paha kēia mau mea a hoʻowahāwahā wale mākou iā lākou. Eia naʻe, ma hope o kēia mau mea, pono mākou e akahele iki, aia paha kahi maʻi laha ʻole i hūnā ʻia ma hope o lākou. I kēia lā e kamaʻilio mākou e pili ana i ia ʻano maʻi. ʻO ia ka CNS Vasculitis.

I ka ʻōlelo maʻalahi, he aha ka CNS Vasculitis?

E noʻonoʻo he kūlanakauhale nui ko kākou kino. A laila ʻo ka lumi hoʻomalu nui o kēia kūlanakauhale ʻo ia ko kākou ʻōnaehana nerve waena (CNS) . Hoʻokomo pū kēia i ko kākou lolo a me ke kaula kuamoʻo . ʻO nā mea a pau a kākou e hana ai me ka ʻike (e like me ka heluhelu ʻana i kēia ʻatikala me ko kākou mau manamana lima) a me nā mea a pau a kākou e hana ai me ka ʻike ʻole (e like me ka hanu ʻana, ka puʻuwai o ka naʻau) ua hoʻomalu ʻia mai kēia lumi hoʻomalu.

Pono kēia lumi hoʻomalu i ka lako koko mau e hana pono ai. Hoʻolako ʻia kēia koko e kahi pūnaewele o nā kīʻaha koko maikaʻi loa. ʻO ka CNS Vasculitis kahi kūlana kahi e pehu ai nā kīʻaha koko e hoʻolako ana i ke koko i ka lolo a me ke kaula spinal, a i ʻole e mumū . E like me ka paʻa ʻana o ka paipu wai i ka ʻōpala a pehu, e ālai ia i ke kahe o ka wai, i ka wā e pehu ai kēia mau kīʻaha koko, e ālai ia i ke kahe o ke koko i ka lolo. Hiki i kēia ke hōʻino nui i ka hana o ka lolo.

ʻElua mau ʻano nui o ka CNS Vasculitis:

Ua hoʻokaʻawale nā ​​kauka i kēia maʻi i ʻelua ʻāpana nui. ʻO ka hoʻomaopopo ʻana i kēlā e kōkua iā ʻoe e hoʻomaopopo maikaʻi i ka maʻi.

He aha nā hōʻailona e pono ai ʻoe e hopohopo?

Hiki ke ʻokoʻa nā hōʻailona o kēia maʻi mai kēlā kanaka a kēia kanaka. Eia kekahi, ʻoiai ua ʻike ʻia kēia mau hōʻailona i nā maʻi ʻē aʻe, ʻaʻohe pono e hopohopo ke ʻike ʻoe iā lākou. Eia nō naʻe, inā hoʻomau kēia mau hōʻailona, ​​​​he mea nui loa ia e ʻike i ke kauka a ʻimi i ka ʻōlelo aʻo.

Nā pilikia e hiki mai ana ma muli o kēia maʻi

I loko o ka CNS Vasculitis, ʻōlelo mākou e pehu nā kīʻaha koko a mānoanoa nā paia, e ālai ana i ke kahe ʻana o ke koko. Inā ʻaʻole i kāohi ʻia kēia kūlana, hiki iā ia ke hōʻeha nui i ka lolo a me ke kaula spinal, a hiki ke loaʻa nā pilikia e hoʻoweliweli ai i ke ola.

• Hahau: Hana ʻia ka hahau ke ʻoki loa ʻia ke kahe koko i kahi ʻāpana o ka lolo.
• Nā Hoʻouka Ischemic Kuikilana (TIAs): Ua kapa ʻia kēia mau mea he "mini-strokes." He mau mea hōʻoki manawa pōkole lākou i ke kahe koko, e hōʻike ana i nā hōʻailona o ka hahau e hele mai a hele aku no ka manawa pōkole. Eia nō naʻe, hiki iā lākou ke lilo i mea mua i kahi hahau nui.
• Nā Aneurysms o ka lolo: Lilo nā kīʻaha koko pehu i nāwaliwali, pehu e like me ka pōpō, a hiki ke pohā koke. He kūlana pilikia kēia, he mea hoʻoweliweli i ke ola.

No ke aha e kū mai ai kēia ʻano maʻi? (Nā kumu)

He maʻi autoimmune ka CNS Vasculitis. No ka hoʻomaopopo ʻana i kēia, e lawe kākou i kahi laʻana liʻiliʻi. E noʻonoʻo he pūʻali koa pale i loko o ko kākou kino. ʻO ia ko kākou ʻōnaehana pale . ʻO ka hana a kēia pūʻali koa, ʻo ia ke kaua aku i nā germs (e like me nā virus a me nā bacteria) e komo i loko o ke kino mai waho a pale iā kākou mai nā maʻi.

Eia nō naʻe, i loko o kahi maʻi autoimmune, ua kuhihewa ko kākou mau pale ponoʻī a hoʻomaka e hoʻouka i kā kākou mau hunaola a me nā ʻiʻo olakino ma kahi o nā mea komo hewa ʻē. I loko o ka CNS Vasculitis, hoʻouka kēia ʻōnaehana pale i nā kīʻaha koko i loko o ka lolo a me ke kaula spinal.

Nā kumu o ka Vasculitis CNS Lua

Ke ʻōlelo nei mākou ua hoʻokumu ʻia ke ʻano lua e kekahi maʻi ʻē aʻe. Eia kekahi o nā kumu hiki:

• Nā maʻi autoimmune ʻē aʻe: Nā maʻi e like me lupus, Sjögren's syndrome, Behçet's syndrome.
• Nā maʻi viral: Nā mea e like me ka maʻi Epstein-Barr (EBV), ka maʻi Varicella-zoster, ka mea e hoʻoulu ai i ka moa.
• Nā maʻi bacteria: Nā maʻi e like me ka maʻi puʻupuʻu a me ka syphilis.

Pehea e ʻike ai ke kauka i kēia maʻi?

He hana paʻakikī iki ka ʻike ʻana i kēia maʻi. No ka mea ua like nā hōʻailona me nā maʻi maʻamau ʻē aʻe, hana ke kauka i kahi hana i kapa ʻia ʻo "differential diagnosis." ʻO ia hoʻi, hoʻāʻo ʻo ia a hōʻoia ʻaʻole kēia maʻi, pākahi, ma muli o nā maʻi maʻamau ʻē aʻe e hiki ke hoʻoulu i kēia mau hōʻailona (e.g., migraine, epilepsy).

E nānā mua kāu kauka iā ʻoe a nīnau iā ʻoe i kahi nīnau kikoʻī e pili ana i kāu mau hōʻailona. He mea nui e kikoʻī e pili ana i ka wā i hoʻomaka ai kāu mau hōʻailona, ​​​​inā paha e hele mai a hele aku, a inā paha e ʻoi aku ka ʻino i kekahi mau manawa o ka lā.

Ma hope o kēlā, hiki iā ʻoe ke kuhikuhi ʻia e hana i kekahi mau hoʻokolohua e like me kēia:

• MRI a me CT scan: E kiʻi i nā kiʻi o ka lolo a me ke kaula kuamoʻo e ʻike ai inā he pehu, hōʻino, a i ʻole nā ​​​​​​mea ʻē.
• Angiogram: He hoʻāʻo e pili ana i ka hoʻokomo ʻana i kahi wai kūikawā i loko o nā kīʻaha koko a me ka lawe ʻana i nā kiʻi X-ray e ʻike ai pehea ke ʻano o nā kīʻaha koko, inā ua ālai ʻia a pehu paha.
• Biopsy: Hana pinepine ʻia kēia e hōʻoia i ka hōʻailona. Lawe ʻia kahi ʻāpana liʻiliʻi loa o ka ʻiʻo o ka lolo a nānā ʻia ma lalo o kahi microscope e ʻike inā he mumū i loko o nā kīʻaha koko.
• Lumbar Puncture / Spinal Tap: Lawe ʻia kahi hāpana liʻiliʻi o ka wai o ka lolo spinal (CSF) e hoʻopuni ana i ke kaula spinal mai ka iwi kuamoʻo a nānā ʻia no ka helu kiʻekiʻe o nā keʻokeʻo koko a me nā hōʻailona o ka mumū.
• Nā Hoʻāʻo Koko: E nānā i ke koko no nā māka o ka mumū i loko o ke kino (e like me ESR, C-reactive protein).

Hiki paha iā ʻoe ke kuhikuhi ʻia i kahi rheumatologist .

Pehea e mālama ʻia ai?

ʻO ka pahuhopu nui o ka mālama ʻana i ka CNS vasculitis ʻo ia ke kāohi ʻana i ka mumū i loko o nā kīʻaha koko a hoʻōki i ka hōʻino ʻana i ka lolo a me ke kaula spinal.

I ka manawa pinepine, hoʻohana ʻia nā lāʻau lapaʻau he nui no ka mālama ʻana:

1. Corticosteroids: He mau lāʻau anti-inflammatory ikaika kēia. Kōkua lākou i ka hoʻomalu koke ʻana i ka hana o ka ʻōnaehana pale. Hiki iā ʻoe ke hoʻomaka me kahi mahele nui i ka wā mua.

2. Nā mea hoʻopau i ka pale ʻana i ka maʻi:Hana kēia mau lāʻau lapaʻau ma ka kaohi ʻana i ka ʻōnaehana pale kino overactive a ke kāohi nei iā ia mai ka hoʻouka ʻana i ke kino ponoʻī.

ʻOiai hiki ke hāʻawi mua ʻia nā lāʻau lapaʻau kiʻekiʻe, ma hope o kekahi mau mahina, i ka wā e kaohi ʻia ai nā hōʻailona, ​​e hōʻemi mālie ke kauka i ka nui. ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka hoʻihoʻi ʻana i ka maʻi i ka hoʻomaha ʻana . ʻO ia hoʻi, he manawa lōʻihi i ka wā e nalowale loa ai nā hōʻailona a i ʻole he akahai loa.

Inā loaʻa iā ʻoe ke ʻano lua, pono ʻoe e mālama i ka maʻi kumu i hoʻokumu ai (e.g. lupus).

Pehea e ola ai me kēia maʻi?

ʻAʻohe lāʻau lapaʻau no kēia maʻi i kēia manawa. Akā, ʻaʻole ia he manaʻo e nalowale kākou i ka manaʻolana. Me ka lāʻau kūpono, hiki i nā kānaka he nui ke noho me ka ʻole o nā hōʻailona no nā mahina a i ʻole nā ​​makahiki, i ke kala ʻana.

ʻAʻole hoʻopōkole pinepine ka CNS Vasculitis i ka manaʻolana ola. Eia nō naʻe, inā loaʻa nā pilikia koʻikoʻi, e like me ka hahau ʻana a i ʻole ka haki ʻana o ka aneurysm, hiki ke hoʻoweliweli i ke ola. ʻO ia ke kumu he mea nui loa ka ʻike mua ʻana i ka maʻi a loaʻa ka lāʻau kūpono.

He mea maʻamau i kekahi ke makaʻu i ka wā e ʻike ai lākou he maʻi lolo ko lākou. Akā e hoʻomanaʻo, me ka ʻepekema lapaʻau holomua o kēia wā, hiki ke mālama maikaʻi ʻia kēia kūlana. ʻO ka mea nui loa, ʻo ia ke kamaʻilio ākea me kāu kauka. E haʻi iā ia i nā mea āpau āu e loaʻa nei, kou hopohopo, kou makaʻu, a me kou mau loli i nā hōʻailona. A laila hiki iā ia ke hoʻomohala i ka hoʻolālā lapaʻau kūpono loa nāu.