Ua ʻike anei ʻoe i kahi puʻupuʻu liʻiliʻi ma lalo o ka ʻili o ka ʻāʻī o kāu pēpē, ka ʻāʻī lima, a i ʻole ke poʻo i hopohopo ai ʻoe? A i ʻole ua ʻōlelo paha kāu kauka iā ia i ka wā o ka scan i kou wā hāpai? He ʻano maʻi paha kēia i kapa ʻia ʻo Cystic Hygroma . He mea maʻamau ke manaʻo iki i ka makaʻu ke lohe ʻoe i kēia inoa. Akā i ka manawa e ʻike ai ʻoe i ke ʻano o ia mea, e nalo aku kēlā makaʻu a e ʻike maikaʻi ʻoe i ke ʻano e hana ai me ia.
I ka ʻōlelo maʻalahi, he aha ka Cystic Hygroma?
He cyst piha wai ka Cystic Hygroma, a he nui paha nā cysts. Ua like ia me kahi pōpō wai. Hoʻomohala pinepine ʻia kēia mau mea ma ke poʻo a i ʻole ka ʻāʻī o kahi pēpē. Akā i kekahi manawa hiki iā lākou ke ulu ma nā wahi e like me nā ʻāʻī lima a me ka umauma.
ʻO ke kumu o kēia, aia kahi ālai ʻana i loko o ka ʻōnaehana lymphatic i loko o ko kākou kino. E noʻonoʻo i kēia ʻōnaehana lymphatic e like me kahi ʻōnaehana e wehe ana i nā ʻōpala mai ko kākou kino. ʻO kēia ʻōnaehana ka mea e kānana i nā mea ʻino e like me nā germs a kōkua i ka mālama ʻana i ke kino i ke olakino. No laila, inā he ālai ʻana ma kekahi wahi o kēia ʻōnaehana i ka wā e ulu ana ka pēpē i loko o ka ʻōpū, hōʻiliʻili ka wai ma laila a hana ʻia kahi cyst e like me kēia.
He maʻi laha ʻole kēia. ʻO ke ʻano kēia, hoʻokahi i loko o 8,000 mau pēpē i hoʻopilikia ʻia e kēia maʻi. Eia kekahi, ʻaʻole nā pēpē āpau me ka Cystic Hygroma i loaʻa nā pilikia olakino nui ʻē aʻe. Ua hānau ʻia kekahi mau pēpē me ke olakino piha me kēia maʻi.
I kekahi manawa e ho'ōla pono'ī kēia mau pu'upu'u me ka ʻole o ka lā'au lapa'au. Eia na'e, inā ʻa'ole, ʻo ke ʻoki ʻana e wehe iā lākou ke koho maikaʻi loa, no ka mea hiki iā lākou ke hōʻino i nā kino a puni, hoʻoulu i nā maʻi, a hoʻoulu i ka ʻoluʻolu ʻole i ka wā e ulu ana ka pēpē.
He aha nā hōʻailona o kēia?
Pili nā hōʻailona i ka wahi a me ka nui o ka puʻupuʻu. I kekahi manawa, hiki i ka puʻupuʻu ke hoʻopilikia i ka hana maʻamau o nā ʻōpū a puni. E nānā kākou i nā hōʻailona nui.
| Hōʻailona | Wehewehena |
|---|---|
| Ka pehu ʻana ma lalo o ka ʻili | Loaʻa paha i kahi pēpē hānau hou kahi palupalu a pehu ma lalo o ko lākou ʻili. I kekahi manawa he uliuli iki paha ke kala. |
| Ka paʻakikī o ka hanu ʻana a me ke ale ʻana | Inā aia ka puʻupuʻu ma kahi kokoke i ka puʻu a i ʻole ka ʻōpū hanu, hiki i ka pēpē ke paʻakikī i ka hanu ʻana a me ke ale ʻana i ka wā e hānai waiū ana. |
| ulu kūpilikiʻi | Ma muli o nā pilikia hānai, lohi iki paha ko lākou ulu ʻana ma mua o nā pēpē ʻē aʻe. |
| Ka hoʻonui ʻia ʻana o ka puʻupuʻu a me ka maʻi | E ulu pū ka cyst i ka wā e ulu ana ka pēpē. Eia kekahi, inā loaʻa ka maʻi i ka cyst a kahe paha ke koko i loko o ka cyst, hiki iā ia ke nui koke. |
| Nā hopena ma nā iwi a me nā niho | Inā waiho ʻole ʻia ka mālama ʻole no ka manawa lōʻihi, e hōʻino ʻia paha ka iwi a me nā niho a puni ka puʻupuʻu. |
He aha nā kumu o ka Cystic Hygroma?
Hiki i nā genes o ka pēpē a me ke kaiapuni i loko o ka ʻōpū ke hoʻopilikia i ka ulu ʻana o kēia ʻōnaehana lymphatic. ʻO kahi pilikia me ka ulu ʻana o kēia ʻōnaehana ke kumu nui o Cystic Hygroma.
I kekahi manawa hiki ke hana ia ma kona iho me ka ʻole o kekahi maʻi ʻē aʻe. Eia nō naʻe, i kekahi mau hihia hiki ke pili i nā kūlana genetic . Eia kekahi laʻana:
- ʻO ka maʻi Turner
- ʻO ka maʻi Down
- ʻO ka maʻi Noonan
Ke hana nei nā kauka i nā hoʻokolohua kūikawā e ʻike ai inā he pilina me nā kūlana e like me kēia.
Inā loaʻa kēia ʻano maʻi i nā pākeke, hiki ke kumu ʻia e kekahi ʻano ulia ( trauma ) a i ʻole kahi maʻi hanu ma mua. Eia nō naʻe, i ka hapanui o nā hihia, he paʻakikī ke loaʻa kahi kumu kikoʻī no kēia ʻano maʻi i nā pākeke.
Pehea e ʻike ai nā kauka i kēia maʻi?
I ka wā hāpai
ʻO ka hapa pinepine, ʻo ka ultrasound i ka wā hāpai e hōʻike i kēia mau mea:ʻO kēia ka manawa mua e ʻike ai ke kauka i kēia puʻupuʻu. Hiki ke ʻike ʻia ma kahi o 20 mau pule o ka hāpai ʻana.
Inā hōʻike ke kiʻi i kahi mea e like me kēia, e paipai ke kauka e hana i kekahi mau hoʻokolohua hou aʻe e hōʻoia i ʻole he mau pilikia hoʻoilina ʻē aʻe o ka pēpē.
- CVS (Chorionic Villus Sampling) : Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka placenta o ke pēpē a hoʻāʻo iā ia no nā kūlana genetic.
- Amniocentesis: Pili kēia i ka lawe ʻana i kahi liʻiliʻi o ka wai (wai amniotic) i loko o ka ʻōpū o ke pēpē a hoʻāʻo iā ia.
Mai makaʻu e nīnau e pili ana i kēia mau hoʻokolohua. E wehewehe pono kāu kauka i nā mea āpau iā ʻoe. Pono nō hoʻi ʻoe e hana i nā scan maʻamau e nānā i nā loli i ka puʻupuʻu a me nā pilikia ʻē aʻe.
E hoʻolālā pinepine kāu kauka e hānau i kāu pēpē ma o ka ʻoki cesarean (C-section) ma kahi o 38 mau pule. Pono ʻoe e koho i kahi haukapila me kahi Neonatal Intensive Care Unit (NICU) a me nā kauka ʻoki keiki . ʻO kēia no ka mea pono i ka haukapila nā pono āpau e pono ai e mālama i kāu pēpē inā pono ʻo ia i ka mālama ulia pōpilikia ma hope o ka hānau ʻana. E kōkua kāu kauka iā ʻoe e koho i kahi haukapila kūpono no kēia.
Ma hope o ka hānau ʻana
I kekahi manawa ʻike ʻia kēia puʻupuʻu ma hope o ka hānau ʻana o ke pēpē. Inā hana ʻia kēia, e kauoha ke kauka i nā hoʻokolohua e like me ka X-ray umauma, ultrasound scan, a i ʻole MRI/CT scan e hōʻoia inā he cystic hygroma ia.
He aha nā lāʻau lapaʻau?
ʻO ka lāʻau lapaʻau nui a kūleʻa loa no ka cystic hygroma, ʻo ia ka wehe loa ʻana i ka ʻōpū ma o ke ʻoki ʻana.
Eia nō naʻe, inā waiho ʻia kahi ʻāpana liʻiliʻi o ka puʻupuʻu i ka wā o ke ʻoki ʻana, aia ma kahi o 15% ka pilikia o ka hoʻi hou ʻana mai. Aia kekahi mau lāʻau ʻē aʻe, ʻoiai ʻaʻole lākou i holomua e like me ke ʻoki ʻana.
- Kemoterapia
- Hoʻōla radiation
- Nā steroid
- Sclerotherapy: ʻO kēia ka hoʻokomo ʻana i kahi lāʻau lapaʻau kūikawā i loko o ka puʻupuʻu, e hoʻemi ana.
He aha nā pilikia e hiki mai ana?
Aia kahi pilikia o nā pilikia i loko o ia ʻano kūlana. Akā he mea nui e makaʻala i kēia mau mea ma mua. Hoʻomaopopo mau nā kauka i kēia mau pilikia a lawe i nā hana e pono ai e pale aku iā lākou.
- Hiki ke hoʻonui a emi paha ka nui o ka wai amniotic i loko o ka ʻōpū i ka wā hāpai.
- I kekahi mau hihia, aia paha ka pilikia o ka hāʻule ʻana.
- Inā nui ka puʻupuʻu, hiki ke ālai i ke ala ea o ke pēpē.
- Aia paha kekahi mau loli i ke ʻano o ka maka.
- Hiki i ka ʻōpū ke hana i kahi maʻi ʻili e like me ka cellulitis .
- Aia paha he mau pilikia e like me ka hōʻino ʻana o nā aʻalolo a i ʻole ke kahe nui ʻana o ke koko ma hope o ke ʻoki ʻana.
- ʻOiai ma hope o ke ʻoki ʻana, aia kahi manawa liʻiliʻi e ulu hou ai ka puʻupuʻu.
Mai hopohopo ke lohe ʻoe i kēia mau mea. ʻAʻole e hiki mai kēia mau mea a pau. He mau mea "hiki" wale nō kēia. Ua ʻike kāu hui lapaʻau i kēia mau pilikia a pau a ua aʻo ʻia lākou e hana me lākou.
Leka Lawe-Home
- He puʻupuʻu piha wai ka Cystic Hygroma e ulu ana ma muli o kahi pilikia me ka ʻōnaehana lymphatic o kahi pēpē. ʻAʻole ia he maʻi kanesa.
- I kekahi manawa, hiki ke ʻike pinepine ʻia kēia ma ka ultrasound i ka wā hāpai.
- Ma muli o ka pili ʻana o kēia ʻano me kekahi mau maʻi genetic, e ʻōlelo aku kāu kauka i ka hoʻāʻo ʻana no ia.
- ʻO ke ʻano nui o ka lāʻau lapaʻau, ʻo ia ka wehe ʻana i ka puʻupuʻu ma o ke ʻoki ʻana. Mai hopohopo, he poʻe akamai nā kauka ʻoki keiki i kēia.
- Inā he mau hopohopo a kānalua paha kāu, e kamaʻilio koke me kāu kauka. Mai hoʻoholo ma muli o ka ʻike i loaʻa ma ka pūnaewele.











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