Ke hopohopo nei ʻoe e pili ana i kahi puʻupuʻu liʻiliʻi ma ka ʻāʻī o kāu pēpē a i ʻole ma kahi ʻē aʻe o ko lākou kino? A i ʻole inā ʻoe e hāpai ana i kahi pēpē, ua ʻōlelo anei ke kauka i kekahi mau pilikia me ka ulu ʻana o ka pēpē i ka wā o ke scan? I kekahi manawa he mea maʻamau ke manaʻo nui i ka makaʻu ke lohe a ʻike paha ʻoe i nā mea e like me kēia. I kēia lā e kamaʻilio mākou e pili ana i kahi mea āu e pono ai e makaʻala i ka manawa e like me kēia. ʻO ia ke ʻano i kapa ʻia ʻo Cystic Hygroma .
I ka ʻōlelo maʻalahi, he aha ka Cystic Hygroma?
E noʻonoʻo i ko kākou kino he ʻōnaehana i kapa ʻia ʻo ka ʻōnaehana lymphatic. Ua like kēia me kahi ʻōnaehana hoʻolei ʻōpala i loko o ko kākou kino. ʻO kēia ka mea e wehe ai i nā mea pono ʻole a me nā mea ʻawahia mai ko kākou kino a lawe iā lākou ma o ka ʻōnaehana koko ma o kahi wai i kapa ʻia ʻo ka wai lymph me ke kōkua o nā hunaola koko keʻokeʻo. I kēia manawa, i kekahi manawa i ka wā e noho ana ke pēpē i loko o ka ʻōpū, inā ʻaʻole ulu pono kēia ʻōnaehana lymphatic, a inā paha he mea paʻa i kekahi wahi i loko, hōʻiliʻili kēlā wai lymphatic ma kahi hoʻokahi a hana i kahi ʻeke piha i ka wai, ʻo ia hoʻi, he cyst . ʻO ia ka mea a mākou e kapa nei he cystic hygroma.
ʻIke pinepine ʻia kēia ma ka ʻāʻī o ka pēpē . Akā hiki nō hoʻi ke ulu aʻe ma kahi ʻē aʻe o ke kino. Hiki ke ʻike ʻia kēia mau puʻupuʻu i kekahi manawa i ka wā o ka ultrasound scan ʻoiai ke pēpē i loko o ka ʻōpū. A i ʻole hiki iā lākou ke ʻike ʻia he puʻupuʻu liʻiliʻi a puʻupuʻu paha ma lalo o ka ʻili ma hope o ka hānau ʻana o ke pēpē. Inā hana kēia i ka wā hāpai, aia kekahi manawa ka pilikia o ka hāʻule ʻana o ka pēpē a i ʻole ka hānau make ʻana .
ʻO wai ka mea i hoʻopilikia nui ʻia e kēia kūlana?
Hiki ke loaʻa kēia ʻano i kapa ʻia ʻo cystic hygroma i kekahi pēpē . ʻO kēia no ka mea hiki ke hana ʻia i kekahi manawa e kahi loli genetic e hoʻopilikia ai i ke ʻano o ka ulu ʻana o ka ʻōnaehana lymphatic o ka pēpē. Hiki iā ia ke hana i kekahi manawa ma kāna iho me ka ʻole o nā maʻi ʻē aʻe. A i ʻole, hiki nō hoʻi ke hana me nā kūlana genetic e like me Down syndrome , Turner syndrome , a i ʻole Noonan syndrome .
Akā, he mea kupanaha, hiki ʻole ke loaʻa pinepine i nā pākeke . ʻO ka maʻamau, hiki mai ia ma hope o kekahi ʻano ulia kino a i ʻole kahi maʻi hanu .
Pehea ka maʻamau o kēia ʻano?
ʻO kaʻoiaʻiʻo, he mea kakaikahi loa nā cystic hygromas. He 6% lākou o nā puʻupuʻu ʻaʻole maʻi kanesa / maikaʻi ʻole i nā keiki. He mea kakaikahi loa lākou i nā pākeke.
He aha nā hōʻailona o kēia?
Hiki ke ʻokoʻa nā hōʻailona o kahi cystic hygroma ma muli o ke ʻano o ka cyst i hana ʻia.Ma muli o ka nui a me ka wahi. E nānā kākou i nā hōʻailona maʻamau:
- Me he pehu a puʻupuʻu paha ma lalo o ka ʻili .
- Hiki i kahi i loaʻa ai ka puʻupuʻu ke lilo i kala polū i kekahi manawa.
- Ke hoʻopā ʻoe, palupalu ka hua.
- ʻIke pinepine ʻia ma ka ʻāʻī , akā hiki ke loaʻa ma nā wahi a pau o ke kino.
- Hiki i ka nui o ka ʻōpū ke ʻano like me ka nui o ka pomelo a i ka nui o ka pī nui . Hiki ke hoʻonui ʻia kēia i ka wā e ulu ana ka pēpē.
I kēia manawa, e nānā kākou i kekahi o nā hōʻailona i hiki ke lilo i mea koʻikoʻi iki . Eia nā mea āu e makaʻala nui ai:
- Hiki ke hoʻopāpā ʻia ke ʻano o waho o kekahi ʻāpana o ke kino .
- Hiki ke hōʻino ʻia nā iwi a i ʻole nā ʻōpū o loko .
- Hiki i ka pēpē ke pilikia i ka ʻai ʻana a me ka inu ʻana .
- Hiki ke loaʻa nā pilikia hanu (pale ʻia ke ala ea).
- Hiki ke nui ke kahe koko (hemorrhage).
- Hiki ke loaʻa ka maʻi .
E like me kaʻu i ʻōlelo ai ma mua, inā loaʻa iā ʻoe kahi cystic hygroma i ka wā hāpai, aia kahi pilikia o ka hāʻule ʻana a i ʻole ka hānau make ʻana no ka mea hiki i ka puʻupuʻu ke hoʻopilikia i ka ulu ʻana o ka fetus. I kekahi manawa, hiki i kēia puʻupuʻu ke hoʻoulu i ka nui o ka wai e hōʻiliʻili i loko o ka fetus (hydrops). Inā hana ʻia kēia, hiki iā ia ke make i ka fetus.
No ke aha i hoʻokumu ʻia ai kēia cystic hygroma? He aha nā kumu?
ʻO kaʻoiaʻiʻo, ʻaʻole i ʻike ʻia ke kumu kikoʻī o ka cystic hygroma . Hoʻokumu ʻia kēia puʻupuʻu ma muli o ka hōʻino ʻia o ka ʻōnaehana lymphatic aʻu i ʻōlelo ai i ka wā fetal. A i ʻole i nā pākeke, hiki ke hana ʻia ma muli o kahi ulia kino a i ʻole kahi maʻi hanu. Ke hōʻino ʻia ka ʻōnaehana lymphatic, ʻaʻole kahe ka wai lymph i loko o ke koko a hōʻiliʻili ma lalo o ka ʻili, e hana ana i kahi puʻupuʻu piha i ka wai.
Manaʻo kekahi mau haʻawina e pili ana paha nā kumu o ke kaiapuni, e like me ka puhipaka a me ka inu ʻona i ka wā hāpai . Manaʻo kekahi mau haʻawina ua hoʻokumu ʻia nā cystic hygromas e nā loli genetic a i ʻole nā mutations e hoʻopilikia i ka ulu ʻana o ka ʻōnaehana lymphatic.
ʻO ka hapa pinepine, hiki wale kēia mau mea, akā i kekahi manawa hiki iā lākou ke hui pū me nā kūlana genetic e like me Down syndrome , Turner syndrome , a i ʻole Noonan syndrome .
Pehea e ʻike ai nā kauka i kēia?
ʻIke pinepine ʻia kahi cystic hygroma ma mua o ka piha ʻana o nā makahiki ʻelua o kahi pēpē . Inā hāpai ʻoe, hiki ke ʻike ʻia i ka wā o kahi scan ultrasound prenatal maʻamau. ʻO Alpha-fetoprotein, kahi i hana ʻia ma waena o 15 a me 20 mau pule.ʻO kahi hoʻāʻo koko i kapa ʻia ʻo "alpha-fetoprotein" e kōkua pū i ka hōʻoia ʻana i ka maʻi.
Inā hōʻike nā hoʻokolohua i ka wā hāpai he ʻano ʻē i nā chromosomes o ka pēpē, hiki i ka pēpē ke pilikia i ka loaʻa ʻana o ka cystic hygroma. A laila e nānā pono kāu kauka i ka ulu ʻana o ka fetus e hōʻoia i ke olakino o ka pēpē.
Ma hope o ka hānau ʻana o ke pēpē, e nānā kino ke kauka i ka puʻupuʻu a hiki paha ke hana i kahi X-ray , ultrasound , a i ʻole MRI scan e hōʻoia i ka hōʻailona. A laila wale nō e hoʻomohala ʻia ai kahi hoʻolālā lapaʻau e kūpono i ke kūlana o kāu pēpē.
He aha ka lāʻau lapaʻau no kēia?
ʻOkoʻa ke ʻano o ka mālama ʻana no kēlā me kēia pēpē me ka cystic hygroma. ʻO ka pahuhopu nui o ke kauka, ʻo ia ka wehe loa ʻana i ka puʻupuʻu, inā hiki. Hiki i ka mālama ʻana ke komo pū me:
- ʻO ke ʻoki kino e wehe i ka puʻupuʻu .
- Ka wehe ʻana i ke kahe i loko o ka cyst me kahi nila (i kapa ʻia hoʻi ʻo "Percutaneous drainage").
- Ke hoʻohuli nei i ke kahe mai ka puʻupuʻu i kekahi ʻāpana o ke kino (ua kapa ʻia kēia he sclerotherapy ).
- Ke wehe ʻana i ka puʻupuʻu me ka hoʻohana ʻana i ka laser therapy .
- Ke hoʻemi nei i ka nui o ka puʻupuʻu (ua kapa ʻia kēia he radiofrequency ablation ).
Akā i kekahi manawa ʻaʻole pono ka lāʻau lapaʻau . ʻO kēia no ka mea e nalowale ana kēia mau puʻupuʻu iā lākou iho i kekahi manawa. Eia kekahi, i kekahi manawa ma hope o ka lāʻau lapaʻau, inā he pōʻino i ka ʻōnaehana lymphatic, hiki i ka puʻupuʻu ke ulu hou . ʻOkoʻa ka holomua o ka lāʻau lapaʻau. I ka hapanui o nā hihia, inā hiki i ke kauka lapaʻau ke wehe i nā ʻiʻo ʻē aʻe i loko o ka puʻupuʻu, e maikaʻi paha ka hopena.
Hiki i nā lāʻau lapaʻau ke hoʻoulu i nā pilikia?
Inā wehe ʻia kahi puʻupuʻu ma ke ʻoki ʻana, hiki iā ia ke waiho i kahi ʻōpala i kekahi manawa . Aia kēia i ka nui o ka puʻupuʻu a me kona wahi. Eia nō naʻe, aia kekahi mau ʻano hana ʻē aʻe i kēia manawa, e like me ka laser therapy, e waiho ana i ka emi ʻana o ka ʻōpala ma mua o ke ʻoki kuʻuna.
ʻO ka mea nui loa, ma hope o ka mālama ʻana, ʻoiai ke ola hou ʻana mai ke ʻoki ʻana, pono ʻoe e mālama i kahi i loaʻa ai ka puʻupuʻu me he mea lā he ʻeha.
Aia kahi pilikia o ka maʻi ma hope o kekahi lāʻau lapaʻau. No laila, e nānā i ka cystic hygroma no kekahi kahe ʻana o ka pus keʻokeʻo a melemele paha, nā loli o ke kala, ka nui, ka mehana, a i ʻole ka ʻeha . Inā manaʻo ʻoe he maʻi kāu pēpē, e ʻike koke i kāu kauka .
Pehea lā e hiki ai iā kākou ke pale aku i kēia kūlana?
ʻOiai ʻaʻole ʻike ʻia ke kumu kikoʻī o ka cystic hygroma, he paʻakikī ke pale aku . Eia nō naʻe, hiki iā ʻoe ke hana i kēia mau mea e kōkua ai i kāu pēpē e ulu olakino:
- Ma mua o kou hāpai ʻana , e kamaʻilio me kāu kauka e pili ana i ka loaʻa ʻana o kahi hoʻokolohua genetic . E kōkua kēia iā ʻoe e hoʻomaopopo i kou pilikia o ka loaʻa ʻana o kahi keiki me kahi maʻi genetic.
- E pale loa i ka puhipaka a me ka inu ʻona i ka wā hāpai .
- E hele i nā hoʻokolohua lapaʻau maʻamau i kou wā hāpai i hiki iā ʻoe ke nānā i ke olakino o kāu pēpē e ulu ana.
- E ʻai i ka meaʻai kaulike a noho olakino .
He aha ka mea e hiki mai ana? He aha nā manawa kūpono e ho'ōla ai?
Aia ka wānana ma luna o kekahi mau kumu . ʻO kēia mau mea i ka wā i ʻike ai ke kauka i ka cystic hygroma, inā pili ka puʻupuʻu me kekahi maʻi ʻē aʻe, ka nui o ka puʻupuʻu, a me kona wahi.
Inā wehe ʻia ka puʻupuʻu ma ke ʻoki ʻana , maikaʻi loa ka manawa e hoʻōla ai inā hiki i ke kauka lapaʻau ke wehe palekana i nā ʻiʻo keu i loko o ka puʻupuʻu. Eia nō naʻe, inā ʻaʻole hiki ke wehe loa ʻia, aia ma kahi o 15% ka pilikia e hoʻi hou mai ka puʻupuʻu .
ʻO ka ʻike mua ʻana a me ka mālama mua ʻana nā ala maikaʻi loa e hoʻokō ai i nā hopena maikaʻi loa. Hiki i kēia ke hōʻemi i ka pilikia o nā pilikia e like me ka hōʻino ʻana o nā kino a me nā loli i ke ʻano e hiki ke hana ma muli o ka puʻupuʻu.
Inā kū mai ka cystic hygroma me kahi ʻano chromosomal, e like me Down syndrome , ua hoʻonui ʻia ka pilikia o ka hāʻule ʻana a me ka hānau make ʻana . E nānā pono kāu mea mālama ola i ka ʻōpū e ulu ana i kou wā hāpai e hōʻoia i ke olakino o ka pēpē.
Āhea ʻoe e ʻike ai i ke kauka?
Inā ʻike ʻoe i kekahi mea e like me kēia e pili ana i ka puʻupuʻu o kāu pēpē , e ʻike pono i ke kauka :
- Inā piʻi ka nui o ka puʻupuʻu .
- Inā loli ke kala .
- Inā e liki ana kahi wai melemele a keʻokeʻo paha .
- Inā he ʻulaʻula, ʻeha ke pā, a wela paha .
- Inā hōʻeha a ʻoluʻolu ʻole paha ia i ka pēpē.
- Inā e pāpā ʻia ana ka pēpē mai ka ʻai ʻana .
Inā pilikia kāu pēpē i ka hanu ʻana, e kelepona koke aku i ka 1990 (Suvaseriya Ambulance Service) a i ʻole e hele i ka keʻena ulia pōpilikia kokoke loa.
He aha nā nīnau koʻikoʻi e nīnau aku ai i ke kauka?
Ke hālāwai ʻoe me ke kauka, mai poina e nīnau i nā nīnau e like me kēia:
- " Pono anei kaʻu pēpē i ke ʻoki ʻana e wehe ai i kēia puʻupuʻu? "
- "No kēia hua""Aia kekahi pōʻino i nā ʻōpū, nā iwi, a i ʻole nā aʻalolo?"
- " He aha nā hopena ʻaoʻao o ka lāʻau āu e manaʻo nei? "
ʻO ka mea hope loa, aia kekahi mau mea e pono ai ʻoe e hoʻomanaʻo ...
He mea maʻamau ke hopohopo a me ka makaʻu ke ʻike ʻoe i kahi mea e like me ka puʻupuʻu nui ma ka ʻāʻī o kāu pēpē hānau hou. Akā, mai hopohopo. E hāʻawi kāu kauka i kāu pēpē i ka lāʻau lapaʻau maikaʻi loa a hana e hoʻēmi i ka puʻupuʻu i ka hiki a hiki paha ke wehe palekana.
Hiki ke pili pū ʻia ka cystic hygroma me nā kūlana genetic ʻē aʻe, no laila inā ʻoe e kali ana i kahi keiki a makemake ʻoe e ʻike i kou pilikia o ka loaʻa ʻana o kahi keiki me kahi kūlana genetic, e kamaʻilio me kāu kauka e pili ana i ka hoʻāʻo genetic .
ʻO ka mea pōʻino, i kekahi manawa hiki ke hana ʻia kahi hāʻule ʻana o ka pēpē a i ʻole ka hānau make ʻana. Inā hana ʻia kēlā, e haʻi aku kāu kauka iā ʻoe e pili ana i nā kumuwaiwai a i ʻole ke alakaʻi e hiki ke kōkua iā ʻoe e hoʻomanawanui i ka ʻeha. Mai ʻeha hoʻokahi, e kiʻi i ke kōkua āu e pono ai.
ʻO Cystic Hygroma, Cystic Hygroma, Nā Lymph Nodes, Puʻupuʻu o ka Pēpē, Hāpai Keiki, Nā Maʻi Hoʻoilina, Ola Kino o ke Keiki











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