Ua makaʻu iki paha ʻoe i kou ʻike ʻana i kahi puʻupuʻu hou ma kou kino, ma ka lima paha, ka wāwae, a i ʻole ka ʻōpū? He mea maʻamau ka makaʻu iki ʻana i kou ʻike ʻana i ia ʻano puʻupuʻu. Akā, ʻaʻole weliweli nā puʻupuʻu a pau. Eia nō naʻe, i kekahi manawa aia kahi manawa liʻiliʻi e hiki ai ke lilo i ʻano puʻupuʻu kakaikahi i kapa ʻia ʻo 'Desmoid Tumor' a mākou e kamaʻilio nei i kēia lā. No laila i kēia lā e kamaʻilio mākou e pili ana i nā mea āpau ma ke ʻano maʻalahi loa, ma ke ʻano hiki iā ʻoe ke hoʻomaopopo.
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He aha ka Desmoid Tumor?
I ka ʻōlelo maʻalahi, he puʻupuʻu kēia, a he puʻupuʻu paha, i hana ʻia mai nā ʻiʻo o ko kākou kino. Akā, ʻaʻole kēia e like me nā puʻupuʻu momona (Lipoma) a kākou e ʻike mau ai ma lalo o ka ʻili. Hoʻokumu ʻia kēia mau puʻupuʻu i loko o nā ʻiʻo fibrous o ko kākou kino. I ka pololei, hoʻokumu ʻia lākou i loko o nā ʻiʻo ikaika e like me nā tendon e hoʻopili ai i ko kākou mau ʻiʻo i ko kākou mau iwi a me nā ligaments e hoʻopili ai i ko kākou mau iwi kekahi i kekahi. Loaʻa ka inoa "Desmoid" mai kahi huaʻōlelo Helene i manaʻo ʻia "e like me ke kāʻei."
ʻO ka nīnau nui āu e nīnau nei iā ʻoe iho i kēia manawa, "He maʻi kanesa kēia?" Hoʻokaʻawale pinepine ʻia nā ʻōpū desmoid he benign no ka mea ʻaʻole lākou e laha (metastasize) mai kekahi ʻāpana o ke kino i kekahi e like me nā maʻi kanesa maʻamau.
Akā ma ʻaneʻi pono kākou e hoʻomaopopo i kahi mea nui loa. ʻOiai ʻaʻole e pālahalaha kēia mau puʻupuʻu, i kekahi manawa hiki iā lākou ke ulu wikiwiki loa (ʻino) . Ke hana ʻia kēlā, hiki i ka puʻupuʻu ke ulu a hōʻino i nā ʻiʻo olakino, nā aʻalolo, a me nā kīʻaha koko a puni ka puʻupuʻu. Ma muli o kēia ʻano, ma kekahi mau ʻano hana lākou e like me ke kanesa. ʻO ia ke kumu e pono ai mākou e hopohopo e pili ana i kēia.
He mea kākaʻikahi loa kēia. Loaʻa wale lākou i 2 a 4 mau hihia no kēlā me kēia miliona ma ka honua holoʻokoʻa. Hiki iā lākou ke loaʻa i kēlā me kēia makahiki, i loko o kekahi, akā ʻoi aku ka maʻamau i nā wahine i ko lākou mau makahiki 30.
He aha nā kumu e hiki mai ai kēia mau mea?
ʻOiai he paʻakikī ke ʻōlelo pololei i ke kumu, ua ʻike ʻia he nui ka pilikia o ka hoʻomohala ʻana i kēia mau mea i kekahi mau hihia.
- Nā kūlana hoʻoilina: ʻO ka poʻe me ka Familial Adenomatous Polyposis (FAP), kahi kūlana hoʻoilina e hoʻoulu ai i ka maʻi ʻaʻai colon, ʻoi aku ka nui o ka loaʻa ʻana o nā ʻōpū desmoid.
- Hāpai keiki: Ua manaʻoʻiʻo ʻia ʻo ka hormone 'estrogen', ka mea e hoʻonui ai i ke kino i ka wā hāpai keiki, pili pū kekahi.
- Nā ʻeha koʻikoʻi i ke kino: I kekahi manawa hiki ke ulu aʻe kahi puʻupuʻu e like me kēia ma hope o ke ʻoki ʻana a i ʻole ma kahi o kahi ʻeha koʻikoʻi.
He aha nā hōʻailona o kahi puʻupuʻu Desmoid?
Aia nā hōʻailona o kēia ma kahi o ke kino i loaʻa ai ka puʻupuʻu. I kekahi manawa hiki ke loaʻa me ka ʻole o nā hōʻailona. E nānā kākou pehea e ʻokoʻa ai nā hōʻailona nui.
| Kahi o ka puʻupuʻu | Nā hōʻailona hiki ke loaʻa |
|---|---|
| Kokoke i ka ʻili (nā lima, nā wāwae, ka ʻāʻī, ke poʻo) | He puʻu i ʻeha ʻole a ʻeha iki paha a hiki ke hoʻopā ʻia ma ka lima. |
| I loko o ka ʻōpū ) | Hiki i kēia mau mea ke ulu wikiwiki aʻe. ʻO ke kaomi ma luna o nā kīʻaha koko a me nā aʻalolo i loko o ka ʻōpū hiki ke hoʻoulu i ka ʻeha nui, ka mae ʻana o ka ʻōpū, ka ʻōʻō ʻana, a me ka nalowale o ka hoʻohana ʻana o nā lālā . I kekahi manawa, hiki ke loaʻa nā kūlana koʻikoʻi e like me ka poloka ʻana o ka ʻōpū a me ke kahe ʻana o ke koko i ka rectal. |
Pehea ʻoe e ʻike pono ai inā he Desmoid Tumor kēia?
Inā he puʻupuʻu kou, e hana kāu kauka i kekahi mau hoʻokolohua e hoʻoholo pono ai i ke ʻano o ia mea.
1. Ke nānā ʻana i ka ultrasound: Hoʻohana kēia i nā nalu kani alapine kiʻekiʻe e nānā i loko o ka puʻupuʻu. Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā paʻa ka puʻupuʻu a piha paha i ka wai.
2. Nā kiʻi ʻē aʻe: Kōkua kēia i ka ʻike inā pili ka puʻupuʻu me nā ʻiʻo a puni a inā hiki ke wehe palekana ʻia me ke ʻoki ʻana.
- MRI scan (Magnetic Resonance Imaging): Hoʻohana i kahi kahua magnetic ikaika e lawe i nā kiʻi maopopo a kikoʻī loa.
- CT scan (Computerized Tomography): Hoʻohui ʻia kekahi mau kukuna X e hana i kahi kiʻi piha o ka puʻupuʻu.
3. Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi a paʻa loa . Wehe ʻia kahi ʻāpana liʻiliʻi o ka puʻupuʻu, a i ʻole ka puʻupuʻu holoʻokoʻa, a nānā ʻia ma lalo o kahi microscope. ʻO kēia wale nō ka hoʻāʻo e hiki ke haʻi iā ʻoe 100% inā he puʻupuʻu desmoid a i ʻole kekahi mea ʻē aʻe.
Pehea e mālama ʻia ai?
Inā hōʻoia ka biopsy he puʻupuʻu desmoid ia, e koho kāu kauka i ka lāʻau kūpono loa nāu. Hoʻoholo ʻia ka lāʻau e nā kumu he nui, me ka nui o ka puʻupuʻu, kona wahi, pehea ka wikiwiki o kona ulu ʻana, a me kāu mau hōʻailona.
- E kali a nānā: Mai kahaha, ʻaʻole e nui aʻe kekahi mau puʻupuʻu me ka ʻole o kekahi lāʻau lapaʻau. Hiki i kekahi ke emi iho i ka hala ʻana o ka manawa. No laila, inā liʻiliʻi ka puʻupuʻu, ma waho o ka ʻōpū, a ʻaʻohe hōʻailona, hiki i kāu kauka ke hoʻoholo e nānā iā ia no kekahi manawa.
- ʻOki kino: Hana ʻia ke ʻoki kino i nā manawa a pau e hiki ai ke wehe loa i ka puʻupuʻu. Eia nō naʻe, hiki ke paʻakikī ke wehe i nā puʻupuʻu i loko o ka ʻōpū. Eia kekahi, ma hope o ke ʻoki kino, aia kahi manawa kūpono e ulu hou ai ka puʻupuʻu ma kahi hoʻokahi.
- Lapaʻau radiation: Hoʻohana wale ʻia kēia lāʻau lapaʻau, me ke ʻoki ʻana, a i ʻole me ka lāʻau lapaʻau. He kūpono ia no nā poʻe he nui. Eia nō naʻe, inā aia ka puʻupuʻu i loko o ka ʻōpū, ʻaʻole paha e hiki kēia no ka mea hiki i ka radiation ke hōʻino i nā ʻōpū koʻikoʻi kokoke.
- Lāʻau lapaʻau: ʻAʻohe lāʻau lapaʻau kūikawā no kēia mau puʻupuʻu. Eia nō naʻe, hoʻohana ʻia nā ʻano lāʻau like ʻole, me nā lāʻau anti-cancer, e hoʻēmi i nā puʻupuʻu a i ʻole e hoʻōki iā lākou mai ka ulu ʻana.
- Nā lāʻau lapaʻau hou ʻē aʻe:
- ʻO ka hoʻopau ʻana o ke alapine radio: Hoʻokomo ʻia nā mea like me ke nila i loko o ka puʻupuʻu a hoʻohana ʻia nā nalu lekiō e hoʻoulu i ka wela, e luku ana i ka puʻupuʻu.
- Cryoablation: Hoʻohana ʻia kahi probe e hoʻopaʻa a luku i ka ʻiʻo tumor.
ʻO ka mea nui loa, na kāu hui lapaʻau e hoʻoholo i kahi o kēia mau lāʻau lapaʻau i kūpono loa iā ʻoe. No laila, mai kānalua e kūkākūkā i kekahi mau nīnau a hopohopo paha āu e loaʻa ai me lākou.
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- He ʻano puʻupuʻu laha ʻole nā puʻupuʻu desmoid. ʻAʻole lākou e laha ma ke kino e like me ke kanesa. Eia nō naʻe, hiki iā lākou ke ulu koke a hōʻino i nā ʻiʻo a puni.
- Inā ʻike ʻoe i kahi puʻupuʻu hou, puʻupuʻu, a pehu paha ma kekahi wahi o kou kino , mai hopohopo a hoʻowahāwahā paha, akā e hōʻike pono i ke kauka.
- ʻO kahi biopsy wale nō ke hōʻoia inā he puʻupuʻu desmoid kēia.
- ʻOkoʻa ka lāʻau lapaʻau mai kēlā kanaka a kēia kanaka. Na kāu kauka e hoʻoholo i ka lāʻau lapaʻau maikaʻi loa nāu ma hope o ka nānā pono ʻana i kou kūlana.
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