Loaʻa iā ʻoe kahi maʻi i kapa ʻia ʻo `(Porphyria)`? A i ʻole he maʻi kēia i loaʻa i kekahi āu i ʻike ai? Ke ʻeha nei ʻoe i nā hōʻailona e like me ka ʻeha nui o ka ʻōpū, ka luaʻi ʻana, a me ka nāwaliwali o ke kino? A laila ua haʻi aku paha kāu kauka iā ʻoe e pili ana i kahi lāʻau pale i kapa ʻia ʻo `Givosiran`. He mea weliweli iki paha ka inoa i ka wā mua, akā mai hopohopo. I kēia lā, e kamaʻilio mākou e pili ana i kēia lāʻau lapaʻau ma ke ʻano maʻalahi hiki iā ʻoe ke hoʻomaopopo.
He aha maoli kēia lāʻau lapaʻau i kapa ʻia ʻo Givosiran?
I ka ʻōlelo maʻalahi, ʻo `Givosiran` kahi lāʻau pale i hāʻawi ʻia e mālama i kahi maʻi i kapa ʻia ʻo `(Porphyria)`. I loko o kēia maʻi, hōʻiliʻili kahi kemika ʻawaʻawa i kapa ʻia ʻo `(Porphyrins)` i loko o ko mākou kino. E like me ka wā e piha ai ka ʻōpala i loko o ko mākou hale, i ka wā e hōʻiliʻili ai kēia mau mea ʻawaʻawa i loko o ke kino, ʻike ʻoe i nā hōʻailona koʻikoʻi e like me ka ʻeha nui o ka ʻōpū, ka luaʻi ʻana, a me ka nalowale ʻana o nā lālā. I kēia manawa, ʻo ka hana a kēia lāʻau pale `Givosiran`, ʻo ia ka hōʻemi ʻana i ka hoʻokumu ʻia ʻana o kēlā mau `(Porphyrins)` ʻawaʻawa i loko o ke kino. ʻO ia hoʻi, hana ia e like me ke kāohi ʻana i ka hoʻokumu ʻia ʻana o nā ʻōpala. Ke emi ka nui o kēia mau mea ʻawaʻawa, emi nui nā hōʻailona āu e ʻike ai.
Loaʻa pinepine kēia lāʻau lapaʻau ma lalo o ka inoa inoa ʻo 'GIVLAARI'. Eia kekahi, hiki i nā kauka ke kuhikuhi iā ia no nā maʻi ʻē aʻe. Mai hopohopo no ia mea.
Nā mea āu e haʻi aku ai i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau
Pono kāu kauka e ʻike i kou mōʻaukala olakino piha ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau. No laila, inā loaʻa iā ʻoe kekahi o kēia mau mea, e hōʻoia e haʻi i kāu kauka
me ka hūnā ʻole i kekahi mea .
- Maʻi puʻupaʻa : Inā he mau pilikia puʻupaʻa kou.
- Maʻi akepaʻa : Inā loaʻa iā ʻoe kekahi maʻi akepaʻa.
- Nā Allergies : Inā loaʻa iā ʻoe kekahi mau allergies (allergies) ʻaʻole wale i kēia lāʻau lapaʻau, akā i kekahi lāʻau lapaʻau ʻē aʻe, meaʻai, a i ʻole kala, e ʻoluʻolu e haʻi mai iā mākou e pili ana.
- Hāpai keiki : Inā hāpai ʻoe a i ʻole e kali ana i kahi pēpē.
- Inā he makuahine hānai waiū ʻoe: Inā ʻoe e hānai waiū ana i kāu pēpē.
He mea nui loa ka hāʻawi pololei ʻana i kēia ʻike no kou palekana.
Pehea ʻoe e hoʻohana ai i kēia lāʻau lapaʻau?
ʻAʻole kēia he lāʻau lapaʻau hiki iā ʻoe ke lawe i ka home. ʻO 'Givosiran'
kahi inikini i hāʻawi ʻia ma lalo o ka ʻili .Hāʻawi ʻia kēia iā ʻoe e ke kauka a i ʻole ke kahu maʻi i aʻo ʻia ma ka haukapila a i ʻole ke keʻena lapaʻau. No laila, ʻaʻole pono ʻoe e hopohopo e pili ana i ka nui o ka lāʻau a pehea e lawe ai.
Hiki ke hāʻawi ʻia kēia lāʻau lapaʻau i nā keiki?
ʻAe, i kekahi manawa hāʻawi ʻia kēia lāʻau lapaʻau i nā keiki. Akā, pono ia i ka mālama kūikawā. Inā makemake kāu keiki i kēia lāʻau lapaʻau, e kamaʻilio me ke kauka keiki e pili ana i ia mea a e ʻike i nā kikoʻī.
He aha ka mea e hana ai inā ʻoe e lawe i ka overdose?
Hāʻawi ʻia kēia ma kahi haukapila, no laila ua haʻahaʻa loa ka manawa e hiki ai kēia. Eia nō naʻe, inā manaʻo ʻoe ua overdose ʻoe, e kelepona koke aku
i ke Kikowaena ʻIke Poisons National ma ka Halemai Lahui ʻo Colombo . A i ʻole e hele
i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa.
ʻO ka mea nui loa, ua kuhikuhi ʻia kēia lāʻau lapaʻau nou wale nō. Mai kaʻana like i kēia lāʻau lapaʻau me kekahi.
He aha inā e hala wau i ka lā pale?
He mea nui loa ka loaʻa ʻana o kāu mau lāʻau pale i ka manawa kūpono no kēia lāʻau lapaʻau. No laila, mai poina i nā lā o kāu keʻena lapaʻau. Inā ʻaʻole hiki iā ʻoe ke hele i kāu lā i hoʻonohonoho ʻia ma muli o kahi pilikia, e ʻoluʻolu e kelepona i kāu kauka a keʻena lapaʻau paha ma mua a e hoʻomaopopo iā lākou.
Nā mea ʻē aʻe e launa pū me kēia lāʻau lapaʻau
Hiki i kekahi mau lāʻau lapaʻau ke hoʻopilikia i ka wā e lawe ʻia ai me 'Givosiran'. No laila, pono ʻoe e haʻi i kāu kauka
e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei. Hoʻokomo pū kēia i nā lāʻau lapaʻau no nā maʻi ʻē aʻe, nā huaora, nā lāʻau lapaʻau kuʻuna, a me nā mea kanu.
ʻOi aku, mai lawe pū me kēia mau lāʻau lapaʻau ʻo 'Givosiran': Hiki nō hoʻi ke loaʻa nā pilikia me kēia mau mea:- Caffeine - loaʻa i loko o ke kī a me ke kofe
- ʻO Dextromethorphan (aia i loko o kekahi mau syrups cough)
ʻAʻole i piha kēia papa inoa. No laila, ʻoi aku ka maikaʻi o ka haʻi ʻana i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe ai. Eia kekahi, e haʻi iā lākou inā ʻoe e puhipaka ana, inu waiʻona, a hoʻohana paha i nā lāʻau ʻē aʻe.
Nā mea e noʻonoʻo ai i ka wā o ka mālama ʻana
E nānā pono kāu kauka iā ʻoe i kou wā e loaʻa ana i kēia lāʻau pale. Hiki paha iā lākou ke kauoha i
nā hoʻāʻo koko e ʻike ai pehea ka hopena o ka lāʻau i kou kino.
He aha nā hopena ʻaoʻao e hiki mai ana?
E like me nā lāʻau lapaʻau āpau, hiki i ka `Givosiran` ke hana i kekahi mau hopena ʻaoʻao. Eia naʻe, ʻaʻole loaʻa i nā kānaka a pau. He koʻikoʻi kekahi, a he mea maʻamau kekahi. He mea nui e makaʻala i kēia mau mea.
Nā hopena ʻaoʻao o ka lāʻau pale Givosiran🚨 Inā ʻike ʻoe i kēia mau hōʻailona, e haʻi koke i kāu kauka🙂 ʻAʻole lākou he mea koʻikoʻi, akā inā hoʻomau lākou, pono ʻoe e haʻi i
kāu kauka. | Nā hopena alerika | ʻŌhūhū ʻili, maneʻo, pehu o ka maka, nā lehelehe, ke alelo a i ʻole ka puʻu. |
| ʻEha puʻupaʻa | Ka emi ʻana o ka mimi i hoʻopuka ʻia, ka pehu ʻana o nā kuʻekuʻe wāwae, nā lima, a i ʻole nā wāwae. |
| ʻEha o ke akepaʻa | ʻEha ma ka ʻaoʻao ʻākau o luna o ka ʻōpū, nalowale ka makemake e ʻai, nausea, ʻōpala māmā, mimi melemele ʻeleʻele a ʻeleʻele paha, melemele o nā maka a i ʻole ka ʻili, luhi ʻē. |
| ʻO ka maʻi pancreatitis | ʻEha nui o ka ʻōpū e like me ke kua e pālahalaha ana, ʻeha e ʻoi aku ka ʻino ma hope o ka ʻai ʻana a i ʻole ke hoʻopā ʻia ka ʻōpū, kuni, nausea, a me ka luaʻi. |
| Luhi | Manaʻo o ke ola ʻole. |
| Ka luaʻi | Manaʻo e luaʻi ana. |
| ʻEha ma kahi i hoʻokomo ʻia | ʻUlaʻula, ʻeha, a pehu iki paha ma kahi i inikini ʻia. |
Inā loaʻa iā ʻoe kekahi mau hōʻailona ʻē aʻe i ʻōlelo ʻole ʻia ma kēia papa inoa, e haʻi i kāu kauka e pili ana iā lākou.
Leka Lawe-Home
- ʻO ke ʻano o "Givosiran" ʻo ia hoʻi ʻo " Porphyria"He lāʻau pale kūikawā i hāʻawi ʻia ma ka haukapila a i ʻole ke keʻena lapaʻau e mālama ai i kahi maʻi.
- Ma mua o ka hoʻomaka ʻana i ka lāʻau lapaʻau, e hōʻoia e haʻi i kāu kauka e pili ana i nā maʻi ʻē aʻe āu e loaʻa nei, nā lāʻau lapaʻau āu e lawe nei, nā maʻi allergies, a inā paha ʻoe e hāpai ana.
- Inā loaʻa iā ʻoe kekahi mau hopena ʻino e like me ka ʻeha nui o ka ʻōpū , ka melemele o nā maka, a i ʻole ka emi ʻana o ka mimi ʻana , e ʻimi koke i ke kōkua lapaʻau me ka hoʻokaʻulua ʻole.
- Mai poina i kāu mau manawa i hoʻonohonoho ʻia no ke keʻena lapaʻau. He mea nui loa kēia no ka holomua o ka lāʻau lapaʻau.
- Inā he mau nīnau kāu, hopohopo, a makaʻu paha e pili ana i kēia lāʻau lapaʻau, e kamaʻilio ākea me kāu kauka e pili ana.
ʻO Givosiran, GIVLAARI, Porphyria, Porphyria, lāʻau pale, inikini Givosiran sinhala, mālama ʻana iā Porphyria sinhala, nā hopena ʻaoʻao, akepaʻa, nā puʻupaʻa, ʻeha ʻōpū
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