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Ke ʻeha nui nei kāu keiki i ka ʻōpū? He Hemolytic Uremic Syndrome (HUS) paha ia!

Ke ʻeha nui nei kāu keiki i ka ʻōpū? He Hemolytic Uremic Syndrome (HUS) paha ia!

Ua loaʻa anei i kāu keiki liʻiliʻi ka maʻi diarrhea me ka ʻeha ʻōpū no kekahi mau lā? Hiki paha iā ʻoe ke ʻike i ke koko i loko. He mea maʻamau iā ʻoe, ma ke ʻano he makua, ke hopohopo nui i ka wā e hana ʻia ai kēlā. Ke loaʻa iā ʻoe nā hōʻailona e like me kēia, hiki ke ʻoi aku ma mua o ka ʻeha ʻōpū maʻalahi. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi hiki ke koʻikoʻi, akā hiki ke mālama ʻia inā ʻike mua ʻia. ʻO ia hoʻi (Hemolytic Uremic Syndrome) , a i ʻole (HUS) no ka pōkole.

He aha ka Hemolytic Uremic Syndrome (HUS)? E hoʻomaopopo maʻalahi kākou.

ʻAe, e nānā kākou i kēia (HUS). I ka ʻōlelo maʻalahi, he ʻano ia kahi e ālai ʻia ai nā kīʻaha koko liʻiliʻi i loko o ko kākou mau puʻupaʻa . E noʻonoʻo e like me ka paipu wai e ālai ʻia ana a pau ke kahe ʻana o ka wai. ʻO kēia ālai ʻana ke kumu o ʻekolu mau mea nui e hana ʻia:

1. Ua luku ʻia kou mau hunaola koko ʻulaʻula: I ka lāʻau lapaʻau, ua kapa ʻia kēia he anemia hemolytic . ʻO nā hunaola koko ʻulaʻula ka mea e lawe i ka oxygen ma o ko kākou kino. No laila, i ka wā e luku ʻia ai lākou, e emi ana ka nui o ka oxygen e pono ai ke kino.

2. Ke emi nei ka helu o nā platelets i loko o ke koko: Ua kapa ʻia kēia ʻano he thrombocytopenia . He mau ʻāpana liʻiliʻi nā platelets e kōkua i ko mākou kāpili ʻana i ke koko i ka wā e kahe ai ke koko. Ke emi kēia mau mea, lilo ia i mea paʻakikī ke hoʻōki i ke kahe ʻana o ke koko, a hiki ke loaʻa nā palapū ma ke kino holoʻokoʻa.

3. Ka hōʻino ʻana o nā puʻupaʻa: ʻO kēia ka mea weliweli loa. Ke hana pono ʻole nā ​​puʻupaʻa, ʻaʻole hiki iā lākou ke wehe i nā huahana ʻōpala e hōʻiliʻili ana i loko o ke kino. Ua kapa ʻia hoʻi kēia ʻo (Acute Kidney Injury - AKI) .

ʻOiai hiki i ka HUS ke hoʻopilikia i kekahi, ʻo ka hapa nui o ia mea i hoʻoulu ʻia e kahi maʻi bacteria , ʻoiai ʻo Escherichia coli , i ʻike nui ʻia ʻo E. coli . ʻO kēia bacteria ke kumu o ka maʻi diarrhea, ʻoiai ka maʻi diarrhea koko. Eia nō naʻe, ʻo ka syndrome kahi hōʻiliʻili o nā hōʻailona, ​​​​a hiki nō hoʻi ke loaʻa ka HUS ma muli o nā kumu ʻē aʻe ma mua o E. coli.

ʻAʻole hiki i kēia kūlana (HUS) ke hoʻopilikia wale i nā puʻupaʻa, akā i kekahi manawa i nā ʻāpana ʻē aʻe e like me ka puʻuwai a me ka lolo. Eia naʻe, ʻo ka hapa nui o ia mea e hoʻopilikia ai i nā puʻupaʻa.

ʻO ka mea nui loa: Inā loaʻa iā ʻoe a i ʻole kāu keiki ka maʻi kahe koko a i ʻole he maʻi kahe no nā lā ʻekolu a ʻoi aku, e ʻike pono i ke kauka. Inā ʻaʻole mālama ʻia, hiki i ka HUS ke lilo i mea koʻikoʻi a hoʻoweliweli i ke ola.

Aia kekahi mau ʻano HUS like ʻole?

ʻAe, aia kekahi mau ʻano nui o (HUS). E aʻo iki kākou e pili ana iā lākou:

1. "Maʻamau" (HUS): ʻO kēia ke ʻano maʻamau . Hoʻokumu pinepine ʻia e kahi maʻi bacteria, ʻoiai ʻo E. coli, e hoʻopilikia ana i ko mākou ʻōpū liʻiliʻi a me ka colon.

2. "ʻAno ʻole" (HUS) (aHUS): He mea kākaʻikahi iki kēia.ʻO ka pinepine, ʻo kēia ma muli o nā kumu genetic, ʻo ia hoʻi, ua hoʻoilina ʻia mai nā mākua a i nā keiki.

3. "Lua" (HUS): Loaʻa kēia ʻano ma ka pili ʻana me nā kūlana olakino ʻē aʻe. No ka laʻana, hiki ke hana ʻia e kekahi mau lāʻau lapaʻau, nā maʻi ʻē aʻe, a i ʻole ka hāpai ʻana.

E aʻo iki kākou e pili ana i ka "Atypical" (HUS) (aHUS)

He kūlana laha ʻole ka (aHUS). Hiki iā ia ke hana i nā hōʻailona like me ka mea ma mua:

  • Ua hoʻemi ʻia nā pae o nā hunaola koko ʻulaʻula.
  • Ua emi ka helu platelet.
  • Ka hāʻule koke ʻana o ka puʻupaʻa (ka hāʻule koke ʻana o ka puʻupaʻa) .
  • Ke koko kiʻekiʻe (hypertension) a i ʻole ka hiki ʻole ke kaohi i ke koko.

ʻO kēia kūlana (aHUS) he maʻi hoʻoilina maʻamau. ʻO ia hoʻi, ua hana ʻia e kekahi mau loli (nā mutations) i loko o kā mākou mau genes. Eia nō naʻe, inā paha aia kēia kūlana hoʻoilina, ua hoʻoulu ʻia e kekahi maʻi, maʻi, a i ʻole ke kumu o ke kaiapuni.

Pehea ka maʻamau o (HUS)?

Ma waena o 5% a me 15% o ka poʻe i loaʻa i ka maʻi diarrhea i hoʻokumu ʻia e ka bacteria (E. coli) e loaʻa iā lākou ka HUS . ʻO ke ʻano i kapa ʻia ʻo (aHUS) he mea kākaʻikahi loa ia. Loaʻa ia ma kahi o hoʻokahi i loko o hoʻokahi miliona kānaka.

He aha nā hōʻailona nui o (HUS)?

He mea nui loa e ʻike ʻoe i kēia mau hōʻailona.

Nā hōʻailona mua i ʻike ʻia:

  • Ka maʻi kahe: Hele pinepine ʻia me ke koko.
  • ʻEha ʻōpū.
  • Ka luaʻi a me ka luaʻi.
  • ʻEha poʻo .
  • ʻĀnuenue a me ke kuni.

Nā hiʻohiʻona ʻē aʻe i ʻike ʻia:

  • ʻEha maʻalahi.
  • ʻIli keʻokeʻo (keʻokeʻo): Hiki ke keʻokeʻo ka ʻaoʻao o loko o ka ihu a me loko o ka waha.
  • Ka huikau.
  • Hoʻopaʻa ʻana.
  • Nā kūlana e like me ka hahau ʻana.
  • Ka wikiwiki o ka puʻuwai (arrhythmia).

Inā lilo ke kūlana o (HUS) i mea koʻikoʻi, hiki i nā hunaola koko ʻulaʻula i luku ʻia ke hana i nā ʻōpū koko a hōʻino i nā ʻōpū e like me nā puʻupaʻa. A laila ʻaʻole hiki i nā puʻupaʻa ke kānana pono i nā huahana ʻōpala. ʻO kēia ka mea a mākou e kapa nei (Acute Kidney Injury - AKI) . Eia nā hōʻailona o ia mea:

  • Ke koko i loko o ka mimi (hematuria).
  • Hoʻonui ʻia nā pae o nā mea ʻawahia i loko o ke koko: Hiki i kēia ke hōʻeha a me ka manaʻo o ka maʻi.
  • Ke koko kiʻekiʻe.
  • Ka paʻakikī o ka hanu ʻana (dyspnea).
  • Edema: Hiki ke pehu, ʻoiai ma nā wāwae a me nā kuʻekuʻe wāwae.
  • Ka emi ʻana o ka mimi i hoʻopuka ʻia (oliguria).

He aha nā kumu nui o (HUS)?

ʻO ka hapa nui o nā hihia o HUS i hoʻokumu ʻia e kekahi mau ʻano bacteria E. coli. Hoʻopuka kēia mau bacteria i kahi toxin i kapa ʻia ʻo Shiga toxin . Hoʻopōʻino kēia toxin i ka uhi o ko mākou ʻōpū liʻiliʻi a hoʻoulu i ka maʻi diarrhea. Komo pū kēia toxin i ke kahe koko, e luku ana i nā hunaola koko ʻulaʻula a hōʻino i nā puʻupaʻa.

ʻOi aku ka nui o kou loaʻa ʻana i kahi maʻi E. coli mai:

  • ʻAiʻo i moʻa ʻole ʻia: ʻoi aku ka pipi, ka pipi wili ʻia.
  • Waiū i hoʻomaʻemaʻe ʻole ʻia a me nā mea inu huaʻai: ʻO ka Pasteurization kahi hana hoʻomehana mālie e pepehi ai i nā mea ʻino e like me ka bacteria.
  • Nā huaʻai a me nā mea kanu lepo i holoi ʻole ʻia.

Ua kapa ʻia kēia mau ʻano E. coli e hana ana i nā mea ʻawahia ʻo Shiga toxin-producing E. coli (STEC) . ʻO ke ʻano STEC maʻamau ma ʻAmelika ʻĀkau ʻo E. coli O157:H7 .

ʻAʻole pinepine loa, hiki i kekahi mau lāʻau lapaʻau a me nā mea ke hana i ka "secondary (HUS)". Nā Laʻana:

  • Nā lāʻau lapaʻau anti-cancer (nā lāʻau Chemotherapy): e like me (bleomycin), (cisplatin), (gemcitabine).
  • Nā lāʻau lapaʻau immunosuppressant: e like me (cyclosporine), (tacrolimus).
  • Quinine: He lāʻau lapaʻau no ka maʻi malaria.
  • Kekahi mau lāʻau lapaʻau : (oxymorphone), (ecstasy), (cocaine).

He mea laha anei ka (HUS)?

ʻAʻole, ʻaʻole laha ka HUS.

Eia nō naʻe, hiki ke laha nā bacteria E. coli. Hiki ke laha kēia bacteria ma o ka meaʻai a mea inu paha i haumia ʻia, a i ʻole ma ke komo ʻana i nā ʻōpala o ke kanaka a holoholona paha me ka maʻi diarrhea i loaʻa iā E. coli. No laila, he mea nui e makaʻala loa i ka maʻemaʻe.

ʻO wai ka mea e ulu nui ai (HUS)?

ʻOiai hiki i kekahi ke hoʻomohala i ka HUS, ʻoi aku ka nui o ka pilikia o kēia poʻe:

  • No nā keiki liʻiliʻi ma lalo o 5 mau makahiki.
  • No ka poʻe me ka ʻōnaehana pale kino nāwaliwali (immunocompromised).
  • Inā ua loaʻa i kekahi o kou ʻohana ʻo HUS ma mua (ʻoi aku hoʻi ʻo aHUS).
  • Inā loaʻa iā ʻoe kahi maʻi E. coli: ʻOi aku hoʻi mai nā mea e like me ka ʻiʻo i moʻa pono ʻole ʻia a me ka waiū i hoʻomaʻemaʻe ʻole ʻia.
  • Hoʻopili pololei me kahi mea i loaʻa i ka maʻi diarrhea i hoʻokumu ʻia e (E. coli).

Pehea ʻoe e ʻike ai inā loaʻa iā ʻoe (HUS)? (Diagnosis)

Ke ʻike ʻoe i ke kauka, e hana ʻo ia i kēia mau mea:

  • E nīnau e pili ana i kou mōʻaukala olakino .
  • E nīnau e pili ana i ka mōʻaukala olakino o kou ʻohana .
  • Hana ʻia kahi hoʻokolokolo kino .

Inā hāpai kēia mau mea i ka kānalua o kahi kūlana i kapa ʻia ʻo (HUS), e kauoha ke kauka i kekahi mau hoʻokolohua hou aʻe.

He aha ke ʻano o nā hoʻokolohua e hana ʻia?

  • Urinalysis: Lawe ʻia kahi laʻana o kāu mimi a nānā ʻia no ka protein a i ʻole ke koko.
  • Hoʻāʻo koko: Lawe ʻia kahi hāpana koko e nānā i nā mea e like me ka helu ʻana o nā cell koko ʻulaʻula, nā pae platelet, a me ka hana maikaʻi o kou mau puʻupaʻa a me ke akepaʻa.
  • Hoʻāʻo ʻōpala: Lawe ʻia kahi hāpana ʻōpala a nānā ʻia no ke alo o nā bacteria e hoʻoulu ai i ka HUS, e like me E. coli O157.
  • Hoʻāʻo ʻana i ka genetics: I kekahi manawa, hiki ke hoʻouna ʻia kahi hāpana o kou koko no ka hoʻāʻo ʻana i ka genetics. Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā he maʻi genetic kou e like me aHUS a he aha ka lāʻau lapaʻau maikaʻi loa iā ʻoe.
  • ʻO ka biopsy puʻupaʻa: ʻO kēia ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka puʻupaʻa a nānā iā ia ma lalo o kahi microscope e ʻike i ka nui o ka pōʻino i hana ʻia i nā puʻupaʻa a me ke kumu. ʻAʻole pono nā kānaka a pau i kēia.

Pehea e hiki ai i nā hoʻokolohua ke hōʻoia he HUS kāu?

  • Mai nā hoʻāʻo mimi: Inā he koko a protein paha i loko o ka mimi.
  • Nā hoʻāʻo koko: Inā haʻahaʻa nā pae o nā sela koko ʻulaʻula a me nā platelet, a inā paha ua kiʻekiʻe nā waiwai e hōʻike ana i ka hana o nā puʻupaʻa (e like me ka creatinine).
  • Nā hoʻāʻo ʻana i ka ʻōpala: Inā loaʻa nā bacteria e like me (E. coli O157).
  • ʻO ka biopsy puʻupaʻa: Hiki ke ʻike ʻia nā hōʻino kikoʻī i nā puʻupaʻa.

Pehea e mālama ʻia ai (HUS)?

Inā ua ʻike ʻia ʻoe me HUS, pono ʻoe e lawe ʻia i ka haukapila a mālama ʻia. ʻO nā koho lapaʻau e komo pū ana:

  • Nā wai intravenous (IV) a me/a i ʻole ka hānai ʻana i ka paipu (ʻai enteral): Kōkua kēia i ka pale ʻana i ka maloʻo ʻana o ka wai a hāʻawi i ka meaʻai e pono ai.
  • Nā lāʻau lapaʻau:
  • Hoʻāʻo lākou e hōʻemi i ka hōʻino ʻia o nā puʻupaʻa ma ka hāʻawi ʻana i nā lāʻau hoʻohaʻahaʻa koko (nā lāʻau antihypertensive) .
  • Hiki ke hāʻawi ʻia i nā kānaka me aHUS nā lāʻau lapaʻau kūikawā e like me eculizumab a i ʻole ravulizumab . Ma mua o ka hoʻomaka ʻana i kēia mau lāʻau lapaʻau, he mea nui e loaʻa ka lāʻau pale no nā maʻi meningococcal a me pneumococcal , no ka mea, hoʻonui kēia mau lāʻau i ka pilikia o ka loaʻa ʻana o kēlā mau maʻi.
  • Pono paha ʻoe e lawe i nā antibiotics no ka liʻiliʻi he ʻelua pule.
  • Nā hoʻoili koko: He mea nui loa ka hāʻawi ʻana i nā hunaola koko ʻulaʻula a me nā platelet i kekahi me (HUS). Hoʻēmi nā hunaola koko ʻulaʻula i nā hōʻailona o ka anemia, e like me ka hanu pōkole a me ka puʻuwai wikiwiki. Kōkua nā platelets i ke kāpili ʻana o ke koko, e hōʻemi ana i ke kahe ʻana o ke koko a me ka palapū.

Inā ua hōʻino nui ʻia nā puʻupaʻa, pono paha ka dialysis e hoʻomaʻemaʻe i ke koko a hiki i ka hoʻōla ʻana o nā puʻupaʻa. Inā hāʻule loa puʻupaʻa ma muli o HUS, pono paha kahi hoʻoili puʻupaʻa .

Hiki ke ho'ōla loa ʻia ka HUS?

ʻAe, nui ka poʻe e ho'ōla mai ka HUS me ka ʻole o ka hōʻeha mau loa ʻana i ko lākou olakino.

Eia nō naʻe, hiki i kekahi poʻe, ʻoiai nā kamaliʻi ʻōpio, ke loaʻa i ka maʻi puʻupaʻa mau loa (CKD) i 20% a 50%. Hiki i ka maʻi puʻupaʻa hope loa (ESK) ke ulu i 3% a 5%. Hōʻike nā haʻawina e hoʻopilikia ana ʻo CKD i kahi 45% o nā pākeke.

ʻOi aku ma mua o 85% o ka poʻe i loaʻa i ka HUS e hoʻōla piha i kā lākou hana puʻupaʻa. Eia nō naʻe, inā e hoʻōla piha lākou, aia kahi manawa liʻiliʻi e loaʻa ai iā lākou ke koko kiʻekiʻe a i ʻole nā ​​​​pilikia puʻupaʻa ʻē aʻe i ka wā e hiki mai ana.

Hiki ke pale ʻia ka HUS?

Eia kekahi mau mea hiki iā ʻoe ke hana e kōkua i ka pale ʻana i ka maʻi E. coli, kahi kumu nui o HUS. He mea nui loa kēia mau mea no ʻoe a me kou ʻohana:

  • E pale i ka ʻauʻau ʻana i nā wahi lepo (nā loko, nā muliwai), ʻoiai inā manaʻo ʻoe he kiʻekiʻe ka nui o nā bacteria i loko o ka wai.
  • Inā loaʻa iā ʻoe ka maʻi diarrhea, mai ʻauʻau.
  • E hōʻalo i ka inu ʻana i nā mea inu maka ʻole i hoʻomaʻemaʻe ʻia (waiū, wai huaʻai).
  • E hoʻomaʻemaʻe mau i nā lako kīhini (nā pahi, nā ʻō, nā puna) a me nā wahi e hoʻomākaukau ai i ka meaʻai (nā pākaukau, nā papa ʻokiʻoki, nā kīʻaha).
  • E hoʻomoʻa maikaʻi i nā hua manu a me nā ʻiʻo i wili ʻia a hiki i ka mahana o loko o 71 degere Celsius (160 degere Fahrenheit), a me ka moa i ka mahana o loko o 74 degere Celsius (165 degere Fahrenheit).
  • I ka wā e hoʻoheheʻe ai i ka ʻiʻo, e waiho i loko o ka microwave a i ʻole ka pahu hau. Mai hoʻoheheʻe iā ia ma kahi e hoʻomākaukau ai i ka meaʻai a i ʻole i loko o ka wai wela.
  • E hoʻokaʻawale i nā meaʻai maka a me nā meaʻai i moʻa ʻia.
  • E holoi pono i kou mau lima me ke kopa a me ka wai wela ma mua o ka ʻai ʻana, ma hope o ka hoʻohana ʻana i ka lua, ma hope o ka hoʻololi ʻana i nā diaper o nā keiki liʻiliʻi, a ma hope o ka hoʻopā ʻana i nā holoholona mahiʻai.

E noʻonoʻo wale, ma ka hahai ʻana i kēia mau ʻanuʻu maʻalahi, hiki iā ʻoe ke pale iā ʻoe iho mai kahi kūlana koʻikoʻi e like me kēia.

He aha kāu e manaʻo ai inā loaʻa iā ʻoe (HUS)?

Me ka ʻike kūpono a me ka mālama ʻana, hoʻōla piha ka hapa nui o ka poʻe me HUS me ka ʻole o ka hōʻino mau loa i ko lākou olakino. Eia nō naʻe, aia kahi pilikia o ka loaʻa ʻana o ke koko kiʻekiʻe a i ʻole nā ​​​​​​kūlana ʻē aʻe e hoʻopilikia ai i nā puʻupaʻa i ka wā e hiki mai ana.

ʻO nā hihia koʻikoʻi o HUS, ʻoiai inā pili lākou i nā ʻōpū ʻē aʻe, e like me ka lolo, hiki ke make inā ʻaʻole mālama ʻia.

He aha nā manawa kūpono e ola ai (HUS)?

Me ka ʻike kūpono a me ka mālama ʻana, ʻoi aku ma mua o 90% o ka poʻe e ola ana i ka HUS. No laila he mea nui e pale aku i ka hopohopo a e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona.

Pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe a i ʻole kāu keiki ka maʻi diarrhea nui, he mea nui loa e hoʻāʻo e hoʻomaʻū hou i kou kino.Hiki i nā mea inu hoʻomaʻemaʻe wai, e like me Jeevani, ke kōkua i ka hoʻololi ʻana i nā electrolytes i nalowale. Pono paha nā pēpē a me nā keiki liʻiliʻi e hāʻawi i ka waiū umauma a i ʻole ka waiū waiū. E nīnau i ke kauka e pili ana i ke ala maikaʻi loa e mālama ai i kāu keiki i ka wai.

Āhea wau e ʻike ai i ke kauka?

E ʻike koke i ke kauka inā loaʻa iā ʻoe kēia mau hōʻailona:

  • Ka maʻi kahe koko.
  • Ka maʻi kahe e mau ana ma mua o ʻekolu lā.
  • Pehu kino.
  • ʻIli e palaho maʻalahi.
  • Luhi nui.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

Hiki iā ʻoe ke nīnau i ke kauka i kēia mau nīnau:

  • Pehea ʻoe e hōʻoia ai inā loaʻa iaʻu ka Hemolytic Uremic Syndrome?
  • Pehea i loaʻa ai iaʻu ka Hemolytic Uremic Syndrome?
  • Inā ʻaʻohe oʻu Hemolytic Uremic Syndrome, he aha nā maʻi ʻē aʻe e loaʻa iaʻu?
  • He aha nā lāʻau lapaʻau āu e paipai nei?
  • E hōʻino mau ʻia anei koʻu mau puʻupaʻa?
  • E loaʻa anei iaʻu ke koko kiʻekiʻe a i ʻole nā ​​pilikia puʻupaʻa ʻē aʻe i ka wā e hiki mai ana?

He aha ka triad o ka Hemolytic Uremic Syndrome?

ʻO ka triad ka hui pū ʻana o ʻekolu mau hōʻailona nui e hōʻike ana i kahi maʻi.

ʻO ka Hemolytic Uremic Syndrome triad e komo pū ana me:

1. Ka hōʻino ʻana i kou mau hunaola koko ʻulaʻula (microangiopathic hemolytic anemia) .

2. Ka emi mālie ʻana o ka helu o nā platelets i loko o kou koko (thrombocytopenia) .

3. ʻEha puʻupaʻa koʻikoʻi .

Inā loaʻa iaʻu ka maʻi pākī, ʻo ia hoʻi he Hemolytic Uremic Syndrome koʻu?

ʻOiai he maʻi kahe kou, ʻaʻole ia he manaʻo he maʻi Hemolytic Uremic Syndrome kou. Eia nō naʻe, inā he maʻi kahe koko kou, a inā paha he koʻikoʻi kou maʻi kahe (a hiki i ka maʻi kahe wai a i ʻole e mau ana ma mua o ʻekolu lā), pono ʻoe e ʻike i ke kauka.

He aha ka ʻokoʻa ma waena o (Hemolytic Uremic Syndrome) a me (Thrombotic Thrombocytopenic Purpura - TTP)?

ʻO ka Hemolytic Uremic Syndrome (HUS) a me ka Thrombotic Thrombocytopenic Purpura (TTP) ʻelua mau kūlana like. I ka TTP, hana ʻia nā ʻōpū koko i loko o nā kīʻaha koko liʻiliʻi. ʻOiai ua hoʻohui pū nā kauka iā HUS a me TTP, ua manaʻo ʻia lākou he mau kūlana kaʻawale.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He manawa pōkole ka maʻi kahe, akā he ʻano ʻoluʻolu ʻole. Hoʻomaikaʻi pinepine ia i hoʻokahi a ʻelua paha lā. Eia nō naʻe, inā he maʻi kahe koko kou, a inā he maʻi kahe kou no nā lā ʻekolu a ʻoi aku, me ka luhi, ka maeʻele, a i ʻole ka emi ʻana o ka mimi ke hele ʻoe i ka lua, ua hiki i ka manawa e ʻike koke ai i ke kauka.

ʻO kahi maʻi i kapa ʻia ʻo Hemolytic Uremic Syndrome hiki ke hōʻino nui i kou mau puʻupaʻa a hoʻopilikia i nā kino ʻē aʻe.ʻO ka wikiwiki o kou loaʻa ʻana o ka lāʻau no kēia, ʻo ka emi ʻana o ka hiki ke hōʻino ʻia kou mau puʻupaʻa i ka wā lōʻihi. No laila, e makaʻala i nā hōʻailona, ​​e mālama i ka hoʻomaʻemaʻe maikaʻi, a e ʻimi i ke kōkua lapaʻau inā he mau hopohopo kāu. He mea nui loa kou olakino iā ʻoe!


ʻO ka maʻi Hemolytic Uremic, HUS, Maʻi Pūpū, Ka maʻi kahe, E. coli, Nā ʻulaʻula koko, Nā platelets, Ola kino o ke keiki

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ke ʻeha nui nei kāu keiki i ka ʻōpū? He Hemolytic Uremic Syndrome (HUS) paha ia!
Nā Maʻi Pūpū5 Iulai 2026

Ke ʻeha nui nei kāu keiki i ka ʻōpū? He Hemolytic Uremic Syndrome (HUS) paha ia!

Ua loaʻa anei i kāu keiki liʻiliʻi ka maʻi diarrhea me ka ʻeha ʻōpū no kekahi mau lā? Hiki paha iā ʻoe ke ʻike i ke koko i loko. He mea maʻamau iā ʻoe, ma ke ʻano he makua, ke hopohopo nui i ka wā e hana ʻia ai kēlā. Ke loaʻa iā ʻoe nā hōʻailona e like me kēia, hiki ke ʻoi aku ma mua o ka ʻeha ʻōpū maʻalahi. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi hiki ke koʻikoʻi, akā hiki ke mālama ʻia inā ʻike mua ʻia. ʻO ia hoʻi (Hemolytic Uremic Syndrome) , a i ʻole (HUS) no ka pōkole.

He aha ka Hemolytic Uremic Syndrome (HUS)? E hoʻomaopopo maʻalahi kākou.

ʻAe, e nānā kākou i kēia (HUS). I ka ʻōlelo maʻalahi, he ʻano ia kahi e ālai ʻia ai nā kīʻaha koko liʻiliʻi i loko o ko kākou mau puʻupaʻa . E noʻonoʻo e like me ka paipu wai e ālai ʻia ana a pau ke kahe ʻana o ka wai. ʻO kēia ālai ʻana ke kumu o ʻekolu mau mea nui e hana ʻia:

1. Ua luku ʻia kou mau hunaola koko ʻulaʻula: I ka lāʻau lapaʻau, ua kapa ʻia kēia he anemia hemolytic . ʻO nā hunaola koko ʻulaʻula ka mea e lawe i ka oxygen ma o ko kākou kino. No laila, i ka wā e luku ʻia ai lākou, e emi ana ka nui o ka oxygen e pono ai ke kino.

2. Ke emi nei ka helu o nā platelets i loko o ke koko: Ua kapa ʻia kēia ʻano he thrombocytopenia . He mau ʻāpana liʻiliʻi nā platelets e kōkua i ko mākou kāpili ʻana i ke koko i ka wā e kahe ai ke koko. Ke emi kēia mau mea, lilo ia i mea paʻakikī ke hoʻōki i ke kahe ʻana o ke koko, a hiki ke loaʻa nā palapū ma ke kino holoʻokoʻa.

3. Ka hōʻino ʻana o nā puʻupaʻa: ʻO kēia ka mea weliweli loa. Ke hana pono ʻole nā ​​puʻupaʻa, ʻaʻole hiki iā lākou ke wehe i nā huahana ʻōpala e hōʻiliʻili ana i loko o ke kino. Ua kapa ʻia hoʻi kēia ʻo (Acute Kidney Injury - AKI) .

ʻOiai hiki i ka HUS ke hoʻopilikia i kekahi, ʻo ka hapa nui o ia mea i hoʻoulu ʻia e kahi maʻi bacteria , ʻoiai ʻo Escherichia coli , i ʻike nui ʻia ʻo E. coli . ʻO kēia bacteria ke kumu o ka maʻi diarrhea, ʻoiai ka maʻi diarrhea koko. Eia nō naʻe, ʻo ka syndrome kahi hōʻiliʻili o nā hōʻailona, ​​​​a hiki nō hoʻi ke loaʻa ka HUS ma muli o nā kumu ʻē aʻe ma mua o E. coli.

ʻAʻole hiki i kēia kūlana (HUS) ke hoʻopilikia wale i nā puʻupaʻa, akā i kekahi manawa i nā ʻāpana ʻē aʻe e like me ka puʻuwai a me ka lolo. Eia naʻe, ʻo ka hapa nui o ia mea e hoʻopilikia ai i nā puʻupaʻa.

ʻO ka mea nui loa: Inā loaʻa iā ʻoe a i ʻole kāu keiki ka maʻi kahe koko a i ʻole he maʻi kahe no nā lā ʻekolu a ʻoi aku, e ʻike pono i ke kauka. Inā ʻaʻole mālama ʻia, hiki i ka HUS ke lilo i mea koʻikoʻi a hoʻoweliweli i ke ola.

Aia kekahi mau ʻano HUS like ʻole?

ʻAe, aia kekahi mau ʻano nui o (HUS). E aʻo iki kākou e pili ana iā lākou:

1. "Maʻamau" (HUS): ʻO kēia ke ʻano maʻamau . Hoʻokumu pinepine ʻia e kahi maʻi bacteria, ʻoiai ʻo E. coli, e hoʻopilikia ana i ko mākou ʻōpū liʻiliʻi a me ka colon.

2. "ʻAno ʻole" (HUS) (aHUS): He mea kākaʻikahi iki kēia.ʻO ka pinepine, ʻo kēia ma muli o nā kumu genetic, ʻo ia hoʻi, ua hoʻoilina ʻia mai nā mākua a i nā keiki.

3. "Lua" (HUS): Loaʻa kēia ʻano ma ka pili ʻana me nā kūlana olakino ʻē aʻe. No ka laʻana, hiki ke hana ʻia e kekahi mau lāʻau lapaʻau, nā maʻi ʻē aʻe, a i ʻole ka hāpai ʻana.

E aʻo iki kākou e pili ana i ka "Atypical" (HUS) (aHUS)

He kūlana laha ʻole ka (aHUS). Hiki iā ia ke hana i nā hōʻailona like me ka mea ma mua:

  • Ua hoʻemi ʻia nā pae o nā hunaola koko ʻulaʻula.
  • Ua emi ka helu platelet.
  • Ka hāʻule koke ʻana o ka puʻupaʻa (ka hāʻule koke ʻana o ka puʻupaʻa) .
  • Ke koko kiʻekiʻe (hypertension) a i ʻole ka hiki ʻole ke kaohi i ke koko.

ʻO kēia kūlana (aHUS) he maʻi hoʻoilina maʻamau. ʻO ia hoʻi, ua hana ʻia e kekahi mau loli (nā mutations) i loko o kā mākou mau genes. Eia nō naʻe, inā paha aia kēia kūlana hoʻoilina, ua hoʻoulu ʻia e kekahi maʻi, maʻi, a i ʻole ke kumu o ke kaiapuni.

Pehea ka maʻamau o (HUS)?

Ma waena o 5% a me 15% o ka poʻe i loaʻa i ka maʻi diarrhea i hoʻokumu ʻia e ka bacteria (E. coli) e loaʻa iā lākou ka HUS . ʻO ke ʻano i kapa ʻia ʻo (aHUS) he mea kākaʻikahi loa ia. Loaʻa ia ma kahi o hoʻokahi i loko o hoʻokahi miliona kānaka.

He aha nā hōʻailona nui o (HUS)?

He mea nui loa e ʻike ʻoe i kēia mau hōʻailona.

Nā hōʻailona mua i ʻike ʻia:

  • Ka maʻi kahe: Hele pinepine ʻia me ke koko.
  • ʻEha ʻōpū.
  • Ka luaʻi a me ka luaʻi.
  • ʻEha poʻo .
  • ʻĀnuenue a me ke kuni.

Nā hiʻohiʻona ʻē aʻe i ʻike ʻia:

  • ʻEha maʻalahi.
  • ʻIli keʻokeʻo (keʻokeʻo): Hiki ke keʻokeʻo ka ʻaoʻao o loko o ka ihu a me loko o ka waha.
  • Ka huikau.
  • Hoʻopaʻa ʻana.
  • Nā kūlana e like me ka hahau ʻana.
  • Ka wikiwiki o ka puʻuwai (arrhythmia).

Inā lilo ke kūlana o (HUS) i mea koʻikoʻi, hiki i nā hunaola koko ʻulaʻula i luku ʻia ke hana i nā ʻōpū koko a hōʻino i nā ʻōpū e like me nā puʻupaʻa. A laila ʻaʻole hiki i nā puʻupaʻa ke kānana pono i nā huahana ʻōpala. ʻO kēia ka mea a mākou e kapa nei (Acute Kidney Injury - AKI) . Eia nā hōʻailona o ia mea:

  • Ke koko i loko o ka mimi (hematuria).
  • Hoʻonui ʻia nā pae o nā mea ʻawahia i loko o ke koko: Hiki i kēia ke hōʻeha a me ka manaʻo o ka maʻi.
  • Ke koko kiʻekiʻe.
  • Ka paʻakikī o ka hanu ʻana (dyspnea).
  • Edema: Hiki ke pehu, ʻoiai ma nā wāwae a me nā kuʻekuʻe wāwae.
  • Ka emi ʻana o ka mimi i hoʻopuka ʻia (oliguria).

He aha nā kumu nui o (HUS)?

ʻO ka hapa nui o nā hihia o HUS i hoʻokumu ʻia e kekahi mau ʻano bacteria E. coli. Hoʻopuka kēia mau bacteria i kahi toxin i kapa ʻia ʻo Shiga toxin . Hoʻopōʻino kēia toxin i ka uhi o ko mākou ʻōpū liʻiliʻi a hoʻoulu i ka maʻi diarrhea. Komo pū kēia toxin i ke kahe koko, e luku ana i nā hunaola koko ʻulaʻula a hōʻino i nā puʻupaʻa.

ʻOi aku ka nui o kou loaʻa ʻana i kahi maʻi E. coli mai:

  • ʻAiʻo i moʻa ʻole ʻia: ʻoi aku ka pipi, ka pipi wili ʻia.
  • Waiū i hoʻomaʻemaʻe ʻole ʻia a me nā mea inu huaʻai: ʻO ka Pasteurization kahi hana hoʻomehana mālie e pepehi ai i nā mea ʻino e like me ka bacteria.
  • Nā huaʻai a me nā mea kanu lepo i holoi ʻole ʻia.

Ua kapa ʻia kēia mau ʻano E. coli e hana ana i nā mea ʻawahia ʻo Shiga toxin-producing E. coli (STEC) . ʻO ke ʻano STEC maʻamau ma ʻAmelika ʻĀkau ʻo E. coli O157:H7 .

ʻAʻole pinepine loa, hiki i kekahi mau lāʻau lapaʻau a me nā mea ke hana i ka "secondary (HUS)". Nā Laʻana:

  • Nā lāʻau lapaʻau anti-cancer (nā lāʻau Chemotherapy): e like me (bleomycin), (cisplatin), (gemcitabine).
  • Nā lāʻau lapaʻau immunosuppressant: e like me (cyclosporine), (tacrolimus).
  • Quinine: He lāʻau lapaʻau no ka maʻi malaria.
  • Kekahi mau lāʻau lapaʻau : (oxymorphone), (ecstasy), (cocaine).

He mea laha anei ka (HUS)?

ʻAʻole, ʻaʻole laha ka HUS.

Eia nō naʻe, hiki ke laha nā bacteria E. coli. Hiki ke laha kēia bacteria ma o ka meaʻai a mea inu paha i haumia ʻia, a i ʻole ma ke komo ʻana i nā ʻōpala o ke kanaka a holoholona paha me ka maʻi diarrhea i loaʻa iā E. coli. No laila, he mea nui e makaʻala loa i ka maʻemaʻe.

ʻO wai ka mea e ulu nui ai (HUS)?

ʻOiai hiki i kekahi ke hoʻomohala i ka HUS, ʻoi aku ka nui o ka pilikia o kēia poʻe:

  • No nā keiki liʻiliʻi ma lalo o 5 mau makahiki.
  • No ka poʻe me ka ʻōnaehana pale kino nāwaliwali (immunocompromised).
  • Inā ua loaʻa i kekahi o kou ʻohana ʻo HUS ma mua (ʻoi aku hoʻi ʻo aHUS).
  • Inā loaʻa iā ʻoe kahi maʻi E. coli: ʻOi aku hoʻi mai nā mea e like me ka ʻiʻo i moʻa pono ʻole ʻia a me ka waiū i hoʻomaʻemaʻe ʻole ʻia.
  • Hoʻopili pololei me kahi mea i loaʻa i ka maʻi diarrhea i hoʻokumu ʻia e (E. coli).

Pehea ʻoe e ʻike ai inā loaʻa iā ʻoe (HUS)? (Diagnosis)

Ke ʻike ʻoe i ke kauka, e hana ʻo ia i kēia mau mea:

  • E nīnau e pili ana i kou mōʻaukala olakino .
  • E nīnau e pili ana i ka mōʻaukala olakino o kou ʻohana .
  • Hana ʻia kahi hoʻokolokolo kino .

Inā hāpai kēia mau mea i ka kānalua o kahi kūlana i kapa ʻia ʻo (HUS), e kauoha ke kauka i kekahi mau hoʻokolohua hou aʻe.

He aha ke ʻano o nā hoʻokolohua e hana ʻia?

  • Urinalysis: Lawe ʻia kahi laʻana o kāu mimi a nānā ʻia no ka protein a i ʻole ke koko.
  • Hoʻāʻo koko: Lawe ʻia kahi hāpana koko e nānā i nā mea e like me ka helu ʻana o nā cell koko ʻulaʻula, nā pae platelet, a me ka hana maikaʻi o kou mau puʻupaʻa a me ke akepaʻa.
  • Hoʻāʻo ʻōpala: Lawe ʻia kahi hāpana ʻōpala a nānā ʻia no ke alo o nā bacteria e hoʻoulu ai i ka HUS, e like me E. coli O157.
  • Hoʻāʻo ʻana i ka genetics: I kekahi manawa, hiki ke hoʻouna ʻia kahi hāpana o kou koko no ka hoʻāʻo ʻana i ka genetics. Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā he maʻi genetic kou e like me aHUS a he aha ka lāʻau lapaʻau maikaʻi loa iā ʻoe.
  • ʻO ka biopsy puʻupaʻa: ʻO kēia ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka puʻupaʻa a nānā iā ia ma lalo o kahi microscope e ʻike i ka nui o ka pōʻino i hana ʻia i nā puʻupaʻa a me ke kumu. ʻAʻole pono nā kānaka a pau i kēia.

Pehea e hiki ai i nā hoʻokolohua ke hōʻoia he HUS kāu?

  • Mai nā hoʻāʻo mimi: Inā he koko a protein paha i loko o ka mimi.
  • Nā hoʻāʻo koko: Inā haʻahaʻa nā pae o nā sela koko ʻulaʻula a me nā platelet, a inā paha ua kiʻekiʻe nā waiwai e hōʻike ana i ka hana o nā puʻupaʻa (e like me ka creatinine).
  • Nā hoʻāʻo ʻana i ka ʻōpala: Inā loaʻa nā bacteria e like me (E. coli O157).
  • ʻO ka biopsy puʻupaʻa: Hiki ke ʻike ʻia nā hōʻino kikoʻī i nā puʻupaʻa.

Pehea e mālama ʻia ai (HUS)?

Inā ua ʻike ʻia ʻoe me HUS, pono ʻoe e lawe ʻia i ka haukapila a mālama ʻia. ʻO nā koho lapaʻau e komo pū ana:

  • Nā wai intravenous (IV) a me/a i ʻole ka hānai ʻana i ka paipu (ʻai enteral): Kōkua kēia i ka pale ʻana i ka maloʻo ʻana o ka wai a hāʻawi i ka meaʻai e pono ai.
  • Nā lāʻau lapaʻau:
  • Hoʻāʻo lākou e hōʻemi i ka hōʻino ʻia o nā puʻupaʻa ma ka hāʻawi ʻana i nā lāʻau hoʻohaʻahaʻa koko (nā lāʻau antihypertensive) .
  • Hiki ke hāʻawi ʻia i nā kānaka me aHUS nā lāʻau lapaʻau kūikawā e like me eculizumab a i ʻole ravulizumab . Ma mua o ka hoʻomaka ʻana i kēia mau lāʻau lapaʻau, he mea nui e loaʻa ka lāʻau pale no nā maʻi meningococcal a me pneumococcal , no ka mea, hoʻonui kēia mau lāʻau i ka pilikia o ka loaʻa ʻana o kēlā mau maʻi.
  • Pono paha ʻoe e lawe i nā antibiotics no ka liʻiliʻi he ʻelua pule.
  • Nā hoʻoili koko: He mea nui loa ka hāʻawi ʻana i nā hunaola koko ʻulaʻula a me nā platelet i kekahi me (HUS). Hoʻēmi nā hunaola koko ʻulaʻula i nā hōʻailona o ka anemia, e like me ka hanu pōkole a me ka puʻuwai wikiwiki. Kōkua nā platelets i ke kāpili ʻana o ke koko, e hōʻemi ana i ke kahe ʻana o ke koko a me ka palapū.

Inā ua hōʻino nui ʻia nā puʻupaʻa, pono paha ka dialysis e hoʻomaʻemaʻe i ke koko a hiki i ka hoʻōla ʻana o nā puʻupaʻa. Inā hāʻule loa puʻupaʻa ma muli o HUS, pono paha kahi hoʻoili puʻupaʻa .

Hiki ke ho'ōla loa ʻia ka HUS?

ʻAe, nui ka poʻe e ho'ōla mai ka HUS me ka ʻole o ka hōʻeha mau loa ʻana i ko lākou olakino.

Eia nō naʻe, hiki i kekahi poʻe, ʻoiai nā kamaliʻi ʻōpio, ke loaʻa i ka maʻi puʻupaʻa mau loa (CKD) i 20% a 50%. Hiki i ka maʻi puʻupaʻa hope loa (ESK) ke ulu i 3% a 5%. Hōʻike nā haʻawina e hoʻopilikia ana ʻo CKD i kahi 45% o nā pākeke.

ʻOi aku ma mua o 85% o ka poʻe i loaʻa i ka HUS e hoʻōla piha i kā lākou hana puʻupaʻa. Eia nō naʻe, inā e hoʻōla piha lākou, aia kahi manawa liʻiliʻi e loaʻa ai iā lākou ke koko kiʻekiʻe a i ʻole nā ​​​​pilikia puʻupaʻa ʻē aʻe i ka wā e hiki mai ana.

Hiki ke pale ʻia ka HUS?

Eia kekahi mau mea hiki iā ʻoe ke hana e kōkua i ka pale ʻana i ka maʻi E. coli, kahi kumu nui o HUS. He mea nui loa kēia mau mea no ʻoe a me kou ʻohana:

  • E pale i ka ʻauʻau ʻana i nā wahi lepo (nā loko, nā muliwai), ʻoiai inā manaʻo ʻoe he kiʻekiʻe ka nui o nā bacteria i loko o ka wai.
  • Inā loaʻa iā ʻoe ka maʻi diarrhea, mai ʻauʻau.
  • E hōʻalo i ka inu ʻana i nā mea inu maka ʻole i hoʻomaʻemaʻe ʻia (waiū, wai huaʻai).
  • E hoʻomaʻemaʻe mau i nā lako kīhini (nā pahi, nā ʻō, nā puna) a me nā wahi e hoʻomākaukau ai i ka meaʻai (nā pākaukau, nā papa ʻokiʻoki, nā kīʻaha).
  • E hoʻomoʻa maikaʻi i nā hua manu a me nā ʻiʻo i wili ʻia a hiki i ka mahana o loko o 71 degere Celsius (160 degere Fahrenheit), a me ka moa i ka mahana o loko o 74 degere Celsius (165 degere Fahrenheit).
  • I ka wā e hoʻoheheʻe ai i ka ʻiʻo, e waiho i loko o ka microwave a i ʻole ka pahu hau. Mai hoʻoheheʻe iā ia ma kahi e hoʻomākaukau ai i ka meaʻai a i ʻole i loko o ka wai wela.
  • E hoʻokaʻawale i nā meaʻai maka a me nā meaʻai i moʻa ʻia.
  • E holoi pono i kou mau lima me ke kopa a me ka wai wela ma mua o ka ʻai ʻana, ma hope o ka hoʻohana ʻana i ka lua, ma hope o ka hoʻololi ʻana i nā diaper o nā keiki liʻiliʻi, a ma hope o ka hoʻopā ʻana i nā holoholona mahiʻai.

E noʻonoʻo wale, ma ka hahai ʻana i kēia mau ʻanuʻu maʻalahi, hiki iā ʻoe ke pale iā ʻoe iho mai kahi kūlana koʻikoʻi e like me kēia.

He aha kāu e manaʻo ai inā loaʻa iā ʻoe (HUS)?

Me ka ʻike kūpono a me ka mālama ʻana, hoʻōla piha ka hapa nui o ka poʻe me HUS me ka ʻole o ka hōʻino mau loa i ko lākou olakino. Eia nō naʻe, aia kahi pilikia o ka loaʻa ʻana o ke koko kiʻekiʻe a i ʻole nā ​​​​​​kūlana ʻē aʻe e hoʻopilikia ai i nā puʻupaʻa i ka wā e hiki mai ana.

ʻO nā hihia koʻikoʻi o HUS, ʻoiai inā pili lākou i nā ʻōpū ʻē aʻe, e like me ka lolo, hiki ke make inā ʻaʻole mālama ʻia.

He aha nā manawa kūpono e ola ai (HUS)?

Me ka ʻike kūpono a me ka mālama ʻana, ʻoi aku ma mua o 90% o ka poʻe e ola ana i ka HUS. No laila he mea nui e pale aku i ka hopohopo a e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona.

Pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe a i ʻole kāu keiki ka maʻi diarrhea nui, he mea nui loa e hoʻāʻo e hoʻomaʻū hou i kou kino.Hiki i nā mea inu hoʻomaʻemaʻe wai, e like me Jeevani, ke kōkua i ka hoʻololi ʻana i nā electrolytes i nalowale. Pono paha nā pēpē a me nā keiki liʻiliʻi e hāʻawi i ka waiū umauma a i ʻole ka waiū waiū. E nīnau i ke kauka e pili ana i ke ala maikaʻi loa e mālama ai i kāu keiki i ka wai.

Āhea wau e ʻike ai i ke kauka?

E ʻike koke i ke kauka inā loaʻa iā ʻoe kēia mau hōʻailona:

  • Ka maʻi kahe koko.
  • Ka maʻi kahe e mau ana ma mua o ʻekolu lā.
  • Pehu kino.
  • ʻIli e palaho maʻalahi.
  • Luhi nui.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

Hiki iā ʻoe ke nīnau i ke kauka i kēia mau nīnau:

  • Pehea ʻoe e hōʻoia ai inā loaʻa iaʻu ka Hemolytic Uremic Syndrome?
  • Pehea i loaʻa ai iaʻu ka Hemolytic Uremic Syndrome?
  • Inā ʻaʻohe oʻu Hemolytic Uremic Syndrome, he aha nā maʻi ʻē aʻe e loaʻa iaʻu?
  • He aha nā lāʻau lapaʻau āu e paipai nei?
  • E hōʻino mau ʻia anei koʻu mau puʻupaʻa?
  • E loaʻa anei iaʻu ke koko kiʻekiʻe a i ʻole nā ​​pilikia puʻupaʻa ʻē aʻe i ka wā e hiki mai ana?

He aha ka triad o ka Hemolytic Uremic Syndrome?

ʻO ka triad ka hui pū ʻana o ʻekolu mau hōʻailona nui e hōʻike ana i kahi maʻi.

ʻO ka Hemolytic Uremic Syndrome triad e komo pū ana me:

1. Ka hōʻino ʻana i kou mau hunaola koko ʻulaʻula (microangiopathic hemolytic anemia) .

2. Ka emi mālie ʻana o ka helu o nā platelets i loko o kou koko (thrombocytopenia) .

3. ʻEha puʻupaʻa koʻikoʻi .

Inā loaʻa iaʻu ka maʻi pākī, ʻo ia hoʻi he Hemolytic Uremic Syndrome koʻu?

ʻOiai he maʻi kahe kou, ʻaʻole ia he manaʻo he maʻi Hemolytic Uremic Syndrome kou. Eia nō naʻe, inā he maʻi kahe koko kou, a inā paha he koʻikoʻi kou maʻi kahe (a hiki i ka maʻi kahe wai a i ʻole e mau ana ma mua o ʻekolu lā), pono ʻoe e ʻike i ke kauka.

He aha ka ʻokoʻa ma waena o (Hemolytic Uremic Syndrome) a me (Thrombotic Thrombocytopenic Purpura - TTP)?

ʻO ka Hemolytic Uremic Syndrome (HUS) a me ka Thrombotic Thrombocytopenic Purpura (TTP) ʻelua mau kūlana like. I ka TTP, hana ʻia nā ʻōpū koko i loko o nā kīʻaha koko liʻiliʻi. ʻOiai ua hoʻohui pū nā kauka iā HUS a me TTP, ua manaʻo ʻia lākou he mau kūlana kaʻawale.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He manawa pōkole ka maʻi kahe, akā he ʻano ʻoluʻolu ʻole. Hoʻomaikaʻi pinepine ia i hoʻokahi a ʻelua paha lā. Eia nō naʻe, inā he maʻi kahe koko kou, a inā he maʻi kahe kou no nā lā ʻekolu a ʻoi aku, me ka luhi, ka maeʻele, a i ʻole ka emi ʻana o ka mimi ke hele ʻoe i ka lua, ua hiki i ka manawa e ʻike koke ai i ke kauka.

ʻO kahi maʻi i kapa ʻia ʻo Hemolytic Uremic Syndrome hiki ke hōʻino nui i kou mau puʻupaʻa a hoʻopilikia i nā kino ʻē aʻe.ʻO ka wikiwiki o kou loaʻa ʻana o ka lāʻau no kēia, ʻo ka emi ʻana o ka hiki ke hōʻino ʻia kou mau puʻupaʻa i ka wā lōʻihi. No laila, e makaʻala i nā hōʻailona, ​​e mālama i ka hoʻomaʻemaʻe maikaʻi, a e ʻimi i ke kōkua lapaʻau inā he mau hopohopo kāu. He mea nui loa kou olakino iā ʻoe!


ʻO ka maʻi Hemolytic Uremic, HUS, Maʻi Pūpū, Ka maʻi kahe, E. coli, Nā ʻulaʻula koko, Nā platelets, Ola kino o ke keiki

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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