I kekahi manawa ke ʻike ʻoe i kahi puʻupuʻu liʻiliʻi a i ʻole ka puʻupuʻu ma kou kino, makaʻu iki ʻoe, ʻeā? "He aha kēia? He mea weliweli anei?" Manaʻo ʻoe i hoʻokahi tausani mau mea. ʻOiaʻiʻo, ʻaʻole weliweli nā puʻupuʻu āpau. Akā, pono kekahi o lākou e hopohopo iki iā kākou. ʻO Histiocytoma kekahi o lākou. He mea ʻē paha ke kani ʻana o ka inoa, akā e kamaʻilio maʻalahi kākou e pili ana.
He aha maoli ka Histiocytoma?
I ka ʻōlelo maʻalahi, ʻo ka histiocytoma kahi ʻano puʻupuʻu e hana ʻia i loko o kou kino. Hana ʻia kēia mau puʻupuʻu i kahi ʻano cell kūikawā i kapa ʻia ʻo histiocytes . I kēia manawa ke noʻonoʻo nei paha ʻoe, "He aha kēia mau histiocytes?"
ʻO kēia mau histiocytes he mau pūnaewele pale maʻamau i loko o ko kākou kino. ʻO ia hoʻi, he ʻano pūnaewele lākou e kōkua i ka pale ʻana iā kākou mai nā maʻi a me nā maʻi. Loaʻa lākou ma nā wahi he nui o ko kākou kino. No ka laʻana, hiki ke loaʻa kēia mau pūnaewele i loko o ka iwi iwi, ke kahe koko, ka ʻili, nā māmā, ke akepaʻa, ka spleen, a me nā lymph nodes.
Akā i kekahi manawa hiki i kēia mau pūnaewele histiocyte ke hele i nā ʻiʻo kahi i noho ʻole ai lākou a hōʻuluʻulu ma laila a hana i nā puʻupuʻu , a i ʻole e like me kā mākou e kapa nei iā lākou, histiocytomas. Maopopo iā ʻoe?
He maʻi ʻaʻai anei kēia histiocytoma?
ʻO kēia ka nīnau nui loa a ka poʻe he nui. Inā he maʻi kanesa ka histiocytoma a ʻaʻole paha , pili ia i ke ʻano o ka histiocytoma āu .
- He maikaʻi kekahi, ʻo ia hoʻi, ʻaʻole lākou he maʻi ʻaʻai a ʻaʻole ia e hōʻeha nui i ke kino.
- Eia nō naʻe, hiki i kekahi mau ʻano ke lilo i mea ʻino , ʻo ia hoʻi, ua hana ʻia lākou me nā hunaola kanesa a hiki ke ulu a laha i nā ʻāpana ʻē aʻe o ke kino.
No laila, ʻaʻole pono ʻoe e hopohopo ke ʻike ʻoe i ka histiocytoma, akā he mea nui loa ia e ʻimi pono i ke aʻo lapaʻau.
Aia kekahi mau ʻano histiocytoma like ʻole?
ʻAe, aia nā ʻano histiocytomas like ʻole. E kamaʻilio kākou e pili ana i kekahi o nā ʻano nui.
1. ʻO ka Sarcoma Pleomorphic Undifferentiated (UPS)
ʻO ka histiocytoma fibrous malignant kēia i ʻike mua ʻia, he ʻano maʻi kanesa kēia. Hoʻomohala pinepine ia i loko o nā ʻiʻo palupalu, e like me kou mau ʻiʻo a me nā ʻiʻo momona. Eia nō naʻe, hiki ʻole ke ulu pinepine i loko o ka iwi.
- ʻO wai ka mea e loaʻa pinepine ai?: ʻO ia ka mea maʻamau i ka poʻe ʻelemakule, ʻoiai nā kāne.
- Ma hea lākou e loaʻa ai?: Hiki iā lākou ke loaʻa ma nā wahi āpau o ke kino, akā ʻoi aku ka maʻamau ma nā lima, nā wāwae, a me ka ʻōpū. Hiki nō hoʻi iā lākou ke loaʻa i kekahi manawa ma nā wahi i hana ʻia ai ka radiation therapy.
- Nā ʻano:Ulu koke kēia mau puʻupuʻu a hiki ke laha (metastasize) i nā ʻāpana ʻē aʻe o ke kino. No laila, pono ʻoe e makaʻala loa i kēia.
2. ʻO ka Histiocytoma Fibrous Benign (BFH)
ʻO kēia ke ʻano maʻamau o ka puʻupuʻu palupalu . E like me ka inoa e hōʻike nei, he benign ia, ʻo ia hoʻi, ʻaʻole ia he maʻi kanesa. ʻIke ʻia ia he puʻu fibrous.
- Ma hea e hana ʻia ai?: Hiki ke hana ma nā wahi āpau o ke kino.
- He mea nui: ʻOiai ʻaʻole kēia he maʻi kanesa, pono pinepine lākou i ka mālama ʻia no ka mea hiki iā lākou ke ulu a hōʻeha i ka ʻeha a me ka ʻoluʻolu ʻole.
3. ʻO ka Histiocytoma Fibrous Angiomatoid (AMFH)
He ʻano hua laha ʻole kēia.
- ʻO wai ka mea e loaʻa pinepine ai?: Hoʻopilikia pinepine ia i nā keiki a me nā ʻōpio.
- Ma hea e loaʻa ai?: ʻIke pinepine ʻia ia he puʻu e ulu mālie ana ma nā lima a i ʻole nā wāwae.
- Nā Hōʻailona: ʻAʻole ʻike ka hapa nui o ka poʻe i ka ʻeha nui mai kēia. I kekahi manawa hiki ke kuhihewa ʻia he hematoma, he puʻupuʻu i hana ʻia e ke koko e hōʻiliʻili ana ma ka ʻili o ka ʻili.
- Lapaʻau: Hiki ke ho'ōla ʻia kēia ʻano me ka lāʻau lapaʻau . Eia naʻe, he mea kākaʻikahi loa (ma kahi o 1%) hiki ke laha i nā ʻāpana mamao o ke kino.
4. ʻO ka Histiocytoma ʻili
Ua kapa ʻia kēia ʻo Dermatofibroma a i ʻole Superficial Benign Fibrous Histiocytoma .
- Ma hea kahi e loaʻa ai?: ʻIke pinepine ʻia ma ka ʻili , ʻoi aku hoʻi ma nā wāwae haʻahaʻa.
- ʻO wai ka mea e loaʻa pinepine ai?: ʻOi aku ka maʻamau i nā wahine ma mua o nā kāne.
- Lapaʻau: Inā ʻaʻole ʻoe e ʻike i ka ʻoluʻolu ʻole a i ʻole nā hōʻailona nui, ʻaʻole pono ʻoe e wehe i kēia.
E noʻonoʻo he wahi ʻeleʻele liʻiliʻi kou ma kou wāwae e like me he mea lā ua hāpai iki ʻia. He histiocytoma ʻili paha ia. Akā ʻoi aku ka maikaʻi o ke ʻike ʻana i ke kauka e hōʻoia.
He aha ka ʻokoʻa ma waena o ka histiocytoma a me ka mast cell tumor?
ʻOiai ʻo nā ʻano ʻōpū ʻelua e hana ʻia i loko o ke kino, ʻokoʻa ke ʻano o nā cell i hana ʻia ai lākou. Hana ʻia ka Histiocytoma mai nā cell histiocyte. Hana ʻia kahi tumor cell mast mai nā cell mast. Hana ʻia kēia mau cell mast i loko o ko kākou iwi iwi a hiki ke loaʻa i nā ʻiʻo hoʻopili.
ʻO wai ka mea e maʻalahi i ka histiocytoma?
Hoʻololi kēlā ma muli o ke ʻano o ka histiocytoma.
- Eia kekahi laʻana, ʻo UPS (Undifferentiated Pleomorphic Sarcoma) a mākou i kamaʻilio ai ma muaʻOi aku ka maʻamau o ia i nā kāne ma mua o nā wahine, a ʻoi aku ka nui o ka pilikia o ka loaʻa ʻana me ka makahiki.
- Eia nō naʻe, ʻike pinepine ʻia ka AMFH (Angiomatoid Fibrous Histiocytoma) i nā keiki, nā ʻōpio, a me nā mākua ʻōpio.
- ʻOi aku ka maʻamau o ka Cutaneous Histiocytoma i nā wahine, a ʻike pinepine ʻia i nā pākeke ʻōpio a i ʻole nā mākua waena.
Pehea ka maʻamau o ka histiocytoma?
Hoʻololi nō hoʻi kēia ma muli o ke ʻano.
- ʻO ka Benign fibrous histiocytoma (BFH) a me ka cutaneous histiocytoma ʻelua mau ʻano i ʻike ʻole ʻia .
- ʻOiai ʻaʻole ʻo UPS kahi ʻano maʻi kanesa maʻamau, ʻo ia ke kuleana no ma waena o 20% a me 30% o nā sarcomas palupalu.
- Ua manaʻo ʻia ʻo AMFH he mea laha ʻole loa .
He aha nā hōʻailona o ka histiocytoma?
Hiki ke ʻokoʻa nā hōʻailona ma muli o ke ʻano o ka histiocytoma āu e loaʻa ai.
Nā ʻano o ka sarcoma pleomorphic undifferentiated (UPS):
- He puʻu a pehu paha e ulu mālie ana .
- ʻEha .
- I kekahi manawa aia ka mae wale ma ia wahi.
- He ʻano ʻūlū .
- Ka pehu ʻana ma ka lima a i ʻole ka wāwae.
- Kuni .
- ʻAʻohe ʻono o ka meaʻai .
- Ka paʻa ʻana o ka ʻōpū .
- Ka emi ʻana o ke kaumaha .
Nā ʻano o ka Benign Fibrous Histiocytoma (BFH):
- He puʻupuʻu e ulu ana a i ʻole ka pehu ʻana.
- ʻO ia ka ʻeha .
- Nānā: ʻAʻole loaʻa pinepine kēia ʻano BFH i loko o ka waha. Eia nō naʻe, inā hana ia, hiki iā ia ke pilikia i ka ale ʻana (dysphasia) , ka pilikia o ka hanu ʻana (dyspnea) , a i ʻole ka pilikia o ka ʻōlelo ʻana.
Nā ʻano o ka angiomatoid fibrous histiocytoma (AMFH):
- Kuni .
- Ka emi ʻana o ke kaumaha .
- ʻO ke anemia ke ʻano o ka nele i ke koko.
- ʻEha .
- ʻOluʻolu ke hoʻopā ʻia.
Nā ʻano o ka Histiocytoma ʻili:
- He wahi ʻeleʻele ma ka ʻili (pinepine ma nā wāwae lalo).
- ʻIke ʻia he puʻu i hoʻokiʻekiʻe ʻia .
He aha ke kumu o ka histiocytoma?
Hiki ke pili kēia mau puʻupuʻu i kekahi manawa me nā mea e like me ka chemotherapy a me ka radiation . Pili pū lākou me kekahi mau kūlana olakino, e like me ka maʻi Paget o ka umauma. Hiki iā lākou ke ʻike ʻia ma hope o ka trauma a i ʻole ka ʻeha .
Akā, i ka ʻoiaʻiʻo, ʻaʻole maopopo i nā loea ke kumu o ka histiocytoma e ulu ai ma kahi mua.
Pehea e ʻike ʻia ai ka histiocytoma? (Diagnosis)
Ke hele ʻoe e ʻike i ke kauka, e nīnau mua ʻo ia e pili ana i kāu mau hōʻailona a hana i kahi nānā maka o ka puʻupuʻu. A laila, hana paha ʻo ia i kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona. ʻO kekahi o lākou:
- Dermoscopy: Ma kēia, hoʻohana ke kauka i kahi mea hana lima kūikawā e nānā pono i nā puʻupuʻu a me nā kiko ma kou ʻili.
- Nā kukuna X: Hiki i kēia mau kiʻi ke hōʻike i ke kūlana o nā iwi a me nā ʻiʻo palupalu. Hiki iā lākou ke hoʻoholo inā ua hoʻopilikia ka puʻupuʻu i nā iwi.
- Ultrasound: Hiki i kēia ke hāʻawi i kahi nānā maikaʻi i ke kūlana o nā ʻiʻo palupalu i loko o ke kino. Hiki iā ia ke kōkua i ka hoʻoholo ʻana i ke ʻano a me ka nui o ka puʻupuʻu.
- Magnetic Resonance Imaging (MRI): Hiki ke hana i kahi MRI inā makemake ʻoe e kiʻi i kahi kiʻi kikoʻī o ke cartilage a me nā iwi.
- Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi loa e hōʻoia i ka hōʻailona . Ma kēia, lawe ʻia kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka puʻupuʻu a hoʻouna ʻia i kahi keʻena hoʻokolohua no ka hoʻāʻo ʻana. E hoʻoholo pono kēia inā he histiocytoma ia, he aha ke ʻano, a inā he maʻi kanesa a ʻaʻole paha.
ʻAe kēia mau hoʻokolohua i ke kauka e hoʻokaʻawale pololei a ʻike inā he histiocytoma a i ʻole kekahi ʻano ʻē aʻe e like me ka puʻupuʻu.
Pono anei e wehe ʻia ka histiocytoma?
Hoʻoholo ʻia nō hoʻi kēlā e ke ʻano a me ke kūlana .
- Inā he ʻino paha ka puʻupuʻu a i ʻole e hōʻeha nui ai, e ʻōlelo paha ke kauka e wehe ʻia ke ʻoki kino .
- ʻAʻole pono e wehe ʻia kekahi mau ʻano histiocytomas, e like me nā dermatofibromas a mākou i kūkākūkā ai ma mua, ke ʻole lākou e hoʻoulu i nā hōʻailona nui.
Pehea e mālama ʻia ai ka histiocytoma?
ʻO ke ʻano o ka lāʻau i ʻōlelo ʻia no ʻoe e hilinaʻi ʻia ma nā kumu he nui, me ke ʻano o ka histiocytoma, kona nui, a me kona wahi.
- Hoʻopau pinepine ʻia nā histiocytomas ʻino ma ke ʻoki kino . Ma hope o kēlā, hoʻohana ʻia ka chemotherapy a i ʻole ka radiation therapy e luku i nā hunaola kanesa i koe.
- I kekahi mau hihia, hāʻawi paha ke kauka i ka radiation therapy a i ʻole chemotherapy mua e hoʻēmi i ka puʻupuʻu ma mua o ke ʻoki ʻana.
Hiki ke ho'ōla ʻia ka histiocytoma?
ʻAe. I ka hapanui o nā hihia, hiki ke ho'ōla ʻia nā histiocytomas kanesa. Eia naʻe,ʻO ka ʻike mua ʻana a me ka mālama mua ʻana nā manawa kūpono loa no ka hoʻōla holomua. No laila, inā ʻike ʻoe i kekahi mau puʻupuʻu a i ʻole nā loli i kou kino, e ʻike koke i ke kauka.
Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
E like me nā lāʻau lapaʻau āpau, aia kekahi mau hopena ʻaoʻao. E loli kēia ma muli o ke ʻano o ka lāʻau lapaʻau āu e loaʻa ai.
Nā hopena ʻaoʻao hiki ke hana ʻia o ke ʻoki kino:
- ʻEha
- Maʻi
- Ka luaʻi a me ka luaʻi
- Nā ʻūpā koko
- ʻEha a puni ka ʻeha
- Ke kahe ʻana o ke koko
- Ka hopena maʻi i ka anesthesia
Nā hopena ʻaoʻao hiki ke loaʻa mai ka chemotherapy:
- Luhi
- Pohō lauoho
- Nā maʻi
- ʻEha maʻalahi
- Anemia
- Ka maʻi pākī
- Ka paʻa ʻana o ka ʻōpū
- Nā loli kaumaha
- Nā pilikia hānau keiki
- Nā loli o ke ʻano
Nā hopena ʻaoʻao hiki ke loaʻa mai ka radiation therapy:
- Luhi
- Nā loli o ka ʻili ( e.g. ʻulaʻula, maloʻo, maneʻo)
ʻAʻole hiki kēia mau hopena ʻaoʻao i nā kānaka a pau. ʻAʻole paha i loaʻa i kekahi poʻe. E kamaʻilio me kāu kauka e pili ana i ia mea.
Pehea e hiki ai iā ʻoe ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i ka histiocytoma?
E like me kā mākou i ʻōlelo ai ma mua, ʻoiai ʻaʻole maopopo loa nā kumu kikoʻī o ka histiocytoma , he paʻakikī ke ʻōlelo pehea e pale loa ai.
Eia nō naʻe, ua ʻōlelo ʻia ʻo ka hahai ʻana i kahi nohona olakino , e like me ka ʻai ʻana i ka meaʻai kaulike, ka hoʻoikaika kino mau , a me ka noho ʻana mai nā huahana paka, hiki ke hōʻemi nui i ka pilikia o ka hoʻomohala ʻana i nā sarcomas (kahi ʻano puʻupuʻu kanesa).
He mea make anei ka Angiomatoid Fibrous Histiocytoma (AMFH)?
Hiki i ka AMFH ke make inā pālahalaha ia i nā ʻāpana ʻē aʻe o ke kino. Eia nō naʻe, inā ʻike mua ʻia, hiki ke mālama pono ʻia a ho'ōla ʻia. I ka hapa nui o ka manawa, ulu mālie kēia ʻano puʻupuʻu. No laila, hiki pinepine ke wehe i ka puʻupuʻu ma mua o ka laha ʻana i nā ʻāpana ʻē aʻe o ke kino.
Āhea wau e ʻike ai i ke kauka?
Inā ʻike ʻoe i kahi puʻupuʻu, puʻupuʻu, a i ʻole kahi loli ʻili ma kou kino i kēlā me kēia manawa, a inā he kānalua kāu e pili ana i ia mea, e ʻike pono i ke kauka.A laila hiki iā ia ke holo i nā hoʻokolohua e ʻike pono ai i ke kumu. Hiki paha he histiocytoma a i ʻole kekahi pilikia olakino ʻē aʻe. Eia nō naʻe, hiki i kāu kauka ke kōkua iā ʻoe e hoʻolālā i kahi hoʻolālā lapaʻau kūpono iā ʻoe a kōkua iā ʻoe e hōʻemi i kāu mau hōʻailona. Mai hoʻokaʻulua, he mea naʻauao ke hōʻike i kekahi mau hopohopo, ʻoiai inā he liʻiliʻi lākou.
Leka Lawe-Home
He ʻoiaʻiʻo ʻaʻole mākou i ʻike pono i ke kumu o ka histiocytoma, no laila hiki ke hopohopo. Eia nō naʻe, me ka ʻike mua ʻana a me ka mālama kūpono, ʻoi aku ka kiʻekiʻe o ka manawa e ho'ōla piha ai.
- Inā ʻike ʻoe i kahi puʻupuʻu hou, pehu ʻana, a i ʻole kahi loli o ka ʻili ma kou kino, mai hoʻomāmā.
- E ʻimi koke i ke kōkua lapaʻau.
- E hana i nā hoʻokolohua a kāu kauka e haʻi aku ai iā ʻoe.
- Inā pono ka lāʻau lapaʻau, e kū i mua me ka makaʻu ʻole, no ka mea, i ka hapanui o nā hihia, hiki ke ho'ōla ʻia kēia mau mea.
ʻAʻole ʻoe hoʻokahi, he nui ka poʻe e kū nei i nā kūlana like. E kamaʻilio me kāu kauka a me kou ʻohana e pili ana i kēia. Me kā lākou kōkua, hiki iā ʻoe ke lanakila ma luna o kēia kūlana.
histiocytoma , puʻupuʻu, maʻi ʻaʻai, maʻi ʻili, histiocyte, maikaʻi ʻole, ʻino











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