Ua lohe paha ʻoe e hiki ke ulu ka maʻi kanesa i loko o ka maka? Ua ʻike paha ʻoe i kahi loli iki i kou ʻike, a i ʻole kekahi mea e like me kahi kiko ʻeleʻele i loko o kou maka. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi kanesa e pili ana i kekahi mea like, akā he mea kakaikahi loa ia, ʻo ia hoʻi, ʻike pinepine ʻole ʻia. Ua kapa ʻia kēia ʻo Intraocular Melanoma . Mai hopohopo, e wehewehe maʻalahi kākou i nā mea āpau e pili ana i kēia.
He aha kēia melanoma intraocular?
I ka ʻōlelo maʻalahi, ʻo ka Intraocular Melanoma kahi maʻi kanesa e ulu ana i loko o ko kākou mau maka. Aia kekahi ʻano cell e hāʻawi ana i ke kala i ko kākou mau maka, i kapa ʻia ʻo melanocytes . Hoʻomaka kēia maʻi kanesa ke hoʻomaka kēia mau cell e ulu nui a hiki ʻole ke kāohi ʻia. I kekahi manawa hiki i kēia ke hoʻololi i ka ʻike, ka nalowale ʻana o ka ʻike, a i ʻole ka nalowale loa o ka ʻike .
Ma hea i loko o ka maka e hana ai kēia? (E aʻo e pili ana i ka Uvea)
ʻO ka maʻamau, ulu ka Intraocular Melanoma ma ka papa waena o ka maka. Ua kapa ʻia kēia ʻo uvea . E noʻonoʻo ua like ka maka me kahi pōpō liʻiliʻi. ʻO ka ʻāpana keʻokeʻo ma waho ua kapa ʻia ʻo sclera . ʻO ka ʻāpana i loko o ka maka e ʻike i ka mālamalama a kaohi i ka ʻike ʻana ʻo ia ka retina . Ma waena o kēlā mau mea ʻelua ʻo ka uvea .
ʻEkolu mau ʻāpana nui o ka uvea :
- ʻIris: ʻO kēia ka ʻāpana o ka maka e hāʻawi iā ia i kona kala, ke kala polū a me ka ʻeleʻele āu i ʻike ai i kekahi poʻe.
- Kino ciliary: He apo kēia o nā ʻiʻo ma hope o ka iris. Kōkua ia i ka hoʻomalu ʻana i ka lens i loko o ka maka.
- Choroid: ʻO kēia ka membrane e loaʻa ana nā kīʻaha koko he nui e hoʻolako i ka maka me ka oxygen a me nā meaʻai.
ʻO ka hapa pinepine, hoʻomaka ka melanoma ma ka choroid . I kekahi manawa, hiki i kēia maʻi kanesa ke laha (metastasize) mai loko o ka maka a i nā ʻāpana ʻē aʻe o ke kino. ʻO ke akepaʻa ka wahi maʻamau o ka laha ʻana.
He mea nui e hoʻomaopopo he ʻelua mau kūlana like ʻole ka melanoma intraocular a me ka melanoma ʻili . ʻOiai like ke ʻano o ke kelepona, he ʻelua mau maʻi like ʻole kēia.
Hiki i kēia ke kumu maoli i ka nalowale o ka ʻike?
ʻAe, hiki i kekahi poʻe me ka melanoma intraocular ke loaʻa nā pilikia ʻike. ʻO ka nui o ka nalowale o ka ʻike e pili ana i ka nui o ka puʻupuʻu a me ka lōʻihi o kona noho ʻana i loko o ka maka. I kekahi manawa, ʻo ka melanoma i loaʻa no ka manawa lōʻihi hiki ke kumu i ka nalowale piha ʻana o ka ʻike. No laila he mea nui e ʻike mua iā ia.
ʻO wai ka mea e loaʻa pinepine ai kēia maʻi? (Nā kumu pilikia)
Aia kekahi mau mea pilikia e hiki ke hoʻopilikia i ka ulu ʻana o ka melanoma i loko o ka maka. ʻO ke ʻano kēia, ʻoi aku ka nui o ka loaʻa ʻana o ka maʻi i ka poʻe me kēia mau mea ma mua o nā poʻe ʻē aʻe.
- No ka poʻe me ka ʻili keʻokeʻo loa: ʻO ia hoʻi, ka poʻe me ka ʻili māmā, nā maka, a me ke kala o ka lauoho.
- Nā maka ʻōmaʻomaʻo a i ʻole ka ʻili ʻōmaʻomaʻo.
- Ma waena o 70 a 80 mau makahiki: Piʻi iki kēia pilikia i kou wā ʻelemakule.
- Inā ua loaʻa i kekahi o kou ʻohana ʻo Uveal Melanoma ma mua: Eia naʻe, he mea kakaikahi loa kēia.
Pehea ka maʻamau o kēia?
ʻO ka melanoma intraocular ke ʻano maʻamau o ka maʻi kanesa e ulu ana i loko o ka maka i nā pākeke, akā ma ke ʻano holoʻokoʻa he maʻi kanesa kakaikahi loa ia. No ka laʻana, ma kahi ʻāina e like me ʻAmelika Hui Pū ʻIa, aia wale nō ma kahi o 2,500 mau hihia hou o ka maʻi i ʻike ʻia i kēlā me kēia makahiki. ʻO ke ʻano kēia, ʻaʻole ia he maʻi e hoʻopilikia i nā mea āpau.
No ke aha e ulu ai ka melanoma i loko o ka maka? (Nā kumu)
Hōʻike ko kākou mau genes i nā pūnaewele i loko o ko kākou kino pehea e māhele ai a pehea e hana ai. Hana ʻia kēia mau genes i ka DNA . E noʻonoʻo, inā he mutation , ʻo ia hoʻi, he loli, i loko o kēia gene, hiki iā ia ke hoʻouna i nā ʻōlelo kuhikuhi hewa i nā pūnaewele. ʻO ia ka manawa e māhelehele ai nā pūnaewele me ke kāohi ʻole, e alakaʻi ana i ka maʻi kanesa.
Hana ʻia kekahi mea like ma ka melanoma i loko o ka maka. Loaʻa i nā melanocytes, a mākou i kamaʻilio ai ma mua, i loko o ka maka, nā ʻōlelo kuhikuhi hewa mai ko lākou mau genes. A laila hoʻonui nui kēlā mau cell a hana i nā puʻupuʻu kanesa .
He aha nā hōʻailona o kēia? (Nā mea e hopohopo ai)
I kekahi manawa, ʻoiai inā loaʻa iā ʻoe ka melanoma intraocular, ʻaʻole paha e hōʻike i kekahi mau hōʻailona . A i ʻole, no ka mea aia ke kanesa i loko o ka maka, kahi hiki ʻole iā mākou ke ʻike mai waho, hiki ke paʻakikī ke ʻike i nā hōʻailona.
Eia nō naʻe, i ka wā e ʻike ʻia ai nā hōʻailona, hiki iā ʻoe ke ʻike i nā mea e like me:
- Nā wahi makapō a i ʻole ka emi ʻana o ka ʻike: Me he mea lā ʻaʻole hiki iā ʻoe ke ʻike i kekahi mau wahi ke nānā aku ʻoe.
- ʻIke pōwehiwehi a ʻike haʻahaʻa paha.
- Nā loli i ke kūlana o ka maka: me he mea lā ua piholo a puka mai paha ka maka.
- Nā loli i ka nui a i ʻole ke ʻano o ka kiko ʻeleʻele ma waenakonu o ka maka (pupil).
- He wahi ʻeleʻele ma ka iris.
- Ka neʻe ʻana o ka lens i loko o ka maka: Hiki ke hana ʻia kēia inā he melanoma i loko o ke kino ciliary .
- ʻIke pālua.
- ʻEha maka.
- Nā mea lana a i ʻole nā ʻālohilohi o ke kukui. E noʻonoʻo, i kekahi manawa ʻike koke ʻoe i kahi kiko ʻeleʻele a i ʻole kekahi mea e like me ka pōpō kaula e lana ana i mua o kou mau maka, ʻeā? Pēlā nō.
- Ka wehe ʻana o ka retina: Hiki ke hana kēia, ʻoiai inā he melanoma i loko o ka choroid .
Pehea e ʻike ai ke kauka i kēia? (Diagnosis)
Inā loaʻa iā ʻoe kēia mau hōʻailona, e nīnau mua kāu kauka iā ʻoe e pili ana i kou kūlana a lawe i kahi mōʻaukala lapaʻau. A laila e hana lākou i kahi hoʻokolokolo maka . E nānā kēia i kou ʻike a hoʻohana i nā mea hana kūikawā e nānā i loko o kou maka. I kekahi manawa, hiki ke hoʻohana ʻia nā kulu maka kūikawā e hoʻonui i ka pupil ma waenakonu o kou maka. E ʻae kēia i ke kauka e ʻike maopopo i nā ʻano ma hope o kou maka.
Hiki ke hana ʻia kekahi mau hoʻokolohua ʻē aʻe:
- Angiography: Nānā kēia i nā poloka a i ʻole nā leaka i loko o nā kīʻaha koko i loko o ka choroid .
- Ultrasound: Hiki i kēia ke ana i ka nui o nā ʻano i loko o ka maka a nānā i nā puʻupuʻu. Ua like ia me kahi scan e nānā ana i kahi pēpē i loko o ka ʻōpū.
Inā ʻike kāu kauka i kēia he melanoma intraocular, hiki iā lākou ke kauoha i nā hoʻokolohua kiʻi hou a i ʻole nā hoʻokolohua koko. Hoʻohana ʻia kēia mau mea e hoʻoholo ai i ke kahua o ke kanesa. ʻO ia hoʻi, e ʻike inā ua pālahalaha ke kanesa ma waho o ka maka i nā ʻāpana ʻē aʻe o ke kino.
He aha nā lāʻau lapaʻau no kēia?
Inā ʻaʻohe ou hōʻailona mai kahi puʻupuʻu i loko o kou maka, ʻaʻole i hoʻopilikia ʻia kou ʻike, a he liʻiliʻi ka puʻupuʻu (ʻaʻole iʻoi aku ma mua o 2.5 milimita ka mānoanoa), ʻaʻole pono paha ʻoe e hoʻomaka koke i ka lāʻau lapaʻau . Hiki i kāu kauka ke ʻōlelo aku i kahi mea i kapa ʻia ʻo " kali makaʻala ." ʻO ia hoʻi ke kali ʻana i kekahi manawa ma mua o ka hoʻomaka ʻana i ka lāʻau lapaʻau, me ka nānā mau ʻana i ka puʻupuʻu e ʻike inā ulu ia.
Eia nō naʻe, inā makemake ʻoe i ka lāʻau lapaʻau, ʻo nā lāʻau lapaʻau maʻamau ka radiation therapy a i ʻole ke ʻoki kino . ʻO ka lāʻau lapaʻau kūpono iā ʻoe e hilinaʻi ʻia i nā mea e like me:
- Ma hea kahi o ka puʻupuʻu.
- Ka nui a me ka mānoanoa o ka puʻupuʻu.
- Inā ua pālahalaha ke kanesa i nā ʻāpana ʻē aʻe o ke kino.
- Kou makahiki a me kou olakino laulā.
Pehea e hana ʻia ai ke ʻoki kino?
Aia kekahi mau ʻano hana no ka melanoma intraocular:
- ʻOki waho: Ma kēia, wehe ʻia ka puʻupuʻu kanesa a me kahi liʻiliʻi o nā ʻiʻo olakino a puni ia mai waho o ka maka i loko.
- Ka wehe piha ʻana o ka maka (Enucleation):I kēia, ua wehe ʻia ka maka a me kekahi hapa o ke aʻalolo optic.
Loaʻa i kēia mau ʻoki kino āpau kekahi mau pilikia o ka nalowale ʻana o ka ʻike. ʻOiai hiki ke hoʻokomo ʻia kahi maka prosthetic ma hope o ka enucleation, ʻaʻole e hāʻawi ka maka i ka ʻike.
He aha nā ʻano hana o ka radiation therapy?
ʻO ka radiation therapy kahi ʻano hana e luku ai i nā ʻōpū kanesa me ka hoʻohana ʻana i nā nui kiʻekiʻe o ka radiation. Ma muli o ka nui a me kahi o kāu ʻōpū, hiki i kāu kauka ke kuhikuhi i kēia mau mea:
- Lapaʻau radiation waho: Ma kēia, kuhikuhi ʻia nā kukuna radiation i ka puʻupuʻu mai waho o ke kino. Hiki i nā ʻenehana kūikawā, e like me ka radiation proton beam, ke kuhikuhi pololei i ka puʻupuʻu, e hōʻemi ana i ka hōʻino ʻana i ka maka a me ka ʻiʻo lolo a puni.
- Lapaʻau radiation kūloko: Pili kēia i ke kau ʻana i nā "hua" radioactive i loko o ka maka, kokoke i ka puʻupuʻu. Ua kapa nā kauka i kēia ʻano hana he radioactive plaque therapy . Aia kēia mau "hua" i loko o kahi disk metala (Plaque/Disk). Pale kēia i ka radiation mai ka hōʻino ʻana i nā ʻāpana ʻē aʻe o ka maka.
He aha nā lāʻau lapaʻau ʻē aʻe i loaʻa?
Aia kekahi mau ʻano lapaʻau ʻē aʻe:
- ʻO ka lāʻau hoʻomehana transpupillary (TTT): Hoʻohana kēia i ka wela mai nā kukuna laser e luku ai i ka puʻupuʻu.
- Endoresection: Pili kēia i ka wehe ʻana i ka puʻupuʻu mai loko mai o ka maka.
He aha nā manawa kūpono e ho'ōla ai inā loaʻa iā ʻoe kēia maʻi? (Outlook)
Ua hōʻike ʻia ma ka noiʻi ma waena o 40% a me 50% o ka poʻe me ka intraocular melanoma e laha i nā ʻāpana ʻē aʻe o ke kino. No kēlā mau hihia, ma kahi o 90% e laha i ke akepaʻa . ʻOi aku ka nui o ka laha ʻana o nā melanoma e ulu ana ma ke kino choroid a me ciliary ma mua o nā melanoma e ulu ana ma ka iris .
Akā e hoʻomanaʻo, e like me nā maʻi kanesa āpau, ʻo ka wikiwiki o ka ʻike ʻia ʻana o kēia a hoʻomaka ka mālama ʻana, ʻoi aku ka nui o ka manawa e ho'ōla ʻia ai.
Hiki iā kākou ke pale aku i kēia mai ka hana ʻana?
ʻO kaʻoiaʻiʻo, ʻaʻole hiki iā mākou ke kāohi i nā kumu pilikia he nui no ka hoʻomohala ʻana i ka melanoma intraocular, e like me ka makahiki a me ke kala o ka ʻili. Eia nō naʻe, ʻo ka mea nui loa hiki iā ʻoe ke hana, ʻo ia ke ʻike pinepine i kahi ophthalmologist a nānā i kou mau maka. Ma kēlā ala, inā he pilikia, hiki ke ʻike mua ʻia.
He aha kaʻu e hana ai inā loaʻa iaʻu kēia maʻi?
Inā ʻōlelo ke kauka he maʻi kēia kou,ʻO ka mea nui loa, ʻo ia ke kamaʻilio mau me ia a nānā pono i ke kūlana. Pono paha ʻoe e hana i nā hoʻokolohua kiʻi akepaʻa i kēlā me kēia manawa e ʻike ai inā ua laha ka maʻi kanesa. Mai hopohopo, e hāʻawi kāu kauka iā ʻoe i nā ʻōlelo aʻoaʻo a pau āu e pono ai.
He aha kaʻu e nīnau aku ai i ke kauka?
Inā loaʻa iā ʻoe ka melanoma intraocular, makemake paha ʻoe e nīnau i kāu kauka e like me:
- Pehea ka nui o ka hua?
- He aha nā lāʻau lapaʻau e kūpono iaʻu?
- E hoʻopilikia anei ka lāʻau lapaʻau i koʻu ʻike?
- Aia kekahi mau hoʻokolohua lapaʻau e hiki iaʻu ke komo?
- Hiki ke hoʻi hou mai ke kanesa ma hope o ka mālama ʻia?
Leka Lawe-Home
ʻO ka Intraocular Melanoma kahi ʻano maʻi kanesa e hoʻopilikia ana i nā cell i loko o ka maka, ʻoiai ka uvea . Hiki i nā hōʻailona ke komo pū me ka nalowale o ka ʻike a me nā loli i ke ʻano o ka maka. Hiki iā ia ke laha i nā ʻāpana ʻē aʻe o ke kino, e like me ke akepaʻa. ʻO ka radiation therapy a me ke ʻoki kino nā lāʻau lapaʻau nui. ʻOiai he maʻi kakaikahi loa kēia, he mea nui loa ka ʻike mua ʻana a me ka mālama kūpono. No laila, e mālama i kou mau maka a mai poina e hana i nā hoʻokolohua maka maʻamau.
ʻO ka Melanoma Intraocular, Kanesa Maka, Uveal Melanoma, Nā Hōʻailona Kanesa Maka, Lāʻau Kanesa Maka, Poho ʻIke











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