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Ke ʻike nei ʻoe i nā manaʻo ʻē i loko o kou kino? Malia paha he mea nui e ʻike e pili ana i ka Multiple System Atrophy (MSA)!

Ke ʻike nei ʻoe i nā manaʻo ʻē i loko o kou kino? Malia paha he mea nui e ʻike e pili ana i ka Multiple System Atrophy (MSA)!

Ke manaʻo nei paha ʻoe e loli ana nā mea i loko o kou kino i nā ʻano hiki ʻole iā ʻoe ke kaohi? I kekahi manawa ua like ia me kou nalowale ʻana i kou kaulike ke hele ʻoe, a i ʻole ʻoe e poniuniu ke kū koke ʻoe. ʻO kēia nā mea a mākou e nānā ʻole ai i kekahi manawa, akā hiki iā lākou ke lilo i mau hōʻailona o kekahi mau maʻi neurological kakaʻikahi. I kēia lā e kamaʻilio mākou e pili ana i kekahi ʻano maʻi i paʻakikī iki, akā he mea nui loa ia e makaʻala. ʻO ia ka Multiple System Atrophy (MSA) .

He aha maoli ka Multiple System Atrophy (MSA)?

I ka ʻōlelo maʻalahi, ʻo ka Multiple System Atrophy (MSA) kahi maʻi neurological laha ʻole kahi e nāwaliwali mālie ai nā ʻāpana o ko kākou lolo, ʻo ia hoʻi, e hōʻino. I ka hala ʻana o ka manawa, hoʻomaka ka hōʻino ʻana o nā hana a me nā hiki o ko kākou kino i kāohi ʻia e kēia mau ʻāpana o ka lolo. He ʻano koʻikoʻi maoli kēia, no ka mea, he paʻakikī ke hoʻōla piha mai ia mea.

I ka wā ma mua, ua kapa ʻia ʻo MSA ma nā inoa like ʻole. Ua lohe paha ʻoe i nā inoa e like me `Shy-Drager syndrome`, `Sporadic olivopontocerebellar atrophy`, `Striatonigral degeneration`. Ma hope wale nō i ʻike ai nā kauka he mau hiʻohiʻona maʻamau kēia mau kūlana a pau. ʻO ia ke kumu i hoʻohui ai lākou iā lākou a hāʻawi iā lākou i kahi inoa hou, `Multiple System Atrophy` (MSA). ʻOkoʻa nā hōʻailona ma muli o ka ʻāpana o ka lolo i hōʻino ʻia. ʻO ia ke kumu e ʻike ai kēlā me kēia kanaka i ka hui pū ʻana o nā hōʻailona.

ʻElua ʻano MSA, ʻeā? He aha lākou?

ʻAe, no ka ʻike maopopo ʻana i ke kūlana o MSA, ua hoʻokaʻawale nā ​​kauka iā ia i ʻelua ʻano nui, ma muli o nā hōʻailona e ʻike ʻia:

1. MSA-C : ʻO ke ʻano o ka 'C' ma ʻaneʻi no ka 'cerebellar'. Hoʻopilikia nui kēia ʻano i kou hiki ke hoʻonohonoho i kāu mau neʻe ʻana. ʻO ia hoʻi, nalowale kou kaulike , kahi a nā kauka i kapa ai he 'ataxia'. ʻO kēia ka hōʻailona nui o kēia ʻano. I ka manawa like, hiki iā ʻoe ke ʻike i nā pilikia me nā ʻōnaehana hoʻomalu aunoa o ke kino ('autonomic dysfunction`) a me ka hāʻule pinepine.

2. MSA-P : ʻO ke ʻano o ka 'P' ma ʻaneʻi no ka 'parkinsonism'. Ma kēia ʻano, ʻike ʻia nā hōʻailona like me ka maʻi Parkinson. ʻOiai ʻoi aku ka ʻike ʻia o kēia mau hōʻailona o Parkinson i nā pae mua, i ka hala ʻana o ka manawa, hiki ke ʻike ʻia nā pilikia me ka ʻōnaehana nerve autonomic a me nā hōʻailona o ka 'ataxia'.

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia maʻi MSA? Pehea ka maʻamau?

Hoʻopilikia pinepine ka MSA i nā pākeke ma luna o 30 mau makahiki. ʻIke nui ʻia nā hōʻailona ma waena o 50 a me 59 mau makahiki. Hiki iā ia ke hoʻopilikia i kekahi, me ka nānā ʻole i ke kāne.

Akā, he maʻi laha ʻole ka MSA. Wahi a nā loea he 0.6 a i ʻole 0.7 wale nō hihia hou no 100,000 poʻe i kēlā me kēia makahiki. Ua manaʻo ʻia ka huina o nā hihia ma waena o 3.4 a me 4.9 no 100,000. No laila hiki iā ʻoe ke ʻike i ke ʻano o kēia mea laha ʻole.

He aha ka mea e hana ʻia i ke kino me ka MSA? ʻO wai nā ʻāpana o ka lolo i hoʻopilikia ʻia?

He maʻi holomua ka MSA e hoʻopilikia ana i nā ʻāpana like ʻole o ka lolo. Pili nā hōʻailona i ka ʻāpana o ka lolo i hoʻopilikia ʻia. ʻO nā wahi nui o ka lolo i hoʻopilikia ʻia e ka MSA:

  • Nā ganglia basal : Aia kēia mau mea ma waenakonu o ka lolo. Hoʻohui lākou i nā ʻāpana like ʻole o ka lolo a kōkua iā lākou e hana pū. Ua like ia me ka lumi hoʻomalu nui o ka lolo .
  • ʻO ka lolo : ʻO kēia ka mea e kaohi i nā kaʻina hana he nui i loko o ko kākou kino. ʻO ia hoʻi, nā mea e hana koke ʻia me ka ʻole o ko kākou noʻonoʻo ʻana iā lākou, no ka laʻana, ka hanu ʻana, ka helu o ka puʻuwai, a me ke koko. He mea nui kēia no ke ola.
  • ʻO Cerebellum : Aia kēia ma ke kua o ke poʻo, ma ke kumu. ʻO ia ke kuleana nui no ka kaohi ʻana i ka neʻe ʻana a me ka mālama ʻana i ke kaulike. Hana pū ia me nā ʻāpana ʻē aʻe o ka lolo. Ke aʻo nei nā kānaka noiʻi e pili ana i kāna hana piha, akā ua hōʻike kekahi mau hōʻike e pili pū ana ia i ko kākou mau manaʻo a me ka hoʻoholo ʻana.

No laila, ke hōʻino ʻia kēia mau ʻāpana o ka lolo, ʻaʻole hiki ke hana pono ʻia nā hana i kāohi ʻia e kēlā mau ʻāpana. No ka laʻana, inā ua hōʻino ʻia ka `Brainstem`, hiki ke loaʻa nā pilikia me nā mea hana aunoa e like me ke koko.

He aha nā hōʻailona o ka MSA? Pehea mākou e ʻike ai iā lākou?

He mea maʻamau kekahi mau hōʻailona o ka MSA i nā ʻano ʻelua, a he kikoʻī kekahi i kēlā me kēia ʻano. Akā, hoʻokahi mea i maʻamau i nā ʻano ʻelua, ʻo ia ka hana pono ʻole o ke kanaka. I ka ʻōlelo maʻalahi, hele hewa nā ʻōnaehana hoʻokele ponoʻī o kou kino .

Nā hōʻailona i hoʻokumu ʻia e nā pilikia me ka ʻōnaehana nerve autonomic:

  • ʻO ka hypotension Orthostatic : ʻO kēia ka wā e hāʻule koke ai kou koko, e hoʻoulu ai i ka poniuniu , ke hoʻololi ʻoe i ke kūlana, no ka laʻana, ke kū koke ʻoe mai ka noho ʻana.
  • ʻAʻole hiki ke kāohi i ka mimi (`urinary incontinence`) a me ka hiki ʻole ke kāohi i ka ʻōpala (`fecal incontinence`).
  • ʻO ka hana pono ʻole o ka moekolohe, ʻoi aku hoʻi i nā kāne, ʻo ia ka paʻakikī o ka loaʻa ʻana o kahi kūkulu (erectile dysfunction).
  • Ka maʻi hiamoe wikiwiki o ka maka (REM) : E like me ka maʻi o Parkinson, ke moeʻuhane ʻoe, hana maoli ʻoe i nā mea āu i hana ai i kāu mau moeʻuhane. Hiki iā ʻoe ke ʻuwā a hoʻolei paha i kou mau lima.
  • Ka emi ʻana o ka hou ʻana (anhidrosis).
  • Nā pilikia ʻike.
  • Waha maloʻo.
  • ʻAneʻane hiamoe.
  • Ka lohi o ka hoʻoheheʻe ʻana a me ka paʻa ʻana o ka ʻōpū.

E noʻonoʻo e hiki ke ʻike ʻia ka nui o kēia mau hōʻailona autonomic i nā mahina, a i ʻole nā ​​​​makahiki, ma mua o ka ʻike ʻia ʻana o nā hōʻailona motor. Hana ʻia kēia ma waena o 20% a me 75% o nā maʻi MSA.

Nā ʻano noʻonoʻo a me nā naʻau

Ma kahi o ka hapakolu o ka poʻe me MSA e ʻike i nā pilikia me ko lākou hiki ke noʻonoʻo a me ka noʻonoʻo. Loaʻa iā lākou ka paʻakikī ke kāohi i ko lākou mau manaʻo. Hiki i kēia ke alakaʻi i nā pilikia olakino noʻonoʻo e like me:

  • Hopohopo.
  • Kaumaha.
  • ʻO ka paʻa ʻole o ka naʻau: ʻO ia hoʻi, e uē ana a ʻakaʻaka pono ʻole.
  • Nā hoʻouka kaua panic.
  • Nā manaʻo e hōʻeha a pepehi paha iā ʻoe iho.

Nā hiʻohiʻona e pili ana i ka neʻe ʻana

Nā ʻano o MSA-C (ʻano cerebellar):

ʻO kēia ʻano ke kumu nui o ka 'ataxia' (nalowale ke kaulike). ʻO ka 'cerebellum' kahi ʻāpana o ka lolo e pāʻani ana i kahi kuleana nui i ka hoʻomalu ʻana i nā neʻe ʻana o nā ʻiʻo. No laila, ke nalowale kēlā hoʻonohonoho ʻana, hiki ke hana ʻia nā mea e like me kēia:

  • Nā neʻe ʻana o nā lālā i kaohi ʻole ʻia a haunaele .
  • Haʻalulu hana : ʻO ke ʻano kēia ke hoʻāʻo ʻoe e hana i kekahi mea, e piʻi aʻe ka haʻalulu ma kou mau lālā.
  • Ke hele wāwae me nā wāwae ākea loa .
  • ʻO ka ʻūlū ʻana o nā maka i hiki ʻole ke kāohi ʻia (nystagmus).

Nā ʻano o ka MSA-P (ʻano Parkinsonism):

Hoʻomaka pinepine kēia ʻano hōʻailona ma kekahi ʻaoʻao o ke kino a laila laha i nā ʻaoʻao ʻelua. Penei ke ʻano o kēia mau hōʻailona:

  • Nā neʻe lohi (bradykinesia), me he mea lā ua make ke kino .
  • Manaʻo o ke ʻoʻoleʻa a me ka ʻoʻoleʻa i ke kino, e hopena ana i kahi kūlana e like me ke kūlou ʻana i mua.
  • Nā hele wāwae pinepine ʻana i ka wā e hele ana.
  • Ke kūpikipikiʻō nei i ka wā e ʻōlelo ana, ka ʻōlelo maopopo ʻole .

No ke aha e hana ʻia ai kēia MSA? He aha ke kumu?

ʻAʻole ʻike ʻia ke kumu kikoʻī o MSA , akā manaʻo nā loea e pili ana ia i kahi protein kūikawā i kapa ʻia ʻo `alpha-synuclein`, hiki ke hōʻiliʻili ma nā ʻāpana like ʻole o ko kākou lolo. Ua manaʻo ʻia hoʻi kēia protein like ke kumu nui o ka maʻi Parkinson.

He mau kemika koʻikoʻi nā protein no ko kākou kino e hana. Kōkua lākou i nā mea he nui, e like me ke kamaʻilio ʻana ma waena o nā ʻōnaehana like ʻole o ke kino a me ka lawe ʻana i nā hui kemika a puni. Eia nō naʻe, inā hōʻiliʻili kēia mau protein ma nā wahi kūpono ʻole, hiki iā lākou ke hōʻino. Manaʻo nā loea ʻo kēia hōʻino ke kumu o ka make mālie ʻana o ka ʻiʻo o ka lolo ma MSA.

Ke noiʻi nei nā kānaka ʻepekema i ke kumu e hōʻiliʻili ai kēia protein 'alpha-synuclein' ma kekahi mau wahi o ka lolo. Manaʻo pū lākou e hoʻololi paha kekahi mau hoʻololi genetic i ke ʻano o ka hoʻohana ʻana o kekahi mau cell i kēia 'alpha-synuclein'. Aia kekahi hōʻike e holo ana ke ʻano MSA-C i loko o nā ʻohana. Eia nō naʻe, ʻaʻohe loulou genetic i loaʻa no ke ʻano MSA-P.

ʻO ka mea nui loa, ʻaʻole he maʻi lele ka MSA . ʻAʻole hiki iā ʻoe ke loaʻa mai kekahi mea ʻē aʻe, ʻaʻole hoʻi hiki iā ʻoe ke hoʻolaha aku i kekahi.

Pehea ʻoe e ʻike pono ai inā loaʻa iā ʻoe ka MSA? He aha nā hoʻokolohua e hana ʻia?

Aia ka MSAʻO ke ala wale nō e maopopo ai he 100%, ʻo ia ke nānā ʻana i nā ʻiʻo o ka lolo ma hope o ka make ʻana o kekahi, no ka mea, ʻaʻohe ala e ʻike pono ai inā ua hōʻiliʻili ʻia ka 'alpha-synuclein' ma nā wahi o ka lolo i ka wā e ola ana kekahi.

ʻOiai ke ola nei kekahi, kānalua nā kauka i ka MSA ma muli o nā hōʻailona, ​​​​ka mōʻaukala lapaʻau, ka mōʻaukala ʻohana, a inā paha e pane lākou i kekahi mau lāʻau lapaʻau. ʻO ka pinepine, ʻo ka maʻi Parkinson a i ʻole kekahi maʻi neʻe like ʻē aʻe, a hoʻololi ʻia ka hōʻailona i MSA ma hope ke ulu aʻe nā hōʻailona hou a i ʻole e pau ka hana ʻana o kekahi mau lāʻau lapaʻau.

Aia kekahi mau hiʻohiʻona koʻikoʻi e hiki ke hoʻokaʻawale i ka MSA mai ka maʻi o Parkinson:

  • Holo wikiwiki ka MSA : He mau makahiki no kekahi me ka maʻi Parkinson e hoʻomohala i nā pilikia me ka ʻōnaehana nerve autonomic. Akā i loko o MSA, hiki i kēia mau pilikia ke hoʻomaka i loko o hoʻokahi makahiki.
  • ʻIke ʻokoʻa kekahi mau hōʻailona : ʻOi aku ka koʻikoʻi o nā hōʻailona o ka ʻōnaehana nerve autonomic i ka MSA. Eia nō naʻe, ʻoi aku ka liʻiliʻi o ka koʻikoʻi o nā mea e like me ka haʻalulu, a ʻaʻole paha. Hiki ke ʻokoʻa ke ʻano o ka laha ʻana o nā hōʻailona ma ke kino holoʻokoʻa.
  • ʻAʻole holo pono nā lāʻau lapaʻau : ʻO Levodopa ka lāʻau lapaʻau nui no ka maʻi Parkinson. Eia nō naʻe, ʻaʻole maikaʻi ka levodopa i ka MSA. ʻO kēia ke kumu nui e manaʻo ai nā kauka he MSA paha ia a ʻaʻole ʻo Parkinson.

He aha nā hoʻokolohua e hana ʻia nei no kēia?

He kakaikahi loa nā hoʻokolohua e kōkua pololei i ka ʻike ʻana i ka MSA. Hana ʻia ka hapa nui o nā hoʻokolohua e kāpae i nā maʻi ʻē aʻe a e hōʻiliʻili i nā hōʻike hou aʻe e kākoʻo i ke kānalua he MSA paha ia. ʻO kekahi o kēia mau mea:

  • ʻO ke kiʻi ʻana i ka resonance imaging (MRI) : Hiki i kēia ke hōʻike i nā wahi o ka lolo i hōʻino ʻia. Hiki i kēia ke kōkua i ka hana ʻana i kahi hōʻailona pololei. He mea pono nō hoʻi ia i ka ʻike ʻana i ka MSA-C, no ka mea hiki iā ia ke hōʻike i kahi ʻano kaha keʻa ma kahi ʻāpana o ka lolo (ka hōʻailona "hot cross bun"). Eia nō naʻe, hiki ke ʻike ʻia kēia hōʻailona i nā maʻi ʻē aʻe, no laila ʻaʻole lawa ka ʻike ʻana i ka MSA ma kāna iho.
  • Hoʻāʻo ʻana i ka genetic : Hiki i kēia ke nānā i kahi mutation genetic e hoʻopilikia i ke ʻano o ke kino o ke kanaka e hana ai i ka alpha-synuclein. ʻOi aku ka maʻalahi o kēia mau hoʻāʻo e ʻike i nā mutation genetic e pili ana me MSA-C i waena o ka poʻe Kepanī.
  • ʻO ka biopsy ʻili : Hiki i kekahi mau ʻano biopsy ʻili ke ʻike i nā hōʻailona o ka hōʻiliʻili ʻana o ka alpha-synuclein i loko o nā ʻiʻo nerve. Eia nō naʻe, pono ka noiʻi hou aku e hoʻoholo ai inā he pono kēia e lilo i ʻāpana maʻamau o ke kaʻina hana diagnostic.

E haʻi aku kāu kauka iā ʻoe e pili ana i nā hoʻokolohua ʻē aʻe e kūpono a pehea e hiki ai iā lākou ke kōkua iā ʻoe. E noʻonoʻo lākou i kou mōʻaukala olakino, ka mōʻaukala ʻohana, a me nā mea ʻē aʻe e hana i ka hoʻoholo maikaʻi loa nāu.

Aia kekahi lāʻau lapaʻau no ka MSA? Hiki ke ho'ōla ʻia?

I kēia manawa, ʻaʻohe lāʻau lapaʻau i loaʻa no ka MSA.No laila, ʻo ke kumu nui o ka mālama ʻana, ʻo ia ke kāohi ʻana i nā hōʻailona no ka lōʻihi e hiki ai. ʻO ka mālama ʻana no nā hōʻailona MSA e pili ana i nā kumu he nui, me nā hōʻailona o ka mea maʻi a me ko lākou koʻikoʻi.

He aha nā lāʻau lapaʻau a i ʻole nā ​​​​​​lāʻau lapaʻau i hoʻohana ʻia?

Nui nā ʻano lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i nā hōʻailona o MSA. ʻO ke ʻano o ka lāʻau lapaʻau āu e loaʻa ai e hilinaʻi ia i kāu mau hōʻailona a me nā kumu ʻē aʻe. ʻO kāu kauka ke kanaka maikaʻi loa e ʻōlelo aku i ka lāʻau lapaʻau maikaʻi loa nāu, no ka mea, ʻo lākou ka poʻe ʻike nui loa i kou kūlana. E wehewehe pū lākou iā ʻoe i nā hopena ʻaoʻao o nā lāʻau lapaʻau.

He mea nui: He kūlana ka MSA i hiki ke ʻike ʻia e ke kauka i aʻo ʻia a mākaukau hoʻi. No laila, mai hoʻāʻo e ʻike a mālama paha i nā hōʻailona iā ʻoe iho me ka ʻole o ke kamaʻilio ʻana me ke kauka.

Aia kekahi ala e pale ai i ka hoʻomohala ʻana o MSA?

ʻAʻole ʻike ka poʻe loea i ke kumu o ka MSA a i ʻole nā ​​​​​​mea e kōkua ai iā ia. No laila, ʻaʻohe ala e pale aku ai a hōʻemi paha i ka pilikia i kēia manawa .

He aha ke ʻano o ka wā e hiki mai ana e hiki i kekahi me MSA ke manaʻo?

ʻO ka maʻamau, ʻike mua ka poʻe me MSA i nā hōʻailona e pili ana i ka neʻe ʻana. Ke ʻoi aku ka ʻino o kēia kūlana i ka hala ʻana o ka manawa. Ma kahi o ka hapalua o nā maʻi e pono ai ke kōkua i ka hele wāwae ʻana i kēia manawa. ʻO ia hoʻi ka hoʻohana ʻana i ke koʻokoʻo a i ʻole ka mea hele wāwae. Ma kahi o ʻelima mau makahiki ma hope o ka hoʻomaka ʻana o MSA, ma kahi o 60% o nā maʻi e pono ai e hoʻohana i ka noho huila. I loko o ʻeono a ʻewalu mau makahiki, ma ka liʻiliʻi o ka hapalua o nā maʻi e hoʻopaʻa ʻia ma kahi moe.

I ka holomua ʻana o ka maʻi, pono paha nā kaʻina hana hou a i ʻole nā ​​hana komo e mālama i nā hana o ke kino a pale i nā pilikia weliweli. ʻO kekahi o kēia mau mea:

  • ʻO Tracheostomy e mālama i ka hanu ʻana.
  • ʻO ka hānai ʻana ma o kahi ʻōmole ('Tube feeding' / `enteral nutrition`).
  • Nā catheters noho indwelling a i ʻole urostomy no ka incontinence urinary.
  • ʻO Colostomy no nā pilikia o ka neʻe ʻana o ka ʻōpū.

Pehea ka lōʻihi o ka MSA?

He maʻi mau loa ka MSA no ke ola holoʻokoʻa. ʻO ka awelika o ke ola me ka maʻi he ʻeono a ʻumi mau makahiki . I nā hihia ʻoi aku ka ʻino, hiki ke mau a hiki i 15 mau makahiki. Eia nō naʻe, i nā hihia ʻoi aku ka ʻino, hiki ke pōkole loa ke ola. ʻO kēia mau hihia koʻikoʻi ka maʻamau e komo pū me kēia mau hōʻailona:

  • Lilo nā hōʻailona o ka ʻōnaehana nerve autonomic i mea koʻikoʻi ma mua o ka hoʻomaka ʻana o nā hōʻailona pili i ka neʻe ʻana.
  • Ka ʻelemakule i ka wā i ʻike ʻia ai.
  • Loaʻa nā hōʻailona neʻe e hoʻoulu ai i ka hāʻule pinepine.

He aha ka manaʻo no kēia kūlana?

ʻAʻole maikaʻi loa ka nānā ʻana no ka MSA. Ke ʻoi aku ka ʻino o nā hōʻailona o kēia maʻi, e hoʻopilikia pinepine ana i nā hana o ke kino a alakaʻi i nā pilikia make. ʻO nā pilikia e hiki ai ke alakaʻi i ka make:

  • Pneumonia.
  • Hiki i nā maʻi ʻaʻai mimi (UTI) ke hana i ka sepsis (ka lāʻau make koko).
  • Ka make koke (pinepine i ka pō, ma muli o nā haunaele i ke ʻano o ka lolo e kaohi ai i ka hanu ʻana i ka wā hiamoe).

Pehea wau e mālama ai iaʻu iho/kaʻu mea aloha? He aha kaʻu mea e hopohopo ai?

Loaʻa i ka poʻe me MSA nā hōʻailona holomua. ʻO ke ʻano kēia, i ka wā e hiki ai nā hōʻailona i kahi pae, ʻaʻole hiki iā lākou ke noho kūʻokoʻa. Hiki i ke kūlana ke hoʻopilikia i kou hiki ke noʻonoʻo, ʻōlelo, a hoʻoholo i nā hoʻoholo nou iho. Ma muli o kēia mau mea āpau, he mea nui e kamaʻilio me kāu poʻe aloha e pili ana i kāu mau makemake no ka wā e hiki mai ana a e hana i kahi hoʻolālā no kāu mālama olakino inā ʻaʻole hiki iā ʻoe ke hoʻoholo .

Āhea ʻoe e ʻike ai i ke kauka?

He nui nā hōʻailona mua o MSA he mau mea āu e kūkākūkā ai me ke kauka. ʻO kēia mau mea:

  • Moekolohe.
  • ʻO ka hypotension Orthostatic (ka dizziness mau a i ʻole ka nāwaliwali no ke kumu ʻole).
  • Nā pilikia hiamoe a me ka apnea hiamoe (ka hanu ʻana i ka wā hiamoe).

Inā ʻike ke kauka iā ʻoe me kahi maʻi neʻe e like me ka maʻi Parkinson, he mea nui e kamaʻilio me lākou e pili ana i nā loli i kāu mau hōʻailona. E hoʻonohonoho kāu kauka i nā kipa hahai e nānā i kou kūlana a hoʻoponopono i kāu lāʻau lapaʻau. Hiki iā ʻoe ke kamaʻilio e pili ana i nā loli āu e ʻike ai i kēia mau kipa. He mea maʻamau no ka poʻe i ʻike ʻia me ka maʻi Parkinson ke hoʻololi i kā lākou hōʻailona ma hope, i ka wā e ulu ai nā hōʻailona hou a i ʻole i ka wā e pau ai ka hana pono ʻana o ka levodopa.

ʻIke pinepine ka poʻe me MSA i nā hōʻailona ʻē aʻe, ʻoiai nā pilikia olakino noʻonoʻo. He mea nui e ʻimi i ka lāʻau no nā pilikia olakino noʻonoʻo e pili ana i ka MSA, a me nā hōʻailona kino. Hiki i kāu kauka ke ʻōlelo i ka lāʻau a kuhikuhi paha iā ʻoe i kahi loea olakino noʻonoʻo.

I ka hōʻuluʻulu manaʻo (Leka Lawe-Home)

He maʻi koʻikoʻi ka Multiple System Atrophy (MSA) a he maʻi make loa ia. ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau pololei a lāʻau lapaʻau paha no kēia maʻi i kēia manawa.

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Eia nō naʻe, hiki ke mālama ʻia ka nui o kona mau hōʻailona , ​​a aia nā ala e hōʻemi ai i nā hopena a me nā hōʻailona. Me ka mālama ʻana, hiki i nā poʻe he nui ke mālama i ko lākou ola maikaʻi no nā makahiki, hoʻolilo i ka manawa waiwai me nā mea aloha, a hoʻohana pono i ko lākou manawa. No laila, he mea nui e hoʻokele i nā hōʻailona me ka ʻōlelo aʻoaʻo lapaʻau kūpono, me ka ʻole o ka hoʻonāukiuki.


`ʻO ka Atrophy Pūnaehana Nui, MSA, Maʻi Neurological, Maʻi Lolo, Nā Hōʻailona o Parkinson, Nā Maʻi Neʻe, Nā Pilikia o ka ʻŌnaehana Nervous Autonomic

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua e hana ʻia nei no kēia?

He kakaikahi loa nā hoʻokolohua e kōkua pololei i ka ʻike ʻana i ka MSA. Hana ʻia ka hapa nui o nā hoʻokolohua e kāpae i nā maʻi ʻē aʻe a e hōʻiliʻili i nā hōʻike hou aʻe e kākoʻo i ke kānalua he MSA paha ia. ʻO kekahi o kēia mau mea:

He aha nā lāʻau lapaʻau a i ʻole nā ​​​​​​lāʻau lapaʻau i hoʻohana ʻia?

Nui nā ʻano lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i nā hōʻailona o MSA. ʻO ke ʻano o ka lāʻau lapaʻau āu e loaʻa ai e hilinaʻi ia i kāu mau hōʻailona a me nā kumu ʻē aʻe. ʻO kāu kauka ke kanaka maikaʻi loa e ʻōlelo aku i ka lāʻau lapaʻau maikaʻi loa nāu, no ka mea, ʻo lākou ka poʻe ʻike nui loa i kou kūlana. E wehewehe pū lākou iā ʻoe i nā hopena ʻaoʻao o nā lāʻau lapaʻau.

He aha ka manaʻo no kēia kūlana?

ʻAʻole maikaʻi loa ka nānā ʻana no ka MSA. Ke ʻoi aku ka ʻino o nā hōʻailona o kēia maʻi, e hoʻopilikia pinepine ana i nā hana o ke kino a alakaʻi i nā pilikia make. ʻO nā pilikia e hiki ai ke alakaʻi i ka make:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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E ʻoluʻolu e helu: 9 + 9 =
Ke ʻike nei ʻoe i nā manaʻo ʻē i loko o kou kino? Malia paha he mea nui e ʻike e pili ana i ka Multiple System Atrophy (MSA)!

Ke ʻike nei ʻoe i nā manaʻo ʻē i loko o kou kino? Malia paha he mea nui e ʻike e pili ana i ka Multiple System Atrophy (MSA)!

Ke manaʻo nei paha ʻoe e loli ana nā mea i loko o kou kino i nā ʻano hiki ʻole iā ʻoe ke kaohi? I kekahi manawa ua like ia me kou nalowale ʻana i kou kaulike ke hele ʻoe, a i ʻole ʻoe e poniuniu ke kū koke ʻoe. ʻO kēia nā mea a mākou e nānā ʻole ai i kekahi manawa, akā hiki iā lākou ke lilo i mau hōʻailona o kekahi mau maʻi neurological kakaʻikahi. I kēia lā e kamaʻilio mākou e pili ana i kekahi ʻano maʻi i paʻakikī iki, akā he mea nui loa ia e makaʻala. ʻO ia ka Multiple System Atrophy (MSA) .

He aha maoli ka Multiple System Atrophy (MSA)?

I ka ʻōlelo maʻalahi, ʻo ka Multiple System Atrophy (MSA) kahi maʻi neurological laha ʻole kahi e nāwaliwali mālie ai nā ʻāpana o ko kākou lolo, ʻo ia hoʻi, e hōʻino. I ka hala ʻana o ka manawa, hoʻomaka ka hōʻino ʻana o nā hana a me nā hiki o ko kākou kino i kāohi ʻia e kēia mau ʻāpana o ka lolo. He ʻano koʻikoʻi maoli kēia, no ka mea, he paʻakikī ke hoʻōla piha mai ia mea.

I ka wā ma mua, ua kapa ʻia ʻo MSA ma nā inoa like ʻole. Ua lohe paha ʻoe i nā inoa e like me `Shy-Drager syndrome`, `Sporadic olivopontocerebellar atrophy`, `Striatonigral degeneration`. Ma hope wale nō i ʻike ai nā kauka he mau hiʻohiʻona maʻamau kēia mau kūlana a pau. ʻO ia ke kumu i hoʻohui ai lākou iā lākou a hāʻawi iā lākou i kahi inoa hou, `Multiple System Atrophy` (MSA). ʻOkoʻa nā hōʻailona ma muli o ka ʻāpana o ka lolo i hōʻino ʻia. ʻO ia ke kumu e ʻike ai kēlā me kēia kanaka i ka hui pū ʻana o nā hōʻailona.

ʻElua ʻano MSA, ʻeā? He aha lākou?

ʻAe, no ka ʻike maopopo ʻana i ke kūlana o MSA, ua hoʻokaʻawale nā ​​kauka iā ia i ʻelua ʻano nui, ma muli o nā hōʻailona e ʻike ʻia:

1. MSA-C : ʻO ke ʻano o ka 'C' ma ʻaneʻi no ka 'cerebellar'. Hoʻopilikia nui kēia ʻano i kou hiki ke hoʻonohonoho i kāu mau neʻe ʻana. ʻO ia hoʻi, nalowale kou kaulike , kahi a nā kauka i kapa ai he 'ataxia'. ʻO kēia ka hōʻailona nui o kēia ʻano. I ka manawa like, hiki iā ʻoe ke ʻike i nā pilikia me nā ʻōnaehana hoʻomalu aunoa o ke kino ('autonomic dysfunction`) a me ka hāʻule pinepine.

2. MSA-P : ʻO ke ʻano o ka 'P' ma ʻaneʻi no ka 'parkinsonism'. Ma kēia ʻano, ʻike ʻia nā hōʻailona like me ka maʻi Parkinson. ʻOiai ʻoi aku ka ʻike ʻia o kēia mau hōʻailona o Parkinson i nā pae mua, i ka hala ʻana o ka manawa, hiki ke ʻike ʻia nā pilikia me ka ʻōnaehana nerve autonomic a me nā hōʻailona o ka 'ataxia'.

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia maʻi MSA? Pehea ka maʻamau?

Hoʻopilikia pinepine ka MSA i nā pākeke ma luna o 30 mau makahiki. ʻIke nui ʻia nā hōʻailona ma waena o 50 a me 59 mau makahiki. Hiki iā ia ke hoʻopilikia i kekahi, me ka nānā ʻole i ke kāne.

Akā, he maʻi laha ʻole ka MSA. Wahi a nā loea he 0.6 a i ʻole 0.7 wale nō hihia hou no 100,000 poʻe i kēlā me kēia makahiki. Ua manaʻo ʻia ka huina o nā hihia ma waena o 3.4 a me 4.9 no 100,000. No laila hiki iā ʻoe ke ʻike i ke ʻano o kēia mea laha ʻole.

He aha ka mea e hana ʻia i ke kino me ka MSA? ʻO wai nā ʻāpana o ka lolo i hoʻopilikia ʻia?

He maʻi holomua ka MSA e hoʻopilikia ana i nā ʻāpana like ʻole o ka lolo. Pili nā hōʻailona i ka ʻāpana o ka lolo i hoʻopilikia ʻia. ʻO nā wahi nui o ka lolo i hoʻopilikia ʻia e ka MSA:

  • Nā ganglia basal : Aia kēia mau mea ma waenakonu o ka lolo. Hoʻohui lākou i nā ʻāpana like ʻole o ka lolo a kōkua iā lākou e hana pū. Ua like ia me ka lumi hoʻomalu nui o ka lolo .
  • ʻO ka lolo : ʻO kēia ka mea e kaohi i nā kaʻina hana he nui i loko o ko kākou kino. ʻO ia hoʻi, nā mea e hana koke ʻia me ka ʻole o ko kākou noʻonoʻo ʻana iā lākou, no ka laʻana, ka hanu ʻana, ka helu o ka puʻuwai, a me ke koko. He mea nui kēia no ke ola.
  • ʻO Cerebellum : Aia kēia ma ke kua o ke poʻo, ma ke kumu. ʻO ia ke kuleana nui no ka kaohi ʻana i ka neʻe ʻana a me ka mālama ʻana i ke kaulike. Hana pū ia me nā ʻāpana ʻē aʻe o ka lolo. Ke aʻo nei nā kānaka noiʻi e pili ana i kāna hana piha, akā ua hōʻike kekahi mau hōʻike e pili pū ana ia i ko kākou mau manaʻo a me ka hoʻoholo ʻana.

No laila, ke hōʻino ʻia kēia mau ʻāpana o ka lolo, ʻaʻole hiki ke hana pono ʻia nā hana i kāohi ʻia e kēlā mau ʻāpana. No ka laʻana, inā ua hōʻino ʻia ka `Brainstem`, hiki ke loaʻa nā pilikia me nā mea hana aunoa e like me ke koko.

He aha nā hōʻailona o ka MSA? Pehea mākou e ʻike ai iā lākou?

He mea maʻamau kekahi mau hōʻailona o ka MSA i nā ʻano ʻelua, a he kikoʻī kekahi i kēlā me kēia ʻano. Akā, hoʻokahi mea i maʻamau i nā ʻano ʻelua, ʻo ia ka hana pono ʻole o ke kanaka. I ka ʻōlelo maʻalahi, hele hewa nā ʻōnaehana hoʻokele ponoʻī o kou kino .

Nā hōʻailona i hoʻokumu ʻia e nā pilikia me ka ʻōnaehana nerve autonomic:

  • ʻO ka hypotension Orthostatic : ʻO kēia ka wā e hāʻule koke ai kou koko, e hoʻoulu ai i ka poniuniu , ke hoʻololi ʻoe i ke kūlana, no ka laʻana, ke kū koke ʻoe mai ka noho ʻana.
  • ʻAʻole hiki ke kāohi i ka mimi (`urinary incontinence`) a me ka hiki ʻole ke kāohi i ka ʻōpala (`fecal incontinence`).
  • ʻO ka hana pono ʻole o ka moekolohe, ʻoi aku hoʻi i nā kāne, ʻo ia ka paʻakikī o ka loaʻa ʻana o kahi kūkulu (erectile dysfunction).
  • Ka maʻi hiamoe wikiwiki o ka maka (REM) : E like me ka maʻi o Parkinson, ke moeʻuhane ʻoe, hana maoli ʻoe i nā mea āu i hana ai i kāu mau moeʻuhane. Hiki iā ʻoe ke ʻuwā a hoʻolei paha i kou mau lima.
  • Ka emi ʻana o ka hou ʻana (anhidrosis).
  • Nā pilikia ʻike.
  • Waha maloʻo.
  • ʻAneʻane hiamoe.
  • Ka lohi o ka hoʻoheheʻe ʻana a me ka paʻa ʻana o ka ʻōpū.

E noʻonoʻo e hiki ke ʻike ʻia ka nui o kēia mau hōʻailona autonomic i nā mahina, a i ʻole nā ​​​​makahiki, ma mua o ka ʻike ʻia ʻana o nā hōʻailona motor. Hana ʻia kēia ma waena o 20% a me 75% o nā maʻi MSA.

Nā ʻano noʻonoʻo a me nā naʻau

Ma kahi o ka hapakolu o ka poʻe me MSA e ʻike i nā pilikia me ko lākou hiki ke noʻonoʻo a me ka noʻonoʻo. Loaʻa iā lākou ka paʻakikī ke kāohi i ko lākou mau manaʻo. Hiki i kēia ke alakaʻi i nā pilikia olakino noʻonoʻo e like me:

  • Hopohopo.
  • Kaumaha.
  • ʻO ka paʻa ʻole o ka naʻau: ʻO ia hoʻi, e uē ana a ʻakaʻaka pono ʻole.
  • Nā hoʻouka kaua panic.
  • Nā manaʻo e hōʻeha a pepehi paha iā ʻoe iho.

Nā hiʻohiʻona e pili ana i ka neʻe ʻana

Nā ʻano o MSA-C (ʻano cerebellar):

ʻO kēia ʻano ke kumu nui o ka 'ataxia' (nalowale ke kaulike). ʻO ka 'cerebellum' kahi ʻāpana o ka lolo e pāʻani ana i kahi kuleana nui i ka hoʻomalu ʻana i nā neʻe ʻana o nā ʻiʻo. No laila, ke nalowale kēlā hoʻonohonoho ʻana, hiki ke hana ʻia nā mea e like me kēia:

  • Nā neʻe ʻana o nā lālā i kaohi ʻole ʻia a haunaele .
  • Haʻalulu hana : ʻO ke ʻano kēia ke hoʻāʻo ʻoe e hana i kekahi mea, e piʻi aʻe ka haʻalulu ma kou mau lālā.
  • Ke hele wāwae me nā wāwae ākea loa .
  • ʻO ka ʻūlū ʻana o nā maka i hiki ʻole ke kāohi ʻia (nystagmus).

Nā ʻano o ka MSA-P (ʻano Parkinsonism):

Hoʻomaka pinepine kēia ʻano hōʻailona ma kekahi ʻaoʻao o ke kino a laila laha i nā ʻaoʻao ʻelua. Penei ke ʻano o kēia mau hōʻailona:

  • Nā neʻe lohi (bradykinesia), me he mea lā ua make ke kino .
  • Manaʻo o ke ʻoʻoleʻa a me ka ʻoʻoleʻa i ke kino, e hopena ana i kahi kūlana e like me ke kūlou ʻana i mua.
  • Nā hele wāwae pinepine ʻana i ka wā e hele ana.
  • Ke kūpikipikiʻō nei i ka wā e ʻōlelo ana, ka ʻōlelo maopopo ʻole .

No ke aha e hana ʻia ai kēia MSA? He aha ke kumu?

ʻAʻole ʻike ʻia ke kumu kikoʻī o MSA , akā manaʻo nā loea e pili ana ia i kahi protein kūikawā i kapa ʻia ʻo `alpha-synuclein`, hiki ke hōʻiliʻili ma nā ʻāpana like ʻole o ko kākou lolo. Ua manaʻo ʻia hoʻi kēia protein like ke kumu nui o ka maʻi Parkinson.

He mau kemika koʻikoʻi nā protein no ko kākou kino e hana. Kōkua lākou i nā mea he nui, e like me ke kamaʻilio ʻana ma waena o nā ʻōnaehana like ʻole o ke kino a me ka lawe ʻana i nā hui kemika a puni. Eia nō naʻe, inā hōʻiliʻili kēia mau protein ma nā wahi kūpono ʻole, hiki iā lākou ke hōʻino. Manaʻo nā loea ʻo kēia hōʻino ke kumu o ka make mālie ʻana o ka ʻiʻo o ka lolo ma MSA.

Ke noiʻi nei nā kānaka ʻepekema i ke kumu e hōʻiliʻili ai kēia protein 'alpha-synuclein' ma kekahi mau wahi o ka lolo. Manaʻo pū lākou e hoʻololi paha kekahi mau hoʻololi genetic i ke ʻano o ka hoʻohana ʻana o kekahi mau cell i kēia 'alpha-synuclein'. Aia kekahi hōʻike e holo ana ke ʻano MSA-C i loko o nā ʻohana. Eia nō naʻe, ʻaʻohe loulou genetic i loaʻa no ke ʻano MSA-P.

ʻO ka mea nui loa, ʻaʻole he maʻi lele ka MSA . ʻAʻole hiki iā ʻoe ke loaʻa mai kekahi mea ʻē aʻe, ʻaʻole hoʻi hiki iā ʻoe ke hoʻolaha aku i kekahi.

Pehea ʻoe e ʻike pono ai inā loaʻa iā ʻoe ka MSA? He aha nā hoʻokolohua e hana ʻia?

Aia ka MSAʻO ke ala wale nō e maopopo ai he 100%, ʻo ia ke nānā ʻana i nā ʻiʻo o ka lolo ma hope o ka make ʻana o kekahi, no ka mea, ʻaʻohe ala e ʻike pono ai inā ua hōʻiliʻili ʻia ka 'alpha-synuclein' ma nā wahi o ka lolo i ka wā e ola ana kekahi.

ʻOiai ke ola nei kekahi, kānalua nā kauka i ka MSA ma muli o nā hōʻailona, ​​​​ka mōʻaukala lapaʻau, ka mōʻaukala ʻohana, a inā paha e pane lākou i kekahi mau lāʻau lapaʻau. ʻO ka pinepine, ʻo ka maʻi Parkinson a i ʻole kekahi maʻi neʻe like ʻē aʻe, a hoʻololi ʻia ka hōʻailona i MSA ma hope ke ulu aʻe nā hōʻailona hou a i ʻole e pau ka hana ʻana o kekahi mau lāʻau lapaʻau.

Aia kekahi mau hiʻohiʻona koʻikoʻi e hiki ke hoʻokaʻawale i ka MSA mai ka maʻi o Parkinson:

  • Holo wikiwiki ka MSA : He mau makahiki no kekahi me ka maʻi Parkinson e hoʻomohala i nā pilikia me ka ʻōnaehana nerve autonomic. Akā i loko o MSA, hiki i kēia mau pilikia ke hoʻomaka i loko o hoʻokahi makahiki.
  • ʻIke ʻokoʻa kekahi mau hōʻailona : ʻOi aku ka koʻikoʻi o nā hōʻailona o ka ʻōnaehana nerve autonomic i ka MSA. Eia nō naʻe, ʻoi aku ka liʻiliʻi o ka koʻikoʻi o nā mea e like me ka haʻalulu, a ʻaʻole paha. Hiki ke ʻokoʻa ke ʻano o ka laha ʻana o nā hōʻailona ma ke kino holoʻokoʻa.
  • ʻAʻole holo pono nā lāʻau lapaʻau : ʻO Levodopa ka lāʻau lapaʻau nui no ka maʻi Parkinson. Eia nō naʻe, ʻaʻole maikaʻi ka levodopa i ka MSA. ʻO kēia ke kumu nui e manaʻo ai nā kauka he MSA paha ia a ʻaʻole ʻo Parkinson.

He aha nā hoʻokolohua e hana ʻia nei no kēia?

He kakaikahi loa nā hoʻokolohua e kōkua pololei i ka ʻike ʻana i ka MSA. Hana ʻia ka hapa nui o nā hoʻokolohua e kāpae i nā maʻi ʻē aʻe a e hōʻiliʻili i nā hōʻike hou aʻe e kākoʻo i ke kānalua he MSA paha ia. ʻO kekahi o kēia mau mea:

  • ʻO ke kiʻi ʻana i ka resonance imaging (MRI) : Hiki i kēia ke hōʻike i nā wahi o ka lolo i hōʻino ʻia. Hiki i kēia ke kōkua i ka hana ʻana i kahi hōʻailona pololei. He mea pono nō hoʻi ia i ka ʻike ʻana i ka MSA-C, no ka mea hiki iā ia ke hōʻike i kahi ʻano kaha keʻa ma kahi ʻāpana o ka lolo (ka hōʻailona "hot cross bun"). Eia nō naʻe, hiki ke ʻike ʻia kēia hōʻailona i nā maʻi ʻē aʻe, no laila ʻaʻole lawa ka ʻike ʻana i ka MSA ma kāna iho.
  • Hoʻāʻo ʻana i ka genetic : Hiki i kēia ke nānā i kahi mutation genetic e hoʻopilikia i ke ʻano o ke kino o ke kanaka e hana ai i ka alpha-synuclein. ʻOi aku ka maʻalahi o kēia mau hoʻāʻo e ʻike i nā mutation genetic e pili ana me MSA-C i waena o ka poʻe Kepanī.
  • ʻO ka biopsy ʻili : Hiki i kekahi mau ʻano biopsy ʻili ke ʻike i nā hōʻailona o ka hōʻiliʻili ʻana o ka alpha-synuclein i loko o nā ʻiʻo nerve. Eia nō naʻe, pono ka noiʻi hou aku e hoʻoholo ai inā he pono kēia e lilo i ʻāpana maʻamau o ke kaʻina hana diagnostic.

E haʻi aku kāu kauka iā ʻoe e pili ana i nā hoʻokolohua ʻē aʻe e kūpono a pehea e hiki ai iā lākou ke kōkua iā ʻoe. E noʻonoʻo lākou i kou mōʻaukala olakino, ka mōʻaukala ʻohana, a me nā mea ʻē aʻe e hana i ka hoʻoholo maikaʻi loa nāu.

Aia kekahi lāʻau lapaʻau no ka MSA? Hiki ke ho'ōla ʻia?

I kēia manawa, ʻaʻohe lāʻau lapaʻau i loaʻa no ka MSA.No laila, ʻo ke kumu nui o ka mālama ʻana, ʻo ia ke kāohi ʻana i nā hōʻailona no ka lōʻihi e hiki ai. ʻO ka mālama ʻana no nā hōʻailona MSA e pili ana i nā kumu he nui, me nā hōʻailona o ka mea maʻi a me ko lākou koʻikoʻi.

He aha nā lāʻau lapaʻau a i ʻole nā ​​​​​​lāʻau lapaʻau i hoʻohana ʻia?

Nui nā ʻano lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i nā hōʻailona o MSA. ʻO ke ʻano o ka lāʻau lapaʻau āu e loaʻa ai e hilinaʻi ia i kāu mau hōʻailona a me nā kumu ʻē aʻe. ʻO kāu kauka ke kanaka maikaʻi loa e ʻōlelo aku i ka lāʻau lapaʻau maikaʻi loa nāu, no ka mea, ʻo lākou ka poʻe ʻike nui loa i kou kūlana. E wehewehe pū lākou iā ʻoe i nā hopena ʻaoʻao o nā lāʻau lapaʻau.

He mea nui: He kūlana ka MSA i hiki ke ʻike ʻia e ke kauka i aʻo ʻia a mākaukau hoʻi. No laila, mai hoʻāʻo e ʻike a mālama paha i nā hōʻailona iā ʻoe iho me ka ʻole o ke kamaʻilio ʻana me ke kauka.

Aia kekahi ala e pale ai i ka hoʻomohala ʻana o MSA?

ʻAʻole ʻike ka poʻe loea i ke kumu o ka MSA a i ʻole nā ​​​​​​mea e kōkua ai iā ia. No laila, ʻaʻohe ala e pale aku ai a hōʻemi paha i ka pilikia i kēia manawa .

He aha ke ʻano o ka wā e hiki mai ana e hiki i kekahi me MSA ke manaʻo?

ʻO ka maʻamau, ʻike mua ka poʻe me MSA i nā hōʻailona e pili ana i ka neʻe ʻana. Ke ʻoi aku ka ʻino o kēia kūlana i ka hala ʻana o ka manawa. Ma kahi o ka hapalua o nā maʻi e pono ai ke kōkua i ka hele wāwae ʻana i kēia manawa. ʻO ia hoʻi ka hoʻohana ʻana i ke koʻokoʻo a i ʻole ka mea hele wāwae. Ma kahi o ʻelima mau makahiki ma hope o ka hoʻomaka ʻana o MSA, ma kahi o 60% o nā maʻi e pono ai e hoʻohana i ka noho huila. I loko o ʻeono a ʻewalu mau makahiki, ma ka liʻiliʻi o ka hapalua o nā maʻi e hoʻopaʻa ʻia ma kahi moe.

I ka holomua ʻana o ka maʻi, pono paha nā kaʻina hana hou a i ʻole nā ​​hana komo e mālama i nā hana o ke kino a pale i nā pilikia weliweli. ʻO kekahi o kēia mau mea:

  • ʻO Tracheostomy e mālama i ka hanu ʻana.
  • ʻO ka hānai ʻana ma o kahi ʻōmole ('Tube feeding' / `enteral nutrition`).
  • Nā catheters noho indwelling a i ʻole urostomy no ka incontinence urinary.
  • ʻO Colostomy no nā pilikia o ka neʻe ʻana o ka ʻōpū.

Pehea ka lōʻihi o ka MSA?

He maʻi mau loa ka MSA no ke ola holoʻokoʻa. ʻO ka awelika o ke ola me ka maʻi he ʻeono a ʻumi mau makahiki . I nā hihia ʻoi aku ka ʻino, hiki ke mau a hiki i 15 mau makahiki. Eia nō naʻe, i nā hihia ʻoi aku ka ʻino, hiki ke pōkole loa ke ola. ʻO kēia mau hihia koʻikoʻi ka maʻamau e komo pū me kēia mau hōʻailona:

  • Lilo nā hōʻailona o ka ʻōnaehana nerve autonomic i mea koʻikoʻi ma mua o ka hoʻomaka ʻana o nā hōʻailona pili i ka neʻe ʻana.
  • Ka ʻelemakule i ka wā i ʻike ʻia ai.
  • Loaʻa nā hōʻailona neʻe e hoʻoulu ai i ka hāʻule pinepine.

He aha ka manaʻo no kēia kūlana?

ʻAʻole maikaʻi loa ka nānā ʻana no ka MSA. Ke ʻoi aku ka ʻino o nā hōʻailona o kēia maʻi, e hoʻopilikia pinepine ana i nā hana o ke kino a alakaʻi i nā pilikia make. ʻO nā pilikia e hiki ai ke alakaʻi i ka make:

  • Pneumonia.
  • Hiki i nā maʻi ʻaʻai mimi (UTI) ke hana i ka sepsis (ka lāʻau make koko).
  • Ka make koke (pinepine i ka pō, ma muli o nā haunaele i ke ʻano o ka lolo e kaohi ai i ka hanu ʻana i ka wā hiamoe).

Pehea wau e mālama ai iaʻu iho/kaʻu mea aloha? He aha kaʻu mea e hopohopo ai?

Loaʻa i ka poʻe me MSA nā hōʻailona holomua. ʻO ke ʻano kēia, i ka wā e hiki ai nā hōʻailona i kahi pae, ʻaʻole hiki iā lākou ke noho kūʻokoʻa. Hiki i ke kūlana ke hoʻopilikia i kou hiki ke noʻonoʻo, ʻōlelo, a hoʻoholo i nā hoʻoholo nou iho. Ma muli o kēia mau mea āpau, he mea nui e kamaʻilio me kāu poʻe aloha e pili ana i kāu mau makemake no ka wā e hiki mai ana a e hana i kahi hoʻolālā no kāu mālama olakino inā ʻaʻole hiki iā ʻoe ke hoʻoholo .

Āhea ʻoe e ʻike ai i ke kauka?

He nui nā hōʻailona mua o MSA he mau mea āu e kūkākūkā ai me ke kauka. ʻO kēia mau mea:

  • Moekolohe.
  • ʻO ka hypotension Orthostatic (ka dizziness mau a i ʻole ka nāwaliwali no ke kumu ʻole).
  • Nā pilikia hiamoe a me ka apnea hiamoe (ka hanu ʻana i ka wā hiamoe).

Inā ʻike ke kauka iā ʻoe me kahi maʻi neʻe e like me ka maʻi Parkinson, he mea nui e kamaʻilio me lākou e pili ana i nā loli i kāu mau hōʻailona. E hoʻonohonoho kāu kauka i nā kipa hahai e nānā i kou kūlana a hoʻoponopono i kāu lāʻau lapaʻau. Hiki iā ʻoe ke kamaʻilio e pili ana i nā loli āu e ʻike ai i kēia mau kipa. He mea maʻamau no ka poʻe i ʻike ʻia me ka maʻi Parkinson ke hoʻololi i kā lākou hōʻailona ma hope, i ka wā e ulu ai nā hōʻailona hou a i ʻole i ka wā e pau ai ka hana pono ʻana o ka levodopa.

ʻIke pinepine ka poʻe me MSA i nā hōʻailona ʻē aʻe, ʻoiai nā pilikia olakino noʻonoʻo. He mea nui e ʻimi i ka lāʻau no nā pilikia olakino noʻonoʻo e pili ana i ka MSA, a me nā hōʻailona kino. Hiki i kāu kauka ke ʻōlelo i ka lāʻau a kuhikuhi paha iā ʻoe i kahi loea olakino noʻonoʻo.

I ka hōʻuluʻulu manaʻo (Leka Lawe-Home)

He maʻi koʻikoʻi ka Multiple System Atrophy (MSA) a he maʻi make loa ia. ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau pololei a lāʻau lapaʻau paha no kēia maʻi i kēia manawa.

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Eia nō naʻe, hiki ke mālama ʻia ka nui o kona mau hōʻailona , ​​a aia nā ala e hōʻemi ai i nā hopena a me nā hōʻailona. Me ka mālama ʻana, hiki i nā poʻe he nui ke mālama i ko lākou ola maikaʻi no nā makahiki, hoʻolilo i ka manawa waiwai me nā mea aloha, a hoʻohana pono i ko lākou manawa. No laila, he mea nui e hoʻokele i nā hōʻailona me ka ʻōlelo aʻoaʻo lapaʻau kūpono, me ka ʻole o ka hoʻonāukiuki.


`ʻO ka Atrophy Pūnaehana Nui, MSA, Maʻi Neurological, Maʻi Lolo, Nā Hōʻailona o Parkinson, Nā Maʻi Neʻe, Nā Pilikia o ka ʻŌnaehana Nervous Autonomic

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua e hana ʻia nei no kēia?

He kakaikahi loa nā hoʻokolohua e kōkua pololei i ka ʻike ʻana i ka MSA. Hana ʻia ka hapa nui o nā hoʻokolohua e kāpae i nā maʻi ʻē aʻe a e hōʻiliʻili i nā hōʻike hou aʻe e kākoʻo i ke kānalua he MSA paha ia. ʻO kekahi o kēia mau mea:

He aha nā lāʻau lapaʻau a i ʻole nā ​​​​​​lāʻau lapaʻau i hoʻohana ʻia?

Nui nā ʻano lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i nā hōʻailona o MSA. ʻO ke ʻano o ka lāʻau lapaʻau āu e loaʻa ai e hilinaʻi ia i kāu mau hōʻailona a me nā kumu ʻē aʻe. ʻO kāu kauka ke kanaka maikaʻi loa e ʻōlelo aku i ka lāʻau lapaʻau maikaʻi loa nāu, no ka mea, ʻo lākou ka poʻe ʻike nui loa i kou kūlana. E wehewehe pū lākou iā ʻoe i nā hopena ʻaoʻao o nā lāʻau lapaʻau.

He aha ka manaʻo no kēia kūlana?

ʻAʻole maikaʻi loa ka nānā ʻana no ka MSA. Ke ʻoi aku ka ʻino o nā hōʻailona o kēia maʻi, e hoʻopilikia pinepine ana i nā hana o ke kino a alakaʻi i nā pilikia make. ʻO nā pilikia e hiki ai ke alakaʻi i ka make:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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