Ua ʻike anei ʻoe iā PBC, kahi maʻi leo ʻole e hoʻopilikia ai i ke akepaʻa? (Primary Biliary Cholangitis)

ʻO ke akepaʻa kekahi o nā ʻōkana koʻikoʻi loa i loko o kou kino. Ua like ia me kahi hale hana nui. Hana nui ia i nā hana koʻikoʻi, e like me ka wehe ʻana i nā mea ʻawahia mai ka meaʻai a mākou e ʻai ai, ka mālama ʻana i ka ikehu, a me ka hana ʻana i ka bile, ka mea e kōkua ai iā mākou e hoʻoheheʻe i ka meaʻai. No laila, ʻo ka mālama ʻana i kēia hale hana e hana pono ana he mea nui loa ia no ke olakino o ko mākou kino holoʻokoʻa. Akā i kekahi manawa aia nā maʻi e hoʻopilikia mālie i ke akepaʻa, nā maʻi a mākou i lohe ʻole ai. I kēia lā e kamaʻilio mākou e pili ana i kekahi o ia mau maʻi. ʻO ia ka Primary Biliary Cholangitis, a i ʻole PBC e like me kā mākou e kapa nei no ka pōkole.

I ka ʻōlelo maʻalahi, he aha ka PBC?

ʻAe, e mālama kākou i kēia maʻalahi. E like me kaʻu i ʻōlelo ai ma mua, hana ke akepaʻa i kahi wai i kapa ʻia ʻo bile . ʻO kēia ka mea e kōkua iā mākou e hoʻoheheʻe i nā momona i loko o ka meaʻai a mākou e ʻai ai, e omo i kekahi mau huaora, a hoʻopau i ka cholesterol a me nā mea ʻawahia i makemake ʻole ʻia mai ke kino.

I kēia manawa, e noʻonoʻo, aia i loko o ke akepaʻa kahi pūnaewele o nā ʻauwai bile, e like me kahi ʻōnaehana paipu liʻiliʻi. ʻO ka bile a ke akepaʻa e hana ai e hele ma kēia mau ʻauwai liʻiliʻi a mālama ʻia ma laila, e kōkua ana i ka ʻeli ʻana i ka meaʻai i ka wā e pono ai. ʻO ka mea e hana ʻia ma PBC , ua hōʻino ʻia kēia mau ʻauwai bile.

Ke hōʻino ʻia kēia mau ʻauwai, ʻaʻole hiki i ka bile ke kahe pono a hoʻomaka e hōʻiliʻili i loko o ke ake. Ua like ia me kahi paipu wai haki e hoʻopiha ana i ka hale me ka wai. ʻO ka bile e hōʻiliʻili ana ma kēia ʻano e hoʻomaka e hōʻino i nā hunaola ake. Ke hana ʻia kēia hōʻino i ka hala ʻana o ka manawa, hoʻomaka ka ʻiʻo ʻeha e hana ma kahi o nā hunaola ake olakino. Kāhea mākou i kēia maʻi he cirrhosis . Ke lilo ke ake i ʻeha ma kēia ʻano, ua aneane pau kāna hana maʻamau.

ʻO nā pae ʻehā o ka maʻi PBC

ʻAʻole e ʻoi aku ka ʻino o ka PBC i ka manawa hoʻokahi. Hoʻomohala mālie ia, ma o kekahi mau pae. ʻEhā mau pae nui maʻamau.

He aha ke kumu maoli o ka PBC?

He pilikia kēia i loaʻa i nā kānaka he nui. ʻO ka ʻoiaʻiʻo, ʻaʻole i loaʻa i nā kauka ke kumu pololei o PBC. Eia nō naʻe, ʻo ka manaʻo i ʻae ʻia i kēia manawa he maʻi autoimmune ia i hoʻokumu ʻia e ka hui pū ʻana o nā kumu genetic a me ke kaiapuni .

ʻAe, he aha kēia maʻi autoimmune?

ʻO ia ka wā e hoʻouka mau ai ko kākou mau pūnaewele ponoʻī i nā ʻauwai bile ma kēia ʻano e hoʻomaka ai ka pōʻino aʻu i ʻōlelo ai ma mua.

ʻAʻole hiki ke ʻōlelo ʻia ua hoʻoili ʻia kēia maʻi mai kēlā hanauna a i kēia hanauna ma o nā genes. ʻO ia hoʻi, ʻaʻohe kānāwai no ka mea wale nō he maʻi ko ka makuahine, e loaʻa pū ana kāna kaikamahine iā ia. Eia nō naʻe, inā he PBC kekahi o ka ʻohana, ʻoiai he hoahānau pili (makuahine, kaikuahine, a kaikunāne paha), ʻoi aku ka nui o ka pilikia o ka loaʻa ʻana o kēia maʻi i kekahi poʻe ma mua o ke kanaka maʻamau. No laila, hiki ke manaʻo ʻia he pilina genetic.

ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i ka PBC?

ʻOiai hiki i kekahi ke loaʻa i ka PBC, aia kekahi poʻe i kahi pilikia kiʻekiʻe iki. E nānā kākou iā wai lākou.

He aha nā hōʻailona?

ʻO kēia ka mea nui loa. ʻO ka mea weliweli e pili ana i ka PBC, ʻaʻole hōʻike ka nui o ka poʻe i kekahi mau hōʻailona i nā pae mua. I kekahi manawa ʻike ʻia ia ma ke ʻano ulia pōpilikia ke hana ʻia kahi hoʻāʻo koko no kekahi maʻi ʻē aʻe.

Akā i ka holomua ʻana o ka maʻi, hiki ke ʻike ʻia nā hōʻailona e like me kēia:

• Luhi: ʻO kahi hōʻailona nui ka manaʻo luhi loa me ke kumu ʻike ʻole ʻia, ʻoiai ke hiamoe nei.
• ʻIli maneʻo: E ʻike paha ʻoe i ka maneʻo hiki ʻole ke hoʻomanawanui ma kou kino holoʻokoʻa, ʻoi aku hoʻi ma kou mau poho lima a me kou mau kapuwaʻi.
• Nā maka maloʻo a me ka waha: Hoʻemi ʻia ka hana ʻana o nā waimaka i loko o nā maka a me ka lawai i loko o ka waha, e hana ana i ka maloʻo.
• ʻEha hui a me ka iwi.
• ʻEha iki a ʻoluʻolu ʻole paha ma ka ʻaoʻao ʻākau o luna o ka ʻōpū.

I ka holomua ʻana o ka maʻi (i ke kahua o ka cirrhosis), hiki ke ʻike ʻia nā hōʻailona e like me ka pehu ʻana o nā wāwae, ka wai i loko o ka ʻōpū, a me ka melemele ʻana o nā maka a me ka ʻili (jaundice).

Āhea ʻoe e ʻike ai i ke kauka?

Inā ʻo ʻoe, ʻoiai inā he wahine ʻoe ma waena o 30 a me 60 mau makahiki, ke ʻike nei i nā hōʻailona e like me ka luhi mau a me ka ʻili ʻili me ke kumu ʻole, mai hoʻokuʻu wale iā ia me he "ʻelemakule wale nō" a "nui loa ka hana." E ʻike koke i kāu kauka a kamaʻilio e pili ana.

E nānā ke kauka iā ʻoe a, inā pono, e kauoha i kekahi mau hoʻāʻo koko. Hiki ke maʻalahi ka ʻike ʻana i kēia maʻi ma ka nānā ʻana i nā enzymes ate a me nā antibodies kikoʻī (AMA - Antimitochondrial Antibodies). No laila, mai hoʻowahāwahā i nā hōʻailona. ʻO ka wikiwiki o ka ʻike ʻia ʻana, ʻo ka nui o ka hiki ke mālama ʻia a kaohi ʻia.