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Ke loli nei ke ʻano o nā hunaola koko ʻulaʻula i loko o kou koko? E kamaʻilio kākou e pili ana i ka (Poikilocytosis)!

Ke loli nei ke ʻano o nā hunaola koko ʻulaʻula i loko o kou koko? E kamaʻilio kākou e pili ana i ka (Poikilocytosis)!

Ke luhi nei ʻoe i kekahi manawa a me ka palaualelo no ke kumu ʻole? A i ʻole ua nānā paha kekahi kauka i kāu hōʻike hoʻāʻo koko a ʻōlelo i kahi mea e like me, "Aia kahi loli iki i ke ʻano o kou mau keʻena koko ʻulaʻula?" I kēlā mau manawa, ʻo kekahi o nā huaʻōlelo a mākou e lohe ai ʻo `(Poikilocytosis)` (puana ʻia: poi-ki-lo-say-to-sis). Mai makaʻu nui i kou lohe ʻana i kēia inoa. ʻAʻole kēia he maʻi, akā hiki ke lilo i hōʻailona e hana ana kekahi mea ʻē aʻe i loko o ko mākou kino. No laila, he mea nui loa ka makaʻala i kēia.

He aha maoli ka `(Poikilocytosis)`?

I ka ʻōlelo maʻalahi, ʻo ke ʻano o ka "Poikilocytosis" he nui nā ʻano (ʻo ia hoʻi, ʻoi aku ma mua o 10%) o nā hunaola koko ʻulaʻula i loko o ko kākou koko. I kēia manawa ke noʻonoʻo nei paha ʻoe, "No ke aha he mea nui ke ʻano o nā hunaola koko ʻulaʻula?"

E noʻonoʻo wale, pono nā ʻāpana ʻē aʻe a pau, nā ʻiʻo, a me nā ʻōkana i loko o ko kākou kino i ka ikehu e ola a hana. Hāʻawi ʻia kēlā ikehu e ka oxygen. ʻO wai ka mea ʻike, ʻo kēia oxygen, e like me ka lawe ʻana mai i kahi pahu kinoea i ka home, e lawe ʻia ana ma ke kino holoʻokoʻa? ʻO ia ko kākou mau hunaola koko ʻulaʻula. ʻO ka maʻamau, inā ʻoe e lawe i kahi hunaola koko ʻulaʻula olakino, ua like ko lākou nui a me ke ʻano. E like me kahi kālā poepoe (e like me ka disk) he ʻūpā iki ma nā ʻaoʻao ʻelua.

No laila, inā loli ke ʻano o kēia mau hunaola koko ʻulaʻula (`(Poikilocytosis)`) a i ʻole e loli ka nui (aia kekahi i kapa ʻia ʻo `(Anisocytosis)`), ʻaʻole hiki iā lākou ke lawe pono i ka oxygen. ʻO ia ka manawa e loaʻa ai iā mākou nā maʻi e like me ka anemia (nele o ke koko i loko o ke koko). ʻO ia hoʻi, ʻaʻole lawa ka oxygen i nā hunaola o ke kino, ʻo ia hoʻi ka ikehu.

He aha nā ʻano ʻē o nā hunaola koko ʻulaʻula? (Poikilocytes)

Hoʻokaʻawale nā ​​kauka i kēia mau ʻulaʻula koko ʻano ʻē (i kapa ʻia hoʻi ʻo 'Poikilocytes') ma ko lākou helehelena. Inā loaʻa iā ʻoe ka '(Poikilocytosis)' i loko o kahi hāpana koko, hiki iā ʻoe ke ʻike i hoʻokahi a ʻoi aku paha o kēia mau mea:

  • Nā Acanthocytes / Spur cell : Ua like kēia me ka lālā kākalaioa. He mau puka lōʻihi, ākea, a me he kui lā ko lākou e puka mai ana mai ka membrane cell.
  • Nā Codocytes / Nā pūnaewele i manaʻo ʻia : Ua like kēia me kahi papa i manaʻo ʻia. Aia kahi pōʻai ʻeleʻele ma waenakonu.
  • Nā Dacrocytes / Nā pūnaewele waimaka : ʻAno waimaka. He lahilahi a ʻoi kekahi ʻaoʻao o ke kelepona.
  • Nā Drepanocytes / Nā pūnaewele sickle : He mau pūnaewele lahilahi kēia, ʻano sickle i ʻike ʻia i loko o ka poʻe me ka maʻi cell sickle.
  • Nā Echinocytes : E like me ka ʻurchin kai, ua uhi ʻia ke kelepona me nā kākalaioa ma nā mamao like ma loko.
  • Nā Elliptocytes / Ovalocytes a i ʻole nā ​​​​​​pūnaewele Cigar : He ʻano oval kēia a he lōʻihi loa. Hiki iā lākou ke ʻokoʻa i ka nui mai ke ʻano hua manu a i ke ʻano cigar.
  • Nā Schistocytes : He mau ʻāpana kēia o nā hunaola koko ʻulaʻula. He ʻano ʻinoʻino a haki ko lākou helehelena, akā hiki ke lilo i kekahi ʻano.
  • Nā Spherocytes: Pōʻai. E like me ka pōpō liʻiliʻi.

Hiki ke pili i kēlā me kēia ʻano me nā kūlana olakino kikoʻī.

He aha nā hōʻailona o kēia maʻi?

ʻOkoʻa nā hōʻailona o ka "Poikilocytosis" ma muli o ke kumu, akā ua like pinepine lākou me nā mea i ʻike ʻia i ka anemia.

Eia kekahi mau hōʻailona o ka anemia:

  • Ka nāwaliwali a i ʻole ka luhi loa (manaʻo wale nō i ka luhi).
  • Paʻakikī ka hanu ʻana (dyspnea) - ka pōkole o ka hanu ʻana me nā hana liʻiliʻi.
  • Puʻuwai wikiwiki a ʻano ʻole paha (arrhythmia).
  • I kekahi manawa lohe ʻoe i ke kani "whooshing" i loko o kou mau pepeiao (`(pulsatile tinnitus)`).
  • ʻEha poʻo .
  • Pōʻaiʻī .
  • ʻIli keʻokeʻo .
  • ʻEha ka umauma .

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​ʻoi aku ka maikaʻi o ka ʻimi ʻana i ke kōkua lapaʻau.

No ke aha lā kēia e hana nei? He aha nā kumu?

Hiki ke hoʻokaʻawale ʻia nā kumu o kēia mau ʻano ʻulaʻula ʻano ʻē i ʻelua mau ʻāpana nui: hoʻoilina a loaʻa . Hiki i kekahi mau kūlana, e like me Myelodysplastic Syndrome, ke hana i nā mea ʻelua.

Nā Kūlana Hoʻoilina

I ka hapanui o nā hihia, ʻo nā kumu hānau hou ke kumu o kahi hewa i ka ʻike genetic (DNA) e pono ai kahi ʻulaʻula koko e ulu, hana, a ola pono. ʻO nā ʻulaʻula koko me ia mau ʻano ʻē e haki koke ma mua o ka hiki ʻana o ke kino ke hana i nā ʻulaʻula hou. Ua kapa ʻia kēia he anemia hemolytic .

ʻO kekahi mau maʻi hānau e hoʻoulu ai i ka `(Poikilocytosis)`:

  • `(ʻEliptocytosis hoʻoilina)`
  • `(Spherocytosis hoʻoilina)`
  • ʻO ka maʻi McLeod
  • `(Ka hemahema o Pyruvate Kinase)`
  • `(Maʻi Kelepona Sickle)` (Maʻi Kelepona Sickle)
  • `(Thalassemia)`

He mau mea kēia i hoʻoili ʻia mai nā hanauna mai.

Nā Kūlana i Loaʻa

I ka hala ʻana o ka manawa, hiki i kekahi mau kūlana olakino ke hoʻololi i ke ʻano o nā hunaola koko ʻulaʻula. No ka laʻana, inā ʻaʻole lawa ka nui o nā meaʻai e pono ai ke kino e hana i nā hunaola koko ʻulaʻula olakino, e like me ka huaora B12, folate, a me ka hao, hiki ke loaʻa nā ʻano anemia like ʻole. ʻO ka Poikilocytosis kahi hōʻailona maʻamau o kēia mau hemahema meaʻai. Hiki ke hana ʻia e nā maʻi e hoʻopilikia i ka hana ʻana o nā hunaola koko ʻulaʻula, e like me kekahi mau maʻi kanesa.

ʻO kekahi o nā kūlana ma hope e hoʻoulu ai i ka `(Poikilocytosis)`:

  • Anemia Hemolytic Autoimmune
  • Nā kuni (inā nui)
  • `(Maʻi Celiac)`
  • Nā maʻi like ʻole
  • Anemia nele i ka hao
  • Maʻi puʻupaʻa
  • Leukemia (maʻi ʻaʻai koko)
  • Maʻi ʻAke
  • ʻO ka anemia Megaloblastic (ma muli o ka nele o ka huaora B12 a i ʻole ka folate)
  • ʻO ka Myelofibrosis
  • Ka lāʻau make (e.g. kēpau)
  • Ka hopena i ka hoʻoili koko
  • Ka hopena i ka splenectomy
  • Nahu nahesa

He aha nā pilikia e hiki ai i kēia ke hana?

Hiki ke mālama ʻia nā maʻi he nui e hoʻoulu ai i ka poikilocytosis me ka lāʻau lapaʻau, a hiki ke ho'ōla loa ʻia kekahi. Eia nō naʻe, inā ʻaʻole mālama ʻia, hiki i kekahi mau maʻi ke lilo i mea koʻikoʻi a hiki i ka hoʻoweliweli i ke ola. No ka laʻana, inā loaʻa iā ʻoe ka anemia, hiki iā ʻoe ke luhi loa a hiki ʻole iā ʻoe ke hana i kāu mau hana o kēlā me kēia lā. Inā nalowale ʻoe i nā hunaola koko ʻulaʻula olakino i ka hala ʻana o ka manawa, hiki iā ia ke alakaʻi i nā maʻi e like me ka hāʻule ʻana o nā ʻōkana .

ʻOi loa aku i nā keiki ʻōpio, inā loaʻa ka anemia i mālama ʻole ʻia, hiki iā ia ke hoʻopilikia i ko lākou ulu ʻana a me ka ulu ʻana.

No laila, i ka manawa i hoʻoholo ai kāu kauka i ke kumu pololei o kāu Poikilocytosis, e hāʻawi ʻo ia i ka lāʻau e pono ai e pale aku i nā pilikia e like me kēia.

Pehea ʻoe e ʻike pono ai i kēia? (Diagnosis)

ʻO ka hoʻāʻo nui e hiki ai i ke kauka ke hoʻohana e ʻike i ka poikilocytosis he peripheral blood smear (PBS) . Pili kēia i kahi loea lab e lawe ana i kahi kulu o kāu hāpana koko a nānā iā ia ma lalo o kahi microscope. A laila hiki iā lākou ke ʻike i ka nui o kāu mau hunaola koko ʻulaʻula i ʻano ʻē a me ke ʻano o lākou.

ʻOi aku ka maʻamau o kekahi mau ʻano cell i nā kūlana maʻi kikoʻī. Eia nō naʻe, ʻoiai i loko o ke kūlana maʻi like, hiki ke loaʻa nā ʻano cell like ʻole. No ka laʻana, i nā kūlana e like me `(Hemolytic Anemia)`, `(Megaloblastic Anemia)`, `(Myelofibrosis)`, `(Thalassemia)`, hiki ke ʻike ʻia kekahi mau ʻano cell ʻē.

Pono paha kāu mau kauka e hana i kekahi mau hoʻokolohua hou aʻe e ʻike pono ai i ke kumu o kāu poikilocytosis.

Nā hoʻokolohua hou aʻe e ʻike ai i ke kumu o `(Poikilocytosis)`

Hana pinepine ʻia kahi helu koko piha (CBC) me kahi PBS. Hiki i ka CBC ke hāʻawi i ka ʻike he nui e pili ana i nā ʻāpana i loko o kou koko, me ko lākou mau pae a me nā nui. Hiki i kekahi o nā waiwai i loko o ka CBC ke hāʻawi i ka ʻike hou aku e pili ana i nā ʻāpana koko ʻulaʻula, hiki ke kōkua i ka hoʻoholo ʻana i ke kumu o Poikilocytosis. ʻO kēia mau waiwai:

  • ʻO ka ʻawelike o ke kino (MCV) : ʻO ka nui awelika o kou mau hunaola koko ʻulaʻula.
  • ʻO ka ʻawelika o ka Hemoglobin Kino ʻulaʻula (MCH) : ʻO ka nui awelika o ka hemoglobin i loko o kou mau hunaola koko ʻulaʻula.
  • ʻO ke ʻano o ka nui o ka hemoglobin kino (MCHC)ʻO ka awelika o ka nui o ka hemoglobin i loko o kou mau hunaola koko ʻulaʻula.
  • ʻO ka laulā o ka hoʻolaha ʻana o nā keena koko ʻulaʻula (RDW) : Pehea ka ʻokoʻa o ka nui o kou mau keena koko ʻulaʻula.

Eia kekahi, hiki i kāu kauka ke nānā i kāu mau huaora B12, folate, a me nā pae hao, a hiki ke kauoha i nā hoʻokolohua hana ate.

He aha nā lāʻau lapaʻau no kēia?

Hoʻopili ʻia ka lāʻau lapaʻau i ke kumu o kāu poikilocytosis a me ke koʻikoʻi o kāu mau hōʻailona.

E hoʻomanaʻo, inā ʻo ke kumu o kēia kūlana he hemahema meaʻai (e like me ka hao, ka hemahema o ka wikamina B12), ʻo ka lawe ʻana i nā mea hoʻopihapiha meaʻai kūpono, a i ʻole ka hoʻololi ʻana i kahi meaʻai waiwai i ka wikamina B12 a i ʻole folate, hiki ke hoʻoponopono pinepine i kēia kūlana '(Poikilocytosis)'.

Pono ka nānā pono ʻana i nā maʻi hānau he nui. Pono paha ʻoe i nā hoʻoili koko maʻamau e hōʻoia i loaʻa iā ʻoe nā hunaola koko ʻulaʻula olakino. A i ʻole pono paha ʻoe i ka lāʻau lapaʻau ma muli o ka loaʻa ʻana o nā hōʻailona.

Hiki ke pale ʻia kēia kūlana?

ʻAʻole hiki iā mākou ke pale aku i nā kumu hānau o ka "Poikilocytosis." Eia nō naʻe, hiki iā mākou ke hōʻemi i ka pilikia o kekahi mau kumu ma hope.

ʻO kekahi o nā ala maikaʻi loa e mālama ai i kāu mau hunaola koko ʻulaʻula, ʻo ia ka loaʻa ʻana o nā meaolaola e pono ai kou kino e hana iā lākou. E hōʻoia i loaʻa iā ʻoe ka lawa o nā huaora B, folate, a me ka hao . ʻO kēia nā mea nui e pono ai kou kino e hana i nā hunaola koko ʻulaʻula olakino. Kōkua nō hoʻi ia i ka palena ʻana i ka nui o ka waiʻona āu e inu ai . ʻO ka nui o ka waiʻona hiki ke hoʻolilo i mea paʻakikī i kou kino ke omo i kēia mau meaolaola.

He aha ka mea e hiki mai ana? (Outlook)

Ma keʻano laulā, inā he maʻi ma hope ke kumu o ka `(Poikilocytosis)`, maikaʻi ka wānana. I nā hihia o nā kumu hānau, ʻokoʻa ka wānana ma muli o ke kūlana kumu. No ka laʻana, ʻoiai ua manaʻo ʻia he pōkole ke ola o ka poʻe me ka `(Sickle Cell Disease)`, ua hiki i nā lāʻau lapaʻau hou ke ola no nā makahiki he 50 a ʻoi me ka kaohi ʻana i nā hōʻailona.

Āhea ʻoe e ʻike ai i ke kauka?

Inā loaʻa iā ʻoe nā hōʻailona o ka anemia (nā mea a mākou i kamaʻilio ai ma mua, e like me ka luhi a me ka nāwaliwali), e ʻike pono i ke kauka.

ʻOiai inā manaʻo ʻoe ua olakino ʻoe a ʻaʻohe hōʻailona, ​​​​he mea nui e hana i nā nānā makahiki. Hiki i kāu kauka ke nānā i kāu mau hunaola koko. ʻO kahi hoʻāʻo koko maʻalahi, e like me ka helu koko piha (CBC), hiki ke kōkua i ka ʻike a me ka mālama ʻana i nā pilikia olakino ma mua o ko lākou lilo ʻana i mea koʻikoʻi.

He maʻi koʻikoʻi anei kēia "Poikilocytosis"?

ʻAʻole koʻikoʻi ka `(Poikilocytosis)`. Eia naʻe,Hiki iā ia ke lilo i hōʻailona o kahi maʻi olakino e hiki ai ke alakaʻi i nā pilikia inā ʻaʻole mālama ʻia. No laila, he mea nui e hoʻomaopopo pono i ke kumu o ka `(Poikilocytosis)` a e ʻimi i ka lāʻau lapaʻau inā pono.

ʻOiai paha he ʻano koʻikoʻi ka poikilocytosis, ʻaʻole ia. He ʻano wale nō ia o kou mau koko ʻulaʻula a nā kauka e hoʻohana ai e loiloi i kou olakino. Inā ʻike ʻoe he ʻano ʻē kou mau koko ʻulaʻula, mai kānalua e nīnau i kāu kauka e pili ana i ia mea. Hiki iā ia ke haʻi iā ʻoe inā e hoʻopilikia ana i kou olakino a, inā pēlā, he aha kāu e hiki ai ke hana e hoʻopau i ke ʻano a i ʻole e hoʻokele i ke ʻano kumu.

Nā mea nui a mākou e hoʻomanaʻo ai (Leka Lawe-Home)

ʻAe, ʻo nā kumu nui e hoʻomanaʻo ai mai nā mea a mākou i kamaʻilio ai, ʻo ia kēia:

  • ʻO ka poikilocytosis ka wā e ʻoi aku ma mua o 10% o kāu mau keʻena koko ʻulaʻula i ke ʻano kūpono ʻole.
  • ʻAʻole kēia he maʻi, akā he hōʻailona paha ia o kahi maʻi kumu.
  • Hiki ke ʻike ʻia nā hōʻailona o ka anemia (luhi, nāwaliwali, keʻokeʻo) i kēia hihia.
  • Hiki i nā kumu ke hānau ʻia a i loaʻa paha (nā hemahema meaʻai, kekahi mau maʻi).
  • Hiki ke ʻike ʻia kēia me kahi hoʻāʻo koko maʻalahi (`PBS`, `CBC`).
  • Aia ka lāʻau lapaʻau ma muli o ke kumu, akā hiki ke mālama pinepine ʻia.
  • ʻO ka mālama ʻana i kahi meaʻai olakino e hiki ke kōkua i ka pale ʻana i kekahi o nā kumu o ka hoʻomaka ʻana ma hope.
  • Inā he mau hōʻailona kou a i ʻole kānalua paha no kēia, ʻoi aku ka maikaʻi o ke kipa ʻana i ke kauka no ka ʻōlelo aʻo.

No laila, ke lana nei koʻu manaʻo he mea pono kēia ʻike iā ʻoe. E noho olakino!


ʻO Poikilocytosis, Nā Kelepona Koko ʻUlaʻula, Ke ʻAno o nā Kelepona Koko, Anemia, Nā Hoʻāʻo Koko, Ola Kino, Anemia, Nā Kelepona Koko ʻUlaʻula, Hoʻāʻo Koko

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ke loli nei ke ʻano o nā hunaola koko ʻulaʻula i loko o kou koko? E kamaʻilio kākou e pili ana i ka (Poikilocytosis)!

Ke loli nei ke ʻano o nā hunaola koko ʻulaʻula i loko o kou koko? E kamaʻilio kākou e pili ana i ka (Poikilocytosis)!

Ke luhi nei ʻoe i kekahi manawa a me ka palaualelo no ke kumu ʻole? A i ʻole ua nānā paha kekahi kauka i kāu hōʻike hoʻāʻo koko a ʻōlelo i kahi mea e like me, "Aia kahi loli iki i ke ʻano o kou mau keʻena koko ʻulaʻula?" I kēlā mau manawa, ʻo kekahi o nā huaʻōlelo a mākou e lohe ai ʻo `(Poikilocytosis)` (puana ʻia: poi-ki-lo-say-to-sis). Mai makaʻu nui i kou lohe ʻana i kēia inoa. ʻAʻole kēia he maʻi, akā hiki ke lilo i hōʻailona e hana ana kekahi mea ʻē aʻe i loko o ko mākou kino. No laila, he mea nui loa ka makaʻala i kēia.

He aha maoli ka `(Poikilocytosis)`?

I ka ʻōlelo maʻalahi, ʻo ke ʻano o ka "Poikilocytosis" he nui nā ʻano (ʻo ia hoʻi, ʻoi aku ma mua o 10%) o nā hunaola koko ʻulaʻula i loko o ko kākou koko. I kēia manawa ke noʻonoʻo nei paha ʻoe, "No ke aha he mea nui ke ʻano o nā hunaola koko ʻulaʻula?"

E noʻonoʻo wale, pono nā ʻāpana ʻē aʻe a pau, nā ʻiʻo, a me nā ʻōkana i loko o ko kākou kino i ka ikehu e ola a hana. Hāʻawi ʻia kēlā ikehu e ka oxygen. ʻO wai ka mea ʻike, ʻo kēia oxygen, e like me ka lawe ʻana mai i kahi pahu kinoea i ka home, e lawe ʻia ana ma ke kino holoʻokoʻa? ʻO ia ko kākou mau hunaola koko ʻulaʻula. ʻO ka maʻamau, inā ʻoe e lawe i kahi hunaola koko ʻulaʻula olakino, ua like ko lākou nui a me ke ʻano. E like me kahi kālā poepoe (e like me ka disk) he ʻūpā iki ma nā ʻaoʻao ʻelua.

No laila, inā loli ke ʻano o kēia mau hunaola koko ʻulaʻula (`(Poikilocytosis)`) a i ʻole e loli ka nui (aia kekahi i kapa ʻia ʻo `(Anisocytosis)`), ʻaʻole hiki iā lākou ke lawe pono i ka oxygen. ʻO ia ka manawa e loaʻa ai iā mākou nā maʻi e like me ka anemia (nele o ke koko i loko o ke koko). ʻO ia hoʻi, ʻaʻole lawa ka oxygen i nā hunaola o ke kino, ʻo ia hoʻi ka ikehu.

He aha nā ʻano ʻē o nā hunaola koko ʻulaʻula? (Poikilocytes)

Hoʻokaʻawale nā ​​kauka i kēia mau ʻulaʻula koko ʻano ʻē (i kapa ʻia hoʻi ʻo 'Poikilocytes') ma ko lākou helehelena. Inā loaʻa iā ʻoe ka '(Poikilocytosis)' i loko o kahi hāpana koko, hiki iā ʻoe ke ʻike i hoʻokahi a ʻoi aku paha o kēia mau mea:

  • Nā Acanthocytes / Spur cell : Ua like kēia me ka lālā kākalaioa. He mau puka lōʻihi, ākea, a me he kui lā ko lākou e puka mai ana mai ka membrane cell.
  • Nā Codocytes / Nā pūnaewele i manaʻo ʻia : Ua like kēia me kahi papa i manaʻo ʻia. Aia kahi pōʻai ʻeleʻele ma waenakonu.
  • Nā Dacrocytes / Nā pūnaewele waimaka : ʻAno waimaka. He lahilahi a ʻoi kekahi ʻaoʻao o ke kelepona.
  • Nā Drepanocytes / Nā pūnaewele sickle : He mau pūnaewele lahilahi kēia, ʻano sickle i ʻike ʻia i loko o ka poʻe me ka maʻi cell sickle.
  • Nā Echinocytes : E like me ka ʻurchin kai, ua uhi ʻia ke kelepona me nā kākalaioa ma nā mamao like ma loko.
  • Nā Elliptocytes / Ovalocytes a i ʻole nā ​​​​​​pūnaewele Cigar : He ʻano oval kēia a he lōʻihi loa. Hiki iā lākou ke ʻokoʻa i ka nui mai ke ʻano hua manu a i ke ʻano cigar.
  • Nā Schistocytes : He mau ʻāpana kēia o nā hunaola koko ʻulaʻula. He ʻano ʻinoʻino a haki ko lākou helehelena, akā hiki ke lilo i kekahi ʻano.
  • Nā Spherocytes: Pōʻai. E like me ka pōpō liʻiliʻi.

Hiki ke pili i kēlā me kēia ʻano me nā kūlana olakino kikoʻī.

He aha nā hōʻailona o kēia maʻi?

ʻOkoʻa nā hōʻailona o ka "Poikilocytosis" ma muli o ke kumu, akā ua like pinepine lākou me nā mea i ʻike ʻia i ka anemia.

Eia kekahi mau hōʻailona o ka anemia:

  • Ka nāwaliwali a i ʻole ka luhi loa (manaʻo wale nō i ka luhi).
  • Paʻakikī ka hanu ʻana (dyspnea) - ka pōkole o ka hanu ʻana me nā hana liʻiliʻi.
  • Puʻuwai wikiwiki a ʻano ʻole paha (arrhythmia).
  • I kekahi manawa lohe ʻoe i ke kani "whooshing" i loko o kou mau pepeiao (`(pulsatile tinnitus)`).
  • ʻEha poʻo .
  • Pōʻaiʻī .
  • ʻIli keʻokeʻo .
  • ʻEha ka umauma .

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​ʻoi aku ka maikaʻi o ka ʻimi ʻana i ke kōkua lapaʻau.

No ke aha lā kēia e hana nei? He aha nā kumu?

Hiki ke hoʻokaʻawale ʻia nā kumu o kēia mau ʻano ʻulaʻula ʻano ʻē i ʻelua mau ʻāpana nui: hoʻoilina a loaʻa . Hiki i kekahi mau kūlana, e like me Myelodysplastic Syndrome, ke hana i nā mea ʻelua.

Nā Kūlana Hoʻoilina

I ka hapanui o nā hihia, ʻo nā kumu hānau hou ke kumu o kahi hewa i ka ʻike genetic (DNA) e pono ai kahi ʻulaʻula koko e ulu, hana, a ola pono. ʻO nā ʻulaʻula koko me ia mau ʻano ʻē e haki koke ma mua o ka hiki ʻana o ke kino ke hana i nā ʻulaʻula hou. Ua kapa ʻia kēia he anemia hemolytic .

ʻO kekahi mau maʻi hānau e hoʻoulu ai i ka `(Poikilocytosis)`:

  • `(ʻEliptocytosis hoʻoilina)`
  • `(Spherocytosis hoʻoilina)`
  • ʻO ka maʻi McLeod
  • `(Ka hemahema o Pyruvate Kinase)`
  • `(Maʻi Kelepona Sickle)` (Maʻi Kelepona Sickle)
  • `(Thalassemia)`

He mau mea kēia i hoʻoili ʻia mai nā hanauna mai.

Nā Kūlana i Loaʻa

I ka hala ʻana o ka manawa, hiki i kekahi mau kūlana olakino ke hoʻololi i ke ʻano o nā hunaola koko ʻulaʻula. No ka laʻana, inā ʻaʻole lawa ka nui o nā meaʻai e pono ai ke kino e hana i nā hunaola koko ʻulaʻula olakino, e like me ka huaora B12, folate, a me ka hao, hiki ke loaʻa nā ʻano anemia like ʻole. ʻO ka Poikilocytosis kahi hōʻailona maʻamau o kēia mau hemahema meaʻai. Hiki ke hana ʻia e nā maʻi e hoʻopilikia i ka hana ʻana o nā hunaola koko ʻulaʻula, e like me kekahi mau maʻi kanesa.

ʻO kekahi o nā kūlana ma hope e hoʻoulu ai i ka `(Poikilocytosis)`:

  • Anemia Hemolytic Autoimmune
  • Nā kuni (inā nui)
  • `(Maʻi Celiac)`
  • Nā maʻi like ʻole
  • Anemia nele i ka hao
  • Maʻi puʻupaʻa
  • Leukemia (maʻi ʻaʻai koko)
  • Maʻi ʻAke
  • ʻO ka anemia Megaloblastic (ma muli o ka nele o ka huaora B12 a i ʻole ka folate)
  • ʻO ka Myelofibrosis
  • Ka lāʻau make (e.g. kēpau)
  • Ka hopena i ka hoʻoili koko
  • Ka hopena i ka splenectomy
  • Nahu nahesa

He aha nā pilikia e hiki ai i kēia ke hana?

Hiki ke mālama ʻia nā maʻi he nui e hoʻoulu ai i ka poikilocytosis me ka lāʻau lapaʻau, a hiki ke ho'ōla loa ʻia kekahi. Eia nō naʻe, inā ʻaʻole mālama ʻia, hiki i kekahi mau maʻi ke lilo i mea koʻikoʻi a hiki i ka hoʻoweliweli i ke ola. No ka laʻana, inā loaʻa iā ʻoe ka anemia, hiki iā ʻoe ke luhi loa a hiki ʻole iā ʻoe ke hana i kāu mau hana o kēlā me kēia lā. Inā nalowale ʻoe i nā hunaola koko ʻulaʻula olakino i ka hala ʻana o ka manawa, hiki iā ia ke alakaʻi i nā maʻi e like me ka hāʻule ʻana o nā ʻōkana .

ʻOi loa aku i nā keiki ʻōpio, inā loaʻa ka anemia i mālama ʻole ʻia, hiki iā ia ke hoʻopilikia i ko lākou ulu ʻana a me ka ulu ʻana.

No laila, i ka manawa i hoʻoholo ai kāu kauka i ke kumu pololei o kāu Poikilocytosis, e hāʻawi ʻo ia i ka lāʻau e pono ai e pale aku i nā pilikia e like me kēia.

Pehea ʻoe e ʻike pono ai i kēia? (Diagnosis)

ʻO ka hoʻāʻo nui e hiki ai i ke kauka ke hoʻohana e ʻike i ka poikilocytosis he peripheral blood smear (PBS) . Pili kēia i kahi loea lab e lawe ana i kahi kulu o kāu hāpana koko a nānā iā ia ma lalo o kahi microscope. A laila hiki iā lākou ke ʻike i ka nui o kāu mau hunaola koko ʻulaʻula i ʻano ʻē a me ke ʻano o lākou.

ʻOi aku ka maʻamau o kekahi mau ʻano cell i nā kūlana maʻi kikoʻī. Eia nō naʻe, ʻoiai i loko o ke kūlana maʻi like, hiki ke loaʻa nā ʻano cell like ʻole. No ka laʻana, i nā kūlana e like me `(Hemolytic Anemia)`, `(Megaloblastic Anemia)`, `(Myelofibrosis)`, `(Thalassemia)`, hiki ke ʻike ʻia kekahi mau ʻano cell ʻē.

Pono paha kāu mau kauka e hana i kekahi mau hoʻokolohua hou aʻe e ʻike pono ai i ke kumu o kāu poikilocytosis.

Nā hoʻokolohua hou aʻe e ʻike ai i ke kumu o `(Poikilocytosis)`

Hana pinepine ʻia kahi helu koko piha (CBC) me kahi PBS. Hiki i ka CBC ke hāʻawi i ka ʻike he nui e pili ana i nā ʻāpana i loko o kou koko, me ko lākou mau pae a me nā nui. Hiki i kekahi o nā waiwai i loko o ka CBC ke hāʻawi i ka ʻike hou aku e pili ana i nā ʻāpana koko ʻulaʻula, hiki ke kōkua i ka hoʻoholo ʻana i ke kumu o Poikilocytosis. ʻO kēia mau waiwai:

  • ʻO ka ʻawelike o ke kino (MCV) : ʻO ka nui awelika o kou mau hunaola koko ʻulaʻula.
  • ʻO ka ʻawelika o ka Hemoglobin Kino ʻulaʻula (MCH) : ʻO ka nui awelika o ka hemoglobin i loko o kou mau hunaola koko ʻulaʻula.
  • ʻO ke ʻano o ka nui o ka hemoglobin kino (MCHC)ʻO ka awelika o ka nui o ka hemoglobin i loko o kou mau hunaola koko ʻulaʻula.
  • ʻO ka laulā o ka hoʻolaha ʻana o nā keena koko ʻulaʻula (RDW) : Pehea ka ʻokoʻa o ka nui o kou mau keena koko ʻulaʻula.

Eia kekahi, hiki i kāu kauka ke nānā i kāu mau huaora B12, folate, a me nā pae hao, a hiki ke kauoha i nā hoʻokolohua hana ate.

He aha nā lāʻau lapaʻau no kēia?

Hoʻopili ʻia ka lāʻau lapaʻau i ke kumu o kāu poikilocytosis a me ke koʻikoʻi o kāu mau hōʻailona.

E hoʻomanaʻo, inā ʻo ke kumu o kēia kūlana he hemahema meaʻai (e like me ka hao, ka hemahema o ka wikamina B12), ʻo ka lawe ʻana i nā mea hoʻopihapiha meaʻai kūpono, a i ʻole ka hoʻololi ʻana i kahi meaʻai waiwai i ka wikamina B12 a i ʻole folate, hiki ke hoʻoponopono pinepine i kēia kūlana '(Poikilocytosis)'.

Pono ka nānā pono ʻana i nā maʻi hānau he nui. Pono paha ʻoe i nā hoʻoili koko maʻamau e hōʻoia i loaʻa iā ʻoe nā hunaola koko ʻulaʻula olakino. A i ʻole pono paha ʻoe i ka lāʻau lapaʻau ma muli o ka loaʻa ʻana o nā hōʻailona.

Hiki ke pale ʻia kēia kūlana?

ʻAʻole hiki iā mākou ke pale aku i nā kumu hānau o ka "Poikilocytosis." Eia nō naʻe, hiki iā mākou ke hōʻemi i ka pilikia o kekahi mau kumu ma hope.

ʻO kekahi o nā ala maikaʻi loa e mālama ai i kāu mau hunaola koko ʻulaʻula, ʻo ia ka loaʻa ʻana o nā meaolaola e pono ai kou kino e hana iā lākou. E hōʻoia i loaʻa iā ʻoe ka lawa o nā huaora B, folate, a me ka hao . ʻO kēia nā mea nui e pono ai kou kino e hana i nā hunaola koko ʻulaʻula olakino. Kōkua nō hoʻi ia i ka palena ʻana i ka nui o ka waiʻona āu e inu ai . ʻO ka nui o ka waiʻona hiki ke hoʻolilo i mea paʻakikī i kou kino ke omo i kēia mau meaolaola.

He aha ka mea e hiki mai ana? (Outlook)

Ma keʻano laulā, inā he maʻi ma hope ke kumu o ka `(Poikilocytosis)`, maikaʻi ka wānana. I nā hihia o nā kumu hānau, ʻokoʻa ka wānana ma muli o ke kūlana kumu. No ka laʻana, ʻoiai ua manaʻo ʻia he pōkole ke ola o ka poʻe me ka `(Sickle Cell Disease)`, ua hiki i nā lāʻau lapaʻau hou ke ola no nā makahiki he 50 a ʻoi me ka kaohi ʻana i nā hōʻailona.

Āhea ʻoe e ʻike ai i ke kauka?

Inā loaʻa iā ʻoe nā hōʻailona o ka anemia (nā mea a mākou i kamaʻilio ai ma mua, e like me ka luhi a me ka nāwaliwali), e ʻike pono i ke kauka.

ʻOiai inā manaʻo ʻoe ua olakino ʻoe a ʻaʻohe hōʻailona, ​​​​he mea nui e hana i nā nānā makahiki. Hiki i kāu kauka ke nānā i kāu mau hunaola koko. ʻO kahi hoʻāʻo koko maʻalahi, e like me ka helu koko piha (CBC), hiki ke kōkua i ka ʻike a me ka mālama ʻana i nā pilikia olakino ma mua o ko lākou lilo ʻana i mea koʻikoʻi.

He maʻi koʻikoʻi anei kēia "Poikilocytosis"?

ʻAʻole koʻikoʻi ka `(Poikilocytosis)`. Eia naʻe,Hiki iā ia ke lilo i hōʻailona o kahi maʻi olakino e hiki ai ke alakaʻi i nā pilikia inā ʻaʻole mālama ʻia. No laila, he mea nui e hoʻomaopopo pono i ke kumu o ka `(Poikilocytosis)` a e ʻimi i ka lāʻau lapaʻau inā pono.

ʻOiai paha he ʻano koʻikoʻi ka poikilocytosis, ʻaʻole ia. He ʻano wale nō ia o kou mau koko ʻulaʻula a nā kauka e hoʻohana ai e loiloi i kou olakino. Inā ʻike ʻoe he ʻano ʻē kou mau koko ʻulaʻula, mai kānalua e nīnau i kāu kauka e pili ana i ia mea. Hiki iā ia ke haʻi iā ʻoe inā e hoʻopilikia ana i kou olakino a, inā pēlā, he aha kāu e hiki ai ke hana e hoʻopau i ke ʻano a i ʻole e hoʻokele i ke ʻano kumu.

Nā mea nui a mākou e hoʻomanaʻo ai (Leka Lawe-Home)

ʻAe, ʻo nā kumu nui e hoʻomanaʻo ai mai nā mea a mākou i kamaʻilio ai, ʻo ia kēia:

  • ʻO ka poikilocytosis ka wā e ʻoi aku ma mua o 10% o kāu mau keʻena koko ʻulaʻula i ke ʻano kūpono ʻole.
  • ʻAʻole kēia he maʻi, akā he hōʻailona paha ia o kahi maʻi kumu.
  • Hiki ke ʻike ʻia nā hōʻailona o ka anemia (luhi, nāwaliwali, keʻokeʻo) i kēia hihia.
  • Hiki i nā kumu ke hānau ʻia a i loaʻa paha (nā hemahema meaʻai, kekahi mau maʻi).
  • Hiki ke ʻike ʻia kēia me kahi hoʻāʻo koko maʻalahi (`PBS`, `CBC`).
  • Aia ka lāʻau lapaʻau ma muli o ke kumu, akā hiki ke mālama pinepine ʻia.
  • ʻO ka mālama ʻana i kahi meaʻai olakino e hiki ke kōkua i ka pale ʻana i kekahi o nā kumu o ka hoʻomaka ʻana ma hope.
  • Inā he mau hōʻailona kou a i ʻole kānalua paha no kēia, ʻoi aku ka maikaʻi o ke kipa ʻana i ke kauka no ka ʻōlelo aʻo.

No laila, ke lana nei koʻu manaʻo he mea pono kēia ʻike iā ʻoe. E noho olakino!


ʻO Poikilocytosis, Nā Kelepona Koko ʻUlaʻula, Ke ʻAno o nā Kelepona Koko, Anemia, Nā Hoʻāʻo Koko, Ola Kino, Anemia, Nā Kelepona Koko ʻUlaʻula, Hoʻāʻo Koko

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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