Ke nāwaliwali mālie nei kou mau ʻiʻo? Hiki paha i kēia ke ʻano o ka Primary Lateral Sclerosis (PLS)?

Ke manaʻo nei ʻoe i kekahi manawa ua kaumaha iki kou mau wāwae, me he mea lā ua hana ʻia lākou i ka pōhaku? A i ʻole ke manaʻo nei ʻoe e nalowale ana kou kaulike i kou hele ʻana, a i ʻole e nalowale mālie ana kou ikaika i kou mau lālā? Inā ʻaʻole e hiki koke mai kēia mau hōʻailona, ​​akā e piʻi mālie a mālie, he mea nui paha iā ʻoe ke makaʻala i kēia ʻano i kapa ʻia ʻo Primary Lateral Sclerosis (PLS). Mai hopohopo, e kamaʻilio mākou e pili ana i nā mea āpau ma nā ʻōlelo maʻalahi.

I ka ʻōlelo maʻalahi, he aha ka sclerosis lateral mua (PLS)?

ʻO ka Primary Lateral Sclerosis, a i ʻole PLS no ka pōkole, he maʻi ia e hoʻopilikia ai i ko mākou mau aʻalolo a me nā ʻiʻo. Hoʻonāwaliwali mālie a/a i ʻole e paʻakikī ko mākou mau ʻiʻo.

I ka manawa pinepine, hoʻomaka mua kēia mau hōʻailona ma kou mau wāwae. I ka hala ʻana o ka manawa, hiki i kēia nāwaliwali a me ka ʻoʻoleʻa ke laha i nā ʻiʻo ʻē aʻe i loko o kou kino. He ʻano holomua kēia, ʻo ia hoʻi, e ʻoi mālie ana nā hōʻailona i ka hala ʻana o ka manawa.

ʻAʻohe lāʻau lapaʻau kūikawā no kēia maʻi (PLS), no laila ke kuhikuhi nui ʻia nei ka mālama ʻana i ka kaohi ʻana i nā hōʻailona a me ke kōkua ʻana iā ʻoe e hana maʻalahi i nā hana o kēlā me kēia lā. No ka laʻana, me ka hoʻohana ʻana i kahi mea kōkua e like me ke koʻokoʻo a i ʻole ka mea hele wāwae .

He maʻi kakaikahi loa kēia, ʻo ia hoʻi, ʻaʻole ia i ʻike pinepine ʻia i loko o ke kaiāulu.

He aha ka ʻokoʻa ma waena o PLS a me ALS?

Ua lohe paha ʻoe i kahi maʻi i kapa ʻia ʻo Amyotrophic Lateral Sclerosis (ALS) . ʻOiai ʻo nā maʻi ʻelua e pili ana i nā aʻalolo a me nā ʻiʻo, aia nā ʻokoʻa maopopo ma waena o nā mea ʻelua. No ka hoʻomaopopo ʻana i kēia, e nānā mua kākou pehea e kāohi ai ko kākou kino i ka neʻe ʻana.

Aia kekahi ʻano kūikawā o ke aʻalolo e lawe ana i nā leka mai ko kākou lolo i ko kākou mau ʻiʻo, kapa mākou iā lākou he mau neurons motor . ʻElua ʻano o kēia:

1. Nā Neuron Motor Luna (UMN): ʻO kēia nā 'uea nui' e lawe i nā leka mai ka lolo a i ke kaula kuamoʻo.

2. Nā Neuron Motor Haʻahaʻa (LMN): ʻO kēia nā 'sub-neurons' e lawe pololei i nā leka mai ke kaula spinal i nā ʻiʻo.

I kēia manawa, he mea nui loa ia e hoʻomaopopo i kēia ʻokoʻa.

Hiki i nā hōʻailona mua o ALS ke like loa me nā hōʻailona o PLS. No laila, i kekahi manawa e ʻike mua paha ke kauka iā ʻoe me PLS a laila hoʻololi iā ia i ALS ke ulu nā hōʻailona e hoʻopilikia pū i ka LMN. No kēia kumu, no ka hōʻoia pono ʻana i ka PLS, pono e nānā ʻia nā hōʻailona no ka liʻiliʻi o ʻekolu a ʻehā mau makahiki .

He aha nā hōʻailona o ka PLS?

Hōʻike mālie loa nā hōʻailona o PLS. Eia kekahi o nā hōʻailona mua āu e ʻike ai:

• ʻOʻoleʻa o nā ʻiʻo ma nā wāwae.
• Ka nāwaliwali o nā ʻiʻo ma nā wāwae.
• Ka paʻakikī i ka hele wāwae a i ʻole ka pilikia i ka mālama ʻana i ke kaulike.
• ʻŪmiʻi ʻana o nā ʻiʻo a i ʻole nā ​​ʻūmiʻi ʻeha a i ʻole ka ʻūmiʻi.

I ka holomua ʻana o ka maʻi, hiki ke ʻike ʻia nā hōʻailona ʻē aʻe:

• ʻOʻoleʻa a me ka nāwaliwali o nā ʻiʻo ma nā manamana lima, nā lima, a me nā lima.
• Ka paʻakikī o ka kaohi ʻana i ka mimi(Pono koke e mimi a me ke kahe ʻana o ka mimi).
• ʻEha kua a me ka ʻāʻī.

I nā hihia kakaikahi loa, hiki ke hoʻopilikia ʻia nā ʻiʻo o ke alelo. I kēia hihia, e ʻike paha ʻoe i nā hōʻailona e like me:

• ʻŌlelo pahee (Dysarthria).
• Ka paʻakikī i ka ale ʻana i ka meaʻai (Dysphagia).

He aha ke kumu o ka PLS?

ʻO kaʻoiaʻiʻo, ʻaʻole mākou i ʻike i ke kumu kikoʻī o PLS i nā pākeke. ʻO ka hapa nui o ka manawa, hiki wale mai ia me ka ʻole o ke kumu maopopo.

Eia nō naʻe, aia kekahi ʻano PLS kakaikahi loa e hoʻopilikia ai i nā keiki a me nā ʻōpio. Hoʻokumu ʻia ia e kahi mutation genetic (loli i ka DNA).

ʻO ka mea nui , ʻaʻole he maʻi hoʻoilina ka PLS. ʻO ke ʻano kēia, hiki iā ʻoe ke loaʻa iā ia inā ʻaʻohe mea o kou ʻohana i loaʻa iā ia ma mua.

ʻO wai ka mea i pilikia nui?

Hiki i kekahi ke loaʻa i ka PLS. Eia nō naʻe, ʻike pinepine ʻia nā maʻi ma kahi o 50 mau makahiki. Eia nō naʻe, hiki ke ulu i nā poʻe ʻōpio a ʻoi aku paha ma mua o kēlā. ʻOi aku ka maʻamau o ke ʻano i nā kāne ma mua o nā wahine .

Pehea e ʻike ʻia ai kēia maʻi?

Ma hope o ke aʻo ʻana e pili ana i kāu mau hōʻailona, ​​e hana kāu kauka i kahi hoʻokolohua kino a me ka neurological. Hiki iā lākou ke hana i nā hoʻokolohua e kāpae i nā kūlana ʻē aʻe i loaʻa nā hōʻailona like me PLS, e like me ALS a i ʻole multiple sclerosis. ʻO kekahi o kēia mau hoʻokolohua:

• Nā hoʻāʻo koko: E nānā i nā kumu ʻē aʻe.
• Nā hoʻokolohua Electrodiagnostic: Ke ana kēia i ka maikaʻi o ka hana ʻana o kou mau aʻalolo a me nā ʻiʻo.
• MRI scan: E kiʻi i nā kiʻi kikoʻī o ka lolo a me ke kaula spinal e ʻike ai inā he mau pilikia ʻē aʻe.
• ʻO ke kī ʻana o ka lumbar (spinal tap): Pili kēia i ka lawe ʻana i kahi wai liʻiliʻi mai kou iwi kuamoʻo a nānā iā ia no nā mea ʻē.

He aha nā lāʻau lapaʻau?

E like me kā mākou i ʻōlelo ai ma mua, ʻaʻohe lāʻau lapaʻau kūikawā no PLS. ʻO ke kumu o ka lāʻau lapaʻau ʻo ia ke kāohi ʻana i nā hōʻailona a me ke kōkua ʻana iā ʻoe e ola kūʻokoʻa e like me ka hiki.

• Nā lāʻau lapaʻau: Hāʻawi ʻia nā lāʻau lapaʻau e hōʻemi i ka ʻoʻoleʻa o nā ʻiʻo, ka ʻōʻopa, a me ka paʻakikī i ke ale ʻana (e like me Baclofen, Tizanidine, Quinine, Diazepam).
• Hoʻōla kino: Paipai ʻia ka hoʻoikaika kino e hōʻemi i ka nāwaliwali o nā mākala, hoʻonui i ka maʻalahi, a mālama i ka neʻe maikaʻi ʻana o nā hono.
• Nā mea kōkua: Hoʻohana ʻia nā mea e like me ke koʻokoʻo, ka mea hele wāwae , a i ʻole ka noho huila e kōkua iā ʻoe e neʻe kūʻokoʻa.
• ʻŌlelo lapaʻau: Inā pilikia ʻoe i ka ʻōlelo ʻana, hiki iā ia ke kōkua.

Āhea ʻoe e ʻike ai i ke kauka?

Inā manaʻo ʻoe e piʻi mālie ana kou ʻiʻo paʻakikī a nāwaliwali paha, e ʻike pono i kāu kauka.

Eia kekahi, inā ua ʻike mua ʻia ʻoe me PLS a ʻo ka lāʻau lapaʻau āu e lawe nei e hoʻonui ana i kāu mau hōʻailona a i ʻole ke kumu o nā hopena ʻaoʻao, e haʻi i kāu kauka e pili ana i kēlā.

Inā ʻeha ʻoe ma muli o ka hāʻule koke ʻana a i ʻole kahi ulia pōpilikia, e hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila.

He mea maʻamau ke kaumaha i ka wā e emi mālie ai kou ikaika o nā ʻiʻo a ʻaʻole hiki iā ʻoe ke hana i nā mea āu i hana ai ma mua. Inā ʻoe e hopohopo nei no kēia mau loli kino, hiki i ke kamaʻilio ʻana me ke kākāʻōlelo olakino noʻonoʻo ke kōkua.